MCID: CHR033
MIFTS: 30

Chordoid Glioma malady

Categories: Neuronal diseases, Rare diseases, Cancer diseases

Aliases & Classifications for Chordoid Glioma

Aliases & Descriptions for Chordoid Glioma:

Name: Chordoid Glioma 12 56 14
Chordoid Glioma of the Third Ventricle 69

Characteristics:

Orphanet epidemiological data:

56
chordoid glioma
Age of onset: Adult; Age of death: adult;

Classifications:

Orphanet: 56  
Rare neurological diseases


External Ids:

Disease Ontology 12 DOID:3774
NCIt 47 C5592
SNOMED-CT 64 128789002
Orphanet 56 ORPHA251674
ICD10 via Orphanet 34 C71.9
UMLS 69 C1322252

Summaries for Chordoid Glioma

MalaCards based summary : Chordoid Glioma, also known as chordoid glioma of the third ventricle, is related to third ventricle chordoid glioma and glioma. An important gene associated with Chordoid Glioma is GFAP (Glial Fibrillary Acidic Protein), and among its related pathways/superpathways are Neuroscience and Signaling by ERBB4. Affiliated tissues include brain, thyroid and testes, and related phenotypes are Increased proliferation and behavior/neurological

Related Diseases for Chordoid Glioma

Diseases related to Chordoid Glioma via text searches within MalaCards or GeneCards Suite gene sharing:

(show top 50) (show all 203)
id Related Disease Score Top Affiliating Genes
1 third ventricle chordoid glioma 12.3
2 glioma 10.7
3 lucey-driscoll syndrome 10.3 MUC1 S100B
4 secondary pulmonary hemosiderosis 10.3 MUC1 S100B
5 invasive mole 10.3 MUC1 S100B
6 myoma 10.3 MUC1 S100B
7 pemphigus vegetans 10.3 MUC1 S100B
8 corneal intraepithelial neoplasm 10.3 MUC1 S100B
9 subglottis verrucous carcinoma 10.3 MUC1 S100B
10 clear cell ependymoma 10.3 MUC1 S100B
11 endocardium cancer 10.3 MUC1 S100B
12 precursor t-lymphoblastic lymphoma/leukemia 10.3 MUC1 S100B
13 mediastinum liposarcoma 10.3 MUC1 S100B
14 bronchial mucus gland adenoma 10.2 GFAP S100B
15 adenofibroma 10.2 GFAP S100B
16 vagina leiomyosarcoma 10.2 GFAP MUC1
17 pulmonary neuroendocrine tumor 10.2 MUC1 S100B
18 hypogonadotropic hypogonadism-retinitis pigmentosa syndrome 10.2 GFAP S100B
19 uterine corpus leiomyomatosis 10.2 MUC1 S100B
20 piussan lenaerts mathieu syndrome 10.2 GFAP S100B
21 auricular cancer 10.2 GFAP S100B
22 skin glomus tumor 10.2 GFAP S100B
23 pediculus humanus corporis infestation 10.2 GFAP S100B
24 diarrhea, chronic, with villous atrophy 10.2 MUC1 S100B
25 cauda equina intradural extramedullary astrocytoma 10.2 GFAP MUC1
26 lacrimal gland mucoepidermoid carcinoma 10.2 MUC1 PGR
27 cervical lymphoepithelioma-like carcinoma 10.2 MUC1 PGR
28 exotropia 10.2 MUC1 PGR
29 desmoid tumor 10.2 MUC1 S100B
30 marfanoid hypermobility syndrome 10.2 MUC1 PGR
31 monostotic fibrous dysplasia 10.2 MUC1 S100B
32 bladder adenocarcinoma 10.2 MUC1 PGR
33 poliomyelitis 10.2 MUC1 PGR
34 papilloma 10.2 MUC1 PGR
35 avian influenza 10.2 MUC1 NKX2-1
36 popliteal pterygium syndrome, bartsocas-papas type 10.2 MUC1 S100B
37 nipple neoplasm 10.2 MUC1 PGR
38 sebaceous adenoma 10.2 MUC1 PGR
39 urea cycle disorder 10.2 GFAP S100B
40 mesenchymoma 10.2 MUC1 PGR
41 chromosome 9p deletion syndrome 10.2 GFAP NKX2-1
42 congenital muscular dystrophy with hyperlaxity 10.2 MUC1 NKX2-1
43 perinatal necrotizing enterocolitis 10.2 MUC1 PGR
44 mongolian spot 10.2 MUC1 S100B
45 central nervous system embryonal carcinoma 10.2 MUC1 NF2
46 immunodeficiency due to a classical component pathway complement deficiency 10.2 MUC1 NF2
47 anus adenocarcinoma 10.2 MUC1 PGR
48 sclerosing hemangioma 10.2 MUC1 PGR
49 pediatric cns embryonal cell carcinoma 10.2 GFAP NF2
50 lung clear cell carcinoma 10.2 MUC1 PGR

Graphical network of the top 20 diseases related to Chordoid Glioma:



Diseases related to Chordoid Glioma

Symptoms & Phenotypes for Chordoid Glioma

GenomeRNAi Phenotypes related to Chordoid Glioma according to GeneCards Suite gene sharing:

26
id Description GenomeRNAi Source Accession Score Top Affiliating Genes
1 Increased proliferation GR00094-A 8.62 NF2 TP53

MGI Mouse Phenotypes related to Chordoid Glioma:

44
id Description MGI Source Accession Score Top Affiliating Genes
1 behavior/neurological MP:0005386 9.63 GFAP NF2 NKX2-1 PGR S100B TP53
2 neoplasm MP:0002006 9.26 TP53 NF2 NKX2-1 PGR
3 normal MP:0002873 9.02 GFAP NKX2-1 PGR S100B TP53

Drugs & Therapeutics for Chordoid Glioma

Search Clinical Trials , NIH Clinical Center for Chordoid Glioma

Genetic Tests for Chordoid Glioma

Anatomical Context for Chordoid Glioma

MalaCards organs/tissues related to Chordoid Glioma:

39
Brain, Thyroid, Testes, Hypothalamus

Publications for Chordoid Glioma

Articles related to Chordoid Glioma:

(show top 50) (show all 64)
id Title Authors Year
1
Chordoid Glioma with Intraventricular Dissemination: A Case Report with Perfusion MR Imaging Features. ( 26798226 )
2016
2
Chordoid glioma of the third ventricle: a patient presenting with SIADH and a review of this rare tumor. ( 26879322 )
2016
3
Corrigendum to "The radiological findings of chordoid glioma: report of two cases, one case with MR spectroscopy" [Clin Imaging 39 (2015) 1086-1089]. ( 27133706 )
2016
4
Chordoid glioma: A new paradigm of hypothalamic dysfunction? ( 27798757 )
2016
5
Neurogenic fever in a patient with a chordoid glioma. ( 27856533 )
2016
6
Expanded Endoscopic Transnasal Approach to the Chordoid Glioma of the Third Ventricle : The First Case Ever Reported. ( 27847580 )
2016
7
Chordoid Glioma of Third Ventricle With an Epidermoid Cyst: Coexistence or Common Histogenesis? ( 27194402 )
2016
8
Chordoid glioma. ( 26668411 )
2015
9
Chordoid glioma: Case report and review of the literature. ( 25648470 )
2015
10
Chordoid glioma: a rare radiologically, histologically, and clinically mystifying lesion. ( 26018908 )
2015
11
Suprasellar chordoid neoplasm with expression of thyroid transcription factor 1: evidence that chordoid glioma of the third ventricle and pituicytoma may form part of a spectrum of lineage-related tumors of the basal forebrain. ( 25934249 )
2015
12
The radiological findings of chordoid glioma: report of two cases, one case with MR spectroscopy. ( 26275847 )
2015
13
Chordoid glioma of the third ventricle. ( 26543291 )
2015
14
Expression of thyroid transcription factor 1 in a chordoid glioma. ( 25248954 )
2014
15
Neuro-Ophthalmologic Features of Chordoid Glioma. ( 24113763 )
2013
16
Chordoid glioma of the third ventricle: four cases including one case with papillary features. ( 22716306 )
2013
17
Therapeutic approach to chordoid glioma of the third ventricle. ( 23615418 )
2013
18
Chordoid glioma of the third ventricle. ( 22754136 )
2012
19
Cytology of chordoid glioma of the third ventricle. ( 22246938 )
2012
20
Chordoid glioma: a rare suprasellar mass. ( 22644806 )
2012
21
Chordoid glioma in suprasellar location with extension into the third ventricle: smear preparation morphology of a rare tumor. ( 22246933 )
2012
22
CD99 is expressed in chordoid glioma and suggests ependymal origin. ( 22102064 )
2012
23
Chordoid glioma: a case report and literature review. ( 21192197 )
2011
24
Rarest of the rare: Chordoid glioma infiltrating the optic chiasm. ( 21697970 )
2011
25
Chordoid glioma of the third ventricle: a case report with review of literature. ( 21743188 )
2011
26
Chordoid glioma : a case report of unusual location and neuroradiological characteristics. ( 20717514 )
2010
27
Chordoid glioma: imaging pearls of a unique third ventricular tumor. ( 21059517 )
2010
28
Chordoid glioma: ten years of a low-grade tumor with high morbidity. ( 20808539 )
2010
29
Chordoid glioma with calcification and neurofilament expression: case report and review of the literature (Iwami et al. Surg Neurol 2008;10.1016/j.surneu.2007.07.032). ( 19329155 )
2009
30
Chordoid glioma: a case report and molecular characterization of five cases. ( 18652591 )
2009
31
Chordoid glioma of the third ventricle: a report of two cases, one with ultrastructural findings. ( 18498285 )
2009
32
Diabetes insipidus, panhypopituitarism, and severe mental status deterioration in a patient with chordoid glioma: case report and literature review. ( 19364693 )
2009
33
Chordoid glioma with calcification and neurofilament expression: case report and review of the literature. ( 18262609 )
2009
34
Chordoid glioma of the third ventricle attached to the optic chiasm. Successful removal through a trans-lamina terminalis approach. ( 18597929 )
2008
35
Chordoid glioma: report of two rare examples with unusual features. ( 18246456 )
2008
36
Chordoid glioma of the third ventricle. ( 18936876 )
2008
37
An incidentally detected third ventricle chordoid glioma. ( 18040120 )
2007
38
Extraventricular unusual glioma in a child with extensive myxoid change resembling chordoid glioma. ( 17965223 )
2007
39
Chordoid glioma of the third ventricle. ( 16568345 )
2006
40
Test and teach. A recurrent third ventricular brain tumour. Diagnosis: Chordoid glioma of the third ventricle. ( 16753749 )
2006
41
Third ventricular chordoid glioma with unusual aggressive behavior. ( 17185888 )
2006
42
Chordoid glioma of the third ventricle: Report of a case with cytologic features and utility during intraoperative consultation. ( 17152286 )
2006
43
The elusive origin of chordoid glioma. ( 16594734 )
2006
44
Origin of chordoid glioma of the third ventricle. ( 16594739 )
2006
45
Third ventricular chordoid glioma: clinicopathological study of two cases with evidence for a poor clinical outcome despite low grade histological features. ( 16008819 )
2005
46
Chordoid glioma: clinicopathologic profile and differential diagnosis of an uncommon tumor. ( 15504076 )
2004
47
Suprasellar chordoid glioma combined with Rathke's cleft cyst. ( 14629303 )
2003
48
Immunohistochemical and ultrastructural study of chordoid glioma of the third ventricle: its tanycytic differentiation. ( 12748871 )
2003
49
Chordoid glioma: report of a case with unusual histologic features, ultrastructural study and review of the literature. ( 12814253 )
2003
50
Third ventricular chordoid glioma: case report and review of the literature. ( 12765825 )
2003

Variations for Chordoid Glioma

Expression for Chordoid Glioma

Search GEO for disease gene expression data for Chordoid Glioma.

Pathways for Chordoid Glioma

Pathways related to Chordoid Glioma according to GeneCards Suite gene sharing:

id Super pathways Score Top Affiliating Genes
1 11.43 GFAP NF2 NKX2-1 S100B
2
Show member pathways
11.17 GFAP PGR S100B

GO Terms for Chordoid Glioma

Biological processes related to Chordoid Glioma according to GeneCards Suite gene sharing:

id Name GO ID Score Top Affiliating Genes
1 DNA damage response, signal transduction by p53 class mediator resulting in cell cycle arrest GO:0006977 8.96 MUC1 TP53
2 DNA damage response, signal transduction by p53 class mediator resulting in transcription of p21 class mediator GO:0006978 8.62 MUC1 TP53

Molecular functions related to Chordoid Glioma according to GeneCards Suite gene sharing:

id Name GO ID Score Top Affiliating Genes
1 enzyme binding GO:0019899 8.8 NKX2-1 PGR TP53

Sources for Chordoid Glioma

3 CDC
7 CNVD
9 Cosmic
10 dbSNP
11 DGIdb
16 ExPASy
18 FMA
28 GO
29 GTR
30 HGMD
31 HMDB
32 HPO
33 ICD10
34 ICD10 via Orphanet
35 ICD9CM
36 IUPHAR
37 KEGG
38 LifeMap
40 MedGen
42 MeSH
43 MESH via Orphanet
44 MGI
46 NCI
47 NCIt
48 NDF-RT
51 NINDS
52 Novoseek
54 OMIM
55 OMIM via Orphanet
59 PubMed
60 QIAGEN
65 SNOMED-CT via Orphanet
67 TGDB
68 Tocris
69 UMLS
70 UMLS via Orphanet
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