MCID: CHR033
MIFTS: 30

Chordoid Glioma malady

Categories: Neuronal diseases, Rare diseases, Cancer diseases

Aliases & Classifications for Chordoid Glioma

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Sources:
11Disease Ontology, 13DISEASES, 31ICD10 via Orphanet, 45NCIt, 54Orphanet, 62SNOMED-CT, 68UMLS
See all MalaCards sources

Aliases & Descriptions for Chordoid Glioma:

Name: Chordoid Glioma 11 54 13
 
Chordoid Glioma of the Third Ventricle 68

Characteristics:

Orphanet epidemiological data:

54
chordoid glioma:
Age of onset: Adult; Age of death: adult

Classifications:



External Ids:

Disease Ontology11 DOID:3774
NCIt45 C5592
SNOMED-CT62 128789002
Orphanet54 ORPHA251674
ICD10 via Orphanet31 C71.9

Summaries for Chordoid Glioma

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MalaCards based summary: Chordoid Glioma, also known as chordoid glioma of the third ventricle, is related to third ventricle chordoid glioma and glioma. An important gene associated with Chordoid Glioma is GFAP (Glial Fibrillary Acidic Protein), and among its related pathways are Signaling by ERBB4 and Neuroscience. Affiliated tissues include brain, thyroid and hypothalamus, and related mouse phenotypes are Increased proliferation and neoplasm.

Related Diseases for Chordoid Glioma

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Diseases related to Chordoid Glioma via text searches within MalaCards or GeneCards Suite gene sharing:

(show top 50)    (show all 203)
idRelated DiseaseScoreTop Affiliating Genes
1third ventricle chordoid glioma12.3
2glioma10.7
3lucey-driscoll syndrome10.3MUC1, S100B
4secondary pulmonary hemosiderosis10.3MUC1, S100B
5invasive mole10.3MUC1, S100B
6myoma10.3MUC1, S100B
7pemphigus vegetans10.3MUC1, S100B
8corneal intraepithelial neoplasm10.3MUC1, S100B
9subglottis verrucous carcinoma10.3MUC1, S100B
10clear cell ependymoma10.3MUC1, S100B
11endocardium cancer10.3MUC1, S100B
12precursor t-lymphoblastic lymphoma/leukemia10.3MUC1, S100B
13mediastinum liposarcoma10.3MUC1, S100B
14bronchial mucus gland adenoma10.2GFAP, S100B
15adenofibroma10.2GFAP, S100B
16vagina leiomyosarcoma10.2GFAP, MUC1
17pulmonary neuroendocrine tumor10.2MUC1, S100B
18hypogonadotropic hypogonadism-retinitis pigmentosa syndrome10.2GFAP, S100B
19uterine corpus leiomyomatosis10.2MUC1, S100B
20piussan lenaerts mathieu syndrome10.2GFAP, S100B
21auricular cancer10.2GFAP, S100B
22skin glomus tumor10.2GFAP, S100B
23pediculus humanus corporis infestation10.2GFAP, S100B
24diarrhea, chronic, with villous atrophy10.2MUC1, S100B
25cauda equina intradural extramedullary astrocytoma10.2GFAP, MUC1
26lacrimal gland mucoepidermoid carcinoma10.2MUC1, PGR
27cervical lymphoepithelioma-like carcinoma10.2MUC1, PGR
28exotropia10.2MUC1, PGR
29desmoid tumor10.2MUC1, S100B
30marfanoid hypermobility syndrome10.2MUC1, PGR
31monostotic fibrous dysplasia10.2MUC1, S100B
32bladder adenocarcinoma10.2MUC1, PGR
33poliomyelitis10.2MUC1, PGR
34papilloma10.2MUC1, PGR
35avian influenza10.2MUC1, NKX2-1
36popliteal pterygium syndrome, bartsocas-papas type10.2MUC1, S100B
37nipple neoplasm10.2MUC1, PGR
38sebaceous adenoma10.2MUC1, PGR
39urea cycle disorder10.2GFAP, S100B
40mesenchymoma10.2MUC1, PGR
41chromosome 9p deletion syndrome10.2GFAP, NKX2-1
42congenital muscular dystrophy with hyperlaxity10.2MUC1, NKX2-1
43perinatal necrotizing enterocolitis10.2MUC1, PGR
44mongolian spot10.2MUC1, S100B
45central nervous system embryonal carcinoma10.2MUC1, NF2
46immunodeficiency due to a classical component pathway complement deficiency10.2MUC1, NF2
47anus adenocarcinoma10.2MUC1, PGR
48sclerosing hemangioma10.2MUC1, PGR
49pediatric cns embryonal cell carcinoma10.2GFAP, NF2
50lung clear cell carcinoma10.2MUC1, PGR

Graphical network of the top 20 diseases related to Chordoid Glioma:



Diseases related to chordoid glioma

Symptoms & Phenotypes for Chordoid Glioma

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GenomeRNAi Phenotypes related to Chordoid Glioma according to GeneCards Suite gene sharing:

26
idDescriptionGenomeRNAi Source AccessionScoreTop Affiliating Genes
1GR00094-A10.3NF2, TP53

MGI Mouse Phenotypes related to Chordoid Glioma according to GeneCards Suite gene sharing:

41
idDescriptionMGI Source AccessionScoreTop Affiliating Genes
1MP:00020069.3NF2, NKX2-1, PGR, TP53
2MP:00053868.3GFAP, NF2, NKX2-1, PGR, S100B, TP53
3MP:00028738.0GFAP, NKX2-1, PGR, S100B, TP53

Drugs & Therapeutics for Chordoid Glioma

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Interventional clinical trials:

Search ClinicalTrials, NIH Clinical Center for Chordoid Glioma

Genetic Tests for Chordoid Glioma

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Anatomical Context for Chordoid Glioma

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MalaCards organs/tissues related to Chordoid Glioma:

36
Brain, Thyroid, Hypothalamus, Testes

Publications for Chordoid Glioma

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Articles related to Chordoid Glioma:

(show top 50)    (show all 64)
idTitleAuthorsYear
1
Chordoid Glioma with Intraventricular Dissemination: A Case Report with Perfusion MR Imaging Features. (26798226)
2016
2
Chordoid glioma of the third ventricle: a patient presenting with SIADH and a review of this rare tumor. (26879322)
2016
3
Corrigendum to "The radiological findings of chordoid glioma: report of two cases, one case with MR spectroscopy" [Clin Imaging 39 (2015) 1086-1089]. (27133706)
2016
4
Chordoid glioma: A new paradigm of hypothalamic dysfunction? (27798757)
2016
5
Neurogenic fever in a patient with a chordoid glioma. (27856533)
2016
6
Expanded Endoscopic Transnasal Approach to the Chordoid Glioma of the Third Ventricle : The First Case Ever Reported. (27847580)
2016
7
Chordoid Glioma of Third Ventricle With an Epidermoid Cyst: Coexistence or Common Histogenesis? (27194402)
2016
8
Chordoid glioma. (26668411)
2015
9
Chordoid glioma: Case report and review of the literature. (25648470)
2015
10
Chordoid glioma: a rare radiologically, histologically, and clinically mystifying lesion. (26018908)
2015
11
Suprasellar chordoid neoplasm with expression of thyroid transcription factor 1: evidence that chordoid glioma of the third ventricle and pituicytoma may form part of a spectrum of lineage-related tumors of the basal forebrain. (25934249)
2015
12
The radiological findings of chordoid glioma: report of two cases, one case with MR spectroscopy. (26275847)
2015
13
Chordoid glioma of the third ventricle. (26543291)
2015
14
Expression of thyroid transcription factor 1 in a chordoid glioma. (25248954)
2014
15
Neuro-Ophthalmologic Features of Chordoid Glioma. (24113763)
2013
16
Chordoid glioma of the third ventricle: four cases including one case with papillary features. (22716306)
2013
17
Therapeutic approach to chordoid glioma of the third ventricle. (23615418)
2013
18
Chordoid glioma of the third ventricle. (22754136)
2012
19
Cytology of chordoid glioma of the third ventricle. (22246938)
2012
20
Chordoid glioma: a rare suprasellar mass. (22644806)
2012
21
Chordoid glioma in suprasellar location with extension into the third ventricle: smear preparation morphology of a rare tumor. (22246933)
2012
22
CD99 is expressed in chordoid glioma and suggests ependymal origin. (22102064)
2012
23
Chordoid glioma: a case report and literature review. (21192197)
2011
24
Rarest of the rare: Chordoid glioma infiltrating the optic chiasm. (21697970)
2011
25
Chordoid glioma of the third ventricle: a case report with review of literature. (21743188)
2011
26
Chordoid glioma : a case report of unusual location and neuroradiological characteristics. (20717514)
2010
27
Chordoid glioma: imaging pearls of a unique third ventricular tumor. (21059517)
2010
28
Chordoid glioma: ten years of a low-grade tumor with high morbidity. (20808539)
2010
29
Chordoid glioma with calcification and neurofilament expression: case report and review of the literature (Iwami et al. Surg Neurol 2008;10.1016/j.surneu.2007.07.032). (19329155)
2009
30
Chordoid glioma: a case report and molecular characterization of five cases. (18652591)
2009
31
Chordoid glioma of the third ventricle: a report of two cases, one with ultrastructural findings. (18498285)
2009
32
Diabetes insipidus, panhypopituitarism, and severe mental status deterioration in a patient with chordoid glioma: case report and literature review. (19364693)
2009
33
Chordoid glioma with calcification and neurofilament expression: case report and review of the literature. (18262609)
2009
34
Chordoid glioma of the third ventricle attached to the optic chiasm. Successful removal through a trans-lamina terminalis approach. (18597929)
2008
35
Chordoid glioma: report of two rare examples with unusual features. (18246456)
2008
36
Chordoid glioma of the third ventricle. (18936876)
2008
37
An incidentally detected third ventricle chordoid glioma. (18040120)
2007
38
Extraventricular unusual glioma in a child with extensive myxoid change resembling chordoid glioma. (17965223)
2007
39
Chordoid glioma of the third ventricle. (16568345)
2006
40
Test and teach. A recurrent third ventricular brain tumour. Diagnosis: Chordoid glioma of the third ventricle. (16753749)
2006
41
Third ventricular chordoid glioma with unusual aggressive behavior. (17185888)
2006
42
Chordoid glioma of the third ventricle: Report of a case with cytologic features and utility during intraoperative consultation. (17152286)
2006
43
The elusive origin of chordoid glioma. (16594734)
2006
44
Origin of chordoid glioma of the third ventricle. (16594739)
2006
45
Third ventricular chordoid glioma: clinicopathological study of two cases with evidence for a poor clinical outcome despite low grade histological features. (16008819)
2005
46
Chordoid glioma: clinicopathologic profile and differential diagnosis of an uncommon tumor. (15504076)
2004
47
Suprasellar chordoid glioma combined with Rathke's cleft cyst. (14629303)
2003
48
Immunohistochemical and ultrastructural study of chordoid glioma of the third ventricle: its tanycytic differentiation. (12748871)
2003
49
Chordoid glioma: report of a case with unusual histologic features, ultrastructural study and review of the literature. (12814253)
2003
50
Third ventricular chordoid glioma: case report and review of the literature. (12765825)
2003

Variations for Chordoid Glioma

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Expression for genes affiliated with Chordoid Glioma

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Search GEO for disease gene expression data for Chordoid Glioma.

Pathways for genes affiliated with Chordoid Glioma

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Pathways related to Chordoid Glioma according to GeneCards Suite gene sharing:

idSuper pathwaysScoreTop Affiliating Genes
1
Show member pathways
9.0GFAP, PGR, S100B
28.6GFAP, NF2, NKX2-1, S100B

GO Terms for genes affiliated with Chordoid Glioma

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Biological processes related to Chordoid Glioma according to GeneCards Suite gene sharing:

idNameGO IDScoreTop Affiliating Genes
1DNA damage response, signal transduction by p53 class mediator resulting in cell cycle arrestGO:00069779.4MUC1, TP53
2DNA damage response, signal transduction by p53 class mediator resulting in transcription of p21 class mediatorGO:00069789.1MUC1, TP53

Molecular functions related to Chordoid Glioma according to GeneCards Suite gene sharing:

idNameGO IDScoreTop Affiliating Genes
1enzyme bindingGO:00198999.0NKX2-1, PGR, TP53

Sources for Chordoid Glioma

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2CDC
6CNVD
10DGIdb
15ExPASy
16FDA
17FMA
27GTR
28HGMD
29HMDB
30ICD10
31ICD10 via Orphanet
32ICD9CM
33IUPHAR
34KEGG
37MedGen
39MeSH
40MESH via Orphanet
41MGI
44NCI
45NCIt
46NDF-RT
49NINDS
50Novoseek
52OMIM
53OMIM via Orphanet
57PubMed
58QIAGEN
63SNOMED-CT via Orphanet
67Tumor Gene Family of Databases
68UMLS
69UMLS via Orphanet