MCID: CHR033
MIFTS: 33

Chordoid Glioma

Categories: Neuronal diseases, Rare diseases, Cancer diseases

Aliases & Classifications for Chordoid Glioma

MalaCards integrated aliases for Chordoid Glioma:

Name: Chordoid Glioma 12 55 14
Chordoid Glioma of the Third Ventricle 69

Characteristics:

Orphanet epidemiological data:

55
chordoid glioma
Age of onset: Adult; Age of death: adult;

Classifications:

Orphanet: 55  
Rare neurological diseases


External Ids:

Disease Ontology 12 DOID:3774
NCIt 46 C5592
SNOMED-CT 64 128789002
Orphanet 55 ORPHA251674
ICD10 via Orphanet 33 C71.9
UMLS 69 C1322252

Summaries for Chordoid Glioma

MalaCards based summary : Chordoid Glioma, also known as chordoid glioma of the third ventricle, is related to third ventricle chordoid glioma and glioma. An important gene associated with Chordoid Glioma is GFAP (Glial Fibrillary Acidic Protein), and among its related pathways/superpathways are Neuroscience and Signaling by ERBB4. Affiliated tissues include brain, thyroid and hypothalamus, and related phenotypes are Increased proliferation and behavior/neurological

Related Diseases for Chordoid Glioma

Diseases related to Chordoid Glioma via text searches within MalaCards or GeneCards Suite gene sharing:

(show top 50) (show all 217)
# Related Disease Score Top Affiliating Genes
1 third ventricle chordoid glioma 12.4
2 glioma 10.8
3 localized hypertrophic neuropathy 10.4 MUC1 S100B
4 sclerosing perineurioma 10.4 MUC1 S100B
5 reticular perineurioma 10.4 MUC1 S100B
6 non-functioning pituitary adenoma 10.4 MUC1 S100B
7 epithelioid malignant peripheral nerve sheath tumor 10.4 MUC1 S100B
8 ossifying fibromyxoid tumor 10.4 MUC1 S100B
9 myxofibrosarcoma 10.4 MUC1 S100B
10 eccrine porocarcinoma 10.4 MUC1 S100B
11 aggressive digital papillary adenocarcinoma 10.4 MUC1 S100B
12 monophasic synovial sarcoma 10.4 MUC1 S100B
13 pleomorphic liposarcoma 10.4 MUC1 S100B
14 spindle cell sarcoma 10.4 MUC1 S100B
15 parachordoma 10.4 GFAP MUC1
16 spindle cell rhabdomyosarcoma 10.4 GFAP MUC1
17 functioning pituitary adenoma 10.4 MUC1 S100B
18 meningeal melanocytoma 10.4 MUC1 S100B
19 dendritic cell tumor 10.4 MUC1 S100B
20 gemistocytic astrocytoma 10.4 GFAP S100B
21 hemangiopericytoma, malignant 10.4 MUC1 S100B
22 dysembryoplastic neuroepithelial tumor 10.3 GFAP S100B
23 polymorphous low-grade adenocarcinoma 10.3 MUC1 S100B
24 breast mucoepidermoid carcinoma 10.3 MUC1 PGR
25 angiocentric glioma 10.3 GFAP S100B
26 breast scirrhous carcinoma 10.3 MUC1 PGR
27 endosalpingiosis 10.3 MUC1 PGR
28 intraneural perineurioma 10.3 MUC1 S100B
29 pineocytoma 10.3 GFAP S100B
30 malignant mixed mullerian tumor 10.3 MUC1 PGR
31 mucinous bronchioloalveolar adenocarcinoma 10.3 MUC1 NKX2-1
32 endometrial mucinous adenocarcinoma 10.3 MUC1 PGR
33 apocrine adenocarcinoma 10.3 MUC1 PGR
34 papillary ependymoma 10.3 GFAP S100B
35 malignant fibroxanthoma 10.3 MUC1 S100B
36 sarcomatoid mesothelioma 10.3 MUC1 NKX2-1
37 subependymal giant cell astrocytoma 10.3 GFAP S100B
38 granular cell tumor 10.3 GFAP S100B
39 perivascular epithelioid cell tumor 10.3 MUC1 PGR
40 sertoli-leydig cell tumor 10.3 MUC1 PGR
41 histiocytic sarcoma 10.3 MUC1 S100B
42 extraskeletal ewing sarcoma 10.3 MUC1 NKX2-1
43 pilomatrixoma 10.3 MUC1 S100B
44 sclerosing hemangioma 10.3 MUC1 NKX2-1
45 dermoid cyst 10.3 MUC1 PGR
46 traumatic brain injury 10.3 GFAP S100B
47 pancreatic gastrinoma 10.3 GFAP S100B
48 chickenpox 10.3 MUC1 PGR
49 breast secretory carcinoma 10.3 MUC1 PGR
50 malignant peritoneal mesothelioma 10.3 MUC1 NF2

Graphical network of the top 20 diseases related to Chordoid Glioma:



Diseases related to Chordoid Glioma

Symptoms & Phenotypes for Chordoid Glioma

GenomeRNAi Phenotypes related to Chordoid Glioma according to GeneCards Suite gene sharing:

25
# Description GenomeRNAi Source Accession Score Top Affiliating Genes
1 Increased proliferation GR00094-A 8.62 NF2 TP53

MGI Mouse Phenotypes related to Chordoid Glioma:

43
# Description MGI Source Accession Score Top Affiliating Genes
1 behavior/neurological MP:0005386 9.63 NKX2-1 PGR S100B TP53 GFAP NF2
2 neoplasm MP:0002006 9.26 NKX2-1 PGR TP53 NF2
3 normal MP:0002873 9.02 NKX2-1 PGR S100B TP53 GFAP

Drugs & Therapeutics for Chordoid Glioma

Search Clinical Trials , NIH Clinical Center for Chordoid Glioma

Genetic Tests for Chordoid Glioma

Anatomical Context for Chordoid Glioma

MalaCards organs/tissues related to Chordoid Glioma:

38
Brain, Thyroid, Hypothalamus, Testes

Publications for Chordoid Glioma

Articles related to Chordoid Glioma:

(show top 50) (show all 68)
# Title Authors Year
1
The trans-laminar terminalis approach reduces mortalities associated with chordoid glioma resections: A case report and a review of 20a8^years of literature. ( 29066234 )
2018
2
Chordoid glioma of the third ventricle: report of a rapidly progressive case. ( 28315998 )
2017
3
Chordoid Glioma: A Neoplasm Found in the Anterior Part of the Third Ventricle. ( 28708638 )
2017
4
Management in chordoid glioma: Avoiding the pitfalls in this rare and challenging entity. ( 28681757 )
2017
5
Chordoid glioma of the third ventricle: a patient presenting with SIADH and a review of this rare tumor. ( 26879322 )
2016
6
Expanded Endoscopic Transnasal Approach to the Chordoid Glioma of the Third Ventricle : The First Case Ever Reported. ( 27847580 )
2016
7
Neurogenic fever in a patient with a chordoid glioma. ( 27856533 )
2016
8
Corrigendum to "The radiological findings of chordoid glioma: report of two cases, one case with MR spectroscopy" [Clin Imaging 39 (2015) 1086-1089]. ( 27133706 )
2016
9
Chordoid Glioma of Third Ventricle With an Epidermoid Cyst: Coexistence or Common Histogenesis? ( 27194402 )
2016
10
Chordoid glioma: A new paradigm of hypothalamic dysfunction? ( 27798757 )
2016
11
Chordoid Glioma with Intraventricular Dissemination: A Case Report with Perfusion MR Imaging Features. ( 26798226 )
2016
12
Chordoid glioma: Case report and review of the literature. ( 25648470 )
2015
13
Chordoid glioma. ( 26668411 )
2015
14
Suprasellar chordoid neoplasm with expression of thyroid transcription factor 1: evidence that chordoid glioma of the third ventricle and pituicytoma may form part of a spectrum of lineage-related tumors of the basal forebrain. ( 25934249 )
2015
15
The radiological findings of chordoid glioma: report of two cases, one case with MR spectroscopy. ( 26275847 )
2015
16
Chordoid glioma: a rare radiologically, histologically, and clinically mystifying lesion. ( 26018908 )
2015
17
Chordoid glioma of the third ventricle. ( 26543291 )
2015
18
Expression of thyroid transcription factor 1 in a chordoid glioma. ( 25248954 )
2014
19
Chordoid glioma of the third ventricle: four cases including one case with papillary features. ( 22716306 )
2013
20
Therapeutic approach to chordoid glioma of the third ventricle. ( 23615418 )
2013
21
Neuro-Ophthalmologic Features of Chordoid Glioma. ( 24113763 )
2013
22
Cytology of chordoid glioma of the third ventricle. ( 22246938 )
2012
23
Chordoid glioma of the third ventricle. ( 22754136 )
2012
24
CD99 is expressed in chordoid glioma and suggests ependymal origin. ( 22102064 )
2012
25
Chordoid glioma: a rare suprasellar mass. ( 22644806 )
2012
26
Chordoid glioma in suprasellar location with extension into the third ventricle: smear preparation morphology of a rare tumor. ( 22246933 )
2012
27
Chordoid glioma of the third ventricle: a case report with review of literature. ( 21743188 )
2011
28
Chordoid glioma: a case report and literature review. ( 21192197 )
2011
29
Rarest of the rare: Chordoid glioma infiltrating the optic chiasm. ( 21697970 )
2011
30
Chordoid glioma : a case report of unusual location and neuroradiological characteristics. ( 20717514 )
2010
31
Chordoid glioma: ten years of a low-grade tumor with high morbidity. ( 20808539 )
2010
32
Chordoid glioma: imaging pearls of a unique third ventricular tumor. ( 21059517 )
2010
33
Chordoid glioma of the third ventricle: a report of two cases, one with ultrastructural findings. ( 18498285 )
2009
34
Diabetes insipidus, panhypopituitarism, and severe mental status deterioration in a patient with chordoid glioma: case report and literature review. ( 19364693 )
2009
35
Chordoid glioma: a case report and molecular characterization of five cases. ( 18652591 )
2009
36
Chordoid glioma with calcification and neurofilament expression: case report and review of the literature. ( 18262609 )
2009
37
Chordoid glioma with calcification and neurofilament expression: case report and review of the literature (Iwami et al. Surg Neurol 2008;10.1016/j.surneu.2007.07.032). ( 19329155 )
2009
38
Chordoid glioma of the third ventricle attached to the optic chiasm. Successful removal through a trans-lamina terminalis approach. ( 18597929 )
2008
39
Chordoid glioma of the third ventricle. ( 18936876 )
2008
40
Chordoid glioma: report of two rare examples with unusual features. ( 18246456 )
2008
41
An incidentally detected third ventricle chordoid glioma. ( 18040120 )
2007
42
Extraventricular unusual glioma in a child with extensive myxoid change resembling chordoid glioma. ( 17965223 )
2007
43
Third ventricular chordoid glioma with unusual aggressive behavior. ( 17185888 )
2006
44
Chordoid glioma of the third ventricle. ( 16568345 )
2006
45
Test and teach. A recurrent third ventricular brain tumour. Diagnosis: Chordoid glioma of the third ventricle. ( 16753749 )
2006
46
Chordoid glioma of the third ventricle: Report of a case with cytologic features and utility during intraoperative consultation. ( 17152286 )
2006
47
Origin of chordoid glioma of the third ventricle. ( 16594739 )
2006
48
The elusive origin of chordoid glioma. ( 16594734 )
2006
49
Third ventricular chordoid glioma: clinicopathological study of two cases with evidence for a poor clinical outcome despite low grade histological features. ( 16008819 )
2005
50
Chordoid glioma: clinicopathologic profile and differential diagnosis of an uncommon tumor. ( 15504076 )
2004

Variations for Chordoid Glioma

Expression for Chordoid Glioma

Search GEO for disease gene expression data for Chordoid Glioma.

Pathways for Chordoid Glioma

Pathways related to Chordoid Glioma according to GeneCards Suite gene sharing:

# Super pathways Score Top Affiliating Genes
1 11.46 GFAP NF2 NKX2-1 S100B
2
Show member pathways
11.17 GFAP PGR S100B

GO Terms for Chordoid Glioma

Biological processes related to Chordoid Glioma according to GeneCards Suite gene sharing:

# Name GO ID Score Top Affiliating Genes
1 DNA damage response, signal transduction by p53 class mediator resulting in cell cycle arrest GO:0006977 9.16 MUC1 TP53
2 long-term synaptic potentiation GO:0060291 8.96 GFAP S100B
3 DNA damage response, signal transduction by p53 class mediator resulting in transcription of p21 class mediator GO:0006978 8.62 MUC1 TP53

Molecular functions related to Chordoid Glioma according to GeneCards Suite gene sharing:

# Name GO ID Score Top Affiliating Genes
1 enzyme binding GO:0019899 9.13 NKX2-1 PGR TP53
2 identical protein binding GO:0042802 8.92 GFAP PGR S100B TP53

Sources for Chordoid Glioma

3 CDC
7 CNVD
9 Cosmic
10 dbSNP
11 DGIdb
16 ExPASy
18 FMA
27 GO
28 GTR
29 HGMD
30 HMDB
31 HPO
32 ICD10
33 ICD10 via Orphanet
34 ICD9CM
35 IUPHAR
36 KEGG
37 LifeMap
39 MedGen
41 MeSH
42 MESH via Orphanet
43 MGI
45 NCI
46 NCIt
47 NDF-RT
50 NINDS
51 Novoseek
53 OMIM
54 OMIM via Orphanet
58 PubMed
60 QIAGEN
65 SNOMED-CT via HPO
66 SNOMED-CT via Orphanet
67 TGDB
68 Tocris
69 UMLS
70 UMLS via Orphanet
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