MCID: CHY006
MIFTS: 36

Chylous Ascites malady

Categories: Rare diseases, Cardiovascular diseases, Fetal diseases

Aliases & Classifications for Chylous Ascites

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Sources:
45NIH Rare Diseases, 51Orphanet, 65UMLS, 47Novoseek, 28ICD10 via Orphanet, 37MESH via Orphanet, 66UMLS via Orphanet, 61The Human Phenotype Ontology
See all MalaCards sources

Aliases & Descriptions for Chylous Ascites:

Name: Chylous Ascites 45 51 65
Congenital Chylous Ascites 45 65
 
Ascites Chylous 47

Characteristics:



Classifications:



External Ids:

Orphanet51 1160
ICD10 via Orphanet28 I89.8
MESH via Orphanet37 D002915
UMLS via Orphanet66 C0008732
UMLS65 C0008732, C2930811

Summaries for Chylous Ascites

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MalaCards based summary: Chylous Ascites, also known as congenital chylous ascites, is related to liver disease and peritonitis, and has symptoms including lymphedema, abnormality of the skin and neoplasm. An important gene associated with Chylous Ascites is ALB (Albumin). Affiliated tissues include liver, heart and lymph node.

Related Diseases for Chylous Ascites

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Graphical network of the top 20 diseases related to Chylous Ascites:



Diseases related to chylous ascites

Symptoms for Chylous Ascites

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Symptoms:

 51 (show all 7)
  • ascitis
  • lymphedema
  • subcutaneous nodules/lipomas/tumefaction/swelling
  • glaucoma
  • intestinal/colonic anomaly
  • pancreatitis
  • neoplasms/tumors

HPO human phenotypes related to Chylous Ascites:

(show all 8)
id Description Frequency HPO Source Accession
1 lymphedema hallmark (90%) HP:0001004
2 abnormality of the skin typical (50%) HP:0000951
3 neoplasm occasional (7.5%) HP:0002664
4 abnormality of the intestine occasional (7.5%) HP:0002242
5 pancreatitis occasional (7.5%) HP:0001733
6 glaucoma occasional (7.5%) HP:0000501
7 chylous ascites HP:0012281
8 glaucoma HP:0000501

Drugs & Therapeutics for Chylous Ascites

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Drugs for Chylous Ascites (from DrugBank, HMDB, Dgidb, PharmGKB, IUPHAR, NovoSeek, BitterDB):

idNameStatusPhaseClinical TrialsCas NumberPubChem Id
1
Octreotideapproved, investigationalPhase 219883150-76-9383414, 6400441
Synonyms:
(4R,7S,10S,13R,16S,19R)-10-(4-aminobutyl)-19-[[(2R)-2-amino-3-phenylpropanoyl]amino]-16-benzyl-N-[(2R,3R)-1,3-dihydroxybutan-2-yl]-7-[(1R)-1-hydroxyethyl]-13-(1H-indol-3-ylmethyl)-6,9,12,15,18-pentaoxo-1,2-dithia-5,8,11,14,17-pentazacycloicosane-4-carboxamide
10-(4-Aminobutyl)-19-((2-amino-3-phenylpropanoyl)amino)-16-benzyl-7-(1-hydroxyethyl)-N-(2-hydroxy-1-(hydroxymethyl)propyl)-13-(1H-indol-3-ylmethyl)-6,9,12,15,18-pentaoxo-1,2-dithia-5,8,11,14,17-pentaa
10-(4-aminobutyl)-19-[(2-amino-3-phenylpropanoyl)amino]-16-benzyl-N-(1,3-dihydroxybutan-2-yl)-7-(1-hydroxyethyl)-13-(1H-indol-3-ylmethyl)-6,9,12,15,18-pentaoxo-1,2-dithia-5,8,11,14,17-pentazacycloicosane-4-carboxamide
10-(4-aminobutyl)-19-[(2-amino-3-phenylpropanoyl)amino]-16-benzyl-N-[(2R,3R)-1,3-dihydroxybutan-2-yl]-7-(1-hydroxyethyl)-13-(1H-indol-3-ylmethyl)-6,9,12,15,18-pentaoxo-1,2-dithia-5,8,11,14,17-pentazacycloicosane-4-carboxamide
79517-01-4 (acetate salt)
83150-76-9
AC1L1GVU
AC1L8LCD
AC1L9M4X
C07306
C5H12O2.C4H10
CHEBI:427278
CHEBI:611465
CHEMBL1680
CID383414
CID448601
CID54374
D-Phenylalanyl-L-cysteinyl-L-phenylalanyl-D-tryptophyl-L-lysyl-L-threonyl-L-cysteinyl-L-threoninol cyclic (2-7)-disulfide
D-Phenylalanyl-L-cysteinyl-L-phenylalanyl-D-tryptophyl-L-lysyl-L-threonyl-N-((1R,2R)-2-hydroxy-1-(hydroxymethyl)propyl)-L-cysteinamide cyclic (2-7)-disulfide
D-Phenylalanyl-L-cysteinyl-L-phenylalanyl-D-tryptophyl-L-lysyl-L-threonyl-N-((1R,2R)-2-hydroxy-1-(hydroxymethyl)propyl)-L-cysteinamide cyclic (2->7)-disulfide
D00442
DRG-0115
HMS2090C09
HS-2020
L-Cysteinamide, D-phenylalanyl-L-cysteinyl-L-phenylalanyl-D-tryptophyl-L-lysyl-L- threonyl-N-(2-hydroxy-1-(hydroxymethyl)propyl)-, cyclic (2->7)-disulfide, (R-(R*
L000453
 
LS-177735
LS-187135
Longastatin
NCGC00181796-01
NCI60_025753
Ocphyl
Octreotida
Octreotida [Spanish]
Octreotide
Octreotide (USAN/INN)
Octreotide Acetate
Octreotide Acetate Salt
Octreotide [USAN:INN:BAN]
Octreotide acetate
Octreotide-LAR
Octreotidum
Octreotidum [Latin]
Octrotide
SAN 201-995
SM 201-995
SMS 201-995
SMS-201-995
Sandostatin
Sandostatine
Sandoz 201-995
UNII-RWM8CCW8GP
nchembio.184-comp3
zacycloicosane-4-carboxamide acetate
2
SomatostatinPhase 215351110-01-153481605
Synonyms:
growth hormone-inhibiting hormone (GHIH)
 
somatotropin release-inhibiting factor (SRIF)
somatotropin release-inhibiting hormone
3Gastrointestinal AgentsPhase 26401
4Antineoplastic Agents, HormonalPhase 24256

Interventional clinical trials:

idNameStatusNCT IDPhase
1Treatment With Octreotide in Patients With LymphangioleiomyomatosisCompletedNCT00005906Phase 2

Search NIH Clinical Center for Chylous Ascites

Genetic Tests for Chylous Ascites

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Anatomical Context for Chylous Ascites

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MalaCards organs/tissues related to Chylous Ascites:

33
Liver, Heart, Lymph node, T cells, Prostate, Bone, Breast

Animal Models for Chylous Ascites or affiliated genes

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Publications for Chylous Ascites

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Articles related to Chylous Ascites:

(show top 50)    (show all 550)
idTitleAuthorsYear
1
Case report of chylous ascites with strangulated ileus and review of the literature. (26026475)
2015
2
Successful Minimally Invasive Treatment of Intractable, Postoperative Chylous Ascites Via Percutaneous Lymph Vessel Embolization. (25933643)
2015
3
Change of Chylous Ascites During Low-Density Lipoprotein Apheresis in a Patient With Idiopathic Nephrotic Syndrome. (25256915)
2014
4
Chylous ascites and chylothorax as presentation of a systemic progression of discoid lupus. (23364658)
2013
5
Chylous ascites after laparoscopic hand-assisted donor nephrectomy: Is it specific for the left-side? (23662011)
2013
6
Successful management of chylous ascites with total parenteral nutrition and octreotide in children. (24506391)
2013
7
Chylous ascites mimicking peritonitis after laparoscopic Roux-en-Y gastric bypass for morbid obesity. (20947450)
2012
8
Congenital chylous ascites and lymphedema in Down's syndrome. (22418947)
2012
9
Diagnosis and management of congenital neonatal chylous ascites. (23935276)
2012
10
Atraumatic chylous ascites: systematic review on symptoms and causes. (21398159)
2011
11
Cholelithiasis in a neonate with chylous ascites. (20182428)
2010
12
Congenital plaque-type glomuvenous malformation associated with chylous ascites. (21510024)
2010
13
Fatal chylous ascites, pericarditis and extensive venous thrombosis, due to an aggressive T cell non-Hodgkin lymphoma. (18679682)
2009
14
Coughing may lead to spontaneous chylothorax and chylous ascites. (21487566)
2007
15
Voluminous fetal chylous ascites: a case of complete spontaneous prenatal regression. (17135749)
2007
16
Chylous ascites following operation for para-aortic lymph node dissection in a patient with cervical cancer. (16515637)
2006
17
A female with hemihypertrophy and chylous ascites - Klippel-Trenaunay syndrome or Proteus syndrome: a diagnostic dilemma. (16957479)
2006
18
Octreotide therapy for chylous ascites in a chronic dialysis patient. (16109079)
2005
19
A curious case of ascites. Chylous ascites caused by Kaposi's sarcoma. (12647476)
2003
20
The diagnosis and management of postoperative chylous ascites. (11792897)
2002
21
A case of primary chylous ascites resolved within 4 months by exclusive breast-feeding. (10936987)
2000
22
Chylous ascites: a rare complication of radical gastrectomy. (10829366)
2000
23
Chylous ascites caused by an occult pancreatic malignancy. (10868546)
1999
24
Ruptured lymphocele as a cause of chylous ascites: demonstration by lymphoscintigraphy. (9890497)
1999
25
An unusual case of gastroschisis with gallbladder evisceration and late postrepair chylous ascites. (9434035)
1997
26
Menetrier's disease: report of a transient case associated with chylous ascites. (9260809)
1997
27
Small cell carcinoma of the lung presenting as chylous ascites: a unique case. (9646203)
1997
28
Neonatal chylous ascites--report of three cases and review of the literature. (9099650)
1997
29
Rapid resolution of chylous ascites after liver transplantation using somatostatin analog and total parenteral nutrition. (8629307)
1996
30
Postcaval thrombosis and delayed shunt migration after pleuro-peritoneal venous shunting for concurrent chylothorax and chylous ascites in a dog. (9012108)
1996
31
Chylothorax and chylous ascites due to malignant lymphoma. (7725834)
1995
32
Chylous ascites in cats: nine cases (1978-1993). (7890576)
1994
33
Chylous ascites: A rare complication of liver cirrhosis. (17590704)
1993
34
Recessively determined chylous ascites--a case report and possible mouse model. (1342868)
1992
35
Chylous ascites in three dogs. (1537695)
1992
36
Aspergillus hepatosplenic abscesses and chylous ascites: successful treatment with fluconazole. (1341456)
1992
37
Chylous ascites: a rare complication of vagotomy. Case report. (1676311)
1991
38
Chylous ascites and continuous ambulatory peritoneal dialysis. (1745391)
1991
39
Chylous ascites as a presenting sign of prostatic adenocarcinoma. (2077299)
1990
40
Chronic lymphocytic leukemia presenting with massive chylous ascites. (2186618)
1990
41
Chylous ascites and encapsulating peritonitis: unusual complications of spontaneous bacterial peritonitis. (3578227)
1987
42
Chylous ascites following retroperitoneal lymph node dissection successfully treated with peritoneovenous shunt. (3682840)
1987
43
Case records of the Massachusetts General Hospital. Weekly clinicopathological exercises. Case 20-1986. A 68-year-old man with a malabsorption, chylous ascites, and mesenteric mass. (3702943)
1986
44
Sonographic appearance of chylous ascites. (6427292)
1984
45
Total parenteral nutrition in post-Warren shunt chylous ascites. (107924)
1979
46
Chylous ascites: the first reported surgical cure by direct ligation. (671201)
1978
47
Hairy cell leukemia with chylous ascites. (578227)
1977
48
CONGENITAL MULTILOCULAR MESENTERIC CYST WITH CHYLOUS ASCITES. (14208042)
1964
49
CHYLOUS ASCITES IN NEWBORN MICE. (14205977)
1964
50
Chylous ascites: an analysis of its etiology. (14405264)
1960

Variations for Chylous Ascites

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Expression for genes affiliated with Chylous Ascites

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Search GEO for disease gene expression data for Chylous Ascites.

Pathways for genes affiliated with Chylous Ascites

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GO Terms for genes affiliated with Chylous Ascites

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Sources for Chylous Ascites

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2CDC
14ExPASy
15FDA
16FMA
24GTR
25HGMD
26HMDB
27ICD10
28ICD10 via Orphanet
29ICD9CM
30IUPHAR
31KEGG
34MedGen
36MeSH
37MESH via Orphanet
38MGI
41NCI
42NCIt
43NDF-RT
46NINDS
47Novoseek
49OMIM
50OMIM via Orphanet
54PubMed
55QIAGEN
60SNOMED-CT via Orphanet
64Tumor Gene Family of Databases
65UMLS
66UMLS via Orphanet