MCID: DFF020
MIFTS: 13

Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia malady

Categories: Rare diseases, Neuronal diseases

Aliases & Classifications for Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia

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Aliases & Descriptions for Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia:

Name: Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia 48 68
 
Dipnech 48

Classifications:



Summaries for Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia

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NIH Rare Diseases:48 Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia (dipnech) is a rare and poorly understood lung condition that is characterized by the abnormal proliferation of certain cells (called pulmonary neuroendocrine cells) in the lungs. the world health organization's definition of dipnech is purely based on the characteristics of abnormal lung tissue examined under a microscope (histological). however, people with this diagnosis may have no obvious symptoms or may exhibit features of airway disease (i.e. a chronic, nonproductive cough, shortness of breath with exertion and wheezing). it is considered to be a precancerous condition as studies suggest it is a precursor for pulmonary carcinoid tumors. the underlying cause of dipnech is currently unknown. because so few cases have been reported in the medical literature, there is limited information on the prognosis and management of this condition. last updated: 12/14/2016

MalaCards based summary: Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia, also known as dipnech, is related to neuroendocrine tumor and adenocarcinoma. Affiliated tissues include lung.

Wikipedia:71 Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia (DIPNECH) is a diffuse parenchymal lung... more...

Related Diseases for Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia

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Diseases related to Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia via text searches within MalaCards or GeneCards Suite gene sharing:

idRelated DiseaseScoreTop Affiliating Genes
1neuroendocrine tumor10.0
2adenocarcinoma10.0
3pulmonary neuroendocrine tumor9.9
4hemangioendothelioma9.9
5epithelioid hemangioendothelioma9.9

Graphical network of diseases related to Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia:



Diseases related to diffuse idiopathic pulmonary neuroendocrine cell hyperplasia

Symptoms & Phenotypes for Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia

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Drugs & Therapeutics for Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia

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Interventional clinical trials:

Search ClinicalTrials, NIH Clinical Center for Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia

Genetic Tests for Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia

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Anatomical Context for Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia

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MalaCards organs/tissues related to Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia:

36
Lung

Publications for Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia

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Articles related to Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia:

(show all 36)
idTitleAuthorsYear
1
Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia and Granulomatous Inflammation Mimicking High-Grade Malignancy on FDG-PET/CT. (27775945)
2017
2
Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia: A Case With Long-term Follow-up. (27768634)
2016
3
Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia (DIPNECH)-An uncommon precursor of a common cancer? (26724142)
2016
4
Expression of developing neural transcription factors in diffuse idiopathic pulmonary neuroendocrine cell hyperplasia (DIPNECH). (27300020)
2016
5
Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia syndrome. (27076588)
2016
6
Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia and Neuroendocrine Hyperplasia of Infancy. (27514602)
2016
7
Imaging appearances of diffuse idiopathic pulmonary neuroendocrine cell hyperplasia. (25496668)
2015
8
Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia (DIPNECH) and the Role of Somatostatin analogs: A Case Series. (26112453)
2015
9
Pulmonary Peripheral Carcinoids after Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia and Tumorlets: Report of 3 Cases. (26613062)
2015
10
Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia (DIPNECH). (26472691)
2015
11
Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia (DIPNECH) and multiple pulmonary epithelioid hemangioendothelioma (PEH): a case report. (26591632)
2015
12
Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia of the Lung (DIPNECH): Current Best Evidence. (26104490)
2015
13
A Rare Case of Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia. (26609460)
2015
14
Double lung transplantation for diffuse idiopathic pulmonary neuroendocrine cell hyperplasia. (25321455)
2014
15
The Clinical Course of Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia. (25275948)
2014
16
Sarcoid-like reaction in diffuse idiopathic pulmonary neuroendocrine cell hyperplasia. (25398121)
2014
17
Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia with a central and peripheral carcinoid and multiple tumorlets: a case report emphasizing the role of neuropeptide hormones and human gonadotropin-alpha. (24006219)
2013
18
Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia: case report and review of literature. (23641717)
2013
19
Association of small foci of diffuse idiopathic pulmonary neuroendocrine cell hyperplasia (DIPNECH) with adenocarcinoma of the lung. (23988499)
2013
20
mTOR/p70S6K in diffuse idiopathic pulmonary neuroendocrine cell hyperplasia. (22298367)
2012
21
Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia with multiple synchronous carcinoid tumors. (22386668)
2012
22
Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia (DIPNECH) masquerading as metastatic carcinoma with multiple pulmonary deposits. (23154018)
2012
23
Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia and the associated lung neuroendocrine tumors: clinical experience with a rare entity. (21751183)
2012
24
Morphology and antigen expression profile of pulmonary neuroendocrine cells in reactive proliferations and diffuse idiopathic pulmonary neuroendocrine cell hyperplasia (DIPNECH). (22014055)
2011
25
Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia: an unusual cause of cyclical ectopic adrenocorticotrophic syndrome. (21172958)
2011
26
Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia: 7-year follow-up of a rare clinicopathologic syndrome. (21826622)
2011
27
Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia: a systematic overview. (21471097)
2011
28
Unilateral diffuse idiopathic pulmonary neuroendocrine cell hyperplasia and multiple carcinoids treated with surgical resection. (20502273)
2010
29
Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia: a report of two cases. (20594278)
2010
30
Spectrum of pulmonary neuroendocrine cell proliferation: diffuse idiopathic pulmonary neuroendocrine cell hyperplasia, tumorlet, and carcinoids. (20729444)
2010
31
Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia accompanied by airflow obstruction. (19547861)
2009
32
Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia (DIPNECH) in association with an adenocarcinoma: a case report. (18218143)
2008
33
Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia: an under-recognised spectrum of disease. (17099078)
2007
34
Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia. (17349572)
2007
35
Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia and a typical carcinoid tumor. (16678628)
2006
36
Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia as a precursor to pulmonary neuroendocrine tumors. (15136447)
2004

Variations for Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia

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Expression for genes affiliated with Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia

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Search GEO for disease gene expression data for Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia.

Pathways for genes affiliated with Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia

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GO Terms for genes affiliated with Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia

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Sources for Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia

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2CDC
6CNVD
10DGIdb
15ExPASy
16FDA
17FMA
27GTR
28HGMD
29HMDB
30ICD10
31ICD10 via Orphanet
32ICD9CM
33IUPHAR
34KEGG
37MedGen
39MeSH
40MESH via Orphanet
41MGI
44NCI
45NCIt
46NDF-RT
49NINDS
50Novoseek
52OMIM
53OMIM via Orphanet
57PubMed
58QIAGEN
63SNOMED-CT via Orphanet
67Tumor Gene Family of Databases
68UMLS
69UMLS via Orphanet