DPL
MCID: DSS022
MIFTS: 17

Disseminated Peritoneal Leiomyomatosis (DPL) malady

Category: Rare diseases

Aliases & Classifications for Disseminated Peritoneal Leiomyomatosis

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Sources:
31ICD10 via Orphanet, 48NIH Rare Diseases, 54Orphanet, 68UMLS
See all MalaCards sources

Aliases & Descriptions for Disseminated Peritoneal Leiomyomatosis:

Name: Disseminated Peritoneal Leiomyomatosis 48 54
Leiomyomatosis Peritonealis Disseminate 48 54
Diffuse Peritoneal Leiomyomatosis 48 54
 
Dpl 48 54
Lpd 48 54
Leiomyomatosis Peritonealis Disseminata 68

Characteristics:

Orphanet epidemiological data:

54
leiomyomatosis peritonealis disseminate:
Prevalence: <1/1000000 (Worldwide); Age of onset: Adult; Age of death: normal life expectancy

Classifications:



External Ids:

Orphanet54 ORPHA71274
ICD10 via Orphanet31 D20.1

Summaries for Disseminated Peritoneal Leiomyomatosis

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NIH Rare Diseases:48 Disseminated peritoneal leiomyomatosis (dpl) is a rare condition which is characterized by nodules or small lumps of smooth muscle cells located on the peritoneum (lining of the abdominal wall) and abdominal organs.the condition is usually benign (noncancerous) but in rare cases has become cancerous. although it can be seen in post-menopausal women and very rarely in men, dpl occurs most often in women of childbearing age. most women with dpl are pregnant, taking the birth control pill, or have uterine leioyomas or estrogen-secreting tumors. some people with dpl have no signs or symptoms of the condition. when present, symptoms may include abdominal and pelvic pain; rectal or vaginal bleeding; and less commonly constipation. the cause of dpl is unknown but may be linked to hormonal and genetic factors. some cases of dpl resolve when hormone levels are returned to normal. however, surgery may be suggested based on the size and location of the tumor. last updated: 12/21/2015

MalaCards based summary: Disseminated Peritoneal Leiomyomatosis, also known as leiomyomatosis peritonealis disseminate, is related to diffuse peritoneal leiomyomatosis and autoimmune lymphoproliferative syndrome. Affiliated tissues include smooth muscle.

Related Diseases for Disseminated Peritoneal Leiomyomatosis

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Diseases related to Disseminated Peritoneal Leiomyomatosis via text searches within MalaCards or GeneCards Suite gene sharing:

(show all 13)
idRelated DiseaseScoreTop Affiliating Genes
1diffuse peritoneal leiomyomatosis12.2
2autoimmune lymphoproliferative syndrome10.8
3lymphoid interstitial pneumonia10.8
4systemic epstein-barr virus-positive t-cell lymphoproliferative disease of childhood10.8
5leiomyomatosis10.5
6peritonitis10.5
7leiomyoma10.1
8astrocytoma10.0
9ataxia9.8
10constipation9.8
11endometriosis9.8
12uterine disease9.8
13benign metastasizing leiomyoma9.8

Graphical network of diseases related to Disseminated Peritoneal Leiomyomatosis:



Diseases related to disseminated peritoneal leiomyomatosis

Symptoms & Phenotypes for Disseminated Peritoneal Leiomyomatosis

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Drugs & Therapeutics for Disseminated Peritoneal Leiomyomatosis

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Interventional clinical trials:

idNameStatusNCT IDPhase
1French National Registry of Rare Peritoneal Surface MalignanciesActive, not recruitingNCT02834169

Search NIH Clinical Center for Disseminated Peritoneal Leiomyomatosis

Genetic Tests for Disseminated Peritoneal Leiomyomatosis

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Anatomical Context for Disseminated Peritoneal Leiomyomatosis

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MalaCards organs/tissues related to Disseminated Peritoneal Leiomyomatosis:

36
Smooth muscle

Publications for Disseminated Peritoneal Leiomyomatosis

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Articles related to Disseminated Peritoneal Leiomyomatosis:

(show all 27)
idTitleAuthorsYear
1
A Case of Simultaneous Benign Metastasizing Leiomyomas and Disseminated Peritoneal Leiomyomatosis Following Endoscopic Power Morcellation for Uterine Disease. (27748666)
2017
2
Disseminated peritoneal leiomyomatosis postmorcellated resection of uterine leiomyomatous tissue. (27649643)
2016
3
Disseminated Peritoneal Leiomyomatosis After Open Power Morcellation: A Case Report. (27679078)
2015
4
Disseminated peritoneal leiomyomatosis with chronic constipation: a case report. (24708548)
2014
5
IMAGING DIAGNOSIS-DISSEMINATED PERITONEAL LEIOMYOMATOSIS IN A DOG. (24870205)
2014
6
Disseminated Peritoneal Leiomyomatosis Clinically and Radiologically Mimicking Malignancy. (24196195)
2013
7
Disseminated peritoneal leiomyomatosis with endometriosis. (22546423)
2012
8
Disseminated peritoneal leiomyomatosis. (23365481)
2011
9
Disseminated peritoneal leiomyomatosis after hysterectomy: a case report. (22010532)
2011
10
A case of disseminated peritoneal leiomyomatosis and diffuse uterine leiomyomatosis. (21485735)
2011
11
Disseminated peritoneal leiomyomatosis after laparoscopic supracervical hysterectomy with characteristic molecular cytogenetic findings of uterine leiomyoma. (20842731)
2010
12
Disseminated peritoneal leiomyomatosis responds to systemic chemotherapy. (19039249)
2009
13
A case of disseminated peritoneal leiomyomatosis developing after laparoscope-assisted myomectomy. (18946223)
2009
14
Follow-up in patients with disseminated peritoneal leiomyomatosis: a report of an unusual, high-risk case. (21686624)
2009
15
Disseminated peritoneal leiomyomatosis. (18400601)
2008
16
Disseminated peritoneal leiomyomatosis: an unusual complication of laparoscopic myomectomy. (18193441)
2008
17
Disseminated peritoneal leiomyomatosis: magnetic resonance imaging and differential diagnosis. (17991082)
2007
18
Disseminated peritoneal leiomyomatosis: a case report. (17883066)
2007
19
Disseminated peritoneal leiomyomatosis coexisting with leiomyoma of the uterine body. (16341539)
2006
20
Disseminated peritoneal leiomyomatosis. A benign entity mimicking carcinomatosis. (10985626)
2000
21
Disseminated peritoneal leiomyomatosis. Clonality analysis by X chromosome inactivation and cytogenetics of a clinically benign smooth muscle proliferation. (9176406)
1997
22
Disseminated peritoneal leiomyomatosis. An unusual case. (7991470)
1994
23
Disseminated peritoneal leiomyomatosis in a horse. (7989243)
1994
24
Cytogenetics of multiple uterine leiomyomas, parametrial leiomyoma and disseminated peritoneal leiomyomatosis. (2018368)
1991
25
Disseminated peritoneal leiomyomatosis with malignant change, in a male. (2114697)
1990
26
Immunohistologic detection of estrogen and progesterone receptors in disseminated peritoneal leiomyomatosis. (2707953)
1989
27
Disseminated peritoneal leiomyomatosis. (141779)
1977

Variations for Disseminated Peritoneal Leiomyomatosis

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Expression for genes affiliated with Disseminated Peritoneal Leiomyomatosis

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Search GEO for disease gene expression data for Disseminated Peritoneal Leiomyomatosis.

Pathways for genes affiliated with Disseminated Peritoneal Leiomyomatosis

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GO Terms for genes affiliated with Disseminated Peritoneal Leiomyomatosis

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Sources for Disseminated Peritoneal Leiomyomatosis

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2CDC
6CNVD
10DGIdb
15ExPASy
16FDA
17FMA
27GTR
28HGMD
29HMDB
30ICD10
31ICD10 via Orphanet
32ICD9CM
33IUPHAR
34KEGG
37MedGen
39MeSH
40MESH via Orphanet
41MGI
44NCI
45NCIt
46NDF-RT
49NINDS
50Novoseek
52OMIM
53OMIM via Orphanet
57PubMed
58QIAGEN
63SNOMED-CT via Orphanet
67Tumor Gene Family of Databases
68UMLS
69UMLS via Orphanet