MCID: ENT008
MIFTS: 31

Enteropathy-Associated T-Cell Lymphoma malady

Rare diseases, Cancer diseases, Gastrointestinal diseases, Blood diseases, Immune diseases categories

Aliases & Classifications for Enteropathy-Associated T-Cell Lymphoma

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Sources:
41NIH Rare Diseases, 47Orphanet, 60UMLS, 34MESH via Orphanet, 26ICD10 via Orphanet, 61UMLS via Orphanet, 25ICD10
See all sources

Enteropathy-Associated T-Cell Lymphoma, Aliases & Descriptions:

Name: Enteropathy-Associated T-Cell Lymphoma 41 47 60
High-Grade Pleomorphic Peripheral T-Cell Lymphoma 41
Enteropathy-Type T-Cell Lymphoma 47
Intestinal T-Cell Lymphoma 47
 
Eatcl 41
Ettl 47
Eatl 47


Classifications:



Characteristics (Orphanet epidemiological data):

47

External Ids:

Orphanet47 86880
MESH via Orphanet34 D058527
ICD10 via Orphanet26 C84.4
UMLS via Orphanet61 C0456889
ICD1025 C86.2

Summaries for Enteropathy-Associated T-Cell Lymphoma

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MalaCards based summary: Enteropathy-Associated T-Cell Lymphoma, also known as high-grade pleomorphic peripheral t-cell lymphoma, is related to hodgkin lymphoma and celiac disease. An important gene associated with Enteropathy-Associated T-Cell Lymphoma is CD3G (CD3g molecule, gamma (CD3-TCR complex)), and among its related pathways are ERK Signaling and PEDF Induced Signaling. The compounds threonine and prednisolone have been mentioned in the context of this disorder. Affiliated tissues include t cells, colon and lymph node, and related mouse phenotypes are immune system and hematopoietic system.

Related Diseases for Enteropathy-Associated T-Cell Lymphoma

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Graphical network of the top 20 diseases related to Enteropathy-Associated T-Cell Lymphoma:



Diseases related to enteropathy-associated t-cell lymphoma

Symptoms for Enteropathy-Associated T-Cell Lymphoma

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Drugs & Therapeutics for Enteropathy-Associated T-Cell Lymphoma

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Drug clinical trials:

Search ClinicalTrials for Enteropathy-Associated T-Cell Lymphoma

Search NIH Clinical Center for Enteropathy-Associated T-Cell Lymphoma

Genetic Tests for Enteropathy-Associated T-Cell Lymphoma

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Anatomical Context for Enteropathy-Associated T-Cell Lymphoma

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MalaCards organs/tissues related to Enteropathy-Associated T-Cell Lymphoma:

31
T cells, Colon, Lymph node, Brain, Small intestine, Nk cells, B cells

Animal Models for Enteropathy-Associated T-Cell Lymphoma or affiliated genes

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MGI Mouse Phenotypes related to Enteropathy-Associated T-Cell Lymphoma:

35
idDescriptionMGI Source AccessionScoreTop Affiliating Genes
1MP:00053878.5CD3G, CCL11, TIA1
2MP:00053978.2CD3G, CCL11, TIA1

Publications for Enteropathy-Associated T-Cell Lymphoma

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Articles related to Enteropathy-Associated T-Cell Lymphoma:

(show top 50)    (show all 110)
idTitleAuthorsYear
1
Treatment response in Enteropathy Associated T-cell Lymphoma; survival in a large multicenter cohort. (25716069)
2015
2
An unusual case of enteropathy-associated T-cell lymphoma with CD20 positivity. (25308040)
2014
3
Enteropathy-associated T cell lymphoma as a complication of silent celiac disease. (25568762)
2014
4
Enteropathy associated T cell lymphoma - a case report of an uncommon extranodal T cell lymphoma. (25478355)
2014
5
Enteropathy-associated T-cell lymphoma diagnosed and followed-up by using double-balloon enteroscopy. (23541443)
2013
6
Classic versus type II enteropathy-associated T-cell lymphoma: diagnostic considerations. (23991736)
2013
7
Enteropathy associated T cell lymphoma in celiac disease: a large retrospective study. (23313469)
2013
8
Autologous stem cell transplantation for enteropathy-associated T-cell lymphoma: a retrospective study by the EBMT. (23361910)
2013
9
Brentuximab in the treatment of CD30-positive enteropathy-associated T-cell lymphoma. (23411380)
2013
10
Obscure gastrointestinal bleeding and video capsule retention due to enteropathy-associated T-cell lymphoma. (24719605)
2013
11
Challenges in the diagnosis of enteropathy-associated T cell lymphoma. (23964351)
2013
12
Type II enteropathy-associated T-cell lymphoma: a multicenter analysis from the Asia Lymphoma Study Group. (22641357)
2012
13
High frequency of fatal haemophagocytic lymphohistiocytosis syndrome in enteropathy-associated T cell lymphoma. (22100722)
2012
14
How I treat enteropathy-associated T-cell lymphoma. (22271451)
2012
15
Enteropathy-associated T-cell lymphoma, lacking MHC class II, with immune-privileged site recurrence, presenting as bilateral ocular vitreous humour involvement - a case report. (22963578)
2012
16
Second line chemotherapy in patients with enteropathy-associated T cell lymphoma: a retrospective single center analysis. (21520002)
2012
17
An unusual enteropathy-associated T-cell lymphoma with MYC translocation arising in a Japanese patient: a case report. (22654438)
2012
18
Supratentorial metastatic enteropathy-associated T-cell lymphoma: A case report and literature review. (23230525)
2012
19
Early radiological findings on CT in a patient with enteropathy-associated T cell lymphoma. (22670007)
2011
20
Enteropathy-associated T-cell lymphoma: epidemiology, clinical features, and current treatment strategies. (21912848)
2011
21
Type II enteropathy-associated T-cell lymphoma: a distinct aggressive lymphoma with frequent I^I' T-cell receptor expression. (21921780)
2011
22
A case of enteropathy-associated T-cell lymphoma: diagnosis by flow cytometric immunophenotyping and genome analysis using ascitic fluid. (21604213)
2011
23
Pathological and immunohistological findings and genetic aberrations of intestinal enteropathy-associated T cell lymphoma in Japan. (21323966)
2011
24
Phenotypic and genomic analysis of an exceptional case of enteropathy associated T-cell lymphoma. (20226524)
2010
25
Enteropathy-associated T-cell lymphoma: a review on clinical presentation, diagnosis, therapeutic strategies and perspectives. (21050687)
2010
26
Enteropathy associated T-cell lymphoma resulting in restrictive cardiomyopathy and mimicking myocardial infarction. (22767479)
2010
27
Enteropathy associated T-cell lymphoma and its precursor lesions. (20206108)
2010
28
Enteropathy-associated T-cell lymphoma--a clinicopathologic and array comparative genomic hybridization study. (20399483)
2010
29
Enteropathy associated T cell lymphoma: common in coeliac disease. (21686880)
2009
30
Management of Enteropathy-Associated T-Cell Lymphoma: An Algorithmic Approach. (20740143)
2009
31
The phenotype of intraepithelial lymphocytes in Taiwanese enteropathy-associated T-cell lymphoma is distinct from that of the West. (18518903)
2008
32
Effect of a gluten-free diet on the risk of enteropathy-associated T-cell lymphoma in celiac disease. (17934841)
2008
33
Survival in refractory coeliac disease and enteropathy-associated T-cell lymphoma: retrospective evaluation of single-centre experience. (17470479)
2007
34
Indigo carmine chromoendoscopic appearances of enteropathy-associated T-cell lymphoma during double-balloon endoscopy in a patient with celiac disease. (17614075)
2007
35
Abdominal computed tomography in refractory coeliac disease and enteropathy associated T-cell lymphoma. (17461472)
2007
36
Successful treatment of enteropathy-associated T cell lymphoma with autologous stem cell transplant. (16865575)
2006
37
Lymphomatous infiltration of the peripheral nervous system in enteropathy-associated T-cell lymphoma. (15804227)
2005
38
Enteropathy-associated T-cell lymphoma with initial manifestation in the CNS. (12771280)
2003
39
Refractory sprue, coeliac disease, and enteropathy-associated T-cell lymphoma. French Coeliac Disease Study Group. (10963198)
2000
40
Refractory coeliac disease: a window between coeliac disease and enteropathy associated T cell lymphoma. (11232488)
2000
41
Enteropathy-associated T-cell lymphoma and its immunocarcinogenic correlates: case report and review of the literature. (9754448)
1998
42
Enteropathy-associated T-cell lymphomas have a cytotoxic T-cell phenotype. (9363445)
1997
43
Enteropathy-associated T-cell lymphoma: a case report with radiographic and computed tomography appearance. (9179268)
1997
44
Molecular analysis of T-cell clonality in ulcerative jejunitis and enteropathy-associated T-cell lymphoma. (9250161)
1997
45
HLA antigen expression in enteropathy associated T cell lymphoma. (8813950)
1996
46
Demonstration of the oligoclonality of an enteropathy associated T-cell lymphoma by monoclonal antibodies and PCR analysis of the T-cell receptor V-beta repertoire on fixed tissue. (8621191)
1996
47
Pleural lymphoma in a patient presenting with malabsorption: an illustration of the clinicopathological behaviour in a case of enteropathy associated T cell lymphoma. (8244122)
1993
48
Epstein-Barr virus (EBV) in enteropathy-associated T-cell lymphoma (EATL). (8393922)
1993
49
Low-grade intestinal lymphoma of intraepithelial T lymphocytes with concomitant enteropathy-associated T cell lymphoma: case report suggesting a possible histogenetic relationship. (2789173)
1989
50
Enteropathy-associated T cell lymphoma (malignant histiocytosis of the intestine) is recognized by a monoclonal antibody (HML-1) that defines a membrane molecule on human mucosal lymphocytes. (3260750)
1988

Variations for Enteropathy-Associated T-Cell Lymphoma

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Expression for genes affiliated with Enteropathy-Associated T-Cell Lymphoma

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Search GEO for disease gene expression data for Enteropathy-Associated T-Cell Lymphoma.

Pathways for genes affiliated with Enteropathy-Associated T-Cell Lymphoma

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Compounds for genes affiliated with Enteropathy-Associated T-Cell Lymphoma

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Sources:
43Novoseek, 28IUPHAR, 12DrugBank
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Compounds related to Enteropathy-Associated T-Cell Lymphoma according to GeneCards Suite gene sharing:

idCompoundScoreTop Affiliating Genes
1threonine439.1CCL11, TIA1
2prednisolone43 28 1210.8CCL11, TIA1

GO Terms for genes affiliated with Enteropathy-Associated T-Cell Lymphoma

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Products for genes affiliated with Enteropathy-Associated T-Cell Lymphoma

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Sources for Enteropathy-Associated T-Cell Lymphoma

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3CDC
13ExPASy
14FMA
22GTR
23HGMD
24HMDB
25ICD10
26ICD10 via Orphanet
27ICD9CM
28IUPHAR
29KEGG
33MeSH
34MESH via Orphanet
35MGI
38NCIt
39NDF-RT
42NINDS
43Novoseek
45OMIM
46OMIM via Orphanet
50PubMed
51QIAGEN
56SNOMED-CT via Orphanet
60UMLS
61UMLS via Orphanet