MCID: FBR028
MIFTS: 24

Fibrosing Mediastinitis malady

Categories: Rare diseases, Respiratory diseases, Bone diseases

Aliases & Classifications for Fibrosing Mediastinitis

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Sources:
46NIH Rare Diseases, 52Orphanet, 66UMLS, 29ICD10 via Orphanet, 38MESH via Orphanet, 67UMLS via Orphanet
See all MalaCards sources

Aliases & Descriptions for Fibrosing Mediastinitis:

Name: Fibrosing Mediastinitis 46 52
Mediastinal Fibrosis 46 52 66
Igg4-Related Mediastinitis 46 52
 
Sclerosing Mediastinitis 46 52
Idiopathic Mediastinal Fibrosis 46
Idiopathic Hilar Fibrosis 66

Characteristics:

Orphanet epidemiological data:

52
mediastinal fibrosis:
Inheritance: Not applicable

Classifications:



External Ids:

Orphanet52 ORPHA63999
ICD10 via Orphanet29 J98.5
MESH via Orphanet38 C536136
UMLS via Orphanet67 C0221386, C0264573

Summaries for Fibrosing Mediastinitis

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NIH Rare Diseases:46 Fibrosing mediastinitis is a condition that affects the area between the lungs (mediastinum) which contains the heart, large blood vessels, windpipe (trachea), esophagus, and lymph nodes. people with fibrosing mediastinitis have varying amounts of scar tissue in the mediastinum which may cause problems for the organs located there. for example, some affected people may develop blocked airways that can interfere with lung function. others may have compressed blood vessels which can slow or prevent blood flow to and from the heart. the exact cause of fibrosing mediastinitis is not fully understood, but it is not inherited. many cases are linked to a specific type of fungal infection called histoplasmosis. treatment depends on which structures of the mediastinum are affected, the severity of the scarring and, in some cases, the cause of the condition. last updated: 11/5/2014

MalaCards based summary: Fibrosing Mediastinitis, also known as mediastinal fibrosis, is related to mediastinitis and superior vena cava syndrome. Affiliated tissues include heart, lung and trachea.

Related Diseases for Fibrosing Mediastinitis

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Graphical network of the top 20 diseases related to Fibrosing Mediastinitis:



Diseases related to fibrosing mediastinitis

Symptoms for Fibrosing Mediastinitis

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Drugs & Therapeutics for Fibrosing Mediastinitis

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Interventional clinical trials:

idNameStatusNCT IDPhase
1Cohort Study of IgG4RDRecruitingNCT01670695Phase 0

Search NIH Clinical Center for Fibrosing Mediastinitis

Genetic Tests for Fibrosing Mediastinitis

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Anatomical Context for Fibrosing Mediastinitis

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MalaCards organs/tissues related to Fibrosing Mediastinitis:

34
Heart, Lung, Trachea, Lymph node, Bone, Thyroid, Breast

Animal Models for Fibrosing Mediastinitis or affiliated genes

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Publications for Fibrosing Mediastinitis

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Articles related to Fibrosing Mediastinitis:

(show top 50)    (show all 135)
idTitleAuthorsYear
1
Tuberculosis-associated Fibrosing Mediastinitis: Case Report and Literature Review. (27625898)
2016
2
Successful stenting of left pulmonary veins stenosis resulting from fibrosing mediastinitis. (25586119)
2015
3
Pulmonary Hypertension due to Fibrosing Mediastinitis Treated Successfully With Stenting of Pulmonary VeinA Stenoses. (25840104)
2015
4
Catheter-based intervention for pulmonary vein stenosis due to fibrosing mediastinitis: The Mayo Clinic experience. (26925456)
2015
5
The role of PET scan in monitoring the progression of fibrosing mediastinitis. (26414539)
2015
6
Fibrosing mediastinitis complicating prior histoplasmosis is associated with human leukocyte antigen DQB1*04:02 - a case control study. (25940591)
2015
7
Idiopathic fibrosing mediastinitis: spectrum of imaging findings with emphasis on its association with IgG4-related disease. (26257115)
2015
8
Fibrosing Mediastinitis Mimicking Sarcoidosis. (24405501)
2014
9
Fibrosing mediastinitis mimicking postpartum heart failure. (25417662)
2014
10
Thoracoscopic pneumonectomy in management of histoplasmosis and fibrosing mediastinitis. (25282249)
2014
11
Fibrosing mediastinitis: an unusual cause of pulmonary symptoms. (23807725)
2013
12
Anaplastic large cell lymphoma mimicking fibrosing mediastinitis. (24292756)
2013
13
The treatment of superior vena cava syndrome secondary to idiopathic fibrosing mediastinitis with balloon angioplasty and stenting. (23265133)
2012
14
Malignant Wegener's granulomatosis with fibrosing mediastinitis and vena cava superior syndrome. (22260549)
2012
15
Fibrosing mediastinitis with severe bilateral pulmonary artery narrowing: RV-RPA bypass with a homograft conduit. (22719157)
2012
16
Fibrosing mediastinitis: clinical presentation, therapeutic outcomes, and adaptive immune response. (22033450)
2011
17
Sarcoidosis-associated fibrosing mediastinitis with resultant pulmonary hypertension: a case report and review of the literature. (19797887)
2010
18
Fibrosing mediastinitis causing acute ostial left main myocardial infarction. (20814057)
2010
19
Fibrosing mediastinitis associated with complete occlusion of the left main pulmonary artery. (19101331)
2009
20
An unusual case of Aspergillus fibrosing mediastinitis. (19766844)
2009
21
Unilateral pulmonary vein stenosis secondary to idiopathic fibrosing mediastinitis. (21687296)
2009
22
Fibrosing mediastinitis as a rare sequel of iatrogenic rupture of bronchogenic cyst--a case report. (17561459)
2008
23
Extra-anatomic bypass of the superior vena cava after successful stenting for fibrosing mediastinitis. (18179952)
2008
24
Fibrosing mediastinitis associated with BehAset's disease: CT findings. (17920874)
2007
25
Unilateral pulmonary edema due to pulmonary venous obstruction from fibrosing mediastinitis. (16520136)
2006
26
Successful management of idiopathic fibrosing mediastinitis with superior vena cava thrombosis. (15758892)
2005
27
Fibrosing mediastinitis and thrombosis of superior vena cava associated with BehAset's disease. (14680916)
2003
28
Restenosis of superior vena cava after treatment using a self-expanding metallic stent in a patient with idiopathic fibrosing mediastinitis. (17670068)
2003
29
Late superior vena cava perforation and aortic laceration after stenting to treat superior vena cava syndrome secondary to fibrosing mediastinitis. (12368518)
2002
30
Stent placement in the treatment of pulmonary artery stenosis secondary to fibrosing mediastinitis. (11535776)
2001
31
Fibrosing mediastinitis. (11353121)
2001
32
A case of fibrosing mediastinitis with obstruction of superior vena cava and downhill esophageal varices: a rare cause of upper gastrointestinal hemorrhage. (10192621)
1999
33
Localized idiopathic fibrosing mediastinitis as a cause of superior vena cava syndrome: a case report. (9492750)
1998
34
Fibrosing mediastinitis: CT and MR findings. (9867275)
1998
35
Tuberculous fibrosing mediastinitis: radiologic findings. (8956619)
1996
36
Chest case of the day. Fibrosing mediastinitis. (7785585)
1995
37
Relief of superior vena cava syndrome due to fibrosing mediastinitis using the Palmaz stent. (8020305)
1994
38
Cervical manifestations of fibrosing mediastinitis: a diagnostic and therapeutic dilemma. (8253566)
1993
39
Coronary artery bypass grafting with unanticipated fibrosing mediastinitis. (2306156)
1990
40
Fibrosing mediastinitis in the posterior thorax. (2763944)
1989
41
Magnetic resonance imaging of fibrosing mediastinitis. (3875221)
1985
42
Venoocclusive pulmonary infarct: an unusual complication of fibrosing mediastinitis. (6602515)
1983
43
Pulmonary scintigraphy in fibrosing mediastinitis due to histoplasmosis. (7205381)
1981
44
Pulmonary infarct: an unusual manifestation of fibrosing mediastinitis. (7357976)
1980
45
Tracheal stenosis: an unusual presenting complication of idiopathic fibrosing mediastinitis. (7412344)
1980
46
Mediastinal granuloma and fibrosing mediastinitis. (421573)
1979
47
Pulmonary artery occlusion following fibrosing mediastinitis due to histoplasmosis. (421398)
1979
48
Pulmonary artery obstruction with fibrosing mediastinitis. (672256)
1978
49
Bilateral pulmonary artery obstruction due to fibrosing mediastinitis: case report. (818588)
1976
50
Technique for reconstruction of superior vena cava in fibrosing mediastinitis. (4697444)
1973

Variations for Fibrosing Mediastinitis

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Expression for genes affiliated with Fibrosing Mediastinitis

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Search GEO for disease gene expression data for Fibrosing Mediastinitis.

Pathways for genes affiliated with Fibrosing Mediastinitis

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GO Terms for genes affiliated with Fibrosing Mediastinitis

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Sources for Fibrosing Mediastinitis

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2CDC
6CNVD
10DGIdb
15ExPASy
16FDA
17FMA
25GTR
26HGMD
27HMDB
28ICD10
29ICD10 via Orphanet
30ICD9CM
31IUPHAR
32KEGG
35MedGen
37MeSH
38MESH via Orphanet
39MGI
42NCI
43NCIt
44NDF-RT
47NINDS
48Novoseek
50OMIM
51OMIM via Orphanet
55PubMed
56QIAGEN
61SNOMED-CT via Orphanet
65Tumor Gene Family of Databases
66UMLS
67UMLS via Orphanet