MCID: FBR028
MIFTS: 29

Fibrosing Mediastinitis malady

Rare diseases, Respiratory diseases categories
Download this MalaCard

Summaries for Fibrosing Mediastinitis

About this section
Sources:
43NIH Rare Diseases, 33MalaCards
See all sources

Fully expand this MalaCard
NIH Rare Diseases:43 Fibrosing mediastinitis refers to scarring in the chest that can entrap the esophagus, the heart, the lymph nodes, and the major blood vessels that carry blood to and from the heart. the “mediastinum” refers specifically to the area between the lungs. the scarring may involve a single mass or be diffusely spread throughout the cavity.  in rare cases, fibrosing mediastinitis may extend into the soft tissues of the neck, the back of the chest, and into the lung. last updated: 4/23/2010

MalaCards: Fibrosing Mediastinitis, also known as mediastinal fibrosis, is related to mediastinitis and superior vena cava syndrome. Affiliated tissues include lung, lymph node and heart.

Aliases & Classifications for Fibrosing Mediastinitis

About this section
Sources:
43NIH Rare Diseases, 49Orphanet, 62UMLS, 36MESH via Orphanet, 26ICD10 via Orphanet, 59SNOMED-CT via Orphanet, 63UMLS via Orphanet
See all sources

Classifications:

Malacards categories (disease lists): (See all malacards categories)
Global: Rare diseases
Anatomical: Respiratory diseases


Aliases & Descriptions:

fibrosing mediastinitis 43 49
mediastinal fibrosis 43 49 62
sclerosing mediastinitis 43 49
idiopathic mediastinal fibrosis 43
idiopathic hilar fibrosis 62


External Ids:

MESH via Orphanet36 C536136
ICD10 via Orphanet26 J98.5
SNOMED-CT via Orphanet59 21247003, 361196000, 7377003
UMLS via Orphanet63 C0221386, C0264573

Related Diseases for Fibrosing Mediastinitis

About this section
Sources:
17GeneCards, 18GeneDecks
See all sources

Graphical network of the top 20 diseases related to Fibrosing Mediastinitis:



Diseases related to fibrosing mediastinitis

Symptoms for Fibrosing Mediastinitis

About this section

Drugs & Therapeutics for Fibrosing Mediastinitis

About this section
Sources:
42NIH Clinical Center, 6ClinicalTrials
See all sources

Drug clinical trials:

Search ClinicalTrials for Fibrosing Mediastinitis

Search NIH Clinical Center for Fibrosing Mediastinitis

Genetic Tests for Fibrosing Mediastinitis

About this section

Anatomical Context for Fibrosing Mediastinitis

About this section
Sources:
33MalaCards
See all sources

MalaCards organs/tissues related to Fibrosing Mediastinitis:

33
Lung, Lymph node, Heart, Thyroid, Breast, Trachea

Animal Models for Fibrosing Mediastinitis or affiliated genes

About this section

Publications for Fibrosing Mediastinitis

About this section
Sources:
52PubMed
See all sources

Articles related to Fibrosing Mediastinitis:

(show top 50)    (show all 117)
idTitleAuthorsYear
1
Fibrosing Mediastinitis Mimicking Sarcoidosis. (24405501)
2014
2
Fibrosing mediastinitis mimicking bronchogenic carcinoma. (23372962)
2013
3
Fibrosing mediastinitis: an unusual cause of pulmonary symptoms. (23807725)
2013
4
Anaplastic large cell lymphoma mimicking fibrosing mediastinitis. (24292756)
2013
5
Fibrosing mediastinitis as a cause of right claudication. (21562863)
2012
6
The treatment of superior vena cava syndrome secondary to idiopathic fibrosing mediastinitis with balloon angioplasty and stenting. (23265133)
2012
7
Percutaneous vascular stent implantation as treatment for central vascular obstruction due to fibrosing mediastinitis. (21422386)
2011
8
Bilateral breast enlargement: an unusual presentation of superior vena cava obstruction in a hemodialysis patient with fibrosing mediastinitis. (19949792)
2011
9
Pulmonary artery stenosis secondary to fibrosing mediastinitis: management with cutting balloon angioplasty and endovascular stenting. (21278182)
2011
10
Sarcoidosis-associated fibrosing mediastinitis with resultant pulmonary hypertension: a case report and review of the literature. (19797887)
2010
11
Fibrosing mediastinitis associated with complete occlusion of the left main pulmonary artery. (19101331)
2009
12
Fibrosing mediastinitis and occlusion of pulmonary veins after radiofrequency ablation. (19853136)
2009
13
Fibrosing mediastinitis as an untypical complication of tuberculosis: case report. (19920801)
2009
14
An unusual case of Aspergillus fibrosing mediastinitis. (19766844)
2009
15
Fibrosing mediastinitis as a rare sequel of iatrogenic rupture of bronchogenic cyst--a case report. (17561459)
2008
16
Fibrosing mediastinitis mimicking malignancy at CT: negative FDG uptake in integrated FDG PET/CT imaging. (16944162)
2007
17
Fibrosing mediastinitis manifesting as thoracic prevertebral thin band-like mass on MRI and PET-CT. (17704310)
2007
18
Successful steroid treatment for fibrosing mediastinitis and sclerosing cervicitis. (17307498)
2007
19
Fibrosing mediastinitis associated with BehAset's disease: CT findings. (17920874)
2007
20
Fibrosing mediastinitis presenting as pulmonary stenosis: stenting works. (17399816)
2007
21
Unilateral pulmonary edema due to pulmonary venous obstruction from fibrosing mediastinitis. (16520136)
2006
22
Successful management of idiopathic fibrosing mediastinitis with superior vena cava thrombosis. (15758892)
2005
23
Complete resolution of fibrosing mediastinitis with corticosteroid therapy. (16108250)
2005
24
Fibrosing mediastinitis as a cause of superior vena cava syndrome. (15296918)
2004
25
Fibrosing mediastinitis and thrombosis of superior vena cava associated with BehAset's disease. (14680916)
2003
26
Late superior vena cava perforation and aortic laceration after stenting to treat superior vena cava syndrome secondary to fibrosing mediastinitis. (12368518)
2002
27
Elective stenting in superior vena cava syndrome caused by idiopathic fibrosing mediastinitis: use of self-expandable wallstent. (12462674)
2002
28
Fibrosing mediastinitis secondary to zygomycosis in a twenty-two-month-old child. (12150186)
2002
29
Tuberculous fibrosing mediastinitis: CT and MRI findings. (11428422)
2001
30
Percutaneous stenting of right pulmonary artery stenosis in fibrosing mediastinitis. (10700067)
2000
31
A case of fibrosing mediastinitis with obstruction of superior vena cava and downhill esophageal varices: a rare cause of upper gastrointestinal hemorrhage. (10192621)
1999
32
Localized idiopathic fibrosing mediastinitis as a cause of superior vena cava syndrome: a case report. (9492750)
1998
33
Fibrosing mediastinitis associated with Riedel's thyroiditis--computed tomographic findings: case report. (9879270)
1998
34
Successful treatment of sclerosing cervicitis and fibrosing mediastinitis with tamoxifen. (9106605)
1997
35
Tuberculous fibrosing mediastinitis: radiologic findings. (8956619)
1996
36
Fibrosing mediastinitis causing nonvisualization of one lung on pulmonary scintigraphy. (8344031)
1993
37
Cervical manifestations of fibrosing mediastinitis: a diagnostic and therapeutic dilemma. (8253566)
1993
38
Chronic fibrosing mediastinitis and superior vena caval obstruction from blastomycosis. (1417237)
1992
39
Coronary artery bypass grafting with unanticipated fibrosing mediastinitis. (2306156)
1990
40
Fibrosing mediastinitis in the posterior thorax. (2763944)
1989
41
Scintigraphy compared to other imaging modalities in benign superior vena caval obstruction accompanying fibrosing mediastinitis. (2819591)
1989
42
Pulmonary vascular occlusion and fibrosing mediastinitis. (3943394)
1986
43
Magnetic resonance imaging of spiral vein graft bypass of superior vena cava in fibrosing mediastinitis. (3769568)
1986
44
Pulmonary scintigraphy in fibrosing mediastinitis due to histoplasmosis. (7205381)
1981
45
Pulmonary infarct: an unusual manifestation of fibrosing mediastinitis. (7357976)
1980
46
Tracheal stenosis: an unusual presenting complication of idiopathic fibrosing mediastinitis. (7412344)
1980
47
Mediastinal granuloma and fibrosing mediastinitis. (421573)
1979
48
Pulmonary artery occlusion following fibrosing mediastinitis due to histoplasmosis. (421398)
1979
49
Mediastinal granuloma and fibrosing mediastinitis. (510018)
1979
50
Progressive fibrosing mediastinitis. (5954469)
1966

Variations for Fibrosing Mediastinitis

About this section

Expression for genes affiliated with Fibrosing Mediastinitis

About this section
Sources:
15Gene Expression Omnibus DataSets
See all sources

Search GEO for disease gene expression data for Fibrosing Mediastinitis.

Pathways for genes affiliated with Fibrosing Mediastinitis

About this section

Compounds for genes affiliated with Fibrosing Mediastinitis

About this section

GO Terms for genes affiliated with Fibrosing Mediastinitis

About this section

Products for genes affiliated with Fibrosing Mediastinitis

About this section
  • Antibodies
  • Proteins
  • Lysates
  • Antibodies

Sources for Fibrosing Mediastinitis

About this section
4CDC
13ExPASy
14FMA
22GTR
23HGMD
24HMDB
25ICD10
26ICD10 via Orphanet
27ICD9CM
29IUPHAR
30KEGG
35MeSH
36MESH via Orphanet
37MGI
40NCIt
41NDF-RT
44NINDS
45Novoseek
47OMIM
48OMIM via Orphanet
52PubMed
53QIAGEN
59SNOMED-CT via Orphanet
62UMLS
63UMLS via Orphanet