MCID: FBR028
MIFTS: 25

Fibrosing Mediastinitis malady

Categories: Rare diseases, Respiratory diseases, Bone diseases

Aliases & Classifications for Fibrosing Mediastinitis

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Sources:
45NIH Rare Diseases, 51Orphanet, 65UMLS, 28ICD10 via Orphanet, 37MESH via Orphanet, 66UMLS via Orphanet
See all MalaCards sources

Aliases & Descriptions for Fibrosing Mediastinitis:

Name: Fibrosing Mediastinitis 45 51
Mediastinal Fibrosis 45 51 65
Igg4-Related Mediastinitis 45 51
 
Sclerosing Mediastinitis 45 51
Idiopathic Mediastinal Fibrosis 45
Idiopathic Hilar Fibrosis 65

Classifications:



External Ids:

Orphanet51 63999
ICD10 via Orphanet28 J98.5
MESH via Orphanet37 C536136
UMLS via Orphanet66 C0221386, C0264573
UMLS65 C0221386, C0264573

Summaries for Fibrosing Mediastinitis

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NIH Rare Diseases:45 Fibrosing mediastinitis is a condition that affects the area between the lungs (mediastinum) which contains the heart, large blood vessels, windpipe (trachea), esophagus, and lymph nodes. people with fibrosing mediastinitis have varying amounts of scar tissue in the mediastinum which may cause problems for the organs located there. for example, some affected people may develop blocked airways that can interfere with lung function. others may have compressed blood vessels which can slow or prevent blood flow to and from the heart. the exact cause of fibrosing mediastinitis is not fully understood, but it is not inherited. many cases are linked to a specific type of fungal infection called histoplasmosis. treatment depends on which structures of the mediastinum are affected, the severity of the scarring and, in some cases, the cause of the condition. last updated: 11/5/2014

MalaCards based summary: Fibrosing Mediastinitis, also known as mediastinal fibrosis, is related to igg4-related disease and neuronitis. Affiliated tissues include lung, heart and lymph node.

Related Diseases for Fibrosing Mediastinitis

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Graphical network of the top 20 diseases related to Fibrosing Mediastinitis:



Diseases related to fibrosing mediastinitis

Symptoms for Fibrosing Mediastinitis

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Drugs & Therapeutics for Fibrosing Mediastinitis

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Interventional clinical trials:

idNameStatusNCT IDPhase
1Cohort Study of IgG4RDRecruitingNCT01670695Phase 0

Search NIH Clinical Center for Fibrosing Mediastinitis

Genetic Tests for Fibrosing Mediastinitis

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Anatomical Context for Fibrosing Mediastinitis

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MalaCards organs/tissues related to Fibrosing Mediastinitis:

33
Lung, Heart, Lymph node, Trachea, Bone, Endothelial, Thyroid

Animal Models for Fibrosing Mediastinitis or affiliated genes

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Publications for Fibrosing Mediastinitis

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Articles related to Fibrosing Mediastinitis:

(show top 50)    (show all 133)
idTitleAuthorsYear
1
12/15 Lipoxygenase regulation of colorectal tumorigenesis is determined by the relative tumor levels of its metabolite 12-HETE and 13-HODE in animal models. (25576922)
2015
2
Basal cell adenoma-clinicopathological, immunohistochemical analysis and surgical considerations of a rare salivary gland tumor with review of literature. (25838763)
2015
3
Acute torsion of uterine remnantA leiomyoma with Mayer-Rokitansky-KA1ster-Hauser syndrome. (24842677)
2014
4
Editorial comment: improving awareness of nonanesthesia-related malignant hyperthermia presentations: a tale of two brothers. (25611020)
2014
5
A rare cause of hyperthyroidism: functioning thyroid metastases. (25301427)
2014
6
Pityriasis lichenoides in an Asian population. (23488769)
2013
7
Association between copy-number variations of the human histamine H4 receptor gene and atopic dermatitis in a Chinese population. (23517361)
2013
8
Differences Between Hepatocellular Carcinoma and Hepatitis B Virus Infection in Patients With and Without Cirrhosis. (24132624)
2013
9
Characterization of fungal keratitis in alpacas: 11 cases (2003-2012). (24261813)
2013
10
Association between vitamin D receptor genetic polymorphisms and acute cellular rejection in liver-transplanted patients. (22220717)
2012
11
Carbon ion radiation therapy improves the prognosis of unresectable adult bone and soft-tissue sarcoma of the head and neck. (21745719)
2012
12
A case of pulmonary alveolar microlithiasis. (22022196)
2011
13
NT-proBNP: a cardiac biomarker to assess prognosis in non-Hodgkin lymphoma. (21333352)
2011
14
Genetic variation in lipid desaturases and its impact on the development of human disease. (20565855)
2010
15
Topological layers in the HIV-1 gp120 inner domain regulate gp41 interaction and CD4-triggered conformational transitions. (20227370)
2010
16
Diagnostic intracranial pressure monitoring and surgical management in idiopathic normal pressure hydrocephalus: a 6-year review of 214 patients. (20023540)
2010
17
Clinical spectrum of the pseudotumor cerebri complex in children. (19902218)
2010
18
Rett syndrome diagnostic criteria: lessons from the Natural History Study. (21104896)
2010
19
Albinism: Images in ophthalmology. (21234225)
2009
20
Expression of receptor for advanced glycation end products (RAGE) is related to prognosis in patients with esophageal squamous cell carcinoma. (19023628)
2009
21
Expression of survivin in lung eosinophils is associated with pathology in a mouse model of allergic asthma. (19395375)
2009
22
Identification of the active site of DS-epimerase 1 and requirement of N-glycosylation for enzyme function. (19004833)
2009
23
Pathophysiology and treatment of patients with type 2 diabetes exhibiting failure to oral drugs. (18171434)
2008
24
Activation of the unfolded protein response by deltaF508 CFTR. (18458236)
2008
25
The altered apoptotic pathways in cisplatin and etoposide-resistant melanoma cells are drug specific. (17119454)
2006
26
Association of coronary artery disease with polymorphisms of angiotensin-converting enzyme and methylenetetrahydrofolate reductase gene. (19039150)
2006
27
Smoking and the sudden infant death syndrome. (16898673)
2006
28
Cavernous hemangioma of the anterior mediastinum: case report and 50-year review of Japanese cases. (16764313)
2006
29
ABO blood-group antigens in oral cancer. (15615870)
2005
30
Myiasis in an urban setting: A case report. (18159443)
2004
31
HDL-cholesterol-- active or passive participant in the pathogenesis of atherosclerosis]. (14755929)
2003
32
Comparison of oral versus intravenous iron therapy in predialysis patients of chronic renal failure receiving recombinant human erythropoietin. (12725261)
2003
33
Pharmacogenomics of psychiatric drug treatment. (12778835)
2003
34
In nonhepatic cells, cholesterol 7alpha-hydroxylase induces the expression of genes regulating cholesterol biosynthesis, efflux, and homeostasis. (10946023)
2000
35
Cyclosporine-induced autologous graft-versus-host disease in patients with acute myeloid leukemia undergoing non-myeloablative chemotherapy without progenitor cell reinfusion. (10578157)
1999
36
Primary sequence, secondary structure, gene structure, and assembly properties suggests that the lens-specific cytoskeletal protein filensin represents a novel class of intermediate filament protein. (9628810)
1998
37
Cationic amino acid transporter-2 mRNA induction by tumor necrosis factor-alpha in vascular endothelial cells. (9473147)
1997
38
Ion channel targeting in neurons. (9363678)
1997
39
Surgical strategy of cochlear implantation in patients with chronic middle ear disease. (9390845)
1997
40
Pathologic findings in a case of primary progressive aphasia. (8309574)
1994
41
Morphologic findings in biopsied skeletal muscle and cultured fibroblasts from a female patient with Danon's disease (lysosomal glycogen storage disease without acid maltase deficiency). (7699392)
1994
42
TNF alpha expressing cells in epidermal tumors: correlation with ICAM-1 induction on keratinocytes and Langerhans cell distribution. (7919125)
1994
43
Precise localization of the excision repair gene, ERCC5, to human chromosome 13q32.3-q33.1 by direct R-banding fluorescence in situ hybridization. (1483924)
1992
44
Agenesis of the dorsal pancreas with polysplenia syndrome: CT features. (1430442)
1992
45
Oestrogen receptor and epidermal growth factor receptor expression in male breast carcinoma. (1538271)
1992
46
Relationship between amino-acid metabolism and immune functions in human lymphocytes. (16839956)
1991
47
Late development of localized band keratopathy in relation to a Molteno tube. (2743783)
1989
48
Immunological features in different clinical forms of strongyloidiasis. (6623593)
1983
49
Observations on an epidemic of paratyphoid fever in Dundee, 1941. (20475679)
1944
50

Variations for Fibrosing Mediastinitis

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Expression for genes affiliated with Fibrosing Mediastinitis

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Search GEO for disease gene expression data for Fibrosing Mediastinitis.

Pathways for genes affiliated with Fibrosing Mediastinitis

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GO Terms for genes affiliated with Fibrosing Mediastinitis

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Sources for Fibrosing Mediastinitis

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2CDC
14ExPASy
15FDA
16FMA
24GTR
25HGMD
26HMDB
27ICD10
28ICD10 via Orphanet
29ICD9CM
30IUPHAR
31KEGG
34MedGen
36MeSH
37MESH via Orphanet
38MGI
41NCI
42NCIt
43NDF-RT
46NINDS
47Novoseek
49OMIM
50OMIM via Orphanet
54PubMed
55QIAGEN
60SNOMED-CT via Orphanet
64Tumor Gene Family of Databases
65UMLS
66UMLS via Orphanet