MCID: FBR028
MIFTS: 25

Fibrosing Mediastinitis malady

Respiratory category

Summaries for Fibrosing Mediastinitis

Sources:
43NIH Rare Diseases, 33MalaCards
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NIH Rare Diseases:43 Fibrosing mediastinitis refers to scarring in the chest that can entrap the esophagus, the heart, the lymph nodes, and the major blood vessels that carry blood to and from the heart. the “mediastinum” refers specifically to the area between the lungs. the scarring may involve a single mass or be diffusely spread throughout the cavity.  in rare cases, fibrosing mediastinitis may extend into the soft tissues of the neck, the back of the chest, and into the lung. last updated: 4/23/2010

MalaCards: Fibrosing Mediastinitis, also known as mediastinal fibrosis, is related to superior vena cava syndrome and retroperitoneal fibrosis. Affiliated tissues include lymph node, heart and lung.

Aliases & Classifications for Fibrosing Mediastinitis

Sources:
43NIH Rare Diseases, 49Orphanet, 61UMLS, 36MESH via Orphanet, 26ICD10 via Orphanet, 58SNOMED-CT via Orphanet, 62UMLS via Orphanet
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Classifications:

Malacards categories (disease lists): (See all malacards categories)
Anatomical: Respiratory


Aliases & Descriptions:

fibrosing mediastinitis 43 49
mediastinal fibrosis 43 49 61
sclerosing mediastinitis 43 49
idiopathic mediastinal fibrosis 43
idiopathic hilar fibrosis 61


External Ids:

MESH via Orphanet36 C536136
ICD10 via Orphanet26 J98.5
SNOMED-CT via Orphanet58 21247003, 361196000, 7377003
UMLS via Orphanet62 C0221386, C0264573

Related Diseases for Fibrosing Mediastinitis

Sources:
17GeneCards, 18GeneDecks
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Diseases related to Fibrosing Mediastinitis via text searches within MalaCards or GeneCards/GeneDecks gene sharing:

(show all 22)
idRelated DiseaseScoreTop Affiliating Genes
1superior vena cava syndrome10.6
2retroperitoneal fibrosis10.4
3multifocal fibrosclerosis10.3
4pulmonary edema10.2
5pulmonary sarcoidosis10.2
6pulmonary vein stenosis10.2
7spondylarthropathy10.2
8xanthogranulomatous pyelonephritis10.1
9blastomycosis10.1
10bronchogenic carcinoma10.1
11anaplastic large cell lymphoma10.1
12thyroiditis10.1
13tuberculosis10.1
14bronchogenic cyst10.1
15zygomycosis10.1
16somatostatin analog10.1
17riedel thyroiditis10.1
18mast syndrome10.1
19sclerosing cholangitis10.0
20acne10.0
21aortic disease10.0
22synovitis10.0

Graphical network of the top 20 diseases related to Fibrosing Mediastinitis:



Diseases related to fibrosing mediastinitis

Clinical Features for Fibrosing Mediastinitis

Drugs & Therapeutics for Fibrosing Mediastinitis

Sources:
5CenterWatch, 42NIH Clinical Center, 6ClinicalTrials
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Approved drugs:

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Drug clinical trials:

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Search CenterWatch for Fibrosing Mediastinitis

Genetic Tests for Fibrosing Mediastinitis

Anatomical Context for Fibrosing Mediastinitis

Sources:
33MalaCards
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MalaCards organs/tissues related to Fibrosing Mediastinitis:

33
Lymph node, Heart, Lung, Thyroid, Breast, Trachea

Animal Models for Fibrosing Mediastinitis or affiliated genes

Sources:
28inGenious Targeting Laboratory
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Publications for Fibrosing Mediastinitis

Sources:
51PubMed
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Articles related to Fibrosing Mediastinitis:

(show top 50)    (show all 119)
idTitleAuthorsYear
1
Fibrosing mediastinitis mimicking bronchogenic carcinoma. (23372962)
2013
2
Fibrosing mediastinitis causing ostial coronary artery compression in a young woman: idiopathic or IgG4? (23603700)
2013
3
Fibrosing mediastinitis as a cause of right claudication. (21562863)
2012
4
The treatment of superior vena cava syndrome secondary to idiopathic fibrosing mediastinitis with balloon angioplasty and stenting. (23265133)
2012
5
Fibrosing mediastinitis with severe bilateral pulmonary artery narrowing: RV-RPA bypass with a homograft conduit. (22719157)
2012
6
Fibrosing mediastinitis causing ostial coronary artery compression in a young woman. (23257305)
2012
7
Fibrosing mediastinitis as a rare mechanism of pulmonary oedema in sarcoidosis. (20123854)
2010
8
Fibrosing mediastinitis causing acute ostial left main myocardial infarction. (20814057)
2010
9
Fibrosing mediastinitis and occlusion of pulmonary veins after radiofrequency ablation. (19853136)
2009
10
An unusual case of Aspergillus fibrosing mediastinitis. (19766844)
2009
11
Unilateral pulmonary vein stenosis secondary to idiopathic fibrosing mediastinitis. (21687296)
2009
12
Rare fibrosing granulomatous mediastinitis of tuberculosis with involvement of the transverse sinus. (17320609)
2007
13
A Potential Role for F-18 FDG PET/CT in Evaluation and Management of Fibrosing Mediastinitis. (17710023)
2007
14
Computed tomography and the idiopathic form of proliferative fibrosing mediastinitis. (17721332)
2007
15
Computed tomography findings in fibrosing mediastinitis. (17604768)
2007
16
Unilateral pulmonary edema due to pulmonary venous obstruction from fibrosing mediastinitis. (16520136)
2006
17
Complete resolution of fibrosing mediastinitis with corticosteroid therapy. (16108250)
2005
18
Cardiovascular collapse induced by position-dependent pulmonary vein occlusion in a patient with fibrosing mediastinitis. (16129994)
2005
19
Fibrosing mediastinitis causing rapidly progressive dyspnea, pulmonary edema and death in a 16 yr old male. (15510714)
2004
20
Fibrosing mediastinitis and thrombosis of superior vena cava associated with BehAset's disease. (14680916)
2003
21
Superior vena cava syndrome due to fibrosing mediastinitis histologically identical to xanthogranulomatous pyelonephritis. (12583620)
2003
22
Late superior vena cava perforation and aortic laceration after stenting to treat superior vena cava syndrome secondary to fibrosing mediastinitis. (12368518)
2002
23
Stent placement in the treatment of pulmonary artery stenosis secondary to fibrosing mediastinitis. (12119325)
2002
24
Tuberculous fibrosing mediastinitis: CT and MRI findings. (11428422)
2001
25
Stent placement in the treatment of pulmonary artery stenosis secondary to fibrosing mediastinitis. (11535776)
2001
26
Fibrosing mediastinitis. (11353121)
2001
27
Fibrosing mediastinitis. (11353120)
2001
28
Venous and arterial changes in pulmonary veno-occlusive disease, mitral stenosis and fibrosing mediastinitis. (10678631)
2000
29
Fibrosing mediastinitis associated with Riedel's thyroiditis--computed tomographic findings: case report. (9879270)
1998
30
Fibrosing mediastinitis: CT and MR findings. (9867275)
1998
31
Successful treatment of sclerosing cervicitis and fibrosing mediastinitis with tamoxifen. (9106605)
1997
32
Tuberculous fibrosing mediastinitis: radiologic findings. (8956619)
1996
33
The radiographic findings of fibrosing mediastinitis. (7774324)
1994
34
Cervical manifestations of fibrosing mediastinitis: a diagnostic and therapeutic dilemma. (8253566)
1993
35
Chronic fibrosing mediastinitis and superior vena caval obstruction from blastomycosis. (1417237)
1992
36
Pulmonary hypertension secondary to fibrosing mediastinitis. (1752029)
1991
37
Fibrosing mediastinitis in the posterior thorax. (2763944)
1989
38
Pulmonary vascular occlusion and fibrosing mediastinitis. (3943394)
1986
39
Magnetic resonance imaging of spiral vein graft bypass of superior vena cava in fibrosing mediastinitis. (3769568)
1986
40
Calcific fibrosing mediastinitis: demonstration of pulmonary vascular obstruction by magnetic resonance imaging. (6333789)
1984
41
Fibrosing mediastinitis. Causing pulmonary artery and vein obstruction with hemoptysis. (6572820)
1983
42
Angiographic and scintigraphic findings in fibrosing mediastinitis. (6221853)
1983
43
CT of fibrosing mediastinitis: findings and their utility. (6603112)
1983
44
Pulmonary scintigraphy in fibrosing mediastinitis due to histoplasmosis. (7205381)
1981
45
Pulmonary infarct: an unusual manifestation of fibrosing mediastinitis. (7357976)
1980
46
Pulmonary artery occlusion following fibrosing mediastinitis due to histoplasmosis. (421398)
1979
47
Pulmonary artery obstruction with fibrosing mediastinitis. (672256)
1978
48
Technique for reconstruction of superior vena cava in fibrosing mediastinitis. (4697444)
1973
49
Superior vena caval obstruction secondary to fibrosing mediastinitis. (4699947)
1973
50
Fibrosing mediastinitis. An unusual cause for cor pulmonale. (6025202)
1967

Genetic Variations for Fibrosing Mediastinitis

Expression for genes affiliated with Fibrosing Mediastinitis

Sources:
15Gene Expression Omnibus DataSets
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Search GEO for disease gene expression data for Fibrosing Mediastinitis.

Pathways for genes affiliated with Fibrosing Mediastinitis

Compounds for genes affiliated with Fibrosing Mediastinitis

GO Terms for genes affiliated with Fibrosing Mediastinitis

Products for genes affiliated with Fibrosing Mediastinitis

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Sources for Fibrosing Mediastinitis

3CDC
13ExPASy
14FMA
22GTR
23HGMD
24HMDB
25ICD10
26ICD10 via Orphanet
27ICD9CM
29IUPHAR
30KEGG
35MeSH
36MESH via Orphanet
37MGI
40NCIt
41NDF-RT
44NINDS
45Novoseek
47OMIM
48OMIM via Orphanet
51PubMed
52QIAGEN
58SNOMED-CT via Orphanet
61UMLS
62UMLS via Orphanet