MCID: FBR028
MIFTS: 25

Fibrosing Mediastinitis malady

Categories: Rare diseases, Respiratory diseases, Bone diseases

Aliases & Classifications for Fibrosing Mediastinitis

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Sources:
45NIH Rare Diseases, 51Orphanet, 65UMLS, 28ICD10 via Orphanet, 37MESH via Orphanet, 66UMLS via Orphanet
See all MalaCards sources

Aliases & Descriptions for Fibrosing Mediastinitis:

Name: Fibrosing Mediastinitis 45 51
Mediastinal Fibrosis 45 51 65
Igg4-Related Mediastinitis 45 51
 
Sclerosing Mediastinitis 45 51
Idiopathic Mediastinal Fibrosis 45
Idiopathic Hilar Fibrosis 65

Classifications:



External Ids:

Orphanet51 63999
ICD10 via Orphanet28 J98.5
MESH via Orphanet37 C536136
UMLS via Orphanet66 C0221386, C0264573
UMLS65 C0221386, C0264573

Summaries for Fibrosing Mediastinitis

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NIH Rare Diseases:45 Fibrosing mediastinitis is a condition that affects the area between the lungs (mediastinum) which contains the heart, large blood vessels, windpipe (trachea), esophagus, and lymph nodes. people with fibrosing mediastinitis have varying amounts of scar tissue in the mediastinum which may cause problems for the organs located there. for example, some affected people may develop blocked airways that can interfere with lung function. others may have compressed blood vessels which can slow or prevent blood flow to and from the heart. the exact cause of fibrosing mediastinitis is not fully understood, but it is not inherited. many cases are linked to a specific type of fungal infection called histoplasmosis. treatment depends on which structures of the mediastinum are affected, the severity of the scarring and, in some cases, the cause of the condition. last updated: 11/5/2014

MalaCards based summary: Fibrosing Mediastinitis, also known as mediastinal fibrosis, is related to mediastinitis and superior vena cava syndrome. Affiliated tissues include heart, lung and trachea.

Related Diseases for Fibrosing Mediastinitis

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Graphical network of the top 20 diseases related to Fibrosing Mediastinitis:



Diseases related to fibrosing mediastinitis

Symptoms for Fibrosing Mediastinitis

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Drugs & Therapeutics for Fibrosing Mediastinitis

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Interventional clinical trials:

idNameStatusNCT IDPhase
1Cohort Study of IgG4RDRecruitingNCT01670695Phase 0

Search NIH Clinical Center for Fibrosing Mediastinitis

Genetic Tests for Fibrosing Mediastinitis

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Anatomical Context for Fibrosing Mediastinitis

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MalaCards organs/tissues related to Fibrosing Mediastinitis:

33
Heart, Lung, Trachea, Lymph node, Breast, Endothelial, Bone

Animal Models for Fibrosing Mediastinitis or affiliated genes

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Publications for Fibrosing Mediastinitis

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Articles related to Fibrosing Mediastinitis:

(show top 50)    (show all 135)
idTitleAuthorsYear
1
Fibrosing mediastinitis: a rare complication of histoplasmosis. (26538131)
2015
2
Successful stenting of left pulmonary veins stenosis resulting from fibrosing mediastinitis. (25586119)
2015
3
Pulmonary Hypertension due to Fibrosing Mediastinitis Treated Successfully With Stenting of Pulmonary VeinA Stenoses. (25840104)
2015
4
Catheter-based intervention for pulmonary vein stenosis due to fibrosing mediastinitis: The Mayo Clinic experience. (26925456)
2015
5
Pulmonary Hypertension Complicating Fibrosing Mediastinitis. (26554778)
2015
6
Fibrosing Mediastinitis Mimicking Sarcoidosis. (24405501)
2014
7
Fibrosing mediastinitis mimicking postpartum heart failure. (25417662)
2014
8
Fibrosing mediastinitis: a squeeze on arterial and venous segments of the heart. (25024126)
2014
9
Fibrosing mediastinitis mimicking bronchogenic carcinoma. (23372962)
2013
10
Fibrosing mediastinitis: an unusual cause of pulmonary symptoms. (23807725)
2013
11
Anaplastic large cell lymphoma mimicking fibrosing mediastinitis. (24292756)
2013
12
Fibrosing mediastinitis as a cause of right claudication. (21562863)
2012
13
The treatment of superior vena cava syndrome secondary to idiopathic fibrosing mediastinitis with balloon angioplasty and stenting. (23265133)
2012
14
Percutaneous vascular stent implantation as treatment for central vascular obstruction due to fibrosing mediastinitis. (21422386)
2011
15
Bilateral breast enlargement: an unusual presentation of superior vena cava obstruction in a hemodialysis patient with fibrosing mediastinitis. (19949792)
2011
16
Sarcoidosis-associated fibrosing mediastinitis with resultant pulmonary hypertension: a case report and review of the literature. (19797887)
2010
17
Fibrosing mediastinitis associated with complete occlusion of the left main pulmonary artery. (19101331)
2009
18
Fibrosing mediastinitis and occlusion of pulmonary veins after radiofrequency ablation. (19853136)
2009
19
Fibrosing mediastinitis as an untypical complication of tuberculosis: case report. (19920801)
2009
20
An unusual case of Aspergillus fibrosing mediastinitis. (19766844)
2009
21
Fibrosing mediastinitis as a rare sequel of iatrogenic rupture of bronchogenic cyst--a case report. (17561459)
2008
22
Fibrosing mediastinitis mimicking malignancy at CT: negative FDG uptake in integrated FDG PET/CT imaging. (16944162)
2007
23
Fibrosing mediastinitis manifesting as thoracic prevertebral thin band-like mass on MRI and PET-CT. (17704310)
2007
24
Successful steroid treatment for fibrosing mediastinitis and sclerosing cervicitis. (17307498)
2007
25
Fibrosing mediastinitis associated with BehAset's disease: CT findings. (17920874)
2007
26
Unilateral pulmonary edema due to pulmonary venous obstruction from fibrosing mediastinitis. (16520136)
2006
27
Successful management of idiopathic fibrosing mediastinitis with superior vena cava thrombosis. (15758892)
2005
28
Fibrosing mediastinitis as a cause of superior vena cava syndrome. (15296918)
2004
29
Fibrosing mediastinitis and thrombosis of superior vena cava associated with BehAset's disease. (14680916)
2003
30
Late superior vena cava perforation and aortic laceration after stenting to treat superior vena cava syndrome secondary to fibrosing mediastinitis. (12368518)
2002
31
Elective stenting in superior vena cava syndrome caused by idiopathic fibrosing mediastinitis: use of self-expandable wallstent. (12462674)
2002
32
Fibrosing mediastinitis secondary to zygomycosis in a twenty-two-month-old child. (12150186)
2002
33
Tuberculous fibrosing mediastinitis: CT and MRI findings. (11428422)
2001
34
Percutaneous stenting of right pulmonary artery stenosis in fibrosing mediastinitis. (10700067)
2000
35
A case of fibrosing mediastinitis with obstruction of superior vena cava and downhill esophageal varices: a rare cause of upper gastrointestinal hemorrhage. (10192621)
1999
36
Localized idiopathic fibrosing mediastinitis as a cause of superior vena cava syndrome: a case report. (9492750)
1998
37
Successful treatment of sclerosing cervicitis and fibrosing mediastinitis with tamoxifen. (9106605)
1997
38
Fibrosing mediastinitis causing nonvisualization of one lung on pulmonary scintigraphy. (8344031)
1993
39
Chronic fibrosing mediastinitis and superior vena caval obstruction from blastomycosis. (1417237)
1992
40
Fibrosing mediastinitis in the posterior thorax. (2763944)
1989
41
Scintigraphy compared to other imaging modalities in benign superior vena caval obstruction accompanying fibrosing mediastinitis. (2819591)
1989
42
Pulmonary vascular occlusion and fibrosing mediastinitis. (3943394)
1986
43
Magnetic resonance imaging of spiral vein graft bypass of superior vena cava in fibrosing mediastinitis. (3769568)
1986
44
Pulmonary scintigraphy in fibrosing mediastinitis due to histoplasmosis. (7205381)
1981
45
Pulmonary infarct: an unusual manifestation of fibrosing mediastinitis. (7357976)
1980
46
Tracheal stenosis: an unusual presenting complication of idiopathic fibrosing mediastinitis. (7412344)
1980
47
Mediastinal granuloma and fibrosing mediastinitis. (421573)
1979
48
Pulmonary artery occlusion following fibrosing mediastinitis due to histoplasmosis. (421398)
1979
49
Progressive fibrosing mediastinitis. (5954469)
1966
50

Variations for Fibrosing Mediastinitis

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Expression for genes affiliated with Fibrosing Mediastinitis

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Search GEO for disease gene expression data for Fibrosing Mediastinitis.

Pathways for genes affiliated with Fibrosing Mediastinitis

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GO Terms for genes affiliated with Fibrosing Mediastinitis

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Sources for Fibrosing Mediastinitis

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2CDC
14ExPASy
15FDA
16FMA
24GTR
25HGMD
26HMDB
27ICD10
28ICD10 via Orphanet
29ICD9CM
30IUPHAR
31KEGG
34MedGen
36MeSH
37MESH via Orphanet
38MGI
41NCI
42NCIt
43NDF-RT
46NINDS
47Novoseek
49OMIM
50OMIM via Orphanet
54PubMed
55QIAGEN
60SNOMED-CT via Orphanet
64Tumor Gene Family of Databases
65UMLS
66UMLS via Orphanet