MCID: FBR028
MIFTS: 28

Fibrosing Mediastinitis malady

Rare diseases, Respiratory diseases categories
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Summaries for Fibrosing Mediastinitis

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NIH Rare Diseases:42 Fibrosing mediastinitis is a condition that affects the area between the lungs (mediastinum) which contains the heart, large blood vessels, windpipe (trachea), esophagus, and lymph nodes. people with fibrosing mediastinitis have varying amounts of scar tissue in the mediastinum which may cause problems for the organs located there. for example, some affected people may develop blocked airways that can interfere with lung function. others may have compressed blood vessels which can slow or prevent blood flow to and from the heart. the exact cause of fibrosing mediastinitis is not fully understood, but it is not inherited. many cases are linked to a specific type of fungal infection called histoplasmosis. treatment depends on which structures of the mediastinum are affected, the severity of the scarring and, in some cases, the cause of the condition. last updated: 11/5/2014

MalaCards based summary: Fibrosing Mediastinitis, also known as mediastinal fibrosis, is related to mediastinitis and superior vena cava syndrome. Affiliated tissues include lung, heart and trachea.

Aliases & Classifications for Fibrosing Mediastinitis

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Sources:
42NIH Rare Diseases, 48Orphanet, 62UMLS, 35MESH via Orphanet, 26ICD10 via Orphanet, 63UMLS via Orphanet
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Fibrosing Mediastinitis, Aliases & Descriptions:

Name: Fibrosing Mediastinitis 42 48
Mediastinal Fibrosis 42 48 62
Idiopathic Mediastinal Fibrosis 42 62
 
Sclerosing Mediastinitis 42 48
Idiopathic Hilar Fibrosis 62


Classifications:

Malacards categories (disease lists): (See all malacards categories)
Global: Rare diseases
Anatomical: Respiratory diseases


External Ids:

MESH via Orphanet35 C536136
ICD10 via Orphanet26 J98.5
UMLS via Orphanet63 C0221386, C0264573

Related Diseases for Fibrosing Mediastinitis

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Graphical network of the top 20 diseases related to Fibrosing Mediastinitis:



Diseases related to fibrosing mediastinitis

Symptoms for Fibrosing Mediastinitis

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Drugs & Therapeutics for Fibrosing Mediastinitis

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Drug clinical trials:

Search ClinicalTrials for Fibrosing Mediastinitis

Search NIH Clinical Center for Fibrosing Mediastinitis

Genetic Tests for Fibrosing Mediastinitis

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Anatomical Context for Fibrosing Mediastinitis

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MalaCards organs/tissues related to Fibrosing Mediastinitis:

32
Lung, Heart, Trachea, Lymph node, Thyroid, Breast

Animal Models for Fibrosing Mediastinitis or affiliated genes

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Publications for Fibrosing Mediastinitis

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Articles related to Fibrosing Mediastinitis:

(show top 50)    (show all 120)
idTitleAuthorsYear
1
Fibrosing Mediastinitis Mimicking Sarcoidosis. (24405501)
2014
2
Fibrosing mediastinitis: a squeeze on arterial and venous segments of the heart. (25024126)
2014
3
Fibrosing mediastinitis mimicking bronchogenic carcinoma. (23372962)
2013
4
Fibrosing mediastinitis: an unusual cause of pulmonary symptoms. (23807725)
2013
5
Anaplastic large cell lymphoma mimicking fibrosing mediastinitis. (24292756)
2013
6
Fibrosing mediastinitis as a cause of right claudication. (21562863)
2012
7
The treatment of superior vena cava syndrome secondary to idiopathic fibrosing mediastinitis with balloon angioplasty and stenting. (23265133)
2012
8
Percutaneous vascular stent implantation as treatment for central vascular obstruction due to fibrosing mediastinitis. (21422386)
2011
9
Bilateral breast enlargement: an unusual presentation of superior vena cava obstruction in a hemodialysis patient with fibrosing mediastinitis. (19949792)
2011
10
Pulmonary artery stenosis secondary to fibrosing mediastinitis: management with cutting balloon angioplasty and endovascular stenting. (21278182)
2011
11
Sarcoidosis-associated fibrosing mediastinitis with resultant pulmonary hypertension: a case report and review of the literature. (19797887)
2010
12
Fibrosing mediastinitis associated with complete occlusion of the left main pulmonary artery. (19101331)
2009
13
Fibrosing mediastinitis and occlusion of pulmonary veins after radiofrequency ablation. (19853136)
2009
14
Fibrosing mediastinitis as an untypical complication of tuberculosis: case report. (19920801)
2009
15
An unusual case of Aspergillus fibrosing mediastinitis. (19766844)
2009
16
Fibrosing mediastinitis as a rare sequel of iatrogenic rupture of bronchogenic cyst--a case report. (17561459)
2008
17
Fibrosing mediastinitis mimicking malignancy at CT: negative FDG uptake in integrated FDG PET/CT imaging. (16944162)
2007
18
Fibrosing mediastinitis manifesting as thoracic prevertebral thin band-like mass on MRI and PET-CT. (17704310)
2007
19
Successful steroid treatment for fibrosing mediastinitis and sclerosing cervicitis. (17307498)
2007
20
Fibrosing mediastinitis associated with BehAset's disease: CT findings. (17920874)
2007
21
Fibrosing mediastinitis presenting as pulmonary stenosis: stenting works. (17399816)
2007
22
Unilateral pulmonary edema due to pulmonary venous obstruction from fibrosing mediastinitis. (16520136)
2006
23
Successful management of idiopathic fibrosing mediastinitis with superior vena cava thrombosis. (15758892)
2005
24
Complete resolution of fibrosing mediastinitis with corticosteroid therapy. (16108250)
2005
25
Fibrosing mediastinitis as a cause of superior vena cava syndrome. (15296918)
2004
26
Fibrosing mediastinitis and thrombosis of superior vena cava associated with BehAset's disease. (14680916)
2003
27
Late superior vena cava perforation and aortic laceration after stenting to treat superior vena cava syndrome secondary to fibrosing mediastinitis. (12368518)
2002
28
Elective stenting in superior vena cava syndrome caused by idiopathic fibrosing mediastinitis: use of self-expandable wallstent. (12462674)
2002
29
Fibrosing mediastinitis secondary to zygomycosis in a twenty-two-month-old child. (12150186)
2002
30
Tuberculous fibrosing mediastinitis: CT and MRI findings. (11428422)
2001
31
Percutaneous stenting of right pulmonary artery stenosis in fibrosing mediastinitis. (10700067)
2000
32
A case of fibrosing mediastinitis with obstruction of superior vena cava and downhill esophageal varices: a rare cause of upper gastrointestinal hemorrhage. (10192621)
1999
33
Localized idiopathic fibrosing mediastinitis as a cause of superior vena cava syndrome: a case report. (9492750)
1998
34
Fibrosing mediastinitis associated with Riedel's thyroiditis--computed tomographic findings: case report. (9879270)
1998
35
Successful treatment of sclerosing cervicitis and fibrosing mediastinitis with tamoxifen. (9106605)
1997
36
Tuberculous fibrosing mediastinitis: radiologic findings. (8956619)
1996
37
Fibrosing mediastinitis causing nonvisualization of one lung on pulmonary scintigraphy. (8344031)
1993
38
Cervical manifestations of fibrosing mediastinitis: a diagnostic and therapeutic dilemma. (8253566)
1993
39
Chronic fibrosing mediastinitis and superior vena caval obstruction from blastomycosis. (1417237)
1992
40
Coronary artery bypass grafting with unanticipated fibrosing mediastinitis. (2306156)
1990
41
Fibrosing mediastinitis in the posterior thorax. (2763944)
1989
42
Scintigraphy compared to other imaging modalities in benign superior vena caval obstruction accompanying fibrosing mediastinitis. (2819591)
1989
43
Pulmonary vascular occlusion and fibrosing mediastinitis. (3943394)
1986
44
Magnetic resonance imaging of spiral vein graft bypass of superior vena cava in fibrosing mediastinitis. (3769568)
1986
45
Pulmonary infarct: an unusual manifestation of fibrosing mediastinitis. (7357976)
1980
46
Tracheal stenosis: an unusual presenting complication of idiopathic fibrosing mediastinitis. (7412344)
1980
47
Mediastinal granuloma and fibrosing mediastinitis. (421573)
1979
48
Pulmonary artery occlusion following fibrosing mediastinitis due to histoplasmosis. (421398)
1979
49
Mediastinal granuloma and fibrosing mediastinitis. (510018)
1979
50
Progressive fibrosing mediastinitis. (5954469)
1966

Variations for Fibrosing Mediastinitis

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Expression for genes affiliated with Fibrosing Mediastinitis

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Search GEO for disease gene expression data for Fibrosing Mediastinitis.

Pathways for genes affiliated with Fibrosing Mediastinitis

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Compounds for genes affiliated with Fibrosing Mediastinitis

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GO Terms for genes affiliated with Fibrosing Mediastinitis

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Products for genes affiliated with Fibrosing Mediastinitis

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Sources for Fibrosing Mediastinitis

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3CDC
13ExPASy
14FMA
22GTR
23HGMD
24HMDB
25ICD10
26ICD10 via Orphanet
27ICD9CM
28IUPHAR
29KEGG
34MeSH
35MESH via Orphanet
36MGI
39NCIt
40NDF-RT
43NINDS
44Novoseek
46OMIM
47OMIM via Orphanet
51PubMed
52QIAGEN
58SNOMED-CT via Orphanet
62UMLS
63UMLS via Orphanet