MCID: FLL013
MIFTS: 35

Follicular Dendritic Cell Sarcoma malady

Blood diseases, Cancer diseases, Rare diseases categories

Aliases & Classifications for Follicular Dendritic Cell Sarcoma

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Sources:
10Disease Ontology, 51Orphanet, 65UMLS, 36MeSH, 42NCIt, 59SNOMED-CT, 28ICD10 via Orphanet, 37MESH via Orphanet, 66UMLS via Orphanet
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Aliases & Descriptions for Follicular Dendritic Cell Sarcoma:

Name: Follicular Dendritic Cell Sarcoma 10 51
Dendritic Cell Sarcoma, Follicular 65 36
 
Follicular Dendritic Cell Tumour 10


Classifications:



Characteristics (Orphanet epidemiological data):

51
follicular dendritic cell sarcoma:
Age of onset: All ages


External Ids:

Disease Ontology10 DOID:6262
NCIt42 C9281
MeSH36 D054740
Orphanet51 86902
SNOMED-CT59 128816008
ICD10 via Orphanet28 C96.4
MESH via Orphanet37 D054740
UMLS via Orphanet66 C1260325

Summaries for Follicular Dendritic Cell Sarcoma

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Wikipedia:68 Follicular dendritic cell sarcoma (FDCS) is an extremely rare neoplasm. While the existence of FDC... more...

MalaCards based summary: Follicular Dendritic Cell Sarcoma, also known as dendritic cell sarcoma, follicular, is related to thymoma and dendritic cell sarcoma. An important gene associated with Follicular Dendritic Cell Sarcoma is CR2 (Complement Component (3d/Epstein Barr Virus) Receptor 2), and among its related pathways are Immune response Lectin induced complement pathway and Hematopoietic cell lineage. Affiliated tissues include tonsil, bone and lymph node.

Disease Ontology:10 A dendritic cell sarcoma cancer that effects the follicular dendritic cells.

Related Diseases for Follicular Dendritic Cell Sarcoma

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Diseases related to Follicular Dendritic Cell Sarcoma via text searches within MalaCards or GeneCards Suite gene sharing:

(show top 50)    (show all 58)
idRelated DiseaseScoreTop Affiliating Genes
1thymoma30.3KIT, NKX2-1
2dendritic cell sarcoma11.4
3sarcoma11.4
4pemphigus10.8
5tonsillitis10.8
6paraneoplastic pemphigus10.8
7mediastinitis10.6
8myasthenia gravis10.5
9pharyngitis10.5
10thyroiditis10.5
11hepatitis10.4
12cervicitis10.4
13castleman disease10.4
14kaposi sarcoma10.3
15leukemia10.3
16interdigitating dendritic cell sarcoma10.3
17amyloidosis10.3
18cellulitis10.3
19myeloid leukemia10.3
20peritonitis10.3
21non-secretory myeloma10.2CR1, CR2
22pancreatic non-functioning delta cell tumor10.2CR1, CR2
23laryngeal small cell carcinoma10.2CR1, CR2
24tabatznik syndrome10.2CR1, CR2
25pilocytic astrocytoma of cerebellum10.2CR1, CR2
26catamenial pneumothorax10.2CR1, CR2
27complement factor i deficiency10.2CR1, CR2
28autosomal dominant medullary cystic kidney disease with hyperuricemia10.2CR1, CR2
29dennis fairhurst moore syndrome10.2CR1, CR2
30macular holes10.1CR2, NKX2-1
31braddock syndrome10.1DSG1, DSP
32autoimmune disease of the nervous system10.0DSG1, DSP
33acute frontal sinusitis10.0CR2, KIT
34peri-anal fistula10.0DSG1, DSP
35localized pulmonary fibrosis10.0CR2, KIT
36bursitis10.0DSG1, DSP
37hay-wells syndrome10.0DSG1, DSP
38ichthyosis - hypotrichosis - sclerosing cholangitis10.0DSG1, DSP
39hole retinal cyst10.0KIT, NKX2-1
40retinal artery occlusion10.0KIT, NKX2-1
41histiocytoma10.0CR1, CR2, DSP
42oral hairy leukoplakia9.9KIT, NKX2-1
43progressive sensorineural hearing loss - hypertrophic cardiomyopathy9.9KIT, NKX2-1
44clear cell chondrosarcoma9.9DSP, KIT
45pancoast tumor9.9DSG1, DSP
46periodontal disease9.9DSP, KIT
47pulmonary neuroendocrine tumor9.9KIT, NKX2-1
48alcoholic psychosis9.9DSG1, DSP
49benign hypertensive renal disease9.9KIT, NKX2-1
50silent myocardial infarction9.9KIT, NKX2-1

Graphical network of the top 20 diseases related to Follicular Dendritic Cell Sarcoma:



Diseases related to follicular dendritic cell sarcoma

Symptoms for Follicular Dendritic Cell Sarcoma

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Drugs & Therapeutics for Follicular Dendritic Cell Sarcoma

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Interventional clinical trials:

idNameStatusNCT IDPhase
1Study of Intratumoral G100 Therapy in Patients With Or Without Pembrolizumab With Follicular Non-Hodgkin's LymphomaRecruitingNCT02501473Phase 1, Phase 2

Search NIH Clinical Center for Follicular Dendritic Cell Sarcoma


Cochrane evidence based reviews: Dendritic Cell Sarcoma, Follicular

Genetic Tests for Follicular Dendritic Cell Sarcoma

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Anatomical Context for Follicular Dendritic Cell Sarcoma

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MalaCards organs/tissues related to Follicular Dendritic Cell Sarcoma:

33
Tonsil, Bone, Lymph node, Liver, Thyroid, Spleen, T cells

Animal Models for Follicular Dendritic Cell Sarcoma or affiliated genes

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Publications for Follicular Dendritic Cell Sarcoma

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Articles related to Follicular Dendritic Cell Sarcoma:

(show top 50)    (show all 164)
idTitleAuthorsYear
1
Follicular Dendritic Cell Sarcoma: Cytogenetics and pathological findings. (26355964)
2015
2
Follicular Dendritic Cell Sarcoma of Lymph Node: A report of a Patient with Chronic Myeloid Leukemia Treated with Imatinib. (26261702)
2015
3
Follicular dendritic cell sarcoma of the tonsil. (25512260)
2015
4
Follicular dendritic cell sarcoma of the right tonsil: A case report and literature review. (25621026)
2015
5
Intraperitoneal follicular dendritic cell sarcoma: role of chemotherapy and bone marrow allotransplantation in locally advanced disease? (25698886)
2015
6
Paraneoplastic pemphigus associated with primary pulmonar follicular dendritic cell sarcoma showing good response to treatment. (25388966)
2014
7
Extranodal follicular dendritic cell sarcoma of the soft palate: a case report. (25674273)
2014
8
Response of follicular dendritic cell sarcoma to gemcitabine and docetaxel: report of two cases and literature review. (25009738)
2014
9
Follicular Dendritic Cell Sarcoma Presenting As a Thyroid Mass. (24663046)
2014
10
A 46-year-old Chinese woman presenting with retroperitoneal follicular dendritic cell sarcoma: a case report. (24708915)
2014
11
Recalcitrant paraneoplastic pemphigus associated with follicular dendritic cell sarcoma: response to prolonged rituximab and ciclosporin therapy. (25367731)
2014
12
Mediastinal follicular dendritic cell sarcoma with paraneoplastic pemphigus. (25406405)
2014
13
Inflammatory pseudotumor-like follicular dendritic cell sarcoma of the spleen: a report of six cases with increased IgG4-positive plasma cells. (23714251)
2013
14
A rare case of follicular dendritic cell sarcoma involving multiple bones. (23640234)
2013
15
Follicular dendritic cell sarcoma associated with hyaline-vascular Castleman's disease. (23914648)
2013
16
Transformation of Castleman's disease into follicular dendritic cell sarcoma, presenting as an asymptomatic intra-abdominal mass. (23981949)
2013
17
Cytogenetic abnormalities in follicular dendritic cell sarcoma: report of two cases and literature review. (23422480)
2013
18
Pathology quiz case 1. Follicular dendritic cell sarcoma (FDS). (22801898)
2012
19
Computed tomography and 18F-fluoro-2-deoxyglucose positron emission tomography findings of primary pulmonary follicular dendritic cell sarcoma: case report and a literature review. (21795995)
2012
20
Follicular dendritic cell sarcoma of the tonsil. (23251062)
2012
21
Follicular Dendritic Cell Sarcoma of the Head and Neck Expressing Thyroid Transcription Factor-1: A Case Report With Clinicopathologic and Immunohistochemical Literature Review. (21836499)
2012
22
I^-Synuclein is a promising new marker for staining reactive follicular dendritic cells, follicular dendritic cell sarcoma, Kaposi sarcoma, and benign and malignant vascular tumors. (21959308)
2011
23
Follicular dendritic cell sarcoma of the liver: unusual presentation of a rare tumor and literature review. (21813397)
2011
24
Follicular dendritic cell sarcoma of the lung: a report of two cases highlighting its pathological features and diagnostic pitfalls. (21240069)
2011
25
Follicular dendritic cell sarcoma of the tonsil. (20499431)
2010
26
Follicular dendritic cell sarcoma of the abdomen: the imaging findings. (20191073)
2010
27
Follicular dendritic cell sarcoma of small intestine with aberrant T-cell marker expression. (19883432)
2009
28
Follicular dendritic cell sarcoma with microtubuloreticular structure and virus-like particle production in vitro. (19432677)
2009
29
SIR 2008 annual meeting film panel case: Castleman disease complicated by follicular dendritic cell sarcoma. (18656005)
2008
30
Cytogenetic abnormality 46,XX,add(21)(q11.2) in a patient with follicular dendritic cell sarcoma. (18786443)
2008
31
Intra-abdominal follicular dendritic cell sarcoma with marked pleomorphic features and aberrant expression of neuroendocrine markers: report of a case with immunohistochemical analysis. (17721283)
2007
32
Follicular dendritic cell sarcoma of the tonsil: a case report and literature review. (17500398)
2007
33
Clinicopathologic study of intraabdominal extranodal follicular dendritic cell sarcoma]. (18194598)
2007
34
Follicular dendritic cell sarcoma: a report of 14 cases and a review of the literature. (17373675)
2007
35
Interwoven dendritic processes of follicular dendritic cell sarcoma demonstrated on ultrafast papanicolaou-stained smears: a case report. (17017440)
2006
36
Follicular dendritic cell sarcoma of lymph node--a rare entity. (16696516)
2006
37
Nodal follicular dendritic cell sarcoma of the axilla presenting as cellulitis. (16403115)
2006
38
Follicular dendritic cell sarcoma mimicking giant cell carcinoma of the pancreas. (16872443)
2006
39
Paraneoplastic pemphigus associated with follicular dendritic cell sarcoma and Castleman disease. (16029358)
2005
40
Autoantibody production from a thymoma and a follicular dendritic cell sarcoma associated with paraneoplastic pemphigus. (16120143)
2005
41
Follicular dendritic cell sarcoma: case report and review of current management principles. (16343408)
2005
42
Symptoms in cancer patients and an unusual tumor: Case 3. Follicular dendritic cell sarcoma. (16361643)
2005
43
Metastatic follicular dendritic cell sarcoma of the stomach: a case report and review of the literature. (15285580)
2004
44
Intracranial follicular dendritic cell sarcoma. Case report. (14705740)
2003
45
Follicular dendritic cell sarcoma of the neck; a case report and literature review. (12393051)
2002
46
Fine needle aspiration cytology of follicular dendritic cell sarcoma. Report of a case with cytologic detection in an extranodal site. (11015984)
2000
47
Extranodal follicular dendritic cell sarcoma of the palate. (10052377)
1999
48
Myxoid variant of follicular dendritic cell sarcoma arising in the breast. (10196389)
1999
49
Follicular dendritic cell sarcoma. Clinicopathologic analysis of 17 cases suggesting a malignant potential higher than currently recognized. (9010103)
1997
50
Follicular dendritic cell sarcoma mimicking diffuse large cell lymphoma: a case report. (9256295)
1997

Variations for Follicular Dendritic Cell Sarcoma

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Expression for genes affiliated with Follicular Dendritic Cell Sarcoma

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Search GEO for disease gene expression data for Follicular Dendritic Cell Sarcoma.

Pathways for genes affiliated with Follicular Dendritic Cell Sarcoma

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GO Terms for genes affiliated with Follicular Dendritic Cell Sarcoma

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Cellular components related to Follicular Dendritic Cell Sarcoma according to GeneCards Suite gene sharing:

idNameGO IDScoreTop Affiliating Genes
1cytoplasmic side of plasma membraneGO:00098989.9DSG1, KIT
2desmosomeGO:00300579.7DSG1, DSP
3cell-cell junctionGO:00059119.2DSG1, DSP, KIT
4extracellular exosomeGO:00700628.2CLU, CR1, CR2, DSG1, DSP

Biological processes related to Follicular Dendritic Cell Sarcoma according to GeneCards Suite gene sharing:

idNameGO IDScoreTop Affiliating Genes
1complement receptor mediated signaling pathwayGO:000243010.1CR1, CR2
2viral entry into host cellGO:004671810.0CR1, CR2
3cellular component disassembly involved in execution phase of apoptosisGO:00069219.6DSG1, DSP
4complement activation, classical pathwayGO:00069589.5CLU, CR1, CR2
5innate immune responseGO:00450878.5CLU, CR1, CR2, KIT

Molecular functions related to Follicular Dendritic Cell Sarcoma according to GeneCards Suite gene sharing:

idNameGO IDScoreTop Affiliating Genes
1virus receptor activityGO:00016189.7CR1, CR2

Sources for Follicular Dendritic Cell Sarcoma

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2CDC
14ExPASy
15FDA
16FMA
24GTR
25HGMD
26HMDB
27ICD10
28ICD10 via Orphanet
29ICD9CM
30IUPHAR
31KEGG
34MedGen
36MeSH
37MESH via Orphanet
38MGI
41NCI
42NCIt
43NDF-RT
46NINDS
47Novoseek
49OMIM
50OMIM via Orphanet
54PubMed
55QIAGEN
60SNOMED-CT via Orphanet
64Tumor Gene Family of Databases
65UMLS
66UMLS via Orphanet