MCID: FLL013
MIFTS: 36

Follicular Dendritic Cell Sarcoma malady

Categories: Blood diseases, Rare diseases, Cancer diseases, Immune diseases

Aliases & Classifications for Follicular Dendritic Cell Sarcoma

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Sources:
11Disease Ontology, 13DISEASES, 52Orphanet, 37MeSH, 66UMLS, 28ICD10, 43NCIt, 29ICD10 via Orphanet, 38MESH via Orphanet, 67UMLS via Orphanet, 60SNOMED-CT
See all MalaCards sources

Aliases & Descriptions for Follicular Dendritic Cell Sarcoma:

Name: Follicular Dendritic Cell Sarcoma 11 13 52
Dendritic Cell Sarcoma, Follicular 37 66
 
Follicular Dendritic Cell Tumour 11

Characteristics:

Orphanet epidemiological data:

52
follicular dendritic cell sarcoma:
Age of onset: All ages

Classifications:



External Ids:

Disease Ontology11 DOID:6262
ICD1028 C96.4
MeSH37 D054740
NCIt43 C9281
SNOMED-CT60 128816008
Orphanet52 ORPHA86902
ICD10 via Orphanet29 C96.4
MESH via Orphanet38 D054740
UMLS via Orphanet67 C1260325

Summaries for Follicular Dendritic Cell Sarcoma

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Wikipedia:69 Follicular dendritic cell sarcoma (FDCS) is an extremely rare neoplasm. While the existence of FDC... more...

MalaCards based summary: Follicular Dendritic Cell Sarcoma, also known as dendritic cell sarcoma, follicular, is related to dendritic cell sarcoma and sarcoma. An important gene associated with Follicular Dendritic Cell Sarcoma is CR2 (Complement C3d Receptor 2), and among its related pathways are IgA-Producing B Cells in the Intestine and Phagocytosis of Microbes. Affiliated tissues include tonsil, lymph node and liver.

Disease Ontology:11 A dendritic cell sarcoma cancer that effects the follicular dendritic cells.

Related Diseases for Follicular Dendritic Cell Sarcoma

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Diseases related to Follicular Dendritic Cell Sarcoma via text searches within MalaCards or GeneCards Suite gene sharing:

(show top 50)    (show all 53)
idRelated DiseaseScoreTop Affiliating Genes
1dendritic cell sarcoma11.8
2sarcoma11.0
3tonsillitis10.5
4pemphigus10.5
5paraneoplastic pemphigus10.5
6penile urethral cancer10.4CR1, CR2
7pancreatic intraductal papillary-mucinous adenoma10.4CR1, CR2
8prostate stromal sarcoma10.4CR1, CR2
9angioma hereditary neurocutaneous10.4CR1, CR2
10teebi kaurah syndrome10.4CR1, CR2
11cerebral arterial disease10.4CR1, CR2
12mediastinitis10.3
13myasthenia gravis10.3
14sporadic idiopathic steroid-resistant nephrotic syndrome with minimal changes10.2CR1, CR2
15vulvar liposarcoma10.2CR2, KIT
16pharyngitis10.1
17thyroiditis10.1
18adenosquamous bile duct carcinoma10.1CLU, CR1, CR2
19hepatitis10.1
20cervicitis10.1
21castleman disease10.1
22short-rib thoracic dysplasia 1210.0CR1, CR2, FCER2
23dens in dente and palatal invaginations10.0CR1, CR2, FCER2
24mixed extragonadal germ cell cancer9.9CR1, CR2, KIT
25breast cancer9.9
26kaposi sarcoma9.9
27nasopharyngeal carcinoma9.9
28reticulum cell sarcoma9.9
29arthritis9.9
30leukemia9.9
31lymphoma9.9
32nasopharyngitis9.9
33thymoma9.9
34cellulitis9.9
35interdigitating dendritic cell sarcoma9.9
36peritonitis9.9
37appendicitis9.9
38myeloid leukemia9.9
39amyloidosis9.9
40liver inflammatory pseudotumor9.9
41acute poisoning by drugs with membrane-stabilizing effect9.8DSG1, DSP
42cardiomyopathy, dilated, 1bb9.8DSG1, DSP
43tropical spastic paraparesis9.8DSP, KIT
44epicardium cancer9.7DSP, KIT
45peripheral t-cell lymphoma9.7DSG1, DSP
46autism spectrum disorder9.7DSG1, DSP
47impetigo9.6DSG1, DSP
48lipoma9.5DSG1, DSP
49diabetic macular edema9.5DSG1, DSP
50cirrhotic cardiomyopathy9.4DSG1, DSP

Graphical network of the top 20 diseases related to Follicular Dendritic Cell Sarcoma:



Diseases related to follicular dendritic cell sarcoma

Symptoms for Follicular Dendritic Cell Sarcoma

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Drugs & Therapeutics for Follicular Dendritic Cell Sarcoma

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Interventional clinical trials:

Search ClinicalTrials, NIH Clinical Center for Follicular Dendritic Cell Sarcoma


Cochrane evidence based reviews: dendritic cell sarcoma, follicular

Genetic Tests for Follicular Dendritic Cell Sarcoma

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Anatomical Context for Follicular Dendritic Cell Sarcoma

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MalaCards organs/tissues related to Follicular Dendritic Cell Sarcoma:

34
Tonsil, Lymph node, Liver, Spleen, Colon, Thyroid, Bone

Animal Models for Follicular Dendritic Cell Sarcoma or affiliated genes

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Publications for Follicular Dendritic Cell Sarcoma

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Articles related to Follicular Dendritic Cell Sarcoma:

(show top 50)    (show all 189)
idTitleAuthorsYear
1
Follicular Dendritic Cell Sarcoma of Appendix Presenting as Acute Appendicitis: An Exceptionally Rare Case Report. (27225654)
2016
2
Computer Tomography Imaging Findings of Abdominal Follicular Dendritic Cell Sarcoma: A Report of 5 Cases. (26735543)
2016
3
Follicular dendritic cell tumour/sarcoma: a commonly misdiagnosed tumour in the thorax Intrathoracic follicular dendritic cell sarcoma. (27206572)
2016
4
Response to rituximab in an anti-muscle-specific receptor tyrosine kinase- and anti-acetylcholine recepto-double-positive myasthenia gravis patient concomitant with follicular dendritic cell sarcoma. (26818174)
2016
5
Paraneoplastic arthritis as first symptom of a liver inflammatory pseudotumor-like follicular dendritic cell sarcoma. (27125361)
2016
6
Paraneoplastic pemphigus and myasthenia gravis, associated with inflammatory pseudotumor-like follicular dendritic cell sarcoma: response to rituximab. (27525088)
2016
7
Follicular Dendritic Cell Sarcoma: Cytogenetics and pathological findings. (26355964)
2015
8
Follicular dendritic cell sarcoma of the tonsil. (25512260)
2015
9
Targeted genomic sequencing of follicular dendritic cell sarcoma reveals recurrent alterations in NF-I_B regulatory genes. (26564005)
2015
10
Follicular dendritic cell sarcoma: two rare cases and a brief review of the literature. (26244020)
2015
11
Extranodal follicular dendritic cell sarcoma: A clinicopathological report of four cases and a literature review. (25435998)
2015
12
Extranodal follicular dendritic cell sarcoma of the soft palate: a case report. (25674273)
2014
13
Follicular Dendritic Cell Sarcoma Presenting As a Thyroid Mass. (24663046)
2014
14
Recalcitrant paraneoplastic pemphigus associated with follicular dendritic cell sarcoma: response to prolonged rituximab and ciclosporin therapy. (25367731)
2014
15
Mediastinal follicular dendritic cell sarcoma with paraneoplastic pemphigus. (25406405)
2014
16
Follicular dendritic cell sarcoma of the stomach: case report and review of the literature. (25489266)
2014
17
Inflammatory pseudotumor-like follicular dendritic cell sarcoma of the spleen: a report of six cases with increased IgG4-positive plasma cells. (23714251)
2013
18
A rare case of follicular dendritic cell sarcoma involving multiple bones. (23640234)
2013
19
Transformation of Castleman's disease into follicular dendritic cell sarcoma, presenting as an asymptomatic intra-abdominal mass. (23981949)
2013
20
Cytogenetic abnormalities in follicular dendritic cell sarcoma: report of two cases and literature review. (23422480)
2013
21
Follicular dendritic cell sarcoma of the tonsil. (23415609)
2013
22
Intraabdominal follicular dendritic cell sarcoma: a report of three cases and review of the literature. (23748832)
2013
23
Extranodal follicular dendritic cell sarcoma with rapid growth in parapharynx: a case report. (23110021)
2012
24
Follicular dendritic cell sarcoma of the tonsil. (23251062)
2012
25
Follicular dendritic cell sarcoma: a diagnostic challenge ! (22842383)
2012
26
Follicular dendritic cell sarcoma of the liver: unusual presentation of a rare tumor and literature review. (21813397)
2011
27
Follicular dendritic cell sarcoma of the lung: a report of two cases highlighting its pathological features and diagnostic pitfalls. (21240069)
2011
28
Cervical follicular dendritic cell sarcoma: a case report and review of the literature. (21658332)
2011
29
Imaging findings of follicular dendritic cell sarcoma: report of four cases. (21228948)
2011
30
Hepatic follicular dendritic cell sarcoma favorably controlled by transcatheter arterial chemoembolization. (21173546)
2010
31
Extranodal follicular dendritic cell sarcoma of the pharyngeal region: a potential diagnostic pitfall, with literature review. (20023258)
2010
32
Clinicopathological features and prognosis assessment of extranodal follicular dendritic cell sarcoma. (20503450)
2010
33
Follicular dendritic cell sarcoma of small intestine with aberrant T-cell marker expression. (19883432)
2009
34
Follicular dendritic cell sarcoma with microtubuloreticular structure and virus-like particle production in vitro. (19432677)
2009
35
Follicular dendritic cell sarcoma of the parotid gland recurring 6 times within 12 years. (19884836)
2009
36
SIR 2008 annual meeting film panel case: Castleman disease complicated by follicular dendritic cell sarcoma. (18656005)
2008
37
Cytogenetic abnormality 46,XX,add(21)(q11.2) in a patient with follicular dendritic cell sarcoma. (18786443)
2008
38
Interwoven dendritic processes of follicular dendritic cell sarcoma demonstrated on ultrafast papanicolaou-stained smears: a case report. (17017440)
2006
39
Nodal follicular dendritic cell sarcoma of the axilla presenting as cellulitis. (16403115)
2006
40
Retroperitoneal follicular dendritic cell sarcoma. (16867894)
2006
41
Autoantibody production from a thymoma and a follicular dendritic cell sarcoma associated with paraneoplastic pemphigus. (16120143)
2005
42
Follicular dendritic cell sarcoma: case report and review of current management principles. (16343408)
2005
43
Intracranial follicular dendritic cell sarcoma. Case report. (14705740)
2003
44
Mediastinal follicular dendritic cell sarcoma. (12604428)
2003
45
Epidermal growth factor receptor expression in follicular dendritic cells: a shared feature of follicular dendritic cell sarcoma and Castleman's disease. (14562277)
2003
46
Follicular dendritic cell sarcoma of the neck; a case report and literature review. (12393051)
2002
47
Follicular dendritic cell sarcoma of the colon mimicking stromal tumour. (11135043)
2001
48
Extranodal follicular dendritic cell sarcoma of the palate. (10052377)
1999
49
Follicular dendritic cell sarcoma and interdigitating reticulum cell sarcoma: a review. (9766802)
1998
50
Follicular dendritic cell sarcoma. Clinicopathologic analysis of 17 cases suggesting a malignant potential higher than currently recognized. (9010103)
1997

Variations for Follicular Dendritic Cell Sarcoma

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Expression for genes affiliated with Follicular Dendritic Cell Sarcoma

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Search GEO for disease gene expression data for Follicular Dendritic Cell Sarcoma.

Pathways for genes affiliated with Follicular Dendritic Cell Sarcoma

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GO Terms for genes affiliated with Follicular Dendritic Cell Sarcoma

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Cellular components related to Follicular Dendritic Cell Sarcoma according to GeneCards Suite gene sharing:

idNameGO IDScoreTop Affiliating Genes
1desmosomeGO:00300579.7DSG1, DSP
2cytoplasmic side of plasma membraneGO:00098989.5DSG1, KIT
3extracellular matrixGO:00310129.4CLU, DSG1, DSP
4lateral plasma membraneGO:00163289.3CLDN1, DSG1
5cell-cell junctionGO:00059118.9DSG1, DSP, KIT
6extracellular exosomeGO:00700627.9CLU, CR1, CR2, DSG1, DSP, FCER2
7plasma membraneGO:00058866.8CLDN1, CR1, CR2, DSG1, DSP, FCER2

Biological processes related to Follicular Dendritic Cell Sarcoma according to GeneCards Suite gene sharing:

idNameGO IDScoreTop Affiliating Genes
1complement receptor mediated signaling pathwayGO:000243010.2CR1, CR2
2complement activation, classical pathwayGO:00069589.8CLU, CR1, CR2
3viral entry into host cellGO:00467189.2CLDN1, CR1, CR2
4innate immune responseGO:00450879.0CLU, CR1, CR2

Molecular functions related to Follicular Dendritic Cell Sarcoma according to GeneCards Suite gene sharing:

idNameGO IDScoreTop Affiliating Genes
1virus receptor activityGO:00016189.2CLDN1, CR1, CR2

Sources for Follicular Dendritic Cell Sarcoma

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2CDC
6CNVD
10DGIdb
15ExPASy
16FDA
17FMA
25GTR
26HGMD
27HMDB
28ICD10
29ICD10 via Orphanet
30ICD9CM
31IUPHAR
32KEGG
35MedGen
37MeSH
38MESH via Orphanet
39MGI
42NCI
43NCIt
44NDF-RT
47NINDS
48Novoseek
50OMIM
51OMIM via Orphanet
55PubMed
56QIAGEN
61SNOMED-CT via Orphanet
65Tumor Gene Family of Databases
66UMLS
67UMLS via Orphanet