MCID: FLL013
MIFTS: 43

Follicular Dendritic Cell Sarcoma

Categories: Cancer diseases, Blood diseases, Rare diseases, Immune diseases

Aliases & Classifications for Follicular Dendritic Cell Sarcoma

MalaCards integrated aliases for Follicular Dendritic Cell Sarcoma:

Name: Follicular Dendritic Cell Sarcoma 12 12 55 14
Dendritic Cell Sarcoma, Not Otherwise Specified 12 69
Dendritic Cell Sarcoma, Follicular 41 69
Dendritic Cell Sarcoma 12 14
Dendritic Cell Sarcoma Not Otherwise Specified 55
Dendritic Cell Sarcoma, Interdigitating 69
Follicular Dendritic Cell Tumour 12

Characteristics:

Orphanet epidemiological data:

55
follicular dendritic cell sarcoma
Age of onset: All ages;

Classifications:



External Ids:

Disease Ontology 12 DOID:6262 DOID:7849
ICD10 32 C96.4
MeSH 41 D054740
NCIt 46 C9281 C27260
UMLS via Orphanet 70 C1301364 C1260325
ICD10 via Orphanet 33 C96.4
MESH via Orphanet 42 D054740

Summaries for Follicular Dendritic Cell Sarcoma

Disease Ontology : 12 A dendritic cell sarcoma cancer that effects the follicular dendritic cells.

MalaCards based summary : Follicular Dendritic Cell Sarcoma, also known as dendritic cell sarcoma, not otherwise specified, is related to dendritic cell tumor and interdigitating dendritic cell sarcoma, and has symptoms including night sweats, fever and fatigue. An important gene associated with Follicular Dendritic Cell Sarcoma is CR2 (Complement C3d Receptor 2), and among its related pathways/superpathways are Innate Immune System and Keratinization. Affiliated tissues include tonsil, lymph node and liver.

Wikipedia : 72 Follicular dendritic cell sarcoma (FDCS) is an extremely rare neoplasm. While the existence of FDC... more...

Related Diseases for Follicular Dendritic Cell Sarcoma

Diseases related to Follicular Dendritic Cell Sarcoma via text searches within MalaCards or GeneCards Suite gene sharing:

(show top 50) (show all 63)
# Related Disease Score Top Affiliating Genes
1 dendritic cell tumor 32.4 CR1 CR2 FCER2
2 interdigitating dendritic cell sarcoma 30.3 CR1 CR2
3 paraneoplastic pemphigus 30.1 DSP EVPL PPL
4 pemphigus 30.1 DSP EVPL PPL
5 castleman disease 30.1 CR1 CR2 EVPL
6 reticulum cell sarcoma 29.9 CR1 CR2 FCER2
7 thymoma 29.4 EVPL KIT PPL
8 sarcoma 11.0
9 tonsillitis 10.4
10 parapharyngeal meningioma 10.4 CR1 CR2
11 langerhans cell sarcoma 10.3 CR1 CR2
12 t-cell/histiocyte rich large b cell lymphoma 10.3 CR1 CR2
13 mediastinitis 10.3
14 lateral medullary syndrome 10.2 CR1 CR2
15 histiocytic sarcoma 10.2 CR1 CR2
16 myasthenia gravis 10.2
17 myasthenia gravis congenital 10.2
18 thyroiditis 10.2
19 spindle cell liposarcoma 10.2 CR2 KIT
20 pharyngitis 10.1
21 pemphigus foliaceus 10.0 EVPL PPL
22 follicular lymphoma 10.0 CR1 CR2 FCER2
23 hepatitis 10.0
24 lymphoma 10.0
25 cervicitis 10.0
26 subcorneal pustular dermatosis 10.0 EVPL PPL
27 inflammatory myofibroblastic tumor 10.0 CR1 CR2 KIT
28 plexiform schwannoma 9.9 DSP KIT
29 bronchiolitis obliterans 9.9 EVPL PPL
30 perineurioma 9.9 DSP KIT
31 breast cancer 9.9
32 intussusception 9.9
33 kaposi sarcoma 9.9
34 cryptorchidism, unilateral or bilateral 9.9
35 thymoma, familial 9.9
36 nasopharyngeal carcinoma 9.9
37 leukemia, chronic myeloid 9.9
38 multiple mitochondrial dysfunctions syndrome 5 9.9
39 arthritis 9.9
40 leukemia 9.9
41 nasopharyngitis 9.9
42 squamous cell carcinoma 9.9
43 liposarcoma 9.9
44 cellulitis 9.9
45 mediastinum sarcoma 9.9
46 small intestinal sarcoma 9.9
47 peritonitis 9.9
48 appendicitis 9.9
49 myeloid leukemia 9.9
50 amyloidosis 9.9

Graphical network of the top 20 diseases related to Follicular Dendritic Cell Sarcoma:



Diseases related to Follicular Dendritic Cell Sarcoma

Symptoms & Phenotypes for Follicular Dendritic Cell Sarcoma

UMLS symptoms related to Follicular Dendritic Cell Sarcoma:


night sweats, fever, fatigue

Drugs & Therapeutics for Follicular Dendritic Cell Sarcoma

Search Clinical Trials , NIH Clinical Center for Follicular Dendritic Cell Sarcoma

Cochrane evidence based reviews: dendritic cell sarcoma, follicular

Genetic Tests for Follicular Dendritic Cell Sarcoma

Anatomical Context for Follicular Dendritic Cell Sarcoma

MalaCards organs/tissues related to Follicular Dendritic Cell Sarcoma:

38
Tonsil, Lymph Node, Liver, Spleen, Thyroid, T Cells, Colon

Publications for Follicular Dendritic Cell Sarcoma

Articles related to Follicular Dendritic Cell Sarcoma:

(show top 50) (show all 219)
# Title Authors Year
1
Retroperitoneal follicular dendritic cell sarcoma in a young woman: Diagnosis and treatment challenges. ( 29395417 )
2018
2
Follicular dendritic cell sarcoma of the porta hepatis. ( 29437813 )
2018
3
Follicular dendritic cell sarcoma of the duodenum: an extremely rare entity. ( 29440239 )
2018
4
Image Gallery: Paraneoplastic pemphigus and follicular dendritic cell sarcoma. ( 29441554 )
2018
5
Follicular Dendritic Cell Sarcoma of the Larynx: Apropos a Rare Case with Review of the Literature. ( 28984342 )
2017
6
Inflammatory Pseudotumor-Like Follicular Dendritic Cell Sarcoma of the Spleen: Computed Tomography Imaging Characteristics in 5 Patients. ( 29287022 )
2017
7
Follicular dendritic cell sarcoma of the liver with metachronous small bowel and splenic metastases: a case report and literature review. ( 28653001 )
2017
8
p16 expression in follicular dendritic cell sarcoma: a potential mimicker of human papillomavirus-related oropharyngeal squamous cell carcinoma. ( 28554574 )
2017
9
Follicular dendritic cell sarcoma of the head and neck. Literature review and report of the tonsil occurrence in a Ugandan patient. ( 28748971 )
2017
10
Hemorrhagic intracranial follicular dendritic cell sarcoma: A case report. ( 29119046 )
2017
11
Genomic analysis of follicular dendritic cell sarcoma by molecular inversion probe array reveals tumor suppressor-driven biology. ( 28621320 )
2017
12
"Medusa-Head" cells, "Starfish" cells, and interconnecting long cytoplasmic processes as diagnostic cytologic clues for follicular dendritic cell sarcoma in fine needle aspiration samples. ( 28160447 )
2017
13
Comprehensive Genomic Profiling of a Rare Thyroid Follicular Dendritic Cell Sarcoma. ( 28975018 )
2017
14
Angioimmunoblastic T-Cell Lymphoma: A Questionable Association with Follicular Dendritic Cell Sarcoma. ( 28197348 )
2017
15
Cytomorphological Findings of Follicular Dendritic Cell Sarcoma on Fine-Needle Aspiration Cytology. ( 29275417 )
2017
16
Follicular dendritic cell sarcoma presenting as colonic intussusception. ( 29256544 )
2017
17
Primary follicular dendritic cell sarcoma of the urinary bladder: the first case report and potential diagnostic pitfalls. ( 28438212 )
2017
18
Follicular dendritic cell sarcoma of the small intestine detected by double-balloon enteroscopy. ( 28543909 )
2017
19
Follicular Dendritic Cell Sarcoma. ( 28353378 )
2017
20
Characteristics, management, and outcomes of patients with follicular dendritic cell sarcoma. ( 28382648 )
2017
21
Recurrent Follicular Dendritic Cell Sarcoma of the Parotid Gland Imaged with 18F-FDG PET/CT. ( 29242731 )
2017
22
Small intestine follicular dendritic cell sarcoma with liver metastasis: A case report. ( 28767565 )
2017
23
Mediastinitis After Endobronchial Ultrasound-Guided Transbronchial Needle Aspiration of a Follicular Dendritic Cell Sarcoma. ( 28843365 )
2017
24
Identification of novel follicular dendritic cell sarcoma markers, FDCSP and SRGN, by whole transcriptome sequencing. ( 28145886 )
2017
25
Follicular dendritic cell sarcoma treated with a variety of chemotherapy. ( 27734516 )
2016
26
Completely resected follicular dendritic cell sarcoma of the posterior mediastinum: report of a case. ( 27001632 )
2016
27
Paraneoplastic pemphigus and myasthenia gravis, associated with inflammatory pseudotumor-like follicular dendritic cell sarcoma: response to rituximab. ( 27525088 )
2016
28
(18)F-FDG PET/CT follow-up of follicular dendritic cell sarcoma. ( 27793634 )
2016
29
Computer Tomography Imaging Findings of Abdominal Follicular Dendritic Cell Sarcoma: A Report of 5 Cases. ( 26735543 )
2016
30
Cytological features of inflammatory pseudotumor-like follicular dendritic cell sarcoma of spleen: A case report. ( 27775241 )
2016
31
Treatment of breast cancer 2 (BRCA2)-mutant follicular dendritic cell sarcoma with a poly ADP-ribose polymerase (PARP) inhibitor: a case report. ( 27488020 )
2016
32
A Rare Case of Epstein-Barr Virus Negative Inflammatory Pseudotumor-like Follicular Dendritic Cell Sarcoma Presenting as a Solitary Colonic Mass in a 53-Year-Old Woman; Case Report and Review of Literature. ( 27299190 )
2016
33
Follicular dendritic cell tumour/sarcoma: a commonly misdiagnosed tumour in the thorax Intrathoracic follicular dendritic cell sarcoma. ( 27206572 )
2016
34
Poster 10 Successful Rehabilitation Outcome from Rare Brain Tumor (Intracranial Follicular Dendritic Cell Sarcoma): A Case Report. ( 27672780 )
2016
35
Follicular Dendritic Cell Sarcoma. ( 26910224 )
2016
36
Follicular dendritic cell sarcoma: clinicopathologic study of 15 cases with emphasis on novel expression of MDM2, somatostatin receptor 2A, and PD-L1. ( 27402219 )
2016
37
Clinicopathological Profile and Outcomes of Follicular Dendritic Cell Sarcoma of the Head and Neck Region - A Study of 10 Cases with Literature Review. ( 27656545 )
2016
38
Synchronous presentation of intra-nodal follicular dendritic cell sarcoma and Castleman disease. ( 27862216 )
2016
39
Follicular dendritic cell sarcoma of the spleen: A case report and review of the literature. ( 27602139 )
2016
40
Response to rituximab in an anti-muscle-specific receptor tyrosine kinase- and anti-acetylcholine recepto-double-positive myasthenia gravis patient concomitant with follicular dendritic cell sarcoma. ( 26818174 )
2016
41
Extranodal Follicular Dendritic Cell Sarcoma Originating in the Pancreas: A Case Report. ( 27082603 )
2016
42
Clinicopathological characteristics of mediastinal follicular dendritic cell sarcoma: report of three cases. ( 27068522 )
2016
43
Follicular Dendritic Cell Sarcoma of Appendix Presenting as Acute Appendicitis: An Exceptionally Rare Case Report. ( 27225654 )
2016
44
MDM2 Expression in Extranodal Abdominal and Retroperitoneal Follicular Dendritic Cell Sarcomas, Mimicking Dedifferentiated Liposarcomas. ( 26180935 )
2016
45
Paraneoplastic arthritis as first symptom of a liver inflammatory pseudotumor-like follicular dendritic cell sarcoma. ( 27125361 )
2016
46
High efficacy of tumor-targeting Salmonella typhimurium A1-R on a doxorubicin- and dactolisib-resistant follicular dendritic-cell sarcoma in a patient-derived orthotopic xenograft PDOX nude mouse model. ( 27105519 )
2016
47
Follicular dendritic cell sarcoma with atypical features surrounding undescended testis: description of a rare case. ( 25889780 )
2015
48
Follicular dendritic cell sarcoma with extensive lymph node involvement: A case report. ( 26171038 )
2015
49
Follicular Dendritic Cell Sarcoma of Lymph Node: A report of a Patient with Chronic Myeloid Leukemia Treated with Imatinib. ( 26261702 )
2015
50
Follicular dendritic cell sarcoma of mediastinum: a key role of radiotherapy in a multidisciplinary approach. ( 26638926 )
2015

Variations for Follicular Dendritic Cell Sarcoma

Expression for Follicular Dendritic Cell Sarcoma

Search GEO for disease gene expression data for Follicular Dendritic Cell Sarcoma.

Pathways for Follicular Dendritic Cell Sarcoma

GO Terms for Follicular Dendritic Cell Sarcoma

Cellular components related to Follicular Dendritic Cell Sarcoma according to GeneCards Suite gene sharing:

# Name GO ID Score Top Affiliating Genes
1 cell surface GO:0009986 9.56 CD274 CLU CR1 KIT
2 extracellular exosome GO:0070062 9.56 CD274 CLU CR1 CR2 DSP EVPL
3 external side of plasma membrane GO:0009897 9.5 CD274 FCER2 KIT
4 ficolin-1-rich granule membrane GO:0101003 9.37 CR1 DSP
5 cornified envelope GO:0001533 9.33 DSP EVPL PPL
6 desmosome GO:0030057 8.8 DSP EVPL PPL

Biological processes related to Follicular Dendritic Cell Sarcoma according to GeneCards Suite gene sharing:

# Name GO ID Score Top Affiliating Genes
1 keratinization GO:0031424 9.5 DSP EVPL PPL
2 complement activation, classical pathway GO:0006958 9.43 CLU CR1 CR2
3 peptide cross-linking GO:0018149 9.37 DSP EVPL
4 cornification GO:0070268 9.33 DSP EVPL PPL
5 regulation of complement activation GO:0030449 9.13 CLU CR1 CR2
6 complement receptor mediated signaling pathway GO:0002430 8.62 CR1 CR2

Sources for Follicular Dendritic Cell Sarcoma

3 CDC
7 CNVD
9 Cosmic
10 dbSNP
11 DGIdb
16 ExPASy
18 FMA
27 GO
28 GTR
29 HGMD
30 HMDB
31 HPO
32 ICD10
33 ICD10 via Orphanet
34 ICD9CM
35 IUPHAR
36 KEGG
37 LifeMap
39 MedGen
41 MeSH
42 MESH via Orphanet
43 MGI
45 NCI
46 NCIt
47 NDF-RT
50 NINDS
51 Novoseek
53 OMIM
54 OMIM via Orphanet
58 PubMed
60 QIAGEN
65 SNOMED-CT via HPO
66 SNOMED-CT via Orphanet
67 TGDB
68 Tocris
69 UMLS
70 UMLS via Orphanet
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