MCID: HPT066
MIFTS: 20

Hepatoportal Sclerosis

Categories: Liver diseases, Rare diseases

Aliases & Classifications for Hepatoportal Sclerosis

MalaCards integrated aliases for Hepatoportal Sclerosis:

Name: Hepatoportal Sclerosis 55
Obliterative Portal Venopathy 55

Characteristics:

Orphanet epidemiological data:

55
hepatoportal sclerosis
Age of onset: All ages;

Classifications:

Orphanet: 55  
Rare hepatic diseases


External Ids:

Orphanet 55 ORPHA64743
ICD10 via Orphanet 33 K74.1

Summaries for Hepatoportal Sclerosis

MalaCards based summary : Hepatoportal Sclerosis, also known as obliterative portal venopathy, is related to portal hypertension and hepatitis. An important gene associated with Hepatoportal Sclerosis is ACE (Angiotensin I Converting Enzyme). Affiliated tissues include liver and endothelial.

Related Diseases for Hepatoportal Sclerosis

Diseases related to Hepatoportal Sclerosis via text searches within MalaCards or GeneCards Suite gene sharing:

(show top 50) (show all 67)
# Related Disease Score Top Affiliating Genes
1 portal hypertension 30.2 F2 GPT
2 hepatitis 29.2 F2 GPT
3 infantile liver failure syndrome 1 10.1
4 aortic valve insufficiency 10.1 ACE ELN
5 aortic valve disease 1 10.0 ACE ELN
6 oliver syndrome 10.0
7 adams-oliver syndrome 10.0
8 nodular regenerative hyperplasia 10.0
9 adams-oliver syndrome 1 10.0
10 aortic aneurysm, familial abdominal, 1 10.0 ACE ELN
11 aortic valve disease 2 10.0 ACE ELN
12 kwashiorkor 9.9 F2 GPT
13 hepatic tuberculosis 9.9 F2 GPT
14 ischemic colitis 9.9 ACE F2
15 arteriosclerosis 9.9 ACE ELN
16 hepatic coma 9.9 F2 GPT
17 retinal artery occlusion 9.9 ACE F2
18 hepatitis d 9.9 F2 GPT
19 hemorrhagic fever 9.9 F2 GPT
20 hepatorenal syndrome 9.9 ACE F2
21 nonalcoholic steatohepatitis 9.9 F2 GPT
22 choledocholithiasis 9.9 F2 GPT
23 analbuminemia 9.9 F2 GPT
24 arteritic anterior ischemic optic neuropathy 9.9 ACE F2
25 hepatitis e 9.9 F2 GPT
26 acute liver failure 9.9 F2 GPT
27 ischemic optic neuropathy 9.9 ACE F2
28 connective tissue disease 9.9 ACE ELN
29 bile duct disease 9.9 F2 GPT
30 intermittent claudication 9.9 ACE F2
31 hepatitis a 9.9 F2 GPT
32 nonarteritic anterior ischemic optic neuropathy 9.9 ACE F2
33 heart conduction disease 9.9 ACE F2
34 cholecystitis 9.9 F2 GPT
35 bilirubin metabolic disorder 9.9 F2 GPT
36 obstructive jaundice 9.9 F2 GPT
37 pulmonary edema 9.9 ACE F2
38 myasthenia gravis 9.9
39 crohn's disease 9.9
40 thrombosis 9.9
41 adenoma 9.9
42 myasthenia gravis congenital 9.9
43 endotheliitis 9.9
44 thrombophilia due to thrombin defect 9.9
45 complement hyperactivation, angiopathic thrombosis, and protein-losing enteropathy 9.9
46 hepatic encephalopathy 9.9 F2 GPT
47 alcoholic hepatitis 9.9 F2 GPT
48 wilson disease 9.8 F2 GPT
49 cholangitis 9.8 F2 GPT
50 autoimmune hepatitis 9.8 F2 GPT

Graphical network of the top 20 diseases related to Hepatoportal Sclerosis:



Diseases related to Hepatoportal Sclerosis

Symptoms & Phenotypes for Hepatoportal Sclerosis

Drugs & Therapeutics for Hepatoportal Sclerosis

Search Clinical Trials , NIH Clinical Center for Hepatoportal Sclerosis

Genetic Tests for Hepatoportal Sclerosis

Anatomical Context for Hepatoportal Sclerosis

MalaCards organs/tissues related to Hepatoportal Sclerosis:

38
Liver, Endothelial

Publications for Hepatoportal Sclerosis

Articles related to Hepatoportal Sclerosis:

(show all 31)
# Title Authors Year
1
A Hepatoportal sclerosis related to the use of herbals and nutritional supplements. Causality or coincidence? ( 27740529 )
2016
2
Progression of Hepatic Adenoma to Carcinoma in the Setting of Hepatoportal Sclerosis in HIV Patient: Case Report and Review of the Literature. ( 27812395 )
2016
3
Hepatoportal sclerosis (obliterative portal venopathy) and nodular regenerative hyperplasia in a patient with myasthenia gravis: A case report and review of the published work. ( 23675894 )
2013
4
Mercaptopurine-induced hepatoportal sclerosis in a patient with Crohn's disease. ( 22841133 )
2013
5
Hepatoportal sclerosis in childhood: descriptive analysis of 12 patients. ( 24133357 )
2013
6
Liver failure and the need for transplantation in 6 patients with hepatoportal sclerosis. ( 23769069 )
2013
7
Induction of elastin expression in vascular endothelial cells relates to hepatoportal sclerosis in idiopathic portal hypertension: possible link to serum anti-endothelial cell antibodies. ( 22288597 )
2012
8
Hepatoportal sclerosis in childhood: some presenting with cholestatic features (a re-evaluation of 12 children). ( 22150463 )
2012
9
The involvement of nitric oxide in the physiopathology of hepatoportal sclerosis. ( 22820432 )
2012
10
Oxaliplatin-induced hepatoportal sclerosis, portal hypertension, and variceal bleeding successfully treated with transjugular intrahepatic portosystemic shunt. ( 22537609 )
2012
11
Hepatoportal sclerosis clinical different evolutionary stages: presentation of 3 cases and literature review. ( 22372805 )
2012
12
Hepatoportal sclerosis: CT and MRI appearance with histopathologic correlation. ( 22268180 )
2012
13
The development of hepatoportal sclerosis and portal hypertension due to didanosine use in HIV. ( 21057809 )
2011
14
Elevated levels of circulating angiotensin converting enzyme in patients with hepatoportal sclerosis. ( 21290180 )
2011
15
Hepatoportal sclerosis and extrahepatic portal venous obstruction associated with anti-phospholipid antibody syndrome in child. ( 20675717 )
2011
16
Variceal bleeding in an adolescent with HIV diagnosed with hepatoportal sclerosis and nodular regenerative hyperplasia. ( 19841596 )
2010
17
Liver failure and the need for transplantation in three patients with hepatoportal sclerosis. ( 19100429 )
2008
18
Hepatoportal sclerosis: a cause of portal hypertension to bear in mind. ( 18279649 )
2008
19
Response to Schiano et al. Hepatoportal sclerosis as a cause of noncirrhotic portal hypertension in patients with HIV. ( 18341510 )
2008
20
Hepatoportal sclerosis as a cause of noncirrhotic portal hypertension in patients with HIV. ( 17640321 )
2007
21
Clinical features, serum interleukin-6, and interferon-gamma levels of 34 turkish patients with hepatoportal sclerosis. ( 17404864 )
2007
22
Liver failure and need for liver transplantation in patients with advanced hepatoportal sclerosis. ( 17414109 )
2007
23
Association of Adams-Oliver syndrome and hepatoportal sclerosis: an additional case. ( 16532468 )
2006
24
Adams-Oliver syndrome and hepatoportal sclerosis: occasional association or common mechanism? ( 15832360 )
2005
25
Hepatoportal sclerosis in a child. ( 15316776 )
2004
26
Hepatoportal sclerosis. ( 8578318 )
1995
27
Hepatoportal sclerosis demonstrated by abdominal ultrasonography. ( 1658085 )
1991
28
Hepatoportal sclerosis in childhood. ( 2421592 )
1986
29
Hepatoportal sclerosis in childhood: a mimic of extrahepatic portal vein obstruction. ( 7252729 )
1981
30
Hepatoportal sclerosis--its relationship to intrahepatic portal venous thrombosis. ( 429020 )
1979
31
Extra- and intrahepatic portal hypertension without cirrhosis (hepatoportal sclerosis). ( 5833586 )
1965

Variations for Hepatoportal Sclerosis

Expression for Hepatoportal Sclerosis

Search GEO for disease gene expression data for Hepatoportal Sclerosis.

Pathways for Hepatoportal Sclerosis

GO Terms for Hepatoportal Sclerosis

Sources for Hepatoportal Sclerosis

3 CDC
7 CNVD
9 Cosmic
10 dbSNP
11 DGIdb
16 ExPASy
18 FMA
27 GO
28 GTR
29 HGMD
30 HMDB
31 HPO
32 ICD10
33 ICD10 via Orphanet
34 ICD9CM
35 IUPHAR
36 KEGG
37 LifeMap
39 MedGen
41 MeSH
42 MESH via Orphanet
43 MGI
45 NCI
46 NCIt
47 NDF-RT
50 NINDS
51 Novoseek
53 OMIM
54 OMIM via Orphanet
58 PubMed
60 QIAGEN
65 SNOMED-CT via HPO
66 SNOMED-CT via Orphanet
67 TGDB
68 Tocris
69 UMLS
70 UMLS via Orphanet
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