MCID: IMM053
MIFTS: 23

Immunotactoid Glomerulopathy

Categories: Rare diseases, Immune diseases, Nephrological diseases

Aliases & Classifications for Immunotactoid Glomerulopathy

MalaCards integrated aliases for Immunotactoid Glomerulopathy:

Name: Immunotactoid Glomerulopathy 49 55
Immunotactoid Glomerulonephritis 49 55
Fibrillary Glomerulonephritis 69

Characteristics:

Orphanet epidemiological data:

55
immunotactoid glomerulopathy
Inheritance: Not applicable; Age of onset: Adult;

Classifications:

Orphanet: 55  
Rare renal diseases


External Ids:

Orphanet 55 ORPHA97567
UMLS via Orphanet 70 C0268749 C2242534
ICD10 via Orphanet 33 N03.6
UMLS 69 C0268749

Summaries for Immunotactoid Glomerulopathy

NIH Rare Diseases : 49 Immunotactoid glomerulopathy, also known as glomerulonephritis with organized monoclonal microtubular immunoglobulin deposits (GOMMID),  is a very uncommon cause of glomerular disease. It is related to a similar disease known as fibrillary glomerulopathy, which is more common. Both disorders probably result from deposits derived from immunoglobulins, but in most cases the cause is idiopathic (unknown). On electron microscopy, immunotactoid glomerulopathy is characterized by the formation of microtubules which are much larger than the fibrils observed in fibrillary glomerulonephritis (30 to 50 versus 16 to 24 nm in diameter). The signs and symptoms include blood (hematuria) and protein (proteinuria) in the urine, kidney insufficiency and high blood pressure. Both fibrillary glomerulonephritis and immunotactoid glomerulopathy have been associated with hepatitis C virus infection and with malignancy and autoimmune disease. Also, patients with immunotactoid glomerulopathy have a greater risk to have chronic lymphocytic leukemia and B cell lymphomas and should be screened for all of these conditions. Treatment is generally determined by the severity of the kidney problems. Last updated: 8/18/2015

MalaCards based summary : Immunotactoid Glomerulopathy, also known as immunotactoid glomerulonephritis, is related to immunotactoid or fibrillary glomerulopathy and fibrillary glomerulonephritis. An important gene associated with Immunotactoid Glomerulopathy is ALB (Albumin). Affiliated tissues include kidney, b cells and bone.

Related Diseases for Immunotactoid Glomerulopathy

Graphical network of the top 20 diseases related to Immunotactoid Glomerulopathy:



Diseases related to Immunotactoid Glomerulopathy

Symptoms & Phenotypes for Immunotactoid Glomerulopathy

Drugs & Therapeutics for Immunotactoid Glomerulopathy

Search Clinical Trials , NIH Clinical Center for Immunotactoid Glomerulopathy

Genetic Tests for Immunotactoid Glomerulopathy

Anatomical Context for Immunotactoid Glomerulopathy

MalaCards organs/tissues related to Immunotactoid Glomerulopathy:

38
Kidney, B Cells, Bone, Skin, Liver, Bone Marrow

Publications for Immunotactoid Glomerulopathy

Articles related to Immunotactoid Glomerulopathy:

(show top 50) (show all 56)
# Title Authors Year
1
Immunotactoid glomerulopathy leading to the discovery of POEMS syndromea8c. ( 28291506 )
2017
2
Immunotactoid glomerulopathy in a patient with hepatitis C viral infection. ( 28230481 )
2017
3
Immunotactoid Glomerulopathy of 10-Years' Duration: Insights Gained From Sequential Biopsies. ( 29270507 )
2017
4
A case report of unusually long lag time between immunotactoid glomerulopathy (itg) diagnosis and diffuse large B-cell lymphoma (DLBCL) development. ( 27686684 )
2016
5
Immunotactoid glomerulopathy with IGM positivity and associated IGM paraprotein. ( 27772927 )
2016
6
End-Stage Kidney Disease Due to Fibrillary Glomerulonephritis and Immunotactoid Glomerulopathy - Outcomes in 66 Consecutive ANZDATA Registry Cases. ( 26418732 )
2015
7
Immunotactoid Glomerulopathy and Cryoglobulinemic Nephropathy: Two Entities with Many Similarities. A Unified Conceptual Approach. ( 26270724 )
2015
8
AJKD Atlas of Renal Pathology: Immunotactoid Glomerulopathy. ( 26408243 )
2015
9
Laser microdissection and proteomic analysis of amyloidosis, cryoglobulinemic GN, fibrillary GN, and immunotactoid glomerulopathy. ( 23411427 )
2013
10
Immunotactoid glomerulopathy: clinicopathologic and proteomic study. ( 22872726 )
2012
11
Chronic lymphocytic leukemia associated with immunotactoid glomerulopathy: a case report of successful treatment with high-dose methylprednisolone in combination with rituximab followed by alemtuzumab. ( 22335532 )
2012
12
Spontaneous remission of immunotactoid glomerulopathy. ( 21934180 )
2011
13
Immunotactoid glomerulopathy and tuberculosis: a novel association. ( 21629347 )
2011
14
A case of recurrent immunotactoid glomerulopathy in an allograft treated with rituximab. ( 19917422 )
2009
15
A case of immunotactoid glomerulopathy with rapid progression to end-stage renal disease. ( 20024509 )
2009
16
A case of immunotactoid glomerulopathy exhibiting nephrotic syndrome successfully treated with corticosteroids and antihypertensive therapy. ( 19367362 )
2009
17
Fibrillary glomerulonephritis and immunotactoid glomerulopathy. ( 18045849 )
2008
18
Plasma cell dyscrasia; LCDD vs Immunotactoid glomerulopathy. ( 18711301 )
2008
19
Long-term remission of paraprotein-induced immunotactoid glomerulopathy after high-dose therapy and autologous blood stem cell transplantation. ( 17605010 )
2007
20
Immunotactoid glomerulopathy with microtubular deposits, with reference to the characteristics of Japanese cases. ( 15909596 )
2005
21
Fibrillary glomerulonephritis and immunotactoid glomerulopathy. ( 15299095 )
2004
22
A 59-year-old woman with immunotactoid glomerulopathy, heavy-chain disease, and non-hodgkin lymphoma. ( 15163227 )
2004
23
Immunotactoid glomerulopathy in an HIV-positive African-American man. ( 14655225 )
2003
24
Immunotactoid glomerulopathy. ( 11961029 )
2002
25
Images in cardiovascular medicine. Fibrillary/immunotactoid glomerulopathy with cardiac involvement. ( 11956134 )
2002
26
Immunotactoid glomerulopathy with massive bone marrow deposits in a patient with IgM kappa monoclonal gammopathy and hypocomplementemia. ( 11479168 )
2001
27
Immunotactoid glomerulopathy in sickle cell anemia. ( 11198611 )
2001
28
Immunotactoid glomerulopathy characterized by steroid-responsive massive subendothelial deposition. ( 11228198 )
2001
29
One case of immunotactoid glomerulopathy: morphological-ultrastructural aspects. ( 11846092 )
2001
30
Successful treatment of recurrence of immunotactoid glomerulopathy in a kidney allograft recipient. ( 10831649 )
2000
31
Immunotactoid glomerulopathy--an unusual deposition disease: report of the first Malaysian case. ( 10879280 )
1999
32
Fibrillary-immunotactoid glomerulopathy with renal deposits of IgAlambda: a rare cause of glomerulonephritis. ( 10604647 )
1999
33
Successful treatment with steroid pulse therapy in a case of immunotactoid glomerulopathy with hypocomplementemia. ( 10074587 )
1998
34
Immunotactoid glomerulopathy associated with idiopathic hypereosinophilic syndrome. ( 9653841 )
1998
35
Hepatitis C viral infection is associated with fibrillary glomerulonephritis and immunotactoid glomerulopathy. ( 9848778 )
1998
36
A case of immunotactoid glomerulopathy with unusual microtubular deposits. ( 9617498 )
1998
37
Immunotactoid glomerulopathy: report of a case. ( 9214417 )
1997
38
Immunotactoid glomerulopathy with extrarenal deposits in the bone, and chronic cholestatic liver disease. ( 8856222 )
1996
39
Clinical features, predictors of disease progression and results of renal transplantation in fibrillary/immunotactoid glomerulopathy. ( 8671905 )
1996
40
Immunotactoid glomerulopathy with unusually thick extracellular microtubules and nodular glomerulosclerosis in a diabetic patient. ( 7479381 )
1995
41
De novo immunotactoid glomerulopathy of the renal allograft: possible association with cytomegalovirus infection. ( 8023832 )
1994
42
Immunotactoid glomerulopathy: the case for Occam's razor. ( 8372842 )
1993
43
Immunotactoid glomerulopathy in a child with Down syndrome. ( 8439490 )
1993
44
Morphologic and clinical features of fibrillary glomerulonephritis versus immunotactoid glomerulopathy. ( 8372831 )
1993
45
Fibrillary glomerulonephritis and immunotactoid glomerulopathy: two entities, not one. ( 8372843 )
1993
46
Immunotactoid glomerulopathy (ITGP): a not fully defined clinicopathologic entity. ( 8516498 )
1993
47
Immunotactoid glomerulopathy. ( 1496977 )
1992
48
Fibrillary (immunotactoid) glomerulopathy. A possible role for kappa light chain in its etiology and/or pathogenesis. ( 1905497 )
1991
49
Nonamyloidotic fibrillary glomerulopathy, immunotactoid glomerulopathy, and the differential diagnosis of filamentous glomerulopathies. ( 2020659 )
1991
50
Immunotactoid glomerulopathy and cutaneous vasculitis. ( 1904680 )
1991

Variations for Immunotactoid Glomerulopathy

Expression for Immunotactoid Glomerulopathy

Search GEO for disease gene expression data for Immunotactoid Glomerulopathy.

Pathways for Immunotactoid Glomerulopathy

GO Terms for Immunotactoid Glomerulopathy

Sources for Immunotactoid Glomerulopathy

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