MCID: INF057
MIFTS: 25

Inflammatory Linear Verrucous Epidermal Nevus

Categories: Rare diseases, Skin diseases

Aliases & Classifications for Inflammatory Linear Verrucous Epidermal Nevus

MalaCards integrated aliases for Inflammatory Linear Verrucous Epidermal Nevus:

Name: Inflammatory Linear Verrucous Epidermal Nevus 49 55 69
Verrucous Epidermal Nevus 49 69
Verrucous Nevus 49 55
Ilven 49 55
Inflammatory Linear Verrucous Epidermal Naevus 49
Linear Verrucose Epidermal Nevus 49
Linear Verrucous Epidermal Nevus 69

Classifications:

Orphanet: 55  
Rare skin diseases


External Ids:

UMLS via Orphanet 70 C0362030 C0473574
ICD10 via Orphanet 33 Q82.5

Summaries for Inflammatory Linear Verrucous Epidermal Nevus

NIH Rare Diseases : 49 Inflammatory linear verrucous epidermal nevus (ILVEN) is a type of skin overgrowth, called epidermal nevus. It is characterized by skin colored, brown, or reddish, wart-like papules (nevi). The nevi join to form patches or plaques that often follow a pattern on the skin known as the "lines of Blaschko". The affected areas of the skin may be red, itchy, and inflamed. ILVEN typically presents from birth to early childhood and often is limited to one side of the lower half of the body. It affects females more often than males. It usually occurs alone; however, rarely ILVEN can be associated with other symptoms as part of an epidermal nevus syndrome. Rarely, ILVEN can become cancerous (for example, basal cell carcinoma or squamous cell carcinoma). ILVEN is caused by a genetic alteration that occurs after conception (somatic mutation). How this alteration leads to the signs and symptoms of ILVEN is not well understood. There is no one treatment or cure for ILVEN. Products used to soften the skin (emollients), moisturizers, and topical steroids may be utilized to relieve symptoms of dryness and itching. Recently, several patients had being treated with laser with good results. Last updated: 3/20/2017

MalaCards based summary : Inflammatory Linear Verrucous Epidermal Nevus, also known as verrucous epidermal nevus, is related to verrucous nevus acanthokeratolytic and linear verrucous nevus syndrome. An important gene associated with Inflammatory Linear Verrucous Epidermal Nevus is CD8A (CD8a Molecule). Affiliated tissues include skin and testes.

Wikipedia : 72 Inflammatory Linear Verrucous Epidermal Nevus (ILVEN) is a rare disease of the skin that presents as... more...

Related Diseases for Inflammatory Linear Verrucous Epidermal Nevus

Diseases related to Inflammatory Linear Verrucous Epidermal Nevus via text searches within MalaCards or GeneCards Suite gene sharing:

(show all 24)
# Related Disease Score Top Affiliating Genes
1 verrucous nevus acanthokeratolytic 12.1
2 linear verrucous nevus syndrome 12.1
3 palmoplantar keratoderma, epidermolytic 11.7
4 pustulosis of palm and sole 10.5
5 psoriasis 10.5
6 nevus, epidermal 10.4
7 psoriasis 11 10.1
8 psoriasis 13 10.1
9 nevoid hypermelanosis, linear and whorled 10.1
10 arthritis 10.1
11 vertebral artery occlusion 10.1
12 ichthyosis 10.1
13 squamous cell carcinoma 10.1
14 epidermolytic hyperkeratosis 10.1
15 epilepsy 10.1
16 erythrokeratodermia variabilis et progressiva 1 10.1
17 ichthyosis vulgaris 10.1
18 lichen planus 10.1
19 mycosis fungoides 10.1
20 psoriasis 2 10.1
21 regional odontodysplasia 10.1
22 psoriasis 7 10.1
23 myofibroma 9.8
24 neurofibromatosis, type iv, of riccardi 9.8

Graphical network of the top 20 diseases related to Inflammatory Linear Verrucous Epidermal Nevus:



Diseases related to Inflammatory Linear Verrucous Epidermal Nevus

Symptoms & Phenotypes for Inflammatory Linear Verrucous Epidermal Nevus

Drugs & Therapeutics for Inflammatory Linear Verrucous Epidermal Nevus

Search Clinical Trials , NIH Clinical Center for Inflammatory Linear Verrucous Epidermal Nevus

Genetic Tests for Inflammatory Linear Verrucous Epidermal Nevus

Anatomical Context for Inflammatory Linear Verrucous Epidermal Nevus

MalaCards organs/tissues related to Inflammatory Linear Verrucous Epidermal Nevus:

38
Skin, Testes

Publications for Inflammatory Linear Verrucous Epidermal Nevus

Articles related to Inflammatory Linear Verrucous Epidermal Nevus:

(show top 50) (show all 68)
# Title Authors Year
1
Inflammatory linear verrucous epidermal nevus: an unusual manifestation. ( 26426377 )
2017
2
Dermoscopy of linear dermatosis along Blaschko's line in childhood: Lichen striatus versus inflammatory linear verrucous epidermal nevus. ( 28925078 )
2017
3
Is Ki-67, keratin 16, involucrin, and filaggrin immunostaining sufficient to diagnose inflammatory linear verrucous epidermal nevus? A report of eight cases and a comparison with psoriasis vulgaris. ( 29166506 )
2017
4
Inflammatory linear verrucous epidermal nevus with a postzygotic GJA1 mutation is a mosaic erythrokeratodermia variabilis et progressiva. ( 27890787 )
2016
5
A Case of Inflammatory Linear Verrucous Epidermal Nevus on the Upper Eyelid. ( 26120188 )
2015
6
Genital/Perigenital Inflammatory Linear Verrucous Epidermal Nevus: A Case Series. ( 26677274 )
2015
7
Inflammatory linear verrucous epidermal nevus and regional odontodysplasia: A rare sorority. ( 26752881 )
2015
8
The challenge to diagnose a clinical case of inflammatory linear verrucous epidermal nevus: is there any ILVEN associated with human papillomavirus infection? ( 25467274 )
2014
9
Inflammatory linear verrucous epidermal nevus with psoriasiform histology. ( 24700964 )
2014
10
A novel technique used in the treatment of inflammatory linear verrucous epidermal nevus: tangential excision. ( 25192746 )
2014
11
A diagnostic dilemma: inflammatory linear verrucous epidermal nevus versus linear psoriasis. ( 23149170 )
2013
12
Treatment of inflammatory linear verrucous epidermal nevus with 2940A nm erbium fractional laser. ( 24112692 )
2013
13
Inflammatory linear verrucous epidermal nevus. ( 24640220 )
2013
14
Inflammatory linear verrucous epidermal nevus: why a combined laser therapy. ( 23692514 )
2013
15
Involucrin in the differential diagnosis between linear psoriasis and inflammatory linear verrucous epidermal nevus: a report of one case. ( 24068133 )
2013
16
Inflammatory linear verrucous epidermal nevus in perineum and vulva: a report of two rare cases. ( 23716825 )
2013
17
Vulvar and perianal condyloma superimposed inflammatory linear verrucous epidermal nevus: a case report and review of the literature. ( 24396613 )
2013
18
Giant inflammatory linear verrucous epidermal nevus: successfully treated with full thickness excision and skin grafting. ( 24249899 )
2013
19
Inflammatory linear verrucous epidermal nevus and epilepsy: remission during valproic acid therapy. ( 23377323 )
2013
20
Is it inflammatory linear verrucous epidermal nevus or linear psoriasis? ( 23652072 )
2013
21
Dermacase. Can you identify this condition? Inflammatory linear verrucous epidermal nevus. ( 22423022 )
2012
22
Carbon dioxide laser: first-line therapy in vulvar inflammatory linear verrucous epidermal nevus. ( 22591503 )
2012
23
Inflammatory linear verrucous epidermal nevus of the digits treated with surgical excision and skin grafting. ( 22882733 )
2012
24
Feline epidermal nevi resembling human inflammatory linear verrucous epidermal nevus. ( 22672841 )
2012
25
Inflammatory linear verrucous epidermal nevus with genital involvement. ( 22545330 )
2012
26
Inflammatory linear verrucous epidermal nevus syndrome with its polymorphic presentation - A rare case report. ( 22557913 )
2012
27
Development of squamous cell carcinoma on an inflammatory linear verrucous epidermal nevus in the genital area. ( 22838090 )
2012
28
Epidermolytic hyperkeratosis in inflammatory linear verrucous epidermal nevus. ( 21772595 )
2011
29
Extensive, adulthood inflammatory linear verrucous epidermal nevus associated with mucinous nevus. ( 21860165 )
2011
30
Inflammatory linear verrucous epidermal nevus successfully treated with methyl-aminolevulinate photodynamic therapy. ( 20402956 )
2010
31
Successful treatment with trichloroacetic acid peeling for inflammatory linear verrucous epidermal nevus. ( 20507413 )
2010
32
Case for diagnosis. Inflammatory linear verrucous epidermal nevus. ( 21152805 )
2010
33
Linear and whorled nevoid hypermelanosis complicated with inflammatory linear verrucous epidermal nevus and ichthyosis vulgaris. ( 17973817 )
2007
34
Does inflammatory linear verrucous epidermal nevus represent a segmental type 1/type 2 mosaic of psoriasis? ( 16484814 )
2006
35
Inflammatory linear verrucous epidermal nevus: a case report and short review of the literature. ( 17121063 )
2006
36
Successful treatment of inflammatory linear verrucous epidermal nevus with tacrolimus and fluocinonide. ( 17241573 )
2006
37
Immunohistochemical differentiation between inflammatory linear verrucous epidermal nevus (ILVEN) and psoriasis. ( 15319153 )
2004
38
Carbon dioxide laser therapy for an inflammatory linear verrucous epidermal nevus: a case report. ( 15583849 )
2004
39
Mycosis fungoides mimicking inflammatory linear verrucous epidermal nevus. ( 15009311 )
2004
40
Inflammatory linear verrucous epidermal nevus. ( 14594588 )
2003
41
Inflammatory linear verrucous epidermal nevus and arthritis: a new association. ( 11295732 )
2001
42
Inflammatory linear verrucous epidermal nevus. ( 11766117 )
2001
43
Full-thickness surgical excision for the treatment of inflammatory linear verrucous epidermal nevus. ( 11562033 )
2001
44
Inflammatory linear verrucous epidermal nevus (ILVEN) and psoriasis in a child? ( 10651962 )
2000
45
Inflammatory linear verrucous epidermal nevus and spinal anomaly. ( 20921697 )
1999
46
Inflammatory linear verrucous epidermal nevus syndrome with bilateral vertebral artery occlusion. ( 10742739 )
1999
47
Adult onset of inflammatory linear verrucous epidermal nevus. ( 10535255 )
1999
48
Perivulvar inflammatory linear verrucous epidermal nevus (ILVEN) treated with CO2 laser. ( 11360427 )
1999
49
Topical calcipotriol for treatment of inflammatory linear verrucous epidermal nevus. ( 9158408 )
1997
50
Bilateral inflammatory linear verrucous epidermal nevus associated with psoriasis. ( 8727782 )
1996

Variations for Inflammatory Linear Verrucous Epidermal Nevus

Expression for Inflammatory Linear Verrucous Epidermal Nevus

Search GEO for disease gene expression data for Inflammatory Linear Verrucous Epidermal Nevus.

Pathways for Inflammatory Linear Verrucous Epidermal Nevus

GO Terms for Inflammatory Linear Verrucous Epidermal Nevus

Sources for Inflammatory Linear Verrucous Epidermal Nevus

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