MCID: INT221
MIFTS: 35

Intravascular Large B-Cell Lymphoma malady

Blood diseases, Cancer diseases, Rare diseases, Immune diseases categories

Aliases & Classifications for Intravascular Large B-Cell Lymphoma

About this section
Sources:
51Orphanet, 65UMLS, 28ICD10 via Orphanet
See all sources

Aliases & Descriptions for Intravascular Large B-Cell Lymphoma:

Name: Intravascular Large B-Cell Lymphoma 51
Angioendotheliomatosis Proliferans Systemisata 51
Malignant Angioendotheliomatosis 51
Angiotropic Large Cell Lymphoma 51
 
Intravascular Lymphomatosis 51
Tappeiner-Pfleger Disease 51
Angioendotheliomatosis 65


Classifications:



External Ids:

Orphanet51 98839
ICD10 via Orphanet28 C83.3

Summaries for Intravascular Large B-Cell Lymphoma

About this section
MalaCards based summary: Intravascular Large B-Cell Lymphoma, also known as angioendotheliomatosis proliferans systemisata, is related to plasmacytoma and b-cell lymphomas. An important gene associated with Intravascular Large B-Cell Lymphoma is BCL6 (B-Cell CLL/Lymphoma 6), and among its related pathways are IL2-mediated signaling events and IL2 signaling events mediated by PI3K. Affiliated tissues include b cells, bone and skin, and related mouse phenotypes are reproductive system and liver/biliary system.

Related Diseases for Intravascular Large B-Cell Lymphoma

About this section

Graphical network of the top 20 diseases related to Intravascular Large B-Cell Lymphoma:



Diseases related to intravascular large b-cell lymphoma

Symptoms for Intravascular Large B-Cell Lymphoma

About this section

Drugs & Therapeutics for Intravascular Large B-Cell Lymphoma

About this section

Interventional clinical trials:

Search ClinicalTrials, NIH Clinical Center for Intravascular Large B-Cell Lymphoma

Genetic Tests for Intravascular Large B-Cell Lymphoma

About this section

Anatomical Context for Intravascular Large B-Cell Lymphoma

About this section

MalaCards organs/tissues related to Intravascular Large B-Cell Lymphoma:

33
B cells, Bone, Skin, Lung, Bone marrow, Prostate, Uterus

Animal Models for Intravascular Large B-Cell Lymphoma or affiliated genes

About this section

MGI Mouse Phenotypes related to Intravascular Large B-Cell Lymphoma:

38
idDescriptionMGI Source AccessionScoreTop Affiliating Genes
1MP:00053898.1B2M, BCL2, BCL6, IL2RB, KMT2A
2MP:00053707.9B2M, BCL6, IL2RB, KMT2A, MME
3MP:00107717.6B2M, BCL2, IL2RB, KMT2A, MME
4MP:00053977.3B2M, BCL2, BCL6, CD5, IL2RB, KMT2A
5MP:00053876.6B2M, BCL2, BCL6, CD5, IL2RB, KMT2A

Publications for Intravascular Large B-Cell Lymphoma

About this section

Articles related to Intravascular Large B-Cell Lymphoma:

(show top 50)    (show all 202)
idTitleAuthorsYear
1
Characteristics of Intravascular Large B-Cell Lymphoma Limited to the Glomerular Capillaries: A Case Report. (26351627)
2015
2
Intravascular large B-cell lymphoma secondary to lymphoplasmacytic lymphoma: a case report and review of literature with clonality analysis. (26045864)
2015
3
Antemortem diagnosis with multiple random skin biopsies and transbronchial lung biopsy in a patient with intravascular large B-cell lymphoma, the so-called Asian variant lymphoma. (24632902)
2014
4
Synchronous invasive ductal carcinoma and intravascular large B-cell lymphoma of the breast: a case report and review of the literature. (24708809)
2014
5
Tandem triplication of the BCL2 gene in CD5-positive intravascular large B cell lymphoma with bone marrow involvement. (24577512)
2014
6
Simultaneous thrombosis of the mesenteric artery and vein as a novel clinical manifestation of intravascular large B-cell lymphoma. (24525901)
2014
7
Benefits of skin biopsy of senile hemangioma in intravascular large B-cell lymphoma: A case report and review of the literature. (24932279)
2014
8
Intravascular large B-cell lymphoma presenting as cauda equina syndrome and showing aberrant cytokeratin expression: a diagnostic challenge. (24614706)
2014
9
Intravascular large B-cell lymphoma confirmed by brain biopsy: a case report. (23420723)
2013
10
Intravascular large B-cell lymphoma presenting with anasarca-type edema and acute renal failure. (23885711)
2013
11
Liver dysfunction and thrombocytopenia diagnosed as intravascular large B-cell lymphoma using a timely and accurate transjugular liver biopsy. (23994980)
2013
12
Intravascular large B-cell lymphoma presenting as acute hemorrhagic cerebral infarct with delirium. (23884226)
2013
13
Mild proteinuria in a patient with glomerularlimited intravascular large B-cell lymphoma. (22541680)
2013
14
Generalized telangiectasia revealing intravascular large B-cell lymphoma. (23406023)
2013
15
Intravascular large B cell lymphoma presenting as cholecystitis: diagnostic challenges persist. (24288109)
2013
16
Intravascular large B-cell lymphoma with hemophagocytic syndrome (Asian variant) in a Caucasian patient. (22808298)
2012
17
Indication for random skin biopsy for the diagnosis of intravascular large B cell lymphoma. (22414723)
2012
18
A fatal case of hemoperitoneum after ultrasound-guided liver biopsy in a patient with intravascular large B-cell lymphoma. (21377915)
2011
19
An autopsy case of lymphomatosis cerebri showing pathological changes of intravascular large B-cell lymphoma in visceral organs. (21382094)
2011
20
Progressive multifocal cerebral infarction from intravascular large B cell lymphoma presenting in a man: a case report. (21251318)
2011
21
Haemophagocytosis-related intravascular large B-cell lymphoma associated with skin eruption. (21279301)
2011
22
Intravascular large B-cell lymphoma of the uterus: a case with favorable clinical outcome. (19948641)
2011
23
18F-FDG PET/CT in a case of intravascular large B-cell lymphoma. (20607536)
2010
24
Intravascular large B-cell lymphoma, an exclusively small vessel disease? A case report and review of literature. (20542564)
2010
25
Central nervous system involvement in intravascular large B-cell lymphoma: a retrospective analysis of 109 patients. (20412122)
2010
26
Neurolymphomatosis involving the trigeminal nerve and deep peroneal nerve in a patient with relapsed intravascular large B-cell lymphoma. (20528901)
2010
27
Fluorodeoxyglucose-PET/CT for diagnosis of intravascular large B-cell lymphoma. (20675506)
2010
28
Intravascular large B cell lymphoma: an elusive cause of pyrexia of unknown origin diagnosed postmortem. (20868278)
2010
29
Intravascular large B-cell lymphoma within a subcutaneous cavernous haemangioma. (20735401)
2010
30
Intravascular large B-cell lymphoma of the skin: typical clinical manifestations and a favourable response to rituximab-containing therapy. (19590171)
2009
31
Intravascular large B cell lymphoma: proposed of the strategy for early diagnosis and treatment of patients with rapid deteriorating condition. (19363707)
2009
32
Gallium scan-prompted skin biopsy revealed intravascular large B-cell lymphoma in a patient who presented with fever of unknown origin. (19387217)
2009
33
Intravascular large B cell lymphoma: when lymphoma is suspected but routine diagnostic work-up is negative. (19883320)
2009
34
Intravascular large B-cell lymphoma: remission after rituximab-cyclophosphamide, doxorubicin, vincristine, and prednisolone chemotherapy. (19632742)
2009
35
Intravascular large B-cell lymphoma presenting in subcutaneous fat tissue and simulating panniculitis clinically. (20415677)
2009
36
Analysis of CXCL9 and CXCR3 expression in a case of intravascular large B-cell lymphoma. (19766346)
2009
37
The addition of rituximab to anthracycline-based chemotherapy significantly improves outcome in 'Western' patients with intravascular large B-cell lymphoma. (18699850)
2008
38
Sustained remission after rituximab-containing chemotherapy for intravascular large B-cell lymphoma. (18434690)
2008
39
Definition, diagnosis, and management of intravascular large B-cell lymphoma: proposals and perspectives from an international consensus meeting. (17577023)
2007
40
Intravascular large B-cell lymphoma presenting as cerebellar and cerebral infarction. (17502477)
2007
41
Asian variant of intravascular large B-cell lymphoma diagnosed by bone marrow biopsy]. (17313078)
2007
42
Intravascular large B-cell lymphoma with multisystem involvement. (16966288)
2006
43
Intravascular large B-cell lymphoma associated with a near-tetraploid karyotype, rearrangement of BCL6, and a t(11;14)(q13;q32). (17116487)
2006
44
Primary bilateral adrenal intravascular large B-cell lymphoma associated with adrenal failure. (12879956)
2003
45
A case of intravascular large B-cell lymphoma with multiple organ involvement. (14739519)
2003
46
Intravascular large B-cell lymphoma presenting as cutaneous panniculitis. (14677722)
2003
47
Intravascular large B-cell lymphoma with a fulminant clinical course: a case report with definite diagnosis post mortem. (12196378)
2002
48
Myeloperoxidase-positive intravascular large B-cell lymphoma. (11419984)
2001
49
Unusual sites of involvement by hematologic malignancies. Case 1. Intravascular large B-cell lymphoma presenting with CNS symptoms. (11579120)
2001
50
Primary cutaneous large B-cell lymphoma of the leg relapsing as cutaneous intravascular large B-cell lymphoma. (11735727)
2001

Variations for Intravascular Large B-Cell Lymphoma

About this section

Expression for genes affiliated with Intravascular Large B-Cell Lymphoma

About this section
Search GEO for disease gene expression data for Intravascular Large B-Cell Lymphoma.

Pathways for genes affiliated with Intravascular Large B-Cell Lymphoma

About this section

GO Terms for genes affiliated with Intravascular Large B-Cell Lymphoma

About this section

Cellular components related to Intravascular Large B-Cell Lymphoma according to GeneCards Suite gene sharing:

idNameGO IDScoreTop Affiliating Genes
1external side of plasma membraneGO:00098979.0B2M, CD5, IL2RB

Biological processes related to Intravascular Large B-Cell Lymphoma according to GeneCards Suite gene sharing:

idNameGO IDScoreTop Affiliating Genes
1positive regulation of B cell proliferationGO:003089010.0BCL2, BCL6
2B cell differentiationGO:003018310.0BCL2, BCL6
3T cell differentiation in thymusGO:00330779.9B2M, BCL2
4cell morphogenesisGO:00009029.7BCL2, BCL6
5negative regulation of cell proliferationGO:00082858.8BCL2, BCL6, KMT2A

Sources for Intravascular Large B-Cell Lymphoma

About this section
2CDC
14ExPASy
15FDA
16FMA
24GTR
25HGMD
26HMDB
27ICD10
28ICD10 via Orphanet
29ICD9CM
30IUPHAR
31KEGG
34MedGen
36MeSH
37MESH via Orphanet
38MGI
41NCI
42NCIt
43NDF-RT
46NINDS
47Novoseek
49OMIM
50OMIM via Orphanet
54PubMed
55QIAGEN
60SNOMED-CT via Orphanet
64Tumor Gene Family of Databases
65UMLS
66UMLS via Orphanet