MCID: PNC019
MIFTS: 30

Pancreatoblastoma malady

Rare diseases, Gastrointestinal diseases, Cancer diseases, Endocrine diseases categories

Aliases & Classifications for Pancreatoblastoma

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Sources:
10Disease Ontology, 45NIH Rare Diseases, 12DISEASES, 51Orphanet, 65UMLS, 36MeSH, 42NCIt, 59SNOMED-CT, 28ICD10 via Orphanet, 37MESH via Orphanet, 66UMLS via Orphanet
See all sources

Aliases & Descriptions for Pancreatoblastoma:

Name: Pancreatoblastoma 10 45 12 51 65 36


Classifications:



Characteristics (Orphanet epidemiological data):

51
pancreatoblastoma:
Inheritance: Not applicable; Prevalence: <1/1000000 (Europe),<1/1000000 (Worldwide); Age of onset: Adult,Childhood; Age of death: adult,early childhood,late childhood


External Ids:

Disease Ontology10 DOID:6823
NCIt42 C4265
MeSH36 C537162
Orphanet51 677
SNOMED-CT59 189814006, 53618008
ICD10 via Orphanet28 C25.1
MESH via Orphanet37 C537162
UMLS via Orphanet66 C0334489

Summaries for Pancreatoblastoma

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Wikipedia:68 Pancreatoblastoma is a rare type of pancreatic cancer. more...

MalaCards based summary: Pancreatoblastoma is related to pancreatitis and beckwith-wiedemann syndrome. An important gene associated with Pancreatoblastoma is AFP (Alpha-Fetoprotein). Affiliated tissues include pancreas, liver and brain.

Related Diseases for Pancreatoblastoma

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Diseases related to Pancreatoblastoma via text searches within MalaCards or GeneCards Suite gene sharing:

(show top 50)    (show all 172)
idRelated DiseaseScoreTop Affiliating Genes
1pancreatitis10.5
2beckwith-wiedemann syndrome10.4
3acinar cell carcinoma10.3
4acrodysostosis10.3AFP, SYP
5urinary bladder small cell neuroendocrine carcinoma10.3AFP, SYP
6mediastinal malignant lymphoma10.3AFP, SYP
7agammaglobulinemia10.3AFP, CHGA
8pineal region teratoma10.3AFP, SYP
9vulvar inverted follicular keratosis10.3AFP, SYP
10hepatocellular clear cell carcinoma10.3AFP, CHGA
11cervix melanoma10.3AFP, CHGA
12cryptosporidiosis - chronic cholangitis - liver disease10.3AFP, CHGA
13seminoma10.3AFP, SYP
14long bone adamantinoma10.3AFP, CHGA
15endometrial stromal sarcoma10.3CHGA, SYP
16flat retinoschisis10.3CHGA, SYP
17ureter small cell carcinoma10.3CHGA, SYP
18auditory system disease10.3CHGA, SYP
19small cell lung cancer, childhood10.2CHGA, SYP
20hemangiopericytoma10.2CHGA, SYP
21gallbladder endocrine tumor10.2CHGA, SYP
22peritoneum cancer10.2CHGA, SYP
23selective iga deficiency disease10.2CHGA, SYP
24subpulmonary stenosis10.2CHGA, SYP
25pituitary adenoma10.2AFP, SYP
26oligodendroglioma10.2CHGA, SYP
27mixed epithelial tumor of ovary10.2AFP, SYP
28pancreatic serous cystic neoplasm10.2CHGA, SYP
29cavernous hemangioma10.2CHGA, SYP
30non-langerhans-cell histiocytosis10.2CHGA, SYP
31pinheiro freire-maia miranda syndrome10.2CHGA, SYP
32vulvar sebaceous carcinoma10.2CHGA, SYP
33kidney pelvis sarcomatoid transitional cell carcinoma10.2CHGA, SYP
34progesterone-receptor positive breast cancer10.2CHGA, SYP
35pediculus humanus capitis infestation10.2CHGA, SYP
36selective igg deficiency disease10.2CHGA, SYP
37periosteal osteogenic sarcoma10.2CHGA, SYP
38cranial nerve palsy10.2CHGA, SYP
39pulmonary embolism10.2CHGA, SYP
40botulism10.2AFP, SYP
41houlston ironton temple syndrome10.2CHGA, SYP
42pericardium leiomyoma10.2AFP, SERPINA1
43ethmoid sinus schneiderian papilloma10.2CHGA, SYP
44pulmonary valve disease10.2CHGA, SYP
45polymicrogyria turricephaly hypogenitalism10.2AFP, SERPINA1
46rete ovarii cystadenofibroma10.2CHGA, SYP
47ureteral disease10.2CHGA, SYP
48imperforate anus10.2CHGA, SYP
49oral hairy leukoplakia10.2CHGA, SYP
50central nervous system fibrosarcoma10.2CHGA, SYP

Graphical network of the top 20 diseases related to Pancreatoblastoma:



Diseases related to pancreatoblastoma

Symptoms for Pancreatoblastoma

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Drugs & Therapeutics for Pancreatoblastoma

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Interventional clinical trials:

Search ClinicalTrials, NIH Clinical Center for Pancreatoblastoma


Cochrane evidence based reviews: Pancreatoblastoma

Genetic Tests for Pancreatoblastoma

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Anatomical Context for Pancreatoblastoma

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MalaCards organs/tissues related to Pancreatoblastoma:

33
Pancreas, Liver, Brain

Animal Models for Pancreatoblastoma or affiliated genes

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Publications for Pancreatoblastoma

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Articles related to Pancreatoblastoma:

(show top 50)    (show all 117)
idTitleAuthorsYear
1
Response of Relapsed Pancreatoblastoma to a Combination of Vinorelbine and Oral Cyclophosphamide. (26056794)
2015
2
Pancreatoblastoma, a Rare Childhood Tumor: A Case Report. (25110242)
2014
3
CT-guided radiofrequency ablation following high-dose chemotherapy of a liver-metastasizing pancreatoblastoma with tumor thrombus in the portal vein. (23828484)
2013
4
The diagnosis and surgical treatment of pancreatoblastoma in adults: a case series and review of the literature. (24081396)
2013
5
Pancreatoblastoma: a rare, adult pancreatic tumor with many faces. (23991735)
2013
6
Congenital pancreatoblastoma: report of an atypical case and review of the literature. (22278199)
2012
7
Management of pancreatoblastoma in children and young adults. (22525406)
2012
8
Pancreatoblastoma: a rare tumor still evolving in clinical presentation and histology. (22572137)
2012
9
Pancreatoblastoma: a report from the European cooperative study group for paediatric rare tumours (EXPeRT). (21696948)
2011
10
Pancreatoblastoma in an adult patient. A case report. (19287117)
2009
11
Imprint cytology of pancreatoblastoma: a case report and review of the literature. (19229998)
2009
12
Childhood pancreatoblastoma: clinical features and immunohistochemistry analysis. (18308466)
2008
13
Revisiting metastatic adult pancreatoblastoma. A case and review of the literature. (18981556)
2008
14
Long-term survival of pancreatoblastoma in children. (18090935)
2007
15
Adrenocorticotropin-secreting pancreatoblastoma. (17642425)
2007
16
Pancreatoblastoma in an adult: case report and review of the literature. (16769539)
2006
17
Pediatric pancreatoblastoma: histopathologic and cytogenetic characterization of tumor and derived cell line. (15721631)
2005
18
Pancreatoblastoma associated with incomplete Beckwith-Wiedemann syndrome: case report and review of the literature. (16080945)
2005
19
Fine-needle aspiration cytology of pancreatoblastoma in a young woman: report of a case and review of the literature. (16138370)
2005
20
Pancreatoblastoma in an adult woman: sonography, CT, and dynamic gadolinium-enhanced MRI features. (15728031)
2005
21
Diagnosis, treatment and outcome of pancreatoblastoma. (15256806)
2004
22
The fine-needle aspiration biopsy cytology of pancreatoblastoma. (15540188)
2004
23
Antenatal manifestation of congenital pancreatoblastoma in a fetus with Beckwith-Wiedemann syndrome. (12673632)
2003
24
Ampullary pancreatoblastoma in an elderly patient: a case report and review of the literature. (14567752)
2003
25
Significance of aberrant (cytoplasmic/nuclear) expression of beta-catenin in pancreatoblastoma. (12533831)
2003
26
Pancreatoblastoma. A case report with special emphasis on squamoid corpuscles with optically clear nuclei rich in biotin. (12920766)
2003
27
Pancreatoblastoma is associated with chromosome 11p loss of heterozygosity and IGF2 overexpression. (12116082)
2002
28
Fine-needle aspiration cytology of pancreatoblastoma. (11477717)
2001
29
Pancreatoblastoma. (11770246)
2001
30
Imaging features of pancreatoblastoma. (11486805)
2001
31
Pancreatoblastoma treated by delayed operation after effective chemotherapy. (11083448)
2000
32
Pancreatoblastoma in an adolescent girl: case report and review of 26 Japanese cases. (9641374)
1998
33
Pancreatoblastoma. (9396538)
1997
34
Pancreatoblastoma in children. Case report and review of the literature. (9007475)
1996
35
Pancreatoblastoma: a histochemical and immunohistochemical analysis. (8944621)
1996
36
Adult pancreatoblastoma: a case report and review of the literature. (8792711)
1996
37
Pancreatoblastoma: case report and review of treatment in the literature. (8699999)
1996
38
Cytogenetic and flow cytometric analysis of a pancreatoblastoma. (7889500)
1995
39
Adenocarcinoma of the pancreas in childhood (pancreatoblastoma): report of a case with good response to chemotherapy. (8804461)
1995
40
Pancreatoblastoma in an older adult. (7605173)
1995
41
Pancreatoblastoma: a case report. (7954063)
1994
42
Pancreatoblastoma and solid and cystic papillary tumor: two tumors related to pancreatic ontogeny. (7809509)
1994
43
Pancreatoblastoma with marked elevation of serum alpha-fetoprotein. An autopsy case report with immunocytochemical study. (1689089)
1990
44
Pancreatoblastoma: MR appearance. (2159494)
1990
45
Use of enzyme histochemistry in the diagnosis of pancreatoblastoma. (2553578)
1989
46
Recurrent pancreatoblastoma with inappropriate adrenocorticotrophic hormone secretion. (2852926)
1988
47
Immunocytochemical markers of uncommon pancreatic tumors. Acinar cell carcinoma, pancreatoblastoma, and solid cystic (papillary-cystic) tumor. (3542187)
1987
48
Immunohistochemical study of pancreatoblastoma. (2449037)
1987
49
Pancreatoblastoma in Japan, with differential diagnosis from papillary cystic tumor (ductuloacinar adenoma) of the pancreas. (3554891)
1987
50
Pancreatoblastoma. A histochemical and ultrastructural analysis. (6141001)
1984

Variations for Pancreatoblastoma

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Expression for genes affiliated with Pancreatoblastoma

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Search GEO for disease gene expression data for Pancreatoblastoma.

Pathways for genes affiliated with Pancreatoblastoma

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GO Terms for genes affiliated with Pancreatoblastoma

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Biological processes related to Pancreatoblastoma according to GeneCards Suite gene sharing:

idNameGO IDScoreTop Affiliating Genes
1hyperosmotic responseGO:00069729.3NTS, SST

Sources for Pancreatoblastoma

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2CDC
14ExPASy
15FDA
16FMA
24GTR
25HGMD
26HMDB
27ICD10
28ICD10 via Orphanet
29ICD9CM
30IUPHAR
31KEGG
34MedGen
36MeSH
37MESH via Orphanet
38MGI
41NCI
42NCIt
43NDF-RT
46NINDS
47Novoseek
49OMIM
50OMIM via Orphanet
54PubMed
55QIAGEN
60SNOMED-CT via Orphanet
64Tumor Gene Family of Databases
65UMLS
66UMLS via Orphanet