MCID: PLM064
MIFTS: 26

Pulmonary Sequestration malady

Categories: Rare diseases, Respiratory diseases, Fetal diseases

Aliases & Classifications for Pulmonary Sequestration

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Aliases & Descriptions for Pulmonary Sequestration:

Name: Pulmonary Sequestration 46

Classifications:



Summaries for Pulmonary Sequestration

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NIH Rare Diseases:46 Pulmonary sequestration is a rare congenital (present from birth) malformation where non-functioning lung tissue is separated from the rest of the lung and supplied with blood from an unusual source, often an artery from systemic circulation. pulmonary sequestrations may be defined as intralobular or extralobular, depending on their location. symptoms may include a chronic  or recurrent cough, respiratory distress or lung infection. treatment depends on the location and may involve surgery. last updated: 8/12/2016

MalaCards based summary: Pulmonary Sequestration is related to congenital pulmonary sequestration and intralobar congenital pulmonary sequestration. An important gene associated with Pulmonary Sequestration is DICER1 (Dicer 1, Ribonuclease III). Affiliated tissues include lung, heart and neutrophil.

Wikipedia:69 A pulmonary sequestration (bronchopulmonary sequestration or cystic lung lesion), is a medical condition... more...

Related Diseases for Pulmonary Sequestration

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Graphical network of the top 20 diseases related to Pulmonary Sequestration:



Diseases related to pulmonary sequestration

Symptoms for Pulmonary Sequestration

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Drugs & Therapeutics for Pulmonary Sequestration

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Drugs for Pulmonary Sequestration (from DrugBank, HMDB, Dgidb, PharmGKB, IUPHAR, NovoSeek, BitterDB):

(show all 7)
idNameStatusPhaseClinical TrialsCas NumberPubChem Id
1
OmalizumabPhase 4139242138-07-4
Synonyms:
242138-07-4
D05251
Ig gamma-1 chain C region
Omalizumab
 
Omalizumab (USAN/INN)
Omalizumab (genetical recombination)
Omalizumab (genetical recombination) (JAN)
Xolair
Xolair (TN)
2
HydroxyureaPhase 2208127-07-13657
Synonyms:
1-HYDROXYUREA
127-07-1
4-03-00-00170 (Beilstein Handbook Reference)
55291_FLUKA
AC1L1GF8
AC1Q4ZXK
AI3-51139
BB_SC-7256
BRN 1741548
BSPBio_002164
Bio1_000451
Bio1_000940
Bio1_001429
Biosupressin
C07044
CCRIS 958
CHEBI:44423
CHEMBL467
CID3657
Carbamohydroxamic Acid
Carbamohydroxamic acid
Carbamohydroximic Acid
Carbamohydroximic acid
Carbamohydroxyamic Acid
Carbamohydroxyamic acid
Carbamoyl Oxime
Carbamoyl oxime
Carbamyl Hydroxamate
Carbamyl hydroxamate
Carrbamoyl Oxime
D00341
D006918
DB01005
DRG-0253
DivK1c_000556
Droxia
Droxia (TM)
Droxia (TN)
E0723DBA-5AF3-49D1-B5F6-59420AB87AC9
EINECS 204-821-7
EU-0100596
FT-0083575
H 8627
H0310
H20210
H8627_SIGMA
HMS1920F09
HMS2091L17
HMS501L18
HSDB 6887
HU
HYDREA (TN)
HYDROXY-UREA
Hidrix
Hidroxicarbamida
Hidroxicarbamida [INN-Spanish]
Hydrea
Hydrea (TM)
Hydrea, Biosupressin, Cytodrox, Hydroxyurea
Hydreia
Hydroxicarbamidum
Hydroxycarbamid
Hydroxycarbamide
Hydroxycarbamide (JAN/INN)
Hydroxycarbamidum
Hydroxycarbamidum [INN-Latin]
Hydroxycarbamine
Hydroxyharnstoff
Hydroxyharnstoff [German]
Hydroxylurea
Hydroxyurea
Hydroxyurea (D4)
Hydroxyurea (USP)
Hydroxyurea [USAN:BAN]
Hydroxyurea(d4)
 
Hydura
Hydurea
I05-0250
IDI1_000556
Idrossicarbamide
Idrossicarbamide [DCIT]
Idrossicarbamide [Dcit]
KBio1_000556
KBio2_001389
KBio2_003957
KBio2_006525
KBio3_001384
KBioGR_000383
KBioSS_001389
LS-709
Litaler
Litalir
Lopac-H-8627
Lopac0_000596
MLS001332381
MLS001332382
MLS002153389
MolMap_000029
MolPort-000-003-971
Mylocel
N-(Aminocarbonyl) Hydroxyamine
N-Carbamoylhydroxylamine
N-HYDROXY UREA
N-Hydroxymocovina
N-Hydroxymocovina [Czech]
N-Hydroxyurea
NCGC00015520-01
NCGC00015520-02
NCGC00015520-07
NCGC00093974-01
NCGC00093974-02
NCGC00093974-03
NCGC00093974-04
NCGC00093974-05
NCI C04831
NCI-C04831
NCI60_002773
NCIMech_000139
NHY
NINDS_000556
NSC 32065
NSC32065
Onco-Carbide
Onco-carbide
Oncocarbide
Oxyurea
S-phase/G-1 interface inhibitor
S1896_Selleck
SK 22591
SMR000059149
SPBio_000247
SPECTRUM1500344
SQ 1089
SQ-1089
Siklos
Spectrum2_000064
Spectrum3_000462
Spectrum4_000012
Spectrum5_000836
Spectrum_000909
Sterile Urea
TL8000673
UNII-X6Q56QN5QC
Ureaphil
WLN: ZVMQ
carbamide oxide
hydroxyaminomethanamide
hydroxyurea
nchembio.573-comp3
nchembio.90-comp4
nchembio749-comp3
tetratogen: inhibits ribonucleoside diphosphate reductase
3
GemcitabinePhase 2192895058-81-460750
Synonyms:
103882-84-4
122111-03-9
2',2'-DiF-dC
2',2'-Difluoro-2'-deoxycytidine
2',2'-Difluorodeoxycytidine
2'-Deoxy-.beta.-D-2',2'-difluorocytidine
2'-Deoxy-2',2'-difluorocytidine
4-Amino-1-[(2R,4R,5R)-3,3-difluoro-4-hydroxy-5-(hydroxymethyl)oxolan-2-yl]pyrimidin-2-one
4-Amino-1-[3,3-difluoro-4-hydroxy-5-(hydroxymethyl) tetrahydrofuran-2-yl]-1H-pyrimidin-2-one
4-amino-1-((2R,4R,5R)-3,3-Difluoro-4-hydroxy-5-(hydroxymethyl)-tetrahydrofuran-2-yl)pyrimidin-2(1H)-one
4-amino-1-((2R,4R,5R)-3,3-difluoro-4-hydroxy-5-(hydroxymethyl)-tetrahydrofuran-2-yl)pyrimidin-2(1H)-one
95058-81-4
AB1004842
AC1L1TUQ
C07650
CCRIS 8984
CHEBI:175901
CHEMBL888
CID60750
Cytidine, 2'-deoxy-2',2'-difluoro-2'-Deoxy-.beta.-D-2',2'-difluorocytidine
D02368
DB00441
DDFC
DFDC
DFdC
DFdCyd
Folfugem
GEO
Gamcitabine
GemLip
Gemcel
 
Gemcin
Gemcitabin
Gemcitabina
Gemcitabina [INN-Spanish]
Gemcitabine
Gemcitabine (USAN/INN)
Gemcitabine HCl
Gemcitabine hydrochloride
Gemcitabine stereoisomer
Gemcitabinum
Gemcitabinum [INN-Latin]
Gemtro
Gemzar
Gemzar (hydrochloride)
HMS2089P10
HSDB 7567
Inno-D07001
LS-59139
LY 188011
LY-188011
LY188011
NCGC00168784-01
NChemBio.2007.10-comp25
NSC 613327
NSC613327
TL8005979
UNII-B76N6SBZ8R
ZINC18279854
Zefei
gemcitabine
nchembio.573-comp7
nchembio.90-comp2
4
protease inhibitorsPhase 25157
Synonyms:
 
protease inhibitors
5
PaclitaxelPhase 2269133069-62-436314
Synonyms:
(2AR-(2aalpha,4beta,4abeta,6beta,9alpha(alpha r*,betas*),11alpha,12alpha,12balpha))-beta-(benzoylamino)-alpha-hydroxybenzenepropanoic acid 6,12b-bis(acetyloxy)-12-(benzoyloxy)-2a,3,4,4a,5,6,9,10,11,12,12a,12b-dodecahydro-4,11-dihydroxy-4a,8,13,13-tetramethyl-5-oxo-7,11-methano-1H-cyclodeca(3,4)benz(1,2-b)oxet-9-yl ester
12-benzoate, 9-ester with (2R,3S)-N-benzoyl-3-phenylisoserine
157069-30-2
33069-62-4
5beta,20-Epoxy-1,2-alpha,4,7beta,10beta,13alpha-hexahydroxytax-11-en-9-one 4,10-diacetate 2-benzoate 13-ester with (2R,3S)-N-benzoyl-3-phenylisoserine
7,11-Methano-1H-cyclodeca[3,4]benz[1,2-b]oxete, benzenepropanoic acid deriv.
7,11-Methano-5H-cyclodeca[3,4]benz[1,2-b]oxete,benzenepropanoic acid deriv.
7-Epi-Paclitaxel
7-Epi-Taxol
7-Epipaclitaxel
7-Epitaxol
7-epi-Paclitaxel
7-epi-Taxol
AB00513812
ABI 007
ABI-007
ABI007
AC-675
AC1L1IOG
AC1L1VJI
AC1L9AVF
ACon1_002231
ANX-513
Abraxane
Abraxane (TN)
Abraxane I.V. Suspension
Abraxis BioScience brand of albumin-bound paclitaxel
Ambotz33069-62-4
Anzatax
Asotax
BIDD:PXR0046
BMS 181339-01
BMS-181339
BMS-181339-01
BPBio1_000320
BRD-A23723433-001-01-2
BRD-A28746609-001-04-0
BRD-K62008436-001-03-1
BSPBio_000290
BSPBio_001152
BSPBio_002614
Bio-0076
Bio1_000362
Bio1_000851
Bio1_001340
Bio2_000416
Bio2_000896
Bristaxol
C07394
C466458
C47H51NO14
CCRIS 8143
CHEBI:103439
CHEBI:45863
CHEMBL100910
CHEMBL418410
CHEMBL48
CID36314
CID441276
CID4666
CID6713921
CID6915727
CPD-8718
Capxol
D00491
DB01229
DHP-107
DHP-208
DRG-0190
DTS-301
DivK1c_000441
EU-0101201
Ebetaxel
EmPAC
Epitaxol
Genaxol
Genetaxyl
Genexol
Genexol-PM
HMS1362J13
HMS1568O12
HMS1792J13
HMS1922K08
HMS1990J13
HMS2090D07
HMS2093K15
HMS501G03
HSDB 6839
I06-0014
IDI1_000441
IDI1_002171
Intaxel
KBio1_000441
KBio2_000492
KBio2_002016
KBio2_002509
KBio2_003060
KBio2_004584
KBio2_005077
KBio2_005628
KBio2_007152
KBio2_007645
KBio3_000903
KBio3_000904
KBio3_001834
KBio3_002987
KBioGR_000492
KBioGR_001893
 
KBioGR_002509
KBioSS_000492
KBioSS_002016
KBioSS_002517
LMPR0104390001
LS-31070
LipoPac
Lopac0_001201
MBT 0206
MEGxp0_001940
MLS000863266
MLS001077297
MLS002154218
MLS002172439
MLS002695976
MPI-5018
Micellar Paclitaxel
Mitotax
MolPort-001-742-627
MolPort-003-665-783
MolPort-003-932-365
NCGC00024995-02
NCGC00024995-03
NCGC00024995-04
NCGC00024995-05
NCGC00024995-06
NCGC00024995-07
NCGC00164367-01
NCGC00164367-02
NCGC00164367-03
NCI60_000601
NINDS_000441
NK 105
NP-010981
NSC 125973
NSC-125973
NSC125973
NSC358882
Nanotaxel
Neuro_000060
Nova-12005
OAS-PAC-100
OncoGel
Onxal
Onxol
Onxol, Taxol, Nov-Onxol, Paclitaxel
P1632
Paclical
Pacligel
Paclitaxel
Paclitaxel (JAN/USP)
Paclitaxel (JAN/USP/INN)
Paclitaxel (Taxol)
Paclitaxel [USAN:INN:BAN]
Paxceed
Paxene
Paxoral
Plaxicel
Praxel
Prestwick0_000155
Prestwick1_000155
Prestwick2_000155
Prestwick3_000155
Probes2_000350
QW 8184
S-8184 Paclitaxel Injectable Emulsion
S1150_Selleck
SDCCGMLS-0066823.P001
SDP-013
SMP1_000228
SMR000394086
SMR000857385
SPBio_000943
SPBio_002229
SPECTRUM1503908
ST50306996
Spectrum2_000872
Spectrum3_001057
Spectrum4_001197
Spectrum5_001491
Spectrum_001536
T 7402
T1912_SIGMA
T7191_SIGMA
T7402_SIGMA
TA1
TAXOL (TN)
TAXOL, 10-EPI,
TXL
TaxAlbin
Taxol
Taxol A
Taxol Konzentrat
Taxol.RTM. (Registered Trademark)
UNII-P88XT4IS4D
UPCMLD-DP108:001
UPCMLD-DP108:002
Vascular Wrap
Xorane
Yewtaxan
abi-007
albumin-bound paclitaxel
cMAP_000068
nab-paclitaxel
nchembio.188-comp1
nchembio.2007.34-comp9
nchembio.215-comp9
nchembio853-comp6
paclitaxel
weekly paclitaxel
6serineNutraceuticalPhase 2883
7
Iron10807439-89-623925
Synonyms:
02583_FLUKA
12310_ALDRICH
12310_RIEDEL
129048-51-7
14067-02-8
161135-39-3
190454-13-8
195161-83-2
199281-22-6
209309_ALDRICH
209309_SIAL
255637_ALDRICH
266213_ALDRICH
266256_ALDRICH
267945_ALDRICH
267953_ALDRICH
26Fe
338141_ALDRICH
356808_ALDRICH
356824_ALDRICH
356832_ALDRICH
39344-71-3
3ZhP
413054_ALDRICH
443783-52-6
44890_ALDRICH
44890_FLUKA
675141-17-0
70884-35-4
73135-38-3
7439-89-6
8011-79-8
8053-60-9
AC1L2N38
ATW 230
ATW 432
Ancor B
Ancor en 80/150
Armco iron
Atomel 28
Atomel 300M200
Atomel 500M
Atomel 95
Atomiron 44MR
Atomiron 5M
Atomiron AFP 25
Atomiron AFP 5
C00023
C3518_SIAL
C3518_SIGMA
CCRIS 1580
CHEBI:18248
CID23925
Carbonyl iron
Copy Powder CS 105-175
D007501
DB01592
DSP 1000
DSP 128B
DSP 135
DSP 135C
DSP 138
Diseases (animal), iron overload
Diseases, iron overload
EF 1000
EF 250
EFV 200/300
EFV 250
EFV 250/400
EINECS 231-096-4
 
Ed-In-Sol
Eisen
Electrolytic iron
F 60 (metal)
FE
FT 3 (element)
Fe
Fe-40
Fe1+
Feronate
Ferretts
Ferro-Caps
Ferro-Time
Ferrousal
Ferrovac E
Ferrum
Ferrum metallicum
GS 6
HF 2 (element)
HL (iron)
HQ (metal)
HS (iron)
HS 4849
HSDB 604
Hemocyte
Hierro
Hoeganaes ATW 230
Hoeganaes EH
IRMM524A_FLUKA
IRMM524B_FLUKA
IRON
Iron (Fe)
Iron (Fe1+)
Iron ion (Fe+)
Iron ion(1+)
Iron monocation
Iron powder
Iron standard for AAS
Iron(1+)
Iron(1+) ion
Iron(III) nitrate solution
Iron, carbonyl
Iron, electrolytic
Iron, elemental
Iron, ion (Fe1+)
Iron, ion (Fe1+) (8CI,9CI)
Iron, reduced
LOHA
LS-3196
MolPort-003-925-001
NC 100
PZh-1M3
PZh-2
PZh1M1
PZh2M
PZh2M1
PZh2M2
PZh3
PZh3M
PZh4M
PZhO
Reduced iron
Remko
SUY-B 2
Siderol
UNII-E1UOL152H7
Vitedyn-Slo
Yieronia
fer
ferrous iron
hierro

Interventional clinical trials:

idNameStatusNCT IDPhase
1Immunologic Basis of Anti-IgE Therapy (Study II: On Patients With Asthma)CompletedNCT00367016Phase 4
2Study to Assess Safety and Impact of SelG1 With or Without Hydroxyurea Therapy in Sickle Cell Disease Patients With Pain CrisesCompletedNCT01895361Phase 2
3Safety and Efficacy of Inhaled Alpha-1 Antitrypsin in Preventing Bronchiolitis Obliterable Syndrome in Lung Transplant RecipientsNot yet recruitingNCT01394835Phase 2
4Nab-pacliatxel Plus Gemcitabine in Korean Patients With Metastatic Pancreatic Ductal AdenocarcinomaNot yet recruitingNCT02426281Phase 2
5Cardiopulmonary Circuits in the Pediatric PopulationCompletedNCT00208728
6Iron Absorption and Utilization During Tuberculosis and After TreatmentRecruitingNCT02176772
7Goal-directed Fluid Resuscitation in Acute PancreatitisTerminatedNCT00853515

Search NIH Clinical Center for Pulmonary Sequestration

Genetic Tests for Pulmonary Sequestration

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Anatomical Context for Pulmonary Sequestration

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MalaCards organs/tissues related to Pulmonary Sequestration:

34
Lung, Heart, Neutrophil, Bone marrow, Liver, Bone, Myeloid

Animal Models for Pulmonary Sequestration or affiliated genes

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Publications for Pulmonary Sequestration

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Articles related to Pulmonary Sequestration:

(show top 50)    (show all 576)
idTitleAuthorsYear
1
Necrotizing arteritis occurring in an intralobar pulmonary sequestration of a patient without systemic vasculitis syndrome. (26874730)
2016
2
Pulmonary haemodynamics in Fontan physiology after lobectomy in a patient with a single ventricle associated with pulmonary sequestration. (27572898)
2016
3
A Case Report and a Short Literature Review of Pulmonary Sequestration Showing Elevated Serum Levels of Carbohydrate Antigen 19-9. (26328799)
2015
4
Pulmonary sequestration: A rare case in a patient with acute chest pain and palpitation mimicking the acute coronary syndrome. (25624605)
2015
5
Pulmonary Sequestration: A 29 Patient Case Series and Review. (26816878)
2015
6
Intralobar pulmonary sequestration in an adult female patient mimicking asthma: A case report. (25159547)
2014
7
Intralobar pulmonary sequestration complicating with cryptococcal infection. (24405867)
2014
8
Intralobular pulmonary sequestration. (24224295)
2013
9
Pulmonary sequestration. (23121876)
2013
10
Video-assisted thoracic surgery for pulmonary sequestration compared with posterolateral thoracotomy. (23773788)
2013
11
Extralobar pulmonary sequestration: a case report. (24354098)
2013
12
A fighter pilot case of pulmonary sequestration. (23316546)
2012
13
Fetal bronchoscopy: its successful use in a case of extralobar pulmonary sequestration. (22631227)
2012
14
Intralobar pulmonary sequestration: an uncommon case with triple arterial supply and systemic venous drainage. (22526550)
2012
15
Pulmonary sequestration infected with nontuberculous mycobacteria: a report of two cases and literature review. (23146810)
2012
16
Extralobar pulmonary sequestration in association with congenital cystic adenomatoid malformation: an unusual abdominal mass. (22295391)
2011
17
Pulmonary sequestration with an exceptionally large feeding artery. (18996709)
2009
18
Extralobar pulmonary sequestration infected with Mycobacterium gordonae. (19154870)
2009
19
Extralobar pulmonary sequestration with hemothorax secondary to pulmonary infarction. (19219338)
2009
20
Prenatal diagnosis of pulmonary sequestration by ultrasound and magnetic resonance imaging. (18218562)
2008
21
Neonatological and pulmonological management of bilateral pulmonary sequestration in a neonate. (19104895)
2008
22
Pulmonary sequestration: a single-institutional series composed of 27 cases. (17382633)
2007
23
Use of multidetector CT angiography and 3D postprocessing in a case of pulmonary sequestration. (17449384)
2007
24
Successful surgical resection of intrapericardial extralobar pulmonary sequestration with congenital pulmonary adenomatoid malformation type II. (16798246)
2006
25
Intrathoracic ectopic lobe of liver presenting as pulmonary sequestration. (16338877)
2005
26
Mediastinal Castleman disease mimicking mediastinal pulmonary sequestration. (16077341)
2005
27
Intralobar pulmonary sequestration with arterial supply from the coronary circulation. (16282915)
2005
28
MDCT demonstration of intralobar pulmonary sequestration of the right upper lobe in an adult. (16304037)
2005
29
Infected infradiaphragmatic retroperitoneal extralobar pulmonary sequestration: a case report. (16361825)
2005
30
Extralobar pulmonary sequestration simulates posterior neurogenic tumor. (15172305)
2004
31
Techniques for treating aberrant arteries during resection of pulmonary sequestration by video-assisted thoracic surgery: report of two cases. (12560908)
2003
32
Treatment of pulmonary sequestration by video-assisted thoracic surgery (VATS). (12799898)
2003
33
Video-assisted thoracoscopic surgery for intralobar pulmonary sequestration. (12605183)
2003
34
Occlusion of an aberrant artery to a pulmonary sequestration using a duct occluder. (12440188)
2002
35
Bacteremic pneumococcal pneumonia: bone marrow release and pulmonary sequestration of neutrophils. (9504579)
1998
36
Color and duplex Doppler sonographic investigation of in utero spontaneous regression of pulmonary sequestration. (8908591)
1996
37
Preoperative evaluation of pulmonary sequestration by helical CT angiography. (8819421)
1996
38
Iloprost attenuates trauma-related pulmonary sequestration of leucocytes and platelets. (7517566)
1994
39
Antenatal detection of subdiaphragmatic pulmonary sequestration: a case report. (8086395)
1994
40
Coexistent intralobar and extralobar pulmonary sequestration: imaging findings. (8498214)
1993
41
Antenatal and postnatal findings in intra-abdominal pulmonary sequestration. (1596767)
1992
42
Prenatal ultrasound detection of intra-abdominal pulmonary sequestration with postnatal MRI correlation. (2047166)
1991
43
Imaging of prenatally detected intra-abdominal extralobar pulmonary sequestration. (2196980)
1990
44
Antenatal sonographic findings in a case of intra-abdominal pulmonary sequestration. (2539574)
1989
45
A case of intralobar pulmonary sequestration with calcification and elevated serum values of carcinoembryonic antigen and carbohydrate antigen 19-9. (2607569)
1989
46
Pulmonary sequestration: ultrasonographic visualization of feeding artery. (2681496)
1989
47
Pulmonary sequestration. (3656026)
1987
48
Radiological case of the month. Extralobar pulmonary sequestration. (3314476)
1987
49
Massive pleural effusion and hypoplasia of the lung accompanying extralobar pulmonary sequestration. (7309037)
1981
50
Surgical management of lung bud anomalies: lobar emphysema, bronchogenic cyst, cystic adenomatoid malformation, and intralobar pulmonary sequestration. (454042)
1979

Variations for Pulmonary Sequestration

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Expression for genes affiliated with Pulmonary Sequestration

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Search GEO for disease gene expression data for Pulmonary Sequestration.

Pathways for genes affiliated with Pulmonary Sequestration

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GO Terms for genes affiliated with Pulmonary Sequestration

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Sources for Pulmonary Sequestration

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2CDC
6CNVD
10DGIdb
15ExPASy
16FDA
17FMA
25GTR
26HGMD
27HMDB
28ICD10
29ICD10 via Orphanet
30ICD9CM
31IUPHAR
32KEGG
35MedGen
37MeSH
38MESH via Orphanet
39MGI
42NCI
43NCIt
44NDF-RT
47NINDS
48Novoseek
50OMIM
51OMIM via Orphanet
55PubMed
56QIAGEN
61SNOMED-CT via Orphanet
65Tumor Gene Family of Databases
66UMLS
67UMLS via Orphanet