MCID: RNL089
MIFTS: 20

Renal Nutcracker Syndrome malady

Rare diseases, Nephrological diseases, Cardiovascular diseases categories

Aliases & Classifications for Renal Nutcracker Syndrome

About this section
Sources:
45NIH Rare Diseases, 51Orphanet, 65UMLS, 37MESH via Orphanet, 66UMLS via Orphanet
See all sources

Aliases & Descriptions for Renal Nutcracker Syndrome:

Name: Renal Nutcracker Syndrome 45 51 65
Left Renal Vein Entrapment Syndrome 45 51
Leiomyomatosis Peritonealis Disseminata 65
 
Nutcracker Syndrome 45
Raine Syndrome 65
Rns 51


Classifications:

Orphanet: 51 
Rare renal diseases


Characteristics (Orphanet epidemiological data):

51
renal nutcracker syndrome:
Age of onset: Adult; Age of death: normal life expectancy


External Ids:

Orphanet51 71273
MESH via Orphanet37 D059228
UMLS via Orphanet66 C3178770

Summaries for Renal Nutcracker Syndrome

About this section
NIH Rare Diseases:45 Renal nutcracker syndrome (ncs) is a condition that occurs when the left renal vein (the vein that carries blood purified by the left kidney) becomes compressed. the signs and symptoms of the condition can vary from person to person. some affected people may be asymptomatic while others develop severe and persistent symptoms. when present, features of ncs may include blood in the urine (hematuria), orthostatic proteinuria, flank pain and/or abdominal pain. some cases of mild ncs in children may be due to changes in body proportions associated with growth. why ncs occurs or becomes symptomatic in adults is less clear. treatment ranges from surveillance to surgical intervention and is based on the severity of symptoms and their expected reversibility when considering the affected person's age and stage of the syndrome. last updated: 8/24/2015

MalaCards based summary: Renal Nutcracker Syndrome, also known as left renal vein entrapment syndrome, is related to orthostatic proteinuria and epilepsy syndrome. Affiliated tissues include kidney, pancreas and liver.

Related Diseases for Renal Nutcracker Syndrome

About this section

Graphical network of the top 20 diseases related to Renal Nutcracker Syndrome:



Diseases related to renal nutcracker syndrome

Symptoms for Renal Nutcracker Syndrome

About this section

Drugs & Therapeutics for Renal Nutcracker Syndrome

About this section

Interventional clinical trials:

Search ClinicalTrials, NIH Clinical Center for Renal Nutcracker Syndrome

Genetic Tests for Renal Nutcracker Syndrome

About this section

Anatomical Context for Renal Nutcracker Syndrome

About this section

MalaCards organs/tissues related to Renal Nutcracker Syndrome:

33
Kidney, Pancreas, Liver

Animal Models for Renal Nutcracker Syndrome or affiliated genes

About this section

Publications for Renal Nutcracker Syndrome

About this section

Articles related to Renal Nutcracker Syndrome:

idTitleAuthorsYear
1
Retroperitoneal laparoscopic extravascular stent placement for renal nutcracker syndrome: initial experience. (24576978)
2014
2
The roles of the liver and pancreas in renal nutcracker syndrome. (25084688)
2014
3
Renal nutcracker syndrome: surgical options. (23932560)
2013
4
Management of renal nutcracker syndrome by retroperitoneal laparoscopic nephrectomy with ex vivo autograft repair and autotransplantation: a case report and review of the literature. (19946558)
2009
5
Current trends in the diagnosis and management of renal nutcracker syndrome: a review. (16431142)
2006

Variations for Renal Nutcracker Syndrome

About this section

Expression for genes affiliated with Renal Nutcracker Syndrome

About this section
Search GEO for disease gene expression data for Renal Nutcracker Syndrome.

Pathways for genes affiliated with Renal Nutcracker Syndrome

About this section

GO Terms for genes affiliated with Renal Nutcracker Syndrome

About this section

Sources for Renal Nutcracker Syndrome

About this section
2CDC
14ExPASy
15FDA
16FMA
24GTR
25HGMD
26HMDB
27ICD10
28ICD10 via Orphanet
29ICD9CM
30IUPHAR
31KEGG
34MedGen
36MeSH
37MESH via Orphanet
38MGI
41NCI
42NCIt
43NDF-RT
46NINDS
47Novoseek
49OMIM
50OMIM via Orphanet
54PubMed
55QIAGEN
60SNOMED-CT via Orphanet
64Tumor Gene Family of Databases
65UMLS
66UMLS via Orphanet