AHL
MCID: ACT032
MIFTS: 31

Acute Hemorrhagic Leukoencephalitis (AHL)

Categories: Cardiovascular diseases, Neuronal diseases, Rare diseases

Aliases & Classifications for Acute Hemorrhagic Leukoencephalitis

MalaCards integrated aliases for Acute Hemorrhagic Leukoencephalitis:

Name: Acute Hemorrhagic Leukoencephalitis 58 12 54 15 17
Ahl 58 12 54
Leukoencephalitis, Acute Hemorrhagic 45 74
Acute Haemorrhagic Leucoencephalitis of Weston Hurst 12
Acute Necrotizing Hemorrhagic Leukoencephalitis 12
Acute Hemorrhagic Encephalomyelitis 12
Weston-Hurst Syndrome 12
Ahle 54

Classifications:



External Ids:

Disease Ontology 12 DOID:10992
OMIM 58 606752
MeSH 45 D004684
NCIt 51 C84535
SNOMED-CT 69 72986009
MedGen 43 C0014077
UMLS 74 C0014077

Summaries for Acute Hemorrhagic Leukoencephalitis

NIH Rare Diseases : 54 Acute hemorrhagic leukoencephalitis (AHLE) is a very rare form of acute disseminated encephalomyelitis that frequently results in death. It is characterized by a brief but intense attack of inflammation in the brain and spinal cord that damages the myelin (the protective covering of the nerve fibers). It may also cause bleeding in the brain, leading to damage of the white matter. Symptoms usually come on quickly and may include fever, neck stiffness, fatigue, headache, nausea, vomiting, seizures, and coma. AHLE has a very poor prognosis, with rapid deterioration and death usually occurring within days to one week after onset of symptoms. Although the exact cause is unclear, AHLE usually follows a viral or bacterial infection, or less often, vaccination for measles or rabies. Some researchers think that an infection or vaccination can initiate an autoimmune process in the body thus leading to AHLE. While favorable outcomes are uncommon, timely treatment with immunosuppressant medications and plasma exchange may lead to an improved outlook.  

MalaCards based summary : Acute Hemorrhagic Leukoencephalitis, also known as ahl, is related to acute disseminated encephalomyelitis and ataxia, combined cerebellar and peripheral, with hearing loss and diabetes mellitus. An important gene associated with Acute Hemorrhagic Leukoencephalitis is CFI (Complement Factor I). Affiliated tissues include brain, spinal cord and myeloid.

Disease Ontology : 12 A very rare form of acute disseminated encephalomyelitis, characterized by a brief but intense attack of inflammation and necrotizing vasculitis of venules and hemorrhage, and edema.

Description from OMIM: 606752

Related Diseases for Acute Hemorrhagic Leukoencephalitis

Graphical network of the top 20 diseases related to Acute Hemorrhagic Leukoencephalitis:



Diseases related to Acute Hemorrhagic Leukoencephalitis

Symptoms & Phenotypes for Acute Hemorrhagic Leukoencephalitis

Clinical features from OMIM:

606752

Drugs & Therapeutics for Acute Hemorrhagic Leukoencephalitis

Search Clinical Trials , NIH Clinical Center for Acute Hemorrhagic Leukoencephalitis

Cochrane evidence based reviews: leukoencephalitis, acute hemorrhagic

Genetic Tests for Acute Hemorrhagic Leukoencephalitis

Anatomical Context for Acute Hemorrhagic Leukoencephalitis

MalaCards organs/tissues related to Acute Hemorrhagic Leukoencephalitis:

42
Brain, Spinal Cord, Myeloid, Cerebellum

Publications for Acute Hemorrhagic Leukoencephalitis

Articles related to Acute Hemorrhagic Leukoencephalitis:

(show top 50) (show all 173)
# Title Authors Year
1
Intravenous immunoglobulin for acute hemorrhagic leukoencephalitis refractory to plasmapheresis. ( 30656033 )
2019
2
Loss of Arabidopsis Halotolerance 2-like (AHL), a 3'-phosphoadenosine-5'-phosphate phosphatase, suppresses insensitive response of Arabidopsis thaliana ring zinc finger 1 (atrzf1) mutant to abiotic stress. ( 30637572 )
2019
3
The Search for Natural Inhibitors of Biofilm Formation and the Activity of the Autoinductor C6-AHL in Klebsiella pneumoniae ATCC 13884. ( 30704099 )
2019
4
Stenotrophomonas maltophilia AHL-Degrading Strains Isolated from Marine Invertebrate Microbiota Attenuate the Virulence of Pectobacterium carotovorum and Vibrio coralliilyticus. ( 30762152 )
2019
5
AL amyloidosis with non-amyloid forming monoclonal immunoglobulin deposition; a case mimicking AHL amyloidosis. ( 30466387 )
2018
6
Effects of Sulfide Flavors on AHL-Mediated Quorum Sensing and Biofilm Formation of Hafnia alvei. ( 30221799 )
2018
7
Embryonic and Larvae of Endemic Celebes Rainbow Fish <I>Marosatherina ladigesi</I> (C.G.E.Ahl, 1936) (Atheriniformes: Telmatherinidae). ( 30221883 )
2018
8
Distribution and characterization of N-acylhomoserine lactone (AHL)-degrading activity and AHL lactonase gene (qsdS) in Sphingopyxis. ( 30391237 )
2018
9
Seed Extract of Psoralea corylifolia and Its Constituent Bakuchiol Impairs AHL-Based Quorum Sensing and Biofilm Formation in Food- and Human-Related Pathogens. ( 30410871 )
2018
10
A Rhodococcal Transcriptional Regulatory Mechanism Detects the Common Lactone Ring of AHL Quorum-Sensing Signals and Triggers the Quorum-Quenching Response. ( 30524404 )
2018
11
The diversity, distribution and function of N-acyl-homoserine lactone (AHL) in industrial anaerobic granular sludge. ( 28946084 )
2018
12
Identification of AHL- and BDSF-Controlled Proteins in Burkholderia cenocepacia by Proteomics. ( 29130174 )
2018
13
mQTL-seq and classical mapping implicates the role of an AT-HOOK MOTIF CONTAINING NUCLEAR LOCALIZED (AHL) family gene in Ascochyta blight resistance of chickpea. ( 29492990 )
2018
14
Purification and characterisation of a quorum quenching AHL-lactonase from the endophytic bacterium Enterobacter sp. CS66. ( 29518220 )
2018
15
Characterization of AiiK, an AHL lactonase, from Kurthia huakui LAM0618T and its application in quorum quenching on Pseudomonas aeruginosa PAO1. ( 29662232 )
2018
16
AHL-lactonase expression in three marine emerging pathogenic Vibrio spp. reduces virulence and mortality in brine shrimp (Artemia salina) and Manila clam (Venerupis philippinarum). ( 29664914 )
2018
17
Conformational studies of Gram-negative bacterial quorum sensing acyl homoserine lactone (AHL) molecules: The importance of the n → π* interaction. ( 29705275 )
2018
18
Chitosan encapsulation modulates the effect of trans-cinnamaldehyde on AHL-regulated quorum sensing activity. ( 29852434 )
2018
19
Enhanced exopolysaccharide production and biofilm forming ability in methicillin resistant Staphylococcus sciuri isolated from dairy in response to acyl homoserine lactone (AHL). ( 29892109 )
2018
20
Acyl-group specificity of AHL synthases involved in quorum-sensing in Roseobacter group bacteria. ( 29977398 )
2018
21
Insights into β-ketoacyl-chain recognition for β-ketoacyl-ACP utilizing AHL synthases. ( 30027952 )
2018
22
Genetic diversity and phenotypic plasticity of AHL-mediated Quorum sensing in environmental strains of Vibrio mediterranei. ( 30116040 )
2018
23
Assessment of the Quorum Sensing Inhibition Activity of a Non-Toxic Chitosan in an N-Acyl Homoserine Lactone (AHL)-Based Escherichia coli Biosensor. ( 30181497 )
2018
24
Diffuse glioblastoma resembling acute hemorrhagic leukoencephalitis. ( 29184769 )
2017
25
Acute hemorrhagic leukoencephalitis after seasonal influenza vaccination. ( 29134580 )
2017
26
HqiA, a novel quorum-quenching enzyme which expands the AHL lactonase family. ( 28424524 )
2017
27
Effects of quorum quenching by AHL lactonase on AHLs, protease, motility and proteome patterns in Aeromonas veronii LP-11. ( 28482205 )
2017
28
Deciphering Physiological Functions of AHL Quorum Quenching Acylases. ( 28674525 )
2017
29
Impact of species delimitation and sampling on niche models and phylogeographical inference: A case study of the East African reed frog Hyperolius substriatus Ahl, 1931. ( 28684366 )
2017
30
Hypersensitive Response of Plasmid-Encoded AHL Synthase Gene to Lifestyle and Nutrient by Ensifer adhaerens X097. ( 28702008 )
2017
31
The first report on Listeria monocytogenes producing siderophores and responds positively to N-acyl homoserine lactone (AHL) molecules by enhanced biofilm formation. ( 28762063 )
2017
32
Membrane fouling induced by AHL-mediated soluble microbial product (SMP) formation by fouling-causing bacteria co-cultured with fouling-enhancing bacteria. ( 28814755 )
2017
33
Acute Hemorrhagic Leukoencephalitis in Children: A Case Report. ( 27217610 )
2016
34
Commentary: Acute Hemorrhagic Leukoencephalitis (Weston-Hurst Syndrome) in a Patient with Relapse-Remitting Multiple Sclerosis. ( 27252706 )
2016
35
Role of gallic and p-coumaric acids in the AHL-dependent expression of flgA gene and in the process of biofilm formation in food-associated Pseudomonas fluorescens KM120. ( 26710926 )
2016
36
Establishing a New Species Encephalitozoon pogonae for the Microsporidian Parasite of Inland Bearded Dragon Pogona vitticeps Ahl 1927 (Reptilia, Squamata, Agamidae). ( 26785360 )
2016
37
Effects of dietary Lactobacillus plantarum and AHL lactonase on the control of Aeromonas hydrophila infection in tilapia. ( 27098117 )
2016
38
AHL, SSD and bimodal CI results in children. ( 27236852 )
2016
39
Non-thermal Plasma Exposure Rapidly Attenuates Bacterial AHL-Dependent Quorum Sensing and Virulence. ( 27242335 )
2016
40
Gene Flow Across Genus Barriers - Conjugation of Dinoroseobacter shibae's 191-kb Killer Plasmid into Phaeobacter inhibens and AHL-mediated Expression of Type IV Secretion Systems. ( 27303368 )
2016
41
Validity and Redescription of Profundulus balsanus Ahl, 1935 (Cyprinodontiformes: Profundulidae). ( 27701203 )
2016
42
Attenuation of Quorum Sensing Regulated Virulence of Pectobacterium carotovorum subsp. carotovorum through an AHL Lactonase Produced by Lysinibacillus sp. Gs50. ( 27911925 )
2016
43
The advertisement calls of <i>Quasipaa</i> <i>shini</i> (Ahl, 1930) (Anura: Dicroglossidae). ( 27988599 )
2016
44
Acute hemorrhagic leukoencephalitis (Weston-Hurst syndrome) in a patient with relapse-remitting multiple sclerosis. ( 26376717 )
2015
45
Identification and analysis of the salt tolerant property of AHL lactonase (AiiATSAWB ) of Bacillus species. ( 25041996 )
2015
46
AHL-type quorum sensing and its regulation on symplasmata formation in Pantoea agglomerans YS19. ( 25283544 )
2015
47
Use of aiiA gene amplification for AHL-lactonase production from endophytic bacterium Enterobacter species. ( 25451751 )
2015
48
Iron limitation enhances acyl homoserine lactone (AHL) production and biofilm formation in clinical isolates of Acinetobacter baumannii. ( 25622119 )
2015
49
Possible Correlation Between Bile Salt Hydrolysis and AHL Deamidation: Staphylococcus epidermidis RM1, a Potent Quorum Quencher and Bile Salt Hydrolase Producer. ( 25800527 )
2015
50
The autoinducer synthases LuxI and AinS are responsible for temperature-dependent AHL production in the fish pathogen Aliivibrio salmonicida. ( 25886758 )
2015

Variations for Acute Hemorrhagic Leukoencephalitis

Expression for Acute Hemorrhagic Leukoencephalitis

Search GEO for disease gene expression data for Acute Hemorrhagic Leukoencephalitis.

Pathways for Acute Hemorrhagic Leukoencephalitis

GO Terms for Acute Hemorrhagic Leukoencephalitis

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