MCID: ANT063
MIFTS: 17

Anti-P200 Pemphigoid

Categories: Rare diseases, Skin diseases

Aliases & Classifications for Anti-P200 Pemphigoid

MalaCards integrated aliases for Anti-P200 Pemphigoid:

Name: Anti-P200 Pemphigoid 59 17

Characteristics:

Orphanet epidemiological data:

59
anti-p200 pemphigoid
Inheritance: Not applicable; Prevalence: <1/1000000 (Worldwide); Age of onset: Adult,Elderly; Age of death: normal life expectancy;

Classifications:

Orphanet: 59  
Rare skin diseases


External Ids:

ICD10 via Orphanet 34 L12.8
Orphanet 59 ORPHA454710

Summaries for Anti-P200 Pemphigoid

MalaCards based summary : Anti-P200 Pemphigoid is related to bullous pemphigoid and epidermolysis bullosa. An important gene associated with Anti-P200 Pemphigoid is LAMC1 (Laminin Subunit Gamma 1). Affiliated tissues include skin, neutrophil and heart.

Related Diseases for Anti-P200 Pemphigoid

Diseases related to Anti-P200 Pemphigoid via text searches within MalaCards or GeneCards Suite gene sharing:

(show all 21)
# Related Disease Score Top Affiliating Genes
1 bullous pemphigoid 11.0
2 epidermolysis bullosa 10.7
3 epidermolysis bullosa acquisita 10.7
4 skin disease 10.5
5 recessive dystrophic epidermolysis bullosa 10.5
6 epidermolysis bullosa dystrophica 10.5
7 ocular cicatricial pemphigoid 10.3
8 dermatitis herpetiformis, familial 10.3
9 dermatitis herpetiformis 10.3
10 pemphigus 10.3
11 autoimmune disease 10.2
12 pemphigus vulgaris, familial 10.2
13 epidermolysis bullosa dystrophica, autosomal recessive 10.2
14 esophagitis 10.2
15 polyneuropathy 10.2
16 pustulosis of palm and sole 10.2
17 bullous skin disease 10.2
18 psoriasis 10.2
19 hypereosinophilic syndrome 10.2
20 linear iga disease 10.2
21 pustular psoriasis 10.2

Graphical network of the top 20 diseases related to Anti-P200 Pemphigoid:



Diseases related to Anti-P200 Pemphigoid

Symptoms & Phenotypes for Anti-P200 Pemphigoid

Drugs & Therapeutics for Anti-P200 Pemphigoid

Interventional clinical trials:


# Name Status NCT ID Phase Drugs
1 Genetic Susceptibility and Influence of the Microbiomae in Bullous Pemphigoid Unknown status NCT02874079

Search NIH Clinical Center for Anti-P200 Pemphigoid

Genetic Tests for Anti-P200 Pemphigoid

Anatomical Context for Anti-P200 Pemphigoid

MalaCards organs/tissues related to Anti-P200 Pemphigoid:

41
Skin, Neutrophil, Heart

Publications for Anti-P200 Pemphigoid

Articles related to Anti-P200 Pemphigoid:

(show top 50) (show all 52)
# Title Authors PMID Year
1
Overlap of Bullous, Anti-Laminin-332, and Anti-p200 Pemphigoid With Concomitant Anti-Contactin-1-Positive Inflammatory Polyneuropathy Treated With Intravenous Immunoglobulins as a Manifestation of Epitope Spreading. 38
30892575 2019
2
[Anti-p200 pemphigoid]. 38
30868255 2019
3
Anti-p200 pemphigoid is the most common pemphigoid disease with serum antibodies against the dermal side by indirect immunofluorescence microscopy on human salt-split skin. 38
30953703 2019
4
Case of anti-p200 pemphigoid accompanying uterine malignancy. 38
29766559 2018
5
Subepidermal autoimmune bullous diseases: overview, epidemiology, and associations. 38
29159697 2018
6
Autoimmune Subepidermal Bullous Diseases of the Skin and Mucosae: Clinical Features, Diagnosis, and Management. 38
28779299 2018
7
Interaction of Psoriasis and Bullous Diseases. 38
30135860 2018
8
Determining the Incidence of Pneumocystis Pneumonia in Patients With Autoimmune Blistering Diseases Not Receiving Routine Prophylaxis. 38
28854309 2017
9
Epidermolysis bullosa acquisita and anti-p200 pemphigoid as major subepidermal autoimmune bullous diseases diagnosed by floor binding on indirect immunofluorescence microscopy using human salt-split skin. 38
28749386 2017
10
Successful treatment of severe anti-p200 pemphigoid in a heart transplant recipient with a single cycle of rituximab. 38
28443302 2017
11
Usefulness of a Simple Immunohistochemical Staining Technique to Differentiate Anti-p200 Pemphigoid From Other Autoimmune Blistering Diseases: A Report of 2 Cases. 38
27095685 2017
12
Clinical and immunological features and outcome of anti-p200 pemphigoid. 38
27037896 2016
13
Laboratory Diagnosis and Clinical Profile of Anti-p200 Pemphigoid. 38
27167149 2016
14
Anti-p200 pemphigoid (anti-laminin-γ1 pemphigoid) demonstrating pathergy. 38
28491985 2015
15
Anti-p200 pemphigoid. 38
24767733 2014
16
Autoimmune blistering dermatoses as systemic diseases. 38
24767184 2014
17
[Anti-p200 pemphigoid: Remission under mycophenolate mofetil (Cellcept®)]. 38
24315224 2013
18
Low sensitivity of type VII collagen enzyme-linked immunosorbent assay in epidermolysis bullosa acquisita: serration pattern analysis on skin biopsy is required for diagnosis. 38
23480491 2013
19
An attempt to develop mouse model for anti-laminin γ1 pemphigoid. 38
23410740 2013
20
Immunoglobulin G deposition to nonhemidesmosomal lamina lucida and early neutrophil involvement are characteristic features in a case of anti-p200 pemphigoid. 38
22963596 2013
21
Sensitive and specific assays for routine serological diagnosis of epidermolysis bullosa acquisita. 38
22341608 2013
22
A long-term study of a patient with anti-p200 pemphigoid: correlation of autoantibody levels with disease activity and an example of epitope spreading. 38
22639938 2012
23
Pemphigoid diseases: pathogenesis, diagnosis, and treatment. 38
21923615 2012
24
Pathogenicity of autoantibodies in anti-p200 pemphigoid. 38
22911854 2012
25
[Anti-p200 pemphigoid: a spectacular response to dapsone]. 38
22078034 2011
26
IgA anti-p200 pemphigoid. 38
22106117 2011
27
Development of a simple enzyme-linked immunosorbent assay for the detection of autoantibodies in anti-p200 pemphigoid. 38
20854435 2011
28
Relapse-associated autoantibodies to BP180 in a patient with anti-p200 pemphigoid. 38
19874345 2010
29
From anti-p200 pemphigoid to anti-laminin gamma1 pemphigoid. 38
20507386 2010
30
Research in practice: diagnosis of subepidermal autoimmune bullous disorders. 38
19192160 2009
31
A case of anti-p200 pemphigoid: evidence for a different pathway in neutrophil recruitment compared with bullous pemphigoid. 38
19077077 2009
32
Anti-laminin gamma-1 pemphigoid. 38
19196964 2009
33
A severe and refractory case of anti-p200 pemphigoid resulting in multiple skin ulcers and scar formation. 38
19060472 2009
34
Anti-p200 pemphigoid associated with annular pustular psoriasis. 38
18573742 2008
35
Metastatic ovarian carcinoma-associated subepidermal blistering disease with autoantibodies to both the p200 dermal antigen and the gamma 2 subunit of laminin 5 showing unusual clinical features. 38
18294311 2008
36
The autoantigen in anti-p200 pemphigoid is synthesized by keratinocytes and fibroblasts and is distinct from nidogen-2. 38
17637825 2008
37
Anti-p200 pemphigoid in a 17-year-old girl successfully treated with systemic corticosteroid and dapsone. 38
17381449 2007
38
Histopathology of anti-p200 pemphigoid. 38
17414431 2007
39
Case of concurrent epidermolysis bullosa acquisita and anti-p200 pemphigoid--how to treat it? 38
17343589 2007
40
Anti-p200 pemphigoid: a novel autoimmune subepidermal blistering disease. 38
17204094 2007
41
Penicillin-induced anti-p200 pemphigoid: an unusual morphology. 38
16955192 2006
42
A case of epidermolysis bullosa acquisita with autoantibody to anti-p200 pemphigoid antigen and exfoliative esophagitis. 38
16707891 2006
43
Subepidermal blistering disease with autoantibodies to both the p200 autoantigen and the alpha3 chain of laminin 5. 38
15858518 2005
44
A case of anti-p200 pemphigoid with autoantibodies against both a novel 200-kD dermal antigen and the 290-kD epidermolysis bullosa acquisita antigen. 38
15316171 2004
45
Two cases of subepidermal blistering disease with anti-p200 or 180-kD bullous pemphigoid antigen associated with psoriasis. 38
15316172 2004
46
[Anti-p200 pemphigoid--a new bullous autoimmune dermatosis]. 38
16281877 2004
47
The autoantigen of anti-p200 pemphigoid is an acidic noncollagenous N-linked glycoprotein of the cutaneous basement membrane. 38
14675190 2003
48
A Korean case of anti-p200 pemphigoid. 38
14584115 2003
49
Immunofluorescence studies using skin sections of recessive dystrophic epidermolysis bullosa patients indicated that the antigen of anti-p200 pemphigoid is not a fragment of type VII collagen. 38
12850304 2003
50
A case of anti-p200 pemphigoid clinically mimicking inflammatory epidermolysis bullosa acquisita. 38
12786845 2003

Variations for Anti-P200 Pemphigoid

Expression for Anti-P200 Pemphigoid

Search GEO for disease gene expression data for Anti-P200 Pemphigoid.

Pathways for Anti-P200 Pemphigoid

GO Terms for Anti-P200 Pemphigoid

Sources for Anti-P200 Pemphigoid

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