MCID: ADT001
MIFTS: 25

Auditory Agnosia

Categories: Ear diseases, Mental diseases, Neuronal diseases

Aliases & Classifications for Auditory Agnosia

MalaCards integrated aliases for Auditory Agnosia:

Name: Auditory Agnosia 12 15 70

Classifications:



External Ids:

Disease Ontology 12 DOID:0060137
UMLS 70 C0234501

Summaries for Auditory Agnosia

Disease Ontology : 12 An agnosia that is a loss of the ability to distinguishing environmental and non-verbal auditory cues including difficulty distinguishing speech from non-speech sounds even though hearing is usually normal.

MalaCards based summary : Auditory Agnosia is related to verbal auditory agnosia and cortical deafness. An important gene associated with Auditory Agnosia is TAGAP (T Cell Activation RhoGTPase Activating Protein), and among its related pathways/superpathways is Synaptic Neurotransmission Pathways: GABAergic Inhibition. Affiliated tissues include brain, temporal lobe and cortex.

Wikipedia : 73 Auditory agnosia is a form of agnosia that manifests itself primarily in the inability to recognize or... more...

Related Diseases for Auditory Agnosia

Diseases related to Auditory Agnosia via text searches within MalaCards or GeneCards Suite gene sharing:

(show top 50) (show all 65)
# Related Disease Score Top Affiliating Genes
1 verbal auditory agnosia 31.8 SRPX2 GABRG2
2 cortical deafness 31.6 PRNP LGI1
3 aphasia 30.7 SRPX2 PRNP
4 landau-kleffner syndrome 30.2 SRPX2 GABRG2
5 speech and communication disorders 29.4 SRPX2 PRNP LGI1
6 phonagnosia 11.1
7 agnosia 10.9
8 branchiootic syndrome 1 10.6
9 epilepsy, focal, with speech disorder and with or without mental retardation 10.3
10 ataxia, combined cerebellar and peripheral, with hearing loss and diabetes mellitus 10.2
11 amusia 10.2
12 encephalitis 10.2
13 anosognosia 10.1
14 visual agnosia 10.1
15 sensorineural hearing loss 10.1
16 germinoma 10.1
17 lactic acidosis 10.1
18 brain injury 10.1
19 traumatic brain injury 10.1
20 alzheimer disease 9.9
21 creutzfeldt-jakob disease 9.9
22 schizophrenia 9.9
23 neural tube defects 9.9
24 macrocephaly/megalencephaly syndrome, autosomal recessive 9.9
25 leigh syndrome 9.9
26 ocular motor apraxia 9.9
27 adrenoleukodystrophy 9.9
28 leber hereditary optic neuropathy, modifier of 9.9
29 frontotemporal lobar degeneration with tdp43 inclusions, grn-related 9.9
30 apraxia 9.9
31 hydrocephalus 9.9
32 hemiplegia 9.9
33 expressive language disorder 9.9
34 nephrotic syndrome 9.9
35 alexia 9.9
36 optic nerve disease 9.9
37 mutism 9.9
38 intracranial embolism 9.9
39 dystonia 9.9
40 herpes simplex 9.9
41 measles 9.9
42 mitochondrial encephalomyopathy 9.9
43 speech disorder 9.9
44 adrenomyeloneuropathy 9.9
45 herpes simplex encephalitis 9.9
46 encephalopathy 9.9
47 megalencephaly 9.9
48 seizure disorder 9.9
49 hereditary optic neuropathy 9.9
50 status epilepticus 9.9 LGI1 GABBR1

Graphical network of the top 20 diseases related to Auditory Agnosia:



Diseases related to Auditory Agnosia

Symptoms & Phenotypes for Auditory Agnosia

Drugs & Therapeutics for Auditory Agnosia

Search Clinical Trials , NIH Clinical Center for Auditory Agnosia

Genetic Tests for Auditory Agnosia

Anatomical Context for Auditory Agnosia

MalaCards organs/tissues related to Auditory Agnosia:

40
Brain, Temporal Lobe, Cortex

Publications for Auditory Agnosia

Articles related to Auditory Agnosia:

(show top 50) (show all 193)
# Title Authors PMID Year
1
Subcortical deafness as a subtype of auditory agnosia after injury of bilateral auditory radiations caused by two cerebrovascular accidents - normal auditory brainstem responses with I-VII waves and abolished consciousness of hearing. 61
33573440 2021
2
Auditory agnosia with anosognosia. 61
33647851 2021
3
Simultaneous auditory agnosia: Systematic description of a new type of auditory segregation deficit following a right hemisphere lesion. 61
33360763 2021
4
Music processing deficits in Landau-Kleffner syndrome: Four case studies in adulthood. 61
32442777 2020
5
Cortical deafness of following bilateral temporal lobe stroke. 61
32386850 2020
6
Auditory Agnosia for Environmental Sounds in Alzheimer's Disease: Not Hearing and Not Listening? 61
31958091 2020
7
Low Heteroplasmy Rates Argue Against the m.3243A>G Variant as the Cause of Auditory Agnosia. 61
31876652 2020
8
Non-fluent/Agrammatic Variant of Primary Progressive Aphasia With Generalized Auditory Agnosia. 61
32676050 2020
9
Central deafness: a review of past and current perspectives. 61
31066317 2019
10
Prominent auditory deficits in primary progressive aphasia: A case study. 61
30878181 2019
11
Late-onset Mitochondrial Encephalopathy, Lactic Acidosis, and Stroke-like Episodes Presenting With Auditory Agnosia. 61
31045719 2019
12
Regression in children with epilepsy. 61
30537476 2019
13
An Uncommon Presentation of Mucopolysaccharidosis Type IIIb. 61
31327975 2019
14
Neuromodulation of Right Auditory Cortex Selectively Increases Activation in Speech-Related Brain Areas in Brainstem Auditory Agnosia. 61
30239465 2018
15
Verbal auditory agnosia in a patient with traumatic brain injury: A case report. 61
29538212 2018
16
Auditory agnosia caused by bilateral putamen haemorrhage. 61
29269367 2017
17
Auditory agnosia associated with bilateral putaminal hemorrhage: A case report of clinical course of recovery. 61
28740065 2017
18
Post traumatic deafness: a pictorial review of CT and MRI findings. 61
27085885 2016
19
Unusual presentations in patients with E200K familial Creutzfeldt-Jakob disease. 61
26806765 2016
20
[Higher Brain Dysfunction in Mitochondrial Myopathy, Encephalopathy, Lactic Acidosis and Stroke-Like Episodes (MELAS)]. 61
26873235 2016
21
Functional Mapping of the Human Auditory Cortex: fMRI Investigation of a Patient with Auditory Agnosia from Trauma to the Inferior Colliculus. 61
26413744 2015
22
Auditory agnosia as a clinical symptom of childhood adrenoleukodystrophy. 61
25544384 2015
23
The mitochondrial DNA 10197 G > A mutation causes MELAS/Leigh overlap syndrome presenting with acute auditory agnosia. 61
24708134 2015
24
Auditory agnosia. 61
25726291 2015
25
Episodic epileptic verbal auditory agnosia in Landau Kleffner syndrome treated with combination diazepam and corticosteroids. 61
24453158 2014
26
[Acquired amusia and musical anhedonia]. 61
24856610 2014
27
Landau-Kleffner syndrome: a study of 29 patients. 61
24315829 2014
28
Auditory dysfunction in patients with cerebrovascular disease. 61
25401133 2014
29
A cardiac cause for deafness. 61
24165506 2013
30
Acquired auditory agnosia in childhood and normal sleep electroencephalography subsequently diagnosed as Landau-Kleffner syndrome: a report of three cases. 61
23121226 2013
31
Auditory agnosia in a patient with nephrotic syndrome. 61
23322309 2013
32
A case of generalized auditory agnosia with unilateral subcortical brain lesion. 61
23342322 2012
33
The speech aversion hypothesis has explanatory power in a Minimal Speech Approach to aloof, non-verbal, severe autism. 61
22004986 2012
34
Changing perspectives on Landau-Kleffner syndrome. 61
21955111 2011
35
Auditory agnosia due to long-term severe hydrocephalus caused by spina bifida - specific auditory pathway versus nonspecific auditory pathway. 61
21413843 2011
36
Benign childhood seizure susceptibility syndrome: three case reports. 61
21628136 2011
37
[A case of transient auditory agnosia and schizophrenia]. 61
21516711 2011
38
Pure word deafness associated with extrapontine myelinolysis. 61
21043052 2010
39
Knowledge and attitudes of allied health professional students regarding the stroke rehabilitation team and the role of the Speech and Language Therapist. 61
20565328 2010
40
Nonverbal auditory agnosia with lesion to Wernicke's area. 61
19698727 2010
41
The assessment of auditory function in CSWS: lessons from long-term outcome. 61
19682057 2009
42
Sign language in Landau-Kleffner syndrome. 61
19682058 2009
43
Pleasurable emotional response to music: a case of neurodegenerative generalized auditory agnosia. 61
19253088 2009
44
An auditory region in the primate insular cortex responding preferentially to vocal communication sounds. 61
19176812 2009
45
Landau-Kleffner syndrome: long-term follow-up. 61
18930363 2009
46
Tone deafness: a model complex cortical phenotype. 61
19149280 2008
47
Acute auditory agnosia as the presenting hearing disorder in MELAS. 61
19011735 2008
48
Electrical status epilepticus in sleep. 61
18555191 2008
49
[Focal brain lesions and language dysfunction]. 61
17966959 2007
50
The perceptions of students in the allied health professions towards stroke rehabilitation teams and the SLP's role. 61
16876816 2007

Variations for Auditory Agnosia

Expression for Auditory Agnosia

Search GEO for disease gene expression data for Auditory Agnosia.

Pathways for Auditory Agnosia

Pathways related to Auditory Agnosia according to GeneCards Suite gene sharing:

# Super pathways Score Top Affiliating Genes
1 9.85 GABRG2 GABBR1

GO Terms for Auditory Agnosia

Cellular components related to Auditory Agnosia according to GeneCards Suite gene sharing:

# Name GO ID Score Top Affiliating Genes
1 dendrite GO:0030425 9.5 PRNP GABRG2 GABBR1
2 GABA-ergic synapse GO:0098982 9.26 GABRG2 GABBR1
3 cell junction GO:0030054 9.26 SRPX2 LGI1 GABRG2 GABBR1
4 extrinsic component of membrane GO:0019898 9.16 PRNP ATG2A
5 synapse GO:0045202 8.92 SRPX2 LGI1 GABRG2 GABBR1

Biological processes related to Auditory Agnosia according to GeneCards Suite gene sharing:

# Name GO ID Score Top Affiliating Genes
1 regulation of postsynaptic membrane potential GO:0060078 8.96 GABRG2 GABBR1
2 gamma-aminobutyric acid signaling pathway GO:0007214 8.62 GABRG2 GABBR1

Sources for Auditory Agnosia

3 CDC
7 CNVD
9 Cosmic
10 dbSNP
11 DGIdb
17 EFO
18 ExPASy
19 FMA
20 GARD
28 GO
29 GTR
30 HMDB
31 HPO
32 ICD10
33 ICD10 via Orphanet
34 ICD9CM
35 IUPHAR
36 KEGG
37 LifeMap
39 LOVD
41 MedGen
44 MeSH
45 MESH via Orphanet
46 MGI
49 NCI
50 NCIt
51 NDF-RT
53 NINDS
54 Novoseek
56 OMIM via Orphanet
57 OMIM® (Updated 20-May-2021)
61 PubMed
63 QIAGEN
68 SNOMED-CT via HPO
69 Tocris
70 UMLS
71 UMLS via Orphanet
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