MCID: CNT031
MIFTS: 31

Central Epithelioid Sarcoma

Categories: Cancer diseases, Rare diseases

Aliases & Classifications for Central Epithelioid Sarcoma

MalaCards integrated aliases for Central Epithelioid Sarcoma:

Name: Central Epithelioid Sarcoma 12 15
Proximal-Type Epithelioid Sarcoma 71

Classifications:



External Ids:

Disease Ontology 12 DOID:7492
NCIt 49 C27472
UMLS 71 C1335563

Summaries for Central Epithelioid Sarcoma

MalaCards based summary : Central Epithelioid Sarcoma, also known as proximal-type epithelioid sarcoma, is related to central nervous system angiosarcoma and vulvar sarcoma. An important gene associated with Central Epithelioid Sarcoma is SMARCB1 (SWI/SNF Related, Matrix Associated, Actin Dependent Regulator Of Chromatin, Subfamily B, Member 1), and among its related pathways/superpathways are Cytoskeletal Signaling and Keratinization. Affiliated tissues include breast, lung and thymus, and related phenotype is Reduced mammosphere formation.

Related Diseases for Central Epithelioid Sarcoma

Diseases in the Epithelioid Sarcoma family:

Central Epithelioid Sarcoma Adult Epithelioid Sarcoma

Diseases related to Central Epithelioid Sarcoma via text searches within MalaCards or GeneCards Suite gene sharing:

(showing 398, show less)
# Related Disease Score Top Affiliating Genes
1 central nervous system angiosarcoma 10.6 SMARCB1 CD34
2 vulvar sarcoma 10.6 SMARCB1 CD34
3 glomangioma 10.6 VIM CD34
4 retroperitoneal leiomyosarcoma 10.6 SMARCB1 CD34
5 alk+ histiocytosis 10.6 CD207 CD1A
6 melanotic neurilemmoma 10.5 SMARCB1 CD34
7 glomangiomyoma 10.5 VIM CD34
8 pediatric liposarcoma 10.5 VIM CD34
9 mesenchymoma 10.5 MB CD34
10 epithelioid malignant peripheral nerve sheath tumor 10.5 SMARCB1 CD34
11 verruciform xanthoma of skin 10.5 CD1E CD1A
12 retroperitoneal sarcoma 10.5 SMARCB1 CD34
13 gallbladder leiomyosarcoma 10.5 MB CD34
14 lung leiomyosarcoma 10.5 KRT5 CD34
15 multifocal motor neuropathy 10.5 CD1E CD1A
16 spermatic cord cancer 10.4 KRT5 CD34
17 angiolipoma 10.4 VIM CD34
18 ovarian solid teratoma 10.4 TNFRSF8 CD34
19 kidney rhabdoid cancer 10.4 SMARCB1 MB
20 esophagus sarcoma 10.4 KRT5 CD34
21 multicentric reticulohistiocytosis 10.4 VIM CD1E
22 interstitial pneumonitis, desquamative, familial 10.4 CD1E CD1A
23 thymus adenocarcinoma 10.4 KRT5 KRT20
24 testicular fibroma 10.4 KRT5 CD34
25 spindle cell lipoma 10.4 VIM CD34
26 central nervous system fibrosarcoma 10.4 KRT7 CD34
27 liposarcoma of bone 10.4 TNFRSF8 CD34
28 breast myofibroblastoma 10.4 MME CD34
29 breast hemangiopericytoma 10.4 KRT7 CD34
30 neurilemmoma 10.4 VIM SMARCB1 CD34
31 nephrogenic adenofibroma 10.4 KRT7 CD34
32 pacinian tumor 10.4 MME CD34
33 urethral villous adenoma 10.4 KRT7 KRT20
34 malignant mesenchymoma 10.4 MB CD34
35 pancreatic serous cystadenocarcinoma 10.4 KRT7 KRT20
36 intrahepatic bile duct adenoma 10.4 KRT7 KRT20
37 seminal vesicle adenocarcinoma 10.4 KRT7 KRT20
38 liver fibroma 10.3 VIM KRT5
39 gastric signet ring cell adenocarcinoma 10.3 KRT7 KRT20
40 lichen nitidus 10.3 CD1E CD1B CD1A
41 cortical thymoma 10.3 CD1E CD1B CD1A
42 breast leiomyoma 10.3 MME CD34
43 atrophic vulva 10.3 KRT7 KRT20
44 dendritic cell thymoma 10.3 CD1E CD1B CD1A
45 bladder lymphoma 10.3 MME KRT20
46 urinary bladder villous adenoma 10.3 KRT7 KRT20
47 cystitis cystica 10.3 KRT7 KRT20
48 histiocytoid hemangioma 10.3 TNFRSF8 CD34
49 bile duct cystadenocarcinoma 10.3 KRT7 KRT20
50 inflammatory liposarcoma 10.3 MME CD34
51 vulva adenocarcinoma 10.3 KRT7 KRT20
52 folliculitis 10.3 CD1E CD1B CD1A
53 jejunal adenocarcinoma 10.3 KRT7 KRT20
54 eyelid carcinoma 10.3 KRT7 KRT20
55 mucinous ovarian cystadenoma 10.3 KRT7 KRT20
56 myoepithelioma 10.3 VIM SMARCB1 KRT18
57 transverse colon cancer 10.3 KRT7 KRT20
58 central nervous system leukemia 10.3 MME CD34
59 jejunal cancer 10.3 KRT7 KRT20
60 cervical polyp 10.3 MME CD34
61 myofibroma 10.3 MB CD34 CD1A
62 malignant syringoma 10.3 KRT7 KRT20
63 pericardial mesothelioma 10.3 VIM KRT5
64 liver sarcoma 10.3 KRT7 CD34
65 langerhans cell histiocytosis 10.3 CD207 CD1C CD1A
66 papillary transitional carcinoma 10.3 KRT7 KRT20
67 proliferating trichilemmal cyst 10.3 KRT7 KRT18
68 ovarian brenner tumor 10.3 KRT7 KRT20
69 skin benign neoplasm 10.3 KRT5 KRT20 CD34
70 sclerosing hepatic carcinoma 10.3 MME CD34
71 heart lymphoma 10.3 VIM MME
72 infantile myofibromatosis 10.3 VIM MB CD34
73 benign metastasizing leiomyoma 10.3 VIM KRT7
74 cervical adenoid cystic carcinoma 10.3 KRT7 CD1C
75 linitis plastica 10.3 KRT7 KRT20
76 sarcomatous intrahepatic cholangiocarcinoma 10.3 KRT7 CD34
77 acute t cell leukemia 10.3 CD34 CD1E CD1B
78 mucinous stomach adenocarcinoma 10.2 KRT7 KRT20
79 liposarcoma 10.2 VIM MB CD34
80 aortic malignant tumor 10.2 KRT7 KRT20 CD34
81 colonic lymphangioma 10.2 KRT7 KRT20 CD34
82 synovium cancer 10.2 SMARCB1 KRT7 CD34
83 ovarian mucinous neoplasm 10.2 KRT7 KRT20
84 thyroid angiosarcoma 10.2 KRT7 KRT20 CD34
85 inverted transitional papilloma 10.2 KRT7 KRT5
86 leprosy 3 10.2 CD1E CD1C CD1B
87 malignant giant cell tumor of soft parts 10.2 MB CD34
88 malignant spiradenoma 10.2 KRT7 KRT5
89 ceruminoma 10.2 KRT7 KRT5
90 intrahepatic gall duct cancer 10.2 KRT7 KRT18
91 ureter adenocarcinoma 10.2 KRT7 KRT5
92 benign breast adenomyoepithelioma 10.2 KRT7 KRT5
93 breast adenomyoepithelioma 10.2 KRT7 KRT5
94 epiglottis cancer 10.2 CD34 CD1D
95 central nervous system sarcoma 10.2 SMARCB1 CD1E CD1B CD1A
96 bone leiomyosarcoma 10.2 KRT7 KRT5
97 microinvasive cervical squamous cell carcinoma 10.2 KRT7 KRT5
98 malignant fibroxanthoma 10.2 VIM TNFRSF8 CD34
99 dendritic cell tumor 10.2 VIM KRT20 CD207 CD1A
100 malignant histiocytosis 10.2 TNFRSF8 CD1E CD1A
101 ceruminous adenocarcinoma 10.2 KRT7 KRT5
102 reticulum cell sarcoma 10.2 VIM TNFRSF8
103 external ear carcinoma 10.2 KRT7 KRT5
104 cervix erosion 10.2 MME KRT5
105 intestinal obstruction 10.2 KRT7 KRT20 CD34
106 gastric squamous cell carcinoma 10.2 KRT7 KRT5
107 mite infestation 10.2 TNFRSF8 CD1B CD1A
108 breast myoepithelial neoplasm 10.2 KRT7 KRT5
109 bladder leiomyoma 10.2 VIM KRT7 CD34
110 odontoma 10.2 VIM KRT5 KRT18
111 warthin tumor 10.2 KRT7 KRT18
112 angiosarcoma 10.2 VIM KRT7 CD34
113 juvenile xanthogranuloma 10.2 PMEL CD1E CD1B CD1A
114 epithelial-myoepithelial carcinoma 10.2 VIM SMARCB1 KRT7
115 fibroma 10.2 VIM KRT7 CD34
116 necrotizing sialometaplasia 10.2 KRT7 KRT5
117 rete testis neoplasm 10.2 TNFRSF8 KRT7
118 monophasic synovial sarcoma 10.2 VIM KRT7 CD34
119 rete testis adenocarcinoma 10.2 TNFRSF8 KRT7
120 conventional fibrosarcoma 10.2 TNFRSF8 MB CD34
121 bile duct mucoepidermoid carcinoma 10.2 KRT7 KRT5
122 cutaneous fibrous histiocytoma 10.2 VIM MME CD34
123 spindle cell sarcoma 10.2 VIM KRT7 CD34
124 breast metaplastic carcinoma 10.2 KRT7 KRT5
125 parachordoma 10.2 VIM KRT7
126 breast mucinous carcinoma 10.2 KRT7 KRT5
127 cystitis 10.2 VIM KRT7 KRT20
128 smooth muscle tumor 10.2 VIM MME CD34
129 epithelioid trophoblastic tumor 10.1 KRT7 KRT18
130 pericardium disease 10.1 TNFRSF8 MB CD34
131 bile duct adenoma 10.1 VIM KRT7 KRT20
132 bone lymphoma 10.1 TNFRSF8 MME
133 middle ear adenocarcinoma 10.1 KRT7 KRT5
134 lung meningioma 10.1 SYP CD34
135 glomangiosarcoma 10.1 SYP CD34
136 mucinous cystadenocarcinoma 10.1 VIM KRT7 KRT20
137 pericardium cancer 10.1 KRT7 KRT5
138 endocervical adenocarcinoma 10.1 VIM KRT7 KRT20
139 lung lymphoma 10.1 TNFRSF8 MME
140 t-cell/histiocyte rich large b cell lymphoma 10.1 TNFRSF8 MME
141 eccrine acrospiroma 10.1 KRT7 KRT5
142 breast lymphoma 10.1 TNFRSF8 MME
143 lung acinar adenocarcinoma 10.1 KRT7 KRT20
144 wolffian duct adenoma 10.1 MME KRT7
145 large cell acanthoma 10.1 KRT7 KRT5
146 breast leiomyosarcoma 10.1 MB KRT7 CD34
147 appendix disease 10.1 KRT7 KRT20
148 mammary paget's disease 10.1 KRT7 KRT20 KRT18
149 mucinous adenocarcinoma 10.1 VIM KRT7 KRT20
150 benign perivascular tumor 10.1 SYP CD34
151 glycogen-rich clear cell breast carcinoma 10.1 SYP KRT20
152 mixed epithelial stromal tumour 10.1 MME KRT7
153 encapsulated thymoma 10.1 CD1E CD1C CD1B CD1A
154 precursor lymphoblastic lymphoma/leukemia 10.1 CD1E CD1C CD1B CD1A
155 cervical adenoma malignum 10.1 MME KRT7
156 sarcomatoid squamous cell skin carcinoma 10.1 MME KRT5 CD34
157 skin sarcoidosis 10.1 CD1E CD1C CD1B CD1A
158 metatypical basal cell carcinoma 10.1 KRT7 KRT5 CD34
159 interdigitating dendritic cell sarcoma 10.1 CD1E CD1C CD1B CD1A
160 benign mesothelioma 10.1 KRT7 KRT5 CD34
161 gray zone lymphoma 10.1 TNFRSF8 MME
162 thymus lipoma 10.1 MB KRT20 CD1B CD1A
163 epididymal neoplasm 10.1 MME KRT7
164 immune system organ benign neoplasm 10.1 MB KRT20 CD1B CD1A
165 benign mesenchymoma 10.1 KRT7 KRT5 CD34
166 breast malignant phyllodes tumor 10.1 MME KRT5 CD34
167 erdheim-chester disease 10.1 CD1E CD1C CD1B CD1A
168 diabetes insipidus, neurohypophyseal 10.1 CD1E CD1C CD1B CD1A
169 ovarian wilms' cancer 10.1 MME KRT7
170 esophageal adenosquamous carcinoma 10.1 KRT7 KRT5
171 clear cell papillary renal cell carcinoma 10.1 MME KRT7
172 heart cancer 10.1 KRT7 KRT5 CD34
173 histiocytoma 10.1 VIM MB CD34 CD1A
174 chromophil adenoma of the kidney 10.1 MME KRT7
175 vulvar apocrine adenocarcinoma 10.1 KRT7 KRT5 KRT20
176 metanephric adenoma 10.1 VIM KRT7 KRT18
177 eccrine sweat gland cancer 10.1 KRT7 KRT5 KRT20
178 pleomorphic carcinoma 10.1 VIM KRT7 KRT18
179 thymus clear cell carcinoma 10.1 KRT7 KRT5 KRT20
180 primary hepatic neuroendocrine carcinoma 10.1 VIM SYP
181 gastrointestinal lymphoma 10.1 TNFRSF8 MME
182 clear cell basal cell carcinoma 10.1 KRT7 KRT5 KRT20
183 urethra clear cell adenocarcinoma 10.1 KRT7 KRT5 KRT20
184 schwannoma of twelfth cranial nerve 10.1 SMARCB1 KRT7
185 borst-jadassohn intraepidermal carcinoma 10.1 KRT7 KRT5 KRT20
186 wolffian duct adenocarcinoma 10.1 MME KRT7
187 paget disease, extramammary 10.1 KRT7 KRT5 KRT20
188 papillary tumor of the pineal region 10.1 VIM SYP
189 nodular medulloblastoma 10.1 SYP SMARCB1
190 inverted papilloma 10.0 KRT7 KRT5 KRT20
191 cystadenofibroma 10.0 MME KRT7
192 intratubular embryonal carcinoma 10.0 TNFRSF8 KRT7 KRT20
193 esophageal adenoid cystic carcinoma 10.0 VIM SYP
194 adenosarcoma 10.0 VIM MME MB
195 prostate stromal sarcoma 10.0 SYP CD34
196 extraosseous chondrosarcoma 10.0 SYP SMARCB1 CD34
197 angiocentric glioma 10.0 VIM SYP
198 eccrine porocarcinoma 10.0 VIM KRT7 KRT5
199 micronodular basal cell carcinoma 10.0 MME KRT5
200 malignant peripheral nerve sheath tumor 10.0 VIM SMARCB1 KRT7 CD34
201 marginal zone b-cell lymphoma 10.0 TNFRSF8 TNFAIP3 MME
202 chordoma 10.0 VIM SMARCB1 KRT7
203 papillary cystadenocarcinoma 10.0 KRT7 KRT20
204 adenomatoid tumor 10.0 VIM KRT7 KRT5
205 cutaneous ganglioneuroma 10.0 SYP KRT20 CD34
206 histiocytosis 10.0 TNFRSF8 CD207 CD1C CD1A
207 adult mesoblastic nephroma 10.0 MME KRT7 CD34
208 pediatric lymphoma 10.0 TNFRSF8 MME
209 chondrosarcoma, extraskeletal myxoid 10.0 SYP SMARCB1 CD34
210 nephrogenic adenoma of urinary bladder 10.0 MME KRT7 KRT20
211 renal adenoma 10.0 MME KRT7
212 breast sarcoma 10.0 MME CD34
213 composite lymphoma 10.0 TNFRSF8 MME
214 female urethral cancer 10.0 MME KRT7 KRT20
215 glandular cystitis 10.0 MME KRT7 KRT20
216 pancreatic mucinous cystadenoma 10.0 MME KRT7 KRT20
217 squamous papillomatosis 10.0 MME KRT7 KRT20
218 bladder clear cell adenocarcinoma 10.0 MME KRT7 KRT20
219 vulva basal cell carcinoma 10.0 SYP KRT5
220 cloacogenic carcinoma 10.0 SYP KRT5
221 breast papillary carcinoma 10.0 SYP KRT5
222 primary cutaneous amyloidosis 10.0 KRT7 KRT5 KRT18
223 rhabdoid meningioma 9.9 VIM SYP SMARCB1
224 myoepithelial carcinoma 9.9 VIM SMARCB1 KRT7 KRT18
225 orbital cancer 9.9 CD34 CD1E CD1C CD1B CD1A
226 ependymoblastoma 9.9 VIM SYP SMARCB1
227 chordoid meningioma 9.9 VIM SYP CD34
228 medullomyoblastoma 9.9 SYP MB
229 rhabdoid tumor predisposition syndrome 1 9.9 VIM SYP SMARCB1
230 seborrheic dermatitis 9.9 CD207 CD1E CD1C CD1B CD1A
231 endometrial clear cell adenocarcinoma 9.9 MME KRT7
232 pineal gland cancer 9.9 SYP SMARCB1 KRT18
233 adult lymphoma 9.9 TNFRSF8 MME
234 glomus tumor 9.9 VIM SYP CD34
235 extraosseous ewings sarcoma-primitive neuroepithelial tumor 9.9 TNFRSF8 SYP
236 hemangiopericytoma, malignant 9.9 VIM SYP CD34
237 adenofibroma 9.9 VIM MME KRT7
238 ovary neuroendocrine neoplasm 9.9 SYP KRT7
239 atypical teratoid rhabdoid tumor 9.9 VIM SYP SMARCB1
240 endometrial transitional cell carcinoma 9.9 SYP KRT7
241 mycosis fungoides 9.9 TNFRSF8 CD1C CD1B CD1A
242 renal oncocytoma 9.9 VIM MME KRT7
243 extraskeletal ewing sarcoma 9.9 VIM SYP
244 mycobacterium tuberculosis 1 9.9 TNFRSF8 CD1C CD1B CD1A
245 angiomyolipoma 9.9 VIM MME KRT7
246 lung combined type small cell carcinoma 9.9 SYP MME
247 mucinous adenofibroma 9.9 SYP KRT7
248 anaplastic ependymoma 9.9 VIM SYP
249 muscle cancer 9.9 SYP MB CD34
250 ductal carcinoma in situ 9.9 MME KRT5 KRT18
251 rectum neuroendocrine neoplasm 9.9 SYP KRT7
252 neurofibroma 9.9 VIM SYP CD34
253 auditory system cancer 9.9 SYP KRT7
254 ganglioglioma 9.9 VIM SYP SMARCB1
255 lymphatic system cancer 9.9 TNFRSF8 MME CD34 CD1E
256 subareolar duct papillomatosis 9.9 MME KRT7 KRT5
257 nipple neoplasm 9.9 MME KRT7 KRT5
258 clear cell hidradenoma 9.9 MME KRT7 KRT5
259 lymphoma, mucosa-associated lymphoid type 9.8 TNFRSF8 TNFAIP3 MME
260 gliofibroma 9.8 SYP CD34
261 eccrine sweat gland neoplasm 9.8 MME KRT7 KRT5
262 epididymis adenocarcinoma 9.8 MME KRT7 KRT5
263 epididymis cancer 9.8 MME KRT7 KRT5
264 pulmonary artery leiomyosarcoma 9.8 MME KRT7 KRT20 CD34
265 ovarian germ cell teratoma 9.8 SYP KRT7
266 olfactory neuroblastoma 9.8 VIM SYP MB
267 mesothelioma, malignant 9.8 VIM KRT7 KRT5 KRT20
268 clear cell meningioma 9.8 VIM SYP SMARCB1 CD34
269 dermis tumor 9.8 MME CD34 CD1E CD1B CD1A
270 adenoid cystic carcinoma 9.8 VIM KRT7 KRT5 KRT20
271 biliary tract benign neoplasm 9.8 SYP KRT7
272 benign peritoneal mesothelioma 9.8 KRT7 KRT5
273 keratosis, seborrheic 9.8 KRT5 CD1E CD1C CD1B CD1A
274 vaginal endometrial stromal sarcoma 9.8 SYP MME CD34
275 mucinous tubular and spindle renal cell carcinoma 9.8 MME KRT7 KRT18 CD34
276 endobronchial leiomyoma 9.8 SYP MME CD34
277 vagina sarcoma 9.8 SYP MME CD34
278 papilloma of choroid plexus 9.8 SYP SMARCB1 KRT7
279 bladder benign neoplasm 9.8 VIM MME KRT7 KRT20
280 ovarian large-cell neuroendocrine carcinoma 9.8 SYP KRT7 KRT20
281 small cell carcinoma of the bladder 9.8 SYP KRT7 KRT20
282 urinary bladder small cell neuroendocrine carcinoma 9.8 SYP KRT7 KRT20
283 krukenberg carcinoma 9.8 SYP KRT7 KRT20
284 vaginal tubulovillous adenoma 9.8 SYP KRT7 KRT20
285 vaginal adenoma 9.8 SYP KRT7 KRT20
286 vaginal benign neoplasm 9.8 SYP KRT7 KRT20
287 appendix adenocarcinoma 9.8 SYP KRT7 KRT20
288 uterus leiomyosarcoma 9.8 TNFRSF8 KRT7 KRT5 CD34
289 alveolar soft part sarcoma 9.8 VIM SYP MB
290 prostate neuroendocrine neoplasm 9.8 SYP KRT7 KRT20
291 horseshoe kidney 9.7 SYP KRT7 KRT20
292 benign teratoma 9.7 SYP KRT7 KRT20
293 skeletal muscle cancer 9.7 SYP SMARCB1 MB CD34
294 basaloid squamous cell carcinoma 9.7 SYP KRT7 KRT20
295 bone benign neoplasm 9.7 SYP CD1E CD1B CD1A
296 lung benign neoplasm 9.7 SYP KRT7 KRT20
297 cholangiocarcinoma 9.7 MME KRT7 KRT20 KRT18
298 middle ear carcinoma 9.7 SYP KRT5
299 adenoid squamous cell carcinoma 9.7 VIM KRT7 KRT5 KRT20 CD34
300 thoracic benign neoplasm 9.7 MME KRT7 KRT5 CD34
301 breast benign neoplasm 9.7 MME KRT7 KRT5 CD34
302 papillary carcinoma 9.7 SYP KRT7 KRT20
303 polyclonal hypergammaglobulinemia 9.7 MME CD1E CD1C CD1B CD1A
304 granulosa cell tumor of the ovary 9.7 VIM SYP KRT7
305 chordoid glioma 9.7 VIM SYP KRT7
306 perivascular epithelioid cell tumor 9.7 VIM SYP MME
307 nephrogenic adenoma of the urethra 9.7 MME KRT7 KRT5 KRT20
308 gastrointestinal stromal tumor 9.7 VIM SYP SMARCB1 CD34
309 urethral benign neoplasm 9.7 MME KRT7 KRT5 KRT20
310 sarcoma, synovial 9.7 VIM TNFRSF8 SMARCB1 KRT7 CD34
311 subleukemic leukemia 9.7 TNFRSF8 SYP MB
312 sertoli-leydig cell tumor 9.7 VIM SYP KRT7
313 breast osteosarcoma 9.7 MME KRT7 KRT5 KRT20
314 sertoli cell tumor 9.7 VIM SYP KRT7
315 merkel cell carcinoma 9.7 SYP KRT7 KRT20
316 fibrolamellar carcinoma 9.7 VIM SYP KRT7
317 tracheal lymphoma 9.7 TNFRSF8 MME
318 glomangiomatosis 9.7 SYP MB KRT18 CD34
319 carcinosarcoma 9.6 VIM MME MB KRT7
320 hidradenoma 9.6 VIM MME KRT7 KRT5
321 malignant histiocytic disease 9.6 CD1E CD1D CD1C CD1B CD1A
322 mycobacterium malmoense 9.6 CD1E CD1D CD1C CD1B CD1A
323 precursor t-lymphoblastic lymphoma/leukemia 9.6 CD1E CD1D CD1C CD1B CD1A
324 rhinoscleroma 9.6 CD1E CD1D CD1C CD1B CD1A
325 spongiotic dermatitis 9.6 CD1E CD1D CD1C CD1B CD1A
326 middle ear adenoma 9.6 SYP KRT7 KRT5
327 inflamed seborrheic keratosis 9.6 CD1E CD1D CD1C CD1B CD1A
328 collecting duct carcinoma 9.6 VIM SMARCB1 MME KRT7 KRT20
329 sensory organ benign neoplasm 9.6 SYP KRT7 KRT5
330 lichen disease 9.6 CD1E CD1D CD1C CD1B CD1A
331 lymphoid interstitial pneumonia 9.6 CD1E CD1D CD1C CD1B CD1A
332 laryngeal small cell carcinoma 9.6 SYP KRT7 KRT5
333 papillary squamous carcinoma 9.6 SYP KRT7 KRT5
334 jejunal neoplasm 9.6 SYP KRT7 KRT20 CD34
335 cutaneous adenocystic carcinoma 9.6 MME KRT7 KRT5 KRT18
336 endobronchial lipoma 9.6 SYP KRT7 KRT5
337 mature teratoma 9.6 TNFRSF8 SYP KRT7
338 sweat gland neoplasm 9.6 SMARCB1 MME KRT7 KRT5 CD34
339 mesenchymal chondrosarcoma 9.6 VIM SYP SMARCB1 KRT7
340 skin disease 9.6 VIM TNFRSF8 KRT5 CD1C CD1A
341 cerebrovascular benign neoplasm 9.6 SYP SMARCB1 KRT7 KRT18
342 hemangioblastoma 9.5 VIM SYP MME CD34
343 cell type benign neoplasm 9.5 SYP KRT7 CD34
344 wilms tumor 1 9.5 SYP SMARCB1 KRT7 CD34
345 thymic carcinoma 9.5 SYP KRT7 KRT20 KRT18
346 neuroendocrine carcinoma 9.5 SYP KRT7 KRT20 KRT18
347 small cell carcinoma 9.5 SYP KRT7 KRT20 KRT18
348 chromophobe renal cell carcinoma 9.5 VIM MME KRT7 KRT20 KRT18
349 cystic teratoma 9.5 SYP KRT7 KRT20 KRT18
350 large cell neuroendocrine carcinoma 9.5 SYP KRT7 KRT20 KRT18
351 small cell cancer of the lung 9.5 SYP KRT7 KRT20 KRT18
352 lymphoepithelioma-like carcinoma 9.5 TNFRSF8 KRT7 KRT5 KRT20 KRT18
353 peripheral t-cell lymphoma 9.5 TNFRSF8 MME CD1D
354 keratinizing squamous cell carcinoma 9.5 SYP SMARCB1 KRT7 KRT5
355 respiratory system benign neoplasm 9.5 SYP KRT7 KRT5 CD34
356 ovarian sex-cord stromal tumor 9.5 MME KRT7
357 reticulohistiocytic granuloma 9.5 CD207 CD1E CD1D CD1C CD1B CD1A
358 non-langerhans-cell histiocytosis 9.5 CD207 CD1E CD1D CD1C CD1B CD1A
359 cystic basal cell carcinoma 9.5 SYP KRT7 KRT5 KRT20
360 sweat gland cancer 9.5 SYP KRT7 KRT5 KRT20
361 large cell carcinoma 9.4 SYP KRT7 KRT5 KRT20
362 lymphoepithelioma-like thymic carcinoma 9.4 TNFRSF8 SYP KRT5 KRT18
363 epithelioid sarcoma 9.4 VIM SYP SMARCB1 KRT7 CD34
364 papillary adenoma 9.4 VIM SYP KRT7 KRT5
365 medulloepithelioma 9.4 VIM SYP SMARCB1 KRT7 KRT20
366 granuloma annulare 9.4 VIM CD1E CD1D CD1C CD1B CD1A
367 ewing sarcoma 9.4 VIM TNFRSF8 SYP CD34
368 thymus cancer 9.4 KRT7 KRT5 CD1E CD1C CD1B CD1A
369 cardiovascular cancer 9.4 SYP MME KRT7 CD34
370 vascular cancer 9.4 SYP MME KRT7 CD34
371 bladder lateral wall cancer 9.4 SYP MME KRT7 KRT20
372 adenosquamous carcinoma 9.4 SYP KRT7 KRT5 KRT18
373 tubular adenocarcinoma 9.4 SYP MME KRT7 KRT20
374 cystadenoma 9.4 SYP MME KRT7 KRT20
375 suppression of tumorigenicity 12 9.4 SYP KRT7 KRT5 KRT18
376 epithelioid cell synovial sarcoma 9.3 SYP KRT7 CD34 CD1D
377 adult xanthogranuloma 9.3 CD34 CD207 CD1E CD1D CD1C CD1B
378 thymus gland disease 9.3 KRT5 CD1E CD1D CD1C CD1B CD1A
379 renal cell carcinoma, nonpapillary 9.3 VIM PMEL MME KRT7 KRT20 KRT18
380 pleomorphic rhabdomyosarcoma 9.3 SYP MME MB KRT7
381 eccrine papillary adenocarcinoma 9.2 SYP MME KRT7 KRT5
382 nasal cavity olfactory neuroblastoma 9.2 SYP MME KRT7 KRT5
383 meningioma, familial 9.2 SYP SMARCB1 CD34 CD1E CD1C CD1B
384 teratoma 9.2 VIM SYP SMARCB1 KRT7 KRT20 KRT18
385 mediastinal cancer 9.1 TNFRSF8 SYP KRT7 KRT5 CD34
386 langerhans cell sarcoma 9.1 TNFRSF8 CD207 CD1E CD1D CD1C CD1B
387 histiocytic and dendritic cell cancer 9.1 TNFRSF8 CD207 CD1E CD1D CD1C CD1B
388 lung clear cell carcinoma 9.1 SYP MB KRT7 KRT5 KRT18
389 spindle cell carcinoma 9.0 VIM SYP KRT7 KRT5 KRT18 CD34
390 basal cell carcinoma 8.9 SYP MME KRT7 KRT5 KRT20 CD34
391 oncocytoma 8.9 VIM SYP MME KRT7 KRT20 KRT18
392 cavernous hemangioma 8.9 VIM SYP MB KRT7 KRT20 KRT18
393 exophthalmos 8.8 SYP CD34 CD1E CD1D CD1C CD1B
394 mixed cell type cancer 8.7 TNFRSF8 SYP MME KRT7 KRT5 CD34
395 lymphatic system disease 8.6 TNFRSF8 MME CD34 CD207 CD1E CD1D
396 balloon cell malignant melanoma 8.5 MME KRT7 KRT5 CD1E CD1D CD1C
397 leber congenital amaurosis 7.5 TNFRSF8 SYP MME KRT7 KRT20 CD34
398 vulvar proximal-type epithelioid sarcoma 5.8 VIM TNFRSF8 TNFAIP3 SYP SMARCB1 PMEL

Graphical network of the top 20 diseases related to Central Epithelioid Sarcoma:



Diseases related to Central Epithelioid Sarcoma

Symptoms & Phenotypes for Central Epithelioid Sarcoma

GenomeRNAi Phenotypes related to Central Epithelioid Sarcoma according to GeneCards Suite gene sharing:

26 (showing 1, show less)
# Description GenomeRNAi Source Accession Score Top Affiliating Genes
1 Reduced mammosphere formation GR00396-S 9.17 CD1A CD1D CD34 KRT18 KRT7 SMARCB1

Drugs & Therapeutics for Central Epithelioid Sarcoma

Search Clinical Trials , NIH Clinical Center for Central Epithelioid Sarcoma

Genetic Tests for Central Epithelioid Sarcoma

Anatomical Context for Central Epithelioid Sarcoma

MalaCards organs/tissues related to Central Epithelioid Sarcoma:

40
Breast, Lung, Thymus, Skin, Bone, Liver, Appendix

Publications for Central Epithelioid Sarcoma

Articles related to Central Epithelioid Sarcoma:

(showing 75, show less)
# Title Authors PMID Year
1
Epithelioid sarcoma of paratesticular region: A case report of an unusual case. 61
30971563 2019
2
Proximal-Type Epithelioid Sarcoma in Skull Base: a Pathological Diagnosis Challenge with Other Intracranial Tumors. 61
29076075 2019
3
Proximal-type epithelioid sarcoma of the oral cavity: a case report and literature review. 61
30087080 2018
4
Ultrasonography findings of proximal-type epithelioid sarcoma of the vulva: A case report. 61
30345044 2018
5
Proximal-type epithelioid sarcoma of the vulva: Cytopathological diagnosis of a rare neoplasm. 61
29683530 2018
6
Immunohistochemical Biomarkers of Mesenchymal Neoplasms in Endocrine Organs: Diagnostic Pitfalls and Recent Discoveries. 61
29340997 2018
7
Expression of CD34 and β-Catenin in Malignant Rhabdoid Tumor of the Liver Mimicking Proximal-Type Epithelioid Sarcoma. 61
28683521 2018
8
Clinicopathological analysis of myxoid proximal-type epithelioid sarcoma. 61
29068073 2018
9
Myoepithelial carcinoma or epithelioid sarcoma - A rare diagnosis with poor prognosis. A case report and review of literature. 61
30053614 2018
10
Proximal-Type Epithelioid Sarcoma: Report of an Unusual Case in the Uterine Cervix. 61
28381140 2017
11
Secondary EWSR1 gene abnormalities in SMARCB1-deficient tumors with 22q11-12 regional deletions: Potential pitfalls in interpreting EWSR1 FISH results. 61
27218413 2016
12
Osteoclast-rich, proximal-type epithelioid sarcoma: clinicopathologic features of 3 unusual cases expanding the histomorphological spectrum. 61
27040929 2016
13
Proximal-type epithelioid sarcoma: a new case report and literature review. 61
27800093 2016
14
Fine-needle-aspiration cytology of a proximal type epithelioid sarcoma: A case report. 61
26138930 2015
15
Malignant extra-renal rhabdoid tumor with unusual presentation: A report of two cases. 61
26881557 2015
16
Successful Treatment with Pazopanib for Multiple Lung Metastases of Inguinal Epithelioid Sarcoma: A Case Report. 61
26500539 2015
17
SMARCB1-deficient Vulvar Neoplasms: A Clinicopathologic, Immunohistochemical, and Molecular Genetic Study of 14 Cases. 61
25651469 2015
18
Proximal-type epithelioid sarcoma-unusual presentation: unilateral vulvar mass. 61
25858929 2015
19
SMARCB1 (INI1)-negative rhabdoid carcinomas of the gastrointestinal tract: clinicopathologic and molecular study of a highly aggressive variant with literature review. 61
24503755 2014
20
Differential microRNA expression profiles between malignant rhabdoid tumor and epithelioid sarcoma: miR193a-5p is suggested to downregulate SMARCB1 mRNA expression. 61
24287458 2014
21
[Epithelioid sarcoma of the orbit]. 61
24337357 2014
22
SMARCB1 expression in epithelioid sarcoma is regulated by miR-206, miR-381, and miR-671-5p on Both mRNA and protein levels. 61
24327545 2014
23
[A case of proximal type epithelioid sarcoma of the perineum]. 61
24322417 2013
24
Vulvar "proximal-type" epithelioid sarcoma: report of a case and review of the literature. 61
23886403 2013
25
Proximal-type epithelioid sarcoma -- case report. 61
23793215 2013
26
Proximal-type Epithelioid Sarcoma of the Head and Neck (HN): A Study with Immunohistochemical and Molecular Analysis of SMARCB1. 61
24308011 2013
27
Proximal-type epithelioid sarcoma of the scrotum: 18F-FDG PET/CT imaging. 61
23242066 2013
28
Proximal-type epithelioid sarcoma of the vulva with INI1 diagnostic utility. 61
21724432 2012
29
Proximal-type epithelioid sarcoma: case report of an unusual presentation. 61
22240247 2012
30
Proximal epithelioid sarcoma of the vulva: a case report and review of current medical literature. 61
22487511 2012
31
Proximal-type Epithelioid Sarcoma Arising in the Inguinal Area. 61
22783522 2012
32
Proximal-type epithelioid sarcoma-a rare soft tissue sarcoma of thigh in a child. 61
23204785 2011
33
p63 immunohistochemical staining is limited in soft tissue tumors. 61
22031315 2011
34
Proximal-type epithelioid sarcoma in pubis. Case report and review of the literature. 61
22169376 2011
35
Intra-articular epithelioid sarcoma showing mixed classic and proximal-type features: report of 2 cases, with immunohistochemical and molecular cytogenetic INI-1 study. 61
21566521 2011
36
An unusual and potentially misleading phenotypic change in a primary gastrointestinal stromal tumour (GIST) under imatinib mesylate therapy. 61
21191613 2011
37
Proximal-type epithelioid sarcoma of the uterine corpus. 61
21255067 2011
38
Proximal-type epithelioid sarcoma of the mons pubis: report of a case. 61
21797131 2011
39
Proximal-type epithelioid sarcoma of the vulva: relationship to malignant extrarenal rhabdoid tumor. 61
20881848 2010
40
Proximal-type epithelioid sarcoma of the maxilla with metastasis to the scalp: Cytologic findings of an unusual malignant tumor. 61
20058307 2010
41
Proximal-type epithelioid sarcoma in the groin presenting as a diagnostic dilemma. 61
19757197 2010
42
Proximal type epithelioid sarcoma arising in the base of the skull: a diagnostic challenge. 61
20360141 2010
43
Epithelioid sarcoma of the parotid gland of a child. 61
19335024 2009
44
[Clinicopathological study of 5 cases of proximal-type epithelioid sarcoma]. 61
19575870 2009
45
Loss of INI1 expression is characteristic of both conventional and proximal-type epithelioid sarcoma. 61
19033866 2009
46
Infrequent SMARCB1/INI1 gene alteration in epithelioid sarcoma: a useful tool in distinguishing epithelioid sarcoma from malignant rhabdoid tumor. 61
18973917 2009
47
A case of proximal-type epithelioid sarcoma which showed positive reactivity to fibroblast growth factor receptor 2-IIIb isotype. 61
18482307 2008
48
Proximal-type epithelioid sarcoma of the scrotum: a difficult diagnosis in an unusual location and review of the literature. 61
18428063 2008
49
Proximal-type epithelioid sarcoma vs. malignant rhabdoid tumor of the vulva: a case report, review of the literature, and an argument for consolidation. 61
17692365 2007
50
[Case of local recurrence of the periurethral proximal-type epithelioid sarcoma successfully treated by repeated regional excision]. 61
18018593 2007
51
Proximal-type epithelioid sarcoma--a rare, aggressive subtype of epithelioid sarcoma presenting as a recurrent perineal mass in a middle-aged male. 61
17341294 2007
52
Proximal-type epithelioid sarcoma of the perineum: calling attention of urologists. 61
17118034 2006
53
Tumoral, quasitumoral and pseudotumoral lesions of the superficial and somatic soft tissue: new entities and new variants of old entities recorded during the last 25 years. Part XII: appendix. 61
17175794 2006
54
Extrarenal rhabdoid tumors of soft tissue: clinicopathological and molecular genetic review and distinction from other soft-tissue sarcomas with rhabdoid features. 61
16704491 2006
55
Prognostic significance of dysadherin expression in epithelioid sarcoma and its diagnostic utility in distinguishing epithelioid sarcoma from malignant rhabdoid tumor. 61
16557275 2006
56
Proximal-type epithelioid sarcoma with elevated serum CA 125: report of a case with CA 125 immunoreactivity. 61
16740043 2006
57
Proximal type epithelioid sarcoma of the scrotum: a source of diagnostic confusion that needs immediate attention: part 2. 61
16541484 2006
58
[Case of proximal-type epithelioid sarcoma of the perineum]. 61
16613163 2006
59
Proximal type epithelioid sarcoma of the scrotum: a source of diagnostic confusion that needs immediate attention. 61
16343734 2006
60
Proximal-type epithelioid sarcoma: report of two cases in the perineum: differential diagnosis and review of soft tissue tumors with epithelioid and/or rhabdoid features. 61
16082246 2005
61
["Proximal type" epithelioid sarcoma of the vulva: differential diagnosis with other extrarenal rhabdoid tumors]. 61
16259280 2005
62
Fine needle aspiration cytology of primary proximal-type epithelioid sarcoma of the perineum: a case report. 61
15966295 2005
63
Molecular cytogenetic characterization of proximal-type epithelioid sarcoma. 61
15334553 2004
64
Proximal-type epithelioid sarcoma in a 36-year-old man: closer immunoelectron-microscopic resemblance of the tumor cells to epithelial cells than to mesenchymal cells. 61
15260853 2004
65
"Proximal-type" epithelioid sarcoma in a young girl. 61
15078349 2004
66
Proximal-type epithelioid sarcoma: case report and result of comparative genomic hybridization. 61
14675288 2004
67
'Proximal-type' epithelioid sarcoma: is Agent Orange still at large? 61
14629885 2003
68
[Recent entities in soft tissue tumor pathology. Part 2]. 61
12843968 2003
69
Radiologic manifestations of proximal-type epithelioid sarcoma of the soft tissues. 61
12239049 2002
70
Fine-needle aspiration cytology of "proximal-type" epithelioid sarcoma. 61
11477718 2001
71
Proximal-type epithelioid sarcoma: a clinicopathologic study of 20 cases. 61
11454997 2001
72
Brief report: Neural differentiation of a novel cell line, YCUS-5, established from proximal-type epithelioid sarcoma of a child. 61
10398195 1999
73
Malignant myoepithelioma of the vulva resembling a rhabdoid tumour. 61
10383714 1999
74
Proximal-type epithelioid sarcoma in the pelvic soft tissues. 61
10223300 1999
75
"Proximal-type" epithelioid sarcoma, a distinctive aggressive neoplasm showing rhabdoid features. Clinicopathologic, immunohistochemical, and ultrastructural study of a series. 61
9042279 1997

Variations for Central Epithelioid Sarcoma

Expression for Central Epithelioid Sarcoma

Search GEO for disease gene expression data for Central Epithelioid Sarcoma.

Pathways for Central Epithelioid Sarcoma

Pathways related to Central Epithelioid Sarcoma according to GeneCards Suite gene sharing:

(showing 9, show less)
# Super pathways Score Top Affiliating Genes
1 12.32 VIM KRT7 KRT5 KRT20 KRT18
2
Show member pathways
12.21 KRT7 KRT5 KRT20 KRT18
3 11.99 CD1E CD1D CD1C CD1B CD1A
4 11.85 CD34 CD1D CD1C CD1B CD1A
5
Show member pathways
11.74 VIM KRT7 KRT5 KRT18
6 11.66 CD1E CD1D CD1C CD1B CD1A
7 11.3 MME CD34 CD207 CD1D CD1C CD1A
8 11.28 TNFRSF8 MME CD34 CD1D CD1C
9 11.16 MME CD34 CD1E CD1D CD1C CD1B

GO Terms for Central Epithelioid Sarcoma

Cellular components related to Central Epithelioid Sarcoma according to GeneCards Suite gene sharing:

(showing 7, show less)
# Name GO ID Score Top Affiliating Genes
1 integral component of plasma membrane GO:0005887 9.91 PMEL MME CD34 CD1E CD1D CD1C
2 endosome GO:0005768 9.73 PMEL CD1E CD1D CD1C CD1B CD1A
3 endosome membrane GO:0010008 9.62 CD1D CD1C CD1B CD1A
4 keratin filament GO:0045095 9.58 KRT7 KRT5 KRT18
5 intermediate filament GO:0005882 9.55 VIM KRT7 KRT5 KRT20 KRT18
6 lysosome GO:0005764 9.43 TNFAIP3 CD34 CD1E CD1D CD1C CD1B
7 external side of plasma membrane GO:0009897 9.1 CD34 CD1E CD1D CD1C CD1B CD1A

Biological processes related to Central Epithelioid Sarcoma according to GeneCards Suite gene sharing:

(showing 7, show less)
# Name GO ID Score Top Affiliating Genes
1 immune response GO:0006955 9.8 CD1E CD1D CD1C CD1B CD1A
2 keratinization GO:0031424 9.67 KRT7 KRT5 KRT20 KRT18
3 regulation of immune response GO:0050776 9.65 CD34 CD1D CD1C CD1B CD1A
4 cornification GO:0070268 9.62 KRT7 KRT5 KRT20 KRT18
5 positive regulation of T cell mediated cytotoxicity GO:0001916 9.55 CD1E CD1D CD1C CD1B CD1A
6 antigen processing and presentation, exogenous lipid antigen via MHC class Ib GO:0048007 9.35 CD1E CD1D CD1C CD1B CD1A
7 antigen processing and presentation, endogenous lipid antigen via MHC class Ib GO:0048006 9.02 CD1E CD1D CD1C CD1B CD1A

Molecular functions related to Central Epithelioid Sarcoma according to GeneCards Suite gene sharing:

(showing 5, show less)
# Name GO ID Score Top Affiliating Genes
1 lipopeptide binding GO:0071723 9.55 CD1E CD1D CD1C CD1B CD1A
2 structural constituent of cytoskeleton GO:0005200 9.5 VIM KRT5 KRT20
3 scaffold protein binding GO:0097110 9.43 VIM KRT5 KRT18
4 exogenous lipid antigen binding GO:0030884 9.35 CD1E CD1D CD1C CD1B CD1A
5 endogenous lipid antigen binding GO:0030883 9.02 CD1E CD1D CD1C CD1B CD1A

Sources for Central Epithelioid Sarcoma

3 CDC
7 CNVD
9 Cosmic
10 dbSNP
11 DGIdb
17 EFO
18 ExPASy
19 FMA
28 GO
29 GTR
30 HMDB
31 HPO
32 ICD10
33 ICD10 via Orphanet
34 ICD9CM
35 IUPHAR
36 KEGG
37 LifeMap
39 LOVD
41 MedGen
43 MeSH
44 MESH via Orphanet
45 MGI
48 NCI
49 NCIt
50 NDF-RT
53 NINDS
54 Novoseek
56 OMIM
57 OMIM via Orphanet
61 PubMed
63 QIAGEN
68 SNOMED-CT via HPO
69 TGDB
70 Tocris
71 UMLS
72 UMLS via Orphanet
Content
Loading form....