MCID: CRT028
MIFTS: 25

Cor Triatriatum

Categories: Cardiovascular diseases, Fetal diseases, Rare diseases

Aliases & Classifications for Cor Triatriatum

MalaCards integrated aliases for Cor Triatriatum:

Name: Cor Triatriatum 20 58 32
Triatrial Heart 20 58

Classifications:

Orphanet: 58  
Rare cardiac malformations
Developmental anomalies during embryogenesis


External Ids:

ICD10 32 Q24.2
ICD10 via Orphanet 33 Q24.2
UMLS via Orphanet 71 C0009995
Orphanet 58 ORPHA1463

Summaries for Cor Triatriatum

GARD : 20 Cor triatriatum is an extremely rare congenital (present at birth) heart defect. The human heart normally has four chambers, two ventricles and two atria. The two atria are normally separated from each other by a partition called the atrial septum and the two ventricles by the ventricle septum. In cor triatriatum there is a small extra chamber above the left atrium (cor triatriatum sinistrum) or right atrium (cor triatriatum dextrum). The presence of this extra atrial chamber can cause slowed passage of the blood from the lungs to the heart and, over time, lead to features of congestive heart failure and obstruction. In children, cor triatriatum may be associated with major congenital cardiac problems. In adults, it is often an isolated finding. Treatment depends upon the symptoms present and may include medical or surgical approaches.

MalaCards based summary : Cor Triatriatum, also known as triatrial heart, is related to cor triatriatum sinister and cor triatriatum dexter. An important gene associated with Cor Triatriatum is NEK1 (NIMA Related Kinase 1). Affiliated tissues include heart, and related phenotypes are craniofacial and renal/urinary system

Wikipedia : 73 Cor triatriatum (or triatrial heart) is a congenital heart defect where the left atrium (cor triatriatum... more...

Related Diseases for Cor Triatriatum

Diseases related to Cor Triatriatum via text searches within MalaCards or GeneCards Suite gene sharing:

(show top 50) (show all 152)
# Related Disease Score Top Affiliating Genes
1 cor triatriatum sinister 11.9
2 cor triatriatum dexter 11.7
3 heart septal defect 11.0
4 atrial heart septal defect 10.9
5 mitral valve stenosis 10.8
6 pulmonary hypertension 10.7
7 ventricular septal defect 10.7
8 cyanosis, transient neonatal 10.7
9 atrial fibrillation 10.7
10 mitral valve insufficiency 10.6
11 tetralogy of fallot 10.6
12 pulmonary edema 10.6
13 patent foramen ovale 10.6
14 atrioventricular septal defect 10.5
15 syncope 10.5
16 pulmonary hypertension, primary, 1 10.5
17 atrial septal defect coronary sinus 10.5
18 dextro-looped transposition of the great arteries 10.4
19 pulmonary vein stenosis 10.4
20 patent ductus arteriosus 1 10.4
21 double outlet right ventricle 10.4
22 pulmonary valve stenosis 10.4
23 pulmonary venous return anomaly 10.4
24 infective endocarditis 10.3
25 endocarditis 10.3
26 tricuspid valve insufficiency 10.3
27 congestive heart failure 10.3
28 mitral valve disease 10.3
29 hypoplastic left heart syndrome 10.3
30 complete atrioventricular canal 10.3
31 double discordia 10.3
32 partial atrioventricular canal 10.3
33 myocardial infarction 10.3
34 congenital mitral stenosis 10.3
35 mitral atresia 10.3
36 cardiogenic shock 10.3
37 progressive familial heart block, type ia 10.2
38 progressive familial heart block, type ib 10.2
39 tricuspid atresia 10.2
40 cardiac arrest 10.2
41 respiratory failure 10.2
42 right bundle branch block 10.2
43 sick sinus syndrome 10.2
44 intracranial embolism 10.2
45 total anomalous pulmonary venous return 1 10.1
46 atrial standstill 1 10.1
47 pulmonary hemosiderosis 10.1
48 ebstein anomaly 10.1
49 pulmonic stenosis 10.1
50 orthostatic intolerance 10.1

Graphical network of the top 20 diseases related to Cor Triatriatum:



Diseases related to Cor Triatriatum

Symptoms & Phenotypes for Cor Triatriatum

MGI Mouse Phenotypes related to Cor Triatriatum:

46
# Description MGI Source Accession Score Top Affiliating Genes
1 craniofacial MP:0005382 8.96 HYAL2 NEK1
2 renal/urinary system MP:0005367 8.62 HYAL2 NEK1

Drugs & Therapeutics for Cor Triatriatum

Search Clinical Trials , NIH Clinical Center for Cor Triatriatum

Genetic Tests for Cor Triatriatum

Anatomical Context for Cor Triatriatum

MalaCards organs/tissues related to Cor Triatriatum:

40
Heart

Publications for Cor Triatriatum

Articles related to Cor Triatriatum:

(show top 50) (show all 999)
# Title Authors PMID Year
1
Cor triatriatum sinister with left anomalous pulmonary venous drainage to innominate vein: what to do with the vertical vein? 61
33136256 2021
2
Cor Triatriatum Associated with Total Anomalous Pulmonary Venous Connection: A Rare but Plausible Combination. 61
33115971 2021
3
Serial cardiopulmonary exercise testing in an asymptomatic young female receiving percutaneous balloon dilatation for cor triatriatum sinistrum at an early age. 61
33127273 2021
4
Computed tomography features of cor triatriatum: an institutional review. 61
33400560 2021
5
Cor Triatriatum can co-exist with Common Pulmonary Venous Atresia. 61
33662307 2021
6
Successful catheter ablation of atrial tachycardia in cor triatriatum sinister: A figure-of-8 reentry in the left atrial membrane. 61
33665113 2021
7
Mid-term outcomes of cor triatriatum repair: comparison of biventricular physiology and univentricular physiology. 61
33168116 2021
8
Psuedo-Cor Triatriatum in an Elderly Patient With Dyspnea of Exertion: An Undescribed Condition Characterized by 3-Dimensional Transesophageal Echocardiography. 61
33459035 2021
9
Deep inside pathology of Cor Triatriatum Sinister. 61
33485916 2021
10
Transesophageal imaging of cor triatriatum sinistrum. 61
32886299 2021
11
Cor triatriatum in adulthood with mitral valve regurgitation and atrial fibrillation. 61
33124099 2021
12
Imperforate cor triatriatum dexter with patent foramen ovale and pulmonic stenosis in three dogs: Diagnostic findings and attempted surgical correction. 61
33186877 2020
13
Supracardiac total anomalous pulmonary venous connection with cor triatriatum sinister: A rare diagnosis confirmed by saline contrast echocardiography. 61
33107635 2020
14
Cor triatriatum dexter associated to Ebstein anomaly with tricuspid double lesion and atrial septal defect. 61
33347428 2020
15
Computed tomography Jellyfishography: a novel volume rendering technique in a case of Cor Triatriatum. 61
33629018 2020
16
Multimodality Imaging of Cor Triatriatum Sinister in an Adult. 61
33778641 2020
17
Loeffler's group 2 cor triatriatum sinistrum with mobile left atrial thrombus - a case report and literature review. 61
33323159 2020
18
Cor Triatriatum Dexter: an unusual cause of neonatal cyanosis. 61
33180763 2020
19
Early results of robotically assisted congenital cardiac surgery: analysis of 242 patients. 61
33232727 2020
20
Catheter ablation of complex atrial tachyarrhythmias in adult patients with cor triatriatum. 61
33078325 2020
21
Cor Triatriatum Sinister (Divided Left Atrium): Histopathologic Features and Clinical Management. 61
32114046 2020
22
Three-dimensional visualization of the left atrium by intracardiac echocardiography facilitates trans-septal catheterization and atrial fibrillation catheter ablation in cor triatriatum sinister: A case report and literature review. 61
32884597 2020
23
Atrial fibrillation cryoablation in cor triatriatum dexter. 61
32294169 2020
24
Intraoperative 2D and 3D transesophageal echocardiographic assessment of cor triatriatum with ostium secundum atrial septal defect in an adult patient. 61
32687092 2020
25
Cardioembolic stroke in a young male with cor triatriatum sinister: a case report. 61
32617501 2020
26
Cor triatriatum with Raghib complex in partial atrioventricular septal defect and common atrium: a rare combination. 61
31250204 2020
27
Anesthetic experience during a laparoscopic appendectomy in a pregnant patient with isolated cor triatriatum sinister. 61
32317889 2020
28
Endoscopic Repair of Obstructive Cor Triatriatum. 61
32337396 2020
29
'Cor triatriatum', or divided left atrium. 61
31601727 2020
30
Multimodality imaging of an asymptomatic giant right atrial appendage aneurysm. 61
31967661 2020
31
A Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous Malformation. 61
33224546 2020
32
A Systematic Review of a Long-forgotten Cause of Atrial Fibrillation and Stroke: Cor Triatriatum. 61
31938652 2019
33
Surgical experience with cor triatriatum repair beyond infancy. 61
31478235 2019
34
Case report - azygos vein drainage into the left atrium in a dog with cor triatriatum dexter and a patent foramen ovale. 61
31747625 2019
35
The strange case of congenital mitral stenosis in an adult man with cor triatriatum. 61
31573705 2019
36
Forme Fruste Cor Triatriatum Dexter by Transesophageal Echocardiography and Its Impact on Percutaneous Heart Procedures: A Case Series. 61
31709369 2019
37
Cor triatriatum sinister in a dog. 61
31446292 2019
38
Cor triatriatum with extremely severe right ventricular pressure in an infant. 61
31376219 2019
39
Hybrid balloon dilation treatment for cor triatriatum dexter in a small breed puppy. 61
31565892 2019
40
Cor Triatriatum Dexter as an Incidental Finding: Role of Two-Dimensional Transthoracic Echocardiography. 61
31720152 2019
41
A Rare Case of Cardiogenic Shock: Cor Triatriatum With Anomalous Pulmonary Venous Return. 61
31496401 2019
42
A Rare Cause of Shock in an Infant: Cor Triatriatum. 61
28463946 2019
43
Bands in the Heart: Multimodality Imaging Review. 61
31373865 2019
44
Successful balloon valvuloplasty of a subpulmonic membrane associated with cor triatriatum dexter: a case report. 61
31521201 2019
45
Combined interventional procedure and cardiopulmonary bypass surgery in a dog with cor triatriatum dexter, patent foramen ovale, and pulmonary stenosis. 61
31380593 2019
46
Cor triatriatum dexter associated with atrial septal defect and mitral valve regurgitation. 61
31549368 2019
47
[Cor triatriatum with associated atrial septal defect]. 61
29935813 2019
48
Cor triatriatum sinistrum diagnosed in the adulthood: a systematic review. 61
31171629 2019
49
Acute Pulmonary Hypertension During Pregnancy Caused by Isolated Cor Triatriatum Sinus With Left Atrial Thrombus. 61
31352794 2019
50
Incomplete Cor Triatriatum Dexter: An Unsettling Guest in the Percutaneous Closure of Atrial Septal Defects. 61
30115569 2019

Variations for Cor Triatriatum

Expression for Cor Triatriatum

Search GEO for disease gene expression data for Cor Triatriatum.

Pathways for Cor Triatriatum

GO Terms for Cor Triatriatum

Sources for Cor Triatriatum

3 CDC
7 CNVD
9 Cosmic
10 dbSNP
11 DGIdb
17 EFO
18 ExPASy
19 FMA
20 GARD
28 GO
29 GTR
30 HMDB
31 HPO
32 ICD10
33 ICD10 via Orphanet
34 ICD9CM
35 IUPHAR
36 KEGG
37 LifeMap
39 LOVD
41 MedGen
44 MeSH
45 MESH via Orphanet
46 MGI
49 NCI
50 NCIt
51 NDF-RT
53 NINDS
54 Novoseek
56 OMIM via Orphanet
57 OMIM® (Updated 20-May-2021)
61 PubMed
63 QIAGEN
68 SNOMED-CT via HPO
69 Tocris
70 UMLS
71 UMLS via Orphanet
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