MCID: CRT028
MIFTS: 24

Cor Triatriatum

Categories: Cardiovascular diseases, Rare diseases

Aliases & Classifications for Cor Triatriatum

MalaCards integrated aliases for Cor Triatriatum:

Name: Cor Triatriatum 54
Triatrial Heart 54

Classifications:



External Ids:

ICD10 34 Q24.2

Summaries for Cor Triatriatum

NIH Rare Diseases : 54 Cor triatriatum is an extremely rare congenital (present at birth) heart defect. The human heart normally has four chambers, two ventricles and two atria. The two atria are normally separated from each other by a partition called the atrial septum and the two ventricles by the ventricle septum. In cor triatriatum there is a small extra chamber above the left atrium (cor triatriatum sinistrum) or right atrium (cor triatriatum dextrum). The presence of this extra atrial chamber can cause slowed passage of the blood from the lungs to the heart and, over time, lead to features of congestive heart failure and obstruction. In children, cor triatriatum may be associated with major congenital cardiac problems. In adults, it is often an isolated finding. Treatment depends upon the symptoms present and may include medical or surgical approaches.

MalaCards based summary : Cor Triatriatum, also known as triatrial heart, is related to cor triatriatum sinister and cor triatriatum dexter. An important gene associated with Cor Triatriatum is HYAL2 (Hyaluronidase 2). The drug Mechlorethamine has been mentioned in the context of this disorder. Affiliated tissues include heart and lung.

Wikipedia : 77 Cor triatriatum (or triatrial heart) is a congenital heart defect where the left atrium (cor triatriatum... more...

Related Diseases for Cor Triatriatum

Diseases related to Cor Triatriatum via text searches within MalaCards or GeneCards Suite gene sharing:

(show top 50) (show all 69)
# Related Disease Score Top Affiliating Genes
1 cor triatriatum sinister 13.0
2 cor triatriatum dexter 12.8
3 atrial fibrillation 10.7
4 atrial heart septal defect 10.7
5 tetralogy of fallot 10.5
6 atrioventricular septal defect 10.5
7 pulmonary hypertension 10.4
8 pulmonary edema 10.4
9 heart disease 10.4
10 atrial septal defect coronary sinus 10.4
11 mitral valve insufficiency 10.4
12 ventricular septal defect 10.4
13 rere-related disorders 10.4
14 transposition of the great arteries 10.4
15 syncope 10.4
16 hypoplastic left heart syndrome 1 10.3
17 hypoplastic left heart syndrome 10.3
18 double outlet right ventricle 10.3
19 double discordia 10.3
20 myocardial infarction 10.3
21 infective endocarditis 10.3
22 endocarditis 10.3
23 patent foramen ovale 10.3
24 complete atrioventricular canal 10.3
25 mitral atresia 10.3
26 pulmonary vein stenosis 10.3
27 pulmonary hypertension, primary, 1 10.2
28 asthma 10.2
29 patent ductus arteriosus 1 10.2
30 hemolytic anemia 10.2
31 congenitally corrected transposition of the great arteries 10.2
32 partial atrioventricular canal 10.2
33 atrial septal aneurysm 10.2
34 cleft mitral valve 10.1
35 spondyloarthropathy 1 10.0
36 pectus excavatum 10.0
37 pulmonary hemosiderosis 10.0
38 anus, imperforate 10.0
39 meckel syndrome, type 1 10.0
40 budd-chiari syndrome 10.0
41 tricuspid atresia 10.0
42 kawasaki disease 10.0
43 acute myocardial infarction 10.0
44 dilated cardiomyopathy 10.0
45 scoliosis 10.0
46 cardiac arrest 10.0
47 omphalocele 10.0
48 thrombosis 10.0
49 respiratory failure 10.0
50 hemosiderosis 10.0

Graphical network of the top 20 diseases related to Cor Triatriatum:



Diseases related to Cor Triatriatum

Symptoms & Phenotypes for Cor Triatriatum

Drugs & Therapeutics for Cor Triatriatum

Drugs for Cor Triatriatum (from DrugBank, HMDB, Dgidb, PharmGKB, IUPHAR, NovoSeek, BitterDB):


# Name Status Phase Clinical Trials Cas Number PubChem Id
1
Mechlorethamine Approved, Investigational 51-75-2 4033

Interventional clinical trials:


# Name Status NCT ID Phase Drugs
1 National Congenital Heart Disease Audit Unknown status NCT02303535

Search NIH Clinical Center for Cor Triatriatum

Genetic Tests for Cor Triatriatum

Anatomical Context for Cor Triatriatum

MalaCards organs/tissues related to Cor Triatriatum:

42
Heart, Lung

Publications for Cor Triatriatum

Articles related to Cor Triatriatum:

(show top 50) (show all 618)
# Title Authors Year
1
Long-standing persistent atrial fibrillation ablation without use of fluoroscopy in a patient with cor triatriatum. ( 30820404 )
2019
2
Cor triatriatum sinister with left anomalous pulmonary venous return to innominate vein. ( 30675831 )
2019
3
Bidirectional flow across a perforate cor triatriatum dexter in a dog with concurrent pulmonary, tricuspid, and mitral valve dysplasia. ( 30797449 )
2019
4
Concurrent cor triatriatum sinister and levoatriocardinal vein in an 11-year-old boy presenting with foudroyant pulmonary edema after appendectomy: A living tribute to the mal-incorporation theory. ( 30821717 )
2019
5
Cor Triatriatum: A Tale of Two Membranes. ( 30828680 )
2019
6
Abnormal Pulmonary Venous Drainage With Cor Triatriatum. ( 30905343 )
2019
7
Cor-Triatriatum Dexter with Associated Cyanosis in a 3-Month-Old Girl. ( 29911016 )
2018
8
Pseudo-Cor Triatriatum Dextrum: A Rare Manifestation of Aorto-Right Atrial Fistula SuccessfullyA Closed by Amplatzer Vascular Plug. ( 29550090 )
2018
9
Cor Triatriatum as an Uncommon Cause of Recurrent Syncope. ( 29633128 )
2018
10
Cyanosis and Stroke due to Functional Cor Triatriatum Dexter in a Neonate. ( 29316539 )
2018
11
Morphological dilemma: Anomalous pulmonary venous confluence or cor triatriatum-does it matter? ( 29296068 )
2018
12
Cor Triatriatum Sinistrum. ( 29538531 )
2018
13
Deployment of a Sapien 3 Transcatheter Valve for Severe Tricuspid Insufficiency in a Patient With Non-obstructive Cor Triatriatum Dexter. ( 29203295 )
2018
14
Cor triatriatum sinister. ( 29476204 )
2018
15
Cor Triatriatum Sinister: An Unusual Cause of Atrial Fibrillation in Adults. ( 29808125 )
2018
16
A Very Rare Case of Cor Triatriatum with Severe Mitral Regurgitation. ( 29875858 )
2018
17
Cor triatriatum dexter. ( 29881596 )
2018
18
Role of Transesophageal 3D Echocardiography in Adult Cor Triatriatum Diagnosis. ( 29633751 )
2018
19
Echocardiographic guidance of pulmonary vein isolation catheter ablation procedure for recurrent atrial fibrillation in partial cor triatriatum. ( 30460674 )
2018
20
It's Crowded Here - A Case of Cor Triatriatum Sinister. ( 29999608 )
2018
21
Outcomes in patients with cor triatriatum sinister. ( 30033682 )
2018
22
Cor Triatriatum: Case Report of Emergency Department Diagnosis. ( 30083639 )
2018
23
Incomplete Cor Triatriatum Dexter: An Unsettling Guest in the Percutaneous Closure of Atrial Septal Defects. ( 30115569 )
2018
24
Cor triatriatum sinistrum in a pregnant woman. ( 30147918 )
2018
25
Selective Partial Obstruction of Inferior Vena Cava Blood Flow During Diastole: Cor Triatriatum Dexter, Large Eustachian Valve, or Chiari Network? ( 30174263 )
2018
26
Agitated saline contrast echocardiography reveals cor triatriatum dexter. ( 30220087 )
2018
27
Subtotal Cor Triatriatum on Dual Source CT. ( 30391251 )
2018
28
Cor triatriatum dexter with right ventricular hypoplasia: Role of multimodality imaging in decision making. ( 30414206 )
2018
29
Minimally Invasive Periareolar Approach to Cor Triatriatum Repair. ( 30547898 )
2018
30
Case 2/2017 - Cor Triatriatum, without Clinical Manifestation, in A 6-Year-Old Girl. ( 28443961 )
2017
31
Cor Triatriatum and Unusual Pulmonary Venous Drainage. ( 28789918 )
2017
32
A Rare Cause of Shock in an Infant: Cor Triatriatum. ( 28463946 )
2017
33
Acquired Cor Triatriatum Sinister After the Fontan Operation and Successful Resection in a Child. ( 29054235 )
2017
34
Imperforated cor triatriatum dexter in a dog with concurrent caudal vena cava wall mineralization. ( 28049537 )
2017
35
Cor triatriatum sinister with an intact interatrial septum and a decompressing vein in a toddler. ( 28260553 )
2017
36
Mutations in HYAL2, Encoding Hyaluronidase 2, Cause a Syndrome of Orofacial Clefting and Cor Triatriatum Sinister in Humans and Mice. ( 28081210 )
2017
37
Anesthetic management of an adult patient with Cor Triatriatum Sinistrum: Utility of transesophageal echocardiography. ( 29274542 )
2017
38
A rare case of pacemaker induced tachycardia in an elderly woman with cor triatriatum sinistrum. ( 29744125 )
2017
39
Three's a Crowd - An Extremely Rare Case of Cor Triatriatum Dexter. ( 28414671 )
2017
40
A Rare Case of Cor Triatriatum Leading to Respiratory Failure and Shock in an 8-Month-Old. ( 28350721 )
2017
41
Cor triatriatum dexter associated with atrial septal defect: Management in a complex clinical case. ( 29178296 )
2017
42
Cor triatriatum and stroke. ( 28790049 )
2017
43
A successful cesarean delivery without fetal or maternal morbidity in an Eisenmenger patient with cor triatriatum sinistrum, double-orifice mitral valve, large ventricular septal defect, and single ventricle who was under long-term bosentan treatment. ( 28424444 )
2017
44
Cor triatriatum sinistrum: presentation of syncope and atrial tachycardia. ( 28196823 )
2017
45
Real-Time Four-Dimensional Echocardiography in the Diagnosis and Management of Cor Triatriatum. ( 30062266 )
2017
46
Cor Triatriatum Sinister with Secundum Atrial Septal Defect. ( 30062267 )
2017
47
Totally Endoscopic Robotic Correction of Cor Triatriatum Sinister Coexisting With Atrial Septal Defect. ( 27922989 )
2016
48
Left atrial appendage closure in a patient with cor triatriatum and ASD: the added value of 3D echocardiography. ( 27044916 )
2016
49
Getting to the right left atrium: Catheter ablation of atrial fibrillation and mitral annular flutter in cor triatriatum. ( 28491746 )
2016
50
Cor Triatriatum: A Review. ( 27913770 )
2016

Variations for Cor Triatriatum

Expression for Cor Triatriatum

Search GEO for disease gene expression data for Cor Triatriatum.

Pathways for Cor Triatriatum

GO Terms for Cor Triatriatum

Sources for Cor Triatriatum

3 CDC
7 CNVD
9 Cosmic
10 dbSNP
11 DGIdb
17 EFO
18 ExPASy
20 FMA
29 GO
30 GTR
31 HGMD
32 HMDB
33 HPO
34 ICD10
35 ICD10 via Orphanet
36 ICD9CM
37 IUPHAR
38 KEGG
39 LifeMap
41 LOVD
43 MedGen
45 MeSH
46 MESH via Orphanet
47 MGI
50 NCI
51 NCIt
52 NDF-RT
55 NINDS
56 Novoseek
58 OMIM
59 OMIM via Orphanet
63 PubMed
65 QIAGEN
70 SNOMED-CT via HPO
71 SNOMED-CT via Orphanet
72 TGDB
73 Tocris
74 UMLS
75 UMLS via Orphanet
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