Cor Triatriatum Sinister disease: Malacards - Research Articles, Drugs, Genes, Clinical Trials

MCID: CRT060 MIFTS: 20	Cor Triatriatum Sinister Categories: Cardiovascular diseases, Fetal diseases, Rare diseases, Respiratory diseases
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Aliases & Classifications for Cor Triatriatum Sinister

MalaCards integrated aliases for Cor Triatriatum Sinister:

Name: Cor Triatriatum Sinister ⁵² ⁵⁸

Cor Triatriatum Sinistrum ⁵² ⁵⁸

Divided Left Atrium ⁵² ⁵⁸

Classifications:

MalaCards categories:
Global: Rare diseases Fetal diseases
Anatomical: Cardiovascular diseases Respiratory diseases

See all MalaCards categories (disease lists)

ICD10: ³³

Congenital malformations, deformations and chromosomal abnormalities

Congenital malformations of the circulatory system

Other congenital malformations of heart

Cor triatriatum

Orphanet: ⁵⁸

Rare cardiac malformations

Developmental anomalies during embryogenesis

External Ids:

ICD10 via Orphanet ³³ Q24.2

Orphanet ⁵⁸ ORPHA99099

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Summaries for Cor Triatriatum Sinister

NIH Rare Diseases : ⁵² Cor triatriatum sinister (CTS) results when the left atrium is divided into two compartments by a membrane. The membrane can vary in size and shape and may have one or more openings. Severe cases of cor triatriatum sinister usually present in infancy and are often associated with other heart defects. In less severe cases, the diagnosis may not be made until later in life. The specific symptoms depend on the degree to which the membrane obstructs the flow of blood and whether or not there are additional heart defects. Symptoms may range from mild shortness of breath during exercise to signs of heart failure and lung congestion. Some people with CTS may not have symptoms. Treatment varies according to the severity of the symptoms. For symptomatic patients, surgery is generally considered the definitive course of therapy.

MalaCards based summary : Cor Triatriatum Sinister, also known as cor triatriatum sinistrum, is related to cor triatriatum and heart septal defect. An important gene associated with Cor Triatriatum Sinister is HYAL2 (Hyaluronidase 2). Affiliated tissues include heart and lung.

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Related Diseases for Cor Triatriatum Sinister

Diseases related to Cor Triatriatum Sinister via text searches within MalaCards or GeneCards Suite gene sharing:

(show top 50) (show all 81)

#	Related Disease	Score
1	cor triatriatum	11.3
2	heart septal defect	10.8
3	mitral valve stenosis	10.8
4	atrial heart septal defect	10.8
5	atrial fibrillation	10.8
6	atrioventricular septal defect	10.6
7	pulmonary hypertension	10.6
8	pulmonary edema	10.6
9	congestive heart failure	10.6
10	mitral valve insufficiency	10.5
11	patent foramen ovale	10.5
12	aortic valve disease 1	10.4
13	pulmonary hypertension, primary, 1	10.4
14	tetralogy of fallot	10.4
15	orthostatic intolerance	10.4
16	myocardial infarction	10.4
17	dextro-looped transposition of the great arteries	10.4
18	partial atrioventricular canal	10.4
19	syncope	10.4
20	cardiogenic shock	10.4
21	progressive familial heart block, type ia	10.3
22	coarctation of aorta	10.3
23	dandy-walker syndrome	10.3
24	meckel syndrome, type 1	10.3
25	anemia, x-linked, with or without neutropenia and/or platelet abnormalities	10.3
26	polydactyly	10.3
27	progressive familial heart block, type ib	10.3
28	deficiency anemia	10.3
29	autosomal recessive disease	10.3
30	right bundle branch block	10.3
31	hemolytic anemia	10.3
32	eisenmenger syndrome	10.3
33	encephalocele	10.3
34	single ventricular heart	10.3
35	occipital encephalocele	10.3
36	renal dysplasia	10.3
37	double-orifice mitral valve	10.3
38	spondyloarthropathy 1	10.3
39	atrial standstill 1	10.3
40	cleft palate, isolated	10.3
41	pulmonary hemosiderosis	10.3
42	stroke, ischemic	10.3
43	ventricular fibrillation, paroxysmal familial, 1	10.3
44	patent ductus arteriosus 1	10.3
45	alpha/beta t-cell lymphopenia with gamma/delta t-cell expansion, severe cytomegalovirus infection, and autoimmunity	10.3
46	kawasaki disease	10.3
47	ventricular septal defect 1	10.3
48	chorea, childhood-onset, with psychomotor retardation	10.3
49	infective endocarditis	10.3
50	cardiac arrest	10.3

Graphical network of the top 20 diseases related to Cor Triatriatum Sinister:

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Symptoms & Phenotypes for Cor Triatriatum Sinister

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Drugs & Therapeutics for Cor Triatriatum Sinister

Search Clinical Trials , NIH Clinical Center for Cor Triatriatum Sinister

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Genetic Tests for Cor Triatriatum Sinister

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Anatomical Context for Cor Triatriatum Sinister

MalaCards organs/tissues related to Cor Triatriatum Sinister:

⁴⁰

Heart, Lung

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Publications for Cor Triatriatum Sinister

Articles related to Cor Triatriatum Sinister:

(show top 50) (show all 174)

#	Title	Authors	PMID	Year
1	A rare association of divided left atrium with mitral valve prolapse. ⁶¹	Ojha V...Yadav S	32557801	2020
2	Anesthetic experience during a laparoscopic appendectomy in a pregnant patient with isolated cor triatriatum sinister. ⁶¹	Kim JH...Kim JY	32317889	2020
3	Cor Triatriatum Sinister (Divided Left Atrium): Histopathologic Features and Clinical Management. ⁶¹	Al Kindi HN...Yacoub MH	32114046	2020
4	'Cor triatriatum', or divided left atrium. ⁶¹	Anderson RH	31601727	2020
5	Cor triatriatum sinister in a dog. ⁶¹	Castagna P...Baron Toaldo M	31446292	2019
6	A Rare Case of Cardiogenic Shock: Cor Triatriatum With Anomalous Pulmonary Venous Return. ⁶¹	Moscoso B...Caffarena JM	31496401	2019
7	[Adult Cor Triatriatum Found by Chance at the Onset of Myocardial Infarction]. ⁶¹	Toyama M...Ohno O	31268012	2019
8	Cor triatriatum sinister mimicking mitral stenosis. ⁶¹	Isik O...Bakiler AR	32082868	2019
9	Cor triatriatum sinister with left anomalous pulmonary venous return to innominate vein. ⁶¹	Jaschinski C...Loukanov T	30675831	2019
10	Concurrent cor triatriatum sinister and levoatriocardinal vein in an 11-year-old boy presenting with foudroyant pulmonary edema after appendectomy: A living tribute to the mal-incorporation theory. ⁶¹	Lee ML...Tu CF	30821717	2019
11	Minimally Invasive Periareolar Approach to Cor Triatriatum Repair. ⁶¹	Gottschalk BH...Chu MWA	30547898	2018
12	Cor Triatriatum: Case Report of Emergency Department Diagnosis. ⁶¹	Halfman C...Greenfield T	30083639	2018
13	Outcomes in patients with cor triatriatum sinister. ⁶¹	Fuchs MM...Egbe AC	30033682	2018
14	[Cardiac arrest in a fitness trainer with apical hypertrophic cardiomyopathy associated with cor triatriatum sinister]. ⁶¹	Bahlmann E...Kuck KH	28852773	2018
15	A Very Rare Case of Cor Triatriatum with Severe Mitral Regurgitation. ⁶¹	Dumani S...Refatllari A	29875858	2018
16	Cor triatriatum sinister. ⁶¹	Stiermaier T...Eitel I	29476204	2018
17	It's Crowded Here - A Case of Cor Triatriatum Sinister. ⁶¹	Malik SA...Pavlides G	29999608	2018
18	Cor Triatriatum Sinister: An Unusual Cause of Atrial Fibrillation in Adults. ⁶¹	Hayes C...Kass M	29808125	2018
19	Acquired Cor Triatriatum Sinister After the Fontan Operation and Successful Resection in a Child. ⁶¹	Zaidi SJ...Siddiqui S	29054235	2017
20	Cor triatriatum sinister with an intact interatrial septum and a decompressing vein in a toddler. ⁶¹	Binsalamah ZM...Heinle JS	28260553	2017
21	Cor Triatriatum Sinister with Secundum Atrial Septal Defect. ⁶¹	Lambert J...Thavendiranathan P	30062267	2017
22	Mutations in HYAL2, Encoding Hyaluronidase 2, Cause a Syndrome of Orofacial Clefting and Cor Triatriatum Sinister in Humans and Mice. ⁶¹	Muggenthaler MM...Chioza BA	28081210	2017
23	Catheter-Based Palliation in an Infant With Obstructed Cor Triatriatum. ⁶¹	Khoury M...Chaturvedi RR	27746092	2016
24	A Very Rare Case of Co-Existence of Cor Triatriatum Sinister and Left Pulmonary Vein Atresia. ⁶¹	Aparci M...Kardesoglu E	27899867	2016
25	Totally Endoscopic Robotic Correction of Cor Triatriatum Sinister Coexisting With Atrial Septal Defect. ⁶¹	Gao C...Wang G	27922989	2016
26	An interatrial tunnel: a rare form of atrial septal defects. ⁶¹	Mahmoud HM...Yacoub M	27545447	2016
27	Mapping and surgical ablation of persistent atrial fibrillation in cor triatriatum sinister. ⁶¹	Chen Y...Cui K	26984862	2016
28	Cor triatriatum sinister with severe obstruction: a rare presentation in an adult. ⁶¹	Narayanapillai J	27495175	2016
29	Hyaluronidase 2 deficiency is a molecular cause of cor triatriatum sinister in mice. ⁶¹	Chowdhury B...Triggs-Raine B	26901790	2016
30	[Subtotal cor triatriatum sinister associated with bilateral partial anomalous pulmonary venous return]. ⁶¹	Isik O...Atay Y	27111313	2016
31	Catheter ablation of persistent atrial fibrillation in a patient with cor triatriatum sinister demonstrating a total common trunk of the pulmonary vein. ⁶¹	Tokuda M...Yoshimura M	25213428	2016
32	Cor Triatriatum Sinister　- Source of Unusual Thrombogenesis in Mitral Stenosis. ⁶¹	Lee CH...Shin DG	26423307	2016
33	Cor triatriatum sinister: a case series. ⁶¹	Isik O...Atay Y	26875126	2016
34	Cor triatriatum sinister: a rare underlying cause of pulmonary hemosiderosis. ⁶¹	Peng S...Deng X	27026847	2016
35	Surgical Treatment of Cor Triatriatum Sinister in a Cat Under Cardiopulmonary Bypass. ⁶¹	Borenstein N...Chetboul V	26414173	2015
36	Cor triatriatum sinister: Is it less sinister in older patients? ⁶¹	Naimo PS...Konstantinov IE	26365398	2015
37	Hemoptysis as a rare presentation of cor triatriatum sinister. ⁶¹	Said SM...Hanley FL	26344680	2015
38	Wong's anomaly - a rare variant of cor triatriatum. ⁶¹	Jayaprakash K...Baiju S	26432738	2015
39	Transcatheter intervention in cor triatriatum sinister. ⁶¹	Patel MB...Vettukattil JJ	26022992	2015
40	Cor triatriatum sinister presenting in the fetus: beware of association with total anomalous pulmonary venous connection. ⁶¹	Yang PK...Shih JC	25359606	2015
41	Cor triatriatum sinister and cryptogenic stroke. ⁶¹	Ridjab DA...Israel CW	23949551	2015
42	Cor triatriatum: a reversible cause of severe pulmonary hypertension. ⁶¹	Howe MJ...Rubenfire M	25745881	2015
43	Profile and outcome of congenital heart diseases in children: a preliminary experience from a tertiary center in sokoto, north Western Nigeria. ⁶¹	Sani UM...Waziri UM	25875404	2015
44	Rare combination of bilateral divided atrial chambers and pulmonary vein stenosis with review of the literature. ⁶¹	Al-Mousily F...Arfi AM	24933300	2015
45	Different Cardiac Anomalies in Mother and Son with 4q-Syndrome. ⁶¹	Marci M...Sanfilippo N	26417463	2015
46	Serendipitous diagnosis of cor triatriatum sinister in a child with Kawasaki disease. ⁶¹	Jhon J...Choi JY	30546526	2015
47	Surgical correction of cor triatriatum sinister in the paediatric population: mid-term results in 15 cases. ⁶¹	Ozyuksel A...Bilal MS	25312520	2015
48	Atrial fibrillation and cor triatriatum sinister: a case report. ⁶¹	Tran HJ...Krishnaswami A	25902348	2015
49	Wheezing as a sign of cor triatriatum sinister culminating in multiple organ failure. ⁶¹	Lee ML...Chien JW	25521992	2014
50	Anomalous left coronary artery connected to the pulmonary artery associated with other cardiac defects: a difficult joint diagnosis. ⁶¹	Laux D...Bonnet D	24898291	2014

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Genes for Cor Triatriatum Sinister

Genes related to Cor Triatriatum Sinister (0 elite genes):

- Elite gene

- Cancer Census gene in COSMIC

#	Symbol	Description	Category	Score	Evidence	PubmedIds
1	HYAL2	Hyaluronidase 2	Protein Coding	7.48	GeneCards inferred via : Publications (show sections)

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Variations for Cor Triatriatum Sinister

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Expression for Cor Triatriatum Sinister

Search GEO for disease gene expression data for Cor Triatriatum Sinister.

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Pathways for Cor Triatriatum Sinister

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GO Terms for Cor Triatriatum Sinister

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Sources for Cor Triatriatum Sinister

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