MCID: CRT060
MIFTS: 20

Cor Triatriatum Sinister

Categories: Cardiovascular diseases, Fetal diseases, Rare diseases, Respiratory diseases

Aliases & Classifications for Cor Triatriatum Sinister

MalaCards integrated aliases for Cor Triatriatum Sinister:

Name: Cor Triatriatum Sinister 52 58
Cor Triatriatum Sinistrum 52 58
Divided Left Atrium 52 58

Classifications:

Orphanet: 58  
Rare cardiac malformations
Developmental anomalies during embryogenesis


External Ids:

ICD10 via Orphanet 33 Q24.2
Orphanet 58 ORPHA99099

Summaries for Cor Triatriatum Sinister

NIH Rare Diseases : 52 Cor triatriatum sinister (CTS) results when the left atrium is divided into two compartments by a membrane. The membrane can vary in size and shape and may have one or more openings. Severe cases of cor triatriatum sinister usually present in infancy and are often associated with other heart defects. In less severe cases, the diagnosis may not be made until later in life. The specific symptoms depend on the degree to which the membrane obstructs the flow of blood and whether or not there are additional heart defects. Symptoms may range from mild shortness of breath during exercise to signs of heart failure and lung congestion. Some people with CTS may not have symptoms. Treatment varies according to the severity of the symptoms. For symptomatic patients, surgery is generally considered the definitive course of therapy.

MalaCards based summary : Cor Triatriatum Sinister, also known as cor triatriatum sinistrum, is related to cor triatriatum and heart septal defect. An important gene associated with Cor Triatriatum Sinister is HYAL2 (Hyaluronidase 2). Affiliated tissues include heart and lung.

Related Diseases for Cor Triatriatum Sinister

Diseases related to Cor Triatriatum Sinister via text searches within MalaCards or GeneCards Suite gene sharing:

(show top 50) (show all 81)
# Related Disease Score Top Affiliating Genes
1 cor triatriatum 11.3
2 heart septal defect 10.8
3 mitral valve stenosis 10.8
4 atrial heart septal defect 10.8
5 atrial fibrillation 10.8
6 atrioventricular septal defect 10.6
7 pulmonary hypertension 10.6
8 pulmonary edema 10.6
9 congestive heart failure 10.6
10 mitral valve insufficiency 10.5
11 patent foramen ovale 10.5
12 aortic valve disease 1 10.4
13 pulmonary hypertension, primary, 1 10.4
14 tetralogy of fallot 10.4
15 orthostatic intolerance 10.4
16 myocardial infarction 10.4
17 dextro-looped transposition of the great arteries 10.4
18 partial atrioventricular canal 10.4
19 syncope 10.4
20 cardiogenic shock 10.4
21 progressive familial heart block, type ia 10.3
22 coarctation of aorta 10.3
23 dandy-walker syndrome 10.3
24 meckel syndrome, type 1 10.3
25 anemia, x-linked, with or without neutropenia and/or platelet abnormalities 10.3
26 polydactyly 10.3
27 progressive familial heart block, type ib 10.3
28 deficiency anemia 10.3
29 autosomal recessive disease 10.3
30 right bundle branch block 10.3
31 hemolytic anemia 10.3
32 eisenmenger syndrome 10.3
33 encephalocele 10.3
34 single ventricular heart 10.3
35 occipital encephalocele 10.3
36 renal dysplasia 10.3
37 double-orifice mitral valve 10.3
38 spondyloarthropathy 1 10.3
39 atrial standstill 1 10.3
40 cleft palate, isolated 10.3
41 pulmonary hemosiderosis 10.3
42 stroke, ischemic 10.3
43 ventricular fibrillation, paroxysmal familial, 1 10.3
44 patent ductus arteriosus 1 10.3
45 alpha/beta t-cell lymphopenia with gamma/delta t-cell expansion, severe cytomegalovirus infection, and autoimmunity 10.3
46 kawasaki disease 10.3
47 ventricular septal defect 1 10.3
48 chorea, childhood-onset, with psychomotor retardation 10.3
49 infective endocarditis 10.3
50 cardiac arrest 10.3

Graphical network of the top 20 diseases related to Cor Triatriatum Sinister:



Diseases related to Cor Triatriatum Sinister

Symptoms & Phenotypes for Cor Triatriatum Sinister

Drugs & Therapeutics for Cor Triatriatum Sinister

Search Clinical Trials , NIH Clinical Center for Cor Triatriatum Sinister

Genetic Tests for Cor Triatriatum Sinister

Anatomical Context for Cor Triatriatum Sinister

MalaCards organs/tissues related to Cor Triatriatum Sinister:

40
Heart, Lung

Publications for Cor Triatriatum Sinister

Articles related to Cor Triatriatum Sinister:

(show top 50) (show all 174)
# Title Authors PMID Year
1
A rare association of divided left atrium with mitral valve prolapse. 61
32557801 2020
2
Anesthetic experience during a laparoscopic appendectomy in a pregnant patient with isolated cor triatriatum sinister. 61
32317889 2020
3
Cor Triatriatum Sinister (Divided Left Atrium): Histopathologic Features and Clinical Management. 61
32114046 2020
4
'Cor triatriatum', or divided left atrium. 61
31601727 2020
5
Cor triatriatum sinister in a dog. 61
31446292 2019
6
A Rare Case of Cardiogenic Shock: Cor Triatriatum With Anomalous Pulmonary Venous Return. 61
31496401 2019
7
[Adult Cor Triatriatum Found by Chance at the Onset of Myocardial Infarction]. 61
31268012 2019
8
Cor triatriatum sinister mimicking mitral stenosis. 61
32082868 2019
9
Cor triatriatum sinister with left anomalous pulmonary venous return to innominate vein. 61
30675831 2019
10
Concurrent cor triatriatum sinister and levoatriocardinal vein in an 11-year-old boy presenting with foudroyant pulmonary edema after appendectomy: A living tribute to the mal-incorporation theory. 61
30821717 2019
11
Minimally Invasive Periareolar Approach to Cor Triatriatum Repair. 61
30547898 2018
12
Cor Triatriatum: Case Report of Emergency Department Diagnosis. 61
30083639 2018
13
Outcomes in patients with cor triatriatum sinister. 61
30033682 2018
14
[Cardiac arrest in a fitness trainer with apical hypertrophic cardiomyopathy associated with cor triatriatum sinister]. 61
28852773 2018
15
A Very Rare Case of Cor Triatriatum with Severe Mitral Regurgitation. 61
29875858 2018
16
Cor triatriatum sinister. 61
29476204 2018
17
It's Crowded Here - A Case of Cor Triatriatum Sinister. 61
29999608 2018
18
Cor Triatriatum Sinister: An Unusual Cause of Atrial Fibrillation in Adults. 61
29808125 2018
19
Acquired Cor Triatriatum Sinister After the Fontan Operation and Successful Resection in a Child. 61
29054235 2017
20
Cor triatriatum sinister with an intact interatrial septum and a decompressing vein in a toddler. 61
28260553 2017
21
Cor Triatriatum Sinister with Secundum Atrial Septal Defect. 61
30062267 2017
22
Mutations in HYAL2, Encoding Hyaluronidase 2, Cause a Syndrome of Orofacial Clefting and Cor Triatriatum Sinister in Humans and Mice. 61
28081210 2017
23
Catheter-Based Palliation in an Infant With Obstructed Cor Triatriatum. 61
27746092 2016
24
A Very Rare Case of Co-Existence of Cor Triatriatum Sinister and Left Pulmonary Vein Atresia. 61
27899867 2016
25
Totally Endoscopic Robotic Correction of Cor Triatriatum Sinister Coexisting With Atrial Septal Defect. 61
27922989 2016
26
An interatrial tunnel: a rare form of atrial septal defects. 61
27545447 2016
27
Mapping and surgical ablation of persistent atrial fibrillation in cor triatriatum sinister. 61
26984862 2016
28
Cor triatriatum sinister with severe obstruction: a rare presentation in an adult. 61
27495175 2016
29
Hyaluronidase 2 deficiency is a molecular cause of cor triatriatum sinister in mice. 61
26901790 2016
30
[Subtotal cor triatriatum sinister associated with bilateral partial anomalous pulmonary venous return]. 61
27111313 2016
31
Catheter ablation of persistent atrial fibrillation in a patient with cor triatriatum sinister demonstrating a total common trunk of the pulmonary vein. 61
25213428 2016
32
Cor Triatriatum Sinister - Source of Unusual Thrombogenesis in Mitral Stenosis. 61
26423307 2016
33
Cor triatriatum sinister: a case series. 61
26875126 2016
34
Cor triatriatum sinister: a rare underlying cause of pulmonary hemosiderosis. 61
27026847 2016
35
Surgical Treatment of Cor Triatriatum Sinister in a Cat Under Cardiopulmonary Bypass. 61
26414173 2015
36
Cor triatriatum sinister: Is it less sinister in older patients? 61
26365398 2015
37
Hemoptysis as a rare presentation of cor triatriatum sinister. 61
26344680 2015
38
Wong's anomaly - a rare variant of cor triatriatum. 61
26432738 2015
39
Transcatheter intervention in cor triatriatum sinister. 61
26022992 2015
40
Cor triatriatum sinister presenting in the fetus: beware of association with total anomalous pulmonary venous connection. 61
25359606 2015
41
Cor triatriatum sinister and cryptogenic stroke. 61
23949551 2015
42
Cor triatriatum: a reversible cause of severe pulmonary hypertension. 61
25745881 2015
43
Profile and outcome of congenital heart diseases in children: a preliminary experience from a tertiary center in sokoto, north Western Nigeria. 61
25875404 2015
44
Rare combination of bilateral divided atrial chambers and pulmonary vein stenosis with review of the literature. 61
24933300 2015
45
Different Cardiac Anomalies in Mother and Son with 4q-Syndrome. 61
26417463 2015
46
Serendipitous diagnosis of cor triatriatum sinister in a child with Kawasaki disease. 61
30546526 2015
47
Surgical correction of cor triatriatum sinister in the paediatric population: mid-term results in 15 cases. 61
25312520 2015
48
Atrial fibrillation and cor triatriatum sinister: a case report. 61
25902348 2015
49
Wheezing as a sign of cor triatriatum sinister culminating in multiple organ failure. 61
25521992 2014
50
Anomalous left coronary artery connected to the pulmonary artery associated with other cardiac defects: a difficult joint diagnosis. 61
24898291 2014

Variations for Cor Triatriatum Sinister

Expression for Cor Triatriatum Sinister

Search GEO for disease gene expression data for Cor Triatriatum Sinister.

Pathways for Cor Triatriatum Sinister

GO Terms for Cor Triatriatum Sinister

Sources for Cor Triatriatum Sinister

3 CDC
7 CNVD
9 Cosmic
10 dbSNP
11 DGIdb
17 EFO
18 ExPASy
19 FMA
28 GO
29 GTR
30 HMDB
31 HPO
32 ICD10
33 ICD10 via Orphanet
34 ICD9CM
35 IUPHAR
36 KEGG
37 LifeMap
39 LOVD
41 MedGen
43 MeSH
44 MESH via Orphanet
45 MGI
48 NCI
49 NCIt
50 NDF-RT
53 NINDS
54 Novoseek
56 OMIM
57 OMIM via Orphanet
61 PubMed
63 QIAGEN
68 SNOMED-CT via HPO
69 TGDB
70 Tocris
71 UMLS
72 UMLS via Orphanet
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