CLE
MCID: EMP011
MIFTS: 34

Emphysema, Congenital Lobar (CLE)

Categories: Fetal diseases, Rare diseases, Respiratory diseases

Aliases & Classifications for Emphysema, Congenital Lobar

MalaCards integrated aliases for Emphysema, Congenital Lobar:

Name: Emphysema, Congenital Lobar 56 52
Congenital Lobar Emphysema 74 52 58 29
Cle 56 74 52
Congenital Lobar Hyperinflation 58
Infantile Lobar Hyperinflation 58

Characteristics:

Orphanet epidemiological data:

58
congenital lobar emphysema
Inheritance: Not applicable; Prevalence: 1-9/100000 (Worldwide); Age of onset: Adult,All ages,Antenatal,Childhood,Infancy,Neonatal; Age of death: normal life expectancy;

OMIM:

56
Inheritance:
autosomal dominant


HPO:

31
emphysema, congenital lobar:
Inheritance autosomal dominant inheritance


Classifications:

Orphanet: 58  
Rare respiratory diseases
Developmental anomalies during embryogenesis


External Ids:

OMIM 56 130710
MESH via Orphanet 44 C535735
ICD10 via Orphanet 33 Q33.8
UMLS via Orphanet 72 C0265797
Orphanet 58 ORPHA1928
MedGen 41 C0265797

Summaries for Emphysema, Congenital Lobar

NIH Rare Diseases : 52 Congenital lobar emphysema is a rare respiratory disorder in which air can enter the lungs but cannot escape, causing overinflation (hyperinflation) of the lobes of the lung. It is most often detected in newborns or young infants, but some cases do not become apparent until adulthood. Signs and symptoms may include difficulty breathing and respiratory distress in infancy, an enlarged chest, compressed lung tissue , cyanosis , and underdevelopment of the cartilage that supports the bronchial tube (bronchial hypoplasia). This disorder may be severe enough to cause associated heart problems (15% of cases) or so mild as to never become apparent. Some cases may be caused by autosomal dominant inheritance while others occur for no apparent reason (sporadic).

MalaCards based summary : Emphysema, Congenital Lobar, also known as congenital lobar emphysema, is related to cutaneous lupus erythematosus and leukoencephalopathy with vanishing white matter. The drugs Sodium citrate and Caffeine have been mentioned in the context of this disorder. Affiliated tissues include lung, heart and kidney, and related phenotypes are emphysema and respiratory distress

Wikipedia : 74 Pneumatosis, also known as emphysema, is the abnormal presence of air or other gas within... more...

More information from OMIM: 130710

Related Diseases for Emphysema, Congenital Lobar

Diseases related to Emphysema, Congenital Lobar via text searches within MalaCards or GeneCards Suite gene sharing:

(showing 73, show less)
# Related Disease Score Top Affiliating Genes
1 cutaneous lupus erythematosus 12.1
2 leukoencephalopathy with vanishing white matter 11.5
3 lupus erythematosus tumidus 11.3
4 lupus erythematosus 10.5
5 cyanosis, transient neonatal 10.4
6 lung disease 10.3
7 bronchomalacia 10.2
8 respiratory failure 10.2
9 ventricular septal defect 10.2
10 heart septal defect 10.2
11 pulmonary emphysema 10.2
12 pemphigus vulgaris, familial 10.2
13 dermatomyositis 10.2
14 ichthyosis 10.2
15 bullous pemphigoid 10.2
16 herpes zoster 10.2
17 pemphigus 10.2
18 bronchopulmonary dysplasia 10.2
19 pectus excavatum 10.2
20 tetralogy of fallot 10.2
21 cystic disease of lung 10.2
22 heart disease 10.2
23 bronchogenic cyst 10.2
24 autoimmune disease 10.1
25 retinal detachment 10.1
26 ichthyosis, congenital, autosomal recessive 4b 10.1
27 helicobacter pylori infection 10.1
28 myopia 10.1
29 esophagitis 10.1
30 peptic esophagitis 10.1
31 macular retinal edema 10.1
32 refractive error 10.1
33 47,xyy 10.1
34 pneumothorax, primary spontaneous 10.0
35 supravalvular aortic stenosis 10.0
36 williams-beuren syndrome 10.0
37 miller-dieker lissencephaly syndrome 10.0
38 pleuropulmonary blastoma 10.0
39 patent ductus arteriosus 1 10.0
40 niemann-pick disease, type b 10.0
41 aplastic anemia 10.0
42 pulmonary fibrosis and/or bone marrow failure, telomere-related, 2 10.0
43 deficiency anemia 10.0
44 pulmonary hypertension 10.0
45 aspiration pneumonia 10.0
46 lissencephaly 10.0
47 pain agnosia 10.0
48 compensatory emphysema 10.0
49 esophageal atresia 10.0
50 meconium aspiration syndrome 10.0
51 patent foramen ovale 10.0
52 niemann-pick disease 10.0
53 pneumothorax 10.0
54 atrial heart septal defect 10.0
55 angiodysplasia 10.0
56 glycogen storage disease 10.0
57 bronchiolitis 10.0
58 interstitial lung disease 10.0
59 rhinitis 10.0
60 embryoma 10.0
61 pneumonia 10.0
62 bronchiectasis 10.0
63 heterotaxy 10.0
64 congenital cytomegalovirus 10.0
65 horseshoe kidney 10.0
66 lymphangiectasis 10.0
67 pulmonary sequestration 10.0
68 pulmonary valves agenesis 10.0
69 cytomegalovirus infection 10.0
70 pulmonary interstitial glycogenosis 10.0
71 virus-associated trichodysplasia spinulosa 10.0
72 rare cause of hypertension 10.0
73 right aortic arch 10.0

Graphical network of the top 20 diseases related to Emphysema, Congenital Lobar:



Diseases related to Emphysema, Congenital Lobar

Symptoms & Phenotypes for Emphysema, Congenital Lobar

Human phenotypes related to Emphysema, Congenital Lobar:

58 31 (showing 4, show less)
# Description HPO Frequency Orphanet Frequency HPO Source Accession
1 emphysema 58 31 hallmark (90%) Very frequent (99-80%) HP:0002097
2 respiratory distress 58 31 hallmark (90%) Very frequent (99-80%) HP:0002098
3 abnormality of immune system physiology 58 31 frequent (33%) Frequent (79-30%) HP:0010978
4 bronchial cartilage hypoplasia 31 HP:0006539

Symptoms via clinical synopsis from OMIM:

56
Pulmonary:
bronchial cartilage hypoplasia
respiratory distress in infancy
hyperinflated lobe of lung
compressed normal lung tissue

Clinical features from OMIM:

130710

Drugs & Therapeutics for Emphysema, Congenital Lobar

Drugs for Emphysema, Congenital Lobar (from DrugBank, HMDB, Dgidb, PharmGKB, IUPHAR, NovoSeek, BitterDB):

(showing 12, show less)
# Name Status Phase Clinical Trials Cas Number PubChem Id
1
Sodium citrate Approved, Investigational 68-04-2
2
Caffeine Approved 58-08-2 2519
3
Citric acid Approved, Nutraceutical, Vet_approved 77-92-9 311
4
Calcium Approved, Nutraceutical 7440-70-2 271
5 Central Nervous System Stimulants
6 Citrate
7 Anticoagulants
8 Neurotransmitter Agents
9 Chelating Agents
10 Calcium, Dietary
11 Caffeine citrate
12 Phosphodiesterase Inhibitors

Interventional clinical trials:

(showing 2, show less)
# Name Status NCT ID Phase Drugs
1 Discovering Laryngomalacia Completed NCT01165489
2 Caffeine Citrate for the Treatment of Apnea Associated With Bronchiolitis in Young Infants: A Randomized, Double Blind, Controlled Trial (RCT) Completed NCT01435486 Caffeine citrate;Normal saline

Search NIH Clinical Center for Emphysema, Congenital Lobar

Genetic Tests for Emphysema, Congenital Lobar

Genetic tests related to Emphysema, Congenital Lobar:

# Genetic test Affiliating Genes
1 Congenital Lobar Emphysema 29

Anatomical Context for Emphysema, Congenital Lobar

MalaCards organs/tissues related to Emphysema, Congenital Lobar:

40
Lung, Heart, Kidney, Fetal Lung, Skin

Publications for Emphysema, Congenital Lobar

Articles related to Emphysema, Congenital Lobar:

(showing 399, show less)
# Title Authors PMID Year
1
Congenital lobar emphysema in a mother and daughter. 61 56
7088614 1982
2
Outcomes of Cases of Prenatally-Diagnosed Congenital Pulmonary Airway Malformation. 61
31745958 2019
3
Type I pleuropulmonary blastoma presenting as congenital pulmonary airway malformation: A report of two cases. 61
31611448 2019
4
Clinical presentation and outcome in congenital pulmonary malformation: 25 year retrospective study in Thailand. 61
31264305 2019
5
Developmental lung anomalies in adults: A pictorial review. 61
31326738 2019
6
Concurrent pulmonary hypoplasia and congenital lobar emphysema in a young dog with tension pneumothorax: a rare congenital pulmonary anomaly. 61
31349870 2019
7
Current operative management of congenital lobar emphysema in children: A report from the Midwest Pediatric Surgery Consortium. 61
30898401 2019
8
Early sonographic manifestation of fetal congenital lobar emphysema. 61
30575052 2019
9
Congenital Lung Malformations. 61
30986318 2019
10
Gene expression profiling reveals differential patterns between microcystic congenital cystic adenomatoid malformation and congenital lobar emphysema. 61
30583279 2019
11
Congenital lobar emphysema. 61
30804620 2019
12
Congenital lobar emphysema: diagnosis and treatment options. 61
31118601 2019
13
Congenital lobar emphysema. 61
29991847 2018
14
Persistent respiratory distress in a neonate: a diagnostic dilemma. 61
29666078 2018
15
Perioperative Complications of Video-Assisted Thoracoscopic Pulmonary Procedures in Neonates and Infants. 61
29510429 2018
16
Conservative post-natal management of antenatally diagnosed congenital pulmonary airway malformations. 61
28960660 2018
17
Near Complete Obliteration of the Left Hemithorax by Congenital Lobar Emphysema in an Adult. 61
29054230 2017
18
Congenital lobar emphysema in a kitten. 61
28370059 2017
19
Long-term outcomes of congenital lung malformations. 61
29110827 2017
20
Pulmonary interstitial glycogenosis associated with a spectrum of neonatal pulmonary disorders. 61
28873355 2017
21
Bilateral congenital lobar emphysema: staged management. 61
28189445 2017
22
Congenital Lobar Emphysema: Anaesthetic Challenges and Review of Literature. 61
29207814 2017
23
Congenital Lobar Emphysema in Infants. 61
29090035 2017
24
Rigid Bronchoscopic Placement of Fogarty Catheter as a Bronchial Blocker for One Lung Isolation and Ventilation in Infants and Children Undergoing Thoracic Surgery: A Single Institution Experience of 27 Cases. 61
28607884 2017
25
An Unusual Presentation of Congenital Lobar Emphysema. 61
28523200 2017
26
Congenital Lobar Emphysema with Pulmonary Extramedullary Hematopoiesis. 61
25652558 2017
27
Williams-Beuren Syndrome and Congenital Lobar Emphysema: Uncommon Association with Common Pathology? 61
28626595 2017
28
Congenital Lung Malformations: Shifting from Open to Thoracoscopic Surgery. 61
27036100 2016
29
An 18-year-old man with recurrent pneumothorax since he was 10-year-old. 61
27257988 2016
30
An Unusual Congenital Anomaly in Fanconi Aplastic Anemia: Congenital Lobar Emphysema. 61
27094981 2016
31
Mediastinal bronchogenic cyst mimicking congenital lobar emphysema. 61
27609589 2016
32
Congenital lobar emphysema: Pitfalls in diagnosis. 61
27625470 2016
33
[Congenital lobar emphysema and pulmonary valve agenesis]. 61
26598446 2016
34
Congenital Lobar Emphysema in an Adult. 61
27275927 2016
35
Congenital Lobar Emphysema: An Approach of Anesthetic Management. 61
27656534 2016
36
Congenital lobar emphysema. A rare cause of hypertension. 61
27381542 2016
37
Imaging of congenital pulmonary malformations. 61
27467867 2016
38
Congenital lobar emphysema concurrent with pneumothorax and pneumomediastinum in a dog. 61
26860354 2016
39
Congenital lobar emphysema: diagnostic and therapeutic challenges. 61
27335360 2016
40
Congenital lobar emphysema: Pitfalls in diagnosis. 61
27185998 2016
41
Congenital lobar emphysema and tension emphysema. 61
26897442 2016
42
Congenital lobar emphysema. 61
26819171 2016
43
Left Upper Lobectomy for Congenital Lobar Emphysema in a Low Weight Infant. 61
27597924 2016
44
[Giant congenital compressive segmental emphysema: diagnosis and treatment]. 61
27303589 2016
45
Congenital pulmonary malformations: metabolomic profile of lung phenotype in infants. 61
25471172 2016
46
Prenatal diagnosis, 3-D virtual rendering and lung sparing surgery by ligasure device in a baby with "CCAM and intralobar pulmonary sequestration". 61
28352794 2016
47
Congenital lobar emphysema presenting as an airway foreign body. 61
26490784 2015
48
Asymptomatic Unilateral Hyperlucent Lung in a Prospective Kidney Donor. 61
27608883 2015
49
Left Main Bronchial Stenosis Mimicking Congenital Lobar Emphysema in an 8-Month-Old Child. 61
26234880 2015
50
Anesthetic management of congenital lobar emphysema in a neonate. 61
26265861 2015
51
Anesthetic Management in Children with Congenital Lobar Emphysema. 61
26324029 2015
52
Congenital lobar emphysema: Intubation and ventilation strategies. 61
25983441 2015
53
Unilateral Obstructive Emphysema in Infancy due to Mediastinal Bronchogenic Cyst-Diagnostic Challenge and Management. 61
26155530 2015
54
Single incision thoracoscopic lobectomy through a 2.5 cm skin incision. 61
26101657 2015
55
Two decades of experience with thoracoscopic lobectomy in infants and children: standardizing techniques for advanced thoracoscopic surgery. 61
25560086 2015
56
Risk of respiratory syncytial virus infection in infants with congenital cystic lung disease. 61
25441859 2015
57
Congenital cystic lesions of the lungs: The perils of misdiagnosis - A single-center experience. 61
25814794 2015
58
Pulmonary imaging abnormalities in an adult case of congenital lobar emphysema. 61
25926923 2015
59
Congenital lobar emphysema: A modified approach to anesthetic management. 61
25624651 2015
60
Congenital cystic lesions of lung in the paediatric population: A 5-year single institutional study with review of literature. 61
25659554 2015
61
Congenital lobar emphysema causing discrepancy between size and symptoms of ventricular septal defect. 61
24384794 2014
62
Congenital cystic lesions of the lung. 61
25448785 2014
63
[Congenital lobar hyperinflation: conservative management as an alternative therapy]. 61
24269550 2014
64
Congenital lobar emphysema presenting at late childhood: A rare case report. 61
25125828 2014
65
Segmental resection for the treatment of congenital pulmonary malformations. 61
24888832 2014
66
Miller-dieker syndrome associated with congenital lobar emphysema. 61
25032053 2014
67
Surgical outcomes for congenital lung malformations: 10 years experience at a single center. 61
24701729 2014
68
A case of congenital lobar emphysema in the middle lobe. 61
24251258 2013
69
Congenital lobar emphysema: 30-year case series in two university hospitals. 61
24068262 2013
70
Lobar emphysema with pneumothorax in an adult: report of a case. 61
22922834 2013
71
Congenital lobar emphysema in a Nigerian neonate: a rare cause of neonatal respiratory distress. 61
24579507 2013
72
Inadvertent chest tube insertion in congenital cystic adenomatoid malformation and congenital lobar emphysema-highlighting an important problem. 61
23986612 2013
73
Congenital cystic lung diseases. 61
23607074 2013
74
Cystic and cavitary lung lesions in children: radiologic findings with pathologic correlation. 61
24605255 2013
75
[Congenital pulmonary malformations: clinical, radiological and treatment features]. 61
23404602 2013
76
Congenital lobar emphysema association with double superior vena cava and horseshoe kidney. 61
23176935 2012
77
Congenital lobar emphysema and intercostal drainage tube insertion: the common fate of an uncommon disease. 61
23285462 2012
78
Bilateral congenital lobar emphysema: A rare cause for respiratory distress in infancy. 61
23189104 2012
79
Congenital lobar emphysema: the role of multislice computed tomography with virtual bronchoscopy in the differential diagnosis with bronchial foreign bodies. 61
22415707 2012
80
Congenital lobar emphysema: Challenges in diagnosis and ventilation. 61
25885618 2012
81
[Congenital lung malformations: natural history and pathophysiological mechanisms]. 61
22542416 2012
82
Revisiting the histopathologic spectrum of congenital pulmonary developmental disorders. 61
22409407 2012
83
Congenital malformation of lung parenchyma: 15 years experience in a thoracic surgical unit. 61
22973779 2012
84
[Congenital lung malformations--when to operate?]. 61
22405122 2012
85
Congenital lung anomalies: can we postpone resection? 61
22244398 2012
86
Asymptomatic congenital lobar emphysema in a young adult. 61
23037488 2012
87
Not all infantile respiratory distress in winter is bronchiolitis: congenital lobar emphysema. 61
22675056 2011
88
[Prenatal diagnosis and management of foetal lung lesions]. 61
22099407 2011
89
Congenital lobar emphysema mimicking as persistent pneumonia in a newborn. 61
24765342 2011
90
The diagnostic value of multislice computed tomography in children with congenital lobar emphysema. 61
21728729 2011
91
Congenital lobar emphysema in neonates: Anaesthetic challenges. 61
21808403 2011
92
Expanding upon the unilateral hyperlucent hemithorax in children. 61
21571653 2011
93
Preoperative MDCT evaluation of congenital lung anomalies in children: comparison of axial, multiplanar, and 3D images. 61
21512069 2011
94
Thoracoscopic lobectomy in infants less than 10 kg with prenatally diagnosed cystic lung disease. 61
21214429 2011
95
[The surgical treatment of the inborn lobar emphysema in children: the comparative analysis]. 61
22408801 2011
96
Congenital lobar emphysema in an adult. 61
21654992 2011
97
Intralobar pulmonary sequestration masquerading as congenital lobar emphysema. 61
21430842 2011
98
Imaging diagnosis--Congenital lobar emphysema in a dog. 61
21322391 2011
99
Anaesthetic management of a case of congenital lobar emphysema. 61
21804718 2011
100
A case of endobronchial polyp mimicking congenital lobar emphysema in an infant. 61
24551443 2011
101
Congenital lobar emphysema associated with polysplenia syndrome. 61
20864788 2010
102
[Congenital lobar emphysema of the newborn. Report of four clinical cases]. 61
20927500 2010
103
Evaluation of early and late complications in patients with congenital lobar emphysema: a 12 year experience. 61
20859016 2010
104
Congenital lung lesions--underlying molecular mechanisms. 61
20610189 2010
105
[Surgical treatment of congenital lung malformations in pediatric patients]. 61
20485937 2010
106
Congenital lobar emphysema: is surgery routinely necessary? 61
20098010 2010
107
Congenital lobar emphysema: pitfalls and management. 61
20075537 2010
108
Hyperechoic congenital lung lesions in a non-selected population: from prenatal detection till perinatal management. 61
19911412 2009
109
[Cystic pulmonary malformations: clinical and radiological polymorphism. A report on 30 cases]. 61
19995653 2009
110
Prenatal presentation and postnatal management of congenital thoracic malformations. 61
19758773 2009
111
Congenital lobar emphysema. 61
20640213 2009
112
Prenatal diagnosis of congenital lobar emphysema: case report and review of the literature. 61
19643792 2009
113
Pleuropulmonary blastoma type I following resection of incidentally found congenital lobar emphysema. 61
19772009 2009
114
Two further cases supporting nonsurgical management in congenital lobar emphysema. 61
19637405 2009
115
Management of fetal lung lesions. 61
19559325 2009
116
[Clinical analysis of 234 cases with congenital malformations of respiratory system]. 61
19951471 2009
117
Congenital cystic pulmonary malformations in children: our experience with 19 patients. 61
25610058 2009
118
Comparison between open and thoracoscopic resection of congenital lung lesions. 61
19231529 2009
119
VATS for congenital lobar emphysema: a case report. 61
19202540 2009
120
Congenital lobar emphysema: a case report. 61
19154591 2009
121
Congenital lobar emphysema: appearance on fetal MRI. 61
18726590 2008
122
[Congenital lobar emphysema: study of a case]. 61
19023504 2008
123
Bronchogenic cyst: an uncommon cause of congenital lobar emphysema. 61
18760579 2008
124
Congenital lobar emphysema: differential diagnosis and therapeutic approach. 61
19261115 2008
125
Congenital bronchopulmonary malformations: a single-center experience and a review of literature. 61
19561895 2008
126
Surgical treatment of 60 patients with pulmonary malformations: what have we learned? 61
18982202 2008
127
Congenital lobar emphysema caused by a very rare great vessel anomaly (left aortic arch, right descending aorta and left ligamentum arteriosum). 61
18937763 2008
128
Congenital lobar emphysema. 61
18596399 2008
129
Open resections for congenital lung malformations. 61
20011487 2008
130
Congenital cystic lung disease: contemporary antenatal and postnatal management. 61
18392629 2008
131
[Congenital lobar emphysema: a rare etiology of hyperechoic lung]. 61
18462976 2008
132
Anesthetic management of a patient with bilateral congenital lobar emphysema. 61
18315649 2008
133
Congenital lobar emphysema. Report of 17 cases. 61
19476142 2008
134
[Clinical spectrum and management of congenital pulmonary cystic lesions]. 61
18581960 2008
135
Congenital lobar emphysema. 61
18222298 2008
136
Cystic lung disease. 61
18158136 2008
137
First decade's experience with thoracoscopic lobectomy in infants and children. 61
18206453 2008
138
Lung resections in children for congenital and acquired lesions. 61
17671788 2007
139
Management of a grade I laryngotracheal cleft in a 4-month-old child with congenital lobar emphysema and severe pulmonary hypertension. 61
17635408 2007
140
Congenital lobar emphysema mimicking cystic mass in a newborn. 61
18265545 2007
141
Ball valve obstruction of a bronchus causing lobar emphysema in a neonate. 61
17206431 2007
142
Antenatal diagnosis of congenital thoracic malformations: early surgery, late surgery, or no surgery? 61
17562505 2007
143
Congenital lobar emphysema and tension pneumothorax in a dog. 61
17459868 2007
144
Fetal congenital lobar emphysema. 61
17389196 2007
145
[Congenital lobar emphysema complicated with right upper lung bronchial dysplasia in a case]. 61
17254474 2006
146
Two cases of prenatally diagnosed congenital lobar emphysema caused by lobar bronchial atresia. 61
17101340 2006
147
Imaging diagnosis: congenital lobar emphysema in an old English sheepdog puppy. 61
17009508 2006
148
Combination of inhalational, intravenous, and local anesthesia for intubation in neonates with congenital lobar emphysema. 61
16918669 2006
149
Selective contralateral balloon occlusion for successful opening of a persistently collapsed lung in congenital lobar emphysema. 61
16885629 2006
150
Spontaneous regression of left upper lobe emphysema after division of large ductus arteriosus in an infant. 61
17172076 2006
151
Is congenital lobar emphysema a surgical disease? 61
16769334 2006
152
Perinatal management of congenital cystic lung lesions in the age of minimally invasive surgery. 61
16677877 2006
153
Management of congenital lung lesions. 61
16581208 2006
154
Congenital lobar emphysema associated with congenital heart disease. 61
16616669 2006
155
Cystic adenomatoid malformation of the lung: review of genetics, prenatal diagnosis, and in utero treatment. 61
16353256 2006
156
[Diagnosis and treatment of congenital bronchopulmonary malformations. A review of 32 cases]. 61
16226879 2005
157
An unusual late presentation of a congenital diaphragmatic hernia. 61
16244861 2005
158
Congenital lobar emphysema: tube thoracostomy not the treatment. 61
16280952 2005
159
Fitness to fly in an infant with congenital lobar emphysema. 61
16235886 2005
160
Congenital Lobar Emphysema: Diagnosis and Management: REPLY. 61
27407825 2005
161
Congenital Lobar Emphysema: Diagnosis and Management. 61
27407826 2005
162
Congenital lobar emphysema and sequestration--treatment by embolization. 61
15995872 2005
163
The CT appearances of delayed amniotic fluid clearance from the lungs in an infant with absent pulmonary valve and congenital lobar emphysema. 61
15824896 2005
164
Adult congenital lung disease. 61
15975811 2005
165
A very unusual presentation of Niemann-Pick disease type B in an infant: similar findings to congenital lobar emphysema. 61
16163596 2005
166
Bilateral congenital lobar emphysema: how should we proceed? 61
15918044 2005
167
No increase in peak systolic velocity of the pulmonary veins over time: a potential marker for congenital lobar emphysema. 61
15887313 2005
168
Video-assisted thoracoscopic surgical excision of cystic lung disease in children. 61
15937825 2005
169
Respiratory distress in neonates. 61
15973026 2005
170
Congenital lobar emphysema: an otolaryngologic perspective. 61
15763296 2005
171
Congenital lobar emphysema and increased nuchal translucency. 61
15685589 2005
172
Foreign-body aspiration mimicking congenital lobar emphysema in a forty-eight-day-old girl. 61
15573390 2005
173
Asymptomatic congenital lung malformations. 61
15770585 2005
174
Congenital lung malformations--antenatal and postnatal evaluation and management. 61
15621470 2005
175
Anaesthetic Management of Congenital Lobar Emphysema : A Report of Two Cases. 61
27407711 2005
176
[Congenital lobar emphysema]. 61
15875475 2005
177
Congenital masses of the lung, cystic adenomatoid malformation versus congenital lobar emphysema: prenatal diagnosis and implications for postnatal treatment. 61
15448330 2004
178
[Surgical management of developmental lung anomalies]. 61
15615472 2004
179
[Congenital bronchial atresia treated with video-assisted thoracoscopic surgery; report of a case]. 61
15285392 2004
180
Anaesthesia for neonatal thoracic surgery. 61
15171506 2004
181
Unilobar congenital pulmonary lymphangiectasis mimicking congenital lobar emphysema: an underestimated presentation? 61
15136998 2004
182
[Congenital lobar emphysema - a radiological diagnosis at first glance?]. 61
15088183 2004
183
Surgical correction of congenital lobar emphysema in a dog. 61
15031555 2004
184
Sequestrations, congenital cystic adenomatoid malformations, and congenital lobar emphysema. 61
15619187 2004
185
Surgical management of infants with congenital lobar emphysema and concomitant congenital heart disease. 61
15769700 2004
186
Congenital anomalies of the tracheobronchial tree, lung, and mediastinum: embryology, radiology, and pathology. 61
14610245 2004
187
Case of congenital lobar emphysema in an 18-month-old boy and review of earlier cases. 61
14521539 2003
188
Spontaneous multiloculated multiseptated pneumomediastinum in a newborn baby: the spinnaker sail is rigged-CT features with pathologic correlation. 61
12856166 2003
189
Use of erythropoietin for bloodless surgery in a Jehovah's witness infant. 61
12950867 2003
190
Pulmonary resection in infants for congenital pulmonary malformation. 61
12853509 2003
191
Congenital lobar emphysema: evaluation and long-term follow-up of thirty cases at a single center. 61
12687596 2003
192
Congenital lobar emphysema: a clinicopathologic evaluation of 14 cases. 61
12776242 2003
193
Congenital cystic lung disease: diagnostic and therapeutic considerations. 61
12739924 2003
194
Experience with thoracoscopic lobectomy in infants and children. 61
12592629 2003
195
Congenital lobar emphysema: a diagnostic challenge and cause of progressive respiratory distress in a 2 month-old infant. 61
12789097 2002
196
Developmental lung anomalies in the adult: radiologic-pathologic correlation. 61
12376599 2002
197
Imaging of congenital cystic lung lesions. 61
12297058 2002
198
Congenital lobar emphysema: Like father, like son. 61
11987106 2002
199
Congenital lobar emphysema. 61
11938429 2002
200
Surgical treatment of congenital lobar emphysema in a puppy. 61
11878268 2002
201
Congenital cystic adenomatoid malformation type 4. 61
11747251 2001
202
Radiographically occult congenital lobar emphysema presenting as unexplained neonatal tachypnea. 61
11536454 2001
203
Continuous caudal epidural analgesia for congenital lobar emphysema: a report of three cases. 61
11473858 2001
204
Prenatal sonographic features of congenital lobar emphysema. 61
11399878 2001
205
The postnatal management of congenital cystic adenomatoid malformation. 61
11344837 2001
206
A case of localized persistent interstitial pulmonary emphysema. 61
11306752 2001
207
Congenital lobar emphysema: experience with 21 cases. 61
11315310 2001
208
[Diagnostic image (23). Congenital lobar emphysema]. 61
11219148 2001
209
Congenital lobar emphysema--the disappearing chest mass: antenatal ultrasound appearance. 61
11320989 2001
210
Congenital lobar emphysema. 61
11232983 2000
211
Congenital malformation of the lung. 61
10952352 2000
212
[Congenital lobar emphysema in adults]. 61
10953572 2000
213
Prenatal diagnosis and management of congenital lobar emphysema. 61
10813352 2000
214
Congenital lobar emphysema occurring in twins. 61
10875103 2000
215
Congenital cystic disease of the lung in infants and children (experience with 57 cases). 61
10661844 1999
216
Congenital parenchymatous malformations of the lung. 61
10501874 1999
217
Imaging of surgical diseases of the newborn chest. Intrapleural mass lesions. 61
10546666 1999
218
Congenital lobar emphysema: diagnostic and therapeutic considerations. 61
10507427 1999
219
Congenital lobar emphysema: antenatal diagnosis and follow up. 61
10901909 1999
220
Outcome of congenital lung abnormalities detected antenatally. 61
10342547 1999
221
[Congenital bronchopulmonary cystic disease]. 61
10021793 1998
222
Congenital lobar emphysema. 61
10216606 1998
223
Flexible bronchoscopy in the management of congenital lobar emphysema in the neonate. 61
9707469 1998
224
[Polyalveolosis: pathogenesis of congenital lobar emphysema?]. 61
9699326 1998
225
Management of congenital lobar emphysema with endobronchial intubation and controlled ventilation. 61
9428854 1998
226
Diagnosis and differentiation of congenital diaphragmatic hernia from other noncardiac thoracic fetal masses. 61
10064203 1998
227
Lung volume reduction for congenital lobar emphysema. 61
9288529 1997
228
Surgical management of congenital lobar emphysema. 61
10868191 1997
229
Congenital malformations of the lung and mediastinum--a quarter century of experience from a single institution. 61
9021566 1997
230
Congenital lobar emphysema in congenital cytomegalovirus infection. 61
8929306 1996
231
Combined sequestration, bronchogenic cyst, and dysgenetic lung simulating congenital lobar emphysema. 61
8969362 1996
232
Congenital lobar emphysema: a review of 10 cases. 61
10830064 1996
233
Bronchoscopic appearances of congenital lobar emphysema. 61
8860077 1996
234
[Congenital lobar emphysema in childhood]. 61
9011675 1996
235
[The late results of the surgical treatment of congenital anomalies of the bronchopulmonary system in childhood]. 61
9011665 1996
236
Adult congenital lobar emphysema in pregnancy. 61
7570448 1995
237
ANAESTHESIA FOR CONGENITAL LOBAR EMPHYSEMA: Author's Reply. 61
28769298 1995
238
ANAESTHESIA FOR CONGENITAL LOBAR EMPHYSEMA. 61
28769297 1995
239
ANAESTHESIA FOR CONGENITAL LOBAR EMPHYSEMA: A Case Report. 61
28769243 1995
240
[Renal infarction following pulmonary surgery in a 13-year-old boy]. 61
7864670 1994
241
Pediatric intrathoracic large airway obstruction: diagnostic and therapeutic considerations. 61
7899124 1994
242
Congenital lung cysts. 61
7850363 1994
243
Congenital lobar emphysema. A case report. 61
7929554 1994
244
Deficiency of cartilage in the segmental bronchi of a child: congenital or acquired? 61
8067871 1994
245
[Congenital lobar emphysema: report of 38 cases]. 61
8086299 1994
246
[Giant lobar emphysema. The cause of a compressive hemithoracic opacity in a newborn infant]. 61
8128096 1994
247
Congenital lobar emphysema: a case with bronchial septum. 61
8157425 1994
248
Use of staplers in congenital lobar emphysema. 61
8110719 1993
249
Congenital lobar emphysema. 61
8039865 1993
250
Malformation of lung in neonates (lobectomy for congenital lobar emphysema and lung cyst). 61
7996503 1993
251
Retained fetal lung liquid in congenital lobar emphysema: a possible predictor of polyalveolar lobe. 61
8414757 1993
252
Bubbly intrapleural mucous simulating congenital lobar emphysema. 61
8233696 1993
253
Surgery for congenital malformations of the lung. 61
8333716 1993
254
The clinical and imaging spectrum of findings in patients with congenital lobar emphysema. 61
1480442 1992
255
[Congenital lobar emphysema successfully treated by right upper lobectomy at five hours after delivery: a case report]. 61
1619818 1992
256
[Congenital lobar emphysema]. 61
1497230 1992
257
Antenatal presentation of a child with congenital lobar emphysema. 61
1560512 1992
258
Radiological case of the month. Absent pulmonic valve presenting with congenital lobar emphysema. 61
1736636 1992
259
[Congenital lobar emphysema in children]. 61
1453643 1992
260
Surgery for congenital malformations of the lung. 61
1605537 1992
261
[Interstitial pulmonary emphysema. Combined therapeutic approach in a retrospective multidisciplinary study]. 61
1791794 1991
262
[Congenital lobar emphysema]. 61
1878159 1991
263
Ventilation-perfusion scintigraphy in an adult with congenital unilateral hyperlucent lung. 61
2225670 1990
264
Congenital bronchopulmonary malformations. Diagnostic and therapeutic considerations. 61
2319779 1990
265
Congenital lobar emphysema. 61
2322975 1990
266
[Congenital lobar emphysema]. 61
2128717 1990
267
Congenital lobar emphysema--a report of 5 cases. 61
2607700 1989
268
[Lung operations in dyspneic newborn infants]. 61
2812085 1989
269
One-lung high-frequency ventilation in the management of an acquired neonatal pulmonary cyst. 61
2709154 1989
270
Congenital lobar emphysema. The roles of CT and V/Q scan. 61
2910626 1989
271
Congenital lobar emphysema. 61
3205240 1988
272
Solubilized xenon 133 lung scintigraphy. 61
3244070 1988
273
Management of an unusual case of congenital lobar emphysema. 61
3237451 1988
274
[Neonatal respiratory distress due to congenital lobar emphysema]. 61
3251128 1988
275
Ventilation management casebook: congenital lobar emphysema. 61
3225673 1988
276
[Prenatal diagnosis and genetic diseases of the lung]. 61
3261024 1988
277
[Anesthetic management of infants with congenital lobar emphysema by using independent lung ventilation]. 61
3446857 1987
278
Successful surgical treatment of a newborn with bilateral congenital lobar emphysema. 61
3430296 1987
279
Ventilation scintigraphy with submicronic radioaerosol as an adjunct in the diagnosis of congenital lobar emphysema. 61
3598706 1987
280
High-frequency jet ventilation for resection of congenital lobar emphysema. 61
3605681 1987
281
Congenital lobar emphysema. 61
3692595 1987
282
[Congenital lobar emphysema]. 61
3589826 1986
283
Congenital lobar emphysema requiring surgery in adult life. 61
3467693 1986
284
Selective bronchial intubation in infants with lobar emphysema: indications, complications, and long-term outcome. 61
3718641 1986
285
[Various cases of congenital lobar emphysema]. 61
3786189 1986
286
[Congenital unilobar pulmonary lymphangiectasis]. 61
3948719 1986
287
Congenital lobar emphysema caused by aplasia of bronchial cartilage in a Pekingese puppy. 61
3946057 1986
288
Congenital lobar emphysema: segmental lobar involvement demonstrated on ventilation and perfusion imaging. 61
4056931 1985
289
The changing spectrum of cystic pulmonary lesions requiring surgical resection in infants. 61
3974268 1985
290
Bronchial atresia associated with a bronchogenic cyst. Evidence of early appearance of atretic segments. 61
3971768 1985
291
Lobus venae azygos and congenital lobar emphysema in an infant. 61
2982179 1985
292
Developmental anomalies of the lung in Nigerian children. 61
6534988 1984
293
Anaesthesia for congenital lobar emphysema resection. A case report. 61
6484768 1984
294
Congenital lobar emphysema due to a bronchogenic cyst. 61
6518067 1984
295
Spontaneous occurrence of localized pulmonary interstitial and endolymphatic emphysema in infancy. 61
6462807 1984
296
Congenital lobar emphysema with tracheal bronchus. 61
6668296 1983
297
CT diagnosis of congenital lobar emphysema. 61
6630644 1983
298
Congenital lobar emphysema: problems in diagnosis and management. 61
6625632 1983
299
Acute worsening of congenital lobar emphysema with subsequent spontaneous improvement. 61
6835772 1983
300
Congenital lobar emphysema. 61
6670131 1983
301
Congenital lobar emphysema of left upper lobe. A case report. 61
6867644 1983
302
Congenital lobar emphysema. 61
7160882 1982
303
[Congenital lobar emphysema in children (presentation of a case)]. 61
7145562 1982
304
Congenital lobar emphysema: a case with bronchial atresia and abnormal bronchial cartilages. 61
7093137 1982
305
Pulmonary function after lobectomy for congenital lobar emphysema and congenital cystic adenomatoid malformation. A follow-up study. 61
6820575 1982
306
[Diagnosis and course of congenital lobar emphysema]. 61
7168213 1982
307
Congenital Lobar emphysema. 61
7344584 1981
308
[Congenital lobar emphysema]. 61
7306335 1981
309
Radioisotopic evaluation of congenital lobar emphysema. 61
6452982 1981
310
[Congenital lobar emphysema]. 61
7227006 1981
311
Polyalveolar lobe: anatomic and physiologic parameters and their relationship to congenital lobar emphysema. 61
7463297 1980
312
Lung growth and airway function after lobectomy in infancy for congenital lobar emphysema. 61
7430353 1980
313
The value of cardiac catheterization and cineangiography in infantile lobar emphysema. 61
7454424 1980
314
Unilateral hyperlucent lung: the case for investigation. 61
7466723 1980
315
[Bronchiolitis]. 61
7426129 1980
316
Surgical management of lung bud anomalies: lobar emphysema, bronchogenic cyst, cystic adenomatoid malformation, and intralobar pulmonary sequestration. 61
454042 1979
317
Congenital lobar emphysema. 61
451655 1979
318
[Congenital lobar emphysema]. 61
426924 1979
319
Congenital cystic malformation of the lung. A form of congenital bronchiolar ("adenomatoid") malformation. 61
571674 1979
320
[Respiratory distress syndrome and pulmonary congenital malformations (author's transl)]. 61
742772 1978
321
Bronchial atresia: a recognizable entity in the pediatric age group. 61
731369 1978
322
The anesthetic management of congenital lobar emphysema. 61
697090 1978
323
Pulmonary perfusion imaging in congenital lobar emphysema. 61
685920 1978
324
Congenital lobar emphysema. 61
657700 1978
325
Radiological case of the month: congenital lobar emphysema. 61
629249 1978
326
"Acquired" lobar emphysema: a complication of respiratory distress in premature infants. 61
592069 1977
327
[Surgical treatment of congenital lobar emphysema of the lung (author's transl)]. 61
604199 1977
328
Congenital lobar emphysema resulting from bronchial sling around a normal right main pulmonary artery. 61
875429 1977
329
Congenital lobar emphysema. 61
882286 1977
330
Congenital lobar emphysema. 61
142346 1977
331
[Congenital lobar emphysema in a child]. 61
864958 1977
332
Continuous positive airway pressure in congenital lobar emphysema. 61
324573 1977
333
[The congenital lobar emphysema (author's transl)]. 61
834456 1977
334
Congenital lobar emphysema. 61
866684 1977
335
Case history number 93: congenital lobar emphysema. 61
1033707 1976
336
Segmental lung resection in the first year of life. 61
938132 1976
337
Congenital lobar emphysema: long-term evaluation of surgically and conservatively treated children. 61
937822 1976
338
The scanning electron microscopy of elastase-induced emphysema. A comparison with emphysema in man. 61
1246121 1976
339
Congenital lung malformations: a unified concept and a case report. 61
1152510 1975
340
[The congenital lobar emphysema--a case of emergency for the thoracical surgery during the early infancy (author's transl)]. 61
1080597 1975
341
[Differentiated surgical therapy in congenital lobar emphysema (author's transl)]. 61
1080599 1975
342
Congenital lobar emphysema. 61
1080600 1975
343
[Congenital lobar emphysema: medical or surgical treatment?]. 61
1136067 1975
344
[Radiographic picture of ventillatory disorders in small children with special reference to congenital lobar emphysema]. 61
4828033 1974
345
Congenital lobar emphysema--pathoanatomic studies of three cases. 61
4219947 1974
346
Dilated lymphatics in congenital lobar emphysema. Report of a second case. 61
4715376 1973
347
[Bilateral congenital lobar emphysema. Successful 1-stage right middle and left upper lobectomy]. 61
4733661 1973
348
Congenital lobar emphysema documented by serial roentgenograms. 61
4698963 1973
349
[Clinical aspects and treatment of congenital lobar emphysema]. 61
4731677 1973
350
[Recent aspects in the etiopathogenesis of congenital lobar emphysema]. 61
5048553 1972
351
[Congenital lobar emphysema: a case report with a 32-year follow-up]. 61
5047643 1972
352
[Congenital lobar emphysema in 2 infants]. 61
5138057 1971
353
Congenital lobar emphysema. 61
5543549 1971
354
Congenital lobar emphysema. 61
5543851 1971
355
[Etiopathogenetic and clinical aspects of congenital lobar emphysema]. 61
5156900 1971
356
[A case of congenital lobar emphysema]. 61
5473231 1970
357
Bilateral congenital lobar emphysema. 61
5454858 1970
358
[Congenital lobar emphysema in children]. 61
5446496 1970
359
[Congenital lobar emphysema]. 61
5444218 1970
360
The role of pulmonary scanning in the diagnosis of congenital lobar emphysema. 61
5466949 1970
361
[Congenital lobar emphysema in a 1-month-old infant]. 61
5385390 1969
362
Congenital lobar emphysema with bronchial atresia. 61
5775061 1969
363
[Congenital lobar emphysema in the infant and child]. 61
5757232 1968
364
[Congenital lobar emphysema of the lung. Clinical and anatomopathological considerations on a case]. 61
5746693 1968
365
[Congenital lobar emphysema in newborn infants (clinical, radiographic and histologic findings on 3 cases)]. 61
5740213 1968
366
[Congenital lobar emphysema]. 61
5686556 1968
367
[Histomorphological studies of lung tissue in congenital lobar emphysema]. 61
5675149 1968
368
Congenital lobar emphysema: report of a case treated by bilateral simultaneous pulmonary resection. 61
5648849 1968
369
[Anesthesiological problems in congenital lobar emphysema in the newborn]. 61
5613774 1967
370
[Successfully treated case of lobectomy for congenital lobar emphysema]. 61
6063395 1967
371
Congenital lobar emphysema. 61
5335098 1967
372
[Congenital lobar emphysema]. 61
5588328 1967
373
[Congenital lobar emphysema and its differential diagnosis]. 61
6067820 1967
374
[A case of congenital lobar emphysema in a 3-week-old infant]. 61
6031862 1967
375
[Congenital lobar emphysema associated with a funnel chest]. 61
5925888 1966
376
Congenital lobar emphysema with dilated septal lymphatics. 61
5936105 1966
377
[Congenital lobar emphysema]. 61
5986185 1966
378
Congenital lobar emphysema: long-term effects and sequelae in treated cases. 61
5931099 1966
379
THE SURGICAL TREATMENT OF CONGENITAL LOBAR EMPHYSEMA. 61
14320371 1965
380
[Case of congenital lobar emphysema in 3-year-old children]. 61
5843774 1965
381
[CONGENITAL LOBAR EMPHYSEMA]. 61
14294604 1965
382
CONGENITAL LOBAR EMPHYSEMA: CASE REPORT OF BILATERAL INVOLVEMENT. 61
14221249 1964
383
[CONGENITAL LOBAR EMPHYSEMA]. 61
14225894 1964
384
[CONGENITAL LOBAR EMPHYSEMA]. 61
14092635 1963
385
[CONGENITAL LOBAR EMPHYSEMA]. 61
14111532 1963
386
[Congenital lobar emphysema]. 61
14453503 1962
387
Congenital lobar emphysema. 61
13962131 1962
388
[On the clinical aspects and therapy of congenital lobar emphysema]. 61
13906337 1962
389
[Surgical treatment of congenital lobar emphysema of the lung]. 61
13755453 1961
390
[Congenital lobar emphysema]. 61
13767597 1961
391
Congenital lobar emphysema. 61
13835026 1959
392
[Congenital lobar emphysema: case cured by lobectomy in the second month of life]. 61
13653875 1959
393
[Congenital lobar emphysema]. 61
13553087 1958
394
Congenital lobar emphysema. 61
13436798 1957
395
[Congenital lobar emphysema]. 61
13471158 1957
396
Congenital lobar emphysema. 61
13328161 1956
397
Congenital lobar emphysema. 61
13159370 1954
398
[Two cases of congenital lobar emphysema]. 61
13181501 1954
399
Congenital lobar emphysema. 61
14911250 1951

Variations for Emphysema, Congenital Lobar

Expression for Emphysema, Congenital Lobar

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