MCID: FBR028
MIFTS: 26

Fibrosing Mediastinitis

Categories: Bone diseases, Rare diseases, Respiratory diseases
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Aliases & Classifications for Fibrosing Mediastinitis

MalaCards integrated aliases for Fibrosing Mediastinitis:

Name: Fibrosing Mediastinitis 19 58 75 33
Mediastinal Fibrosis 19 58 71 33
Idiopathic Mediastinal Fibrosis 19 33
Igg4-Related Mediastinitis 19 58
Sclerosing Mediastinitis 19 58
Idiopathic Hilar Fibrosis 71

Classifications:

Orphanet: 58  
Rare respiratory diseases
Rare systemic and rhumatological diseases


External Ids:

MESH via Orphanet 44 C536136
ICD10 via Orphanet 32 J98.5
UMLS via Orphanet 72 C0221386 C0264573
Orphanet 58 ORPHA63999
ICD11 33 123840075
UMLS 71 C0221386 C0264573

Summaries for Fibrosing Mediastinitis

GARD: 19 Fibrosing mediastinitis is a condition that affects the area between the lungs (mediastinum) which contains the heart, large blood vessels, windpipe (trachea), esophagus, and lymph nodes. People with Fibrosing mediastinitis have varying amounts of scar tissue in the mediastinum which may cause problems for the organs located there. For example, some affected people may develop blocked airways that can interfere with lung function. Others may have compressed blood vessels which can slow or prevent blood flow to and from the heart. The exact cause of Fibrosing mediastinitis is not fully understood, but it is not inherited. Many cases are linked to a specific type of fungal infection called histoplasmosis.

MalaCards based summary: Fibrosing Mediastinitis, also known as mediastinal fibrosis, is related to fibrosclerosis, multifocal and mediastinitis. Affiliated tissues include trachea, heart and lung.

Orphanet: 58 A rare systemic autoimmune disease characterized by an aggressive fibroinflammatory process with infiltration of IgG4-positive plasma cells in the mediastinum, potentially resulting in compression and functional impairment of vital mediastinal structures, and associated with elevated serum IgG4. Clinical symptoms are unspecific and include pain or symptoms due to mass effect. The condition may occur together with IgG4-related disease in other parts of the body.

Wikipedia: 75 Mediastinitis is inflammation of the tissues in the mid-chest, or mediastinum. It can be either acute or... more...

Related Diseases for Fibrosing Mediastinitis

Diseases related to Fibrosing Mediastinitis via text searches within MalaCards or GeneCards Suite gene sharing:

(show top 50) (show all 153)
# Related Disease Score Top Affiliating Genes
1 fibrosclerosis, multifocal 11.2
2 mediastinitis 11.1
3 histoplasmosis 10.7
4 pulmonary hypertension 10.6
5 pulmonary vein stenosis 10.5
6 igg4-related disease 10.5
7 sarcoidosis 1 10.4
8 sarcoidosis 2 10.4
9 functional neutrophil defect 10.4
10 hypertension, essential 10.3
11 pulmonary hypertension, primary, 1 10.2
12 pulmonary edema 10.2
13 tracheal stenosis 10.2
14 behcet syndrome 10.1
15 varicose veins 10.1
16 aspergillosis 10.1
17 ptosis 10.1
18 thrombosis 10.1
19 blastomycosis 10.1
20 cervicitis 10.1
21 histiocytosis 10.1
22 chronic thromboembolic pulmonary hypertension 10.1
23 retroperitoneal fibrosis 10.1
24 cataract 6, multiple types 10.0
25 migraine with or without aura 1 10.0
26 scleroderma, familial progressive 10.0
27 lung cancer 10.0
28 endocardial fibroelastosis 10.0
29 lymphoma, hodgkin, classic 10.0
30 papillon-lefevre syndrome 10.0
31 pancreatic cancer 10.0
32 pulmonary venoocclusive disease 1, autosomal dominant 10.0
33 congenital hemidysplasia with ichthyosiform erythroderma and limb defects 10.0
34 langerhans cell histiocytosis 10.0
35 cholangitis, primary sclerosing 10.0
36 leukemia, acute lymphoblastic 3 10.0
37 peripheral vascular disease 10.0
38 anaplastic large cell lymphoma 10.0
39 peripheral t-cell lymphoma 10.0
40 infective endocarditis 10.0
41 cardiac arrest 10.0
42 hepatic veno-occlusive disease 10.0
43 b-lymphoblastic leukemia/lymphoma 10.0
44 castleman disease 10.0
45 pleurisy 10.0
46 pleural tuberculosis 10.0
47 brucellosis 10.0
48 bartonellosis 10.0
49 sarcoma 10.0
50 anhidrosis 10.0

Graphical network of the top 20 diseases related to Fibrosing Mediastinitis:



Diseases related to Fibrosing Mediastinitis

Symptoms & Phenotypes for Fibrosing Mediastinitis

Drugs & Therapeutics for Fibrosing Mediastinitis

Search Clinical Trials, NIH Clinical Center for Fibrosing Mediastinitis

Genetic Tests for Fibrosing Mediastinitis

Anatomical Context for Fibrosing Mediastinitis

Organs/tissues related to Fibrosing Mediastinitis:

MalaCards : Trachea, Heart, Lung, Bone, Breast, Thyroid

Publications for Fibrosing Mediastinitis

Articles related to Fibrosing Mediastinitis:

(show top 50) (show all 591)
# Title Authors PMID Year
1
A Community-Based Pancreatic Cancer Screening Study in High-Risk Individuals: Preliminary Efficacy and Safety Results. 62
35854467 2022
2
[Mediastinal pseudotumor-necrotizing and sclerosing mediastinitis with pseudomembranes]. 62
35237866 2022
3
Extensive fibrotic wrapping of the heart: a rare echocardiographic diagnosis. 62
35879720 2022
4
Pneumonectomy for Idiopathic Fibrosing Mediastinitis Mimicking Neoplasm in a Child. 62
34582756 2022
5
IgG4-associated fibrosing mediastinitis requiring differentiation from posterior mediastinal tumour: A case report. 62
35582341 2022
6
Fibrosing Mediastinits Causing Obstruction of Left Lower Lobar Bronchus: A Pediatric Case Report. 62
36238519 2022
7
Chronic nonchylous lymphatic pleural effusion in a bottlenose dolphin (Tursiops truncatus). 62
35298406 2022
8
Acute mediastinitis, mediastinal granuloma, and chronic fibrosing mediastinitis: A review. 62
34176697 2022
9
Comparison of fibrosing mediastinitis patients with vs. without markedly increased systolic pulmonary arterial pressure: a single-center retrospective study. 62
35361126 2022
10
Fibrosing Mediastinitis Presenting With Superior Vena Cava Syndrome. 62
35505701 2022
11
CT Appearance of Pulmonary Arteriovenous Malformations and Mimics. 62
34990315 2022
12
[Short-term efficacy and perioperative safety of catheter-based intervention for pulmonary vein stenosis caused by fibrosing mediastinitis]. 62
35045615 2022
13
The hemodynamic spectrum of pulmonary vein stenosis from fibrosing mediastinitis. 62
34536328 2022
14
Clinical Features of Fibrosing Mediastinitis in Japanese Patients: Two Case Reports and a Literature Review. 62
34024847 2021
15
CT features of fibrosing mediastinitis. 62
34167927 2021
16
Imaging of IgG4-related fibrosing mediastinitis. 62
34801186 2021
17
Immunoglobulin G4-Related Aortitis and Severe Aortic Valve Stenosis Treated With Transcatheter Aortic Valve Replacement and Immunosuppression. 62
34333027 2021
18
Pulmonary Histoplasmosis. 62
34498137 2021
19
Successful Transcatheter Recanalization of a Chronically Occluded Left Pulmonary Artery Due to Fibrosing Mediastinitis. 62
34147384 2021
20
Pulmonary hypertension complicating mediastinal fibrosis secondary to tuberculosis: A case report and literature review. 62
34382596 2021
21
Vascular homografts as bypass grafts for superior vena cava syndrome due to idiopathic fibrosing mediastinitis. 62
34041423 2021
22
Rescue of pulmonary artery intra-stent re-stenosis by unzipping an under-sized stent in an adult patient with fibrosing mediastinitis. 62
34074843 2021
23
Refractory pleural effusion as a rare complication of pulmonary vascular stenosis induced by fibrosing mediastinitis: a case report and literature review. 62
33947262 2021
24
[Immunoglobulin G4( IgG4)-related Fibrosing Mediastinitis Localized in the Retrosternal Area:Report of a Case]. 62
33831894 2021
25
A rare case of primary angiosarcoma of the anterior mediastinum. 62
33222090 2021
26
Complete lung collapse as a rare complication of sarcoidosis-associated mediastinal lymphadenopathy. 62
33732471 2021
27
Fibrosing Mediastinitis Associated With Tuberculosis in Children. 62
33710984 2021
28
Evaluation of Outcomes Following Pulmonary Artery Stenting in Fibrosing Mediastinitis. 62
33205295 2021
29
An unusual pediatric case of tuberculosis-associated mediastinal fibrosis with concomitant pulmonary arterial and venous occlusion. 62
33259092 2021
30
CD4+CTLs in Fibrosing Mediastinitis Linked to Histoplasma capsulatum. 62
33328214 2021
31
Tuberculosis lymphadenopathy: A rare etiology of the superior vena cava syndrome. 62
33546823 2021
32
Idiopathic fibrosing mediastinitis. 62
34430869 2021
33
Thoracic Cardiovascular Complications of Tuberculosis. 62
33475319 2021
34
Ptosis and Miosis Associated with Fibrosing Mediastinitis. 62
33431787 2021
35
IgG4-related fibrosing mediastinitis: clinical presentation, treatment efficacy and comparison with IgG4-RD without fibrosing mediastinitis. 62
32896252 2020
36
Rituximab to Treat Fibrosing Mediastinitis-Associated Recurrent Hemoptysis. 62
31356339 2020
37
Imaging features and differential diagnoses of non-neoplastic diffuse mediastinal diseases. 62
33057984 2020
38
[Advances in diagnosis and therapy of pulmonary vascular stenosis induced by fibrosing mediastinitis]. 62
33076618 2020
39
Massive Dilatation of the Hemiazygos Vein Secondary to Fibrosing Mediastinitis. 62
32497639 2020
40
Imaging of IgG4-related fibrosing mediastinitis. 62
32972745 2020
41
A Rare Case of Bronchomediastinal Pulmonary Vein Fistula due to Fibrosing Mediastinitis. 62
33072449 2020
42
A case of IgG4-related anterior mediastinal sclerosing disease coexisting with autoimmune pancreatitis. 62
32705358 2020
43
Successful Stenting of Bilateral Pulmonary Veins Stenosis Secondary to Idiopathic Fibrosing Mediastinitis. 62
32007463 2020
44
A review of endovascular stenting for superior vena cava syndrome in fibrosing mediastinitis. 62
31804157 2020
45
Diagnosis of an unusual case of idiopathic mediastinal fibrosis by 18F-FDG PET/CT. 62
32099588 2020
46
Mediastinal Fibrosis, Pulmonary Vein Stenosis, and the Role of Transesophageal Echocardiography. 62
31806471 2020
47
A Novel Technique for the Management of Massive Hemoptysis: The Customized Endobronchial Silicone Blocker. 62
32352902 2020
48
Fibrosing mediastinitis mimicking as chronic pulmonary thromboembolism. 62
32201604 2020
49
Superior vena cava stenting in IgG4-associated mediastinal fibrosis. 62
32241172 2020
50
Aftermath of pulmonary tuberculosis: computed tomography assessment. 62
32322321 2020

Variations for Fibrosing Mediastinitis

Expression for Fibrosing Mediastinitis

Search GEO for disease gene expression data for Fibrosing Mediastinitis.

Pathways for Fibrosing Mediastinitis

GO Terms for Fibrosing Mediastinitis

Sources for Fibrosing Mediastinitis

2 CDC
6 CNVD
8 Cosmic
9 dbSNP
10 DGIdb
16 EFO
17 ExPASy
18 FMA
19 GARD
27 GO
28 GTR
29 HMDB
30 HPO
31 ICD10
32 ICD10 via Orphanet
33 ICD11
34 ICD9CM
35 IUPHAR
36 LifeMap
38 LOVD
40 MedGen
43 MeSH
44 MESH via Orphanet
45 MGI
48 NCI
49 NCIt
50 NDF-RT
52 NINDS
53 Novoseek
55 ODiseA
56 OMIM via Orphanet
57 OMIM® (Updated 24-Oct-2022)
61 PubChem
62 PubMed
64 QIAGEN
69 SNOMED-CT via HPO
70 Tocris
71 UMLS
72 UMLS via Orphanet
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