HV
MCID: HYD015
MIFTS: 23

Hydroa Vacciniforme (HV)

Categories: Genetic diseases, Rare diseases, Skin diseases

Aliases & Classifications for Hydroa Vacciniforme

MalaCards integrated aliases for Hydroa Vacciniforme:

Name: Hydroa Vacciniforme 52 58 71
Hv 52

Characteristics:

Orphanet epidemiological data:

58
hydroa vacciniforme
Inheritance: Not applicable; Age of onset: Childhood;

Classifications:

Orphanet: 58  
Rare skin diseases


External Ids:

ICD10 via Orphanet 33 L56.4
UMLS via Orphanet 72 C0020241
Orphanet 58 ORPHA330058
UMLS 71 C0020241

Summaries for Hydroa Vacciniforme

MalaCards based summary : Hydroa Vacciniforme, also known as hv, is related to hydroa vacciniforme, familial and hydroa vacciniforme-like lymphoma. Affiliated tissues include skin, t cells and heart.

Wikipedia : 74 Hydroa vacciniforme (HV) is a very rare, chronic photodermatitis-type skin condition with usual onset in... more...

Related Diseases for Hydroa Vacciniforme

Diseases in the Hydroa Vacciniforme family:

Hydroa Vacciniforme, Familial

Diseases related to Hydroa Vacciniforme via text searches within MalaCards or GeneCards Suite gene sharing:

(show top 50) (show all 108)
# Related Disease Score Top Affiliating Genes
1 hydroa vacciniforme, familial 13.0
2 hydroa vacciniforme-like lymphoma 12.7
3 bunion 11.6
4 lymphoma 10.9
5 cutaneous t cell lymphoma 10.8
6 lymphoproliferative syndrome 10.8
7 rare photodermatosis 10.8
8 allergic hypersensitivity disease 10.7
9 exanthem 10.6
10 chronic active epstein-barr virus infection 10.6
11 keratitis, hereditary 10.5
12 peripheral t-cell lymphoma 10.5
13 hydrops, lactic acidosis, and sideroblastic anemia 10.4
14 uveitis 10.4
15 gingivitis 10.4
16 herpes simplex 10.4
17 vasculitis 10.4
18 lupus erythematosus 10.4
19 iridocyclitis 10.4
20 splenomegaly 10.4
21 atrioventricular block 10.3
22 progressive familial heart block, type ia 10.3
23 pfeiffer syndrome 10.3
24 coproporphyria, hereditary 10.3
25 vasculitis, lymphocytic, nodular 10.3
26 halo nevi 10.3
27 hartnup disorder 10.3
28 multinucleated neurons, anhydramnios, renal dysplasia, cerebellar hypoplasia, and hydranencephaly 10.3
29 xeroderma pigmentosum, variant type 10.3
30 dermatitis, atopic 10.3
31 severe cutaneous adverse reaction 10.3
32 microcephaly, epilepsy, and diabetes syndrome 10.3
33 hypertrophic scars 10.3
34 hemophagocytic lymphohistiocytosis 10.3
35 cutaneous lupus erythematosus 10.3
36 erythema multiforme 10.3
37 variola major 10.3
38 anaplastic large cell lymphoma 10.3
39 marginal zone b-cell lymphoma 10.3
40 systemic epstein-barr virus-positive t-cell lymphoma of childhood 10.3
41 nodal marginal zone lymphoma 10.3
42 dermatomyositis 10.3
43 disseminated intravascular coagulation 10.3
44 tetanus 10.3
45 porphyria 10.3
46 iritis 10.3
47 urticaria 10.3
48 dermatitis 10.3
49 purpura 10.3
50 cellulitis 10.3

Graphical network of the top 20 diseases related to Hydroa Vacciniforme:



Diseases related to Hydroa Vacciniforme

Symptoms & Phenotypes for Hydroa Vacciniforme

Drugs & Therapeutics for Hydroa Vacciniforme

Search Clinical Trials , NIH Clinical Center for Hydroa Vacciniforme

Genetic Tests for Hydroa Vacciniforme

Anatomical Context for Hydroa Vacciniforme

MalaCards organs/tissues related to Hydroa Vacciniforme:

40
Skin, T Cells, Heart, Nk Cells, Bone, Kidney, Liver

Publications for Hydroa Vacciniforme

Articles related to Hydroa Vacciniforme:

(show top 50) (show all 261)
# Title Authors PMID Year
1
Diagnosis of T-cell lymphoid proliferations of the skin: putting all the pieces together. 61
31664155 2020
2
Epstein - Barr virus positive T and NK-cell lymphoproliferations: Morphological features and differential diagnosis. 61
31889602 2020
3
Epstein-Barr virus NK and T cell lymphoproliferative disease: report of a 2018 international meeting. 61
31833428 2019
4
Hydroa Vacciniforme-Like Lymphoma with Systemic Symptoms: Two Case Reports. 61
31896851 2019
5
Hydroa vacciniforme-like lymphoma: clinicopathological description, treatment and outcome. 61
31759090 2019
6
EBV-associated hydroa vacciniforme-like T-cell lymphoma. 61
31218678 2019
7
Recent Advances in Cutaneous T-cell Lymphoma: Diagnostic and Prognostic Considerations. 61
31352988 2019
8
Hydroa vacciniforme-like lymphoproliferative disorder: Clinicopathologic study of 41 cases. 61
30654082 2019
9
Hydroa Vacciniforme-Like Lymphoproliferative Disorder With Progression to EBV+ Cytotoxic Peripheral T-Cell Lymphoma. 61
31313696 2019
10
Clinicopathological categorization of hydroa vacciniforme-like lymphoproliferative disorder: an analysis of prognostic implications and treatment based on 19 cases. 61
31315684 2019
11
Hydroa vacciniforme-like lymphoproliferative disorder: an EBV disease with a low risk of systemic illness in whites. 61
31064750 2019
12
Deciphering hydroa vacciniforme. 61
31248873 2019
13
Cutaneous Lymphoproliferative Disorders: What's New in the Revised 4th Edition of the World Health Organization (WHO) Classification of Lymphoid Neoplasms. 61
30199396 2019
14
Hydroa vacciniforme: a distinctive form of Epstein-Barr virus-associated T-cell lymphoproliferative disorders. 61
30998212 2019
15
Photocontact Dermatitis and Its Clinical Mimics: an Overview for the Allergist. 61
29951786 2019
16
Novel mutations of STXBP2 and LYST associated with adult haemophagocytic lymphohistiocytosis with Epstein-Barr virus infection: a case report. 61
30782130 2019
17
Comparative Study of the Clinical Pathology, Immunophenotype, Epstein-Barr Virus Infection Status, and Gene Rearrangements in Adult and Child Patients With Hydroa Vacciniforme-Like Lymphoproliferative Disorder. 61
30085959 2019
18
Clinicopathological analysis of the hydroa vacciniforme-like lymphoproliferative disorder with natural killer cell phenotype compared with cutaneous natural killer T-cell lymphoma. 61
30542432 2018
19
Ocular manifestations of hydroa vacciniforme in a Black child. 61
30585497 2018
20
Hydroa vacciniforme-like lymphoproliferative disorder in an elderly Chinese patient and a literature review of adult cases. 61
29926891 2018
21
Epstein-Barr virus and skin. 61
30484521 2018
22
[Clinical and pathological features of 13 children with Epstein-Barr virus-positive lymphoproliferative disease]. 61
30293280 2018
23
A distinct subtype of Epstein-Barr virus-positive T/NK-cell lymphoproliferative disorder: adult patients with chronic active Epstein-Barr virus infection-like features. 61
29242302 2018
24
Hydroa Vacciniforme-Like Lymphoma in Tibetan Children: 2 Cases and a Literature Review. 61
28445173 2018
25
Adult-onset hydroa vacciniforme-like lymphoma in a long-term resident of the United States. 61
29693057 2018
26
Characterization of skin blister fluids from children with Epstein-Barr virus-associated lymphoproliferative disease. 61
29352500 2018
27
Hydroa vacciniforme-like cutaneous T-cell lymphoma in a child: A case report. 61
29642164 2018
28
Hydroa Vacciniforme-Like T-Cell Lymphoma: A Further Brazilian Case. 61
28248720 2018
29
Hydroa Vacciniforme-Like Cutaneous T-Cell Lymphoma in an Adult Presenting With Facial Edema and Recurrent Oral Ulceration. 61
29473835 2018
30
Overview of EBV-Associated T/NK-Cell Lymphoproliferative Diseases. 61
30662890 2018
31
Epstein-Barr Virus-Positive T/NK-Cell Lymphoproliferative Diseases in Chinese Mainland. 61
30356785 2018
32
EBV-positive lymphoproliferative disease: a case report. 61
31938185 2018
33
Adult-onset Hydroa Vacciniforme: A Rare Occurrence or a Lymphoma Premonition? 61
29204398 2017
34
Epstein-Barr Virus-Associated Vesiculopapular Eruption on the Face of a Patient with Natural Killer T Cell Lymphoma. 61
28966520 2017
35
Two cases of hydroa vacciniforme-like lymphoproliferative disease controlled by anti-inflammatory agents. 61
28543883 2017
36
Primary cutaneous T-cell lymphoma: experience from the Peruvian National Cancer Institute. 61
29166501 2017
37
Epstein-Barr Virus-associated Lymphoproliferative Disorders in the Skin. 61
28477890 2017
38
Hydroa Vacciniforme-like Skin Lesions in Epstein-Barr-Virus-associated T-cell Lymphoproliferation with Subsequent Development of Aggressive NK/T-cell Lymphoma. 61
27826612 2017
39
GATA2 Deficiency and Epstein-Barr Virus Disease. 61
29375553 2017
40
Cutaneous EBV-related lymphoproliferative disorders. 61
27988064 2017
41
Clinicopathological categorization of Epstein-Barr virus-positive T/NK-cell lymphoproliferative disease: an analysis of 42 cases with an emphasis on prognostic implications. 61
27157296 2017
42
[The understanding of Epstein-Barr virus associated lymphoproliferative disorder]. 61
28056294 2016
43
Hydroa vacciniforme and hydroa vacciniforme-like T-cell lymphoma: an uncommon event for transformation. 61
27531667 2016
44
Hydroa vacciniforme-like lymphoma. 61
27507019 2016
45
Association of GATA2 Deficiency With Severe Primary Epstein-Barr Virus (EBV) Infection and EBV-associated Cancers. 61
27169477 2016
46
Epstein-Barr virus reactivation is induced, but abortive, in cutaneous lesions of systemic hydroa vacciniforme and hypersensitivity to mosquito bites. 61
27039668 2016
47
Hydroa Vacciniforme-Like EBV-Positive Cutaneous T-Cell Lymphoma, First Report of 2 Cases in Ecuador. 61
26913846 2016
48
Mature T- and NK-cell non-Hodgkin lymphoma in children and young adolescents. 61
26992145 2016
49
Marked Increase of Circulating Double-Negative γδ T Cells in a Patient With Hydroa Vacciniforme-Like Lymphoma. 61
26915619 2016
50
Progressive scarring facial lesions in a boy. 61
26862404 2016

Variations for Hydroa Vacciniforme

Expression for Hydroa Vacciniforme

Search GEO for disease gene expression data for Hydroa Vacciniforme.

Pathways for Hydroa Vacciniforme

GO Terms for Hydroa Vacciniforme

Sources for Hydroa Vacciniforme

3 CDC
7 CNVD
9 Cosmic
10 dbSNP
11 DGIdb
17 EFO
18 ExPASy
19 FMA
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30 HMDB
31 HPO
32 ICD10
33 ICD10 via Orphanet
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37 LifeMap
39 LOVD
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43 MeSH
44 MESH via Orphanet
45 MGI
48 NCI
49 NCIt
50 NDF-RT
53 NINDS
54 Novoseek
56 OMIM
57 OMIM via Orphanet
61 PubMed
63 QIAGEN
68 SNOMED-CT via HPO
69 TGDB
70 Tocris
71 UMLS
72 UMLS via Orphanet
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