Idiopathic Hypertrophic Pachymeningitis disease: Malacards - Research Articles, Drugs, Genes, Clinical Trials

MCID: IDP081 MIFTS: 17	Idiopathic Hypertrophic Pachymeningitis Categories: Neuronal diseases, Rare diseases
Tissues Related diseases Publications Expand all tables

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Aliases & Classifications for Idiopathic Hypertrophic Pachymeningitis

MalaCards integrated aliases for Idiopathic Hypertrophic Pachymeningitis:

Name: Idiopathic Hypertrophic Pachymeningitis ⁵²

Idiopathic Hypertrophic Craniospinal Pachymeningitis ⁵²

Idiopathic Hypertrophic Cranial Pachymeningitis ⁵²

Idiopathic Hypertrophic Spinal Pachymeningitis ⁵²

Classifications:

MalaCards categories:
Global: Rare diseases
Anatomical: Neuronal diseases

See all MalaCards categories (disease lists)

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Summaries for Idiopathic Hypertrophic Pachymeningitis

NIH Rare Diseases : ⁵² Idiopathic hypertrophic pachymeningitis (IHP) is a rare disorder causing inflammation and thickening of the outer layer (dura) of the brain and/or spinal cord. IHP can be widespread or cause tumor -like lesions. Before IHP can be diagnosed, other conditions including sarcoidosis, tumors, meningioma, infections (syphilis, tuberculosis, and Lyme disease) , and autoimmune diseases ( rheumatoid arthritis , Sjogren's syndrome , Wegener's granulomatosis, and IgG4-related disease) must be ruled out. IHP often presents with headache and cranial nerve impairment . Treatment may involve prednisone and/or an immune suppressing drug. This treatment often improves symptoms, however complete recovery is rare. Surgery may be recommended for people with advanced or severe IHP. Some people with IHP have no symptoms and may not need treatment.

MalaCards based summary : Idiopathic Hypertrophic Pachymeningitis, also known as idiopathic hypertrophic craniospinal pachymeningitis, is related to igg4-related pachymeningitis and headache. Affiliated tissues include brain, spinal cord and neutrophil.

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Related Diseases for Idiopathic Hypertrophic Pachymeningitis

Diseases related to Idiopathic Hypertrophic Pachymeningitis via text searches within MalaCards or GeneCards Suite gene sharing:

(show top 50) (show all 98)

#	Related Disease	Score
1	igg4-related pachymeningitis	12.0
2	headache	10.6
3	meningioma, radiation-induced	10.5
4	meningioma, familial	10.5
5	spinal meningioma	10.5
6	secretory meningioma	10.5
7	lymphoplasmacyte-rich meningioma	10.5
8	tolosa-hunt syndrome	10.4
9	status epilepticus	10.4
10	brain edema	10.4
11	ataxia and polyneuropathy, adult-onset	10.3
12	cranial nerve palsy	10.3
13	thrombosis	10.3
14	uveitis	10.3
15	diabetes insipidus	10.3
16	autoimmune disease	10.3
17	syphilis	10.3
18	vasculitis	10.3
19	systemic autoimmune disease	10.3
20	rapidly involuting congenital hemangioma	10.3
21	quadriplegia	10.3
22	otitis media	10.2
23	sarcoidosis 1	10.2
24	3-methylglutaconic aciduria, type iii	10.2
25	igg4-related disease	10.2
26	hydrocephalus	10.2
27	pituitary apoplexy	10.2
28	neurosarcoidosis	10.2
29	papilledema	10.2
30	neuritis	10.2
31	optic nerve disease	10.2
32	anisocoria	10.1
33	migraine with or without aura 1	10.1
34	thrombophilia due to thrombin defect	10.1
35	yemenite deaf-blind hypopigmentation syndrome	10.1
36	pars planitis	10.1
37	atrioventricular block	10.1
38	horner's syndrome	10.1
39	intermediate uveitis	10.1
40	scleritis	10.1
41	polyneuropathy	10.1
42	transient cerebral ischemia	10.1
43	macular retinal edema	10.1
44	peripheral nervous system disease	10.1
45	thyroiditis	10.1
46	myocarditis	10.1
47	lymphocytic hypophysitis	10.1
48	dysphagia	10.1
49	trigeminal autonomic cephalalgia	10.1
50	lymphoma	10.1

Graphical network of the top 20 diseases related to Idiopathic Hypertrophic Pachymeningitis:

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Symptoms & Phenotypes for Idiopathic Hypertrophic Pachymeningitis

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Drugs & Therapeutics for Idiopathic Hypertrophic Pachymeningitis

Search Clinical Trials , NIH Clinical Center for Idiopathic Hypertrophic Pachymeningitis

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Genetic Tests for Idiopathic Hypertrophic Pachymeningitis

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Anatomical Context for Idiopathic Hypertrophic Pachymeningitis

MalaCards organs/tissues related to Idiopathic Hypertrophic Pachymeningitis:

⁴⁰

Brain, Spinal Cord, Neutrophil, Pituitary

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Publications for Idiopathic Hypertrophic Pachymeningitis

Articles related to Idiopathic Hypertrophic Pachymeningitis:

(show top 50) (show all 110)

#	Title	Authors	PMID	Year
1	Dark as night: Spelunking for spinal solitary fibrous tumors/hemangiopericytomas in the differential of T2 hypointensity. ⁶¹	Carlstrom LP...Morris JM	32507710	2020
2	Intracranial Inflammatory Pseudotumor Associated with Idiopathic Hypertrophic Pachymeningitis Mimicking Malignant Tumor or High-Grade Meningioma. ⁶¹	Han MS...Jung S	31704361	2020
3	Idiopathic Hypertrophic Spinal Pachymeningitis: A Diagnostic Challenge: A Case Report and Review of the Literature. ⁶¹	Alsulaiman A	32140024	2020
4	Headache and Hypoglossal Nerve Palsy in a Child With Idiopathic Hypertrophic Pachymeningitis. ⁶¹	Hsieh DT...Lotze TE	31294820	2019
5	Idiopathic Hypertrophic Spinal Pachymeningitis: A Rare Cause of Spinal Cord Compression. ⁶¹	Kutty RK...Peethambaran A	31744986	2019
6	Idiopathic Hypertrophic Pachymeningitis Mimicking Meningioma with Occlusion of Superior Sagittal Sinus: Case Report and Review of Literature. ⁶¹	Yao A...Xu B	30965168	2019
7	Cerebrospinal fluid cytokine/chemokine/growth factor profiles in idiopathic hypertrophic pachymeningitis. ⁶¹	Zhang X...Kira JI	30784775	2019
8	Letter to the editor: citations for the case report on idiopathic hypertrophic pachymeningitis by Kosuke Tsuchida et al. ⁶¹	Li SJ	30673832	2019
9	Rapidly progressive fatal idiopathic hypertrophic pachymeningitis with brainstem involvement in a child. ⁶¹	Tsuchida K...Tsutsumi H	29730790	2018
10	Hypertrophic Pachymeningitis of the Internal Auditory Canal: A Rare Case of Unilateral Sudden Sensorineural Hearing Loss. ⁶¹	Muelleman T...Staecker H	29938521	2018
11	Diplopia With Dural Fibrotic Thickening. ⁶¹	Brand B...Deputy S	29961529	2018
12	Ocular involvement in idiopathic hypertrophic pachymeningitis associated with eosinophilic angiocentric fibrosis: a case report. ⁶¹	Suarez AR...Martin FG	29924200	2018
13	Marked effectiveness of low-dose oral methotrexate for steroid-resistant idiopathic hypertrophic pachymeningitis: Case report. ⁶¹	Uchida H...Tominaga T	29510265	2018
14	Idiopathic hypertrophic pachymeningitis mimicking hemicrania continua: An unusual clinical case. ⁶¹	Russo A...Tedeschi G	28474987	2018
15	Idiopathic hypertrophic pachymeningitis as a rare cause of cervical compressive myelopathy. ⁶¹	Fukuda A...Reis F	29403257	2017
16	Bacterial meningitis due to Streptococcus pneumoniae following untreated idiopathic hypertrophic pachymeningitis. ⁶¹	Ueno T...Tomiyama M	28870586	2017
17	Concomitant idiopathic hypertrophic spinal pachymeningitis and Guillain-Barré syndrome in a patient: coincidence or a triggering mechanism? ⁶¹	Olubajo F...Arzoglou V	28644069	2017
18	A case of idiopathic hypertrophic pachymeningitis presenting with chronic headache and multiple cranial nerve palsies: A case report. ⁶¹	Huang Y...Gui L	28723776	2017
19	Letter re: Teaching NeuroImages: Idiopathic hypertrophic pachymeningitis. ⁶¹	Budhram A	28583934	2017
20	Author response: Teaching NeuroImages: Idiopathic hypertrophic pachymeningitis. ⁶¹	Wasilewski A...Samkoff L	28583935	2017
21	Rituximab Treatment for Idiopathic Hypertrophic Pachymeningitis. ⁶¹	Jang Y...Lee SK	28271643	2017
22	Central Nervous System Inflammatory Myofibroblastic Tumor Masquerading as Chronic Suppurative Otitis Media. ⁶¹	Singhal N...Tangri R	28904584	2017
23	Unilateral optic disc swelling associated with idiopathic hypertrophic pachymeningitis: a rare cause for a rare clinical finding. ⁶¹	Shankar Iyer R...Ramachandran M	28348267	2017
24	Idiopathic hypertrophic pachymeningitis: an autoimmune IgG4-related disease. ⁶¹	De Virgilio A...Greco A	27592235	2017
25	Effective Response of Methotrexate for Recurrent Idiopathic Hypertrophic Spinal Pachymeningitis. ⁶¹	Park TJ...Kim KH	28127378	2016
26	Teaching NeuroImages: Idiopathic hypertrophic pachymeningitis. ⁶¹	Wasilewski A...Samkoff L	27895252	2016
27	Report of a rare case of atypical lymphoplasmacyte-rich meningioma in the tentorium mimicking idiopathic hypertrophic pachymeningitis. ⁶¹	Cha YJ...Kim SH	26902101	2016
28	[Review of ear and nose and throat involvement in IgG4-RD]. ⁶¹	Tao X...Song B	26911076	2015
29	[IgG4- and MPO-ANCA-associated hypertrophic pachymeningitis]. ⁶¹	Aragones JM...Lucchetti G	26553176	2015
30	Idiopathic Hypertrophic Pachymeningitis in the Craniocervical Junction. ⁶¹	Bang JH...Kim EJ	26512276	2015
31	Idiopathic hypertrophic pachymeningitis mimicking prolactinoma with recurrent vision loss. ⁶¹	Lok JY...Young AL	26238133	2015
32	Infiltrative mass of the skull base and nasopharynx: A diagnostic conundrum. ⁶¹	George MM...Bhalla R	25905016	2015
33	[Lymphocytic hypophysitis and hypertrophic pachymeningitis: description of a possible case associated to IgG4 pathologies]. ⁶¹	Blanco-Canto ME...Porta-Etessam J	26005074	2015
34	Idiopathic hypertrophic spinal pachymeningitis: a case report and review of literature. ⁶¹	Qin LX...Zhang HN	25906379	2015
35	Teaching NeuroImages: Idiopathic hypertrophic spinal pachymeningitis mimicking epidural lymphoma. ⁶¹	Hsu HT...Lai PH	25732370	2015
36	Idiopathic hypertrophic pachymeningitis presenting with occipital neuralgia. ⁶¹	Auboire L...Bienvenu B	25834565	2015
37	Clinico-radiological spectrum and outcome in idiopathic hypertrophic pachymeningitis. ⁶¹	Dash GK...Radhakrishnan A	25703277	2015
38	[Optic neuropathy in a case of recurrent idiopathic hypertrophic pachymeningitis unresponsive to steroids and immunosuppressants]. ⁶¹	Palmero-Fernandez L...Garcia-Sanchez J	25443460	2015
39	[A case of bilateral ophthalmoplegia caused by focal idiopathic hypertrophic pachymeningitis on the anterior cranial fossa]. ⁶¹	Teramoto H...Kamei S	25672863	2015
40	Recurrent cerebral aneurysm formation and rupture within a short period due to invasive aspergillosis of the nasal sinus; pathological analysis of the catastrophic clinical course. ⁶¹	Shinya Y...Saito N	26722566	2015
41	Idiopathic Hypertrophic Spinal Pachymeningitis. ⁶¹	Tosa M...Nemoto N	26234238	2015
42	Interval progression of idiopathic hypertrophic pachymeningitis. ⁶¹	Sethi NK	29443163	2014
43	Arachnoid involved in idiopathic hypertrophic pachymeningitis. ⁶¹	Zhao M...Zuo H	25199674	2014
44	Pachymeningitis in a young child responded to antitubercular therapy: a case report. ⁶¹	Sharma PK...Khilnani P	24092891	2014
45	Idiopathic hypertrophic spinal pachymeningitis with an osteolytic lesion. ⁶¹	Jee TK...Eoh W	25328657	2014
46	Idiopathic hypertrophic pachymeningitis: clinical, laboratory and neuroradiologic features in China. ⁶¹	Zhao M...Zuo H	24589555	2014
47	IgG4-related hypertrophic pachymeningitis: clinical features, diagnostic criteria, and treatment. ⁶¹	Lu LX...Clark SW	24733677	2014
48	Idiopathic hypertrophic pachymeningitis at King Chulalongkorn Memorial Hospital. ⁶¹	Roongpiboonsopit D...Phanthumchinda K	24964678	2014
49	Peace sign in calcified idiopathic hypertrophic pachymeningitis. ⁶¹	Heckmann JG...Oberst G	24534041	2014
50	See no evil, hear no evil…. ⁶¹	Driscoll S...Bilyk JR	23911152	2014

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Genes for Idiopathic Hypertrophic Pachymeningitis

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Variations for Idiopathic Hypertrophic Pachymeningitis

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Expression for Idiopathic Hypertrophic Pachymeningitis

Search GEO for disease gene expression data for Idiopathic Hypertrophic Pachymeningitis.

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Pathways for Idiopathic Hypertrophic Pachymeningitis

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GO Terms for Idiopathic Hypertrophic Pachymeningitis

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