MCID: IDP095
MIFTS: 14

Idiopathic Steroid-Resistant Nephrotic Syndrome

Categories: Nephrological diseases, Rare diseases

Aliases & Classifications for Idiopathic Steroid-Resistant Nephrotic Syndrome

MalaCards integrated aliases for Idiopathic Steroid-Resistant Nephrotic Syndrome:

Name: Idiopathic Steroid-Resistant Nephrotic Syndrome 58
Idiopathic Srns 58

Classifications:

Orphanet: 58  
Rare renal diseases


External Ids:

Orphanet 58 ORPHA567548

Summaries for Idiopathic Steroid-Resistant Nephrotic Syndrome

MalaCards based summary : Idiopathic Steroid-Resistant Nephrotic Syndrome, also known as idiopathic srns, is related to focal segmental glomerulosclerosis and nephrotic syndrome. An important gene associated with Idiopathic Steroid-Resistant Nephrotic Syndrome is SMARCAL1 (SWI/SNF Related, Matrix Associated, Actin Dependent Regulator Of Chromatin, Subfamily A Like 1).

Related Diseases for Idiopathic Steroid-Resistant Nephrotic Syndrome

Graphical network of the top 20 diseases related to Idiopathic Steroid-Resistant Nephrotic Syndrome:



Diseases related to Idiopathic Steroid-Resistant Nephrotic Syndrome

Symptoms & Phenotypes for Idiopathic Steroid-Resistant Nephrotic Syndrome

Drugs & Therapeutics for Idiopathic Steroid-Resistant Nephrotic Syndrome

Search Clinical Trials , NIH Clinical Center for Idiopathic Steroid-Resistant Nephrotic Syndrome

Genetic Tests for Idiopathic Steroid-Resistant Nephrotic Syndrome

Anatomical Context for Idiopathic Steroid-Resistant Nephrotic Syndrome

Publications for Idiopathic Steroid-Resistant Nephrotic Syndrome

Articles related to Idiopathic Steroid-Resistant Nephrotic Syndrome:

(show all 50)
# Title Authors PMID Year
1
The Effect of Oral Cyclophosphamide in the Treatment of Children with Refractory Idiopathic Nephrotic Syndrome. 61
33277452 2020
2
Two cases of idiopathic steroid-resistant nephrotic syndrome complicated with thrombotic microangiopathy. 61
32746791 2020
3
Pre-emptive rituximab and plasma exchange does not prevent disease recurrence following living donor renal transplantation in high-risk idiopathic SRNS. 61
32124030 2020
4
Current understandings in treating children with steroid-resistant nephrotic syndrome. 61
32086590 2020
5
Interventions for idiopathic steroid-resistant nephrotic syndrome in children. 61
31749142 2019
6
Use of genomic and functional analysis to characterize patients with steroid-resistant nephrotic syndrome. 61
29982877 2018
7
Treatment of Genetic Forms of Nephrotic Syndrome. 61
29632851 2018
8
Non-Autoimmune Subclinical and Overt Hypothyroidism in Idiopathic Steroid-resistant Nephrotic Syndrome in Children. 61
28849770 2017
9
A Randomized Controlled Trial of Intravenous versus Oral Cyclophosphamide in Steroid-resistant Nephrotic Syndrome in Children. 61
29217878 2017
10
Mycophenolate mofetil is inferior to tacrolimus in sustaining remission in children with idiopathic steroid-resistant nephrotic syndrome. 61
28318625 2017
11
Childhood idiopathic steroid-resistant nephrotic syndrome at a Single Center in Khartoum. 61
28748888 2017
12
Interventions for idiopathic steroid-resistant nephrotic syndrome in children. 61
27726125 2016
13
Childhood Idiopathic Steroid Resistant Nephrotic Syndrome, Different Drugs And Outcome. 61
28718558 2016
14
Favorable outcome in children with idiopathic steroid-resistant nephrotic syndrome due to mesangial hypercellularity: A distinct disease entity? 61
26493069 2016
15
Long-term outcome of idiopathic steroid-resistant nephrotic syndrome in children: response to comments. 61
26628279 2016
16
Long-term outcome of idiopathic steroid-resistant nephrotic syndrome in children. 61
26335197 2016
17
Immunosuppressive therapy in children with steroid-resistant, frequently-relapsing, and steroid-dependent idiopathic nephrotic syndrome: a single center experience. 61
27054016 2016
18
Cyclosporine in the treatment of childhood idiopathic steroid resistant nephrotic syndrome: a single centre experience in Nigeria. 61
28293374 2016
19
Trends in the histopathology of childhood nephrotic syndrome in Ibadan Nigeria: preponderance of idiopathic focal segmental glomerulosclerosis. 61
26670137 2015
20
Mycophenolate Mofetil Following Rituximab in Children With Steroid-Resistant Nephrotic Syndrome. 61
26101364 2015
21
HISTOPATHOLOGICAL PATTERNS IN PAEDIATRIC IDIOPATHIC STEROID RESISTANT NEPHROTIC SYNDROME. 61
26721026 2015
22
NPHS2 R229Q polymorphism in steroid resistant nephrotic syndrome: is it responsive to immunosuppressive therapy? 61
24519673 2014
23
Effect of galactose on glomerular permeability and proteinuria in steroid-resistant nephrotic syndrome. 61
23793883 2013
24
R: Histological patterns of idiopathic steroid resistant nephrotic syndrome in Egyptian children: A single centre study. 61
24475443 2013
25
Distinct metabolic profile of primary focal segmental glomerulosclerosis revealed by NMR-based metabolomics. 61
24244321 2013
26
Histological patterns of idiopathic steroid resistant nephrotic syndrome in Egyptian children: A single centre study. 61
24475425 2013
27
Treatment with tacrolimus and prednisolone is preferable to intravenous cyclophosphamide as the initial therapy for children with steroid-resistant nephrotic syndrome. 61
22763815 2012
28
[Idiopathic steroid-resistant nephrotic syndrome in child : study of 20 cases]. 61
21681713 2011
29
Rituximab for refractory cases of childhood nephrotic syndrome. 61
21279725 2011
30
Histopathological spectrum of childhood idiopathic steroid-resistant nephrotic syndrome in Tunisia. 61
21387228 2011
31
Interventions for idiopathic steroid-resistant nephrotic syndrome in children. 61
21069676 2010
32
Childhood idiopathic steroid resistant nephrotic syndrome in Southwestern Nigeria. 61
20814150 2010
33
Cyclosporine A and steroid therapy in childhood steroid-resistant nephrotic syndrome. 61
21694937 2010
34
The long-term results of pediatric patients with primary focal and segmental glomerulosclerosis. 61
20061699 2010
35
Long-term outcome of idiopathic steroid-resistant nephrotic syndrome: a multicenter study. 61
19280229 2009
36
SMARCAL1 mutations: a cause of prepubertal idiopathic steroid-resistant nephrotic syndrome. 61
19127206 2009
37
Efficacy and safety of tacrolimus versus cyclosporine in children with steroid-resistant nephrotic syndrome: a randomized controlled trial. 61
19268410 2009
38
Management of steroid resistant nephrotic syndrome. 61
19179716 2009
39
Efficacy of intravenous pulse cyclophosphamide treatment versus combination of intravenous dexamethasone and oral cyclophosphamide treatment in steroid-resistant nephrotic syndrome. 61
18566839 2008
40
Pathophysiology of focal segmental glomerulosclerosis. 61
17216262 2007
41
The clinical effectiveness and cost-effectiveness of treatments for children with idiopathic steroid-resistant nephrotic syndrome: a systematic review. 61
17537341 2007
42
Interventions for idiopathic steroid-resistant nephrotic syndrome in children. 61
16625586 2006
43
Steroid resistant nephrotic syndrome: role of histopathology. 61
16465008 2006
44
Short term efficacy of intravenous dexamethasone and methylprednisolone therapy in steroid resistant nephrotic syndrome. 61
15523124 2004
45
Interventions for idiopathic steroid-resistant nephrotic syndrome in children. 61
15106208 2004
46
Pulse methylprednisolone treatment of idiopathic steroid-resistant nephrotic syndrome. 61
11956887 2002
47
Treatment of focal glomerulosclerosis with pulse steroids and oral cyclophosphamide. 61
11685598 2001
48
Pulse methylprednisolone treatment of idiopathic steroid-resistant nephrotic syndrome. 61
11322372 2001
49
Long-term therapy with enalapril in patients with nephrotic-range proteinuria. 61
8897561 1996
50
Recurrent nephrotic syndrome with three successive renal allografts. 61
6758572 1981

Variations for Idiopathic Steroid-Resistant Nephrotic Syndrome

Expression for Idiopathic Steroid-Resistant Nephrotic Syndrome

Search GEO for disease gene expression data for Idiopathic Steroid-Resistant Nephrotic Syndrome.

Pathways for Idiopathic Steroid-Resistant Nephrotic Syndrome

GO Terms for Idiopathic Steroid-Resistant Nephrotic Syndrome

Sources for Idiopathic Steroid-Resistant Nephrotic Syndrome

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33 ICD10 via Orphanet
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45 MESH via Orphanet
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49 NCI
50 NCIt
51 NDF-RT
53 NINDS
54 Novoseek
56 OMIM via Orphanet
57 OMIM® (Updated 05-Mar-2021)
61 PubMed
63 QIAGEN
68 SNOMED-CT via HPO
69 TGDB
70 Tocris
71 UMLS
72 UMLS via Orphanet
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