ILVEN
MCID: INF057
MIFTS: 26

Inflammatory Linear Verrucous Epidermal Nevus (ILVEN)

Categories: Cancer diseases, Rare diseases, Skin diseases

Aliases & Classifications for Inflammatory Linear Verrucous Epidermal Nevus

MalaCards integrated aliases for Inflammatory Linear Verrucous Epidermal Nevus:

Name: Inflammatory Linear Verrucous Epidermal Nevus 54 60 74
Verrucous Epidermal Nevus 54 74
Verrucous Nevus 54 60
Ilven 54 60
Inflammatory Linear Verrucous Epidermal Naevus 54
Linear Verrucose Epidermal Nevus 54
Linear Verrucous Epidermal Nevus 74

Classifications:

Orphanet: 60  
Rare skin diseases


External Ids:

ICD10 via Orphanet 35 Q82.5
UMLS via Orphanet 75 C0362030 C0473574

Summaries for Inflammatory Linear Verrucous Epidermal Nevus

NIH Rare Diseases : 54 Inflammatory linear verrucous epidermal nevus (ILVEN) is a type of skin overgrowth, called epidermal nevus. It is characterized by skin colored, brown, or reddish, wart-like papules (nevi). The nevi join to form patches or plaques that often follow a pattern on the skin known as the "lines of Blaschko". The affected areas of the skin may be red, itchy, and inflamed. ILVEN typically presents from birth to early childhood and often is limited to one side of the lower half of the body. It affects females more often than males. It usually occurs alone; however, rarely ILVEN can be associated with other symptoms as part of an epidermal nevus syndrome. Rarely, ILVEN can become cancerous (for example, basal cell carcinoma or squamous cell carcinoma). ILVEN is caused by a genetic change that occurs after conception (somatic mutation). How this alteration leads to the signs and symptoms of ILVEN is not well understood. There is no one treatment or cure for ILVEN. Products used to soften the skin (emollients), moisturizers, and topical steroids may be utilized to relieve symptoms of dryness and itching. Recently, several patients have been treated with laser therapy with good results.

MalaCards based summary : Inflammatory Linear Verrucous Epidermal Nevus, also known as verrucous epidermal nevus, is related to verrucous nevus acanthokeratolytic and linear verrucous nevus syndrome. An important gene associated with Inflammatory Linear Verrucous Epidermal Nevus is CD8A (CD8a Molecule). Affiliated tissues include skin and testes.

Wikipedia : 77 Inflammatory Linear Verrucous Epidermal Nevus (ILVEN) is a rare disease of the skin that presents as... more...

Related Diseases for Inflammatory Linear Verrucous Epidermal Nevus

Graphical network of the top 20 diseases related to Inflammatory Linear Verrucous Epidermal Nevus:



Diseases related to Inflammatory Linear Verrucous Epidermal Nevus

Symptoms & Phenotypes for Inflammatory Linear Verrucous Epidermal Nevus

Drugs & Therapeutics for Inflammatory Linear Verrucous Epidermal Nevus

Search Clinical Trials , NIH Clinical Center for Inflammatory Linear Verrucous Epidermal Nevus

Genetic Tests for Inflammatory Linear Verrucous Epidermal Nevus

Anatomical Context for Inflammatory Linear Verrucous Epidermal Nevus

MalaCards organs/tissues related to Inflammatory Linear Verrucous Epidermal Nevus:

42
Skin, Testes

Publications for Inflammatory Linear Verrucous Epidermal Nevus

Articles related to Inflammatory Linear Verrucous Epidermal Nevus:

(show top 50) (show all 89)
# Title Authors Year
1
Successful treatment of inflammatory linear verrucous epidermal nevus (ILVEN) with 308-nm excimer laser: Patient patient required. ( 30648292 )
2019
2
Inflammatory linear verrucous epidermal nevus treated successfully with crisaborole ointment in a 5-year-old boy. ( 30838675 )
2019
3
A case of cutaneous horn arising in verrucous epidermal nevus. ( 29536972 )
2019
4
Inflammatory linear verrucous epidermal nevus associated with erosive monoarthritis. ( 29974513 )
2018
5
Reconstruction of a buttock defect after excision of inflammatory linear verrucous epidermal nevus. ( 29624795 )
2018
6
Successful Treatment of Inflammatory Linear Verrucous Epidermal Nevus with Concomitant Psoriasis Using Etanercept. ( 29606943 )
2018
7
Widely Spread Unilateral Inflammatory Linear Verrucous Epidermal Nevus (ILVEN). ( 30022937 )
2018
8
Treatment of inflammatory linear verrucous epidermal nevus pruritus with thalidomide. ( 30091521 )
2018
9
Inflammatory linear verrucous epidermal nevus responsive to 308-nm excimer laser treatment. ( 30235359 )
2018
10
Verruciform xanthoma overlying inflammatory linear verrucous epidermal nevus and in broad segmental distribution. ( 30337284 )
2018
11
Successful treatment of verrucous epidermal nevus with fractional micro-plasma radio-frequency technology and photodynamic therapy. ( 30130422 )
2018
12
Appearance of Verruca Over Linear Verrucous Epidermal Nevus - An Example of Locus Minoris Resistentiae: A Report of Three Cases. ( 30258804 )
2018
13
Dermoscopy of linear dermatosis along Blaschko's line in childhood: Lichen striatus versus inflammatory linear verrucous epidermal nevus. ( 28925078 )
2017
14
Is Ki-67, keratin 16, involucrin, and filaggrin immunostaining sufficient to diagnose inflammatory linear verrucous epidermal nevus? A report of eight cases and a comparison with psoriasis vulgaris. ( 29166506 )
2017
15
A Case of "Inflammatory Linear Verrucous Epidermal Nevus" (ILVEN) Treated with CO2 Laser Ablation. ( 28785331 )
2017
16
Inflammatory linear verrucous epidermal nevus: an unusual manifestation. ( 26426377 )
2017
17
Nevoid Psoriasis Coexisting with Verrucous Epidermal Nevus. ( 28405565 )
2017
18
Massive Vulvar Linear Verrucous Epidermal Nevus Presenting at Menarche. ( 28093318 )
2017
19
Inflammatory linear verrucous epidermal nevus with a postzygotic GJA1 mutation is a mosaic erythrokeratodermia variabilis et progressiva. ( 27890787 )
2016
20
Dermoscopy of verrucous epidermal nevus: large brown circles as a novel feature for diagnosis. ( 26475079 )
2016
21
Squamous cell carcinoma arising in a multiple verrucous epidermal nevus. ( 28300931 )
2016
22
Inflammatory linear verrucous epidermal nevus and regional odontodysplasia: A rare sorority. ( 26752881 )
2015
23
Genital/Perigenital Inflammatory Linear Verrucous Epidermal Nevus: A Case Series. ( 26677274 )
2015
24
A Case of Inflammatory Linear Verrucous Epidermal Nevus on the Upper Eyelid. ( 26120188 )
2015
25
Bilateral Systematized Epidermolytic Verrucous Epidermal Nevus: A Rare Entity. ( 26288413 )
2015
26
Verrucous epidermal nevus (VEN) successfully treated with indocyanine green (ICG) photodynamic therapy (PDT). ( 27051764 )
2015
27
Inflammatory linear verrucous epidermal nevus with psoriasiform histology. ( 24700964 )
2014
28
A novel technique used in the treatment of inflammatory linear verrucous epidermal nevus: tangential excision. ( 25192746 )
2014
29
The challenge to diagnose a clinical case of inflammatory linear verrucous epidermal nevus: is there any ILVEN associated with human papillomavirus infection? ( 25467274 )
2014
30
Inflammatory linear verrucous epidermal nevus: why a combined laser therapy. ( 23692514 )
2013
31
Inflammatory linear verrucous epidermal nevus in perineum and vulva: a report of two rare cases. ( 23716825 )
2013
32
Involucrin in the differential diagnosis between linear psoriasis and inflammatory linear verrucous epidermal nevus: a report of one case. ( 24068133 )
2013
33
Vulvar and perianal condyloma superimposed inflammatory linear verrucous epidermal nevus: a case report and review of the literature. ( 24396613 )
2013
34
Inflammatory linear verrucous epidermal nevus. ( 24640220 )
2013
35
Inflammatory linear verrucous epidermal nevus and epilepsy: remission during valproic acid therapy. ( 23377323 )
2013
36
A diagnostic dilemma: inflammatory linear verrucous epidermal nevus versus linear psoriasis. ( 23149170 )
2013
37
Is it inflammatory linear verrucous epidermal nevus or linear psoriasis? ( 23652072 )
2013
38
Treatment of inflammatory linear verrucous epidermal nevus with 2940A nm erbium fractional laser. ( 24112692 )
2013
39
Giant inflammatory linear verrucous epidermal nevus: successfully treated with full thickness excision and skin grafting. ( 24249899 )
2013
40
Multiple basal cell carcinomas arising in a verrucous epidermal nevus. ( 23488626 )
2013
41
Development of squamous cell carcinoma on an inflammatory linear verrucous epidermal nevus in the genital area. ( 22838090 )
2012
42
Carbon dioxide laser: first-line therapy in vulvar inflammatory linear verrucous epidermal nevus. ( 22591503 )
2012
43
Inflammatory linear verrucous epidermal nevus of the digits treated with surgical excision and skin grafting. ( 22882733 )
2012
44
Feline epidermal nevi resembling human inflammatory linear verrucous epidermal nevus. ( 22672841 )
2012
45
Dermacase. Can you identify this condition? Inflammatory linear verrucous epidermal nevus. ( 22423022 )
2012
46
Inflammatory linear verrucous epidermal nevus with genital involvement. ( 22545330 )
2012
47
Inflammatory linear verrucous epidermal nevus syndrome with its polymorphic presentation - A rare case report. ( 22557913 )
2012
48
Epidermolytic hyperkeratosis in inflammatory linear verrucous epidermal nevus. ( 21772595 )
2011
49
Extensive, adulthood inflammatory linear verrucous epidermal nevus associated with mucinous nevus. ( 21860165 )
2011
50
Successful treatment with trichloroacetic acid peeling for inflammatory linear verrucous epidermal nevus. ( 20507413 )
2010

Variations for Inflammatory Linear Verrucous Epidermal Nevus

Cosmic variations for Inflammatory Linear Verrucous Epidermal Nevus:

9
# Cosmic Mut ID Gene Symbol COSMIC Disease Classification
(Primary site, Site subtype, Primary histology, Histology subtype)
Mutation CDS Mutation AA GRCh38 Location Conf
1 COSM760 PIK3CA skin,NS,epidermal nevus,linear verrucous c.1624G>A p.E542K 3:179218294-179218294 0
2 COSM33765 AKT1 skin,NS,epidermal nevus,linear verrucous c.49G>A p.E17K 14:104780214-104780214 0

Expression for Inflammatory Linear Verrucous Epidermal Nevus

Search GEO for disease gene expression data for Inflammatory Linear Verrucous Epidermal Nevus.

Pathways for Inflammatory Linear Verrucous Epidermal Nevus

GO Terms for Inflammatory Linear Verrucous Epidermal Nevus

Sources for Inflammatory Linear Verrucous Epidermal Nevus

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