LVHT
MCID: LFT003
MIFTS: 54

Left Ventricular Noncompaction (LVHT)

Categories: Blood diseases, Cardiovascular diseases, Fetal diseases, Genetic diseases, Rare diseases

Aliases & Classifications for Left Ventricular Noncompaction

MalaCards integrated aliases for Left Ventricular Noncompaction:

Name: Left Ventricular Noncompaction 12 52 25 58 36 29 6 15 71
Left Ventricular Hypertrabeculation 12 52 25 58
Noncompaction Cardiomyopathy 25 6 71
Spongy Myocardium 52 25 58
Left Ventricular Myocardial Noncompaction Cardiomyopathy 25 71
Lvnc 52 58
Isolated Noncompaction of the Ventricular Myocardium 25
Non-Compaction of the Left Ventricular Myocardium 25
Left Ventricular Non-Compaction 25
Ventricular Noncompaction, Left 39
Non-Compaction Cardiomyopathy 17
Hypertrabeculation Syndrome 25
Honeycomb Myocardium 25
Fetal Myocardium 25
Lvht 25

Characteristics:

Orphanet epidemiological data:

58
left ventricular noncompaction
Inheritance: Autosomal dominant,Mitochondrial inheritance,X-linked recessive; Age of onset: All ages;

Classifications:



External Ids:

Disease Ontology 12 DOID:0060480
KEGG 36 H01216
ICD10 via Orphanet 33 I42.8
UMLS via Orphanet 72 C1960469
Orphanet 58 ORPHA54260
UMLS 71 C1839832 C1960469 C3164472

Summaries for Left Ventricular Noncompaction

Genetics Home Reference : 25 Left ventricular noncompaction is a heart (cardiac) muscle disorder that occurs when the lower left chamber of the heart (left ventricle), which helps the heart pump blood, does not develop correctly. Instead of the muscle being smooth and firm, the cardiac muscle in the left ventricle is thick and appears spongy. The abnormal cardiac muscle is weak and has an impaired ability to pump blood because it either cannot completely contract or it cannot completely relax. For the heart to pump blood normally, cardiac muscle must contract and relax fully. Some individuals with left ventricular noncompaction experience no symptoms at all; others have heart problems that can include sudden cardiac death. Additional signs and symptoms include abnormal blood clots, irregular heart rhythm (arrhythmia), a sensation of fluttering or pounding in the chest (palpitations), extreme fatigue during exercise (exercise intolerance), shortness of breath (dyspnea), fainting (syncope), swelling of the legs (lymphedema), and trouble laying down flat. Some affected individuals have features of other heart defects. Left ventricular noncompaction can be diagnosed at any age, from birth to late adulthood. Approximately two-thirds of individuals with left ventricular noncompaction develop heart failure.

MalaCards based summary : Left Ventricular Noncompaction, also known as left ventricular hypertrabeculation, is related to left ventricular noncompaction 1 and left ventricular noncompaction 2. An important gene associated with Left Ventricular Noncompaction is MYH7 (Myosin Heavy Chain 7), and among its related pathways/superpathways are Cardiac muscle contraction and Cardiac conduction. The drugs Insulin, Globin Zinc and insulin have been mentioned in the context of this disorder. Affiliated tissues include heart, testes and kidney, and related phenotypes are cardiovascular system and homeostasis/metabolism

Disease Ontology : 12 An intrinsic cardiomyopathy characterized by distinctive (spongy) morphological appearance of the LV myocardium.

NIH Rare Diseases : 52 Left ventricular noncompaction (LVNC) is a rare heart condition. In LVNC the inside wall of the heart is spongy or grooved, instead of smooth. Signs and symptoms of LVNC vary, but may cause life-threatening abnormal heart rhythms and weakness of the heart muscle. Treatments, such as blood thinning medication and defibrillators , are available to control these heart symptoms. In rare cases, heart transplantation is needed.

KEGG : 36 Left ventricular noncompaction (LVNC) is a rare and potentially progressive cardiomyopathy, characterized by the presence of prominent trabeculations of the left ventricle, associated with progressive systolic failure, stroke and arrhythmia. It has been linked to mutations in several genes, including LIM domain binding protein 3 (ZASP), alpha-dystrobrevin (DTNA), and genes encoding the sarcomeric proteins, beta-myosin heavy chain (MYH7), alpha-cardiac actin (ACTC), and cardiac troponin T (TNNT2).

Wikipedia : 74 Non-compaction cardiomyopathy (NCC), is a rare congenital cardiomyopathy that affects both children and... more...

Related Diseases for Left Ventricular Noncompaction

Diseases in the Left Ventricular Noncompaction family:

Left Ventricular Noncompaction 1 Left Ventricular Noncompaction 2
Left Ventricular Noncompaction 7 Left Ventricular Noncompaction 8
Left Ventricular Noncompaction 10

Diseases related to Left Ventricular Noncompaction via text searches within MalaCards or GeneCards Suite gene sharing:

(showing 420, show less)
# Related Disease Score Top Affiliating Genes
1 left ventricular noncompaction 1 35.6 LDB3 DTNA
2 left ventricular noncompaction 2 35.3 TTN LVNC2
3 cardiomyopathy, dilated, 1e 34.7 TTN TPM1 SCN5A NKX2-5 MYH7 LMNA
4 cardiomyopathy, dilated, 1d 34.3 TNNT2 LDB3
5 barth syndrome 34.0 TAZ MYH7 MYBPC3 LDB3 DTNA
6 atrial standstill 1 32.7 TTN TPM1 TNNT2 TAZ SCN5A PKP2
7 dilated cardiomyopathy 32.3 TTN TPM1 TNNT2 TAZ SCN5A PRDM16
8 congestive heart failure 32.2 TTN TNNT2 SCN5A MYH7 MYBPC3 LMNA
9 cardiac conduction defect 32.2 SCN5A MYH7 MYBPC3 LMNA
10 hypertrophic cardiomyopathy 32.1 TTN TPM1 TNNT2 TAZ SCN5A PRDM16
11 heart septal defect 32.0 TNNT2 NKX2-5 ACTC1
12 rare cardiomyopathy 32.0 TTN TPM1 TNNT2 TAZ PKP2 MYH7
13 myopathy 32.0 TTN TPM1 TNNT2 TAZ MYH7B MYH7
14 progressive familial heart block, type ia 32.0 TTN SCN5A MYBPC3
15 heart disease 31.9 TTN TNNT2 TAZ SCN5A PKP2 NKX2-5
16 syncope 31.9 TTN TNNT2 SCN5A
17 left bundle branch hemiblock 31.9 TNNT2 SCN5A PKP2 LMNA
18 cardiac arrest 31.7 TTN TNNT2 SCN5A MYH7 MYBPC3
19 ventricular fibrillation, paroxysmal familial, 1 31.7 TNNT2 SCN5A NKX2-5
20 atrial heart septal defect 31.7 TTN TNNT2 SCN5A NKX2-5 MYH7 ACTC1
21 familial isolated dilated cardiomyopathy 31.7 TTN TPM1 TNNT2 TAZ SCN5A PRDM16
22 atrioventricular block 31.7 TTN SCN5A NKX2-5 MYH7 LMNA
23 peripartum cardiomyopathy 31.7 TTN SCN5A MYH7
24 muscular dystrophy 31.6 TTN TNNT2 PKP2 NKX2-5 MYH7 LMNA
25 lipoprotein quantitative trait locus 31.5 TNNT2 SCN5A NKX2-5 LDB3
26 ebstein anomaly 31.5 TPM1 TNNT2 SCN5A NKX2-5 MYH7 MYBPC3
27 long qt syndrome 31.5 TTN SCN5A PKP2 MYH7 MYBPC3 LMNA
28 sick sinus syndrome 31.5 TTN SCN5A LMNA
29 neuromuscular disease 31.5 TTN SCN5A MYH7 LMNA LDB3
30 cardiomyopathy, familial hypertrophic, 4 31.5 TTN TPM1 TNNT2 MYH7 MYBPC3
31 restrictive cardiomyopathy 31.4 TTN TPM1 TNNT2 PRDM16 MYH7 MYBPC3
32 wolff-parkinson-white syndrome 31.4 TNNT2 SCN5A NKX2-5 MYH7 MYBPC3
33 atrial fibrillation 31.4 TTN TNNT2 SCN5A MYH7 MYBPC3 LMNA
34 catecholaminergic polymorphic ventricular tachycardia 31.4 TPM1 TNNT2 SCN5A PKP2 MYH7 MYBPC3
35 tetralogy of fallot 31.4 TPM1 TNNT2 SCN5A NKX2-5 ACTC1
36 brugada syndrome 31.3 TTN TPM1 TNNT2 SCN5A PKP2 NKX2-5
37 congenital fiber-type disproportion 31.2 TTN MYH7 LMNA ACTC1
38 arrhythmogenic right ventricular cardiomyopathy 31.2 TTN SCN5A PKP2 MYH7 LMNA LDB3
39 noonan syndrome with multiple lentigines 31.1 TNNT2 TAZ SCN5A NKX2-5 MYH7 MYBPC3
40 first-degree atrioventricular block 31.1 SCN5A MYH7 LMNA
41 myofibrillar myopathy 31.1 TTN MYH7 LMNA LDB3
42 cardiomyopathy, familial hypertrophic, 1 31.1 TTN TPM1 TNNT2 MYH7B MYH7 MYBPC3
43 aortic valve disease 2 31.1 TTN TNNT2 NKX2-5 MYH7 MYBPC3
44 laminopathy 31.1 SCN5A LMNA
45 muscular dystrophy, congenital, lmna-related 31.0 TTN MYH7 LMNA LDB3 DTNA
46 holt-oram syndrome 31.0 NKX2-5 MYH7 LMNA
47 second-degree atrioventricular block 30.8 TAZ SCN5A
48 patent foramen ovale 30.7 TNNT2 NKX2-5 ACTC1
49 cardiomyopathy, dilated, 1c, with or without left ventricular noncompaction 12.9
50 left ventricular noncompaction 7 12.8
51 left ventricular noncompaction 8 12.8
52 left ventricular noncompaction 10 12.8
53 cardiomyopathy, dilated, 1aa, with or without left ventricular noncompaction 12.7
54 cardiomyopathy, dilated, 1r 12.2
55 mental retardation, x-linked, syndromic 34 12.1
56 3-methylglutaconic aciduria, type v 11.7
57 cardioencephalomyopathy, fatal infantile, due to cytochrome c oxidase deficiency 4 11.5
58 combined oxidative phosphorylation deficiency 31 11.5
59 cardiomyopathy, dilated, 1b 10.8 TTN SCN5A MYH7 MYBPC3 LMNA
60 familial isolated arrhythmogenic ventricular dysplasia, left dominant form 10.8 TTN PKP2 LMNA LDB3
61 familial isolated arrhythmogenic ventricular dysplasia, biventricular form 10.8 TTN PKP2 LMNA LDB3
62 familial isolated arrhythmogenic ventricular dysplasia, right dominant form 10.8 TTN PKP2 LMNA LDB3
63 ventricular tachycardia, catecholaminergic polymorphic, 1, with or without atrial dysfunction and/or dilated cardiomyopathy 10.8 SCN5A PKP2 MYH7 DTNA
64 muscular disease 10.8 TTN MYH7 LMNA
65 congenital structural myopathy 10.7 TTN TPM1 MYH7
66 intrinsic cardiomyopathy 10.7 TTN TPM1 TNNT2 TAZ SCN5A PKP2
67 myopathy, myofibrillar, 1 10.7 TTN LMNA LDB3
68 long qt syndrome 1 10.7 TNNT2 SCN5A PKP2 NKX2-5 MYH7 MYBPC3
69 familial atrial fibrillation 10.7 TTN SCN5A PKP2 NKX2-5 MYH7 MYBPC3
70 progressive familial heart block 10.7 TNNT2 SCN5A NKX2-5
71 isolated elevated serum creatine phosphokinase levels 10.7 TTN SCN5A LMNA
72 tricuspid valve disease 10.7 TAZ NKX2-5 MYH7
73 rigid spine muscular dystrophy 1 10.7 TTN MYH7 LMNA
74 heart conduction disease 10.7 TNNT2 SCN5A PKP2
75 anomalous left coronary artery from the pulmonary artery 10.7 TAZ PKP2
76 cardiomyopathy, dilated, 1dd 10.7 TTN LDB3
77 hypoplastic left heart syndrome 10.6 TNNT2 TAZ NKX2-5
78 arrhythmogenic right ventricular dysplasia, familial, 1 10.6 TTN PKP2
79 reducing body myopathy 1a 10.6 TTN LDB3
80 muscle tissue disease 10.6 TTN MYH7 LMNA
81 ventricular septal defect 10.6
82 autosomal recessive limb-girdle muscular dystrophy type 2g 10.5 TTN LMNA
83 pulmonary hypertension 10.5
84 unclassified cardiomyopathy 10.5
85 autosomal recessive limb-girdle muscular dystrophy type 2a 10.5 TTN LMNA
86 aortic valve disease 1 10.5
87 patent ductus arteriosus 1 10.4
88 coarctation of aorta 10.4
89 mitral valve insufficiency 10.4
90 third-degree atrioventricular block 10.4 TTN SCN5A
91 hyperlipoproteinemia, type iii 10.4
92 chromosomal triplication 10.4
93 fabry disease 10.3
94 aortic valve insufficiency 10.3
95 alacrima, achalasia, and mental retardation syndrome 10.3
96 heterotaxy 10.3
97 ptosis 10.3
98 arteries, anomalies of 10.3
99 stroke, ischemic 10.3
100 patau syndrome 10.3
101 myocarditis 10.3
102 double-orifice mitral valve 10.3
103 hyaline body myopathy 10.2 TTN MYH7
104 cystinuria 10.2
105 hypotonia-cystinuria syndrome 10.2
106 sotos syndrome 1 10.2
107 systemic lupus erythematosus 10.2
108 endocardial fibroelastosis 10.2
109 muscular dystrophy, becker type 10.2
110 muscular dystrophy, duchenne type 10.2
111 progressive familial heart block, type ib 10.2
112 sinoatrial node disease 10.2
113 right bundle branch block 10.2
114 hypothyroidism 10.2
115 tricuspid valve insufficiency 10.2
116 lupus erythematosus 10.2
117 47,xyy 10.2
118 aneurysm 10.2
119 hypotonia 10.2
120 cardiogenic shock 10.2
121 metabolic myopathy 10.2
122 inclusion body myositis 10.2
123 myositis 10.2
124 anemia, x-linked, with or without neutropenia and/or platelet abnormalities 10.2
125 deficiency anemia 10.2
126 charcot-marie-tooth disease 10.2
127 tooth disease 10.2
128 hereditary neuropathies 10.2
129 cor triatriatum 10.2
130 hereditary spherocytosis 10.2
131 centronuclear myopathy 10.2
132 cardiac arrhythmia 10.1
133 ceroid lipofuscinosis, neuronal, 3 10.1
134 netherton syndrome 10.1
135 orthostatic intolerance 10.1
136 coronary heart disease 1 10.1
137 chromosome 1p36 deletion syndrome 10.1
138 myocardial infarction 10.1
139 cardiomyopathy, familial hypertrophic, 10 10.1
140 ataxia, combined cerebellar and peripheral, with hearing loss and diabetes mellitus 10.1
141 metabolic acidosis 10.1
142 3-methylglutaconic aciduria 10.1
143 sensorineural hearing loss 10.1
144 pulmonary edema 10.1
145 emery-dreifuss muscular dystrophy 10.1
146 neutropenia 10.1
147 endomyocardial fibrosis 10.1
148 polyneuropathy 10.1
149 gonadal dysgenesis 10.1
150 neuronal ceroid lipofuscinosis 10.1
151 turner syndrome 10.1
152 lactic acidosis 10.1
153 heart valve disease 10.1
154 inherited metabolic disorder 10.1
155 hypoglycemia 10.1
156 dystrophinopathies 10.1
157 mitochondrial disorders 10.1
158 familial sick sinus syndrome 10.1
159 rosai-dorfman disease 10.1
160 qualitative or quantitative defects of dystrophin 10.1
161 muscular lipidosis 10.1
162 spondyloarthropathy 1 10.1
163 cleft palate, isolated 10.1
164 cornelia de lange syndrome 1 10.1
165 laryngomalacia 10.1
166 renal hypodysplasia/aplasia 1 10.1
167 epidermolysis bullosa simplex with muscular dystrophy 10.1
168 myopathy, congenital 10.1
169 myopathy, congenital, with fiber-type disproportion 10.1
170 naxos disease 10.1
171 astigmatism 10.1
172 kawasaki disease 10.1
173 palmoplantar keratoderma and woolly hair 10.1
174 endocervical adenocarcinoma 10.1
175 autism spectrum disorder 10.1
176 aphasia 10.1
177 apraxia 10.1
178 aortic dissection 10.1
179 familial woolly hair syndrome 10.1
180 mumps 10.1
181 cornelia de lange syndrome 10.1
182 inflammatory spondylopathy 10.1
183 nephronophthisis 10.1
184 pulmonary tuberculosis 10.1
185 cystic kidney disease 10.1
186 palmoplantar keratosis 10.1
187 acute myocarditis 10.1
188 epidermolysis bullosa simplex 10.1
189 subvalvular aortic stenosis 10.1
190 anterolateral myocardial infarction 10.1
191 apical myocardial infarction 10.1
192 spondylitis 10.1
193 situs inversus 10.1
194 cocaine abuse 10.1
195 cataract 10.1
196 appendicitis 10.1
197 lung disease 10.1
198 vasculitis 10.1
199 cleft lip 10.1
200 acute myocardial infarction 10.1
201 primary ciliary dyskinesia 10.1
202 epidermolysis bullosa with pyloric atresia 10.1
203 48,xyyy 10.1
204 aortopulmonary window 10.1
205 bidirectional tachycardia 10.1
206 single ventricular heart 10.1
207 seizure disorder 10.1
208 congenital left ventricular aneurysm 10.1
209 ciliopathy 10.1
210 focal palmoplantar keratoderma 10.1
211 dextrocardia 10.1
212 charcot-marie-tooth disease, demyelinating, type 1a 10.1
213 myotonic dystrophy 1 10.1
214 pulmonary hypertension, primary, 1 10.1
215 enterocolitis 10.1
216 friedreich ataxia 10.1
217 multiple acyl-coa dehydrogenase deficiency 10.1
218 hemochromatosis, type 1 10.1
219 osteogenic sarcoma 10.1
220 ataxia and polyneuropathy, adult-onset 10.1
221 cardiomyopathy, dilated, with woolly hair and keratoderma 10.1
222 beta-thalassemia 10.1
223 myopathy due to myoadenylate deaminase deficiency 10.1
224 angina pectoris 10.1
225 sleep apnea 10.1
226 basal ganglia calcification 10.1
227 hydrocephalus 10.1
228 congenital dyserythropoietic anemia 10.1
229 macrocytic anemia 10.1
230 glycogen storage disease 10.1
231 hemoglobinopathy 10.1
232 astrocytoma 10.1
233 coronary stenosis 10.1
234 postpoliomyelitis syndrome 10.1
235 poliomyelitis 10.1
236 pulmonary valve stenosis 10.1
237 hyperthyroidism 10.1
238 pulmonary embolism 10.1
239 myocardial stunning 10.1
240 toxoplasmosis 10.1
241 charcot-marie-tooth hereditary neuropathy 10.1
242 sickle cell disease 10.1
243 broken heart syndrome 10.1
244 autonomic dysfunction 10.1
245 genetic neuromuscular disease 10.1
246 skeletal muscle disease 10.1
247 coronary artery dissection, spontaneous 10.0
248 lipomatosis, multiple 10.0
249 myopathy, centronuclear, x-linked 10.0
250 juvenile arthritis 10.0
251 pain agnosia 10.0
252 pleomorphic lipoma 10.0
253 generalized anxiety disorder 10.0
254 primary hyperoxaluria 10.0
255 antiphospholipid syndrome 10.0
256 juvenile rheumatoid arthritis 10.0
257 muscular atrophy 10.0
258 neuropathy 10.0
259 vascular dementia 10.0
260 diastolic heart failure 10.0
261 dextrocardia with situs inversus 10.0
262 atrial septal aneurysm 10.0
263 atrial tachyarrhythmia with short pr interval 10.0
264 cardiomyopathy, familial hypertrophic, 2 10.0
265 cardiomyopathy, familial hypertrophic, 3 10.0
266 pilomatrixoma 10.0
267 fibrosis of extraocular muscles, congenital, 1 10.0
268 hernia, hiatus 10.0
269 hypercholesterolemia, familial, 1 10.0
270 hypertension, essential 10.0
271 marfan syndrome 10.0
272 cyclic neutropenia 10.0
273 sick sinus syndrome 2 10.0
274 noonan syndrome 1 10.0
275 pheochromocytoma 10.0
276 sarcoidosis 1 10.0
277 strabismus 10.0
278 digeorge syndrome 10.0
279 down syndrome 10.0
280 celiac disease 1 10.0
281 craniosynostosis with fibular aplasia 10.0
282 pulmonary venoocclusive disease 2, autosomal recessive 10.0
283 multinucleated neurons, anhydramnios, renal dysplasia, cerebellar hypoplasia, and hydranencephaly 10.0
284 hydrops fetalis, nonimmune 10.0
285 hyper-beta-alaninemia 10.0
286 immune deficiency disease 10.0
287 miller-dieker lissencephaly syndrome 10.0
288 pierre robin syndrome 10.0
289 pulmonary atresia with intact ventricular septum 10.0
290 pulmonic stenosis 10.0
291 sudden infant death syndrome 10.0
292 danon disease 10.0
293 coffin-lowry syndrome 10.0
294 corpus callosum, partial agenesis of, x-linked 10.0
295 cardiomyopathy, infantile histiocytoid 10.0
296 cardiomyopathy, familial hypertrophic, 6 10.0
297 tricuspid atresia 10.0
298 cardiomyopathy, familial hypertrophic, 25 10.0
299 cardiomyopathy, familial hypertrophic, 8 10.0
300 myopathy, myofibrillar, 3 10.0
301 cardiomyopathy, familial hypertrophic, 11 10.0
302 cardiomyopathy, familial hypertrophic, 12 10.0
303 cardiomyopathy, familial hypertrophic, 13 10.0
304 cardiomyopathy, familial hypertrophic, 14 10.0
305 cardiomyopathy, familial hypertrophic, 15 10.0
306 cardiomyopathy, familial hypertrophic, 7 10.0
307 cardiomyopathy, familial hypertrophic, 9 10.0
308 cardiomyopathy, familial hypertrophic, 16 10.0
309 cardiomyopathy, familial hypertrophic, 17 10.0
310 cardiomyopathy, familial hypertrophic, 18 10.0
311 cardiomyopathy, familial hypertrophic, 20 10.0
312 cyanosis, transient neonatal 10.0
313 mannose-binding lectin deficiency 10.0
314 cardiomyopathy, familial hypertrophic, 21 10.0
315 cardiomyopathy, dilated, 1kk 10.0
316 carbonic anhydrase va deficiency, hyperammonemia due to 10.0
317 cardiomyopathy, familial hypertrophic, 26 10.0
318 cardiomyopathy, familial hypertrophic 27 10.0
319 polymicrogyria with or without vascular-type ehlers-danlos syndrome 10.0
320 periventricular nodular heterotopia 10.0
321 early infantile epileptic encephalopathy 10.0
322 autosomal recessive disease 10.0
323 rheumatic heart disease 10.0
324 fibroma 10.0
325 adrenal gland pheochromocytoma 10.0
326 organic acidemia 10.0
327 recessive dystrophic epidermolysis bullosa 10.0
328 dextro-looped transposition of the great arteries 10.0
329 polycystic kidney disease 10.0
330 rasopathy 10.0
331 thalassemia 10.0
332 endocarditis 10.0
333 siderosis 10.0
334 pre-eclampsia 10.0
335 microcephaly 10.0
336 placenta praevia 10.0
337 respiratory failure 10.0
338 hypertensive heart disease 10.0
339 gastroparesis 10.0
340 esophagitis 10.0
341 hemosiderosis 10.0
342 graves' disease 10.0
343 pancytopenia 10.0
344 cardiac sarcoidosis 10.0
345 pulmonary sarcoidosis 10.0
346 eclampsia 10.0
347 familial hypercholesterolemia 10.0
348 peptic esophagitis 10.0
349 pneumothorax 10.0
350 mitral valve stenosis 10.0
351 optic nerve disease 10.0
352 dental caries 10.0
353 transient cerebral ischemia 10.0
354 epidermolysis bullosa 10.0
355 substance abuse 10.0
356 lipomatosis 10.0
357 lysosomal storage disease 10.0
358 ischemia 10.0
359 tricuspid valve stenosis 10.0
360 epidermolysis bullosa dystrophica 10.0
361 kidney disease 10.0
362 double outlet right ventricle 10.0
363 connective tissue disease 10.0
364 mitochondrial metabolism disease 10.0
365 malignant hyperthermia 10.0
366 neurofibromatosis 10.0
367 amyloidosis 10.0
368 mechanical strabismus 10.0
369 congenital nystagmus 10.0
370 pathologic nystagmus 10.0
371 systolic heart failure 10.0
372 hypereosinophilic syndrome 10.0
373 emery-dreifuss syndrome 10.0
374 myotonic dystrophy 10.0
375 polymicrogyria 10.0
376 amyloidosis aa 10.0
377 cutaneous sclerosis 10.0
378 double discordia 10.0
379 infectious myocarditis 10.0
380 mosaic trisomy 22 10.0
381 partial atrioventricular canal 10.0
382 pseudo-turner syndrome 10.0
383 trisomy 22 10.0
384 isolated pierre robin sequence 10.0
385 multiminicore disease 10.0
386 dysphagia 10.0
387 myotonia 10.0
388 ohtahara syndrome 10.0
389 tremor 10.0
390 familial long qt syndrome 10.0
391 atrial standstill 10.0
392 cerebrofacial arteriovenous metameric syndrome 10.0
393 rare hereditary hemochromatosis 10.0
394 autosomal trisomy 10.0
395 rare genetic cardiac disease 10.0
396 overgrowth syndrome 10.0
397 hereditary optic neuropathy 10.0
398 multiple congenital anomalies/dysmorphic syndrome-intellectual disability 10.0
399 atherosclerosis susceptibility 9.9
400 scleroderma, familial progressive 9.9
401 right atrial isomerism 9.9
402 walker-warburg syndrome 9.9
403 omphalocele 9.9
404 microcytic anemia 9.9
405 branch retinal artery occlusion 9.9
406 retinal artery occlusion 9.9
407 diffuse cutaneous systemic sclerosis 9.9
408 quadricuspid aortic valve 9.9
409 body mass index quantitative trait locus 11 9.8
410 body mass index quantitative trait locus 9 9.8
411 body mass index quantitative trait locus 8 9.8
412 body mass index quantitative trait locus 4 9.8
413 body mass index quantitative trait locus 10 9.8
414 body mass index quantitative trait locus 7 9.8
415 body mass index quantitative trait locus 12 9.8
416 body mass index quantitative trait locus 14 9.8
417 body mass index quantitative trait locus 18 9.8
418 body mass index quantitative trait locus 19 9.8
419 body mass index quantitative trait locus 20 9.8
420 tuberous sclerosis 9.8

Graphical network of the top 20 diseases related to Left Ventricular Noncompaction:



Diseases related to Left Ventricular Noncompaction

Symptoms & Phenotypes for Left Ventricular Noncompaction

MGI Mouse Phenotypes related to Left Ventricular Noncompaction:

45 (showing 6, show less)
# Description MGI Source Accession Score Top Affiliating Genes
1 cardiovascular system MP:0005385 10.21 ACTC1 DTNA LDB3 LMNA MIB1 MYBPC3
2 homeostasis/metabolism MP:0005376 10.13 ACTC1 LDB3 LMNA MIB1 MIB2 MIPEP
3 growth/size/body region MP:0005378 10.1 ACTC1 DTNA LDB3 LMNA MIB1 MIB2
4 mortality/aging MP:0010768 10.03 ACTC1 DTNA LDB3 LMNA MIB1 MIB2
5 muscle MP:0005369 9.7 ACTC1 DTNA LDB3 LMNA MYBPC3 MYH7
6 normal MP:0002873 9.32 ACTC1 LMNA MIB1 MIB2 MYH7 NKX2-5

Drugs & Therapeutics for Left Ventricular Noncompaction

Drugs for Left Ventricular Noncompaction (from DrugBank, HMDB, Dgidb, PharmGKB, IUPHAR, NovoSeek, BitterDB):

(showing 2, show less)
# Name Status Phase Clinical Trials Cas Number PubChem Id
1 Insulin, Globin Zinc
2 insulin

Interventional clinical trials:

(showing 10, show less)
# Name Status NCT ID Phase Drugs
1 Prognosis of Isolated Left Ventricular Non-compaction in Adults Unknown status NCT02885363
2 The Genetics of Cardiomyopathy and Heart Failure Unknown status NCT00703443
3 Cardiac Computed Tomography: Characteristics of Isolated Left Ventricular Non-compaction Completed NCT01470014
4 Value of Different Myocardial Parameters to Differentiate Left Ventricular Noncompaction Cardiomyopathy From Other Cardiomyopathies and Healthy Controls by Cardiac Magnetic Resonance Completed NCT01481298
5 Increased Left Ventricular Trabeculation in Athletes - a Marker of Left Ventricular Non-compaction or a Physiological Epiphenomenon of Increased Cardiac Preload? Completed NCT02568072
6 Maternal Lipid Metabolism and Neonatal Heart Function in Diabetes Completed NCT01346527
7 Arrhythmogenic Substrate Assessment in Patients With Primary Cardiomyopathies. A Prospective Follow-up Study Recruiting NCT03304847
8 International Consortium for Multimodality Phenotyping in Adults With Non-compaction Not yet recruiting NCT04424030
9 Analysis of Cardiac Biomarkers, Electrocardiograms and Cardio-pulmonary Exercise Test (CPET) Results in Children With Dilated (DCM), Hypertrophic (HCM) and Left-ventricle Non-compaction (LVNC) Cardiomyopathies Not yet recruiting NCT04316923
10 TranslatiOnal Registry for CardiomyopatHies (TORCH) - Plus as Part of the German Centre for Cardiovascular Research (DZHK) Not yet recruiting NCT04265040

Search NIH Clinical Center for Left Ventricular Noncompaction

Genetic Tests for Left Ventricular Noncompaction

Genetic tests related to Left Ventricular Noncompaction:

# Genetic test Affiliating Genes
1 Left Ventricular Noncompaction 29

Anatomical Context for Left Ventricular Noncompaction

MalaCards organs/tissues related to Left Ventricular Noncompaction:

40
Heart, Testes, Kidney, Skeletal Muscle

Publications for Left Ventricular Noncompaction

Articles related to Left Ventricular Noncompaction:

(showing 922, show less)
# Title Authors PMID Year
1
Phenotype and Functional Analyses in a Transgenic Mouse Model of Left Ventricular Noncompaction Caused by a DTNA Mutation. 61 6
29118297 2017
2
Fine mapping of the 1p36 deletion syndrome identifies mutation of PRDM16 as a cause of cardiomyopathy. 61 6
23768516 2013
3
Mutations in the NOTCH pathway regulator MIB1 cause left ventricular noncompaction cardiomyopathy. 61 6
23314057 2013
4
Sarcomere gene mutations in isolated left ventricular noncompaction cardiomyopathy do not predict clinical phenotype. 6 61
21551322 2011
5
Mutations in sarcomere protein genes in left ventricular noncompaction. 61 6
18506004 2008
6
Genetic analysis in patients with left ventricular noncompaction and evidence for genetic heterogeneity. 6 61
16427346 2006
7
Novel gene mutations in patients with left ventricular noncompaction or Barth syndrome. 61 6
11238270 2001
8
Recommendations for reporting of secondary findings in clinical exome and genome sequencing, 2016 update (ACMG SF v2.0): a policy statement of the American College of Medical Genetics and Genomics. 6
27854360 2017
9
D117N in Cypher/ZASP may not be a causative mutation for dilated cardiomyopathy and ventricular arrhythmias. 6
26419279 2016
10
ACMG policy statement: updated recommendations regarding analysis and reporting of secondary findings in clinical genome-scale sequencing. 6
25356965 2015
11
ACMG recommendations for reporting of incidental findings in clinical exome and genome sequencing. 6
23788249 2013
12
Severe familial left ventricular non-compaction cardiomyopathy due to a novel troponin T (TNNT2) mutation. 6
20083571 2010
13
Coding sequence rare variants identified in MYBPC3, MYH6, TPM1, TNNC1, and TNNI3 from 312 patients with familial or idiopathic dilated cardiomyopathy. 6
20215591 2010
14
Cardiac troponin T mutation in familial cardiomyopathy with variable remodeling and restrictive physiology. 6
18651846 2008
15
Shared genetic causes of cardiac hypertrophy in children and adults. 6
18403758 2008
16
Dilated Cardiomyopathy Overview 6
20301486 2007
17
Echocardiographic-determined septal morphology in Z-disc hypertrophic cardiomyopathy. 6
17097056 2006
18
Dilated cardiomyopathy mutations in three thin filament regulatory proteins result in a common functional phenotype. 6
15923195 2005
19
Myosin binding protein C mutations and compound heterozygosity in hypertrophic cardiomyopathy. 6
15519027 2004
20
Severe disease expression of cardiac troponin C and T mutations in patients with idiopathic dilated cardiomyopathy. 6
15542288 2004
21
A Cypher/ZASP mutation associated with dilated cardiomyopathy alters the binding affinity to protein kinase C. 6
14660611 2004
22
Mutations in Cypher/ZASP in patients with dilated cardiomyopathy and left ventricular non-compaction. 6
14662268 2003
23
Identification of the genotypes causing hypertrophic cardiomyopathy in northern Sweden. 6
12818575 2003
24
Novel mutations in sarcomeric protein genes in dilated cardiomyopathy. 6
12379228 2002
25
Novel cardiac troponin T mutation as a cause of familial dilated cardiomyopathy. 6
11684629 2001
26
Mutations that alter the surface charge of alpha-tropomyosin are associated with dilated cardiomyopathy. 6
11273725 2001
27
Mutations in sarcomere protein genes as a cause of dilated cardiomyopathy. 6
11106718 2000
28
Actin mutations in dilated cardiomyopathy, a heritable form of heart failure. 6
9563954 1998
29
Alpha-tropomyosin and cardiac troponin T mutations cause familial hypertrophic cardiomyopathy: a disease of the sarcomere. 6
8205619 1994
30
Human cardiac troponin T: identification of fetal isoforms and assignment of the TNNT2 locus to chromosome 1q. 6
8088824 1994
31
A significance of school screening electrocardiogram in the patients with ventricular noncompaction. 61
32161993 2020
32
Diagnosis of double-chambered left ventricle using echocardiography. 61
32511806 2020
33
Prevalence of left ventricular hypertrabeculation/noncompaction among patients with congenital dyserythropoietic anemia Type 1 (CDA1). 61
32512057 2020
34
Left Ventricular Noncompaction: Diagnostic Approach, Prognostic Evaluation, and Management Strategies. 61
31008770 2020
35
Anaesthetic management of a parturient with left ventricular noncompaction cardiomyopathy. 61
32169260 2020
36
A case of incessant bundle branch reentry tachycardia occurring after phase 3 right bundle branch block as a first manifestation of left ventricular noncompaction cardiomyopathy in a patient with bicuspid aortic valve. 61
32461894 2020
37
Late gadolinium enhancement on CMRI in patients with LV noncompaction: An overestimated phenomenon? 61
32480266 2020
38
Recreational marathon running does not cause exercise-induced left ventricular hypertrabeculation. 61
32360651 2020
39
The effect of noncompacted myocardial resection on isolated left ventricular noncompaction. 61
32360189 2020
40
Novel KLHL26 variant associated with a familial case of Ebstein's anomaly and left ventricular noncompaction. 61
31985165 2020
41
The role of multimodality imaging in the diagnosis of left ventricular noncompaction. 61
32329049 2020
42
Further delineation of the phenotypic spectrum associated with hemizygous loss-of-function variants in NONO. 61
31883306 2020
43
Left Ventricular Noncompaction and Congenital Heart Disease Increases the Risk of Congestive Heart Failure. 61
32183154 2020
44
Multiple genetic variants in adolescent patients with left ventricular noncompaction cardiomyopathy. 61
31918855 2020
45
Elevated myocardial SORBS2 and the underlying implications in left ventricular noncompaction cardiomyopathy. 61
32143182 2020
46
Bridging the gap between hypertrabeculation phenotype, noncompaction phenotype and left ventricular noncompaction cardiomyopathy. 61
31895132 2020
47
[Overlapping Phenotype: Left Ventricular non-Compaction and Hypertrophic Cardiomyopathy]. 61
32394868 2020
48
Epidemiology and clinical characteristics of atrial fibrillation in patients with inherited heart diseases. 61
31930598 2020
49
Left Ventricular Noncompaction and Cardiogenic Shock. 61
32091931 2020
50
Left Ventricular Noncompaction with Multiple Thrombi in Apical Aneurysm. 61
31645531 2020
51
Left Ventricular Noncompaction: A Rare Cause of Effort Angina Unveiled During Left Heart Catheterization. 61
32005789 2020
52
Familial Mitral Arcade, Tricuspid Dysplasia, Left Ventricular Noncompaction and Short-Chain Acyl-CoA Reductase Deficiency. 61
31870493 2020
53
Influence of observer-dependency on left ventricular hypertrabeculation mass measurement and its relationship with left ventricular volume and ejection fraction -  comparison between manual and semiautomatic CMR image analysis methods. 61
32160262 2020
54
[Genetic analysis of a family with congenital heart defects caused by chromosome 8p23.1 deletion]. 61
31922595 2020
55
Evaluation of myocardial deformation pattern of left ventricular noncompaction by cardiac magnetic resonance tissue tracking. 61
31922499 2020
56
Outcomes in Left Ventricular Noncompaction: Heterogeneity in Results or Heterogeneity in Diagnosing a Heterogeneous Disease? 61
31959005 2020
57
Prognostic Significance of Left Ventricular Noncompaction: Systematic Review and Meta-Analysis of Observational Studies. 61
31959004 2020
58
Left ventricular noncompaction - Risk stratification and genetic consideration. 61
31629663 2020
59
Multisystem Myotilinopathy, including Myopathy and Left Ventricular Noncompaction, due to the MYOT Variant c.179C>T. 61
32509353 2020
60
Irreversible Acquired Noncompaction Cardiomyopathy in a Parturient with Corrected Atrial Septal Defect: A Case Report and Clinical Implications. 61
32181020 2020
61
Association of Wolff-Parkinson-White With Left Ventricular Noncompaction Cardiomyopathy in Children. 61
31626950 2019
62
Left ventricular noncompaction associated with genetic disturbance of folic acid metabolism. 61
31617501 2019
63
Meta-Analysis of the Prognostic Role of Late Gadolinium Enhancement and Global Systolic Impairment in Left Ventricular Noncompaction. 61
30878415 2019
64
Clinical and genetic insights into non-compaction: a meta-analysis and systematic review on 7598 individuals. 61
30980206 2019
65
2019 HRS expert consensus statement on evaluation, risk stratification, and management of arrhythmogenic cardiomyopathy. 61
31078652 2019
66
2019 HRS expert consensus statement on evaluation, risk stratification, and management of arrhythmogenic cardiomyopathy: Executive summary. 61
31676023 2019
67
Left ventricular hypertrabeculation/noncompaction, cardiac phenotype, and neuromuscular disorders. 61
29626229 2019
68
Left Ventricular Noncompaction: Meglio solo che mal accompagnati: Italian proverb: "Better Alone Than in Bad Company". 61
31005523 2019
69
Sudden cardiac arrest as the initial presentation for left ventricular noncompaction cardiomyopathy. 61
31656421 2019
70
Non-compaction cardiomyopathy in pregnancy: a case report of spongy myocardium in both mother and foetus and systematic review of literature. 61
31570025 2019
71
Left ventricular noncompaction and Fabry disease: An unlikely association. 61
31892454 2019
72
Screening for Fabry disease in patients with left ventricular noncompaction. 61
31901299 2019
73
Defects in Trabecular Development Contribute to Left Ventricular Noncompaction. 61
31342111 2019
74
Surgical treatment of cardiac fibroma in a child with left ventricular noncompaction. 61
31376223 2019
75
Left ventricular noncompaction with pulmonary capillary hemangiomatosis-like lesions: case report. 61
31255974 2019
76
Clinical implications of sarcomere and nonsarcomere gene variants in patients with left ventricular noncompaction cardiomyopathy. 61
31397097 2019
77
Biallelic mutation in MYH7 and MYBPC3 leads to severe cardiomyopathy with left ventricular noncompaction phenotype. 61
30924982 2019
78
A novel de novo CASZ1 heterozygous frameshift variant causes dilated cardiomyopathy and left ventricular noncompaction cardiomyopathy. 61
31268246 2019
79
Left Ventricular Trabeculation and Noncompaction Cardiomyopathy: A Review. 61
31799511 2019
80
A large deletion in RYR2 exon 3 is associated with nadolol and flecainide refractory catecholaminergic polymorphic ventricular tachycardia. 61
30912151 2019
81
Semaphorin 3E/PlexinD1 signaling is required for cardiac ventricular compaction. 61
31434798 2019
82
Phenotypic spectrum of ALPK3-related cardiomyopathy. 61
31074094 2019
83
Value of Cardiac Magnetic Resonance Fractal Analysis Combined With Myocardial Strain in Discriminating Isolated Left Ventricular Noncompaction and Dilated Cardiomyopathy. 61
30565346 2019
84
Cardiac Segmental Strain Analysis in Pediatric Left Ventricular Noncompaction Cardiomyopathy. 61
30926406 2019
85
Prognostic role of Pro-BNP levels in left ventricular hypertrabeculation/non-compaction and neuromuscular disorders: results of a pilot study. 61
30919605 2019
86
Noncompaction cardiomyopathy is caused by a novel in-frame desmin (DES) deletion mutation within the 1A coiled-coil rod segment leading to a severe filament assembly defect. 61
30908796 2019
87
Left ventricular noncompaction, morphological, and clinical features for an integrated diagnosis. 61
30612215 2019
88
Expanding the genetic and clinical spectrum of the NONO-associated X-linked intellectual disability syndrome. 61
30773818 2019
89
Identification of a novel exon3 deletion of RYR2 in a family with catecholaminergic polymorphic ventricular tachycardia. 61
30615235 2019
90
Left ventricular noncompaction in a Para athlete. 61
31090793 2019
91
Left Ventricular Twist Mechanics to Identify Left Ventricular Noncompaction in Childhood. 61
31002265 2019
92
Cardiac sarcoidosis mimicking left ventricular noncompaction: An approach to acquired apical hypertrabeculation. 61
30834555 2019
93
Left Ventricular Noncompaction: Phenotype in an Integrated Model of Cardiomyopathy? 61
30947912 2019
94
Prevalence of pathogenic and likely pathogenic variants in the RASopathy genes in patients who have had panel testing for cardiomyopathy. 61
30762279 2019
95
Noncompaction-like membranous structure in left ventricle. 61
30803005 2019
96
Left ventricular noncompaction and orthodromic atrioventricular tachycardia observed in a patient with neurofibromatosis type 1. 61
30949358 2019
97
Left Ventricular noncompaction in a patient with systemic lupus erythematosus. 61
30379642 2019
98
Mitochondrial complex deficiency by novel compound heterozygous TMEM70 variants and correlation with developmental delay, undescended testicle, and left ventricular noncompaction in a Japanese patient: A case report. 61
30899493 2019
99
Abundant electrical myotonia and left ventricular noncompaction: Unusual features of Danon disease due to a novel mutation in LAMP2 gene. 61
30527948 2019
100
A rare case of Ebstein's anomaly with left ventricular noncompaction. 61
30080103 2019
101
A Case of Left Ventricular Noncompaction Presenting as Atrial Fibrillation. 61
31183289 2019
102
Understanding left ventricular hypertrabeculation/noncompaction: pathomorphologic findings and prognostic impact of neuromuscular comorbidities. 61
30570401 2019
103
Catheter ablation of a right posterior accessory pathway in a patient with left ventricular noncompaction: A case report. 61
30702587 2019
104
Left Ventricular Noncompaction in a Child with Turner Syndrome. 61
31827964 2019
105
Left ventricular noncompaction cardiomyopathy: Recent update on genetics, usefulness of biomarkers, and speckle imaging. 61
30487060 2019
106
Left ventricular noncompaction cardiomyopathy: Recent update on genetics, usefulness of biomarker, and speckle imaging. 61
29960849 2019
107
Anticoagulation Therapy in Specific Cardiomyopathies: Isolated Left Ventricular Noncompaction and Peripartum Cardiomyopathy. 61
29911432 2019
108
Left Ventricular Noncompaction: A Rare Case of Nonischemic Cardiomyopathy. 61
31485354 2019
109
Left Ventricular Noncompaction: Cause or Consequence of Myocardial Disease? A Case Report and Literature Review. 61
31509846 2019
110
Unsolved Issue in Left Ventricular Noncompaction: Is the Strange Form of Myocardium Congenital or Acquired? 61
31352452 2019
111
Concise Review: The Current State of Human In Vitro Cardiac Disease Modeling: A Focus on Gene Editing and Tissue Engineering. 61
30302938 2019
112
Prognostic Risk Stratification in Left Ventricular Noncompaction: Still a Long Way to Go. 61
31212280 2019
113
Noncompaction and Takotsubo Syndrome in a Neuromuscular Disorder. 61
31281680 2019
114
Left ventricular noncompaction with intractable heart failure responsive to empagliflozin. 61
30595770 2018
115
Rosai-Dorfman disease and left ventricular noncompaction cardiomyopathy: A heart failure conundrum. 61
30109595 2018
116
Case presentation commentary on "Rosai-Dorfman disease and left ventricular noncompaction cardiomyopathy: A heart failure conundrum." 61
30397865 2018
117
Fetal Noncompaction Cardiomyopathy and Histologic Diagnosis of Spongy Myocardium: Case Report and Review of the Literature. 61
30308683 2018
118
Improvement of the Diagnosis of Left Ventricular Noncompaction Cardiomyopathy After Analyzing Both Advantages and Disadvantages of Echocardiography and CMRI. 61
29859913 2018
119
Cardiac Phenotypes in Hereditary Muscle Disorders: JACC State-of-the-Art Review. 61
30442292 2018
120
An Adolescent with Left Ventricular Noncompaction and Ebstein Anomaly Presenting with Advanced Heart Failure: Discharge from Hospital with a Biventricular Assist Device. 61
30217690 2018
121
Sarcomere gene variants act as a genetic trigger underlying the development of left ventricular noncompaction. 61
30188508 2018
122
Clinical and Genetic Complexities of Left Ventricular Noncompaction: Preventing Overdiagnosis in a Disease We Do Not Understand. 61
30140926 2018
123
Left Ventricular Trabeculations in Athletes: Epiphenomenon or Phenotype of Disease? 61
30367273 2018
124
Genotype-Positive Status Is Associated With Poor Prognoses in Patients With Left Ventricular Noncompaction Cardiomyopathy. 61
30371277 2018
125
Are We Getting Closer to Risk Stratification in Left Ventricular Noncompaction Cardiomyopathy? 61
30371282 2018
126
Left ventricular noncompaction in patients with coronary artery disease: Preliminary analysis of echocardiographic findings. 61
30105764 2018
127
Diagnostic Yield of Genetic Testing in Young Athletes With T-Wave Inversion. 61
29764897 2018
128
High-Risk Cardiovascular Conditions in Sports-Related Sudden Death: Prevalence in 5,169 Schoolchildren Screened via Cardiac Magnetic Resonance. 61
30374227 2018
129
Potential Common Pathogenic Pathways for the Left Ventricular Noncompaction Cardiomyopathy (LVNC). 61
29766225 2018
130
Long-Term Outcomes of Childhood Left Ventricular Noncompaction Cardiomyopathy: Results From a National Population-Based Study. 61
29514799 2018
131
Efficacy of cardiac resynchronization therapy in patients with isolated ventricular noncompaction with dilated cardiomyopathy: a systematic review of the literature. 61
29877973 2018
132
Echocardiographic and clinical markers of left ventricular ejection fraction and moderate or greater systolic dysfunction in left ventricular noncompaction cardiomyopathy. 61
29577407 2018
133
A mutant HCN4 channel in a family with bradycardia, left bundle branch block, and left ventricular noncompaction. 61
29349559 2018
134
Cardiomyopathy Phenotypes and Pregnancy Outcomes with Left Ventricular Noncompaction Cardiomyopathy. 61
29794382 2018
135
Sudden cardiac death in isolated right ventricular hypertrabeculation/noncompaction cardiomyopathy. 61
28901675 2018
136
The TNNI3 Arg192His mutation in a 13-year-old girl with left ventricular noncompaction. 61
30279906 2018
137
Prognosis in Sporadic Left Ventricular Hypertrabeculation With Normal Function. 61
29903361 2018
138
[Make a point on left ventricular noncompaction]. 61
29912226 2018
139
Prevalence of left ventricular hypertrabeculation/noncompaction among children with sickle cell disease. 61
29468808 2018
140
Whole exome sequencing identifies novel candidate mutations in a Chinese family with left ventricular noncompaction. 61
29568952 2018
141
Neddylation mediates ventricular chamber maturation through repression of Hippo signaling. 61
29632206 2018
142
Holt-Oram syndrome in two families diagnosed with left ventricular noncompaction and conduction disease. 61
29755943 2018
143
Left ventricular noncompaction or hypertrophic cardiomyopathy? Both! 61
28803523 2018
144
The highest mortality rates in childhood dilated cardiomyopathy occur during the first year after diagnosis. 61
29224255 2018
145
Predictors of poor outcome in patients with left ventricular noncompaction: Review of the literature. 61
29558024 2018
146
Two Patients with Coincident Noncompacted Myocardium and Hypertrophic Cardiomyopathy. 61
29563375 2018
147
A Rare Case of Left Ventricular Noncompaction in LEOPARD Syndrome. 61
29629024 2018
148
Relationship between the left ventricular size and the amount of trabeculations. 61
29124903 2018
149
The presence of multiple variants affects the clinical phenotype and prognosis in left ventricular noncompaction after surgery. 61
29203216 2018
150
Zinc transporter Slc39a8 is essential for cardiac ventricular compaction. 61
29337306 2018
151
Left Ventricular Noncompaction: From Physiologic Remodeling to Noncompaction Cardiomyopathy. 61
29447732 2018
152
[Left ventricular noncompaction]. 61
30059071 2018
153
Clinical and Echocardiography Features of Diagnosed in Adulthood Isolated Left Ventricular Noncompaction: A Case Series Study. 61
30065511 2018
154
Successful Treatment of an Infant with Left Ventricular Noncompaction Presenting with Fatal Ventricular Arrhythmia Treated with Cardiac Resynchronization Therapy and an Implantable Cardioverter Defibrillator. 61
29808126 2018
155
Whole-Exome Sequencing Reveals GATA4 and PTEN Mutations as a Potential Digenic Cause of Left Ventricular Noncompaction. 61
29874181 2018
156
Advanced Biventricular Heart Failure due to Left Ventricular Noncompaction Cardiomyopathy Leading to the Formation of a Gastric Bezoar: The Implications of Heart Failure on the Gastrointestinal Tract. 61
30364138 2018
157
Usefulness of a left ventricular assist device in patients with left ventricular noncompaction. 61
29686556 2018
158
Is Left Ventricular Noncompaction a Trait, Phenotype, or Disease? The Evidence Points to Phenotype. 61
29212902 2017
159
Acute Kidney Infarction Due to Left Ventricular Thrombus Embolization In Patient with Isolated Left Ventricular Noncompaction: A Case Report. 61
29272223 2017
160
Response by Towbin and Jefferies to Letter Regarding Article, "Cardiomyopathies Due to Left Ventricular Noncompaction, Mitochondrial and Storage Diseases, and Inborn Errors of Metabolism". 61
29217716 2017
161
Genetic Testing in Pediatric Left Ventricular Noncompaction. 61
29212898 2017
162
Case report: Left ventricular noncompaction cardiomyopathy and RASopathies. 61
28911804 2017
163
Cardiomyopathy: An Overview. 61
29431384 2017
164
Complications Associated With Implantable Cardioverter Defibrillators in Adults With Congenital Heart Disease or Left Ventricular Noncompaction Cardiomyopathy (From the NCDR® Implantable Cardioverter-Defibrillator Registry). 61
28917495 2017
165
[Heart transplantation for the treatment of isolated left ventricular myocardial noncompaction. First case in Mexico]. 61
27773363 2017
166
Comparison of Echocardiographic Diagnostic Criteria of Left Ventricular Noncompaction in a Pediatric Population. 61
28776136 2017
167
Cardiomyopathies Due to Left Ventricular Noncompaction, Mitochondrial and Storage Diseases, and Inborn Errors of Metabolism. 61
28912186 2017
168
Prevalence and Prognostic Significance of Left Ventricular Noncompaction in Patients Referred for Cardiac Magnetic Resonance Imaging. 61
28899950 2017
169
Noncompaction cardiomyopathy and heterotaxy syndrome. 61
29445263 2017
170
Autosomal Dominant Polycystic Kidney Patients May Be Predisposed to Various Cardiomyopathies. 61
29270497 2017
171
Left ventricular noncompaction cardiomyopathy with severe coronary artery disease in a young patient with familial hypercholesterolemia. 61
28817544 2017
172
Bradycardia, Syncope, and Left Ventricular Noncompaction Cardiomyopathy. 61
28645472 2017
173
TranslatiOnal Registry for CardiomyopatHies (TORCH) - rationale and first results. 61
28772045 2017
174
Left Ventricular Noncompaction Cardiomyopathy Presenting with Heart Failure in a 35-Year-Old Man. 61
28878579 2017
175
Discordant phenotypes in monozygotic twins with 16p11.2 microdeletions including the SH2B1 gene. 61
28544142 2017
176
Left Ventricular Noncompaction in Older Patients. 61
28864371 2017
177
Can Left Ventricular Noncompaction Be Acquired, and Can It Disappear? 61
28878580 2017
178
Navigating Genetic and Phenotypic Uncertainty in Left Ventricular Noncompaction. 61
28798026 2017
179
Novel Genetic Triggers and Genotype-Phenotype Correlations in Patients With Left Ventricular Noncompaction. 61
28798025 2017
180
A Wide and Specific Spectrum of Genetic Variants and Genotype-Phenotype Correlations Revealed by Next-Generation Sequencing in Patients with Left Ventricular Noncompaction. 61
28855170 2017
181
Consider Cardiac, Neuromuscular, and Hereditary Aspects of Left Ventricular Hypertrabeculation or Noncompaction. 61
28029365 2017
182
Left ventricular noncompaction cardiomyopathy in a patient with trisomy 13: A report and review of the literature. 61
28488311 2017
183
Sudden cardiac death with triple pathologies: A case report. 61
29622970 2017
184
Isolated Ventricular Noncompaction Cardiomyopathy Presenting as Fetal Hydrops at 24 Weeks Gestation. 61
28521630 2017
185
Suspected Malignant Hyperthermia During Biventricular Assist Device Implantation in a Patient With Left Ventricular Noncompaction Cardiomyopathy. 61
27842951 2017
186
Key Questions Relating to Left Ventricular Noncompaction Cardiomyopathy: Is the Emperor Still Wearing Any Clothes? 61
28395867 2017
187
[Aortic Valve Replacement and Mitral Valve Plasty in a Patient with Left Ventricular Noncompaction Associated with Aortic Regurgitation and Mitral Regurgitation;Report of a Case]. 61
28595227 2017
188
Echocardiography fails to detect left ventricular noncompaction in a cohort of patients with noncompaction on cardiac magnetic resonance imaging. 61
28267213 2017
189
Long QT syndrome and left ventricular noncompaction in 4 family members across 2 generations with KCNQ1 mutation. 61
28249770 2017
190
Sick sinus syndrome with HCN4 mutations shows early onset and frequent association with atrial fibrillation and left ventricular noncompaction. 61
28104484 2017
191
Left Ventricular Noncompaction With Muscular Ventricular Septal Defect in Mother and Son. 61
28520539 2017
192
The Enigma of Left Ventricular Hypertrabeculation: Knowledge About Pregnancies, Sports, and Neuromuscular Disorders Is Needed. 61
28494988 2017
193
Ischemic Stroke in a Young Patient Heralding a Left Ventricular Noncompaction Cardiomyopathy. 61
28966588 2017
194
Left Ventricular Noncompaction Cardiomyopathy in Pediatric Patients: A Case Series of a Clinically Heterogeneous Disease. 61
28108756 2017
195
Left ventricular noncompaction-A rare form of cardiomyopathy: Revelation modes and predictors of mortality in adults through 23 cases. 61
28373784 2017
196
Left ventricular noncompaction cardiomyopathy: cardiac, neuromuscular, and genetic factors. 61
28079110 2017
197
Left ventricular noncompaction cardiomyopathy. 61
28469993 2017
198
Long-Term Prognosis of Patients With Left Ventricular Noncompaction - Comparison Between Infantile and Juvenile Types. 61
28154298 2017
199
Naturally Occurring Biventricular Noncompaction in an Adult Domestic Cat. 61
28158907 2017
200
Implantation of left ventricular assist device in a patient with left ventricular non-compaction. 61
28076895 2017
201
Ventricular arrhythmias associated with left ventricular noncompaction: Electrophysiologic characteristics, mapping, and ablation. 61
27890738 2017
202
Identification of TAZ mutations in pediatric patients with cardiomyopathy by targeted next-generation sequencing in a Chinese cohort. 61
28183324 2017
203
Recent advancements in the molecular genetics of left ventricular noncompaction cardiomyopathy. 61
27989498 2017
204
Left Ventricular Noncompaction Cardiomyopathy and Recurrent Polymorphic Ventricular Tachycardia: A Case Report and Literature Review. 61
29035186 2017
205
Homozygous PKP2 deletion associated with neonatal left ventricle noncompaction. 61
27030002 2017
206
Misclassification of hypertrophic cardiomyopathy: validation of diagnostic codes. 61
28848363 2017
207
Primary cardiac hydatid cyst presenting as noncompaction cardiomyopathy. 61
27688059 2017
208
Cardiomyopathy-Associated Gene 1-Sensitive PKC-Dependent Connexin 43 Expression and Phosphorylation in Left Ventricular Noncompaction Cardiomyopathy. 61
29176328 2017
209
Animal Models of Congenital Cardiomyopathies Associated With Mutations in Z-Line Proteins. 61
27171814 2017
210
MIB2 variants altering NOTCH signalling result in left ventricle hypertrabeculation/non-compaction and are associated with Ménétrier-like gastropathy. 61
28013292 2017
211
Revision of Echocardiographic Indications and Findings in Neurologically Ill Patients. 61
28400861 2017
212
Incremental value of contrast echocardiography in the diagnosis of left ventricular noncompaction. 61
27798758 2016
213
Letter by Finsterer and Zarrouk-Mahjoub Regarding Article, "Combination of Whole Genome Sequencing, Linkage, and Functional Studies Implicates a Missense Mutation in Titin as a Cause of Autosomal Dominant Cardiomyopathy With Features of Left Ventricular Noncompaction". 61
27998947 2016
214
Notch signalling in ventricular chamber development and cardiomyopathy. 61
27260948 2016
215
Left Ventricular Noncompaction: Anatomical Phenotype or Distinct Cardiomyopathy? 61
27855805 2016
216
Left Ventricular Noncompaction, or Is It? 61
27855807 2016
217
Obscurin Variants in Patients With Left Ventricular Noncompaction. 61
27855815 2016
218
Fukutin gene mutations that cause left ventricular noncompaction. 61
27521547 2016
219
Long-Term Prognostic Value of Cardiac Magnetic Resonance in Left Ventricle Noncompaction: A Prospective Multicenter Study. 61
27855806 2016
220
Left ventricular hypertrabeculation: a clinical enigma. 61
27852661 2016
221
Interdisciplinary management of left ventricular hypertrabeculation/noncompaction during pregnancy with a wearable defibrillator. 61
27537747 2016
222
Regression of left ventricular hypertrabeculation is associated with improvement in systolic function and favorable prognosis in adult patients with non-ischemic cardiomyopathy. 61
26740463 2016
223
Author's reply. 61
27004963 2016
224
Unmet needs in the cardiologic and neurologic work-up of left ventricular hypertrabeculation/noncompaction. 61
27442845 2016
225
Regression of left ventricular hypertrabeculation/noncompaction. 61
27004964 2016
226
Combination of Whole Genome Sequencing, Linkage, and Functional Studies Implicates a Missense Mutation in Titin as a Cause of Autosomal Dominant Cardiomyopathy With Features of Left Ventricular Noncompaction. 61
27625337 2016
227
Right atrial deformation analysis in isolated left ventricular noncompaction - insights from the three-dimensional speckle tracking echocardiographic MAGYAR-Path Study. 61
27609553 2016
228
Left ventricular noncompaction diagnosed following Graves' disease. 61
27843800 2016
229
Left ventricular noncompaction mimicking hypertrophic obstructive cardiomyopathy. 61
27394980 2016
230
When it rains, it pours: Peripartum cardiomyopathy with features of left-ventricular noncompaction in a hemodialysis patient. 61
27147549 2016
231
Echocardiographic characteristics of isolated left ventricular noncompaction. 61
28458700 2016
232
Calcified left ventricular noncompaction with complete atrioventricular block. 61
27372727 2016
233
Estimation of Prevalence of the Left Ventricular Noncompaction Among Adults. 61
27448685 2016
234
A cortical stroke secondary to an isolated left ventricular noncompaction in a 29-year-old female. 61
27751274 2016
235
[Left ventricular hypertrabeculation and more]. 61
26659847 2016
236
Left Ventricular Noncompaction: A Distinct Genetic Cardiomyopathy? 61
27561770 2016
237
Case images: Diagnosis of a rare combination of hypertrophic and left ventricular noncompaction cardiomyopathy using cardiac magnetic resonance imaging. 61
27439938 2016
238
Left ventricular noncompaction cardiomyopathy in end-stage heart failure patients undergoing orthotopic heart transplantation. 61
27135206 2016
239
The role of cardiac computed tomography in diagnosing left ventricular noncompaction in patients with sinus node dysfunction. 61
27057981 2016
240
Implantable cardioverter defibrillator therapy in young patients with cardiomyopathies and channelopathies: a single Italian centre experience. 61
27136702 2016
241
The hypertrabeculated (noncompacted) left ventricle is different from the ventricle of embryos and ectothermic vertebrates. 61
26516055 2016
242
Anesthetic experience of patient with isolated left ventricular noncompaction: a case report. 61
27274374 2016
243
Prevent Sudden Death in Carvajal Syndrome With Left Ventricular Hypertrabeculation/Noncompaction. 61
27617069 2016
244
Postnatal Outcome of Fetal Left Ventricular Hypertrabeculation/Noncompaction. 61
27033242 2016
245
LVAD as a Bridge to Heart Transplantation in a Patient with Left Ventricular Noncompaction Cardiomyopathy and Advanced Heart Failure. 61
27355148 2016
246
Genetics of Cardiac Developmental Disorders: Cardiomyocyte Proliferation and Growth and Relevance to Heart Failure. 61
26925501 2016
247
Wolff-Parkinson-White and left ventricular noncompaction in a Fabry patient: A case report. 61
27138316 2016
248
Prospective and Retrospective Diagnosis of Barth Syndrome Aided by Next-Generation Sequencing. 61
27124939 2016
249
Cardiac Imaging In Athletes. 61
27486490 2016
250
[Isolated left ventricular noncompaction causing refractory heart failure]. 61
26928017 2016
251
[Left ventricular noncompaction: A clinical and morphological study]. 61
27070772 2016
252
Genetic, Myopathic, and Diagnostic Implications of Left Ventricular Noncompaction. 61
26797382 2016
253
Reply to "Genetic, Myopathic, and Diagnostic Implications of Left Ventricular Noncompaction". 61
26797383 2016
254
Combination of mitochondrial myopathy and biventricular hypertrabeculation/noncompaction. 61
26707596 2016
255
A novel ACTC1 mutation in a young boy with left ventricular noncompaction and arrhythmias. 61
28491642 2016
256
A Striking Coronary Artery Pattern in a Grown-Up Congenital Heart Disease Patient. 61
26881144 2016
257
Left ventricular noncompaction: A rare indication for pediatric heart transplantation. 61
26777414 2016
258
Left Ventricular Noncompaction Combined With Epinephrine-Secreted Pheochromocytoma Inducing Heart Failure. 61
26973259 2016
259
BARTH SYNDROME IN MALE AND FEMALE SIBLINGS CAUSED BY A NOVEL MUTATION IN THE TAZ GENE. 61
30226969 2016
260
A Rare Case of Renal Infarct due to Noncompaction Cardiomyopathy: A Case Report and Literature Review. 61
27022488 2016
261
The Current Approach to Diagnosis and Management of Left Ventricular Noncompaction Cardiomyopathy: Review of the Literature. 61
26881173 2016
262
Isolated Left Ventricular Noncompaction Cardiomyopathy: A Transient Disease? 61
27667386 2016
263
Noncompaction and Dilated Cardiomyopathy in a Patient with Schizophrenia. 61
27547471 2016
264
Fetal left ventricular noncompaction cardiomyopathy and fatal outcome due to complete deficiency of mitochondrial trifunctional protein. 61
26070998 2015
265
Evolving Approaches to Genetic Evaluation of Specific Cardiomyopathies. 61
26472190 2015
266
Sudden Death in a Case of Isolated Left Ventricular Noncompaction: An Autopsy Case Report. 61
26332644 2015
267
PLEKHM2 mutation leads to abnormal localization of lysosomes, impaired autophagy flux and associates with recessive dilated cardiomyopathy and left ventricular noncompaction. 61
26464484 2015
268
Formation and Malformation of Cardiac Trabeculae: Biological Basis, Clinical Significance, and Special Yield of Magnetic Resonance Imaging in Assessment. 61
26440509 2015
269
Interobserver Agreement of the Echocardiographic Diagnosis of LV Hypertrabeculation/Noncompaction. 61
26563854 2015
270
Aortic valve replacement in a patient with left ventricular noncompaction. 61
24732086 2015
271
Cardiomyopathy Phenotypes and Outcomes for Children With Left Ventricular Myocardial Noncompaction: Results From the Pediatric Cardiomyopathy Registry. 61
26164213 2015
272
Noncompaction Cardiomyopathy: Case Presentation with Cardiac Magnetic Resonance Imaging Findings and Literature Review. 61
26900424 2015
273
Tetralogy of Fallot, Down's Syndrome, Left Ventricular Noncompaction, and Multiples Thrombi. 61
28465947 2015
274
Fetal Ventricular Hypertrabeculation/Noncompaction: Clinical Presentation, Genetics, Associated Cardiac and Extracardiac Abnormalities and Outcome. 61
26008764 2015
275
Reply to: Consider the genetic and myopathic background, familial occurrence, and alternative definitions of left ventricular hypertrabeculation/noncompaction. 61
26557751 2015
276
Clinical significance of intermediate left ventricular trabeculations in cardiac magnetic resonance. 61
26567819 2015
277
Consider the genetic and myopathic background, familial occurrence, and alternative definitions of left ventricular hypertrabeculation/noncompaction. 61
26557750 2015
278
Considerations about the genetics of left ventricular hypertrabeculation/non-compaction. 61
26095215 2015
279
Left ventricular hypertrabeculation/noncompaction in hyperoxaluria. 61
26363765 2015
280
Neuromuscular comorbidity, heart failure, and atrial fibrillation as prognostic factors in left ventricular hypertrabeculation/noncompaction. 61
25939437 2015
281
Stroke in a Young Individual with Left Ventricular Noncompaction and Left Atrium Standstill. 61
26413113 2015
282
Left Ventricular Noncompaction Diagnosis and Management Relevant to Pre-participation Screening of Athletes. 61
26141199 2015
283
Tissue Doppler Imaging Measures Correlate Poorly with Left Ventricular Filling Pressures in Pediatric Cardiomyopathy. 61
25943245 2015
284
Exon 3 deletion of ryanodine receptor causes left ventricular noncompaction, worsening catecholaminergic polymorphic ventricular tachycardia, and sudden cardiac arrest. 61
26018045 2015
285
Noncompaction Cardiomyopathy and Stroke: Case Report and Literature Review. 61
26050193 2015
286
Adherence to thresholds: overdiagnosis of left ventricular noncompaction cardiomyopathy. 61
25797302 2015
287
Isolated Noncompaction of the Left Ventricle in Adults. 61
26227197 2015
288
Loss of Function Mutations in NNT Are Associated With Left Ventricular Noncompaction. 61
26025024 2015
289
Left Ventricular Noncompaction: A Clinically Useful Diagnostic Label? 61
26271090 2015
290
Increased Left Ventricular Trabeculation Does Not Necessarily Equate to Left Ventricular Noncompaction in Athletes. 61
26146927 2015
291
Left ventricular noncompaction presenting like a double-chambered left ventricle. 61
25798904 2015
292
3-HMG Coenzyme A Lyase Deficiency: Macrocephaly and Left Ventricular Noncompaction with a Novel Mutation. 61
25708061 2015
293
Noncompaction and embolic myocardial infarction: the importance of oral anticoagulation. 61
26162290 2015
294
Novel Phenotype-Genotype Correlations of Restrictive Cardiomyopathy With Myosin-Binding Protein C (MYBPC3) Gene Mutations Tested by Next-Generation Sequencing. 61
26163040 2015
295
Cardiac deficiency of single cytochrome oxidase assembly factor scox induces p53-dependent apoptosis in a Drosophila cardiomyopathy model. 61
25792727 2015
296
Compound heterozygous or homozygous truncating MYBPC3 mutations cause lethal cardiomyopathy with features of noncompaction and septal defects. 61
25335496 2015
297
Cesarean Delivery in a Parturient with Left Ventricular Noncompaction Complicated by Acute Pulmonary Hypertension After Methylergonovine Administration for Postpartum Hemorrhage. 61
26050249 2015
298
Cardiac CT Angiography in Congestive Heart Failure. 61
26033904 2015
299
Arrhythmias in left ventricular noncompaction. 61
26002396 2015
300
Lamin A/C mutations do not cause left ventricular hypertrabeculation/noncompaction. 61
26175656 2015
301
Big data for a rare disease: Examining heart transplantation for left ventricular noncompaction in the United Network of Organ Sharing registry. 61
25940078 2015
302
A Case With Apical Hypertrophic Cardiomyopathy, Multiple Coronary Artery-Left Ventricular Fistulae, and a Morphological Structure Mimicking Left Ventricular Noncompaction: Statue of Cerberus or Double-Headed Eagle? 61
26078372 2015
303
Letter by Stöllberger and Finsterer regarding article, "Reversible de novo left ventricular trabeculations in pregnant women: implications for the diagnosis of left ventricular noncompaction in low-risk populations". 61
25940970 2015
304
Response to letter regarding article, "Reversible de novo left ventricular trabeculations in pregnant women: implications for the diagnosis of left ventricular noncompaction in low-risk populations". 61
25940971 2015
305
Age-dependency of cardiac and neuromuscular findings in adults with left ventricular hypertrabeculation/noncompaction. 61
25791238 2015
306
Response to: PLEC1 mutation associated with left ventricular hypertrabeculation/noncompaction. 61
25800222 2015
307
PLEC1 mutation associated with left ventricular hypertrabeculation/noncompaction. 61
25791580 2015
308
Left ventricular noncompaction: imaging findings and diagnostic criteria. 61
25905958 2015
309
The importance of the cardiac cycle in the imaging criteria for left ventricular noncompaction. 61
25835456 2015
310
Reply: The importance of cardiac cycle in the imaging criteria for left ventricular noncompaction. 61
25835457 2015
311
Does professional athlete training cause acquired left ventricular hypertrabeculation/noncompaction? 61
25756571 2015
312
Left ventricular hypertrabeculation/noncompaction as a cause of juvenile embolic stroke. 61
24357093 2015
313
Outcomes, arrhythmic burden and ambulatory monitoring of pediatric patients with left ventricular non-compaction and preserved left ventricular function. 61
25665759 2015
314
Clinical usefulness of gated technetium-99m sestamibi myocardial perfusion single-photon emission computed tomography with phase analysis for the management of patients with isolated ventricular noncompaction. 61
30546541 2015
315
Genetic Testing Is Not Required for Diagnosing Left Ventricular Hypertrabeculation / Non-Compaction. 61
26225156 2015
316
Familial Himalayan p wave and left ventricular hypertrabeculation/noncompaction. 61
24724986 2015
317
Whole-exome sequencing identify a new mutation of MYH7 in a Chinese family with left ventricular noncompaction. 61
25550050 2015
318
Increased left ventricular trabeculation does not necessarily equate to left ventricular noncompaction in athletes. 61
25730564 2015
319
Asymptomatic left ventricular noncompaction--implications for athletic participation. 61
25757002 2015
320
Double orifice mitral valve combined with left ventricular noncompaction in a child with Sotos syndrome. 61
30546538 2015
321
Effects of β-blocker therapy on electrocardiographic and echocardiographic characteristics of left ventricular noncompaction. 61
25331160 2015
322
Evaluation and management of left ventricular noncompaction cardiomyopathy. 61
25399629 2015
323
Left ventricular noncompaction in a family with lamin A/C gene mutation. 61
25873806 2015
324
Effects of cardiac resynchronization therapy on left ventricular remodeling and dyssynchrony in patients with left ventricular noncompaction and heart failure. 61
25392055 2015
325
Atypical form of left ventricular noncompaction resembling mass appearance in papillary muscles. 61
23912970 2015
326
Exercise-induced left-ventricular hypertrabeculation in athlete's heart. 61
25544199 2015
327
The genetic background of left ventricular hypertrabeculation / noncompaction remains vague. 61
25499953 2015
328
The genetic background of left ventricular hypertrabeculation/noncompaction remains vague. Response. 61
25522834 2015
329
Pay attention to the skeletal muscles in left ventricular hypertrabeculation / noncompaction. 61
25827786 2015
330
Pay attention to the skeletal muscles in left ventricular hypertrabeculation / noncompaction. Authors' reply. 61
25827787 2015
331
Unusual distribution of noncompaction of left ventricular myocardium. 61
25665274 2015
332
A novel MYH7 gene mutation in a fetus with left ventricular noncompaction. 61
25547560 2015
333
[Diagnostics enigma: left ventricular noncompaction or systemic right ventricle?] 61
28501844 2015
334
Left ventricular noncompaction and athletes: looking for stratification criteria. 61
25560945 2015
335
Left ventricular noncompaction and athletes-reply. 61
25560947 2015
336
Left ventricular hypertrabeculation/noncompaction in juvenile neuronal ceroid lipofuscinosis. 61
25786758 2015
337
Is Left Ventricular Noncompaction Only a Morphological Feature? A Case of Disappearance of Noncompaction after Surgical Correction of Aorto-Right Ventricular Fistula, Interventricular Septal Defect and Aortic Stenosis. 61
28465924 2015
338
Left ventricular noncompaction cardiomyopathy in Duchenne muscular dystrophy carriers. 61
30546524 2015
339
Biventricular Noncompaction Cardiomyopathy in an Adult with Unique Facial Dysmorphisms: Case Report and Brief Review. 61
26266056 2015
340
Juvenile neuronal ceroid-lipofuscinosis with hypertrophic cardiomyopathy and left ventricular noncompaction: a case report. 61
25786759 2015
341
Wearable cardioverter-defibrillator in a patient with left ventricular noncompaction/hypertrabeculation, coronary artery disease, and polyneuropathy. 61
24602189 2015
342
Ebstein's Anomaly, Left Ventricular Noncompaction, and Sudden Cardiac Death. 61
26240764 2015
343
Disappearance of left ventricular hypertrabeculation/noncompaction in vacuolar non-neuromuscular cardiomyopathy. 61
25464391 2015
344
Novel α-actinin 2 variant associated with familial hypertrophic cardiomyopathy and juvenile atrial arrhythmias: a massively parallel sequencing study. 61
25173926 2014
345
Adult left ventricular noncompaction: reappraisal of current diagnostic imaging modalities. 61
25496545 2014
346
Consider a mitochondrial disorder when left ventricular hypertrabeculation/noncompaction is associated with renal cysts. 61
25593544 2014
347
Correction in article "Familial Left Ventricular Noncompaction Associated With a Novel Mutation in the Alphacardiac Actin Gene", Rev Esp Cardiol. 2014;67:857-9. 61
25554359 2014
348
Is surgical removal of the noncompacted layer the clue to treat left ventricular hypertrabeculation/noncompaction? 61
25132187 2014
349
Evolution of electrocardiographic abnormalities in association with neuromuscular disorders and survival in left ventricular hypertrabeculation/noncompaction. 61
24934299 2014
350
Is left ventricular hypertrabeculation/noncompaction in athletes benign? 61
25499320 2014
351
Consider the genetic, myopathic, noncongenital, and familial background of left ventricular hypertrabeculation/noncompaction even in healthy subjects. 61
25264357 2014
352
Familial Ebstein's anomaly, left ventricular noncompaction, and ventricular septal defect associated with an MYH7 mutation. 61
25444217 2014
353
Left ventricular noncompaction: a cardiomyopathy with distinct characteristics and risks. 61
24231893 2014
354
Left ventricular noncompaction: a genetic cardiomyopathy looking for diagnostic criteria. 61
25440092 2014
355
Importance of genetic evaluation and testing in pediatric cardiomyopathy. 61
25429328 2014
356
Novel mutation in exon 14 of the sarcomere gene MYH7 in familial left ventricular noncompaction with bicuspid aortic valve. 61
25415959 2014
357
Clinical outcomes in patients with isolated left ventricular noncompaction and heart failure. 61
25079299 2014
358
A case of an infant with compound heterozygous mutations for hypertrophic cardiomyopathy producing a phenotype of left ventricular noncompaction. 61
25262865 2014
359
Left ventricular noncompaction cardiomyopathy: adult association with 1p36 deletion syndrome. 61
25624984 2014
360
Left ventricular noncompaction: a distinct cardiomyopathy or a trait shared by different cardiac diseases? 61
25443708 2014
361
Left ventricular noncompaction cardiomyopathy: lessons from the past to explain a diagnostic conundrum. 61
25107378 2014
362
Barth Syndrome 61
25299040 2014
363
Familial left ventricular noncompaction associated with a novel mutation in the alpha-cardiac actin gene. 61
25201647 2014
364
Double jeopardy in the echocardiography laboratory: coexistence of two distinct cardiomyopathies? 61
24447051 2014
365
Exome sequencing identifies a mutation in the ACTN2 gene in a family with idiopathic ventricular fibrillation, left ventricular noncompaction, and sudden death. 61
25224718 2014
366
Mitral regurgitation in left ventricular noncompaction cardiomyopathy assessed by cardiac MRI. 61
25799708 2014
367
Isolated left ventricular noncompaction: clinical profile and prognosis in 106 adult patients. 61
24085471 2014
368
Subcutaneous implantable cardioverter-defibrillator: Initial experience. 61
25242675 2014
369
Transesophageal echocardiography monitoring in the delivery of a preeclamptic parturient with severe left ventricular noncompaction. 61
25218959 2014
370
Histopathological evidence of Fabry disease in a female patient with left ventricular noncompaction. 61
25246064 2014
371
Ischemic stroke in left ventricular noncompaction and celiac disease. 61
25086466 2014
372
Hypertrabeculation vs left ventricular noncompaction on echocardiogram: a reason to restrict athletic participation? 61
24911984 2014
373
Association of left ventricular noncompaction with polycystic kidney disease as shown by cardiac magnetic resonance imaging. 61
25120407 2014
374
Cardiovascular magnetic resonance determinants of left ventricular noncompaction. 61
24934759 2014
375
Successful palliation of a child with left ventricular noncompaction cardiomyopathy and tricuspid atresia to Fontan procedure. 61
25087802 2014
376
HCN4 mutations in multiple families with bradycardia and left ventricular noncompaction cardiomyopathy. 61
25145517 2014
377
Reversible de novo left ventricular trabeculations in pregnant women: implications for the diagnosis of left ventricular noncompaction in low-risk populations. 61
25006201 2014
378
Reversible left ventricular trabeculations in pregnancy: is this sufficient to make the diagnosis of left ventricular noncompaction? 61
25006200 2014
379
Distal myosin heavy chain-7 myopathy due to the novel transition c.5566G>A (p.E1856K) with high interfamilial cardiac variability and putative anticipation. 61
24953931 2014
380
Authors' response to the letter to the editor "Left ventricular noncompaction associated with a compound heterozygous MYBPC3 mutation". 61
24830826 2014
381
Left ventricular noncompaction cardiomyopathy: an under-recognized disease diagnosed by echocardiography and computed tomography. 61
24924844 2014
382
Left ventricular noncompaction - a case report. 61
25178616 2014
383
Left ventricular noncompaction associated with a compound heterozygous MYBPC3 mutation. 61
24769156 2014
384
Multimodality imaging of mid-ventricular obstruction in left ventricular noncompaction. 61
24459241 2014
385
Evaluation of risk factors for prediction of outcome in fetal spectrum of atrioventricular septal defects. 61
24102719 2014
386
Possible link between right ventricular coronary sinusoids and noncompaction sinusoids in pulmonary atresia with intact ventricular septum patients that later develop left ventricular noncompaction. 61
24767937 2014
387
Systemic lupus erythematosus and transient left ventricular noncompaction. 61
24863427 2014
388
Left ventricular "pseudo-pseudoaneurysm": an unusual case of focal left ventricular noncompaction. 61
24955062 2014
389
Left ventricular noncompaction associated with hypertrophic cardiomyopathy: echocardiographic diagnosis and genetic analysis of a new pedigree in China. 61
24698237 2014
390
Abnormal cardiac formation in hypertrophic cardiomyopathy: fractal analysis of trabeculae and preclinical gene expression. 61
24704860 2014
391
Left ventricular noncompaction cardiomyopathy: three decades of progress. 61
24794547 2014
392
A combination of left ventricular hypertrabeculation/noncompaction and muscular dystrophy in a stroke patient. 61
24774359 2014
393
Left ventricular hypertrabeculation/noncompaction in an Eritrean war invalid with neuromuscular disease. 61
24768373 2014
394
A case of fetal diagnosis of noncompaction cardiomyopathy and coarctation of the aorta. 61
25032060 2014
395
Clinical spectrum of isolated left ventricular noncompaction: thromboembolic events, malignant left ventricular arrhythmias, and refractory heart failure. 61
24576431 2014
396
Next-generation sequencing (NGS) as a fast molecular diagnosis tool for left ventricular noncompaction in an infant with compound mutations in the MYBPC3 gene. 61
24602869 2014
397
Right ventricular ablation as a therapeutic option for left ventricular hypertrabeculation / noncompaction. 61
24669111 2014
398
Left ventricular non-compaction with viral myocarditis: a rare presentation of a rarer disease. 61
25327072 2014
399
Left ventricular hypertrabeculation/noncompaction and pregnancy. 61
24439859 2014
400
Arrhythmogenic Right Ventricle in Left Ventricular Non-compaction - In response to "Right Ventricular Ablation as a Therapeutic Option for Left Ventricular Hypertrabeculation / noncompaction". 61
24669113 2014
401
Right ventricular morphology and systolic function in left ventricular noncompaction cardiomyopathy. 61
24462071 2014
402
Ventricular arrhythmias due to left ventricular noncompaction cardiomyopathy: a diagnosis in hindsight. 61
23791713 2014
403
Rare combination of left ventricular noncompaction, bicuspid aortic valve and myocardial bridging. Rare case or common genetic mutations? 61
24360154 2014
404
Aortic root replacement in a patient with left ventricular noncompaction. 61
24384213 2014
405
Verapamil-sensitive fascicular ventricular tachycardia in a patient with isolated left ventricular noncompaction. 61
24827485 2014
406
Tachycardia-induced cardiomyopathy due to repetitive monomorphic ventricular ectopy in association with isolated left ventricular non-compaction. 61
24292167 2014
407
[Juvenile neuronal ceroid-lipofuscinosis with hypertrophic cardiomyopathy and left ventricular noncompaction: a case report]. 61
24429647 2014
408
Identification of critical regions and candidate genes for cardiovascular malformations and cardiomyopathy associated with deletions of chromosome 1p36. 61
24454898 2014
409
Guiding the management of ventricular arrhythmias in patients with left ventricular noncompaction cardiomyopathy: a knowledge gap. 61
25290726 2014
410
Left ventricular noncompaction cardiomyopathy: a case report and literature review. 61
25664015 2014
411
[A clinical case of diagnosis of left ventricular noncompaction myocardium in a patient with infectious myocarditis]. 61
24864472 2014
412
Echocardiographic and histopathological diagnosis of left ventricular noncompaction. 61
25563624 2014
413
Left ventricular twist in left ventricular noncompaction. 61
23793875 2014
414
Defining left ventricular noncompaction using cardiac computed tomography. 61
23689383 2014
415
Juvenile 'cryptogenic' stroke from noncompaction in a neuromuscular disease. 61
24481414 2014
416
Inherited cardiomyopathies. 61
25186923 2014
417
Myopathy should determine the anesthetic management in left ventricular hypertrabeculation/noncompaction. 61
24800200 2014
418
Letter by Stollberger and Finsterer regarding article, "mortality and sudden death in pediatric left ventricular noncompaction in a tertiary referral center". 61
24446415 2014
419
Aortic valve replacement for aortic regurgitation with rare left ventricular non-compaction. 61
23196658 2014
420
Response to letter regarding article, "mortality and sudden death in pediatric left ventricular noncompaction in a tertiary referral center". 61
24446416 2014
421
Magnetic resonance assessment of prevalence and correlates of right ventricular abnormalities in isolated left ventricular noncompaction. 61
24176065 2014
422
Incidental diagnosis of a familial left ventricular noncompaction on a chest CT angiography. 61
24018053 2014
423
Familial ebstein anomaly, left ventricular hypertrabeculation, and ventricular septal defect associated with a MYH7 mutation. 61
23956225 2013
424
Hypertrophic cardiomyopathy associated with left ventricular noncompaction cardiomyopathy and coronary fistulae: a case report. One genotype, three phenotypes? 61
24268868 2013
425
Unclassified cardiomyopathies in neuromuscular disorders. 61
24154801 2013
426
Left ventricular noncompaction in patients with bicuspid aortic valve. 61
24044978 2013
427
Left ventricular noncompaction (LVNC) and low mitochondrial membrane potential are specific for Barth syndrome. 61
23361305 2013
428
[Coronary Artery Bypass Grafting (CABG) and simultaneous cardiac resynchronization therapy in a patient with left ventricular noncompaction repeating heart failure]. 61
24322314 2013
429
Grant et al. 1926 did not provide the first description of left ventricular hypertrabeculation/noncompaction. 61
24055237 2013
430
Pathomorphologic findings in left ventricular hypertrabeculation/noncompaction of adults in relation to neuromuscular disorders. 61
24182672 2013
431
New oral anticoagulants for stroke prevention in left ventricular hypertrabeculation/noncompaction? 61
23602298 2013
432
Cardiac myosin-binding protein C gene mutation expressed as hypertrophic cardiomyopathy and left ventricular noncompaction within two families: insights from cardiac magnetic resonance in clinical screening: Camuglia MYBPC3 gene mutation and MRI. 61
23642604 2013
433
Left ventricular noncompaction cardiomyopathy: updated review. 61
24132556 2013
434
Human immunodeficiency virus and left ventricular noncompaction. 61
23958416 2013
435
Prognostic impact of left ventricular noncompaction in patients with Duchenne/Becker muscular dystrophy--prospective multicenter cohort study. 61
23333368 2013
436
A novel method for quantification of left ventricular noncompaction using two-dimensional echocardiography in children. 61
24800010 2013
437
Left ventricular hypertrabeculation/noncompaction coincidentally found in sporadic inclusion body myositis. 61
23462629 2013
438
Left ventricular noncompaction cardiomyopathy. 61
24282766 2013
439
Peripartum cardiomyopathy associated with left ventricular noncompaction phenotype and reversible rigid body rotation. 61
24046479 2013
440
Comparison of systolic and diastolic criteria for isolated LV noncompaction in CMR. 61
23769489 2013
441
A study of tropomyosin's role in cardiac function and disease using thin-filament reconstituted myocardium. 61
23700264 2013
442
Disorders of left ventricular trabeculation/compaction or right ventricular wall formation. 61
23843328 2013
443
CHADS2- and CHA2DS2VASc scores and embolic risk in left ventricular hypertrabeculation/noncompaction. 61
22142779 2013
444
Compacta-thickness--a valuable or unhelpful criterion in the diagnosis of left ventricular noncompaction/hypertrabeculation? 61
23176775 2013
445
Fetal diagnosis of left-ventricular noncompaction cardiomyopathy in identical twins with discordant congenital heart disease. 61
22695766 2013
446
Molecular mechanism of ventricular trabeculation/compaction and the pathogenesis of the left ventricular noncompaction cardiomyopathy (LVNC). 61
23843320 2013
447
Interpreting secondary cardiac disease variants in an exome cohort. 61
23861362 2013
448
Left ventricular noncompaction in Duchenne muscular dystrophy. 61
23914774 2013
449
Ebstein anomaly associated with left ventricular noncompaction: an autosomal dominant condition that can be caused by mutations in MYH7. 61
23794396 2013
450
Barth syndrome. 61
23843353 2013
451
Coexistence of left ventricular noncompaction and aortic interruption. 61
23724972 2013
452
Left ventricular noncompaction complicated by mitral valve prolapse: report of a case. 61
22847676 2013
453
Surgery for congenital aortic stenosis in children with left ventricular noncompaction. 61
23763604 2013
454
Left ventricular hypertrabeculation/non-compaction in a pregnant woman. 61
24217259 2013
455
A rare association of left ventricular diverticulum and noncompaction: continuum of common developmental abnormality? 61
23560538 2013
456
Ebstein's anomaly. 61
24502034 2013
457
Left ventricular hypertrabeculation/noncompaction in β-thalassemia. 61
23553561 2013
458
Mortality and sudden death in pediatric left ventricular noncompaction in a tertiary referral center. 61
23633270 2013
459
Incessant slow bundle branch reentrant ventricular tachycardia in a young patient with left ventricular noncompaction. 61
23747052 2013
460
Left bundle branch block, atrioventricular block, torsade de pointes and long QT syndrome: is this too much for a rare cardiomyopathy? 61
23618687 2013
461
Two different cardiomyopathies in a single patient : hypertrophic cardiomyopathy and left ventricular noncompaction. 61
23263242 2013
462
Left ventricular noncompaction cardiomyopathy. 61
24015429 2013
463
Refinement of echocardiographic criteria for left ventricular noncompaction. 61
21944384 2013
464
Quantification of left ventricular trabeculae using fractal analysis. 61
23663522 2013
465
Quantitative electrocardiographic measures, neuromuscular disorders, and survival in left ventricular hypertrabeculation/noncompaction. 61
23714083 2013
466
Left ventricular hypertrabeculation/noncompaction in gylcogenosis type 1b. 61
23523141 2013
467
Familal left ventricular hypertrabeculation (noncompaction) is myopathic. 61
21788087 2013
468
[Association of left ventricular noncompaction with patent ductus arteriosus: a multimodality imaging approach]. 61
23567774 2013
469
Postoperative normalization of left ventricular noncompaction and new echocardiographic signs in aorta to left ventricular tunnel. 61
23346986 2013
470
Features of left ventricular noncompaction in peripartum cardiomyopathy: a case series. 61
23103144 2013
471
Electrocardiographic findings suggestive of cardiomyopathy: what to look for and what to do next. 61
23478557 2013
472
Inherited cardiomyopathies: molecular genetics and clinical genetic testing in the postgenomic era. 61
23274168 2013
473
Left ventricular non-noncompaction: the mitral valve prolapse of the 21st century? 61
22658573 2013
474
Left-ventricular noncompaction in an infant with trisomy 21. 61
22555891 2013
475
Ebstein's anomaly may be caused by mutations in the sarcomere protein gene MYH7. 61
21604106 2013
476
[Isolated left ventricular non-compaction: a single-center experience]. 61
23337431 2013
477
[Family form of isolated left ventricular noncompaction; case of a mother and her son observed in Gabon]. 61
21676376 2013
478
14-3-3ε gene variants in a Japanese patient with left ventricular noncompaction and hypoplasia of the corpus callosum. 61
23266643 2013
479
Isolated left ventricular noncompaction in a newborn with Pierre-Robin sequence. 61
22447382 2013
480
Implantable loop-recorders in myopathic and non-myopathic patients with left ventricular hypertrabeculation/noncompaction. 61
21652098 2013
481
Noncompaction cardiomyopathy is associated with mechanical dyssynchrony: a potential underlying mechanism for favorable response to cardiac resynchronization therapy. 61
23384632 2013
482
Complex II deficiency--a case report and review of the literature. 61
23322652 2013
483
A very rare case of coexistence of ventricular noncompaction cardiomyopathy, myocardial bridging and atherosclerosis. 61
24570713 2013
484
Sinus node dysfunction as the first manifestation of left ventricular noncompaction with multiple cardiac abnormalities. 61
24086099 2013
485
Inherited heart rhythm disease: negotiating the minefield for the practicing cardiologist. 61
23261322 2013
486
Ultrastructural findings in noncompaction prevail with neuromuscular disorders. 61
24061197 2013
487
A left ventricular noncompaction in a patient with long QT syndrome caused by a KCNQ1 mutation: a case report. 61
22354620 2013
488
Isolated left ventricular noncompaction causing stroke in a 30-year-old woman: case report and literature review. 61
23914034 2013
489
Combination of left ventricular noncompaction and partial atrioventricular canal defect in a 21-year-old male: a case report. 61
23362371 2013
490
Isolated left ventricular noncompaction: a review of three different presentations for a rare disease. 61
23427367 2013
491
[Acute cerebral ischemia: an unusual clinical presentation of isolated left ventricular noncompaction in an adult patient]. 61
23258208 2013
492
Focal left atrial tachycardia in a patient with left ventricular noncompaction. 61
23762071 2013
493
An adult patient with left ventricular noncompaction detected on radionuclide myocardial perfusion imaging. 61
23503407 2013
494
Isolated right ventricular noncompaction in a newborn. 61
22810045 2013
495
Just sinus bradycardia or something more serious? 61
23476865 2013
496
Studies on left ventricular hypertrabeculation/noncompaction: the need for in-depth ultrastructural investigations. 61
24157564 2013
497
Noncompaction in mitochondrial myopathy: visible on microscopy but absent on macroscopic inspection. 61
23736098 2013
498
Progression of neurological and cardiovascular disease in left ventricular hypertrabeculation/noncompaction. 61
22658350 2012
499
14-3-3ε plays a role in cardiac ventricular compaction by regulating the cardiomyocyte cell cycle. 61
23071090 2012
500
Left ventricular noncompaction in patients with β-thalassemia: uncovering a previously unrecognized abnormality. 61
22965286 2012
501
Left ventricular noncompaction cardiomyopathy in Barth syndrome: an example of an undulating cardiac phenotype necessitating mechanical circulatory support as a bridge to transplantation. 61
22427193 2012
502
Surgical repair of left ventricular noncompaction in a patient with a novel mutation of the myosin heavy chain 7 gene. 61
23117287 2012
503
Left ventricular hypertrabeculation/non-compaction in a Duchenne/Becker muscular dystrophy carrier with epilepsy. 61
22592024 2012
504
Familial dilated cardiomyopathy. Clinical and genetic characteristics. 61
23223770 2012
505
Intrafamilial variability for novel TAZ gene mutation: Barth syndrome with dilated cardiomyopathy and heart failure in an infant and left ventricular noncompaction in his great-uncle. 61
23031367 2012
506
Cardiomyopathy mimicking left ventricular noncompaction in a patient with lupus nephritis. 61
28509061 2012
507
A review on advanced atrioventricular block in young or middle-aged adults. 61
22897386 2012
508
A rare combination of left ventricular noncompaction, patent ductus arteriosus, and persistent left superior vena cava demonstrated by multidetector computed tomography and echocardiography. 61
22498449 2012
509
Neurological comorbidity affects prognosis in left ventricular hypertrabeculation/noncompaction. 61
22515930 2012
510
Multimodal imaging in the diagnosis of isolated left ventricular noncompaction. 61
22773171 2012
511
Morphologic heterogeneity in left ventricular noncompaction resulting in accessory left ventricular chambers. 61
23170026 2012
512
Loss of function of hNav1.5 by a ZASP1 mutation associated with intraventricular conduction disturbances in left ventricular noncompaction. 61
22929165 2012
513
Neuromuscular aspects of channelopathies with left-ventricular hypertrabeculation/noncompaction. 61
22706706 2012
514
Left ventricular noncompaction in a patient with multiminicore disease. 61
20729748 2012
515
Diagnosis of left ventricular noncompaction by computed tomography. 61
23077386 2012
516
Isolated left ventricular noncompaction in identical twins. 61
22748355 2012
517
Noncompaction myocardium in association with type Ib glycogen storage disease. 61
22854198 2012
518
A case of left ventricular noncompaction accompanying fasciculo-ventricular accessory pathway and atrial flutter. 61
23170100 2012
519
Reduced left ventricular compacta thickness: a novel echocardiographic criterion for non-compaction cardiomyopathy. 61
22883316 2012
520
Left ventricular noncompaction cardiomyopathy: an overdiagnosed disease. 61
23071178 2012
521
Left ventricular noncompaction cardiomyopathy and aortopathy in a patient with recessive dystrophic epidermolysis bullosa. 61
22991407 2012
522
Noncompaction cardiomyopathy and pregnancy: An alarming coexistence ending in a favourable outcome. 61
23620702 2012
523
Thrombolysis of ischemic stroke from noncompaction in metabolic myopathy. 61
22931737 2012
524
Toxoplasmosis or left ventricular hypertrabeculation / non-compaction. 61
23049627 2012
525
Left ventricular noncompaction: a proposal of new diagnostic criteria by multidetector computed tomography. 61
22981859 2012
526
Videoscopic left cardiac sympathetic denervation for patients with recurrent ventricular fibrillation/malignant ventricular arrhythmia syndromes besides congenital long-QT syndrome. 61
22787014 2012
527
Malonyl coenzyme A decarboxylase deficiency: early dietary restriction and time course of cardiomyopathy. 61
22778304 2012
528
The prognostic significance of fragmented QRS in patients with left ventricular noncompaction cardiomyopathy. 61
22445100 2012
529
Left ventricular noncompaction cardiomyopathy. 61
22658564 2012
530
Left ventricular noncompaction and aneurysm revealed by left ventriculography. 61
21954168 2012
531
Three-dimensional echocardiography for the evaluation of left ventricular noncompaction. 61
22658560 2012
532
Coexistence of left ventricular noncompaction and double-orifice mitral valve in a patient with congestive heart failure. 61
23692732 2012
533
Disappearance of left ventricular hypertrabeculation/noncompaction and sudden death in a patient with Turner mosaic syndrome. 61
22503583 2012
534
Left ventricular hypertrabeculation/noncompaction with epilepsy, other heart defects, minor facial anomalies and new copy number variants. 61
22830313 2012
535
Poliomyelitis and left ventricular hypertrabeculation (noncompaction). 61
22078391 2012
536
Isolated left ventricular noncompaction with a congenital aneurysm presenting with recurrent embolism. 61
22787529 2012
537
Isolated left ventricular noncompaction: what do we really know? 61
22415394 2012
538
Needed--electrocardiographic findings in left ventricular noncompaction. 61
22578906 2012
539
Trabeculated (noncompacted) and compact myocardium in adults: the multi-ethnic study of atherosclerosis. 61
22499849 2012
540
[Non-compaction cardiomyopathy in a 5-generation Chinese family]. 61
22801312 2012
541
[One patient, one mutation and two cardiomyopathies - hypertrophic cardiomyopathy and left ventricular noncompaction]. 61
22386539 2012
542
Left ventricular noncompaction: a 25-year odyssey. 61
22284845 2012
543
Left ventricular noncompaction. 61
22565075 2012
544
Isolated left ventricular noncompaction in sub-Saharan Africa: a clinical and echocardiographic perspective. 61
22235038 2012
545
Cardiac 123I-MIBG scintigraphy and arrhythmic risk in left ventricular noncompaction. 61
22336571 2012
546
Rhythm disorders in isolated left ventricular noncompaction. 61
21639721 2012
547
Differing clinical courses and outcomes in two siblings with Barth syndrome and left ventricular noncompaction. 61
21987083 2012
548
Caseous calcification associated with left ventricular noncompaction: a multimodality diagnostic approach. 61
21807427 2012
549
An unusual cause of cardiac failure. 61
22306783 2012
550
Electrocardiogram in left ventricular hypertrabeculation/noncompaction. 61
22293225 2012
551
Left ventricular noncompaction presenting as peripartum cardiomyopathy. 61
21741100 2012
552
Genetic disorder or toxoplasma myocarditis: a case report of dilated cardiomyopathy with hypertrabeculation in a young asymptomatic woman. 61
22574099 2012
553
Failure of transvenous ICD to terminate ventricular fibrillation in a patient with left ventricular noncompaction and polycystic kidneys. 61
20946291 2012
554
Reproducibility of echocardiographic diagnosis of left ventricular noncompaction. 61
22036126 2012
555
Three-dimensional echocardiographic characterization of patients with left ventricular noncompaction. 61
22154390 2012
556
Echocardiographic diagnosis and prognosis of fetal left ventricular noncompaction. 61
22014428 2012
557
Tiger heart: a variant of isolated left ventricular noncompaction? 61
22719167 2012
558
Progressive left ventricular noncompaction and systolic dysfunction. 61
22826654 2012
559
Isolated left ventricular noncompaction in a 90-year-old man. 61
22740746 2012
560
Left ventricular noncompaction associated with multiple coronary cameral fistulae. 61
22740760 2012
561
Left ventricular noncompaction: clinical-echocardiographic study. 61
22397294 2012
562
Myocardial infarction in a patient with left ventricular noncompaction: a case report. 61
22924011 2012
563
Stroke and Stroke-like Episodes in Muscle Disease. 61
22715346 2012
564
'Idiopathic' acute myocardial infarction in a young patient with noncompaction cardiomyopathy. 61
22825907 2012
565
Left ventricular noncompaction: a diagnostically challenging cardiomyopathy. 61
22664784 2012
566
Pathogenicity of the transition m.3308T>C in left ventricular hypertrabeculation/noncompaction. 61
22777278 2012
567
Predictors of adverse outcome in adolescents and adults with isolated left ventricular noncompaction. 61
22036106 2012
568
Multiple left ventricular thrombi in a patient with left ventricular noncompaction. 61
22949776 2012
569
Coffin-Lowry syndrome and left ventricular noncompaction cardiomyopathy with a restrictive pattern. 61
22009732 2011
570
Heterozygous promotor haplotype LXA/LYB in MBL-deficiency associated with myopathy and left ventricular hypertrabeculation/noncompaction. 61
19301063 2011
571
A rare combination of two rare diseases: left ventricular noncompaction and hypertrophic cardiomyopathy. 61
22051339 2011
572
Neurogenic stunned myocardium presenting as left ventricular hypertrabeculation in childhood: a variant of Takotsubo cardiomyopathy? 61
21478797 2011
573
Left ventricular hypertrabeculation/noncompaction associated with severe anemia, delusion, and polyneuropathy. 61
21295868 2011
574
Rare combination of congenital aplasia of the right pulmonary veins, left ventricular noncompaction, partial membranous obstruction of left-sided pulmonary veins and secundum atrial septal defect. 61
21242010 2011
575
Cardiac magnetic resonance imaging characteristics of isolated left ventricular noncompaction in a Chinese adult Han population. 61
21046254 2011
576
Left ventricular noncompaction/hypertrabeculation: distinctive entity or abnormality, frequently associated with neuromuscular disorders? 61
21985954 2011
577
Exercise-induced atrial and ventricular tachycardias in a patient with left ventricular noncompaction and normal ejection fraction. 61
20565692 2011
578
Frequency of stroke and embolism in left ventricular hypertrabeculation/noncompaction. 61
21784395 2011
579
Left ventricular noncompaction cardiomyopathy. 61
22218001 2011
580
Long-term myocardial recovery after mitral valve replacement in noncompaction cardiomyopathy. 61
21958914 2011
581
Coronary angiography in noncompaction with and without neuromuscular disorders. 61
21161428 2011
582
Left ventricular noncompaction syndrome masquerading or misdiagnosed as congenital long QT syndrome: remember QT prolongation does not equal long QT syndrome. 61
21696549 2011
583
Noncompaction of the left ventricular myocardium in a boy with a novel chromosome 8p23.1 deletion. 61
21834050 2011
584
Isolated noncompaction of the left ventricular myocardium in adults: a systematic overview. 61
21872148 2011
585
Multiple left ventricular inferoseptal clefts. Multimodality imaging appearance and differential diagnosis. 61
21344270 2011
586
Isolated left ventricular noncompaction: a small, noncompacted segment may cause serious complications. 61
20347493 2011
587
Isolated left ventricular noncompaction mimicking ventricular mass. 61
21545516 2011
588
[Incidence of coronary artery disease and outcome of patients with left ventricular noncompaction]. 61
22169419 2011
589
Overreaction to noncompaction in a patient with ankylosing spondylitis, Parkinson disease, migraine and myopathy. 61
19616325 2011
590
Neuromuscular and cardiac comorbidity determines survival in 140 patients with left ventricular hypertrabeculation/noncompaction. 61
20226551 2011
591
Histopathological features of delayed enhancement cardiovascular magnetic resonance in isolated left ventricular noncompaction. 61
21737026 2011
592
Fatal outcome of aortic-valve endocarditis in noncompaction/hypertrabeculation. 61
19733406 2011
593
Left ventricular hypertrabeculation/noncompaction in hereditary inclusion body myopathy. 61
19900728 2011
594
Dilation of the aortic root in mitochondrial disease patients. 61
21406331 2011
595
Ventricular noncompaction and absent thumbs in a newborn with tetrasomy 5q35.2-5q35.3: an association with Hunter-McAlpine syndrome? 61
21567924 2011
596
Implantable cardioverter defibrillator in a young child with left ventricular noncompaction. 61
21798475 2011
597
Left ventricular noncompaction. 61
21119528 2011
598
Left ventricular hypertrabeculation/noncompaction associated with coronary heart disease and myopathy. 61
19342113 2011
599
Left ventricular noncompaction in Sotos syndrome. 61
21484993 2011
600
Noncompaction in a HIV-positive with cortical blindness as initial manifestation of progressive multifocal leucencephalopathy. 61
19328566 2011
601
Complete atrioventricular block and reversible systolic dysfunction in left ventricular hypertrabeculation/non-compaction with metabolic myopathy. 61
21138615 2011
602
Cardiac devices and neuromuscular disorders in left ventricular noncompaction. 61
21334754 2011
603
Left-ventricular noncompaction in a pediatric population: predictors of survival. 61
21188370 2011
604
Electrocardiographic findings at initial diagnosis in children with isolated left ventricular noncompaction. 61
21496170 2011
605
Left ventricular noncompaction: analysis of a pediatric population. 61
21638988 2011
606
Left ventricular non-compaction cardiomyopathy mimicking an infiltrative cardiac disease. 61
19232764 2011
607
Isolated left ventricular noncompaction cardiomyopathy diagnosed by transesophageal echocardiography. 61
21487457 2011
608
Noncompaction cardiomyopathy and dextroversion of the heart. 61
20865233 2011
609
Mutations in the sarcomere gene MYH7 in Ebstein anomaly. 61
21127202 2011
610
Subendocardial fibrosis in left ventricular hypertrabeculation-cause or consequence? 61
21344021 2011
611
Trisomy 13 in a 9-year-old girl with left ventricular noncompaction. 61
21082175 2011
612
Left ventricular noncompaction and coronary artery fistula in an infant with deletion 22q11.2. 61
21153726 2011
613
Identification of a novel TPM1 mutation in a family with left ventricular noncompaction and sudden death. 61
20965760 2011
614
Left ventricular noncompaction associated with a sinoatrial node artery originating from the posterolateral branch of the right coronary artery. 61
21446386 2011
615
Long-term follow-up of patients with isolated left ventricular noncompaction: role of electrocardiography in predicting poor outcome. 61
21617326 2011
616
A neonatal case of left ventricular noncompaction associated with trisomy 18. 61
21848008 2011
617
How to manage left ventricular hypertrabeculation/noncompaction in Fabry's disease? 61
22156620 2011
618
The mitochondrial ND1 3308T>C mutation may not be associated with left ventricular hypertrabeculation/noncompaction. 61
21968326 2011
619
No rationale for a diagnostic ratio in left ventricular hypertrabeculation/noncompaction. 61
20226545 2011
620
Transition m.3308T>C in the ND1 gene is associated with left ventricular hypertrabeculation/noncompaction. 61
21625124 2011
621
Isolated left ventricular noncompaction in a case of sotos syndrome: a casual or causal link? 61
21747990 2011
622
Left ventricular noncompaction in a patient with fabry disease: overdiagnosis, morphological manifestation of fabry disease or two unrelated rare conditions in the same patient? 61
21952291 2011
623
Heart failure, atrial fibrillation and neuromuscular disorders influence mortality in left ventricular hypertrabeculation/noncompaction. 61
21968288 2011
624
An adult patient with isolated left ventricular noncompaction presented with atrial fibrillation and complete atrioventricular block. 61
22041364 2011
625
Ventricular and supraventricular arrhythmias and heart failure in a patient with left ventricular noncompaction and Brugada syndrome. 61
21660923 2011
626
ICD implantation in left ventricular noncompaction: a case report and review of the literature. 61
22113759 2011
627
Exercise-induced right ventricular outflow tract tachycardia in a patient with isolated left ventricular noncompaction. 61
22347651 2011
628
Transient cardiac arrest in patient with left ventricular noncompaction (spongiform cardiomyopathy). 61
21410361 2011
629
Noncompaction cardiomyopathy--a review of eight cases. 61
21428140 2010
630
Arrhythmogenic left ventricular cardiomyopathy associated with noncompaction. 61
21095364 2010
631
A Case of Isolated Left Ventricular Noncompaction with Basal ECG-Tracing Strongly Suggestive for Type-2 Brugada Syndrome. 61
21151698 2010
632
Consensus on unsolved issues of left ventricular hypertrabeculation/noncompaction is warranted. 61
19897256 2010
633
A rare case of coronary artery bypass grafting in a patient with left ventricular noncompaction. 61
21095365 2010
634
Systolic-diastolic coupling of myocardial deformation of the left ventricle in children with left ventricular noncompaction. 61
20878168 2010
635
Shall a pilot with left ventricular hypertrabeculation/noncompaction fly passengers? 61
19428132 2010
636
[Isolated noncompaction of the ventricular myocardium]. 61
21108206 2010
637
Role of device therapy in left ventricular noncompaction cardiomyopathy: is it different from other causes of heart failure? 61
20654730 2010
638
Implantable cardioverter-defibrillator and cardiac resynchronization therapy in patients with left ventricular noncompaction. 61
20493963 2010
639
Left ventricular non-compaction and its cardiac and neurologic implications. 61
20549343 2010
640
Left ventricular noncompaction: a new form of heart failure. 61
20869646 2010
641
Can cardiac magnetic resonance imaging resolve cardiac and neurological enigmas of left ventricular hypertrabeculation/non-compaction? 61
21130972 2010
642
Consider potential pitfalls, myopathy and chromosomal abnormalities when diagnosing left ventricular hypertrabeculation/noncompaction. 61
19201043 2010
643
Even isolated left ventricular hypertrabeculation may indicate multisystem disease. 61
20702960 2010
644
Ebstein's anomaly with left ventricular noncompaction and bicuspid aortic valve. 61
20813287 2010
645
Sudden infant death syndrome and left ventricular hypertrabeculation-hidden arrhythmogenic entity? 61
20981130 2010
646
Left ventricular noncompaction and myocardial fibrosis: a case report. 61
20843341 2010
647
Images in cardiology. A previously undescribed variant of isolated left ventricular noncompaction. 61
20723805 2010
648
Intracavitary "fountains" in left ventricular noncompaction. 61
20633815 2010
649
The importance of genetic counseling, DNA diagnostics, and cardiologic family screening in left ventricular noncompaction cardiomyopathy. 61
20530761 2010
650
Gonadal mosaicism of a TAZ (G4.5) mutation in a Japanese family with Barth syndrome and left ventricular noncompaction. 61
20303308 2010
651
Left ventricular noncompaction is associated with mutations in the mitochondrial genome. 61
20211276 2010
652
Sudden unexpected death due to left ventricular noncompaction of myocardium: case report and review of the literature. 61
20032775 2010
653
[Assessment of left ventricular systolic synchronicity by quantitative tissue velocity imaging in patients with left ventricular noncompaction]. 61
20654096 2010
654
[Echocardiographic standardized myocardial segmentation features in patients with left ventricular noncompaction]. 61
20654097 2010
655
[Clinical and genetic features of left ventricular noncompaction: a continuum in cardiomyopathies]. 61
20860157 2010
656
Callosal agenesis and left ventricular hypertrabeculation/noncompaction. 61
20425847 2010
657
The genetics of dilated cardiomyopathy. 61
20186049 2010
658
[Comparison of clinical and MRI features between dilated cardiomyopathy and left ventricular noncompaction]. 61
20654095 2010
659
[Imaging features of left ventricular noncompaction]. 61
20654093 2010
660
Acquired noncompaction associated with coronary heart disease and myopathy. 61
20457346 2010
661
Evolving molecular diagnostics for familial cardiomyopathies: at the heart of it all. 61
20370590 2010
662
Sustainable myocardial recovery after mitral reconstruction for left ventricular noncompaction. 61
20338359 2010
663
MR imaging features of ventricular noncompaction: emphasis on distribution and pattern of fibrosis. 61
19328640 2010
664
[Left ventricular hypertrabeculation or noncompaction: are new diagnostic criteria required?]. 61
20334812 2010
665
Consider cardiac, neuromuscular, and chromosomal comorbidities in left ventricular hypertrabeculation/noncompaction. 61
20381682 2010
666
In- and outpatients with noncompaction: differences in cardiac and neuromuscular co-morbidity. 61
19095319 2010
667
Ischemic stroke as the first manifestation of severe ventricular hypertrabeculation/non-compaction. 61
20730249 2010
668
[Lack of MR late-enhancement in left ventricular non-compaction in infants and young children]. 61
20018334 2010
669
Ventricular septal defect repair in an infant with severe pulmonary hypertension and preoperatively diagnosed left ventricular noncompaction. 61
19660309 2010
670
Left ventricular hypertrabeculation/noncompaction in a patient with peripartum cardiomyopathy. 61
18793811 2010
671
Lown-Ganong-Levine syndrome in a 3-month-old infant with isolated left ventricular noncompaction. 61
19859765 2010
672
Left ventricular noncompaction cardiomyopathy: what do we know? 61
20700091 2010
673
Left ventricular noncompaction: a rare disorder in adults and its association with 1p36 chromosomal anomaly. 61
20034097 2010
674
Heart transplantation in an adult patient with isolated noncompaction of the left ventricular myocardium. 61
20516759 2010
675
Neuromuscular disorders in left ventricular hypertrabeculation/noncompaction. 61
20632953 2010
676
Arrhythmias and left ventricular hypertrabeculation /noncompaction. 61
20632950 2010
677
A teenager with Marfan syndrome and left ventricular noncompaction. 61
19795159 2010
678
Left ventricular noncompaction: travelling the road from diagnosis to outcomes. 61
20122495 2010
679
Left ventricular noncompaction. 61
20109597 2010
680
Cardiac segmental analysis in left ventricular noncompaction: experience in a pediatric population. 61
19857942 2010
681
[Left ventricular noncompaction concurrent with bronchoectatic disease complicated by secondary AA-amyloidosis with renal involvement]. 61
20364708 2010
682
Left ventricular trabeculae: quantification in different cardiac diseases and impact on left ventricular morphological and functional parameters assessed with cardiac magnetic resonance. 61
19543106 2009
683
Acquired left ventricular hypertrabeculation/noncompaction in myotonic dystrophy type 1. 61
18691779 2009
684
Left ventricular noncompaction: diagnosis by three-dimensional echocardiography. 61
20222350 2009
685
Myopathy, left ventricular noncompaction, and tetralogy of fallot. 61
19816976 2009
686
Isolated left ventricular noncompaction cardiomyopathy accompanied by severe mitral regurgitation. 61
19997546 2009
687
Aortic valve replacement in noncompaction cardiomyopathy at two-year follow-up. 61
19765168 2009
688
Electrocardiographic characteristics at initial diagnosis in patients with isolated left ventricular noncompaction. 61
19766768 2009
689
Sarcomere mutations in cardiomyopathy with left ventricular hypertrabeculation. 61
20031619 2009
690
Left ventricular noncompaction: a rare cause of hydrops fetalis. 61
19506938 2009
691
Isolated left ventricular noncompaction syndrome. 61
19801037 2009
692
Penetrance and risk profile in inherited cardiac diseases studied in a dedicated screening clinic. 61
19616675 2009
693
Reversible isolated left ventricular non-compaction? 61
18694608 2009
694
Analysis of ventricular hypertrabeculation and noncompaction using genetically engineered mouse models. 61
19396388 2009
695
Left ventricular noncompaction: cardiovascular magnetic resonance and echocardiographic imaging of a rare isolated midseptal form. 61
17803244 2009
696
Is left ventricular noncompaction in children truly an isolated lesion? 61
19184169 2009
697
Cardiogenetics, neurogenetics, and pathogenetics of left ventricular hypertrabeculation/noncompaction. 61
19184181 2009
698
Left ventricular noncompaction in children. 61
19664035 2009
699
Noninvasive evaluation of left ventricular noncompaction: what's new in 2009? 61
19184176 2009
700
Left ventricular noncompaction: a cardiomyopathy often mistaken. 61
19700911 2009
701
Images in cardiovascular medicine. Overlapping phenotypes: left ventricular noncompaction and hypertrophic cardiomyopathy. 61
19528341 2009
702
Left ventricular noncompaction by 3-dimensional echocardiography: an overdiagnosis? 61
19470828 2009
703
Left ventricular noncompaction associated with Ebstein's anomaly. 61
19717963 2009
704
Cardiac and neurological implications in beta-thalassemia with left ventricular hypertrabeculation/non-compaction. 61
19482962 2009
705
Possible new syndrome: Left ventricular noncompaction, partial agenesis of the corpus callosum, and developmental delay in a Brazilian child. 61
19396836 2009
706
Isolated left ventricular noncompaction diagnosed by transthoracic threedimensional echocardiography. 61
19484157 2009
707
Left ventricular noncompaction. 61
19318934 2009
708
Fireworks in the left ventricle: Doppler manifestation of left ventricular noncompaction. 61
19460616 2009
709
Stroke from paroxysmal atrial flutter or left ventricular hypertrabeculation/noncompaction, visible only on transesophageal echocardiography. 61
18384895 2009
710
A case of left ventricular noncompaction. 61
19299769 2009
711
Left ventricular noncompaction. 61
20387366 2009
712
Cardiac and neuromuscular implications of left bundle branch block in left ventricular hypertrabeculation/noncompaction. 61
19279992 2009
713
Genetic evaluation of cardiomyopathy--a Heart Failure Society of America practice guideline. 61
19254666 2009
714
A combination of left ventricular noncompaction and double orifice mitral valve. 61
19272135 2009
715
Atrial fibrillation in left ventricular noncompaction with and without neuromuscular disorders is associated with a poor prognosis. 61
18255171 2009
716
Isolated left ventricular hypertrabeculation/noncompaction in a Turner mosaic with male phenotype. 61
19317306 2009
717
Septal hypertrabeculation/noncompaction: cardiac and neurologic implications. 61
19046611 2009
718
Myopathy, apical hypertrophic cardiomyopathy and left ventricular noncompaction within the same family. 61
19317295 2009
719
Replacement of a congenital bicuspid aortic valve in a patient with left ventricular noncompaction. 61
19568396 2009
720
Left ventricular noncompaction. 61
19057090 2009
721
An unusual cause of cardioembolic stroke: isolated left ventricular noncompaction. 61
19131862 2009
722
Ventricular noncompaction in a female patient with nephropathic cystinosis: a case report. 61
19178729 2009
723
Sarcomere mutations in cardiogenesis and ventricular noncompaction. 61
19467449 2009
724
Isolated left ventricular noncompaction as a cause for heart failure and heart transplantation: a single center experience. 61
18663296 2009
725
Aortic valve replacement for aortic regurgitation in a patient with left ventricular noncompaction. 61
19101315 2009
726
[MRI quantification of myocardial function, perfusion, and enhancement in patients with left-ventricular noncompaction]. 61
19303480 2009
727
The diagnosis of left ventricular hypertrabeculation/noncompaction by intraoperative transesophageal echocardiography. 61
18834800 2008
728
Echocardiography in the diagnosis left ventricular noncompaction. 61
19105818 2008
729
Isolated left ventricular noncompaction in children: two cases with different manifestations. 61
25610050 2008
730
Deficiency of mannose-binding lectin, myopathy, calcified endomyocardial fibrosis, and left ventricular noncompaction. 61
18992631 2008
731
Bilateral perisylvian polymicrogyria, periventricular nodular heterotopia, and left ventricular noncompaction in a girl with 10.5-11.1 Mb terminal deletion of 1p36. 61
18925681 2008
732
Congenital aneurysm of the muscular interventricular septum. 61
18313262 2008
733
Cerebrovascular events in left ventricular hypertrabeculation/noncompaction with and without myopathy. 61
18093672 2008
734
Cardiomyopathy of unknown etiology: Barth syndrome unrecognized. 61
19037987 2008
735
Significance of CK-elevation in noncompaction with regard to cardiac and neuromuscular disease. 61
18055044 2008
736
AB0 system and D(Rh o) antigen frequencies in left ventricular hypertrabeculation/noncompaction in relation to cardiac and neuromuscular findings. 61
17727985 2008
737
Left ventricular noncompaction/hypertrabeculation cardiomyopathy. 61
19400533 2008
738
Images in cardiovascular medicine. Ebstein anomaly associated with left ventricular noncompaction. 61
18852371 2008
739
Serious cardioembolic stroke resulting from an overlooked left ventricular noncompaction. 61
18708968 2008
740
Acute metabolic decompensation and sudden death in Barth syndrome: report of a family and a literature review. 61
17846786 2008
741
Does everyone with left ventricular dysfunction need an ICD?: Lessons learned from left ventricular noncompaction. 61
18684273 2008
742
There should not be any "probable" or "possible" left ventricular noncompaction. 61
17643529 2008
743
Diagnosing left ventricular noncompaction by echocardiography and cardiac magnetic resonance imaging and its dependency on neuromuscular disorders. 61
18727062 2008
744
New classification scheme of left ventricular noncompaction and correlation with ventricular performance. 61
18572043 2008
745
Supraventricular arrhythmias in noncompaction of left ventricle: is this a frequent complication? 61
17467827 2008
746
Sinus bradycardia, Wolff Parkinson White, and left ventricular noncompaction: an embryologic connection? 61
17786379 2008
747
Genetic heterogeneity of left-ventricular noncompaction cardiomyopathy. 61
17729299 2008
748
Left ventricular noncompaction and cardiomyopathy: cause, contributor, or epiphenomenon? 61
18382203 2008
749
Implantable cardioverter-defibrillators in patients with left ventricular noncompaction. 61
18373765 2008
750
Prevalence of Barth syndrome in adult left ventricular hypertrabeculation / noncompaction. 61
18365900 2008
751
SCN5A variants in Japanese patients with left ventricular noncompaction and arrhythmia. 61
18368697 2008
752
Atrial parasystole in left ventricular noncompaction: a morphofunctional study by echocardiography and magnetic resonance imaging. 61
18301148 2008
753
An unusual cause of cardioembolic stroke: isolated left ventricular noncompaction. 61
18332842 2008
754
Myocardial fibrosis of left ventricle: magnetic resonance imaging in noncompaction. 61
18219626 2008
755
Left ventricular noncompaction: an unusual cause of ventricular ectopic beats. 61
18488921 2008
756
[Left ventricular noncompaction: a disease in search of a definition]. 61
18364178 2008
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[Sex differences in left ventricular noncompaction in patients with and without neuromuscular disorders]. 61
18364181 2008
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Acquired left ventricular noncompaction as a cardiac manifestation of neuromuscular disorders. 61
18273732 2008
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Isolated left ventricular noncompaction: unusual cause of decompensated heart failure and indication of heart transplantation in the early infancy--case report and literature review. 61
18297218 2008
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Prevalence and characteristics of left ventricular noncompaction in a community hospital cohort of patients with systolic dysfunction. 61
18186774 2008
761
Clinical presentation and genetic analysis of a five generation Chinese family with isolated left ventricular noncompaction. 61
18379140 2008
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Definite, probable, or possible left ventricular hypertrabeculation/noncompaction. 61
17291605 2008
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Cardiac resynchronization therapy in left ventricular hypertrabeculation/non-compaction and myopathy. 61
18029382 2008
764
Left ventricular noncompaction: case of a heart transplant. 61
17600769 2008
765
Isolated left ventricular noncompaction in association with rheumatic mitral stenosis. 61
17336412 2008
766
New-onset heart failure due to heart muscle disease in childhood: a prospective study in the United kingdom and Ireland. 61
18086928 2008
767
Noncompaction and endocarditis in suspected mitochondrial disorder. 61
17303269 2008
768
Comprehensive contrast and 3-dimensional echocardiographic imaging of left ventricular noncompaction cardiomyopathy. 61
17602876 2008
769
[Left ventricular noncompaction: a cardiomyopathy in young individuals. Description of first cases in Africa]. 61
18300520 2007
770
Left ventricular noncompaction: case report and literature review. 61
18338667 2007
771
Complete heart block associated with noncompaction, nail-patella syndrome, and mitochondrial myopathy. 61
17291523 2007
772
Noncompaction and neuromuscular disease with positive troponin-T in a nonagenerian. 61
17929284 2007
773
Acquired noncompaction associated with myopathy. 61
17109978 2007
774
Prognosis of left ventricular hypertrabeculation/noncompaction is dependent on cardiac and neuromuscular comorbidity. 61
17188376 2007
775
Quantification of left ventricular noncompaction and trabecular delayed hyperenhancement with cardiac MRI: correlation with clinical severity. 61
17885073 2007
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[Clinical features of adult left ventricular noncompaction: case report and review]. 61
17940577 2007
777
Thromboembolic complications of left ventricular noncompaction: case report and brief review of the literature. 61
17486570 2007
778
Large recesses associated with left ventricular noncompaction: an unusual presentation of the disease. 61
17123649 2007
779
Reply to 'Differential diagnoses and extracardiac manifestations in left ventricular noncompaction'. 61
17700417 2007
780
Cardiac involveent in type 1 myotonic dystrophy. 61
18072324 2007
781
Left ventricular hypertrabeculation (noncompaction) with prominent calcifications in a patient with mannose-binding lectin deficiency and unclassified myopathy. 61
17868883 2007
782
Differential diagnoses and extracardiac manifestations in left ventricular noncompaction. 61
17700404 2007
783
Reply to 'Left ventricular noncompaction or papillary muscle?'. 61
17700418 2007
784
Left ventricular noncompaction or papillary muscle? 61
17700403 2007
785
Left ventricular noncompaction mimicking peripartum cardiomyopathy. 61
17555940 2007
786
Comparison of two- and three-dimensional transthoracic echocardiography in the assessment of trabeculations and trabecular mass in left ventricular noncompaction. 61
17651107 2007
787
Left ventricular noncompaction with a single coronary artery of anomalous origin. 61
17442437 2007
788
Images in cardiovascular medicine. Isolated left ventricular noncompaction enhanced by echocontrast agent. 61
17646590 2007
789
Left ventricular restoration surgery for isolated left ventricular noncompaction: report of the first successful case. 61
17599523 2007
790
Long-term support with milrinone prior to cardiac transplantation in a neonate with left ventricular noncompaction cardiomyopathy. 61
17551772 2007
791
Ebstein's anomaly and left ventricular noncompaction association. 61
17067700 2007
792
Transient ischemic attack and electrocardiographic abnormalities revealing left ventricular noncompaction. 61
17067702 2007
793
Comparison of regional systolic myocardial velocities in patients with isolated left ventricular noncompaction and patients with idiopathic dilated cardiomyopathy. 61
17543758 2007
794
Cardiologic and neurologic findings in left ventricular hypertrabeculation/noncompaction relating to echocardiographic indication. 61
17023079 2007
795
Consider also extracardiac manifestations in left ventricular noncompaction. 61
17485002 2007
796
Genetic background of left ventricular hypertrabeculation/non-compaction with stroke. 61
17363428 2007
797
Cardiac manifestations in oxidative phosphorylation disorders of childhood. 61
17382120 2007
798
Sporadic isolated left ventricular noncompaction: dread disease or not? 61
17437566 2007
799
A rare combination of left ventricular noncompaction and a right coronary artery-to-right ventricle fistula: echocardiographic features. 61
17384056 2007
800
Disappearance of left ventricular hypertrabeculation/noncompaction after biventricular pacing in a patient with polyneuropathy. 61
17448419 2007
801
Cardiologic and neuromuscular co-morbidity influences mortality of patients with left ventricular hypertrabeculation/noncompaction: comparison with the Austrian general population. 61
17375885 2007
802
Positive troponin-T in noncompaction is associated with neuromuscular disorders and poor outcome. 61
17146603 2007
803
Left ventricular noncompaction in an infant: use of non-ECG-gated cardiac CT. 61
17171353 2007
804
Angiographic diagnosis, prevalence and outcomes for left ventricular noncompaction in children with congenital cardiac disease. 61
17184569 2007
805
Left ventricular noncompaction and mid-caviter narrowing associated with Ebstein's anomaly: three-dimensional transthoracic echocardiographic image. 61
17034883 2007
806
Noncompaction of the ventricular myocardium in a patient with Behçet's disease showing multiple thrombus formations in the right atrium, inferior vena cava and right iliac vein: A case report. 61
22477276 2007
807
Myopathy associated with spherocytosis and left ventricular hypertrabeculation/noncompaction. 61
17166766 2007
808
Left ventricular hypertrabeculation/noncompaction: a cardiac manifestation of myopathy? 61
17505689 2007
809
Superiority of contrast echocardiography over conventional echocardiography in diagnosing left ventricular hypertrabeculation/noncompaction. 61
17196479 2007
810
Don't miss extra-cardiac manifestations of familial left ventricular hypertrabeculation/non-compaction. 61
17027332 2007
811
Magnetic resonance imaging does not always confirm left ventricular noncompaction. 61
16934349 2007
812
Non-compaction on autopsy in Duchenne muscular dystrophy. 61
17077629 2007
813
Stroke and ventricular dysfunction in a patient with isolated left ventricular noncompaction. 61
17675779 2007
814
Myocardial noncompaction: report of three cases. 61
17479651 2007
815
Isolated left ventricular noncompaction in a patient presenting with a subacute myocardial infarction. 61
17612669 2007
816
Association of electrocardiographic abnormalities with cardiac findings and neuromuscular disorders in left ventricular hypertrabeculation/non-compaction. 61
17284898 2007
817
Cardiomyopathy and myopathy in left ventricular noncompaction. 61
17126673 2006
818
Non-indicated oral anticoagulation in left ventricular hypertrabeculation/noncompaction may jeopardize these patients. 61
17035083 2006
819
[Clinical characterizations of patients with isolated left ventricular noncompaction diagnosed by magnetic resonance imaging]. 61
17274895 2006
820
Comparison of regional systolic myocardial velocities in patients with isolated left ventricular noncompaction and patients with idiopathic dilated cardiomyopathy. 61
17098133 2006
821
Pitfalls in the diagnosis of left ventricular hypertrabeculation/non-compaction. 61
17068279 2006
822
[Isolated left ventricular noncompaction]. 61
17089249 2006
823
Left ventricular noncompaction of the ventricular myocardium: ever a challenging diagnosis. 61
17100023 2006
824
New onset heart failure in a 29-year-old: A case report of isolated left ventricular noncompaction. 61
17100036 2006
825
Echocardiography in the diagnosis and management of isolated left ventricular noncompaction: case reports and review of the literature. 61
16944490 2006
826
Live/real time three-dimensional echocardiographic demonstration of left ventricular noncompaction and thrombi. 61
16970725 2006
827
Non-compaction of the right atrium and left ventricle in Ebstein's malformation. 61
17044381 2006
828
Cardiologic and neurologic implications of left ventricular hypertrabeculation, also termed noncompaction. 61
16839437 2006
829
Evaluation of isolated left ventricular noncompaction is suboptimal by two-dimensional transthoracic echocardiography alone. 61
16893720 2006
830
Cardiac and neuromuscular implications in left ventricular hypertrabeculation/non-compaction. 61
16792553 2006
831
Epicardial ablation of ventricular tachycardia associated with isolated ventricular noncompaction. 61
16884520 2006
832
Age-dependency of cardiac and neuromuscular findings in left ventricular noncompaction. 61
16225941 2006
833
Successful heart failure therapy in mitochondrial disorder with noncompaction cardiomyopathy. 61
16502323 2006
834
Neuromuscular implications in left ventricular hypertrabeculation/noncompaction. 61
16364474 2006
835
Comments on a case of left ventricular hypertrabeculation/noncompaction. 61
16698870 2006
836
Myocardial and skeletal muscle biopsy in left ventricular hypertrabeculation/noncompaction. 61
16715198 2006
837
Autonomic dysfunction in left ventricular hypertrabeculation/noncompaction. 61
15967518 2006
838
Cutaneous sclerosis associated with left ventricular noncompaction, myopathy, polyneuropathy and pancytopenia with eosinophilia. 61
16684306 2006
839
Interstitial 1q43-q43 deletion with left ventricular noncompaction myocardium. 61
16762826 2006
840
Isolated left ventricular noncompaction: echocardiographic diagnosis. 61
16640720 2006
841
Left ventricular noncompaction, cardiac magnetic resonance imaging, and neuromuscular disorders. 61
16545660 2006
842
Images in cardiology. Hypertrophic cardiomyopathy and left ventricular hypertrabeculation: evidence for an overlapping phenotype. 61
16501196 2006
843
Paradoxical contributions of non-compacted and compacted segments to global left ventricular dysfunction in isolated left ventricular noncompaction. 61
16490448 2006
844
Preserved systolic function with isolated left ventricular noncompaction in an elderly patient. 61
15894514 2006
845
Delayed enhancement cardiac MR imaging in noncompaction of left ventricular myocardium. 61
16755837 2006
846
Additive value of contrast echocardiography for the diagnosis of noncompaction of the left ventricular myocardium. 61