MCID: LVR004
MIFTS: 30

Liver Inflammatory Pseudotumor

Categories: Gastrointestinal diseases, Liver diseases, Rare diseases

Aliases & Classifications for Liver Inflammatory Pseudotumor

MalaCards integrated aliases for Liver Inflammatory Pseudotumor:

Name: Liver Inflammatory Pseudotumor 12 15
Inflammatory Pseudotumor of the Liver 12 58
Liver Inflammatory Myofibroblastic Tumor 70

Characteristics:

Orphanet epidemiological data:

58
inflammatory pseudotumor of the liver
Inheritance: Not applicable; Age of onset: All ages;

Classifications:

Orphanet: 58  
Rare hepatic diseases


External Ids:

Disease Ontology 12 DOID:918
NCIt 50 C5858
SNOMED-CT 67 717329009
ICD10 via Orphanet 33 K75.8
Orphanet 58 ORPHA90003
UMLS 70 C1333967

Summaries for Liver Inflammatory Pseudotumor

MalaCards based summary : Liver Inflammatory Pseudotumor, also known as inflammatory pseudotumor of the liver, is related to hepatic angiomyolipoma and follicular dendritic cell sarcoma, and has symptoms including fever and pain. An important gene associated with Liver Inflammatory Pseudotumor is AFP (Alpha Fetoprotein). Affiliated tissues include liver, colon and thyroid, and related phenotypes are diabetes mellitus and vomiting

Related Diseases for Liver Inflammatory Pseudotumor

Diseases related to Liver Inflammatory Pseudotumor via text searches within MalaCards or GeneCards Suite gene sharing:

(show top 50) (show all 194)
# Related Disease Score Top Affiliating Genes
1 hepatic angiomyolipoma 30.3 CD34 AFP
2 follicular dendritic cell sarcoma 30.0 CR2 CD34
3 acute cholangitis 29.9 CRP CEACAM5
4 microinvasive gastric cancer 29.9 CEACAM5 AFP
5 choledocholithiasis 29.9 CRP CEACAM5
6 liver cirrhosis 29.9 CRP CD34 AFP
7 gallbladder cancer 29.7 CRP CEACAM5 AFP
8 lymphoplasmacytic inflammatory pseudotumor of the liver 11.6
9 fibrohistiocytic inflammatory pseudotumor of the liver 11.4
10 cholangiocarcinoma 10.5
11 intrahepatic cholangiocarcinoma 10.5
12 cholangitis 10.5
13 obstructive jaundice 10.3
14 sclerosing cholangitis 10.3
15 portal hypertension 10.3
16 crohn's disease 10.3
17 glossopharyngeal nerve paralysis 10.2 CRP AFP
18 pineal region meningioma 10.2 CRP AFP
19 hematocele of tunica vaginalis testis 10.2 CRP AFP
20 tuberculous epididymitis 10.2 CRP AFP
21 infected hydrocele 10.2 CRP AFP
22 epididymo-orchitis 10.2 CRP AFP
23 basidiobolomycosis 10.2 CRP AFP
24 gallbladder disease 1 10.2
25 gastrointestinal stromal tumor 10.2
26 severe congenital neutropenia 10.2
27 rectum cancer 10.2
28 papillary adenocarcinoma 10.2
29 chronic cholangitis 10.2
30 ovarian solid teratoma 10.2 CD34 AFP
31 papillary adenofibroma 10.2 CD34 AFP
32 gallbladder leiomyosarcoma 10.2 CD34 AFP
33 granulomatous hepatitis 10.2 CRP CR2
34 anal fistula 10.2 CRP AFP
35 testicular fibroma 10.2 CD34 AFP
36 sclerosing hepatic carcinoma 10.2 CD34 AFP
37 rosai-dorfman disease 10.1 CRP CR2
38 peliosis hepatis 10.1 CD34 AFP
39 epididymis disease 10.1 CRP AFP
40 endobronchial leiomyoma 10.1 CR2 CD34
41 juvenile arthritis 10.1 CRP CR2
42 plasma protein metabolism disease 10.1 CRP AFP
43 cystic lymphangioma 10.1 CD34 AFP
44 malignant giant cell tumor of soft parts 10.1 CR2 CD34
45 capillary lymphangioma 10.1 CRP CD34
46 subungual glomus tumor 10.1 CRP CD34
47 liver benign neoplasm 10.1 CD34 AFP
48 portal vein thrombosis 10.1 CRP AFP
49 buerger disease 10.1 CRP CD34
50 adult xanthogranuloma 10.1 CR2 CD34

Graphical network of the top 20 diseases related to Liver Inflammatory Pseudotumor:



Diseases related to Liver Inflammatory Pseudotumor

Symptoms & Phenotypes for Liver Inflammatory Pseudotumor

Human phenotypes related to Liver Inflammatory Pseudotumor:

58 (show all 17)
# Description HPO Frequency Orphanet Frequency HPO Source Accession
1 diabetes mellitus 58 Occasional (29-5%)
2 vomiting 58 Occasional (29-5%)
3 fever 58 Frequent (79-30%)
4 cirrhosis 58 Occasional (29-5%)
5 abdominal pain 58 Frequent (79-30%)
6 weight loss 58 Occasional (29-5%)
7 elevated alpha-fetoprotein 58 Excluded (0%)
8 biliary tract abnormality 58 Occasional (29-5%)
9 neoplasm of the liver 58 Obligate (100%)
10 abdominal distention 58 Occasional (29-5%)
11 autoimmune antibody positivity 58 Frequent (79-30%)
12 nausea 58 Occasional (29-5%)
13 asthenia 58 Occasional (29-5%)
14 elevated serum alanine aminotransferase 58 Very rare (<4-1%)
15 elevated serum aspartate aminotransferase 58 Very rare (<4-1%)
16 abnormal liver sonography 58 Obligate (100%)
17 increased hepatitis b virus antibody level 58 Occasional (29-5%)

UMLS symptoms related to Liver Inflammatory Pseudotumor:


fever; pain

Drugs & Therapeutics for Liver Inflammatory Pseudotumor

Search Clinical Trials , NIH Clinical Center for Liver Inflammatory Pseudotumor

Genetic Tests for Liver Inflammatory Pseudotumor

Anatomical Context for Liver Inflammatory Pseudotumor

MalaCards organs/tissues related to Liver Inflammatory Pseudotumor:

40
Liver, Colon, Thyroid, Ovary, Spleen, Bone Marrow, Bone

Publications for Liver Inflammatory Pseudotumor

Articles related to Liver Inflammatory Pseudotumor:

(show top 50) (show all 187)
# Title Authors PMID Year
1
Clinicopathological features and post-resection outcomes of inflammatory pseudotumor of the liver. 61
33649252 2021
2
Liver inflammatory pseudotumor in children: A case report. 61
33612422 2021
3
The dynamic enhanced characterization with low mechanical index gray-scale harmonic imaging inflammatory pseudotumor of liver compared with hepatic VX2 tumor and normal liver. 61
32886457 2020
4
Inflammatory pseudotumor of the liver. 61
32843217 2020
5
Inflammatory Pseudotumor of the Liver: Clinical Case. 61
31328151 2019
6
Inflammatory Pseudotumor of the Liver Presented in a Patient with Cholelithiasis. 61
30410837 2018
7
[A Case of an IgG4-Related Inflammatory Pseudotumor of the Liver Showing Enlargement That Was Difficult to Differentiate from Hepatic Cancer]. 61
29394821 2017
8
A Diagnosis of Inflammatory Pseudotumor of the Liver by Contrast Enhaced Ultrasound and Fine-Needle Biopsy: A Case Report. 61
30755918 2017
9
Two pseudotumor cases mimicking liver malignancy. 61
28944337 2017
10
Inflammatory pseudotumor of the liver. 61
27476013 2016
11
Paraneoplastic arthritis as first symptom of a liver inflammatory pseudotumor-like follicular dendritic cell sarcoma. 61
27125361 2016
12
[Lymphoplasmacytic inflammatory pseudotumor of the liver]. 61
27599958 2016
13
[Inflammatory pseudotumor of the liver: A propos of a case]. 61
26249155 2016
14
Inflammatory pseudotumor of the liver occurring during the course of hepatitis C virus-related hepatocellular carcinoma treatment: A case report. 61
26826935 2016
15
Inflammatory pseudotumor of the liver: A case report and literature review. 61
26361568 2015
16
Inflammatory Pseudotumor of the Liver with Escherichia coli in the Sputum. 61
26347780 2015
17
[An inflammatory pseudotumor of the liver mimicking a metastatic lesion of gallbladder cancer - a case report]. 61
25731452 2014
18
An unusual association of inflammatory pseudotumor of the liver and dorsal pancreatic agenesis presenting as reversible portal hypertension: a case report. 61
25584257 2014
19
Inflammatory pseudotumor of the liver diagnosed as metastatic liver tumor in a patient with a gastrointestinal stromal tumor of the rectum: report of a case. 61
24886578 2014
20
Inflammatory pseudotumor of the liver: a rare case of recurrence following surgical resection. 61
24967025 2014
21
Epstein-Barr virus positive inflammatory pseudotumor of the liver: report of a challenging case and review of the literature. 61
25361938 2014
22
Clinical features, image findings, and prognosis of inflammatory pseudotumor of the liver: a multicenter experience of 45 cases. 61
24516702 2014
23
Peripheral inflammatory pseudotumor of the liver and extensive thrombosis of the portal venous system in a child. 61
23455309 2013
24
Budd-Chiari syndrome secondary to inflammatory pseudotumor of the liver: Report of a case with a 10-year follow-up. 61
24090020 2013
25
Hepatic inflammatory pseudotumor mimicking hepatocellular carcinoma. 61
23683265 2013
26
Recurring multicystic inflammatory pseudotumor of the liver: a case report. 61
23219424 2013
27
[Inflammatory pseudotumor of the liver: a case of recurrence after resection]. 61
23650835 2013
28
Necrotic hepatocellular carcinoma occurring within an inflammatory pseudotumor-like nodule. 61
23448763 2013
29
[An inflammatory pseudotumor of the liver]. 61
23406639 2013
30
A Case of Inflammatory Pseudotumor of the Liver Mimicking Hepatocellular Carcinoma on EOB-MRI and PET. 61
23781250 2013
31
[A case of pancreaticoduodenectomy after the placement of an expandable metallic stent]. 61
23268001 2012
32
Inflammatory pseudotumor of the liver: a rare but distinct tumor-like lesion. 61
23483865 2012
33
Ghost tumor: an inflammatory pseudotumor of the liver. 61
23483864 2012
34
Precise recognition of liver inflammatory pseudotumor may prevent an unnecessary surgery. 61
22783471 2012
35
[Case report: a case of IgG4-associated autoimmune pancreatitis accompanying liver inflammatory pseudotumor]. 61
22523819 2012
36
Inflammatory pseudotumor of the liver and spleen diagnosed by percutaneous needle biopsy. 61
22228976 2012
37
Inflammatory pseudotumor of the liver in association with spilled gallstones 3 years after laparoscopic cholecystectomy: report of a case. 61
22776305 2011
38
Inflammatory pseudotumor of the liver and spleen. 61
26189526 2011
39
Inflammatory pseudotumor of the liver: a case report and review of the literature. 61
21600001 2011
40
Inflammatory pseudotumor of the liver complicated by lung necrosis and pleural empyema: a case report. 61
22606581 2011
41
Clinical clues to suspicion of IgG4-associated sclerosing cholangitis disguised as primary sclerosing cholangitis or hilar cholangiocarcinoma. 61
21091993 2010
42
Inflammatory pseudotumor of the liver diagnosed by needle biopsy: report of three cases (one with neuroendocrine tumor of the rectum and lung). 61
20931439 2010
43
Anaplastic lymphoma kinase (ALK) positive inflammatory pseudotumor of the liver: conservative treatment and long-term follow-up. 61
20178077 2010
44
Inflammatory pseudotumor of the liver associated with Crohn's disease. 61
21172292 2009
45
Inflammatory pseudotumor of the liver: two case reports and a review of the literature. 61
19332915 2009
46
Inflammatory pseudotumor of the liver: case report and review of literature. 61
21318970 2008
47
Inflammatory pseudotumor of the liver: report of eight cases, including three unusual cases, and a literature review. 61
18031372 2007
48
Inflammatory pseudotumor of the liver: an unlikely cause of multiple hepatic lesions. 61
18210937 2007
49
Inflammatory pseudotumor of the liver successfully treated with nonsteroidal anti-inflammatory drugs: a challenge diagnosis for one not so rare entity. 61
18049174 2007
50
Inflammatory pseudotumor of the liver associated with rheumatoid arthritis. 61
17665472 2007

Variations for Liver Inflammatory Pseudotumor

Expression for Liver Inflammatory Pseudotumor

Search GEO for disease gene expression data for Liver Inflammatory Pseudotumor.

Pathways for Liver Inflammatory Pseudotumor

GO Terms for Liver Inflammatory Pseudotumor

Biological processes related to Liver Inflammatory Pseudotumor according to GeneCards Suite gene sharing:

# Name GO ID Score Top Affiliating Genes
1 response to ischemia GO:0002931 8.62 UCHL1 SLC26A5

Sources for Liver Inflammatory Pseudotumor

3 CDC
7 CNVD
9 Cosmic
10 dbSNP
11 DGIdb
17 EFO
18 ExPASy
19 FMA
20 GARD
28 GO
29 GTR
30 HMDB
31 HPO
32 ICD10
33 ICD10 via Orphanet
34 ICD9CM
35 IUPHAR
36 KEGG
37 LifeMap
39 LOVD
41 MedGen
44 MeSH
45 MESH via Orphanet
46 MGI
49 NCI
50 NCIt
51 NDF-RT
53 NINDS
54 Novoseek
56 OMIM via Orphanet
57 OMIM® (Updated 20-May-2021)
61 PubMed
63 QIAGEN
68 SNOMED-CT via HPO
69 Tocris
70 UMLS
71 UMLS via Orphanet
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