MCID: MLG141
MIFTS: 36

Malignant Atrophic Papulosis

Categories: Blood diseases, Bone diseases, Cancer diseases, Cardiovascular diseases, Rare diseases, Skin diseases
Data Licensing
For inquiries, contact:

Aliases & Classifications for Malignant Atrophic Papulosis

MalaCards integrated aliases for Malignant Atrophic Papulosis:

Name: Malignant Atrophic Papulosis 57 19 58 71 75
Degos Disease 57 19 58 75 53
Papulosis Atrophican Maligna 19 58
Kohlmeier-Degos Disease 19 58
Köhlmeier-Degos-Delort-Tricort Syndrome 19
Kohlmeier-Degos-Delort-Tricort Syndrome 58
Degos's Malignant Atrophic Papulosis 19
Papulosis, Malignant Atrophic 57
Atrophic Papulosis, Malignant 19
Köhlmeier-Degos Disease 19

Characteristics:


Inheritance:

Autosomal dominant 58 57

Prevelance:

<1/1000000 (Worldwide) 58

Age Of Onset:

Adult 58

OMIM®:

57 (Updated 08-Dec-2022)
Miscellaneous:
male-to-female ratio 3 to 1
usually occurs in young adults


Classifications:

Orphanet: 58  
Rare systemic and rhumatological diseases
Rare skin diseases


Summaries for Malignant Atrophic Papulosis

GARD: 19 Degos disease is a rare blood vessel disorder. This slows or stops the flow of blood through the affected vessels. Severity of symptoms depends on the extent and location of the affected blood vessels. Some individuals with Degos disease have isolated skin involvement and develop porcelain-white macules on their skin. Other individuals have more wide spread disease. The cause of this condition is currently unknown.

MalaCards based summary: Malignant Atrophic Papulosis, also known as degos disease, is related to dowling-degos disease and dowling-degos disease 1. An important gene associated with Malignant Atrophic Papulosis is APOH (Apolipoprotein H). Affiliated tissues include skin, bone and eye, and related phenotypes are telangiectasia of the skin and papule

Orphanet: 58 Malignant atrophic papulosis (MAP) is a rare, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim. Systemic lesions may affect the gastrointestinal tract and the central nervous system (CNS) and are potentially lethal.

Wikipedia: 75 Degos disease, also known as Köhlmeier-Degos disease or malignant atrophic papulosis, is an extremely... more...

More information from OMIM: 602248

Related Diseases for Malignant Atrophic Papulosis

Diseases related to Malignant Atrophic Papulosis via text searches within MalaCards or GeneCards Suite gene sharing:

(showing 157, show less)
# Related Disease Score Top Affiliating Genes
1 dowling-degos disease 11.9
2 dowling-degos disease 1 11.6
3 dowling-degos disease 2 11.6
4 dowling-degos disease 4 11.6
5 acne inversa, familial, 2, with or without dowling-degos disease 11.6
6 erythrokeratoderma ''en cocardes'' 11.5
7 dowling-degos disease 3 11.2
8 hidradenitis suppurativa 10.6
9 hidradenitis 10.6
10 skin disease 10.6
11 contractures, pterygia, and spondylocarpotarsal fusion syndrome 1a 10.6
12 peritonitis 10.5
13 reticulate acropigmentation of kitamura 10.5
14 lupus erythematosus 10.4
15 systemic lupus erythematosus 10.4
16 systemic scleroderma 10.4
17 vasculitis 10.4
18 acne 10.3
19 scleroderma, familial progressive 10.3
20 systemic lupus erythematosus 1 10.3
21 ptosis 10.3
22 intestinal perforation 10.3
23 connective tissue disease 10.3
24 rare genetic skin disease 10.2
25 kearns-sayre syndrome 10.2
26 vascular disease 10.2
27 purpura 10.2
28 polyradiculopathy 10.2
29 thrombotic microangiopathy 10.2
30 acanthosis nigricans 10.2
31 constrictive pericarditis 10.2
32 keratosis 10.2
33 epidermoid cysts 10.1
34 psoriasis 1 10.1
35 keratosis, seborrheic 10.1
36 psoriasis 2 10.1
37 psoriasis 7 10.1
38 psoriasis 11 10.1
39 psoriasis 13 10.1
40 dyschromatosis universalis hereditaria 10.1
41 psoriasis 10.1
42 autoimmune disease 10.1
43 sarcoidosis 1 10.1
44 thrombocytopenic purpura, autoimmune 10.1
45 3-methylglutaconic aciduria, type iii 10.1
46 stroke, ischemic 10.1
47 muscular dystrophy, congenital merosin-deficient, 1a 10.1
48 sarcoidosis 2 10.1
49 hemorrhage, intracerebral 10.1
50 pulmonary hypertension 10.1
51 exanthem 10.1
52 aphasia 10.1
53 colitis 10.1
54 ischemic colitis 10.1
55 dermatomyositis 10.1
56 meningoencephalitis 10.1
57 thrombotic thrombocytopenic purpura 10.1
58 respiratory failure 10.1
59 nephrotic syndrome 10.1
60 gastroparesis 10.1
61 papilledema 10.1
62 panniculitis 10.1
63 thrombocytopenia due to platelet alloimmunization 10.1
64 pericarditis 10.1
65 transient cerebral ischemia 10.1
66 retinal vascular disease 10.1
67 myelitis 10.1
68 central nervous system disease 10.1
69 gastritis 10.1
70 myopathy 10.1
71 radiculopathy 10.1
72 hemolytic anemia 10.1
73 gastrointestinal system disease 10.1
74 ileus 10.1
75 nervous system disease 10.1
76 rare systemic disease 10.1
77 idiopathic nephrotic syndrome 10.1
78 lupus erythematosus panniculitis 10.1
79 darier-white disease 10.0
80 dilution, pigmentary 10.0
81 dyschromatosis symmetrica hereditaria 10.0
82 ichthyosis vulgaris 10.0
83 lichen sclerosus et atrophicus 10.0
84 vasculitis, lymphocytic, nodular 10.0
85 toe syndactyly, telecanthus, and anogenital and renal malformations 10.0
86 paroxysmal nocturnal hemoglobinuria 10.0
87 ichthyosis 10.0
88 melanoma 10.0
89 acute kidney failure 10.0
90 polyradiculoneuropathy 10.0
91 kidney disease 10.0
92 hemoglobinuria 10.0
93 paraplegia 10.0
94 lichen planus 10.0
95 paresthesia 10.0
96 abducens palsy 9.9
97 behcet syndrome 9.9
98 blepharophimosis, ptosis, and epicanthus inversus 9.9
99 epicanthus 9.9
100 epidermolysis bullosa simplex 1a, generalized severe 9.9
101 epidermolysis bullosa simplex 2f, with mottled pigmentation 9.9
102 renal cell carcinoma, nonpapillary 9.9
103 lentigines 9.9
104 muir-torre syndrome 9.9
105 pemphigus vulgaris, familial 9.9
106 pilonidal sinus 9.9
107 immune deficiency disease 9.9
108 rhabdomyosarcoma 2 9.9
109 ataxia with vitamin e deficiency 9.9
110 spastic paraplegia, ataxia, and mental retardation 9.9
111 neutrophilic dermatosis, acute febrile 9.9
112 nevoid hypermelanosis, linear and whorled 9.9
113 dyschromatosis universalis hereditaria 3 9.9
114 deficiency anemia 9.9
115 cutaneous lupus erythematosus 9.9
116 erythema multiforme 9.9
117 fibroma 9.9
118 epidermolysis bullosa simplex localized type 9.9
119 transverse myelitis 9.9
120 erythema nodosum 9.9
121 blepharophimosis 9.9
122 gastric ulcer 9.9
123 pericardial effusion 9.9
124 neurogenic bladder 9.9
125 bell's palsy 9.9
126 pseudobulbar palsy 9.9
127 quadriplegia 9.9
128 facial paralysis 9.9
129 toxic shock syndrome 9.9
130 childhood type dermatomyositis 9.9
131 encephalomalacia 9.9
132 pharyngitis 9.9
133 protein s deficiency 9.9
134 cryoglobulinemia 9.9
135 antiphospholipid syndrome 9.9
136 keratoacanthoma 9.9
137 spinal cord disease 9.9
138 pyoderma 9.9
139 coronary stenosis 9.9
140 collecting duct carcinoma 9.9
141 epidermolysis bullosa simplex 9.9
142 acquired immunodeficiency syndrome 9.9
143 anal canal squamous cell carcinoma 9.9
144 cataract 9.9
145 herpes zoster 9.9
146 pyoderma gangrenosum 9.9
147 crohn's disease 9.9
148 pemphigus 9.9
149 hypersensitivity vasculitis 9.9
150 anca-associated vasculitis 9.9
151 catastrophic antiphospholipid syndrome 9.9
152 cryopyrin-associated periodic syndrome 9.9
153 lichen planus pigmentosus 9.9
154 lupus erythematosus tumidus 9.9
155 rare vascular disease 9.9
156 discoid lupus erythematosus 9.9
157 pigmentation anomaly of the skin 9.9

Graphical network of the top 20 diseases related to Malignant Atrophic Papulosis:



Diseases related to Malignant Atrophic Papulosis

Symptoms & Phenotypes for Malignant Atrophic Papulosis

Human phenotypes related to Malignant Atrophic Papulosis:

58 30 (showing 37, show less)
# Description HPO Frequency Orphanet Frequency HPO Source Accession
1 telangiectasia of the skin 58 30 Hallmark (90%) Very frequent (99-80%)
HP:0100585
2 papule 58 30 Hallmark (90%) Very frequent (99-80%)
HP:0200034
3 dermal atrophy 58 30 Hallmark (90%) Very frequent (99-80%)
HP:0004334
4 nausea and vomiting 58 30 Frequent (33%) Frequent (79-30%)
HP:0002017
5 fatigue 58 30 Frequent (33%) Frequent (79-30%)
HP:0012378
6 abdominal pain 58 30 Frequent (33%) Frequent (79-30%)
HP:0002027
7 gastrointestinal hemorrhage 58 30 Frequent (33%) Frequent (79-30%)
HP:0002239
8 weight loss 58 30 Frequent (33%) Frequent (79-30%)
HP:0001824
9 gastrointestinal infarctions 58 30 Frequent (33%) Frequent (79-30%)
HP:0005244
10 muscle flaccidity 58 30 Frequent (33%) Frequent (79-30%)
HP:0010547
11 intestinal perforation 58 30 Frequent (33%) Frequent (79-30%)
HP:0031368
12 seizure 58 30 Occasional (7.5%) Occasional (29-5%)
HP:0001250
13 ptosis 58 30 Occasional (7.5%) Occasional (29-5%)
HP:0000508
14 diplopia 58 30 Occasional (7.5%) Occasional (29-5%)
HP:0000651
15 cataract 58 30 Occasional (7.5%) Occasional (29-5%)
HP:0000518
16 cranial nerve paralysis 58 30 Occasional (7.5%) Occasional (29-5%)
HP:0006824
17 myocardial infarction 58 30 Occasional (7.5%) Occasional (29-5%)
HP:0001658
18 abnormal myocardium morphology 58 30 Occasional (7.5%) Occasional (29-5%)
HP:0001637
19 vertigo 58 30 Occasional (7.5%) Occasional (29-5%)
HP:0002321
20 peripheral neuropathy 58 30 Occasional (7.5%) Occasional (29-5%)
HP:0009830
21 migraine 58 30 Occasional (7.5%) Occasional (29-5%)
HP:0002076
22 chest pain 58 30 Occasional (7.5%) Occasional (29-5%)
HP:0100749
23 arterial thrombosis 58 30 Occasional (7.5%) Occasional (29-5%)
HP:0004420
24 respiratory failure 58 30 Occasional (7.5%) Occasional (29-5%)
HP:0002878
25 pleural effusion 58 30 Occasional (7.5%) Occasional (29-5%)
HP:0002202
26 abnormal pericardium morphology 58 30 Occasional (7.5%) Occasional (29-5%)
HP:0001697
27 peritonitis 58 30 Occasional (7.5%) Occasional (29-5%)
HP:0002586
28 amaurosis fugax 58 30 Occasional (7.5%) Occasional (29-5%)
HP:0100576
29 intestinal fistula 58 30 Occasional (7.5%) Occasional (29-5%)
HP:0100819
30 pain insensitivity 58 30 Occasional (7.5%) Occasional (29-5%)
HP:0007021
31 abnormality of the optic nerve 58 30 Occasional (7.5%) Occasional (29-5%)
HP:0000587
32 ischemic stroke 58 30 Occasional (7.5%) Occasional (29-5%)
HP:0002140
33 arteritis 58 30 Occasional (7.5%) Occasional (29-5%)
HP:0012089
34 abnormality of the lower urinary tract 58 30 Occasional (7.5%) Occasional (29-5%)
HP:0010936
35 stroke 30 HP:0001297
36 abnormal conjunctiva morphology 30 HP:0000502
37 constrictive pericarditis 30 HP:0002563

Symptoms via clinical synopsis from OMIM®:

57 (Updated 08-Dec-2022)
Abdomen Gastrointestinal:
gastrointestinal infarctions
gastrointestinal bleeding

Head And Neck Eyes:
avascular patches on conjunctiva and other eye regions

Skin Nails Hair Skin Histology:
wedge-shaped necrosis from epidermis through dermis

Respiratory Lung:
pleural effusion

Skin Nails Hair Skin:
multiple asymptomatic papules with atrophic white scar-like centers surrounded by telangiectatic borders

Neurologic Central Nervous System:
cns infarctions

Clinical features from OMIM®:

602248 (Updated 08-Dec-2022)

Drugs & Therapeutics for Malignant Atrophic Papulosis

Search Clinical Trials, NIH Clinical Center for Malignant Atrophic Papulosis

Genetic Tests for Malignant Atrophic Papulosis

Anatomical Context for Malignant Atrophic Papulosis

Organs/tissues related to Malignant Atrophic Papulosis:

MalaCards : Skin, Bone, Eye, Small Intestine, Spinal Cord, Endothelial, Liver

Publications for Malignant Atrophic Papulosis

Articles related to Malignant Atrophic Papulosis:

(showing 518, show less)
# Title Authors PMID Year
1
Malignant atrophic papulosis (Degos' disease) involving three generations of a family. 62 57
9308565 1997
2
[2 families with malignant atrophic papulosis (Degos disease)]. 62 57
3279324 1988
3
Six cases of malignant atrophic papulosis (Degos' disease) occurring in one family. 62 57
6487548 1984
4
Familial malignant atrophic papulosis. 62 57
6733962 1984
5
Malignant atrophic papulosis (Degos' disease). Two cases occurring in the same family. 62 57
5359899 1969
6
Degos' disease (malignant papulosis). Report of three cases with clues to etiology. 62 57
4176652 1968
7
Malignant atrophic papulosis: endocardial involvement and positive anticardiolipin antibodies. 53 62
16684293 2006
8
Laparoscopic detection of malignant atrophic papulosis (MAP) in a Paediatric patient. 62
35857385 2022
9
Atrophic papulosis (Köhlmeier-Degos disease) revisited: a cross-sectional study on 105 patients. 62
35610757 2022
10
Inflammation and thrombo-occlusive vessel signalling in benign atrophic papulosis (Köhlmeier-Degos disease). 62
35748122 2022
11
Disseminated papular variant of Dowling-Degos disease: Histopathological features in POGLUT1 mutation. 62
36314591 2022
12
Degos disease in a child presenting with acute renal failure. 62
36443642 2022
13
Progressive cribriform and zosteriform hyperpigmentation: a histologic mimicker of Dowling-Degos disease? 62
36457684 2022
14
Interferon receptor dysfunction in a child with malignant atrophic papulosis and CNS involvement. 62
35841902 2022
15
A case report of Dowling-Degos disease caused by POFUT1 exon deletion with possible coexistent CARD14 mutation-related psoriasis. 62
35340079 2022
16
Exploring the pathophysiologic basis of constrictive pericarditis of Kohlmeier Degos disease: A case series and review of the literature. 62
35588602 2022
17
Acquired Dermal Macular Hyperpigmentation Mimicking Dowling Degos Disease: A Case Report. 62
36148207 2022
18
A Particular Bicentric Structure in Dermoscopic Demonstration of Degos Disease. 62
36159151 2022
19
Follicular Dowling-Degos Disease Camouflaged as Comedones: A Case Report and Literature Review. 62
35865417 2022
20
Diffused Degos disease treated with rivaroxaban. 62
35707869 2022
21
Gastrointestinal Kohlmeier-Degos disease: a narrative review. 62
35443671 2022
22
Degos disease complicated by constrictive pericarditis in remote phase: a case report. 62
35365165 2022
23
Dowling-Degos Disease Presenting With Associated Epidermal Inclusion Cysts: A Case Report and Review of the Literature. 62
34816802 2022
24
Evolutionary distinct roles of γ-secretase subunit nicastrin in zebrafish and humans. 62
35016821 2022
25
A fatal case of malignant atrophic papulosis in a pediatric patient. 62
34935194 2022
26
Dissecting the Roles of Innate Cells in the Skin and Intractable Skin Diseases. 62
35753764 2022
27
Neurological Involvement in Malignant Atrophic Papulosis: A Comprehensive Review of Literature. 62
35263846 2022
28
Degos disease with multiple intestinal perforations: A missed-opportunity case report and literature review. 62
36324742 2022
29
Novel deletion of the POFUT1 gene associated with multiple seborrheic keratosis Dowling-Degos disease. 62
34524711 2021
30
Degos disease with renal cell carcinoma. 62
34184287 2021
31
Classic Dowling Degos disease: a rare genodermatosis. 62
31195785 2021
32
A Case of Malignant Atrophic Papulosis With Multiple Complications. 62
34074813 2021
33
Clinico-Pathological Features in Köhlmeier-Degos Disease with Cutaneous and Neurological Involvement. 62
35359530 2021
34
Malignant atrophic papulosis (Degos disease). 62
34570365 2021
35
Follicular Dowling-Degos Disease with Hidradenitis Suppurativa: A Case Report and Review of the Literature. 62
35082614 2021
36
Dowling-Degos disease: a review. 62
33368260 2021
37
Co-occurrence of Dowling-Degos disease and pemphigus vulgaris. 62
33660255 2021
38
Clinical manifestations and treatment outcomes in degos disease: a systematic review. 62
33914972 2021
39
Middle of the breasts pigmentation in a pedigree with POFUT1-related Dowling-Degos disease, expansion of the phenotype. 62
34377138 2021
40
Exacerbation of Galli-Galli Disease Following Dialysis Treatment: A Case Report and Review of Aggravating Factors. 62
34249550 2021
41
Diseases related to Notch glycosylation. 62
33341260 2021
42
Clinical and laboratory prognosticators of atrophic papulosis (Degos disease): a systematic review. 62
33957947 2021
43
Fucosylated Proteome Profiling Identifies a Fucosylated, Non-Ribosomal, Stress-Responsive Species of Ribosomal Protein S3. 62
34070332 2021
44
Follicular Dowling Degos Disease with Lichen Planus in Two Siblings: A Rare Association. 62
34211919 2021
45
Degos-like lesions as a cutaneous manifestation of cytomegalovirus infection: A rare and serious complication in a patient with drug-induced hypersensitivity syndrome. 62
33305840 2021
46
Co-occurrence of Ichthyosis Vulgaris, Dowling-Degos Disease, and Hidradenitis Suppuritiva in Same Patient: An Association or Coincidence? 62
34188288 2021
47
Multiomics Integration in Skin Diseases with Alterations in Notch Signaling Pathway: PlatOMICs Phase 1 Deployment. 62
33546374 2021
48
Comorbid acne inversa and Dowling-Degos disease due to a single NCSTN mutation: is there enough evidence? 62
32894577 2021
49
Comorbid acne inversa and Dowling-Degos disease due to a single NCSTN mutation: is there enough evidence? Reply from the authors. 62
32895925 2021
50
Degos Disease (Malignant Atrophic Papulosis) With Granular IgM on Direct Immunofluorescence. 62
33604213 2021
51
Structure, function, and pathology of protein O-glucosyltransferases. 62
33436558 2021
52
PSENEN Mutation in Coexistent Hidradenitis Suppurativa and Dowling-Degos Disease. 62
33768038 2021
53
Follicular Dowling-Degos Disease and Blepharophimosis-Ptosis-Epicanthus Inversus Syndrome: A Chance or Significant Association. 62
33911305 2021
54
Case Report: Pediatric Malignant Atrophic Papulosis With Small Bowel Perforation and Positivity of Anticardiolipin Antibody. 62
34956979 2021
55
A novel mutation in POFUT1 gene associated with Dowling-Degos disease and hidradenitis suppurativa. 62
32767357 2021
56
Hidradenitis Suppurativa Associated with Galli-Galli Disease: Extending the Link with Dowling-Degos Disease. 62
33488918 2020
57
Scrotal Dowling-Degos disease caused by a novel frameshift variant in gamma-secretase subunit presenile enhancer gene. 62
32478413 2020
58
The deregulation of NOTCH pathway, inflammatory cytokines, and keratinization genes in two Dowling-Degos disease patients with hidradenitis suppurativa. 62
33200913 2020
59
Juvenile dermatomyositis resembling late-stage Degos disease with gastrointestinal perforations successfully treated with combination of cyclophosphamide and rituximab: case-based review. 62
31900501 2020
60
Degos disease: a case report and review of the literature. 62
33115514 2020
61
Novel nicastrin mutation in hidradenitis suppurativa-Dowling-Degos disease clinical phenotype: more than just clinical overlap? 62
32282940 2020
62
Coexistence of acne inversa with psoriasis and Dowling-Degos disease harboring impaired PSENEN-Notch signaling. 62
32852387 2020
63
Bowel perforation from malignant atrophic papulosis treated with eculizumab. 62
33456165 2020
64
[Vulvar Dowling-Degos disease]. 62
32600663 2020
65
Degos disease: A radiological-pathological correlation of the neuroradiological aspects of the disease. 62
32505971 2020
66
Dermoscopy of Follicular Dowling-Degos Disease. 62
32831370 2020
67
Dowling-Degos Disease with Follicular Involvement Associated with Hidradenitis Suppurativa: A Manifestation of Follicular Occlusion Phenomenon? 62
32831371 2020
68
Atypical Disseminated Variant of Galli-Galli Disease: A Review of the Literature. 62
31449063 2020
69
Pleiotropic Role of Notch Signaling in Human Skin Diseases. 62
32545758 2020
70
Dowling-Degos Disease with Hidradenitis Suppurativa and Inflammatory Arthritis in Two Generations. 62
32695705 2020
71
Epidermal keratin 5 expression and distribution is under dermal influence. 62
31692218 2020
72
Degos disease in three patients with a common systemic involvement. 62
30375206 2020
73
Disseminated discoid lupus erythematosus mimicking Degos disease. 62
31429927 2020
74
Enhanced cutaneous Rock2 expression as a marker of Rho Kinase pathway activation in autoimmune disease and Kohlemeier-Degos disease. 62
31778951 2020
75
Malignant Atrophic Papulosis. 62
31799991 2020
76
Early failure of eculizumab in a patient with malignant atrophic papulosis: Is it time for initial combination therapy of eculizumab and treprostinil? 62
31631389 2020
77
Mast cell activation in Dowling-Degos disease. 62
31206596 2019
78
Chronic pleuritis leading to severe pulmonary restriction: a rare complication of Degos disease. 62
31818897 2019
79
Phenotypic expansion of POFUT1 loss of function mutations in a disorder featuring segmental dyspigmentation with eczematous and folliculo-centric lesions. 62
31566882 2019
80
A familial case of Dowling-Degos disease on the vulva. 62
30666695 2019
81
Dramatic neurological debut in a case of Köhlmeier-Degos disease. 62
31183675 2019
82
A case of hidradenitis suppurativa linked to trisomy 1q. 62
31535764 2019
83
Dowling-Degos Disease - A Novel Presentation of An Uncommon Disease. 62
31544084 2019
84
The color of skin: white diseases of the skin, nails, and mucosa. 62
31896410 2019
85
Dowling-Degos Disease and Hidradenitis Suppurativa. Epidemiological and Clinical Study of 15 Patients and Review of the Literature. 62
31120546 2019
86
Dowling-Degos Disease Presenting Primarily with Comedones and Atrophic Scarring. 62
31700856 2019
87
Full ablative versus fractional ablative laser therapy for Dowling-Degos disease. 62
30281812 2019
88
Altered Notch Signaling in Dowling-Degos Disease: Additional Mutations in POGLUT1 and Further Insights into Disease Pathogenesis. 62
30414910 2019
89
Dyschromatosis symmetrica hereditaria and reticulate acropigmentation of Kitamura: An update. 62
30692041 2019
90
Hidradenitis suppurativa of the nape: Description of an atypical phenotype related to severe early-onset disease in men. 62
30561771 2019
91
Degos-Like Lesions In Association With Connective Tissue Diseases: A Report Of Three Cases And Literature Review. 62
31807047 2019
92
Kohlmeier-Degos disease with constrictive pericarditis and atrial fibrillation. 62
29974345 2018
93
A case of co-occurence of Dowling-Degos disease and psoriasis: association or a rarely-seen coincidence? 62
30518180 2018
94
A new nonsense mutation in the POGLUT1 gene in two sisters with Dowling-Degos disease. 62
29569780 2018
95
Atypical presentation of Dowling-Degos disease with novel and recurrent mutations in POFUT1. 62
29797344 2018
96
Dowling-Degos Disease Localized on Vulva Mimicking Condyloma Acuminata. 62
30504986 2018
97
[The benign form of malignant atrophic papulosis (Köhlmeier-Degos disease)]. 62
30264308 2018
98
Vesicular variant of Dowling-Degos disease. 62
29931677 2018
99
Malignant atrophic papulosis with motor aphasia and intestinal perforation: A case report and review of published works. 62
29516548 2018
100
Variant in human POFUT1 reduces enzymatic activity and likely causes a recessive microcephaly, global developmental delay with cardiac and vascular features. 62
29452367 2018
101
Whole exome sequencing in a multi-generation family from India reveals a genetic variation c.10C>T (p.Gln4Ter) in keratin 5 gene associated with Dowling-Degos disease. 62
29600799 2018
102
Novel POFUT1 mutation associated with hidradenitis suppurativa-Dowling-Degos disease firm up a role for Notch signalling in the pathogenesis of this disorder: reply from the authors. 62
29274076 2018
103
Novel POFUT1 mutation associated with hidradenitis suppurativa-Dowling-Degos disease firm up a role for Notch signalling in the pathogenesis of this disorder. 62
29274243 2018
104
Benign Atrophic Papulosis (Degos Disease) With Lymphocytic Vasculitis and Lichen Sclerosus-Like Features. 62
28244939 2018
105
Pediatric Malignant Atrophic Papulosis. 62
29610176 2018
106
A phenotype combining hidradenitis suppurativa with Dowling-Degos disease caused by a founder mutation in PSENEN. 62
28922471 2018
107
The evolution of cerebrovascular changes in Köhlmeier-Degos disease: An 11-year follow-up case report. 62
29239824 2018
108
Concurrent hidradenitis suppurativa and Dowling-Degos disease taken down a 'Notch'. 62
29441533 2018
109
Dowling-Degos disease with mutation in the exon 1 of the keratin 5 gene. 62
28646612 2018
110
Generalized Dowling-Degos disease with hypopigmented lesions: A diagnostic challenge. 62
29176251 2018
111
Multi-organ vaso-occlusive disease: Buerger's or Kohlmeier-Degos disease? 62
29096880 2017
112
[Mutations in presenilin in Dowling-Degos disease: Association with follicular occlusion disorder and the notch-signalling pathway]. 62
29100615 2017
113
Galli-Galli Disease Presenting as a Lentigo-like Eruption: A Further Clinical Feature in the Wide Spectrum of Reticulate Pigment Disorders. 62
30064605 2017
114
Vasculopathies, cutaneous necrosis and emergency in dermatology. 62
28845953 2017
115
Recognizing syndromic hidradenitis suppurativa: a review of the literature. 62
28696038 2017
116
Follicular Dowling-Degos Disease: A Rare Pigmentary Dermatosis. 62
29204397 2017
117
Benign atrophic papulosis (Köhlmeier-Degos disease): the wedge-shaped dermal necrosis can resolve with time. 62
28544089 2017
118
Systemic lupus erythematosus, following prodromal idiopathic thrombocytopenic purpura, presenting with skin lesions resembling malignant atrophic papulosis. 62
28691162 2017
119
PSENEN Mutation Carriers with Co-manifestation of Acne Inversa (AI) and Dowling-Degos Disease (DDD): Is AI or DDD the Subphenotype? 62
28601418 2017
120
Updated review of genetic reticulate pigmentary disorders. 62
28407215 2017
121
Degos disease, not just a scar: lethal outcome in spite of immunomodulatory therapy. 62
28370442 2017
122
Systemic lupus erythematosus with Degos disease: role of dermatoscopy in diagnosis. 62
28444743 2017
123
Congenital Degos Disease: Case Report and Dermoscopic Findings. 62
28317162 2017
124
Degos-Like Lesions Associated with Systemic Lupus Erythematosus. 62
28392651 2017
125
Mutations in γ-secretase subunit-encoding PSENEN underlie Dowling-Degos disease associated with acne inversa. 62
28287404 2017
126
Mutations in POGLUT1 in Galli-Galli/Dowling-Degos disease. 62
27479915 2017
127
Successful Management of Dowling-Degos Disease with Combination of Q-switched Nd: YAG and Fractional Carbon Dioxide Laser. 62
28529428 2017
128
A case of Degos disease in pregnancy. 62
27829877 2016
129
Novel Mutations in PSENEN Gene in Two Chinese Acne Inversa Families Manifested as Familial Multiple Comedones and Dowling-Degos Disease. 62
27900998 2016
130
Dermoscopy in General Dermatology: A Practical Overview. 62
27613297 2016
131
Pathogenicity of POFUT1 mutations in two Chinese families with Dowling-Degos disease. 62
26486618 2016
132
Degos Disease: A Murderous Menace. 62
27688455 2016
133
Structural analysis of Notch-regulating Rumi reveals basis for pathogenic mutations. 62
27428513 2016
134
A dramatic case of malignant atrophic papulosis (Köhlmeier-Degos disease) with fatal outcome. 62
27503064 2016
135
Dowling-Degos disease co-presenting with Darier disease. 62
26685052 2016
136
[Clinicopathological aspects of terra firma-forme dermatosis]. 62
27062007 2016
137
Coexistence of Reticulate Acropigmentation of Kitamura and Dowling-Degos Disease. 62
29210541 2016
138
Degos disease mimicking primary vasculitis of the CNS. 62
26894208 2016
139
Genome-wide linkage and exome sequencing analyses identify an initiation codon mutation of KRT5 in a unique Chinese family with generalized Dowling-Degos disease. 62
26440693 2016
140
Atypical cases of Dowling-Degos disease. 62
27057490 2016
141
Dowling-Degos disease with reticulate acropigmentation of Kitamura: Extended spectrum of a single entity. 62
26955585 2016
142
Dermatoscopic Features of Hyper and Hypopigmented Lesions of Dowling Degos Disease. 62
26955155 2016
143
Laparoscopy shows superiority over endoscopy for early detection of malignant atrophic papulosis gastrointestinal complications: a case report and review of literature. 62
26527039 2015
144
Dowling-Degos disease and malignant melanoma: Association or mere coincidence? 62
26515850 2015
145
Protein O-Glucosyltransferase 1 (POGLUT1) Promotes Mouse Gastrulation through Modification of the Apical Polarity Protein CRUMBS2. 62
26496195 2015
146
Opioid associated intravenous and cutaneous microvascular drug abuse (skin-popping) masquerading as Degos disease (malignant atrophic papulosis) with multiorgan involvement. 62
26437280 2015
147
Dowling-Degos disease with mutations in POFUT1 is clinicopathologically distinct from reticulate acropigmentation of Kitamura. 62
25639155 2015
148
Successful treatment of Dowling-Degos disease using intense pulsed light. 62
25495801 2015
149
Central nervous system involvement in systemic malignant atrophic papulosis (Degos disease): a case report. 62
23786159 2015
150
A case of malignant atrophic papulosis with cranial nerve and peripheral nerve impairment. 62
26312664 2015
151
A case of Degos disease: demonstration of C5b-9-mediated vascular injury. 62
24506660 2015
152
Dowling-Degos disease associated with hidradenitis suppurativa: a case report. 62
25529465 2015
153
Degos Disease Associated with Behçet's Disease. 62
25834376 2015
154
Renal involvement in Malignant Atrophic Papulosis (Degos Disease). 62
25831010 2015
155
Degos disease: report of a case and review of the literature. 62
25686287 2015
156
Pathogenicity of POFUT1 in Dowling-Degos disease: additional mutations and clinical overlap with reticulate acropigmentation of kitamura. 62
25229252 2015
157
Challenging mimickers of primary systemic vasculitis. 62
25399945 2015
158
Acquired neurocutaneous disorders. 62
26564070 2015
159
[Of hair and genes: The continuing story of Dowling-Degos disease]. 62
25530071 2015
160
Degos disease - malignant atrophic papulosis or cutaneointestinal lethal syndrome: rarity of the disease. 62
25926751 2015
161
Two cases of Degos disease with different prognosis. 62
25610362 2014
162
Dowling-Degos disease with diffuse penile pigmentation. 62
24422879 2014
163
The First Report of KRT5 Mutation Underlying Acantholytic Dowling-Degos Disease with Mottled Hypopigmentation in an Indian Family. 62
25284854 2014
164
The dermoscopic variability of Degos disease at different stages of progression. 62
25126461 2014
165
Heterozygous frameshift mutation in keratin 5 in a family with Galli-Galli disease. 62
24372084 2014
166
A case of reticulate acropigmentation of kitamura: dowling degos disease overlap with unusual clinical manifestations. 62
24891663 2014
167
Hidradenitis suppurrativa (acne inversa) as a systemic disease. 62
24767187 2014
168
Case for diagnosis. 62
24937836 2014
169
Degos disease with an intestinal perforation: a case report. 62
24527998 2014
170
Severe neurologic involvement of Degos disease in a pediatric patient. 62
23400246 2014
171
Reflectance confocal microscopy features of Degos disease. 62
23864231 2014
172
Successful treatment of neurological malignant atrophic papulosis in child by corticosteroid combined with intravenous immunoglobulin. 62
24341936 2014
173
Mutations in POGLUT1, encoding protein O-glucosyltransferase 1, cause autosomal-dominant Dowling-Degos disease. 62
24387993 2014
174
Analysis of POFUT1 gene mutation in a Chinese family with Dowling-Degos disease. 62
25157627 2014
175
Association of Dowling-Degos disease and multiple seborrheic keratosis in a "Christmas tree pattern". 62
25405133 2014
176
Malignant and benign forms of atrophic papulosis (Köhlmeier-Degos disease): systemic involvement determines the prognosis. 62
24116834 2014
177
Treatment of Dowling-Degos disease with fractional Er:YAG laser. 62
23464495 2013
178
[Dowling-Degos disease and chronic hidradenitis suppurativa]. 62
24315237 2013
179
Follicular Dowling Degos disease: a rare variant of an evolving dermatosis. 62
24177614 2013
180
The effects of Eculizumab on the pathology of malignant atrophic papulosis. 62
24279613 2013
181
Whole-exome sequencing identifies ADAM10 mutations as a cause of reticulate acropigmentation of Kitamura, a clinical entity distinct from Dowling-Degos disease. 62
23666529 2013
182
Generalized dowling-degos disease: case reports. 62
24003282 2013
183
Dowling-Degos disease and hidradenitis suppurativa: Co occurrence or association? 62
23984231 2013
184
Mutations in POFUT1, encoding protein O-fucosyltransferase 1, cause generalized Dowling-Degos disease. 62
23684010 2013
185
Diseases associated with hidranitis suppurativa: part 2 of a series on hidradenitis. 62
24011308 2013
186
Effective treatment of malignant atrophic papulosis (Köhlmeier-Degos disease) with treprostinil--early experience. 62
23557362 2013
187
Cutaneous manifestations of gastrointestinal disease: part II. 62
23317981 2013
188
Recognizable phenotypes associated with intracranial calcification. 62
23121296 2013
189
Malignant atrophic papulosis (Köhlmeier-Degos disease) - a review. 62
23316694 2013
190
Possible involvement of SDF-1/CXCL12 in the pathogenesis of Degos disease. 62
22951280 2013
191
The spectrum of reticulate pigment disorders of the skin revisited. 62
23018017 2012
192
A novel heterozygous nonsense mutation of keratin 5 in a Chinese family with Dowling-Degos disease. 62
21569119 2012
193
A case of Degos disease successfully treated with corticosteroid combined with cyclophosphamide. 62
20352224 2012
194
Galli-Galli disease is an acantholytic variant of Dowling-Degos disease: additional genetic evidence in a German family. 62
22583733 2012
195
Presentation of reticulate acropigmentation of kitamura and dowling-degos disease overlap. 62
22808308 2012
196
[Extensive Dowling-Degos disease following long term PUVA therapy]. 62
22225744 2012
197
[Galli-Galli disease. Clinical and histopathological investigation using a case series of 18 patients]. 62
21971768 2011
198
A fatal case of Degos' disease which presented with recurrent intestinal perforation. 62
22110848 2011
199
Lethal systemic degos disease with prominent cardio-pulmonary involvement. 62
22121280 2011
200
Dowling-Degos disease: classic clinical and histopathological presentation. 62
22147038 2011
201
Commentary on 'Degos disease: a C5b-9/interferon-α-mediated endotheliopathy syndrome' by Magro et al: a reconsideration of Degos disease as hematologic or endothelial genetic disease. 62
21906486 2011
202
[Malignant atrophic papulosis as an incidental finding on laparoscopy--case report]. 62
21351047 2011
203
Coexistence of reticulate acropigmentation of Kitamura and Dowling-Degos disease. 62
25386285 2011
204
Lack of recurrence of malignant atrophic papulosis of Degos in multivisceral transplant: insights into possible pathogenesis? 62
21763549 2011
205
Dowling-Degos disease involving the vulva and back: case report and review of the literature. 62
21810386 2011
206
Atypical variant of galli-galli disease (grover-like eruption with lentiginous freckling) in a liver transplant patient. 62
21252638 2011
207
Dowling-Degos disease presenting as hypopigmented macules. 62
21571208 2011
208
A case of dowling-degos disease on the vulva. 62
21747621 2011
209
Degos disease with dermatomyositis-like phenomenon: a diagnostic dilemma and a therapeutic challenge. 62
21561585 2011
210
Malignant atrophic papulosis: a case report with severe visual and neurological impairment. 62
21133995 2011
211
Dermoscopic description of a patient with thrombocythemia and factor V Leiden mutation-associated Degos' disease. 62
21506980 2011
212
Unique brown star shape on dermatoscopy of generalized Dowling-Degos disease. 62
21605106 2011
213
Degos disease: a C5b-9/interferon-α-mediated endotheliopathy syndrome. 62
21411783 2011
214
Infantile neurological Degos disease. 62
20659809 2011
215
Degos disease-like presentation in systemic lupus erythematosus. 62
21393965 2011
216
Coexistent Dowling-Degos disease and reticulate acropigmentation of kitamura with progressive seborrheic keratosis. 62
21416772 2011
217
Post-streptococcal vasculopathy with evolution to Degos' disease. 62
21035145 2011
218
Coexistence of vulvar dowling-degos disease and seborrhoeic keratosis. 62
21941561 2011
219
Galli-galli disease: a rare acantholytic variant of dowling-degos disease. 62
21629813 2011
220
Diagnosis and treatment of cutaneous paraneoplastic disorders. 62
21054710 2010
221
Prominent Degos-like skin lesions in a patient with chronic cutaneous lupus erythematosus. 62
20673533 2010
222
Systematic mutation screening of KRT5 supports the hypothesis that Galli-Galli disease is a variant of Dowling-Degos disease. 62
20222933 2010
223
Identification of novel and known KRT5 and KRT14 mutations in 53 patients with epidermolysis bullosa simplex: correlation between genotype and phenotype. 62
20199538 2010
224
Malignant atrophic papulosis with severe gastrointestinal perforation and omental necrosis: a case report. 62
20819456 2010
225
Degos cutaneous disease with features of connective tissue disease. 62
20375824 2010
226
Case for diagnosis. Dowling-Degos disease. 62
20520945 2010
227
Surgery for small bowel perforation in an Asian population: predictors of morbidity and mortality. 62
19997984 2010
228
[Galli-Galli disease presenting as lichenoid papules in the flexures]. 62
20223160 2010
229
Dowling-Degos disease. 62
20191141 2010
230
Dowling-Degos disease: case report and review of the literature. 62
20332593 2010
231
[Malignant atrophic papulosis: report of a case]. 62
20193466 2009
232
[Köhlmeier-Degos disease (Malignant Atrophic Papulosis): a cause of recurrent multiple intestinal perforations]. 62
20187481 2009
233
Degos disease: considerations for reclassification. 62
19700015 2009
234
Köhlmeier-Degos Disease (malignant atrophic papulosis) and neurologic involvement. 62
19722051 2009
235
Degos disease: a new simulator of non-accidental injury. 62
19549203 2009
236
[Necrotic papules on the abdomen]. 62
19629413 2009
237
[Degos' disease: A case report and review of literature]. 62
19727245 2009
238
Three cases of Dowling Degos disease in two families. 62
19584468 2009
239
Degos' disease. 62
19576502 2009
240
Wegener's granulomatosis: a new entity in the growing differential diagnosis of Degos' disease. 62
19040518 2009
241
Degos' disease: a rare condition simulating rheumatic diseases. 62
19301060 2009
242
[Degos' disease as a cutaneous manifestation of systemic lupus erythematosus]. 62
19569280 2009
243
A fatal case of malignant atrophic papulosis. 62
19264586 2009
244
Malignant Atrophic Papulosis (MAP, Degos' disease). 62
19249895 2009
245
Pairing and comparing nine diseases with Degos Disease (Malignant Atrophic Papulosis): an attempt to illustrate our understanding and direct future inquiry. 62
19281715 2009
246
Dermatologic manifestations of colonic disorders. 62
19119511 2009
247
Changing a concept--controversy on the confusing spectrum of the reticulate pigmented disorders of the skin. 62
18564280 2009
248
Haber's syndrome may be a clinical entity different from Dowling-Degos disease. 62
19067693 2009
249
Clinical challenges and images in GI. Image 2: Malignant atrophic papulosis (Degos' disease) with systemic manifestations. 62
18851969 2008
250
Degos' disease with delayed involvement of the gastrointestinal tract. 62
18412807 2008
251
A case of Degos disease with pleuropericardial fibrosis, jejunal perforation, hemiparesis, and widespread cutaneous lesions. 62
18412869 2008
252
Inefficacy of intravenous immunoglobulins and infliximab in Degos' disease. 62
18575050 2008
253
Dermoscopy of Dowling-Degos disease of the vulva. 62
18347308 2008
254
Small bowel infarcts in Degos disease. 62
17435982 2008
255
Dermatological clue to diagnosis of Degos disease in a 2-year-old with obscure chronic abdominal pain. 62
18057165 2008
256
Galli-Galli disease: A case report with review of the literature. 62
18222327 2008
257
Cutaneous manifestations of antiphospholipid antibody syndrome. 62
18207066 2008
258
Diabetes mellitus and Degos disease. 62
19040149 2008
259
Lethal systemic Degos disease with prominent cardio-pulmonary involvement. 62
18176689 2008
260
Degos' disease (malignant atrophic papulosis) as a fatal cause of acute abdomen: report of a case. 62
18751957 2008
261
Identification of a keratin-associated protein with a putative role in vesicle transport. 62
17397964 2007
262
Malignant atrophic papulosis. 62
17692056 2007
263
Generalized red papules with gastrointestinal complications. Diagnosis: malignant atrophic papulosis (Degos' disease). 62
17376207 2007
264
Generalized Dowling-Degos disease. 62
17637446 2007
265
The use of intravenous immunoglobulin in cutaneous and recurrent perforating intestinal Degos disease (malignant atrophic papulosis). 62
17501950 2007
266
The expanding spectrum of Galli-Galli disease. 62
17434047 2007
267
Galli-Galli disease is an acantholytic variant of Dowling-Degos disease. 62
17300252 2007
268
A heterozygous frameshift mutation in the V1 domain of keratin 5 in a family with Dowling-Degos disease. 62
16917491 2007
269
Spotted and rippled reticulate hypermelanosis: a possible variant of Dowling-Degos disease. 62
17199603 2007
270
Benign cutaneous Degos disease in a 16-year-old girl. 62
17300643 2007
271
Dowling-Degos disease with asymmetrical axillary distribution and no KRT 5 exon 1 mutation. 62
17989904 2007
272
Atypical presentation of Dowling-Degos disease. 62
16987294 2006
273
Degos' disease: acute abdomen with skin rash. 62
16974032 2006
274
A gene locus responsible for reticulate pigmented anomaly of the flexures maps to chromosome 17p13.3. 62
16575392 2006
275
Dowling-Degos disease, hidradenitis suppurativa and arthritis in mother and daughter. 62
16681601 2006
276
Loss-of-function mutations in the keratin 5 gene lead to Dowling-Degos disease. 62
16465624 2006
277
Optic nerve and spinal cord manifestations of malignant atrophic papulosis (Degos disease). 62
16421135 2006
278
A fatal case of malignant atrophic papulosis (Degos' disease) in a man with factor V Leinden mutation and lupus anticoagulant. 62
16710585 2006
279
Painful penile ulceration in a patient with malignant atrophic papulosis. 62
16164721 2005
280
Degos disease associated with protein S deficiency. 62
16120164 2005
281
Benign cutaneous Degos disease. 62
16101866 2005
282
Degos disease with an inconspicuous clinical course. 62
15987298 2005
283
A case of systemic malignant atrophic papulosis (Köhlmeier-Degos' disease). 62
15779511 2005
284
Nervous system involvement in Degos disease. 62
15760880 2005
285
Lesions resembling malignant atrophic papulosis in a patient with progressive systemic sclerosis. 62
15773530 2005
286
Degos' disease is probably a distinct entity: a review of clinical and laboratory evidence. 62
15692499 2005
287
A study of immunohistochemical and electron microscopic changes in Dowling-Degos disease. 62
15841654 2005
288
[Systemic lupus erythematosus with atrophic blanche-like palmar lesions]. 62
16285315 2004
289
Dowling-Degos disease with dyschromatosis universalis hereditaria-like pigmentation in a family. 62
15482301 2004
290
[Benign familial Degos disease]. 62
15602389 2004
291
Hidradenitis suppurativa, Dowling-Degos and multiple epidermal cysts: a new follicular occlusion triad. 62
15550138 2004
292
Benign cutaneous Degos' disease: a case report and review of the literature. 62
15492441 2004
293
Is Degos' disease a clinical and histological end point rather than a specific disease? 62
15153891 2004
294
Degos' disease mimicking vasculitis. 62
15188339 2004
295
Inflammatory linear vasculopathy mimicking Degos' disease. 62
15214927 2004
296
Treatment of Dowling-Degos disease with Er:YAG-laser: results after 2.5 years. 62
14641349 2003
297
A case of malignant atrophic papulosis successfully treated with nicotine patches. 62
14511011 2003
298
Malignant atrophic papulosis. Report of a case with multiple ophthalmic findings. 62
14601855 2003
299
Degos' disease: a distinctive pattern of disease, chiefly of lupus erythematosus, and not a specific disease per se. 62
12876488 2003
300
[Benign course of malignant atrophic papulosis (Köhlmeier-Degos disease): lack of vessel occlusion as good prognostic sign?]. 62
16285303 2003
301
Benign cutaneous Degos' disease. 62
12653699 2003
302
Presentation of Degos syndrome as acute small-bowel perforation. 62
12511151 2003
303
Cataracts associated with systemic disorders and syndromes. 62
12441847 2002
304
Immunoglobulin A-associated lymphocytic vasculopathy: a clinicopathologic study of eight patients. 62
12453297 2002
305
Dowling-Degos disease associated with squamous cell carcinomas on the dappled pigmentation. 62
12207603 2002
306
[Malignant atrophic papulosis (Köhlmeier-Degos disease). Failure to respond to interferon alpha-2a, pentoxifylline and aspirin]. 62
12207267 2002
307
Successful treatment of Dowling-Degos disease with Er:YAG laser. 62
12174072 2002
308
Reticulate acropigmentation of Kitamura-Dowling Degos disease overlap: a case report. 62
12207773 2002
309
Malignant atrophic papulosis in an infant. 62
12000397 2002
310
Benign Degos' disease developing during pregnancy and followed for 10 years. 62
12361134 2002
311
[Degos atrophic malignant papulosis. Not always malignant!]. 62
11963222 2002
312
Malignant atrophic papulosis presenting as gastroparesis. 62
11774986 2001
313
Galli-Galli disease: an unrecognized entity or an acantholytic variant of Dowling-Degos disease? 62
11606930 2001
314
[Malignant atrophic papulosis (Köhlmeier-Degos): diagnosis, therapy and course]. 62
11544947 2001
315
Dowling-Degos disease--a heat aggravated variant. 62
11488720 2001
316
[Reticular pigmented anomaly of the flexures. Dowling-Degos disease of the intertrigo type in association with acne inversa]. 62
11475647 2001
317
Dowling-Degos disease affecting the vulva. 62
11501660 2001
318
Benign cutaneous Degos' disease: a case report with emphasis on histopathology as papules chronologically evolve. 62
11285406 2001
319
Malignant atrophic papulosis (Degos' disease): clinicopathological correlations. 62
11451321 2001
320
Evolution of Dowling Degos disease. 62
11211801 2000
321
Penile ulceration in fatal malignant atrophic papulosis (Degos' disease). 62
11122044 2000
322
A case of Dowling-Degos disease suggesting an evolutional sequence. 62
11052235 2000
323
Degos' disease with constrictive pericarditis: a case report. 62
10875739 2000
324
Posterior subcapsular cataract in Degos disease. 62
10926996 2000
325
Degos' disease. 62
10849127 2000
326
Degos disease in a 24-year-old Jordanian male. 62
11370334 2000
327
Degos' disease: a case with cutaneous lesions only: absence of paramyxovirus by PCR. 62
11096208 2000
328
Benign familial Degos disease worsening during immunosuppression. 62
10583060 1999
329
Panniculitis mimicking lupus erythematosus profundus: a new histopathologic finding in malignant atrophic papulosis (Degos disease). 62
10446779 1999
330
Acute abdominal pain as a leading symptom for Degos' disease (malignant atrophic papulosis). 62
10201491 1999
331
Dowling-Degos disease (reticulate pigmented anomaly of the flexures): a clinical and histopathologic study of 6 cases. 62
10071319 1999
332
Effectiveness of topical adapalene in Dowling-Degos disease. 62
10325472 1999
333
[An autopsy case of Degos' disease with ascending thoracic myelopathy]. 62
10349347 1998
334
Benign cutaneous Degos' disease. 62
9892920 1998
335
Degos disease in a patient with acquired immunodeficiency syndrome. 62
9591802 1998
336
Malignant atrophic papulosis. 62
20921728 1998
337
Multiple pink papules with white, depressed centers. Malignant atrophic papulosis (Degos disease). 62
9487219 1998
338
Overlap of reticulate acropigmentation of Kitamura, acropigmentation of Dohi and Dowling-Degos disease in four generations. 62
9621148 1998
339
Hidradenitis suppurativa, Dowling Degos disease and perianal squamous cell carcinoma. 62
9431718 1997
340
Köhlmeier-Degos's disease with primary intestinal manifestation. 62
9361182 1997
341
Degos' disease associated with rheumatoid arthritis. 62
9267113 1997
342
Degos' disease. 62
9222218 1997
343
Haber's syndrome. 62
9159964 1997
344
Reticulate hyperpigmentation. 62
9125768 1997
345
Lesions resembling malignant atrophic papulosis in a patient with dermatomyositis. 62
9039209 1997
346
Dowling Degos disease in association with multiple seborrhoeic warts. 62
9330052 1997
347
[Degos disease]. 62
9686066 1997
348
Malignant atrophic papulosis. 62
9267754 1997
349
Co-existence of leukoderma with features of Dowling-Degos disease: reticulate acropigmentation of Kitamura spectrum in five unrelated patients. 62
9529553 1997
350
Degos' disease: radiological and immunological aspects. 62
8947289 1996
351
Small bowel fistulae in Degos' disease: a case report and literature review. 62
8855750 1996
352
Dowling-Degos disease associated with hidradenitis suppurativa. 62
8959907 1996
353
Skin lesion with a fatal neurologic outcome (Degos' disease) 62
8618659 1996
354
Dowling-degos disease. 62
20947961 1996
355
Malignant atrophic papulosis (Degos' disease) with extensive cardiopulmonary involvement. 62
8838127 1996
356
Absence of antiphospholipid and anti-endothelial cell antibodies in malignant atrophic papulosis: a study of 15 cases. 62
7593788 1995
357
Cutaneous vasculitis with lesions mimicking degos' disease and revealing Crohn's disease. 62
8615069 1995
358
Degos syndrome: malignant atrophic papulosis. 62
7640203 1995
359
Dowling-Degos disease associated with Kitamura's reticulate acropigmentation. 62
7889671 1994
360
[Malignant atrophic papulosis]. 62
7956759 1994
361
Spectrum of reticulate flexural and acral pigmentary disorders in northern India. 62
7962960 1994
362
[Report of a case of malignant atrophic papulosis or Degos disease]. 62
8060787 1994
363
[Abnormal fibrinolysis in Degos disease. A study of 3 cases]. 62
7755309 1994
364
Reticulate acropigmentation of Kitamura: two case reports. 62
8225713 1993
365
Malignant atrophic papulosis. A report of two cases with altered fibrinolysis and platelet function. 62
8252767 1993
366
Degos disease and spastic paraplegia. 62
8403473 1993
367
Antiphospholipid syndrome. 62
8423386 1993
368
[Dowling-Degos disease and Verneuil disease]. 62
8161103 1993
369
Dowling-Degos' disease mimicking chloracne. 62
1387658 1992
370
[Dowling-Degos disease with exclusively genital manifestations]. 62
1628971 1992
371
Malignant atrophic papulosis (Degos' syndrome). 62
1559751 1992
372
Peristomal atrophic papules. Degos' disease (malignant atrophic papulosis). 62
1739309 1992
373
[An autopsy case of Degos disease with neurological symptoms--neuropathological observations and increased platelet aggregation]. 62
1628433 1992
374
Antiphospholipid syndrome and cutaneous vasoocclusive disorders. 62
1931563 1991
375
Dowling-Degos disease and Kitamura's reticulate acropigmentation: support for the concept of a single disease. 62
1911300 1991
376
Endoscopic and histopathologic features of Degos' disease. 62
1915142 1991
377
Dowling-Degos disease, hidradenitis suppurativa, and multiple keratoacanthomas. A disorder that may be caused by a single underlying defect in pilosebaceous epithelial proliferation. 62
2050858 1991
378
Kohlmeier-Degos disease: a multisystem vasculopathy with progressive cerebral infarction. 62
2036078 1991
379
Reticulate pigmented anomaly of the flexures of Dowling Degos disease. 62
1781755 1991
380
Lupus anticoagulant and the skin. A longterm follow-up study of SLE patients with special reference to histopathological findings. 62
1684471 1991
381
Reticulate nonmelanocytic hyperpigmentation anomaly. A probable variant of Dowling-Degos disease. 62
1993563 1991
382
[Papulosis atrophicans maligna--Degos disease]. 62
2290792 1990
383
[Histopathology of malignant atrophic papulosis (Köhlmeier-Degos disease)]. 62
2263564 1990
384
Reticulate pigmented anomaly of the flexures (Dowling-Degos disease): a case report associated with hidradenitis suppurativa and squamous cell carcinoma. 62
2350982 1990
385
An atypical paediatric case of malignant atrophic papulosis (Köhlmeier-Degos disease). 62
2347339 1990
386
[Dowling-Degos disease]. 62
2214946 1990
387
[Malignant atrophic papulosis (Degos' syndrome)]. 62
2184516 1990
388
Malignant atrophic papulosis: response to antiplatelet therapy. 62
2178991 1990
389
[Case report of papulosis atrophicans maligna (Köhlmeier-Degos-Delort-Tricot)]. 62
2633512 1989
390
[Malignant atrophic papulosis (Köhlmeier-Degos disease)]. 62
2676909 1989
391
Degos' disease: a 10-year follow-up of a patient without visceral involvement. 62
2745761 1989
392
A family with Dowling Degos disease showing features of Kitamura's reticulate acropigmentation. 62
2713264 1989
393
[Long-term survival in malignant atrophic papulosis: a case report and review of the Japanese literature]. 62
3059171 1988
394
[Dowling-Degos disease--an autosomal dominant genetic dermatosis]. 62
3188604 1988
395
[A report of an atypical case of Degos' disease with multiple perforations of the stomach and small intestine]. 62
3065608 1988
396
Haber's syndrome and Dowling-Degos disease. 62
2966131 1988
397
Malignant atrophic papulosis (Degos' disease)--diffuse involvement of brain and bowel in an African patient. 62
3342171 1988
398
[Neurocutaneous Degos disease]. 62
3044231 1988
399
[Benign forms of Degos' malignant atrophic papulosis]. 62
3071966 1988
400
Childhood Degos disease with prominent neurological symptoms: report of a clinicopathological case. 62
3125241 1988
401
Degos' disease. A rare cause of multiple intestinal perforation. 62
3448195 1987
402
[Dowling-Degos disease: unsuccessful therapeutic trial with retinoids]. 62
3679816 1987
403
The spectrum of neurologic disease associated with antiphospholipid antibodies. Lupus anticoagulants and anticardiolipin antibodies. 62
3115237 1987
404
The anticardiolipin syndrome. A new way to slice an old pie, or a new pie to slice? 62
3555350 1987
405
The pathology and pathogenesis of malignant atrophic papulosis (Degos' disease). A case study with reference to other vascular disorders. 62
3588409 1987
406
Skin lesion resembling malignant atrophic papulosis in lupus erythematosus. 62
3609417 1987
407
[A case for diagnosis: Degos' malignant atrophic papulosis]. 62
3304092 1987
408
[Dowling-Degos disease]. 62
3674671 1987
409
[Malignant atrophic papulosis (Degos' syndrome) in a suckling infant]. 62
3818332 1986
410
Malignant atrophic papulosis: absence of circulating immune complexes or vasculitis. 62
3734185 1986
411
Reticulate pigmented anomaly of the flexures associating reticulate acropigmentation: one single entity. 62
3950138 1986
412
[Malignant atrophic papulosis (Degos' disease): clinical review. Apropos of a case]. 62
3294988 1986
413
[Dowling-Degos disease (reticulate pigmentation of the flexures)]. 62
3752864 1986
414
[Degos disease: apropos of a case with a genital localization]. 62
3537143 1986
415
Familial malignant atrophic papulosis (Degos' disease)--additional evidence for heredity and a benign course. 62
3942684 1986
416
Scaly papules with atrophy. Degos' disease or malignant atrophic papulosis. 62
3942413 1986
417
Dowling Degos Disease. 62
28150635 1986
418
Fibrinolysis in Degos' disease. 62
4089805 1985
419
Clinical and histologic findings in Degos' syndrome (malignant atrophic papulosis). 62
3884281 1985
420
[Cerebral lesions in a case of Degos' disease]. 62
3833252 1985
421
Degos' disease: association with anticardiolipin antibodies and the lupus anticoagulant. 62
6432197 1984
422
[Dowling-Degos disease]. 62
6485461 1984
423
The spectrum of Dowling-Degos disease. 62
6232941 1984
424
Ophthalmic changes of Degos' disease (malignant atrophic papulosis). 62
6717915 1984
425
Acute renal failure caused by a rapidly progressive arterio-occlusive syndrome--Köhlmeier-Degos' disease? 62
6505651 1984
426
[Degos' malignant atrophic papulosis (Degos-Delort-Tricot syndrome)]. 62
6702290 1984
427
[Familial Degos' atrophic papulosis (mother-daughter)]. 62
6721361 1984
428
Childhood Köhlmeier-Degos disease with atypical skin lesions. 62
6684249 1983
429
The broad spectrum of Dowling Degos disease, including Haber's syndrome--a hereditary abnormal reactivity to stimulation, increasing with age?--Case reports and management. 62
6366012 1983
430
Myelomalacia and hypoglycorrhachia in malignant atrophic papulosis. 62
6683380 1983
431
Is Dowling-Degos disease the same disease as Kitamura's reticulate acropigmentation? 62
6860566 1983
432
Haber's syndrome or Dowling-Degos disease? 62
6847213 1983
433
Dowling-Degos disease (reticulate pigmented anomaly of the flexures) is an autosomal dominant condition. 62
6838773 1983
434
Topical conjunctival corticosteroid therapy for malignant atrophic papulosis (Kohlmeier-Degos disease). 62
6601770 1983
435
Degos disease: neurologic complications and cerebral angiography. 62
6890170 1982
436
Lymphocytes and necrosis of the cutaneous microvasculature in malignant atrophic papulosis: a refined light microscope study. 62
6754777 1982
437
[Genodermatosis in a pair of brothers: Dowling-Degos, Grover, Darier, Hailey-Hailey or Galli-Galli disease?]. 62
7107282 1982
438
Haber's syndrome or Dowling-Degos disease? 62
7065676 1982
439
[Degos' malignant atrophic papulosis]. 62
7072366 1982
440
[Malignant atrophic papulosis with insufficiency of blood fibrinolysis]. 62
7158924 1982
441
Rapidly progressing arterio-occlusive syndrome in a patient receiving long-term hemodialysis. Kohlmeier-Degos disease? 62
7271408 1981
442
[Degos' disease]. 62
7293473 1981
443
[Dowling-Degos disease with involvement of the scalp]. 62
7228673 1981
444
CNS involvement in malignant atrophic papulosis (Kohlmeier-Degos disease): vasculopathy and coagulopathy. 62
7217973 1981
445
[Degos' disease]. 62
7003964 1980
446
Malignant atrophic papulosis (Degos' syndrome): first case report from India. 62
7438535 1980
447
[Degos' disease--vascular findings in a rare endangiopathy]. 62
7442517 1980
448
[Degos malignant atrophic papulosis]. 62
7406369 1980
449
Ultrastructure of early pigmentary changes in Dowling-Degos' disease. 62
7372882 1980
450
[Degos disease (malignant atrophic papulosis)]. 62
7399897 1980
451
[Degos' malignant atrophic papulosis. Ultrastructural study of a new case]. 62
6255828 1980
452
Malignant atrophic papulosis. 62
507855 1979
453
[Malignant atrophic papulosis (Degos' syndrome)]. 62
506456 1979
454
Malignant atrophic papulosis. 62
371654 1979
455
Malignant atrophic papulosis--Degos' syndrome. 62
227201 1979
456
Malignant atrophic papulosis: treatment with aspirin and dipyridamole. 62
718220 1978
457
[Malignant atrophying papulosis (Degos' disease) (author's transl)]. 62
153724 1978
458
Reticulate pigmented anomaly of the flexures. Dowing Degos disease, a new genodermatosis. 62
677911 1978
459
Papulosis atrophicans maligna (Köhlmeier-Degos disease): a disseminated occlusive vasculopathy. 62
727717 1978
460
Calcific constrictive pericarditis in Degos' disease. 62
644373 1978
461
Intrathoracic manifestations of Degos' disease (malignant atrophic papulosis). 62
620562 1978
462
Degos' disease treated with platelet-suppressive drugs. 62
69139 1977
463
[Cerebral form of Degos's disease]. 62
897442 1977
464
[Ultrastructural study of the Dego's disease (report of a new case and literature review) (author's transl)]. 62
889231 1977
465
Intra-endothelial tubular aggregates in malignant atrophic papulosis (Degos' disease). 62
862223 1977
466
Ischemic colitis and malignant atrophic papulosis. 62
871116 1977
467
Mesenteric infarction. 62
835791 1977
468
[Malignant atrophic papulosis with diffuse peritonitis]. 62
869455 1977
469
Nontraumatic perforations of the small intestine. 62
835087 1977
470
Atrophie blanche lesions closely resembling malignant atrophic papulosis (Degos' disease) in systemic lupus erythematosus. 62
1009012 1976
471
Malignant atrophic papulosis of Degos. Report of a patient who failed to respond to fibrinolytic therapy. 62
791153 1976
472
Malignant atrophic papulosis (Degos' disease). 62
1279068 1976
473
Malignant atrophic papulosis (Kohlmeier-Degos disease) in childhood. 62
944388 1976
474
Malignant atrophic papulosis (Degros disease). A report of two cases with clinical and histological studies. 62
1259448 1976
475
Effect of fibrinolytic treatment in malignant atrophic papulosis. 62
1156791 1975
476
[Degos' malignant atrophic papulosis (observation of a case in an infant)]. 62
1163347 1975
477
Exchange autografts in malignant atrophic papulosis (Degos' disease). 62
4607565 1974
478
[Surgical aspects of Degos' disease]. 62
4547809 1974
479
Systemic lupus erythematosus resembling malignant atrophic papulosis. 62
4843199 1974
480
[Malignant atrophic papulosis]. 62
4849135 1974
481
[Malignant atrophic papulosis of Degos]. 62
4793149 1973
482
The role of dermal blood vessels in the pathogenesis of malignant atrophic papulosis (Degos' disease). A study of two cases using enzyme histochemical, fibrinolytic, electron-microscopical and immunological techniques. 62
4351422 1973
483
Systemic thrombosing vasculitis, malignant atrophic papulosis of Degos. Review of the literature. 62
4573731 1973
484
Malignant atrophic papulosis (Degos' syndrome). 62
4562171 1972
485
Degos' disease associated with a "spontaneous cure" of diabetes. 62
5153683 1971
486
Malignant atrophic papulosis (Degos' syndrome). 62
5111694 1971
487
[Degos' malignant atrophic papulosis. Outcome after 28 months' treatment with anticoagulants]. 62
5565923 1971
488
[Digestive manifestations of malignant atrophying papulosis (Degos' disease). Value of laparoscopy]. 62
5533597 1970
489
Malignant atrophic papulosis with mucin in the dermis. A clinical and pathological study, including autopsy. 62
5459756 1970
490
Progressive systemic sclerosis with malignant atrophic papulosis. 62
5350410 1969
491
A case of Degos' disease with electron microscopic findings. 62
5372076 1969
492
[Malignant atrophic papulosis (Degos). Comparison of cases known in the literature, including personal cases]. 62
5380127 1969
493
[Evolution of the ocular lesion of malignant atrophic papulosis]. 62
5400721 1969
494
[The clinical picture of Degos' malignant atrophic papulosis]. 62
4918030 1969
495
Köhlmeier-Degos' disease (malignant atrophic papulosis). Report of the first Scandinavian case. 62
5703972 1968
496
Is degos' disease of viral origin? 62
4173808 1968
497
Is Degos' disease of viral origin? 62
4172305 1968
498
[Degos disease or malignant atrophying papulosis]. 62
5742456 1968
499
Malignant atrophic papulosis. (Degos' syndrome). 62
5644104 1968
500
[Eye lesions in malignant atrophic papulosis (Degos' disease)]. 62
5738859 1968
501
Ocular pathology in malignant atrophic papulosis. Degos' disease. 62
5636016 1968
502
Malignant atrophic papulosis (Degos' syndrome). A case report. 62
4177578 1968
503
Lethal peritonitis from Degos' disease (malign and atrophic papulosis). Report of one case with a review of the literature. 62
5731290 1968
504
[Malignant atrophic papulosis with presence of anti-artery antibodies]. 62
5590514 1967
505
[Malignant atrophic papulosis (Degos). (Fatal cutaneo-intestinal syndrome. Disseminated cutaneo-intestinal thromboangiitis)]. 62
4232876 1966
506
[Malignant papulosis atrophicans (Degos' disease)]. 62
5932965 1966
507
MALIGNANT ATROPHIC PAPULOSIS (DAGOS'S SYNDROME). 62
14190878 1964
508
[DEGOS' MALIGNANT ATROPHIC PAPULOSIS]. 62
14128693 1964
509
[Degos' malignant atrophic papulosis (cutaneo-visceral syndrome)]. 62
14023375 1963
510
Degos' disease (papulosis atrophicans maligna): report of a case with degenerative disease of the central nervous system. 62
13898142 1962
511
[A little known cutaneo-visceral syndrome, malignant atrophic papulosis]. 62
13882035 1961
512
[First ocular localization of malignant atrophic papulosis]. 62
13768480 1961
513
[Malignant atrophic papulosis (Degos type)]. 62
13670639 1959
514
[Malignant atrophic papulosis of Degos with a benign course]. 62
13500861 1957
515
[Degos' malignant atrophic papulosis; anatomicoclinical aspects]. 62
13400830 1956
516
[Cutaneo-muco-intestinal syndrome; study of Degos' malignant atrophic papulosis]. 62
13296939 1956
517
Malignant atrophic papulosis: a fatal cutaneo-intestinal syndrome. 62
13190112 1954
518
[Malignant atrophic papulosis: fatal cutaneo-intestinal syndrome]. 62
13199625 1954

Variations for Malignant Atrophic Papulosis

Expression for Malignant Atrophic Papulosis

Search GEO for disease gene expression data for Malignant Atrophic Papulosis.

Pathways for Malignant Atrophic Papulosis

GO Terms for Malignant Atrophic Papulosis

Sources for Malignant Atrophic Papulosis

2 CDC
6 CNVD
8 Cosmic
9 dbSNP
10 DGIdb
16 EFO
17 ExPASy
18 FMA
19 GARD
27 GO
28 GTR
29 HMDB
30 HPO
31 ICD10
32 ICD10 via Orphanet
33 ICD11
34 ICD9CM
35 IUPHAR
36 LifeMap
38 LOVD
40 MedGen
43 MeSH
44 MESH via Orphanet
45 MGI
48 NCI
49 NCIt
50 NDF-RT
52 NINDS
53 Novoseek
55 ODiseA
56 OMIM via Orphanet
57 OMIM® (Updated 08-Dec-2022)
61 PubChem
62 PubMed
64 QIAGEN
69 SNOMED-CT via HPO
70 Tocris
71 UMLS
72 UMLS via Orphanet
Content
Loading form....