MCID: MLG051
MIFTS: 16

Malignant Glandular Tumor of Peripheral Nerve Sheath

Categories: Cancer diseases, Endocrine diseases, Neuronal diseases

Aliases & Classifications for Malignant Glandular Tumor of Peripheral Nerve Sheath

MalaCards integrated aliases for Malignant Glandular Tumor of Peripheral Nerve Sheath:

Name: Malignant Glandular Tumor of Peripheral Nerve Sheath 12 15
Glandular Malignant Peripheral Nerve Sheath Tumor 70
Glandular Mpnst 12

Classifications:



External Ids:

Disease Ontology 12 DOID:8420
NCIt 50 C6560
SNOMED-CT 67 699659007
UMLS 70 C1333821

Summaries for Malignant Glandular Tumor of Peripheral Nerve Sheath

MalaCards based summary : Malignant Glandular Tumor of Peripheral Nerve Sheath, also known as glandular malignant peripheral nerve sheath tumor, is related to synovium neoplasm and cellular congenital mesoblastic nephroma. An important gene associated with Malignant Glandular Tumor of Peripheral Nerve Sheath is SSX2 (SSX Family Member 2), and among its related pathways/superpathways is Regulation of Wnt-mediated beta catenin signaling and target gene transcription.

Related Diseases for Malignant Glandular Tumor of Peripheral Nerve Sheath

Diseases related to Malignant Glandular Tumor of Peripheral Nerve Sheath via text searches within MalaCards or GeneCards Suite gene sharing:

(show top 50) (show all 60)
# Related Disease Score Top Affiliating Genes
1 synovium neoplasm 10.1 TLE1 SSX2
2 cellular congenital mesoblastic nephroma 10.1 TLE1 SSX2
3 congenital mesoblastic nephroma 10.1 SSX2 SMARCB1
4 spindle cell synovial sarcoma 10.1 TLE1 SSX2
5 kidney sarcoma 10.1 TLE1 SSX2
6 kidney fibrosarcoma 10.1 SSX2 SMARCB1
7 biphasic synovial sarcoma 10.1 TLE1 SSX2
8 kidney hemangiopericytoma 10.0 SSX2 CALB2
9 extraosseous chondrosarcoma 10.0 SSX2 SMARCB1
10 liver fibroma 10.0 SSX2 CALB2
11 lung sarcoma 10.0 SSX2 CALB2
12 epithelioid cell synovial sarcoma 10.0 SSX2 CALB2
13 large cell carcinoma with rhabdoid phenotype 10.0 SMARCB1 CALB2
14 teratoma 10.0 SMARCB1 CALB2
15 kidney clear cell sarcoma 10.0 TLE1 SMARCB1
16 juvenile type testicular granulosa cell tumor 10.0 SMARCB1 CALB2
17 testicular granulosa cell tumor 10.0 SMARCB1 CALB2
18 heart sarcoma 9.9 SSX2 MYOG
19 ovarian small cell carcinoma 9.9 SMARCB1 CALB2
20 medulloepithelioma 9.9 SMARCB1 CALB2
21 malignant mesenchymoma 9.9 SSX2 MYOG
22 glomus tumor 9.9 TLE1 CALB2
23 adult malignant schwannoma 9.9 MYOG B3GAT1
24 kidney cortex disease 9.9 SSX2 MYOG
25 epithelioid sarcoma 9.9 SMARCB1 CALB2
26 pineal region teratoma 9.9 SMARCB1 MYOG
27 olfactory nerve neoplasm 9.8 SMARCB1 MYOG
28 cranial nerve malignant neoplasm 9.8 SMARCB1 MYOG
29 mesenchymal cell neoplasm 9.8 SSX2 MYOG
30 neurilemmoma 9.8 SMARCB1 CALB2
31 well-differentiated liposarcoma 9.8 SSX2 MYOG
32 myoblastoma 9.8 MYOG CALB2
33 cellular neurofibroma 9.8 TLE1 SMARCB1 B3GAT1
34 mesenchymal chondrosarcoma 9.8 SMARCB1 MYOG
35 lung leiomyosarcoma 9.8 MYOG CALB2
36 fallopian tube endometrioid adenocarcinoma 9.8 MYOG CALB2
37 monophasic synovial sarcoma 9.8 TLE1 SSX2 CALB2
38 heart cancer 9.8 MYOG CALB2
39 dedifferentiated liposarcoma 9.8 SSX2 MYOG
40 atypical teratoid rhabdoid tumor 9.7 TLE1 SMARCB1
41 mixed cell type cancer 9.7 MYOG CALB2
42 rhabdomyosarcoma 2 9.7 SSX2 MYOG
43 liposarcoma 9.7 MYOG CALB2
44 renal cell carcinoma, papillary, 1 9.7 SMARCB1 B3GAT1
45 sarcoma 9.7 SSX2 SMARCB1 MYOG
46 retroperitoneal sarcoma 9.7 SSX2 SMARCB1 MYOG
47 hemangiopericytoma, malignant 9.7 TLE1 SSX2 MYOG
48 spindle cell sarcoma 9.7 TLE1 SSX2 MYOG
49 skeletal muscle cancer 9.7 SSX2 SMARCB1 MYOG
50 muscle cancer 9.7 SSX2 SMARCB1 MYOG

Graphical network of the top 20 diseases related to Malignant Glandular Tumor of Peripheral Nerve Sheath:



Diseases related to Malignant Glandular Tumor of Peripheral Nerve Sheath

Symptoms & Phenotypes for Malignant Glandular Tumor of Peripheral Nerve Sheath

Drugs & Therapeutics for Malignant Glandular Tumor of Peripheral Nerve Sheath

Search Clinical Trials , NIH Clinical Center for Malignant Glandular Tumor of Peripheral Nerve Sheath

Genetic Tests for Malignant Glandular Tumor of Peripheral Nerve Sheath

Anatomical Context for Malignant Glandular Tumor of Peripheral Nerve Sheath

Publications for Malignant Glandular Tumor of Peripheral Nerve Sheath

Articles related to Malignant Glandular Tumor of Peripheral Nerve Sheath:

# Title Authors PMID Year
1
Radiation-Induced Glandular Malignant Peripheral Nerve Sheath Tumor. 61
28530162 2017
2
[Malignant peripheric nerve sheath tumor of the orbit: first description of orbital location in a patient with NF1]. 61
20186373 2010
3
Neoplasms with neural differentiation: a review. Part II: Malignant neoplasms. 61
9504678 1998

Variations for Malignant Glandular Tumor of Peripheral Nerve Sheath

Expression for Malignant Glandular Tumor of Peripheral Nerve Sheath

Search GEO for disease gene expression data for Malignant Glandular Tumor of Peripheral Nerve Sheath.

Pathways for Malignant Glandular Tumor of Peripheral Nerve Sheath

Pathways related to Malignant Glandular Tumor of Peripheral Nerve Sheath according to GeneCards Suite gene sharing:

# Super pathways Score Top Affiliating Genes
1 10.52 TLE1 MYOG

GO Terms for Malignant Glandular Tumor of Peripheral Nerve Sheath

Sources for Malignant Glandular Tumor of Peripheral Nerve Sheath

3 CDC
7 CNVD
9 Cosmic
10 dbSNP
11 DGIdb
17 EFO
18 ExPASy
19 FMA
20 GARD
28 GO
29 GTR
30 HMDB
31 HPO
32 ICD10
33 ICD10 via Orphanet
34 ICD9CM
35 IUPHAR
36 KEGG
37 LifeMap
39 LOVD
41 MedGen
44 MeSH
45 MESH via Orphanet
46 MGI
49 NCI
50 NCIt
51 NDF-RT
53 NINDS
54 Novoseek
56 OMIM via Orphanet
57 OMIM® (Updated 05-Apr-2021)
61 PubMed
63 QIAGEN
68 SNOMED-CT via HPO
69 Tocris
70 UMLS
71 UMLS via Orphanet
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