MTT
MCID: MLG041
MIFTS: 30

Malignant Triton Tumor (MTT)

Categories: Cancer diseases, Neuronal diseases, Rare diseases

Aliases & Classifications for Malignant Triton Tumor

MalaCards integrated aliases for Malignant Triton Tumor:

Name: Malignant Triton Tumor 12 59 15
Malignant Peripheral Nerve Sheath Tumor with Rhabdomyosarcomatous Differenciation 59
Malignant Peripheral Nerve Sheath Tumor with Rhabdomyoblastic Differentiation 72
Malignant Peripheral Nerve Sheath Neoplasm with Rhabdomyosarcoma 12
Mpnst with Rhabdomyosarcomatous Differentiation 59
Mpnst with Rhabdomyoblastic Differentiation 12
Mpnst with Rhabdomyosarcoma 12
Malignant Triton Tumour 12
Mtt 59

Characteristics:

Orphanet epidemiological data:

59
malignant triton tumor
Age of onset: All ages; Age of death: any age;

Classifications:

Orphanet: 59  
Rare neurological diseases


External Ids:

Disease Ontology 12 DOID:6707
NCIt 50 C4335
SNOMED-CT 68 354002
UMLS via Orphanet 73 C0334616
Orphanet 59 ORPHA252212
UMLS 72 C0334616

Summaries for Malignant Triton Tumor

MalaCards based summary : Malignant Triton Tumor, also known as malignant peripheral nerve sheath tumor with rhabdomyosarcomatous differenciation, is related to malignant peripheral nerve sheath tumor and neurofibroma. An important gene associated with Malignant Triton Tumor is MB (Myoglobin). Affiliated tissues include lung, small intestine and thyroid, and related phenotypes are cardiovascular system and homeostasis/metabolism

Wikipedia : 75 Malignant triton tumor (MTT) is a relatively rare, aggressive tumor made up of both malignant schwannoma... more...

Related Diseases for Malignant Triton Tumor

Diseases related to Malignant Triton Tumor via text searches within MalaCards or GeneCards Suite gene sharing:

(show top 50) (show all 203)
# Related Disease Score Top Affiliating Genes
1 malignant peripheral nerve sheath tumor 32.8 S100B NF1
2 neurofibroma 30.6 S100B NF1
3 neurilemmoma 30.5 S100B NF1 DES
4 spindle cell sarcoma 30.4 S100B DES
5 rhabdomyosarcoma 30.4 MYOD1 MB DES
6 histiocytoma 30.4 MYOD1 MB
7 liposarcoma 30.4 MB DES
8 adenosarcoma 30.4 MB DES
9 fibrous histiocytoma 30.3 S100B DES
10 hemangiopericytoma, malignant 30.1 S100B DES
11 gas gangrene 30.1 MYOD1 MB
12 botryoid rhabdomyosarcoma 29.8 MYOD1 MB DES
13 mesenchymoma 29.8 MYOD1 MB DES
14 malignant mesenchymoma 29.8 MYOD1 MB DES
15 embryonal rhabdomyosarcoma 29.7 MYOD1 MB DES
16 malignant fibroxanthoma 29.7 S100B MYOD1 DES
17 neurofibrosarcoma 11.4
18 neurofibromatosis, type iv, of riccardi 10.8
19 rare tumor 10.4
20 lymphocytic leukemia 10.4
21 giant cell myocarditis 10.3 MB DES
22 myofibroma 10.3 MB DES
23 neurofibromatosis, type i 10.3
24 bilateral retinoblastoma 10.3 MB DES
25 glioma 10.3
26 pituitary tumors 10.3
27 glial tumor 10.3
28 breast rhabdomyosarcoma 10.3 MYOD1 MB
29 gastric cancer 10.3
30 pleomorphic rhabdomyosarcoma 10.2 MYOD1 MB
31 infantile myofibromatosis 10.2 MB DES
32 gallbladder sarcoma 10.2 MYOD1 DES
33 adult fibrosarcoma 10.2 MYOD1 MB
34 syringocystadenoma papilliferum 10.2 S100B DES
35 ovarian cancer 10.2
36 acute leukemia 10.2
37 myxofibrosarcoma 10.2 S100B DES
38 ossifying fibromyxoid tumor 10.2 S100B DES
39 rhabdoid cancer 10.2 MYOD1 MB
40 uterine sarcoma 10.2 MB DES
41 malignant fibrous histiocytoma of bone 10.2 MYOD1 DES
42 horner's syndrome 10.2 MYOD1 DES
43 syringoma 10.2 S100B DES
44 orbit embryonal rhabdomyosarcoma 10.2 NF1 MB
45 orbit rhabdomyosarcoma 10.2 NF1 MB
46 juvenile xanthogranuloma 10.2 S100B DES
47 pleomorphic liposarcoma 10.2 S100B DES
48 colorectal cancer 10.2
49 neuroblastoma 1 10.2
50 leukemia, acute lymphoblastic 10.2

Graphical network of the top 20 diseases related to Malignant Triton Tumor:



Diseases related to Malignant Triton Tumor

Symptoms & Phenotypes for Malignant Triton Tumor

MGI Mouse Phenotypes related to Malignant Triton Tumor:

46
# Description MGI Source Accession Score Top Affiliating Genes
1 cardiovascular system MP:0005385 9.55 AGO2 DES MB MYOD1 NF1
2 homeostasis/metabolism MP:0005376 9.43 AGO2 DES MB MYOD1 NF1 S100B
3 muscle MP:0005369 8.92 DES MB MYOD1 NF1

Drugs & Therapeutics for Malignant Triton Tumor

Search Clinical Trials , NIH Clinical Center for Malignant Triton Tumor

Genetic Tests for Malignant Triton Tumor

Anatomical Context for Malignant Triton Tumor

MalaCards organs/tissues related to Malignant Triton Tumor:

41
Lung, Small Intestine, Thyroid, Kidney, Spinal Cord

Publications for Malignant Triton Tumor

Articles related to Malignant Triton Tumor:

(show top 50) (show all 114)
# Title Authors PMID Year
1
Malignant triton tumor diagnosed twelve years after radiosurgically treated vestibular schwannoma. 38
31176932 2019
2
Worsening hemoptysis in a rare intrapulmonary triton tumor mimicking lung cancer. 38
31400331 2019
3
Malignant triton tumor: Grand Round presentation of a rare aggressive case thoracolumbar spine tumor. 38
28924675 2019
4
Expert's comment concerning Grand Rounds case entitled "Malignant triton tumor: Grand Round presentation of a rare aggressive case thoracolumbar spine tumor" by S. Ghailane et al. (Eur Spine J; 2017: DOI 10.1007/s00586-017-5277-2). 38
29671111 2019
5
Teaching NeuroImages: Intracranial malignant triton tumor: An uncommon location of a rare tumor. 38
30886081 2019
6
Malignant triton tumor of the gluteal region in a patient unaffected by neurofibromatosis: A case report. 38
29110923 2018
7
Malignant triton tumor of trigeminal nerve-case report. 38
29279963 2018
8
Malignant triton tumor of the duodenum: report of a case. 38
31149515 2018
9
A rare case of intracranial malignant triton tumor arising in the middle cranial fossa: a case report and review of the literature. 38
30509044 2018
10
[A Rare Case of Abdominal Malignant Triton Tumor]. 38
29394776 2017
11
Malignant Triton Tumor (Malignant Peripheral Nerve Sheath Tumor With Rhabdomyoblastic Differentiation) Occurring in a Vascularized Free Flap Reconstruction Graft. 38
28387148 2017
12
A Case of Retroperitoneal Malignant Triton Tumor in a Nigerian Boy. 38
29089742 2017
13
Malignant Triton tumor: a rare cause of sciatic pain and foot drop. 38
28884110 2017
14
Malignant triton tumor of the lung, infiltrating the left atrium and left ventricle, with metastasis to the small intestine. 38
28515751 2017
15
Malignant Triton Tumor of the Kidney. New Location Not Previously Reported. 38
26159374 2017
16
A case of recurrent malignant triton tumor successfully treated with radiotherapy. 38
27146005 2016
17
Insidious malignant triton tumor of the chest wall with late flare-up. 38
28757738 2016
18
A rare case of recurrent malignant triton tumor in a male with NF1: Case report and mini-review. 38
26975033 2016
19
Novel PAX3-NCOA1 Fusions in Biphenotypic Sinonasal Sarcoma With Focal Rhabdomyoblastic Differentiation. 38
26371783 2016
20
Analysis of clinical features and prognosis of malignant triton tumor: A report of two cases and literature review. 38
26788168 2015
21
Primary epididymis malignant triton tumor: case report and review of the literature. 38
26392076 2015
22
Malignant Peripheral Nerve Sheath Tumor With Rhabdomyosarcomatous and Glandular Elements: Rare Epithelial Differentiation in a Triton Tumor. 38
25911565 2015
23
Unusual histological variant of malignant peripheral nerve sheath tumor with rhabdomyoblastic differentiation. 38
25879014 2015
24
Malignant triton tumor of the cervical spine: report of one case and review of the literature. 38
23597523 2015
25
Intracranial malignant triton tumor in a patient with neurofibromatosis type 1: case report and review of the literature. 38
23633163 2014
26
Malignant triton tumor of the anterior mediastinum: A case report. 38
24527089 2014
27
Low-grade malignant triton tumor of the neck: a case report and review of the literature. 38
25328740 2014
28
Malignant Triton Tumor of the Sciatic Nerve as a Secondary Malignancy after Extended Field Radiotherapy and Chemotherapy of Hodgkin's Disease. 38
24803902 2014
29
Vestibular schwannoma management: Part II. Failed radiosurgery and the role of delayed microsurgery. 38
25077309 2013
30
Optimal surgical treatment and urological outcomes in boys with pelvic and urogenital rhabdomyosarcomas and soft tissue sarcomas. 38
23989524 2013
31
A case of malignant peripheral nerve sheath tumor with rhabdomyoblastic differentiation: malignant triton tumor. 38
24474920 2013
32
Malignant triton tumor of the chest wall invading the lung. A case report and literature review. 38
24470743 2013
33
Malignant triton tumor: a rare case. 38
24426617 2013
34
Oncologic manifestations in children with neurofibromatosis type 1 in Turkey. 38
24217072 2013
35
A rare case of retroperitoneal malignant Triton tumor invading renal vein and small intestine. 38
23607247 2013
36
Intrathoracic malignant peripheral nerve sheath tumors: imaging features and implications for management. 38
24133387 2013
37
Clinico-genetic aspects of a pediatric non-neurofibromatosis type 1 malignant triton tumor with loss of chromosome X. 38
22610852 2012
38
A-Z of malignant peripheral nerve sheath tumors. 38
23108260 2012
39
Malignant triton tumor of the retroperitoneum: a case report and review of the literature. 38
22647059 2012
40
Treatment of malignant triton tumor in zygomatic region. 38
22627455 2012
41
A rare case of malignant triton tumor in the cerebellopontine angle. 38
22515616 2012
42
Low-grade malignant triton tumor in the lumbar spine: a rare variant of malignant peripheral nerve sheath tumor with rhabdomyoblastic differentiation. 38
21732991 2012
43
Long-term survival of a patient with a neurofibromatosis Type 1 associated retroperitoneal malignant triton tumor after multi-modality treatment. 38
22011741 2011
44
[A case report of malignant triton tumor in the right parapharyngeal space]. 38
21924110 2011
45
Malignant triton tumor of cervical spine with hemorrhage. 38
21414786 2011
46
Pathology quiz case 1. Diagnosis: Sinonasal malignant Triton tumor (MTT) with intracranial extension. 38
20855691 2010
47
A Rare Malignant Triton Tumor. 38
20671860 2010
48
Intracardiac malignant Triton tumor: a first presentation. 38
20172170 2010
49
Malignant Triton tumor in the retroperitoneal space associated with neurofibromatosis type 1: a case study. 38
21139906 2009
50
A Triton tumor mimicking sacrococcygeal teratoma. 38
19944207 2009

Variations for Malignant Triton Tumor

Expression for Malignant Triton Tumor

Search GEO for disease gene expression data for Malignant Triton Tumor.

Pathways for Malignant Triton Tumor

GO Terms for Malignant Triton Tumor

Biological processes related to Malignant Triton Tumor according to GeneCards Suite gene sharing:

# Name GO ID Score Top Affiliating Genes
1 skeletal muscle tissue development GO:0007519 8.62 NF1 MYOD1

Sources for Malignant Triton Tumor

3 CDC
7 CNVD
9 Cosmic
10 dbSNP
11 DGIdb
17 EFO
18 ExPASy
19 FMA
28 GO
29 GTR
30 HGMD
31 HMDB
32 HPO
33 ICD10
34 ICD10 via Orphanet
35 ICD9CM
36 IUPHAR
37 KEGG
38 LifeMap
40 LOVD
42 MedGen
44 MeSH
45 MESH via Orphanet
46 MGI
49 NCI
50 NCIt
51 NDF-RT
54 NINDS
55 Novoseek
57 OMIM
58 OMIM via Orphanet
62 PubMed
64 QIAGEN
69 SNOMED-CT via HPO
70 TGDB
71 Tocris
72 UMLS
73 UMLS via Orphanet
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