MCID: PMP008
MIFTS: 28

Pemphigus Vegetans

Categories: Skin diseases, Rare diseases

Aliases & Classifications for Pemphigus Vegetans

MalaCards integrated aliases for Pemphigus Vegetans:

Name: Pemphigus Vegetans 59 55 73

Classifications:

Orphanet: 59  
Rare skin diseases


External Ids:

Orphanet 59 ORPHA79479
UMLS via Orphanet 74 C0263316 C0406647
ICD10 via Orphanet 34 L10.1
ICD10 33 L10.1
UMLS 73 C0263316

Summaries for Pemphigus Vegetans

MalaCards based summary : Pemphigus Vegetans is related to pemphigus and paraneoplastic pemphigus. An important gene associated with Pemphigus Vegetans is DSG1 (Desmoglein 1), and among its related pathways/superpathways are Developmental Biology and Keratinization. Affiliated tissues include skin, tongue and lung.

Wikipedia : 76 Pemphigus vegetans is a localized form of pemphigus vulgaris. in which there is a localized vegetating... more...

Related Diseases for Pemphigus Vegetans

Graphical network of the top 20 diseases related to Pemphigus Vegetans:



Diseases related to Pemphigus Vegetans

Symptoms & Phenotypes for Pemphigus Vegetans

Drugs & Therapeutics for Pemphigus Vegetans

Search Clinical Trials , NIH Clinical Center for Pemphigus Vegetans

Genetic Tests for Pemphigus Vegetans

Anatomical Context for Pemphigus Vegetans

MalaCards organs/tissues related to Pemphigus Vegetans:

41
Skin, Tongue, Lung, Colon, Testes, Neutrophil

Publications for Pemphigus Vegetans

Articles related to Pemphigus Vegetans:

(show top 50) (show all 134)
# Title Authors Year
1
Reduced IgG anti-desmocollin autoantibody titre and concomitant improvement in a patient with pemphigus vegetans. ( 29336313 )
2018
2
Pemphigus vegetans with the manifestations of acrodermatitis continua: A rare variant. ( 29058326 )
2018
3
Chronic Paronychia and Onychomadesis in Pemphigus Vegetans: An Unusual Presentation in a Rare Autoimmune Disease. ( 29560011 )
2018
4
Elevated serum eosinophil cationic protein and transforming growth factor-I+ levels in a patient with pemphigus vegetans. ( 29862541 )
2018
5
Pemphigus Vegetans Confined to the Face and Scalp. ( 29551118 )
2018
6
Pemphigus Vegetans in the Inguinal Folds. ( 29937062 )
2018
7
Atypical Clinical and Serological Manifestation of Pemphigus Vegetans: A Case Report and Review of the Literature. ( 28559810 )
2017
8
Pemphigus vegetans arising in umbilicus: Successful clearance with intralesional steroid. ( 28879869 )
2017
9
The Rare Case of Pemphigus Vegetans in Association with Malnutrition Children in the Multidisciplinary Management. ( 28559814 )
2017
10
Successful monotherapy of pemphigus vegetans with minocycline and nicotinamide. ( 27600093 )
2016
11
Cerebriform Cutaneous Lesions in Pemphigus Vegetans. ( 27057025 )
2016
12
Pemphigus vegetans with coexistent herpes simplex infection and deep venous thrombosis of the lower extremities. ( 26178000 )
2015
13
Pemphigus vegetans associated with Gitelman syndrome. ( 26515865 )
2015
14
Vegetating inguinal and perianal lesions: a quiz. Pemphigus vegetans, Hallopeau type. ( 25325567 )
2015
15
IgG/IgA pemphigus representing pemphigus vegetans caused by low titres of IgG and IgA antibodies to desmoglein 3 and IgA antibodies to desmocollin 3. ( 25865168 )
2015
16
Pemphigus vegetans of the folds (intertriginous areas). ( 26051064 )
2015
17
Pemphigus vegetans presenting as a verrucous plaque on the finger. ( 26204944 )
2015
18
Multiple vegetating lesions over the genitalia. Diagnosis: Pemphigus vegetans. ( 25900933 )
2015
19
Pemphigus vegetans localized to unusual sites. ( 26261132 )
2015
20
Treatment of pemphigus vegetans to rituximab refractory to conventional therapy. ( 25230067 )
2014
21
"Pemphigus vegetans of the scalp" ( 25339136 )
2014
22
Cobblestone mouth: An exuberant oral presentation of pemphigus vegetans. ( 25062647 )
2014
23
Localized Pemphigus Vegetans without Mucosal Involvement. ( 24700958 )
2014
24
A case of concurrent pemphigoid vegetans and pemphigus vegetans remitted without oral corticosteroid. ( 24359309 )
2013
25
Two cases of pemphigus vegetans with IgG anti-desmocollin 3 antibodies. ( 23946009 )
2013
26
Pemphigus vegetans of the tongue: a diagnostic and therapeutic challenge. ( 23414160 )
2013
27
Pemphigus vegetans variant of IgA pemphigus, a variant of IgA pemphigus and other autoimmune blistering disorders. ( 23221471 )
2013
28
Pemphigus vegetans: An unusual presentation. ( 23189253 )
2012
29
Pemphigus vegetans associated with intranasal cocaine abuse. ( 22971310 )
2012
30
Oral pemphigus vegetans: a case report. ( 23122017 )
2012
31
Pemphigus vegetans of the nose. ( 22278872 )
2012
32
Pyodermatitis-pyostomatitis vegetans: a differential diagnosis of pemphigus vegetans. ( 22570054 )
2012
33
The neumann type of pemphigus vegetans treated with combination of dapsone and steroid. ( 22346265 )
2011
34
Pemphigus vegetans induced by use of enalapril. ( 22281913 )
2011
35
Facial pemphigus vegetans. ( 21352290 )
2011
36
Pemphigus vegetans: a clinical, histological, immunopathological and prognostic study. ( 21198951 )
2011
37
A rare case of pemphigus vegetans mimicking malignancy on F-18 FDG PET/CT. ( 21285693 )
2011
38
Pemphigus vegetans--immunopathological findings in a rare variant of pemphigus vulgaris. ( 19725838 )
2010
39
Necrotizing fasciitis caused by Cryptococcus neoformans in a patient with pemphigus vegetans. ( 19663839 )
2009
40
Hallopeau type of pemphigus vegetans confined to the right foot: case report. ( 19323913 )
2009
41
Pemphigus vegetans in a patient with colonic cancer. ( 19915243 )
2009
42
Exophytic plaques, blisters, and mouth ulcers. Pemphigus vegetans (PV), Neumann type. ( 19528434 )
2009
43
The use of test skin grafting in pemphigus vegetans. ( 18718831 )
2009
44
Canine hyperplastic intraepidermal pustular and suprabasal acantholytic dermatosis with features of human pemphigus vegetans. ( 17606523 )
2007
45
Pemphigus vegetans Neumann type with anti-desmoglein and anti-periplakin autoantibodies. ( 17951135 )
2007
46
Complete remission of drug-resistant Pemphigus vegetans treated by extracorporeal photopheresis. ( 17567330 )
2007
47
Pemphigus vegetans associated with gastric cancer. ( 17894743 )
2007
48
Pemphigus vegetans of the oral cavity. ( 16650170 )
2006
49
Pemphigus vegetans associated with verrucous lesions: expanding a phenotype. ( 16832564 )
2006
50
Paraneoplastic pemphigus with pemphigus vegetans-like lesions revealing non-Hodgkin lymphoma. ( 17229621 )
2006

Variations for Pemphigus Vegetans

Expression for Pemphigus Vegetans

Search GEO for disease gene expression data for Pemphigus Vegetans.

Pathways for Pemphigus Vegetans

Pathways related to Pemphigus Vegetans according to GeneCards Suite gene sharing:

# Super pathways Score Top Affiliating Genes
1
Show member pathways
12.34 DSC3 DSG1 PPL
2
Show member pathways
11.25 DSC3 DSG1 PPL

GO Terms for Pemphigus Vegetans

Cellular components related to Pemphigus Vegetans according to GeneCards Suite gene sharing:

# Name GO ID Score Top Affiliating Genes
1 cell junction GO:0030054 9.33 DSC3 DSG1 PPL
2 cell-cell junction GO:0005911 9.26 DSC3 DSG1
3 cornified envelope GO:0001533 9.13 DSC3 DSG1 PPL
4 desmosome GO:0030057 8.8 DSC3 DSG1 PPL

Biological processes related to Pemphigus Vegetans according to GeneCards Suite gene sharing:

# Name GO ID Score Top Affiliating Genes
1 homophilic cell adhesion via plasma membrane adhesion molecules GO:0007156 9.16 DSC3 DSG1
2 keratinization GO:0031424 9.13 DSC3 DSG1 PPL
3 cornification GO:0070268 8.8 DSC3 DSG1 PPL

Sources for Pemphigus Vegetans

3 CDC
7 CNVD
9 Cosmic
10 dbSNP
11 DGIdb
17 ExPASy
19 FMA
28 GO
29 GTR
30 HGMD
31 HMDB
32 HPO
33 ICD10
34 ICD10 via Orphanet
35 ICD9CM
36 IUPHAR
37 KEGG
38 LifeMap
40 LOVD
42 MedGen
44 MeSH
45 MESH via Orphanet
46 MGI
49 NCI
50 NCIt
51 NDF-RT
54 NINDS
55 Novoseek
57 OMIM
58 OMIM via Orphanet
62 PubMed
64 QIAGEN
69 SNOMED-CT via HPO
70 SNOMED-CT via Orphanet
71 TGDB
72 Tocris
73 UMLS
74 UMLS via Orphanet
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