MCID: PTY006
MIFTS: 23

Pityriasis Lichenoides Et Varioliformis Acuta

Categories: Rare diseases, Skin diseases

Aliases & Classifications for Pityriasis Lichenoides Et Varioliformis Acuta

MalaCards integrated aliases for Pityriasis Lichenoides Et Varioliformis Acuta:

Name: Pityriasis Lichenoides Et Varioliformis Acuta 53 73
Mucha-Habermann Disease 53
Pleva 53

Classifications:



External Ids:

ICD10 33 L41.0
UMLS 73 C0162852

Summaries for Pityriasis Lichenoides Et Varioliformis Acuta

NIH Rare Diseases : 53 Pityriasis lichenoides et varioliformis acuta (PLEVA) is the acute form of an inflammatory skin condition called pityriasis lichenoides. People with PLEVA may develop a few to more than one hundred scaling papules which may become filled with blood and/or pus, or erode into crusted red-brown spots. Papules may itch or burn, and some people may experience fever or joint pain. Although PLEVA may occur at any age (including infancy), it most commonly affects children and young adults. A skin biopsy is needed to confirm the diagnosis. The exact underlying cause is unknown, but some scientists suspect that it may occur due to an exaggerated immune response to an infection or an overproduction of certain white blood cells (a lymphoproliferative disorder). If treatment is necessary, recommended therapies may include oral antibiotics, sun exposure, topical steroids, immunomodulators (medications used to help regulate or normalize the immune system), phototherapy and/or systemic steroids. PLEVA may last for a few weeks to years, and may fluctuate between getting better and worse before going away on its own.

MalaCards based summary : Pityriasis Lichenoides Et Varioliformis Acuta, also known as mucha-habermann disease, is related to pityriasis lichenoides and febrile ulceronecrotic mucha-habermann disease. An important gene associated with Pityriasis Lichenoides Et Varioliformis Acuta is CD7 (CD7 Molecule). Affiliated tissues include skin, t cells and tongue.

Wikipedia : 76 Pityriasis lichenoides et varioliformis acuta is a disease of the immune system. It is the more severe... more...

Related Diseases for Pityriasis Lichenoides Et Varioliformis Acuta

Diseases related to Pityriasis Lichenoides Et Varioliformis Acuta via text searches within MalaCards or GeneCards Suite gene sharing:

(show all 30)
# Related Disease Score Top Affiliating Genes
1 pityriasis lichenoides 32.3 CD7 TNFRSF8
2 febrile ulceronecrotic mucha-habermann disease 11.8
3 lymphomatoid papulosis 10.7
4 parapsoriasis 10.5
5 pityriasis lichenoides chronica 10.5
6 lymphoma 10.5
7 mumps 10.3
8 hand, foot and mouth disease 10.3
9 mouth disease 10.3
10 influenza 10.3
11 measles 10.3
12 rubella 10.3
13 pityriasis rosea 10.3
14 psoriasis 10.3
15 psoriasis 2 10.3
16 psoriasis 7 10.3
17 toxoplasmosis 10.3
18 severe cutaneous adverse reaction 10.3
19 psoriasis 11 10.3
20 psoriasis 13 10.3
21 erysipeloid 10.3
22 x-linked intellectual disability-macrocephaly-macroorchidism syndrome 10.3
23 cutaneous t cell lymphoma 10.3
24 colon lymphoma 9.6 CD7 TNFRSF8
25 follicular mucinosis 9.5 CD7 TNFRSF8
26 sezary's disease 9.5 CD7 TNFRSF8
27 adult t-cell leukemia 9.4 CD7 TNFRSF8
28 mycosis fungoides 9.3 CD7 TNFRSF8
29 hematologic cancer 9.2 CD7 TNFRSF8
30 t-cell leukemia 9.0 CD7 TNFRSF8

Graphical network of the top 20 diseases related to Pityriasis Lichenoides Et Varioliformis Acuta:



Diseases related to Pityriasis Lichenoides Et Varioliformis Acuta

Symptoms & Phenotypes for Pityriasis Lichenoides Et Varioliformis Acuta

Drugs & Therapeutics for Pityriasis Lichenoides Et Varioliformis Acuta

Search Clinical Trials , NIH Clinical Center for Pityriasis Lichenoides Et Varioliformis Acuta

Genetic Tests for Pityriasis Lichenoides Et Varioliformis Acuta

Anatomical Context for Pityriasis Lichenoides Et Varioliformis Acuta

MalaCards organs/tissues related to Pityriasis Lichenoides Et Varioliformis Acuta:

41
Skin, T Cells, Tongue

Publications for Pityriasis Lichenoides Et Varioliformis Acuta

Articles related to Pityriasis Lichenoides Et Varioliformis Acuta:

(show top 50) (show all 83)
# Title Authors Year
1
Varicella zoster virus as a possible trigger for the development of pityriasis lichenoides et varioliformis acuta: retrospective analysis of our institutional cases. ( 29797478 )
2018
2
Pityriasis lichenoides et varioliformis acuta in skin of color: new observations by dermoscopy. ( 28243491 )
2017
3
Pityriasis Lichenoides et Varioliformis Acuta and Psoriasis Vulgaris: Mere Coincidence or a Rare Association? ( 28218230 )
2017
4
Pityriasis Lichenoides et Varioliformis Acuta: Remission with Hypopigmentation. ( 27301571 )
2016
5
Successful therapy of cyclosporin A in pityriasis lichenoides et varioliformis acuta preceded by hand, foot and mouth disease. ( 26669500 )
2015
6
Pityriasis lichenoides et varioliformis acuta after influenza vaccine. ( 26312710 )
2015
7
Lymphomatoid papulosis misdiagnosed as pityriasis lichenoides et varioliformis acuta: Two case reports and a literature review. ( 25371758 )
2014
8
Febrile ulceronecrotic Mucha-Habermann disease (pityriasis lichenoides et varioliformis acuta fulminans) associated with parvovirus infection. ( 23612031 )
2013
9
Pityriasis lichenoides et varioliformis acuta with numerous CD30(+) cells: a variant mimicking lymphomatoid papulosis and other cutaneous lymphomas. A clinicopathologic, immunohistochemical, and molecular biological study of 13 cases. ( 22472952 )
2012
10
Pityriasis lichenoides et varioliformis acuta: a rare association with the measles, mumps and rubella vaccine. ( 23157791 )
2012
11
Pityriasis lichenoides et varioliformis acuta associated with subcutaneous immunoglobulin administration. ( 22980275 )
2012
12
Febrile ulceronecrotic Mucha-Habermann disease (pityriasis lichenoides et varioliformis acuta fulminans) presenting as Stevens-Johnson syndrome. ( 22084981 )
2012
13
Pityriasis lichenoides et varioliformis acuta: case report and review of the literature. ( 22548038 )
2012
14
Varicella-Zoster Virus As a Possible Cause of Pityriasis Lichenoides et Varioliformis Acuta. ( 22938395 )
2012
15
Pityriasis lichenoides et varioliformis acuta exacerbated after tonsillectomy. ( 21719399 )
2011
16
Pityriasis lichenoides et varioliformis acuta and pityriasis lichenoides chronica: comparison of lesional T-cell subsets and investigation of viral associations. ( 21518386 )
2011
17
A child with PFAPA syndrome complicated by pityriasis lichenoides et varioliformis acuta. ( 21504456 )
2011
18
Pityriasis lichenoides with ulceronecrosis and hyperthermia: a rare variant of pityriasis lichenoides et varioliformis acuta. ( 20228548 )
2010
19
Conjunctival Inflammatory Nodule in a Patient with Pityriasis Lichenoides et Varioliformis Acuta. ( 20740044 )
2010
20
Pityriasis lichenoides et varioliformis acuta: a disease spectrum. ( 20465660 )
2010
21
Dermoscopy of pityriasis lichenoides et varioliformis acuta. ( 21079087 )
2010
22
Resistant pityriasis lichenoides et varioliformis acuta in a 3-year-old boy: successful treatment with methotrexate. ( 20465649 )
2010
23
Successful association in the treatment of pityriasis lichenoides et varioliformis acuta. ( 19175486 )
2009
24
Pityriasis lichenoides et varioliformis acuta in a 2-year-old boy. ( 19236427 )
2009
25
Rapid resolution of pityriasis lichenoides et varioliformis acuta with azithromycin. ( 18280363 )
2008
26
Limbal and bulbar inflammatory nodules in a patient with pityriasis lichenoides et varioliformis acuta. ( 18546922 )
2008
27
Triggering of pityriasis lichenoides et varioliformis acuta by radiocontrast iodide. ( 18608711 )
2008
28
An infantile case of pityriasis lichenoides et varioliformis acuta. ( 17578447 )
2007
29
Febrile ulceronecrotic pityriasis lichenoides et varioliformis acuta with fatal outcome. ( 16503892 )
2006
30
Picture of the month. Pityriasis lichenoides et varioliformis acuta. ( 16203944 )
2005
31
Septic, CD-30 positive febrile ulceronecrotic pityriasis lichenoides et varioliformis acuta. ( 16060878 )
2005
32
Transition of pityriasis lichenoides et varioliformis acuta to febrile ulceronecrotic Mucha-Habermann disease is associated with elevated serum tumour necrosis factor-alpha. ( 15840118 )
2005
33
Febrile ulceronecrotic pityriasis lichenoides et varioliformis acuta with atypical cells. ( 12581137 )
2003
34
Pityriasis lichenoides et varioliformis acuta. ( 12657766 )
2003
35
Pityriasis lichenoides et varioliformis acuta in pregnancy. Does it affect pregnancy outcome? ( 12235483 )
2002
36
Medium-dose ultraviolet A1 therapy for pityriasis lichenoides et varioliformis acuta and pityriasis lichenoides chronica. ( 12196751 )
2002
37
Pityriasis lichenoides et varioliformis acuta during pregnancy. ( 11763391 )
2001
38
Pityriasis lichenoides et varioliformis acuta in pregnancy. ( 11802190 )
2001
39
Expression of cutaneous lymphocyte-associated antigen and TIA-1 by lymphocytes in pityriasis lichenoides et varioliformis acuta and lymphomatoid papulosis: immunohistochemical study. ( 11553311 )
2001
40
T-Cell clonality in pityriasis lichenoides et varioliformis acuta: a heteroduplex analysis of 20 cases. ( 11115158 )
2000
41
Pityriasis lichenoides et varioliformis acuta in pregnancy: a case report. ( 9879156 )
1998
42
Pityriasis lichenoides et varioliformis acuta in HIV-1+ patients: a marker of early stage disease. The Military Medical Consortium for the Advancement of Retroviral Research (MMCARR). ( 9109005 )
1997
43
Lymphomatoid papulosis, pityriasis lichenoides et varioliformis acuta, and anaplastic large-cell (Ki-1+) lymphoma. ( 9270525 )
1997
44
Pityriasis lichenoides et varioliformis acuta and group-A beta hemolytic streptococcal infection. ( 7591466 )
1995
45
Febrile ulceronecrotic pityriasis lichenoides et varioliformis acuta. ( 8288786 )
1994
46
Febrile ulceronecrotic pityriasis lichenoides et varioliformis acuta. ( 7841557 )
1994
47
A widespread hemorrhagic and crusted eruption of recent onset. Pityriasis lichenoides et varioliformis acuta (PLEVA) (Mucha-Habermann disease). ( 8447679 )
1993
48
HIV seropositivity in association with pityriasis lichenoides et varioliformis acuta. ( 1424257 )
1992
49
Lymphomatoid papulosis: clinicopathological comparative study with pityriasis lichenoides et varioliformis acuta. ( 1665158 )
1991
50
Immunohistochemical distinction of lymphomatoid papulosis and pityriasis lichenoides et varioliformis acuta. ( 1691596 )
1990

Variations for Pityriasis Lichenoides Et Varioliformis Acuta

Expression for Pityriasis Lichenoides Et Varioliformis Acuta

Search GEO for disease gene expression data for Pityriasis Lichenoides Et Varioliformis Acuta.

Pathways for Pityriasis Lichenoides Et Varioliformis Acuta

GO Terms for Pityriasis Lichenoides Et Varioliformis Acuta

Biological processes related to Pityriasis Lichenoides Et Varioliformis Acuta according to GeneCards Suite gene sharing:

# Name GO ID Score Top Affiliating Genes
1 immune response GO:0006955 8.62 CD7 TNFRSF8

Sources for Pityriasis Lichenoides Et Varioliformis Acuta

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