PLEVA
MCID: PTY006
MIFTS: 24

Pityriasis Lichenoides Et Varioliformis Acuta (PLEVA)

Categories: Immune diseases, Rare diseases, Skin diseases

Aliases & Classifications for Pityriasis Lichenoides Et Varioliformis Acuta

MalaCards integrated aliases for Pityriasis Lichenoides Et Varioliformis Acuta:

Name: Pityriasis Lichenoides Et Varioliformis Acuta 54 74
Mucha-Habermann Disease 54
Pleva 54

Classifications:



External Ids:

ICD10 34 L41.0
UMLS 74 C0162852

Summaries for Pityriasis Lichenoides Et Varioliformis Acuta

NIH Rare Diseases : 54 Pityriasis lichenoides et varioliformis acuta (PLEVA) is the acute form of an inflammatory skin condition called pityriasis lichenoides. People with PLEVA may develop a few to more than one hundred scaling papules which may become filled with blood and/or pus, or erode into crusted red-brown spots. Papules may itch or burn, and some people may experience fever or joint pain. Although PLEVA may occur at any age (including infancy), it most commonly affects children and young adults. A skin biopsy is needed to confirm the diagnosis. The exact underlying cause is unknown, but some scientists suspect that it may occur due to an exaggerated immune response to an infection or an overproduction of certain white blood cells (a lymphoproliferative disorder). If treatment is necessary, recommended therapies may include oral antibiotics, sun exposure, topical steroids, immunomodulators (medications used to help regulate or normalize the immune system), phototherapy and/or systemic steroids. PLEVA may last for a few weeks to years, and may fluctuate between getting better and worse before going away on its own.

MalaCards based summary : Pityriasis Lichenoides Et Varioliformis Acuta, also known as mucha-habermann disease, is related to pityriasis lichenoides and febrile ulceronecrotic mucha-habermann disease. An important gene associated with Pityriasis Lichenoides Et Varioliformis Acuta is CD7 (CD7 Molecule). Affiliated tissues include skin, t cells and tongue.

Wikipedia : 77 Pityriasis lichenoides et varioliformis acuta (PLEVA) is a disease of the immune system. It is the more... more...

Related Diseases for Pityriasis Lichenoides Et Varioliformis Acuta

Graphical network of the top 20 diseases related to Pityriasis Lichenoides Et Varioliformis Acuta:



Diseases related to Pityriasis Lichenoides Et Varioliformis Acuta

Symptoms & Phenotypes for Pityriasis Lichenoides Et Varioliformis Acuta

Drugs & Therapeutics for Pityriasis Lichenoides Et Varioliformis Acuta

Search Clinical Trials , NIH Clinical Center for Pityriasis Lichenoides Et Varioliformis Acuta

Genetic Tests for Pityriasis Lichenoides Et Varioliformis Acuta

Anatomical Context for Pityriasis Lichenoides Et Varioliformis Acuta

MalaCards organs/tissues related to Pityriasis Lichenoides Et Varioliformis Acuta:

42
Skin, T Cells, Tongue

Publications for Pityriasis Lichenoides Et Varioliformis Acuta

Articles related to Pityriasis Lichenoides Et Varioliformis Acuta:

(show top 50) (show all 102)
# Title Authors Year
1
A case of febrile ulceronecrotic Mucha-Habermann disease with comorbidities. ( 30860167 )
2019
2
A Case of Pityriasis Lichenoides et Varioliformis Acuta Pemphigoides Successfully Treated with Methotrexate and Corticosteroids. ( 30659712 )
2019
3
Clinical Aspects and Treatment of Pityriasis Lichenoides Et Varioliformis Acuta: A Retrospective Vietnamese Study. ( 30745957 )
2019
4
Varicella zoster virus as a possible trigger for the development of pityriasis lichenoides et varioliformis acuta: retrospective analysis of our institutional cases. ( 29797478 )
2018
5
Febrile ulceronecrotic Mucha Habermann disease mimicking aggressive epidermotropic CD8+ cytotoxic T-cell lymphoma: a diagnostic challenge. ( 30325315 )
2018
6
Pityriasis lichenoides et varioliformis acuta in skin of color: new observations by dermoscopy. ( 28243491 )
2017
7
Pityriasis Lichenoides et Varioliformis Acuta and Psoriasis Vulgaris: Mere Coincidence or a Rare Association? ( 28218230 )
2017
8
Pityriasis Lichenoides et Varioliformis Acuta: Remission with Hypopigmentation. ( 27301571 )
2016
9
Seronegative arthritis secondary to Mucha-Habermann disease. ( 27345853 )
2016
10
Successful therapy of cyclosporin A in pityriasis lichenoides et varioliformis acuta preceded by hand, foot and mouth disease. ( 26669500 )
2015
11
Pityriasis lichenoides et varioliformis acuta after influenza vaccine. ( 26312710 )
2015
12
Lymphomatoid papulosis misdiagnosed as pityriasis lichenoides et varioliformis acuta: Two case reports and a literature review. ( 25371758 )
2014
13
Steroid unresponsive case of ulcerative mucha-habermann disease (febrile ulcernecrotic mucha-habermann disease) treated with methotrexate. ( 25484416 )
2014
14
Febrile ulceronecrotic Mucha-Habermann disease (pityriasis lichenoides et varioliformis acuta fulminans) associated with parvovirus infection. ( 23612031 )
2013
15
Mucha-Habermann disease. ( 24051916 )
2013
16
Pityriasis lichenoides et varioliformis acuta with numerous CD30(+) cells: a variant mimicking lymphomatoid papulosis and other cutaneous lymphomas. A clinicopathologic, immunohistochemical, and molecular biological study of 13 cases. ( 22472952 )
2012
17
Pityriasis lichenoides et varioliformis acuta: a rare association with the measles, mumps and rubella vaccine. ( 23157791 )
2012
18
Pityriasis lichenoides et varioliformis acuta associated with subcutaneous immunoglobulin administration. ( 22980275 )
2012
19
Febrile ulceronecrotic Mucha-Habermann disease (pityriasis lichenoides et varioliformis acuta fulminans) presenting as Stevens-Johnson syndrome. ( 22084981 )
2012
20
Pityriasis lichenoides et varioliformis acuta: case report and review of the literature. ( 22548038 )
2012
21
Varicella-Zoster Virus As a Possible Cause of Pityriasis Lichenoides et Varioliformis Acuta. ( 22938395 )
2012
22
Pityriasis lichenoides et varioliformis acuta exacerbated after tonsillectomy. ( 21719399 )
2011
23
Pityriasis lichenoides et varioliformis acuta and pityriasis lichenoides chronica: comparison of lesional T-cell subsets and investigation of viral associations. ( 21518386 )
2011
24
A child with PFAPA syndrome complicated by pityriasis lichenoides et varioliformis acuta. ( 21504456 )
2011
25
Pityriasis lichenoides with ulceronecrosis and hyperthermia: a rare variant of pityriasis lichenoides et varioliformis acuta. ( 20228548 )
2010
26
Conjunctival Inflammatory Nodule in a Patient with Pityriasis Lichenoides et Varioliformis Acuta. ( 20740044 )
2010
27
Pityriasis lichenoides et varioliformis acuta: a disease spectrum. ( 20465660 )
2010
28
Dermoscopy of pityriasis lichenoides et varioliformis acuta. ( 21079087 )
2010
29
Resistant pityriasis lichenoides et varioliformis acuta in a 3-year-old boy: successful treatment with methotrexate. ( 20465649 )
2010
30
Successful association in the treatment of pityriasis lichenoides et varioliformis acuta. ( 19175486 )
2009
31
Pityriasis lichenoides et varioliformis acuta in a 2-year-old boy. ( 19236427 )
2009
32
Rapid resolution of pityriasis lichenoides et varioliformis acuta with azithromycin. ( 18280363 )
2008
33
Limbal and bulbar inflammatory nodules in a patient with pityriasis lichenoides et varioliformis acuta. ( 18546922 )
2008
34
Triggering of pityriasis lichenoides et varioliformis acuta by radiocontrast iodide. ( 18608711 )
2008
35
An infantile case of pityriasis lichenoides et varioliformis acuta. ( 17578447 )
2007
36
Febrile ulceronecrotic pityriasis lichenoides et varioliformis acuta with fatal outcome. ( 16503892 )
2006
37
A case of ulceronecrotic Mucha-Habermann disease with pulmonary involvement. ( 16707893 )
2006
38
Picture of the month. Pityriasis lichenoides et varioliformis acuta. ( 16203944 )
2005
39
Septic, CD-30 positive febrile ulceronecrotic pityriasis lichenoides et varioliformis acuta. ( 16060878 )
2005
40
Transition of pityriasis lichenoides et varioliformis acuta to febrile ulceronecrotic Mucha-Habermann disease is associated with elevated serum tumour necrosis factor-alpha. ( 15840118 )
2005
41
Febrile ulceronecrotic pityriasis lichenoides et varioliformis acuta with atypical cells. ( 12581137 )
2003
42
Pityriasis lichenoides et varioliformis acuta. ( 12657766 )
2003
43
Pityriasis lichenoides et varioliformis acuta in pregnancy. Does it affect pregnancy outcome? ( 12235483 )
2002
44
Medium-dose ultraviolet A1 therapy for pityriasis lichenoides et varioliformis acuta and pityriasis lichenoides chronica. ( 12196751 )
2002
45
Pityriasis lichenoides et varioliformis acuta during pregnancy. ( 11763391 )
2001
46
Pityriasis lichenoides et varioliformis acuta in pregnancy. ( 11802190 )
2001
47
Expression of cutaneous lymphocyte-associated antigen and TIA-1 by lymphocytes in pityriasis lichenoides et varioliformis acuta and lymphomatoid papulosis: immunohistochemical study. ( 11553311 )
2001
48
T-Cell clonality in pityriasis lichenoides et varioliformis acuta: a heteroduplex analysis of 20 cases. ( 11115158 )
2000
49
Mucha-Habermann disease-like eruptions due to Tegafur. ( 10209923 )
1999
50
Pityriasis lichenoides et varioliformis acuta in pregnancy: a case report. ( 9879156 )
1998

Variations for Pityriasis Lichenoides Et Varioliformis Acuta

Expression for Pityriasis Lichenoides Et Varioliformis Acuta

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Pathways for Pityriasis Lichenoides Et Varioliformis Acuta

GO Terms for Pityriasis Lichenoides Et Varioliformis Acuta

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