MCID: PTY006
MIFTS: 24

Pityriasis Lichenoides Et Varioliformis Acuta

Categories: Immune diseases, Rare diseases, Skin diseases

Aliases & Classifications for Pityriasis Lichenoides Et Varioliformis Acuta

MalaCards integrated aliases for Pityriasis Lichenoides Et Varioliformis Acuta:

Name: Pityriasis Lichenoides Et Varioliformis Acuta 54 74
Mucha-Habermann Disease 54
Pleva 54

Classifications:



External Ids:

ICD10 34 L41.0
UMLS 74 C0162852

Summaries for Pityriasis Lichenoides Et Varioliformis Acuta

NIH Rare Diseases : 54 Pityriasis lichenoides et varioliformis acuta (PLEVA) is the acute form of an inflammatory skin condition called pityriasis lichenoides. People with PLEVA may develop a few to more than one hundred scaling papules which may become filled with blood and/or pus, or erode into crusted red-brown spots. Papules may itch or burn, and some people may experience fever or joint pain. Although PLEVA may occur at any age (including infancy), it most commonly affects children and young adults. A skin biopsy is needed to confirm the diagnosis. The exact underlying cause is unknown, but some scientists suspect that it may occur due to an exaggerated immune response to an infection or an overproduction of certain white blood cells (a lymphoproliferative disorder). If treatment is necessary, recommended therapies may include oral antibiotics, sun exposure, topical steroids, immunomodulators (medications used to help regulate or normalize the immune system), phototherapy and/or systemic steroids. PLEVA may last for a few weeks to years, and may fluctuate between getting better and worse before going away on its own.

MalaCards based summary : Pityriasis Lichenoides Et Varioliformis Acuta, also known as mucha-habermann disease, is related to pityriasis lichenoides and febrile ulceronecrotic mucha-habermann disease. An important gene associated with Pityriasis Lichenoides Et Varioliformis Acuta is CD7 (CD7 Molecule). Affiliated tissues include skin, t cells and tongue.

Wikipedia : 77 Pityriasis lichenoides et varioliformis acuta (PLEVA) is a disease of the immune system. It is the more... more...

Related Diseases for Pityriasis Lichenoides Et Varioliformis Acuta

Graphical network of the top 20 diseases related to Pityriasis Lichenoides Et Varioliformis Acuta:



Diseases related to Pityriasis Lichenoides Et Varioliformis Acuta

Symptoms & Phenotypes for Pityriasis Lichenoides Et Varioliformis Acuta

Drugs & Therapeutics for Pityriasis Lichenoides Et Varioliformis Acuta

Search Clinical Trials , NIH Clinical Center for Pityriasis Lichenoides Et Varioliformis Acuta

Genetic Tests for Pityriasis Lichenoides Et Varioliformis Acuta

Anatomical Context for Pityriasis Lichenoides Et Varioliformis Acuta

MalaCards organs/tissues related to Pityriasis Lichenoides Et Varioliformis Acuta:

42
Skin, T Cells, Tongue, Colon

Publications for Pityriasis Lichenoides Et Varioliformis Acuta

Articles related to Pityriasis Lichenoides Et Varioliformis Acuta:

(show top 50) (show all 141)
# Title Authors Year
1
A case of febrile ulceronecrotic Mucha-Habermann disease with comorbidities. ( 30860167 )
2019
2
A Case of Pityriasis Lichenoides et Varioliformis Acuta Pemphigoides Successfully Treated with Methotrexate and Corticosteroids. ( 30659712 )
2019
3
Clinical Aspects and Treatment of Pityriasis Lichenoides Et Varioliformis Acuta: A Retrospective Vietnamese Study. ( 30745957 )
2019
4
Febrile ulceronecrotic Mucha-Habermann disease after levamisole-adulterated cocaine use: an unusual case. ( 29851134 )
2018
5
Febrile ulceronecrotic Mucha Habermann disease mimicking aggressive epidermotropic CD8+ cytotoxic T-cell lymphoma: a diagnostic challenge. ( 30325315 )
2018
6
Varicella zoster virus as a possible trigger for the development of pityriasis lichenoides et varioliformis acuta: retrospective analysis of our institutional cases. ( 29797478 )
2018
7
A Fatal Case of Febrile Ulceronecrotic Mucha-Habermann Disease which Presenting as Toxic Epidermal Necrolysis. ( 29263553 )
2017
8
Pityriasis Lichenoides et Varioliformis Acuta and Psoriasis Vulgaris: Mere Coincidence or a Rare Association? ( 28218230 )
2017
9
Pityriasis lichenoides et varioliformis acuta in skin of color: new observations by dermoscopy. ( 28243491 )
2017
10
A Case of Primary Cutaneous Aggressive Epidermotropic CD8+ Cytotoxic T-cell Lymphoma Misdiagnosed as Febrile Ulceronecrotic Mucha-Habermann Disease. ( 26039505 )
2016
11
Febrile ulceronecrotic Mucha-Habermann disease: proposed diagnostic criteria and therapeutic evaluation. ( 26695875 )
2016
12
Complete resolution of febrile ulceronecrotic Mucha-Habermann disease following infliximab therapy. ( 26790133 )
2016
13
A fatal case of febrile ulceronecrotic Mucha-Habermann disease in a child. ( 27222883 )
2016
14
Febrile ulceronecrotic Mucha-Habermann disease in an 8-year-old boy responding to methotrexate. ( 27368714 )
2016
15
Diagnosis of febrile ulceronecrotic Mucha-Habermann disease: strict clinical criteria are imperative. ( 27607047 )
2016
16
Successful therapy of cyclosporin A in pityriasis lichenoides et varioliformis acuta preceded by hand, foot and mouth disease. ( 26669500 )
2016
17
Pityriasis Lichenoides et Varioliformis Acuta: Remission with Hypopigmentation. ( 27301571 )
2016
18
Seronegative arthritis secondary to Mucha-Habermann disease. ( 27345853 )
2016
19
Febrile ulceronecrotic Mucha-Habermann disease following suspected hemorrhagic chickenpox infection in a 20-month-old boy. ( 25627543 )
2015
20
Methotrexate Treatment in Children with Febrile Ulceronecrotic Mucha-Habermann Disease: Case Report and Literature Review. ( 26413356 )
2015
21
Febrile Ulceronecrotic Mucha-Habermann Disease: Two Cases with Excellent Response to Methotrexate. ( 26584702 )
2015
22
Pityriasis lichenoides et varioliformis acuta after influenza vaccine. ( 26312710 )
2015
23
Pentoxifylline and cyclosporine in the treatment of febrile ulceronecrotic Mucha-Habermann disease. ( 23005254 )
2014
24
Febrile ulceronecrotic Mucha-Habermann disease in a young boy: a case report and review of the literature. ( 24473967 )
2014
25
Lymphomatoid papulosis misdiagnosed as pityriasis lichenoides et varioliformis acuta: Two case reports and a literature review. ( 25371758 )
2014
26
Varicella-zoster virus as a possible cause of pityriasis lichenoides et varioliformis acuta. ( 22938395 )
2014
27
Steroid unresponsive case of ulcerative mucha-habermann disease (febrile ulcernecrotic mucha-habermann disease) treated with methotrexate. ( 25484416 )
2014
28
Febrile ulceronecrotic Mucha-Habermann disease with central nervous system vasculitis. ( 22276640 )
2013
29
Varicella precipitating febrile ulceronecrotic Mucha-Habermann disease. ( 23106817 )
2013
30
Febrile ulceronecrotic mucha habermann disease: case report of a dark-skinned patient. ( 23466681 )
2013
31
Febrile ulceronecrotic Mucha-Habermann disease (pityriasis lichenoides et varioliformis acuta fulminans) associated with parvovirus infection. ( 23612031 )
2013
32
Febrile ulceronecrotic Mucha-Habermann disease. ( 24127370 )
2013
33
Febrile ulceronecrotic Mucha-Habermann disease. ( 24343222 )
2013
34
Syphilis mimicking other dermatological diseases: reactive arthritis and mucha-habermann disease. ( 23467097 )
2013
35
Mucha-Habermann disease. ( 24051916 )
2013
36
Febrile ulceronecrotic Mucha-Habermann disease in a 34-month-old boy: a case report and review of the literature. ( 21906156 )
2012
37
Febrile ulceronecrotic Mucha-Habermann disease (pityriasis lichenoides et varioliformis acuta fulminans) presenting as Stevens-Johnson syndrome. ( 22084981 )
2012
38
Febrile ulceronecrotic Mucha-Habermann disease: a case with systemic symptoms managed with subcutaneous methotrexate. ( 23157793 )
2012
39
Febrile ulceronecrotic Mucha-Habermann disease: treatment with infliximab and intravenous immunoglobulins and review of the literature. ( 23391565 )
2012
40
Pityriasis lichenoides et varioliformis acuta with numerous CD30(+) cells: a variant mimicking lymphomatoid papulosis and other cutaneous lymphomas. A clinicopathologic, immunohistochemical, and molecular biological study of 13 cases. ( 22472952 )
2012
41
Pityriasis lichenoides et varioliformis acuta: a rare association with the measles, mumps and rubella vaccine. ( 23157791 )
2012
42
Pityriasis lichenoides et varioliformis acuta: case report and review of the literature. ( 22548038 )
2012
43
Pityriasis lichenoides et varioliformis acuta associated with subcutaneous immunoglobulin administration. ( 22980275 )
2012
44
A child with PFAPA syndrome complicated by pityriasis lichenoides et varioliformis acuta. ( 21504456 )
2011
45
Pityriasis lichenoides et varioliformis acuta and pityriasis lichenoides chronica: comparison of lesional T-cell subsets and investigation of viral associations. ( 21518386 )
2011
46
Pityriasis lichenoides et varioliformis acuta exacerbated after tonsillectomy. ( 21719399 )
2011
47
High-dose immunoglobulines and extracorporeal photochemotherapy in the treatment of febrile ulceronecrotic Mucha-Habermann disease. ( 20666830 )
2010
48
CASE REPORT Febrile Ulceronecrotic Mucha-Habermann Disease. ( 20697454 )
2010
49
Febrile ulceronecrotic Mucha-Habermann disease in adult patient successfully treated with systemic corticosteroid. ( 21308316 )
2010
50
Pityriasis lichenoides with ulceronecrosis and hyperthermia: a rare variant of pityriasis lichenoides et varioliformis acuta. ( 20228548 )
2010

Variations for Pityriasis Lichenoides Et Varioliformis Acuta

Expression for Pityriasis Lichenoides Et Varioliformis Acuta

Search GEO for disease gene expression data for Pityriasis Lichenoides Et Varioliformis Acuta.

Pathways for Pityriasis Lichenoides Et Varioliformis Acuta

GO Terms for Pityriasis Lichenoides Et Varioliformis Acuta

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