MCID: PRM132
MIFTS: 15

Primary Cutaneous Cd4+ Small/medium-Sized Pleomorphic T-Cell Lymphoma

Categories: Blood diseases, Immune diseases, Rare diseases, Skin diseases

Aliases & Classifications for Primary Cutaneous Cd4+ Small/medium-Sized Pleomorphic T-Cell...

MalaCards integrated aliases for Primary Cutaneous Cd4+ Small/medium-Sized Pleomorphic T-Cell Lymphoma:

Name: Primary Cutaneous Cd4+ Small/medium-Sized Pleomorphic T-Cell Lymphoma 58

Classifications:

Orphanet: 58  
Rare skin diseases
Rare haematological diseases


External Ids:

ICD10 via Orphanet 33 C84.4
Orphanet 58 ORPHA178522

Summaries for Primary Cutaneous Cd4+ Small/medium-Sized Pleomorphic T-Cell...

MalaCards based summary : Primary Cutaneous Cd4+ Small/medium-Sized Pleomorphic T-Cell Lymphoma is related to lymphoma and b-cell lymphoma. An important gene associated with Primary Cutaneous Cd4+ Small/medium-Sized Pleomorphic T-Cell Lymphoma is BCL6 (BCL6 Transcription Repressor), and among its related pathways/superpathways are NF-kappaB Signaling and IgA-Producing B Cells in the Intestine. Affiliated tissues include eye.

Related Diseases for Primary Cutaneous Cd4+ Small/medium-Sized Pleomorphic T-Cell...

Graphical network of the top 20 diseases related to Primary Cutaneous Cd4+ Small/medium-Sized Pleomorphic T-Cell Lymphoma:



Diseases related to Primary Cutaneous Cd4+ Small/medium-Sized Pleomorphic T-Cell Lymphoma

Symptoms & Phenotypes for Primary Cutaneous Cd4+ Small/medium-Sized Pleomorphic T-Cell...

Drugs & Therapeutics for Primary Cutaneous Cd4+ Small/medium-Sized Pleomorphic T-Cell...

Search Clinical Trials , NIH Clinical Center for Primary Cutaneous Cd4+ Small/medium-Sized Pleomorphic T-Cell Lymphoma

Genetic Tests for Primary Cutaneous Cd4+ Small/medium-Sized Pleomorphic T-Cell...

Anatomical Context for Primary Cutaneous Cd4+ Small/medium-Sized Pleomorphic T-Cell...

MalaCards organs/tissues related to Primary Cutaneous Cd4+ Small/medium-Sized Pleomorphic T-Cell Lymphoma:

40
Eye

Publications for Primary Cutaneous Cd4+ Small/medium-Sized Pleomorphic T-Cell...

Articles related to Primary Cutaneous Cd4+ Small/medium-Sized Pleomorphic T-Cell Lymphoma:

(show all 19)
# Title Authors PMID Year
1
Monoclonal plasma cell infiltrates in the setting of cutaneous follicular helper T cell lymphoproliferative disorders. 61
31077877 2019
2
CD30+ T cell enriched primary cutaneous CD4+ small/medium sized pleomorphic T cell lymphoma: A distinct variant of indolent CD4+ T cell lymphoproliferative disease. 61
28965629 2017
3
Differential NFATc1 Expression in Primary Cutaneous CD4+ Small/Medium-Sized Pleomorphic T-Cell Lymphoma and Other Forms of Cutaneous T-Cell Lymphoma and Pseudolymphoma. 61
27097342 2017
4
Clinicopathological and molecular study of primary cutaneous CD4+ small/medium-sized pleomorphic T-cell lymphoma. 61
27550169 2016
5
Neoplastic Cells of Primary Cutaneous CD4+ Small/Medium-sized Pleomorphic T-cell Lymphoma Lack the Expression of Follicular T-helper Cell Defining Chemokine Receptor CXCR5. 61
26928629 2016
6
Methotrexate and etanercept-induced primary cutaneous CD4 positive small/medium-sized pleomorphic T-cell lymphoma. 61
27438209 2016
7
Primary Cutaneous CD4+ Small/Medium-Sized Pleomorphic T-Cell Lymphoma With Expression of Follicular T-Helper Cell Markers and Spontaneous Remission. 61
26724830 2016
8
Dermatopathology update. 61
23273924 2013
9
Expression of programmed death-1 in primary cutaneous CD4-positive small/medium-sized pleomorphic T-cell lymphoma, cutaneous pseudo-T-cell lymphoma, and other types of cutaneous T-cell lymphoma. 61
21989349 2012
10
Reappraisal of the provisional entity primary cutaneous CD4+ small/medium pleomorphic T-cell lymphoma: a series of 10 adult and pediatric patients and review of the literature. 61
21641676 2011
11
Dermal infiltrates of cutaneous T-cell lymphomas with epidermotropism but not other cutaneous lymphomas are abundant with langerinâș dendritic cells. 61
21054571 2011
12
Indolent CD8+ lymphoid proliferation of the ear: report of two cases and review of the literature. 61
21083681 2011
13
Therapeutic hotline: Primary cutaneous CD4 + small/medium-sized pleomorphic T cell lymphoma coexisting with myelodysplastic syndrome transforming into chronic myelomonocytic leukemia successfully treated with cyclophosphamide. 61
21054711 2010
14
Non-mycosis fungoides cutaneous T-cell lymphoma: reclassification according to the WHO-EORTC classification. 61
20132421 2010
15
Primary cutaneous CD4+ small-/medium-sized pleomorphic T-cell lymphoma: a cutaneous nodular proliferation of pleomorphic T lymphocytes of undetermined significance? A study of 136 cases. 61
19461234 2009
16
Primary cutaneous CD4+ small/medium-sized pleomorphic T-cell lymphoma associated with an annular elastolytic giant cell granuloma. 61
19292715 2009
17
Primary cutaneous CD4+ small/medium-sized pleomorphic T-cell lymphoma expresses follicular T-cell markers. 61
18987541 2009
18
Primary cutaneous zygomycosis due to Absidia corymbifera in a patient with cutaneous T cell lymphoma. 61
19301174 2009
19
The new World Health Organization-European Organization for Research and Treatment of Cancer classification for cutaneous lymphomas: a practical marriage of two giants. 61
16225594 2005

Variations for Primary Cutaneous Cd4+ Small/medium-Sized Pleomorphic T-Cell...

Expression for Primary Cutaneous Cd4+ Small/medium-Sized Pleomorphic T-Cell...

Search GEO for disease gene expression data for Primary Cutaneous Cd4+ Small/medium-Sized Pleomorphic T-Cell Lymphoma.

Pathways for Primary Cutaneous Cd4+ Small/medium-Sized Pleomorphic T-Cell...

Pathways related to Primary Cutaneous Cd4+ Small/medium-Sized Pleomorphic T-Cell Lymphoma according to GeneCards Suite gene sharing:

# Super pathways Score Top Affiliating Genes
1 11.47 CXCR5 BCL6
2 10.44 CXCR5 BCL6

GO Terms for Primary Cutaneous Cd4+ Small/medium-Sized Pleomorphic T-Cell...

Sources for Primary Cutaneous Cd4+ Small/medium-Sized Pleomorphic T-Cell...

3 CDC
7 CNVD
9 Cosmic
10 dbSNP
11 DGIdb
17 EFO
18 ExPASy
19 FMA
20 GARD
28 GO
29 GTR
30 HMDB
31 HPO
32 ICD10
33 ICD10 via Orphanet
34 ICD9CM
35 IUPHAR
36 KEGG
37 LifeMap
39 LOVD
41 MedGen
44 MeSH
45 MESH via Orphanet
46 MGI
49 NCI
50 NCIt
51 NDF-RT
53 NINDS
54 Novoseek
56 OMIM via Orphanet
57 OMIM® (Updated 20-May-2021)
61 PubMed
63 QIAGEN
68 SNOMED-CT via HPO
69 Tocris
70 UMLS
71 UMLS via Orphanet
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