| 1 |
Twenty-year-old African American woman with prion disease associated with the G114V <i>PRNP</i> variant. ( 29577079
)
|
Margolesky J....Saporta M.
|
2018 |
| 2 |
Microglia Are Critical in Host Defense Against Prion Disease. ( 29769333
)
|
Carroll J.A....Chesebro B.
|
2018 |
| 3 |
Prion disease: Skin is a source of infectious prions in sCJD. ( 29217825
)
|
Starling S.
|
2018 |
| 4 |
Autologous neural progenitor cell transplantation into newborn mice modeling for E200K genetic prion disease delays disease progression. ( 29494865
)
|
Frid K....Gabizon R.
|
2018 |
| 5 |
|
Takada L.T....Geschwind M.D.
|
2018 |
| 6 |
Presumptive BSE cases with an aberrant prion protein phenotype in Switzerland, 2011: Lack of prion disease in experimentally inoculated cattle and bovine prion protein transgenic mice. ( 29675959
)
|
Serra F....Seuberlich T.
|
2018 |
| 7 |
Acute Neurotoxicity Models of Prion Disease. ( 29393619
)
|
T Islam A.M....Collins S.J.
|
2018 |
| 8 |
Efficient prion disease transmission through common environmental materials. ( 29330304
)
|
Pritzkow S....Soto C.
|
2018 |
| 9 |
Prion disease: Dramatic increases in blood levels of tau and neurofilament light in patients with prion disease. ( 29545623
)
|
Ridler C.
|
2018 |
| 10 |
Cerebrospinal Fluid Prion Disease Biomarkers in Pre-clinical and Clinical Naturally Occurring Scrapie. ( 29572672
)
|
Llorens F....Zerr I.
|
2018 |
| 11 |
MicroRNA-16 targets mRNA involved in neurite extension and branching in hippocampal neurons during presymptomatic prion disease. ( 29277556
)
|
Burak K....Booth S.A.
|
2018 |
| 12 |
Chronic wasting disease: an evolving prion disease of cervids. ( 29887133
)
|
Benestad S.L....Telling G.C.
|
2018 |
| 13 |
Decrease of RyR2 in the prion infected cell line and in the brains of the scrapie infected mice models and the patients of human prion diseases. ( 29676187
)
|
Shi Q....Dong X.P.
|
2018 |
| 14 |
Prion Disease in Dromedary Camels, Algeria. ( 29652245
)
|
Babelhadj B....Vaccari G.
|
2018 |
| 15 |
Alterations in neuronal metabolism contribute to the pathogenesis of prion disease. ( 29915278
)
|
Bourgognon J.M....Steinert J.R.
|
2018 |
| 16 |
The language disorder of prion disease is characteristic of a dynamic aphasia and is rarely an isolated clinical feature. ( 29304167
)
|
Caine D....Mead S.
|
2018 |
| 17 |
Superficial bedside brain biopsy can be a safe and practical approach to confirm a rare form of prion disease in cerebellar ataxia: A case study. ( 28320192
)
|
Rusina R....MatA9j R.
|
2017 |
| 18 |
Evolution of Diagnostic Tests for Chronic Wasting Disease, a Naturally Occurring Prion Disease of Cervids. ( 28783058
)
|
Haley N.J....Richt J.A.
|
2017 |
| 19 |
Seeking a New Paradigm for Alzheimer's Disease: Considering the Roles of Inflammation, Blood-Brain Barrier Dysfunction, and Prion Disease. ( 29359063
)
|
McCaulley M.E....Grush K.A.
|
2017 |
| 20 |
Real-Time Quaking-Induced Conversion for Diagnosis of Prion Disease. ( 28861798
)
|
Satoh K....Nishida N.
|
2017 |
| 21 |
Gastrostomy in patients with prion disease. ( 28509623
)
|
Iwasaki Y....Yoshida M.
|
2017 |
| 22 |
Effects of a naturally occurring amino acid substitution in bovine PrP: a model for inherited prion disease in a natural host species. ( 29262866
)
|
Vrentas C.E....Nicholson E.M.
|
2017 |
| 23 |
Methods for Molecular Diagnosis of Human Prion Disease. ( 28861799
)
|
Wadsworth J.D.F....Collinge J.
|
2017 |
| 24 |
Norway seeks to stamp out prion disease. ( 28385963
)
|
Stokstad E.
|
2017 |
| 25 |
Therapeutic effect of autologous compact bone-derived mesenchymal stem cell transplantation on prion disease. ( 28874230
)
|
Shan Z....Horiuchi M.
|
2017 |
| 26 |
Oral Prion Disease Pathogenesis Is Impeded in the Specific Absence of CXCR5-Expressing Dendritic Cells. ( 28275192
)
|
Bradford B.M....Mabbott N.A.
|
2017 |
| 27 |
Genetic PrP Prion Diseases. ( 28778873
)
|
Kim M.O....Geschwind M.D.
|
2017 |
| 28 |
A multidisciplinary medical network approach is crucial for increasing the number of autopsies for prion disease [Reply to: How can we increase the numbers of autopsies for prion disease? A model system in Japan]. ( 28477717
)
|
Hayashi Y....Inuzuka T.
|
2017 |
| 29 |
Prion disease: 'Anti-prions' block prion disease onset. ( 28685760
)
|
Ridler C.
|
2017 |
| 30 |
Quick and sensitive SPR detection of prion disease-associated isoform (PrP(Sc)) based on its self-assembling behavior on bare gold film and specific interactions with aptamer-graphene oxide (AGO). ( 28570989
)
|
Lou Z....Gu N.
|
2017 |
| 31 |
RT-QuIC Assays for Prion Disease Detection and Diagnostics. ( 28861791
)
|
OrrA^ C.D....Caughey B.
|
2017 |
| 32 |
Genetic human prion disease modelled in PrP transgenic Drosophila. ( 28814578
)
|
Thackray A.M....Bujdoso R.
|
2017 |
| 33 |
Neuroanatomical correlates of prion disease progression - a 3T longitudinal voxel-based morphometry study. ( 27942451
)
|
De Vita E....Hyare H.
|
2017 |
| 34 |
Age and Environment Influences on Mouse Prion Disease Progression: Behavioral Changes and Morphometry and Stereology of Hippocampal Astrocytes. ( 28243355
)
|
Bento-Torres J....PicanAso Diniz C.W.
|
2017 |
| 35 |
Genetic Prion Disease Caused by PRNP Q160X Mutation Presenting with an Orbitofrontal Syndrome, Cyclic Diarrhea, and Peripheral Neuropathy. ( 27716661
)
|
Fong J.C....Geschwind M.D.
|
2017 |
| 36 |
Prion disease pathogenesis in the absence of the commensal microbiota. ( 28708055
)
|
Bradford B.M....Mabbott N.A.
|
2017 |
| 37 |
Correction: Fatal Prion Disease in a Mouse Model of Genetic E200K Creutzfeldt-Jakob Disease. ( 28467504
)
|
Friedman-Levi Y....Gabizon R.
|
2017 |
| 38 |
Prion disease: experimental models and reality. ( 28084518
)
|
Brandner S....Jaunmuktane Z.
|
2017 |
| 39 |
Analysis of miRNA Signatures in Neurodegenerative Prion Disease. ( 28861783
)
|
Bellingham S.A....Hill A.F.
|
2017 |
| 40 |
Prion disease: AI^ pathology in human growth hormone recipients. ( 28418021
)
|
Wood H.
|
2017 |
| 41 |
Disease-associated protein seeding suggests a dissociation between misfolded protein accumulation and neurodegeneration in prion disease. ( 29023184
)
|
Alibhai J....Manson J.
|
2017 |
| 42 |
Treatment with a non-toxic, self-replicating anti-prion delays or prevents prion disease in vivo. ( 28630454
)
|
Diaz-Espinoza R....Soto C.
|
2017 |
| 43 |
Genetic prion disease: Experience of a rapidly progressive dementia center in the United States and a review of the literature. ( 27943639
)
|
Takada L.T....Geschwind M.D.
|
2017 |
| 44 |
Correction: Increased Abundance of M Cells in the Gut Epithelium Dramatically Enhances Oral Prion Disease Susceptibility. ( 28212438
)
|
|
2017 |
| 45 |
Increased circulating microRNAs miR-342-3p and miR-21-5p in natural sheep prion disease. ( 27959774
)
|
Sanz Rubio D....Toivonen J.M.
|
2016 |
| 46 |
Diagnosis of Human Prion Disease Using Real-Time Quaking-Induced Conversion Testing of Olfactory Mucosa and Cerebrospinal Fluid Samples. ( 27942718
)
|
Bongianni M....Zanusso G.
|
2016 |
| 47 |
C-Terminal-Deleted Prion Protein Fragment Is a Major Accumulated Component of Systemic PrP Deposits in Hereditary Prion Disease With a 2-Bp (CT) Deletion in PRNP Codon 178. ( 27634965
)
|
Honda H....Iwaki T.
|
2016 |
| 48 |
MicroRNA abundance is altered in synaptoneurosomes during prion disease. ( 26658803
)
|
Boese A.S....Booth S.A.
|
2016 |
| 49 |
Positive 14-3-3 and tau proteins in a sporadic Creutzfeldt-Jakob disease case and a brief perspective of prion diseases in Colombia. ( 27622622
)
|
EscandA^n-Vargas K....Corral-Prado R.H.
|
2016 |
| 50 |
Prion 2016 Animal Prion Disease Workshop Abstracts. ( 27088807
)
|
|
2016 |
