| 1 |
Kuru, the First Human Prion Disease. ( 30866511
)
|
Liberski PP...Lindenbaum S
|
2019 |
| 2 |
Cellular and Molecular Mechanisms of Prion Disease. ( 30355150
)
|
Sigurdson CJ...Glatzel M
|
2019 |
| 3 |
GPI-anchor signal sequence influences PrPC sorting, shedding and signalling, and impacts on different pathomechanistic aspects of prion disease in mice. ( 30608982
)
|
Puig B...Glatzel M
|
2019 |
| 4 |
Neuroinflammation, Microglia, and Cell-Association during Prion Disease. ( 30650564
)
|
Carroll JA...Chesebro B
|
2019 |
| 5 |
Early neurophysiological biomarkers and spinal cord pathology in inherited prion disease. ( 30698738
)
|
Rudge P...Mead S
|
2019 |
| 6 |
The cell type resolved mouse transcriptome in neuron-enriched brain tissues from the hippocampus and cerebellum during prion disease. ( 30705335
)
|
Majer A...Booth SA
|
2019 |
| 7 |
Unaltered prion disease in mice lacking developmental endothelial locus-1. ( 30743056
)
|
Zhu C...Aguzzi A
|
2019 |
| 8 |
SARM1 deficiency up-regulates XAF1, promotes neuronal apoptosis, and accelerates prion disease. ( 30842236
)
|
Zhu C...Aguzzi A
|
2019 |
| 9 |
Experimental models to study prion disease pathogenesis and identify potential therapeutic compounds. ( 30878006
)
|
Vorberg I...Chiesa R
|
2019 |
| 10 |
The First Report of Polymorphisms and Genetic Features of the prion-like Protein Gene (PRND) in a Prion Disease-Resistant Animal, Dog. ( 30897750
)
|
Won SY...Jeong BH
|
2019 |
| 11 |
Oxidative and Inflammatory Events in Prion Diseases: Can They Be Therapeutic Targets? ( 30636622
)
|
Prasad KN...Bondy SC
|
2019 |
| 12 |
Prions Strongly Reduce NMDA Receptor S-Nitrosylation Levels at Pre-symptomatic and Terminal Stages of Prion Diseases. ( 30710214
)
|
Meneghetti E...Legname G
|
2019 |
| 13 |
A Single Amino Acid Substitution, Found in Mammals with Low Susceptibility to Prion Diseases, Delays Propagation of Two Prion Strains in Highly Susceptible Transgenic Mouse Models. ( 30847740
)
|
Otero A...Castilla J
|
2019 |
| 14 |
A new drug to treat prion diseases. ( 30858584
)
|
Le Bras A
|
2019 |
| 15 |
Feasibility of Remote Assessment of Human Prion Diseases for Research and Surveillance. ( 30861521
)
|
Appleby BS...Mahajan S
|
2019 |
| 16 |
Twenty-year-old African American woman with prion disease associated with the G114V <i>PRNP</i> variant. ( 29577079
)
|
Margolesky J....Saporta M.
|
2018 |
| 17 |
Microglia Are Critical in Host Defense Against Prion Disease. ( 29769333
)
|
Carroll J.A....Chesebro B.
|
2018 |
| 18 |
Prion disease: Skin is a source of infectious prions in sCJD. ( 29217825
)
|
Starling S.
|
2018 |
| 19 |
Autologous neural progenitor cell transplantation into newborn mice modeling for E200K genetic prion disease delays disease progression. ( 29494865
)
|
Frid K....Gabizon R.
|
2018 |
| 20 |
|
Takada L.T....Geschwind M.D.
|
2018 |
| 21 |
Presumptive BSE cases with an aberrant prion protein phenotype in Switzerland, 2011: Lack of prion disease in experimentally inoculated cattle and bovine prion protein transgenic mice. ( 29675959
)
|
Serra F....Seuberlich T.
|
2018 |
| 22 |
Acute Neurotoxicity Models of Prion Disease. ( 29393619
)
|
T Islam A.M....Collins S.J.
|
2018 |
| 23 |
Efficient prion disease transmission through common environmental materials. ( 29330304
)
|
Pritzkow S....Soto C.
|
2018 |
| 24 |
Prion disease: Dramatic increases in blood levels of tau and neurofilament light in patients with prion disease. ( 29545623
)
|
Ridler C.
|
2018 |
| 25 |
Cerebrospinal Fluid Prion Disease Biomarkers in Pre-clinical and Clinical Naturally Occurring Scrapie. ( 29572672
)
|
Llorens F....Zerr I.
|
2018 |
| 26 |
MicroRNA-16 targets mRNA involved in neurite extension and branching in hippocampal neurons during presymptomatic prion disease. ( 29277556
)
|
Burak K....Booth S.A.
|
2018 |
| 27 |
Chronic wasting disease: an evolving prion disease of cervids. ( 29887133
)
|
Benestad S.L....Telling G.C.
|
2018 |
| 28 |
Prion Disease in Dromedary Camels, Algeria. ( 29652245
)
|
Babelhadj B....Vaccari G.
|
2018 |
| 29 |
Alterations in neuronal metabolism contribute to the pathogenesis of prion disease. ( 29915278
)
|
Bourgognon J.M....Steinert J.R.
|
2018 |
| 30 |
The language disorder of prion disease is characteristic of a dynamic aphasia and is rarely an isolated clinical feature. ( 29304167
)
|
Caine D....Mead S.
|
2018 |
| 31 |
Prion diseases with a focus on Creutzfeldt-Jakob disease, a summary of the incidence of Creutzfeldt-Jakob disease in the Czech Republic over the last 17 years, 2000-2017. ( 30630318
)
|
Kol??ov? K...Kyn?l J
|
2018 |
| 32 |
Co-occurrence of chronic traumatic encephalopathy and prion disease. ( 30563563
)
|
Nemani SK...Gambetti P
|
2018 |
| 33 |
MicroRNA Alterations in the Brain and Body Fluids of Humans and Animal Prion Disease Models: Current Status and Perspectives. ( 30083102
)
|
Kanata E...Llorens F
|
2018 |
| 34 |
Post-mortem magnetic resonance imaging in patients with suspected prion disease: Pathological confirmation, sensitivity, specificity and observer reliability. A national registry. ( 30086144
)
|
Gibson LM...Wardlaw JM
|
2018 |
| 35 |
Application of the fragment molecular orbital method to discover novel natural products for prion disease. ( 30166585
)
|
Choi J...Sohn HJ
|
2018 |
| 36 |
Muskelin Coordinates PrPC Lysosome versus Exosome Targeting and Impacts Prion Disease Progression. ( 30174115
)
|
Heisler FF...Kneussel M
|
2018 |
| 37 |
Structural basis for the complete resistance of the human prion protein mutant G127V to prion disease. ( 30181558
)
|
Zheng Z...Lin D
|
2018 |
| 38 |
The most problematic symptoms of prion disease - an analysis of carer experiences. ( 30353798
)
|
Ford L...Mead S
|
2018 |
| 39 |
Mitochondrial dysfunction in preclinical genetic prion disease: A target for preventive treatment? ( 30423473
)
|
Keller G...Gabizon R
|
2018 |
| 40 |
Therapeutic strategies for prion disease: a practical perspective. ( 30508662
)
|
Appleby BS...Wang H
|
2018 |
| 41 |
Ganglioside Synthase Knockout Reduces Prion Disease Incubation Time in Mouse Models. ( 30553837
)
|
Kobayashi A...Miyoshi I
|
2018 |
| 42 |
Recent advances in the histo-molecular pathology of human prion disease. ( 30588685
)
|
Baiardi S...Parchi P
|
2018 |
| 43 |
Toll-like receptor 2 confers partial neuroprotection during prion disease. ( 30596651
)
|
Carroll JA...Chesebro B
|
2018 |
| 44 |
Stimulations of the Culture Medium of Activated Microglia and TNF-Alpha on a Scrapie-Infected Cell Line Decrease the Cell Viability and Induce Marked Necroptosis That Also Occurs in the Brains from the Patients of Human Prion Diseases. ( 30399321
)
|
Ma Y...Dong XP
|
2018 |
| 45 |
Lysosomal Quality Control in Prion Diseases. ( 28421536
)
|
Majumder P...Chakrabarti O
|
2018 |
| 46 |
Myelin Basic Protein Citrullination, a Hallmark of Central Nervous System Demyelination, Assessed by Novel Monoclonal Antibodies in Prion Diseases. ( 28470584
)
|
Jang B...Choi EK
|
2018 |
| 47 |
Toward Therapy of Human Prion Diseases. ( 28961066
)
|
Aguzzi A...Frontzek K
|
2018 |
| 48 |
Translational Research in Alzheimer's and Prion Diseases. ( 29172000
)
|
Di Fede G...Tagliavini F
|
2018 |
| 49 |
An Amino Acid Substitution Found in Animals with Low Susceptibility to Prion Diseases Confers a Protective Dominant-Negative Effect in Prion-Infected Transgenic Mice. ( 29264770
)
|
Otero A...Castilla J
|
2018 |
| 50 |
Development of a quick bioassay for the evaluation of transmission properties of acquired prion diseases. ( 29329906
)
|
Munesue Y...Kobayashi A
|
2018 |
