MCID: PLM004
MIFTS: 28

Pulmonary Artery Leiomyosarcoma

Categories: Cancer diseases, Cardiovascular diseases, Muscle diseases, Respiratory diseases

Aliases & Classifications for Pulmonary Artery Leiomyosarcoma

MalaCards integrated aliases for Pulmonary Artery Leiomyosarcoma:

Name: Pulmonary Artery Leiomyosarcoma 12 15 70
Leiomyosarcoma of the Pulmonary Artery 12

Classifications:



External Ids:

Disease Ontology 12 DOID:7389
NCIt 50 C5373
UMLS 70 C1335572

Summaries for Pulmonary Artery Leiomyosarcoma

Disease Ontology : 12 A leiomyosarcoma that is located in the pulmonary artery.

MalaCards based summary : Pulmonary Artery Leiomyosarcoma, also known as leiomyosarcoma of the pulmonary artery, is related to lung leiomyosarcoma and leiomyosarcoma. An important gene associated with Pulmonary Artery Leiomyosarcoma is CD68 (CD68 Molecule), and among its related pathways/superpathways are Hematopoietic Stem Cell Differentiation Pathways and Lineage-specific Markers and Staphylococcus aureus infection. Affiliated tissues include pulmonary artery and thyroid, and related phenotype is respiratory system.

Related Diseases for Pulmonary Artery Leiomyosarcoma

Diseases related to Pulmonary Artery Leiomyosarcoma via text searches within MalaCards or GeneCards Suite gene sharing:

(show top 50) (show all 332)
# Related Disease Score Top Affiliating Genes
1 lung leiomyosarcoma 30.0 KRT7 CD34
2 leiomyosarcoma 10.6
3 epidermolytic acanthoma 10.3 KRT10 CD68
4 small intestinal sarcoma 10.3 CD68 ANO1
5 perforated corneal ulcer 10.3 PLG CD68
6 glomangioma 10.3 PECAM1 CD34
7 skin epithelioid hemangioma 10.3 PECAM1 CD34
8 aortic malignant tumor 10.3 PECAM1 CD34
9 prostate angiosarcoma 10.3 PECAM1 CD34
10 central nervous system angiosarcoma 10.3 PECAM1 CD34
11 intravascular angioleiomyoma 10.3 PECAM1 CD34
12 central nervous system hemangioma 10.3 PECAM1 CD34
13 heart fibrosarcoma 10.3 PECAM1 CD34
14 ovarian angiosarcoma 10.3 PECAM1 CD34
15 conventional angiosarcoma 10.3 PECAM1 CD34
16 thyroid sarcoma 10.3 PECAM1 CD34
17 pediatric angiosarcoma 10.3 PECAM1 CD34
18 glomangiosarcoma 10.3 PECAM1 CD34
19 hemangioma of spleen 10.3 PECAM1 CD34
20 intramuscular hemangioma 10.3 PECAM1 CD34
21 liposarcoma of bone 10.3 PECAM1 CD34
22 benign perivascular tumor 10.3 PECAM1 CD34
23 hobnail hemangioma 10.3 PECAM1 CD34
24 breast angiosarcoma 10.3 PECAM1 CD34
25 erythema elevatum diutinum 10.3 PECAM1 CD34
26 kaposiform hemangioendothelioma 10.3 PECAM1 CD34
27 cutaneous leiomyosarcoma 10.3 CD68 CD34
28 heart sarcoma 10.3 PECAM1 CD34
29 capillary lymphangioma 10.3 PECAM1 CD34
30 pleomorphic lipoma 10.3 CD68 CD34
31 bacillary angiomatosis 10.3 PECAM1 CD34
32 subungual glomus tumor 10.2 PECAM1 CD34
33 thyroid angiosarcoma 10.2 PECAM1 CD34
34 extraosseous osteosarcoma 10.2 CD68 CD34
35 lymphangiosarcoma 10.2 PECAM1 CD34
36 heart lymphoma 10.2 MME CD68
37 small intestine leiomyosarcoma 10.2 CD34 ANO1
38 parasagittal meningioma 10.2 CD34 ANO1
39 angiokeratoma circumscriptum 10.2 PECAM1 CD34
40 gastric liposarcoma 10.2 CD34 ANO1
41 histiocytoid hemangioma 10.2 PECAM1 CD34
42 deep leiomyoma 10.2 CD34 ANO1
43 hemangioendothelioma 10.2 PLG CD34
44 colon leiomyosarcoma 10.2 CD34 ANO1
45 t-cell/histiocyte rich large b cell lymphoma 10.2 MME CD68
46 angiolipoma 10.2 PECAM1 CD34
47 small intestine leiomyoma 10.2 CD34 ANO1
48 epithelioid neurofibroma 10.2 CD34 B3GAT1
49 retroperitoneal leiomyosarcoma 10.2 CD34 ANO1
50 malignant giant cell tumor of soft parts 10.2 CD68 CD34

Graphical network of the top 20 diseases related to Pulmonary Artery Leiomyosarcoma:



Diseases related to Pulmonary Artery Leiomyosarcoma

Symptoms & Phenotypes for Pulmonary Artery Leiomyosarcoma

MGI Mouse Phenotypes related to Pulmonary Artery Leiomyosarcoma:

46
# Description MGI Source Accession Score Top Affiliating Genes
1 respiratory system MP:0005388 9.1 ANO1 ENO2 GRP KRT19 PECAM1 PLG

Drugs & Therapeutics for Pulmonary Artery Leiomyosarcoma

Search Clinical Trials , NIH Clinical Center for Pulmonary Artery Leiomyosarcoma

Genetic Tests for Pulmonary Artery Leiomyosarcoma

Anatomical Context for Pulmonary Artery Leiomyosarcoma

The Foundational Model of Anatomy Ontology organs/tissues related to Pulmonary Artery Leiomyosarcoma:

19
Pulmonary Artery

MalaCards organs/tissues related to Pulmonary Artery Leiomyosarcoma:

40
Thyroid

Publications for Pulmonary Artery Leiomyosarcoma

Articles related to Pulmonary Artery Leiomyosarcoma:

(show top 50) (show all 58)
# Title Authors PMID Year
1
Pulmonary artery leiomyosarcoma: A clinical dilemma. 61
29487255 2018
2
Pulmonary Artery Leiomyosarcoma Diagnosed by Magnetic Resonance, PET-CT and EBUS-TBNA. 61
28314632 2017
3
[Pulmonary artery leiomyosarcoma: Uncommon and difficult to diagnose]. 61
25983202 2016
4
Retracted: Pulmonary hypertension due to a pulmonary artery leiomyosarcoma: A case report. 61
26478736 2015
5
Treatment of a recurrent pulmonary artery leiomyosarcoma with a combination of surgery, chemotherapy, and radiotherapy: A case report and literature review. 61
25788998 2015
6
When a pulmonary embolism is not a pulmonary embolism: a rare case of primary pulmonary leiomyosarcoma. 61
26653696 2015
7
Leiomyosarcoma of the pulmonary artery diagnosed by endobronchial ultrasound-guided transbronchial needle aspiration. 61
25485274 2014
8
Pulmonary hypertension due to a pulmonary artery leiomyosarcoma: A case report. 61
25161682 2014
9
Pulmonary Hypertension due to a Pulmonary Artery Leiomyosarcoma: A Case Report. 61
23607029 2013
10
Primary leiomyosarcoma of the pulmonary artery: a case of a 20-month survivor after incomplete surgical resection. 61
22214627 2012
11
[The evaluation of combined CT pulmonary and bronchial arteriography for the diagnosis of hemoptysis]. 61
22455942 2012
12
Surgical treatment of pulmonary artery leiomyosarcoma: a good survival without adjuvant therapy. 61
22115240 2011
13
Pulmonary Artery Leiomyosarcoma Diagnosed without Delay. 61
21734884 2011
14
Pulmonary artery leiomyosarcoma: an unusual cause of shortness of breath. 61
19921308 2011
15
Pulmonary artery leiomyosarcoma successfully treated by right pneumonectomy. 61
19917796 2009
16
Thromboembolism in pulmonary artery sarcoma. 61
19300057 2009
17
[Primitive leiomyosarcoma of the pulmonary artery]. 61
17299372 2007
18
A unique case of pulmonary artery leiomyosarcoma. 61
17225849 2006
19
Primary leiomyosarcoma of the pulmonary artery: Is aggressive treatment justified for a long survival? 61
16872981 2006
20
[Pulmonary artery sarcoma during postpartum: CT findings]. 61
16788540 2006
21
Pulmonary artery leiomyosarcoma expressing Epstein-Barr virus in an immunocompetent individual. 61
16631703 2006
22
[Surgical treatment of leiomyosarcoma of the pulmonary artery under artificial circulation]. 61
16710245 2006
23
Pulmonary artery leiomyosarcoma with thyroid metastases. 61
15148841 2003
24
Primary pulmonary artery leiomyosarcoma. 61
12763557 2003
25
Primary leiomyosarcoma of the pulmonary artery: a diagnostic dilemma. 61
12727062 2003
26
[Primary leiomyosarcoma of pulmonary artery: a rare tumor mis-diagnosed as pulmonary embolism]. 61
12614857 2003
27
[Space occupying lesion of unknown origin in the pulmonary trunk: targeted differential diagnosis and surgical therapy in a patient with B symptoms and thoracic pain]. 61
12063706 2002
28
Leiomyosarcoma of the pulmonary artery--a diagnostic chameleon. 61
11675204 2001
29
[A case of primary leiomyosarcoma of the pulmonary artery]. 61
11828728 2001
30
Primary pulmonary artery leiomyosarcoma in an adult dog. 61
11105958 2000
31
Primary leiomyosarcoma of the pulmonary artery mimicking massive pulmonary thromboembolism. 61
11059620 2000
32
[Primary leiomyosarcoma of the pulmonary artery--a case report]. 61
10705756 2000
33
Pulmonary artery leiomyosarcoma. 61
10502913 1999
34
Leiomyosarcoma of the pulmonary artery. 61
9930499 1998
35
Primary leiomyosarcoma of the pulmonary artery confirmed by catheter suction biopsy. 61
9498986 1998
36
Death due to a leiomyosarcoma of the pulmonary artery. 61
8947357 1996
37
[Leiomyosarcoma of the pulmonary artery]. 61
8679722 1996
38
[Primary pulmonary artery sarcoma (e.g. spindle cell sarcoma of the pulmonary artery, pulmonary artery leiomyosarcoma)]. 61
9048105 1996
39
Primary leiomyosarcoma of the pulmonary artery: diagnostic and surgical implications. 61
8279900 1994
40
An autopsy case of pulmonary artery leiomyosarcoma. 61
8465660 1993
41
[Surgical treatment of primary cardiac tumors]. 61
1431401 1992
42
[Primary leiomyosarcoma of the pulmonary artery. Apropos of a case. Review of the literature]. 61
1285625 1992
43
Pulmonary homograft replacement for primary leiomyosarcoma of the pulmonary artery. 61
1513175 1992
44
Leiomyosarcoma of the pulmonary artery. 61
1570996 1992
45
Pulmonary artery leiomyosarcoma. 61
1947375 1991
46
[Leiomyosarcoma of the pulmonary artery. Apropos of a case]. 61
2514646 1989
47
[A case of leiomyosarcoma of the pulmonary artery]. 61
3272556 1988
48
[Leiomyosarcoma of the pulmonary artery--report of 2 cases from clinic practice and review of the literature]. 61
3062281 1988
49
[Primary leiomyosarcoma of the pulmonary artery. Apropos of a case]. 61
3122693 1987
50
Right intracavitary cardiac tumors. Surgical management. 61
3038781 1987

Variations for Pulmonary Artery Leiomyosarcoma

Expression for Pulmonary Artery Leiomyosarcoma

Search GEO for disease gene expression data for Pulmonary Artery Leiomyosarcoma.

Pathways for Pulmonary Artery Leiomyosarcoma

Pathways related to Pulmonary Artery Leiomyosarcoma according to GeneCards Suite gene sharing:

# Super pathways Score Top Affiliating Genes
1 11.2 MME CD68 CD34
2 10.78 PLG KRT19 KRT10
3 10.52 PLG MME

GO Terms for Pulmonary Artery Leiomyosarcoma

Cellular components related to Pulmonary Artery Leiomyosarcoma according to GeneCards Suite gene sharing:

# Name GO ID Score Top Affiliating Genes
1 extracellular exosome GO:0070062 9.23 PLG PECAM1 MME KRT7 KRT19 KRT10

Biological processes related to Pulmonary Artery Leiomyosarcoma according to GeneCards Suite gene sharing:

# Name GO ID Score Top Affiliating Genes
1 keratinization GO:0031424 9.33 KRT7 KRT19 KRT10
2 cornification GO:0070268 9.13 KRT7 KRT19 KRT10
3 glomerular endothelium development GO:0072011 8.62 PECAM1 CD34

Sources for Pulmonary Artery Leiomyosarcoma

3 CDC
7 CNVD
9 Cosmic
10 dbSNP
11 DGIdb
17 EFO
18 ExPASy
19 FMA
20 GARD
28 GO
29 GTR
30 HMDB
31 HPO
32 ICD10
33 ICD10 via Orphanet
34 ICD9CM
35 IUPHAR
36 KEGG
37 LifeMap
39 LOVD
41 MedGen
44 MeSH
45 MESH via Orphanet
46 MGI
49 NCI
50 NCIt
51 NDF-RT
53 NINDS
54 Novoseek
56 OMIM via Orphanet
57 OMIM® (Updated 05-Apr-2021)
61 PubMed
63 QIAGEN
68 SNOMED-CT via HPO
69 Tocris
70 UMLS
71 UMLS via Orphanet
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