MCID: PLM059
MIFTS: 29

Pulmonary Atresia with Ventricular Septal Defect

Categories: Cardiovascular diseases, Fetal diseases, Rare diseases

Aliases & Classifications for Pulmonary Atresia with Ventricular Septal Defect

MalaCards integrated aliases for Pulmonary Atresia with Ventricular Septal Defect:

Name: Pulmonary Atresia with Ventricular Septal Defect 56 52 58 36 6

Characteristics:

OMIM:

56
Inheritance:
autosomal dominant


HPO:

31
pulmonary atresia with ventricular septal defect:
Inheritance autosomal dominant inheritance


Classifications:

Orphanet: 58  
Rare cardiac malformations
Developmental anomalies during embryogenesis


External Ids:

OMIM 56 178370
KEGG 36 H01803
ICD10 via Orphanet 33 Q25.5
UMLS via Orphanet 72 C0344976
Orphanet 58 ORPHA1207
MedGen 41 C0344976

Summaries for Pulmonary Atresia with Ventricular Septal Defect

KEGG : 36 Pulmonary atresia with ventricular septal defect (PA-VSD) is a rare and complex cyanotic congenital heart malformation that has a high incidence of early mortality. PA-VSD presents with complete absence of any communication between the right ventricle and the pulmonary arteries. The blood supply to the pulmonary arteries is provided by a patent arterial duct or by major aorto pulmonary collateral arteries (MAPCAs). Two-thirds of the cases with pulmonary atresia are associated with MAPCAs, which can vary greatly in number and site of origin. PA-VSD shares similarities with tetralogy of Fallot (TOF) and has been considered a severe end of the spectrum of TOF. Although surgical interventions have been employed successfully for a number of years, the long-term prognosis has remained poor with an increased incidence of sudden death. An association between conotruncal cardiac abnormalities and 22q11.2 deletion during fetal life has been investigated and reported to occur in 20% of cases of PA-VSD.

MalaCards based summary : Pulmonary Atresia with Ventricular Septal Defect is related to conotruncal heart malformations and ventricular septal defect. An important gene associated with Pulmonary Atresia with Ventricular Septal Defect is FOXP1 (Forkhead Box P1). Affiliated tissues include heart, lung and thymus, and related phenotypes are ventricular septal defect and pulmonary artery atresia

NIH Rare Diseases : 52 The following summary is from Orphanet , a European reference portal for information on rare diseases and orphan drugs. Orpha Number: 1207 Definition Pulmonary atresia with ventricular septal defect (PA-VSD) is a rare cyanotic congenital heart malformation characterized by underdevelopment of the right ventricular outflow tract and atresia of the pulmonary valve, ventricular septal defect (VSD) and pulmonary collateral vessels. Clinical features depend on the anatomic variability of the lesion and patients may be minimally symptomatic, severely cyanotic or may develop congestive heart failure. PA-VSD may represent a severe form of Tetralogy of Fallot (see this term). Visit the Orphanet disease page for more resources.

More information from OMIM: 178370

Related Diseases for Pulmonary Atresia with Ventricular Septal Defect

Diseases related to Pulmonary Atresia with Ventricular Septal Defect via text searches within MalaCards or GeneCards Suite gene sharing:

(showing 47, show less)
# Related Disease Score Top Affiliating Genes
1 conotruncal heart malformations 11.9
2 ventricular septal defect 11.3
3 heart septal defect 11.3
4 tetralogy of fallot 10.7
5 patent ductus arteriosus 1 10.5
6 cyanosis, transient neonatal 10.5
7 aortic valve insufficiency 10.5
8 single ventricular heart 10.5
9 digeorge syndrome 10.3
10 velocardiofacial syndrome 10.3
11 congestive heart failure 10.3
12 aortopulmonary window 10.3
13 right aortic arch 10.3
14 persistent fifth aortic arch 10.3
15 cardiac conduction defect 10.1
16 pulmonary arteriovenous fistulas 10.1
17 tricuspid atresia 10.1
18 pulmonary hypertension 10.1
19 visceral heterotaxy 10.1
20 atrioventricular block 10.1
21 infective endocarditis 10.1
22 cardiac arrest 10.1
23 dextro-looped transposition of the great arteries 10.1
24 respiratory failure 10.1
25 arteriovenous malformation 10.1
26 eclampsia 10.1
27 amenorrhea 10.1
28 pulmonary valve insufficiency 10.1
29 capillary leak syndrome 10.1
30 pneumothorax 10.1
31 vascular disease 10.1
32 atrial heart septal defect 10.1
33 dental caries 10.1
34 acute kidney failure 10.1
35 tricuspid valve insufficiency 10.1
36 infertility 10.1
37 placental abruption 10.1
38 heterotaxy 10.1
39 47,xyy 10.1
40 athetosis 10.1
41 congenitally corrected transposition of the great arteries 10.1
42 double discordia 10.1
43 mitral atresia 10.1
44 pulmonary arteriovenous malformation 10.1
45 pulmonary sequestration 10.1
46 univentricular heart 10.1
47 monosomy 22 10.1

Graphical network of the top 20 diseases related to Pulmonary Atresia with Ventricular Septal Defect:



Diseases related to Pulmonary Atresia with Ventricular Septal Defect

Symptoms & Phenotypes for Pulmonary Atresia with Ventricular Septal Defect

Human phenotypes related to Pulmonary Atresia with Ventricular Septal Defect:

31 (showing 2, show less)
# Description HPO Frequency HPO Source Accession
1 ventricular septal defect 31 HP:0001629
2 pulmonary artery atresia 31 HP:0004935

Symptoms via clinical synopsis from OMIM:

56
Cardiovascular Heart:
ventricular septal defect

Respiratory Lung:
pulmonary atresia

Clinical features from OMIM:

178370

Drugs & Therapeutics for Pulmonary Atresia with Ventricular Septal Defect

Interventional clinical trials:

(showing 4, show less)
# Name Status NCT ID Phase Drugs
1 Femoral Allogenic Vein Valved Conduit for Palliative Repair of Pulmonary Atresia With Ventricular Septal Defect Completed NCT02861963
2 Management of Prenatally Diagnosed Isolated Right Aortic Arch: the ARCADE Study Completed NCT04029064
3 Congenital Heart Disease (CHD): Hemodynamic Effects of Acute Maternal Hyperoxygenation in the Fetus Recruiting NCT03944837
4 A Review of the Diagnosis, Treatment and Outcomes of Children With Critical Congenital Heart Defects Terminated NCT00208689

Search NIH Clinical Center for Pulmonary Atresia with Ventricular Septal Defect

Genetic Tests for Pulmonary Atresia with Ventricular Septal Defect

Anatomical Context for Pulmonary Atresia with Ventricular Septal Defect

MalaCards organs/tissues related to Pulmonary Atresia with Ventricular Septal Defect:

40
Heart, Lung, Thymus

Publications for Pulmonary Atresia with Ventricular Septal Defect

Articles related to Pulmonary Atresia with Ventricular Septal Defect:

(showing 367, show less)
# Title Authors PMID Year
1
Familial pulmonary atresia. Its occurrence with a ventricular septal defect. 56
7377161 1980
2
Tetralogy of Fallot or Pulmonary Atresia with Ventricular Septal Defect after the Age of 40 Years: A Single Center Study. 61
32438748 2020
3
Surgical Options for Pulmonary Atresia with Ventricular Septal Defect in Neonates and Young Infants. 61
32377890 2020
4
22q11.2 deletion syndrome is associated with increased mortality in adults with tetralogy of Fallot and pulmonary atresia with ventricular septal defect. 61
32145937 2020
5
Complete repair with unifocalization of the only unilateral lung. 61
30875003 2020
6
The prevalence of genetic diagnoses in fetuses with severe congenital heart defects. 61
32341573 2020
7
Midline unifocalization for pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries. 61
32274207 2020
8
Current era outcomes of pulmonary atresia with ventricular septal defect: A single center cohort in Thailand. 61
32198468 2020
9
Novel JAG1 Deletion Variant in Patient with Atypical Alagille Syndrome. 61
31835735 2019
10
Imaging of Pulmonary Atresia With Ventricular Septal Defect. 61
31738213 2019
11
Fetal pulmonary atresia with ventricular septal defect: Features, associations, and outcome in fetuses with different pulmonary circulation supply types. 61
31351012 2019
12
Lecompte Procedure for Relief of Severe Airway Compression in Children With Congenital Heart Disease. 61
31496414 2019
13
Perfusion Methods and Modifications to the Cardiopulmonary Bypass Circuit for Midline Unifocalization Procedures. 61
31548736 2019
14
A Review of the Management of Pulmonary Atresia, Ventricular Septal Defect, and Major Aortopulmonary Collateral Arteries. 61
30831109 2019
15
Surgical results of unifocalization revision. 61
30982588 2019
16
Measurement of Residual Collateral Flow in Pulmonary Atresia With Major Aortopulmonary Collaterals. 61
30928554 2019
17
Catheterization Performed in the Early Postoperative Period After Congenital Heart Surgery in Children. 61
30830282 2019
18
Rare Copy Number Variations Might Not be Involved in the Molecular Pathogenesis of PA-IVS in an Unselected Chinese Cohort. 61
30868185 2019
19
[Joint Cardiovascular Surgeries of Two Hospitals in Shizuoka for Adult Congenital Heart Disease (ACHD) Patients]. 61
31266915 2019
20
Utilisation of a three-dimensional printed model for the management of coronary-pulmonary artery fistula from left main coronary artery. 61
30764888 2019
21
Pulmonary Atresia with Ventricular Septal Defect: Rare Presentation with Coronary-to-Pulmonary Artery Collaterals from Both Right and Left Coronaries. 61
30917743 2019
22
Identification of Rare Copy Number Variants Associated With Pulmonary Atresia With Ventricular Septal Defect. 61
30745907 2019
23
Analysis of achieving an "ideal" outcome following midline unifocalization. 61
30417684 2019
24
Prenatal Diagnosis and Postnatal Outcome of Fetuses with Pulmonary Atresia and Ventricular Septal Defect. 61
30616264 2019
25
Early Childhood Inpatient Costs of Critical Congenital Heart Disease. 61
30268400 2018
26
Correction to: Anatomy of the retro-oesophageal major aortopulmonary collateral arteries in patients with pulmonary atresia with ventricular septal defect: results from preoperative CTA. 61
29744640 2018
27
Catheter, MRI and CT Imaging in Newborns with Pulmonary Atresia with Ventricular Septal Defect and Aortopulmonary Collaterals: Quantifying the Risks of Radiation Dose and Anaesthetic Time. 61
29744658 2018
28
Impact of Phrenic Nerve Palsy and Need for Diaphragm Plication Following Surgery for Pulmonary Atresia With Ventricular Septal Defect and Major Aortopulmonary Collaterals. 61
29545034 2018
29
Live-Born Major Congenital Heart Disease in Denmark: Incidence, Detection Rate, and Termination of Pregnancy Rate From 1996 to 2013. 61
30027209 2018
30
Collateral benefit in pulmonary atresia with ventricular septal defect? 61
29753507 2018
31
Pulmonary atresia with ventricular septal defect and major aortopulmonary collaterals: collateral vessel disease burden and unifocalisation strategies. 61
29978776 2018
32
Surgical algorithm and results for repair of pulmonary atresia with ventricular septal defect and major aortopulmonary collaterals. 61
29789151 2018
33
Repair of Ductus or Hemi-Truncus to One Lung and Major Aortopulmonary Collaterals to the Other Lung. 61
29684371 2018
34
Outcome of neonatal palliative procedure for pulmonary atresia with ventricular septal defect or tetralogy of Fallot with severe pulmonary stenosis: experience in a single tertiary center. 61
30032587 2018
35
Anatomy of the retro-oesophageal major aortopulmonary collateral arteries in patients with pulmonary atresia with ventricular septal defect: results from preoperative CTA. 61
29305732 2018
36
An analysis of patients requiring unifocalization revision following midline unifocalization for pulmonary atresia with ventricular septal defect and major aortopulmonary collaterals. 61
29447337 2018
37
Surgical strategies for pulmonary atresia with ventricular septal defect associated with major aortopulmonary collateral arteries. 61
29802565 2018
38
Aortopulmonary window with pumonary atresia with ventricular septal defect with D-transposition of great arteries: extremely rare anomaly. 61
29898907 2018
39
Prenatal diagnosis of pulmonary atresia with ventricular septal defect. 61
28752252 2018
40
One-stage definitive repair of complete atrioventricular septal defect and pulmonary atresia with major aortopulmonary collateral arteries. 61
29049668 2018
41
The value of dual-source multidetector-row computed tomography in determining pulmonary blood supply in patients with pulmonary atresia with ventricular septal defect. 61
28703845 2018
42
Tei Index Is the Best Echocardiographic Parameter for Assessing Right Ventricle Function in Patients With Unrepaired Congenital Heart Diseases With Outflow Tract Obstruction. 61
29998090 2018
43
Role of computed tomography angiography in the differentiation of feline truncus arteriosus communis from pulmonary atresia with ventricular septal defect. 61
29111286 2017
44
Impact of Pulmonary Flow Study Pressure on Outcomes After One-Stage Unifocalization. 61
28821333 2017
45
Determinants of Adverse Outcomes After Systemic-To-Pulmonary Shunts in Biventricular Circulation. 61
28870391 2017
46
Coronary-pulmonary arterial fistula in a neonate with pulmonary atresia-ventricular septal defect and single coronary artery. 61
28898455 2017
47
Major Aortopulmonary Collateral Arteries With Anatomy Other Than Pulmonary Atresia/Ventricular Septal Defect. 61
28527961 2017
48
Outcomes of palliative right ventricle to pulmonary artery connection for pulmonary atresia with ventricular septal defect. 61
28633393 2017
49
Significant survival advantage of high pulmonary vein index and the presence of native pulmonary artery in pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries: results from preoperative computed tomography angiography. 61
28369397 2017
50
Dental management of pediatric patients affected by pulmonary atresia with ventricular septal defect: A scoping review. 61
28624838 2017
51
Intraoperative Stenting of Pulmonary Artery Stenosis in Children With Congenital Heart Disease. 61
28274523 2017
52
Bilateral Coronary-Pulmonary Artery Fistulas in Pulmonary Atresia With Ventricular Septal Defect. 61
28496023 2017
53
Advances in molecular genetics for pulmonary atresia. 61
27655138 2017
54
Reconstruction of the pulmonary posterior wall using in situ autologous tissue for the treatment of pulmonary atresia with ventricular septal defect. 61
28231853 2017
55
Branch pulmonary artery peel operation in a patient without a native intrapericardial pulmonary artery. 61
28116756 2017
56
Pulmonary flow study predicts survival in pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries. 61
27692766 2016
57
Coronary-Pulmonary Artery Fistulas: A Systematic Review. 61
27768631 2016
58
Pulmonary Atresia with Ventricular Septal Defect and Major Aortopulmonary Collaterals Associated with Left Pulmonary Artery Interruption. 61
27733998 2016
59
Fungal infections in children in the early postoperative period after cardiac surgery for congenital heart disease: a single-centre experience. 61
27222000 2016
60
Outcomes of redo pulmonary valve replacement for bioprosthetic pulmonary valve failure in 61 patients with congenital heart disease. 61
26893380 2016
61
Polytetrafluoroethylene Bicuspid Pulmonary Valve Replacement: A 5-Year Experience in 119 Patients With Congenital Heart Disease. 61
27083247 2016
62
Reverse Szabo technique for stenting a single major aorto-pulmonary collateral vessel in pulmonary atresia with ventricular septal defect. 61
27709098 2016
63
Long-term outcome after treatment of pulmonary atresia with ventricular septal defect: nationwide study of 109 patients born in 1970-2007. 61
26620210 2016
64
An unusual case of left bronchial compression caused by a large patent arterial duct in a child with pulmonary atresia with ventricular septal defect. 61
26796364 2016
65
Pulmonary Valve Replacement With Balloon-Expandable Prosthesis Under Direct Vision: A Novel Therapeutic Approach. 61
27000579 2016
66
Double Aortic Arch Associated with Pulmonary Atresia with Ventricular Septal Defect. 61
27074277 2016
67
Complete Preoperative Evaluation of Pulmonary Atresia with Ventricular Septal Defect with Multi-Detector Computed Tomography. 61
26741649 2016
68
Pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries: primary repair. 61
26811506 2016
69
Accuracy of Fetal Echocardiography in the Differential Diagnosis between Truncus Arteriosus and Pulmonary Atresia with Ventricular Septal Defect. 61
26113195 2016
70
Prenatal differentiation between truncus arteriosus (Types II and III) and pulmonary atresia with ventricular septal defect. 61
25594532 2015
71
Reoperative double ventricular outflow tract reconstruction in grown-up congenital heart disease patients with conotruncal anomalies. 61
26342696 2015
72
An Overview of Pulmonary Atresia and Major Aortopulmonary Collateral Arteries. 61
26467877 2015
73
Right Ventricular Mass is Associated with Exercise Capacity in Adults with Repaired Tetralogy of Fallot. 61
25795311 2015
74
Implantation of an Absorb bioresorbable vascular scaffold in the stenotic aortopulmonary collateral artery of a young child with Alagille syndrome. 61
26011192 2015
75
Surgical Repair of Pulmonary Atresia With Ventricular Septal Defect and Major Aortopulmonary Collaterals With Absent Intrapericardial Pulmonary Arteries. 61
26138766 2015
76
Combination of double aortic arch and interruption of aortic arch in pulmonary atresia with ventricular septal defect. 61
25585494 2015
77
Spectrum of cyanotic congenital heart disease diagnosed by echocardiographic evaluation in patients attending paediatric cardiology clinic of a tertiary cardiac care centre. 61
24914874 2015
78
Fate of right ventricle to pulmonary artery conduits after complete repair of pulmonary atresia and major aortopulmonary collaterals. 61
25805573 2015
79
Right Ventricular Assessment in Adult Congenital Heart Disease Patients with Right Ventricle-to-Pulmonary Artery Conduits. 61
25648672 2015
80
[Epidemiology and outcome of Congolese children who had surgery for heart defects]. 61
26039583 2015
81
[Complex Congenital Heart Disease: The Influence of Prenatal Diagnosis]. 61
26061505 2015
82
[Initial experience with the new Pul-Stent in treating postoperative branch pulmonary artery stenosis]. 61
26165019 2015
83
A central shunt to rehabilitate diminutive pulmonary arteries in patients with pulmonary atresia with ventricular septal defect. 61
25454919 2015
84
Artery fistula causing aortic regurgitation in pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries. 61
25952246 2015
85
Pulmonary atresia with ventricular septal defect and major aortopulmonary collaterals: single-stage complete unifocalization. 61
26320215 2015
86
Bronchial arteries: anatomy, function, hypertrophy, and anomalies. 61
25590386 2015
87
Hybrid stent implantation to the pulmonary artery from peripheral access via recruited systemic-pulmonary shunt. 61
25848371 2015
88
One-stage surgical correction of congenital tracheal stenosis complicated with congenital heart disease in infants and young children. 61
25109422 2015
89
Disease-specific outcome analysis of palliation with the modified Blalock-Taussig shunt. 61
25548346 2015
90
Laterality defects in the national birth defects prevention study (1998-2007): birth prevalence and descriptive epidemiology. 61
25099286 2014
91
Congenital heart disease in 37,294 births in Tunisia: birth prevalence and mortality rate. 61
24103727 2014
92
Establishment of right ventricle-pulmonary artery continuity as the first-stage palliation in older infants with pulmonary atresia with ventricular septal defect may be preferable to use of an arterial shunt. 61
24686154 2014
93
Combined Rastelli and Bentall Procedures for Pulmonary Atresia With Ventricular Septal Defect and a Large Aortopulmonary Collateral Artery and Ascending Aorta Aneurysm. 61
24958054 2014
94
Infected pseudoaneurysm following a modified Blalock-Taussig shunt procedure. 61
24771741 2014
95
[Pulmonary atresia with ventricular septal defect and major aorto-pulmonary collateral arteries: diagnosis and treatment]. 61
25906654 2014
96
[Stent implantation for relief of pulmonary artery branch stenosis]. 61
24969934 2014
97
Early complete repair of pulmonary atresia with ventricular septal defect and major aortopulmonary collaterals. 61
24480261 2014
98
Neonatal right ventricle to pulmonary connection as a palliative procedure for pulmonary atresia with ventricular septal defect or severe tetralogy of Fallot. 61
24047707 2014
99
Use of femoral vein homograft for unifocalizing major aortopulmonary collateral arteries in a patient with pulmonary atresia with ventricular septal defect. 61
24075568 2014
100
A Rare Case of Pulmonary Atresia with Ventricular Septal Defect with a Right Sided Aortic Arch and a Calcified Pulmonary AVM Presenting in an Adult without Cyanosis. 61
25580345 2014
101
Hybrid intraoperative pulmonary artery stenting in redo congenital cardiac surgeries. 61
24581095 2014
102
Coronary artery to pulmonary artery communications in pulmonary atresia with ventricular septal defect. 61
24206891 2013
103
Prevalence of anomalous coronary arteries in pulmonary atresia with ventricular septal defect and major aortopulmonary collaterals. 61
23871887 2013
104
Pulmonary atresia with ventricular septal defect and pulmonary sequestration. 61
24570532 2013
105
Isolated cleft mitral valve with severe regurgitation resulting in a left inferior pulmonary vein varix diagnosed from cardiovascular magnetic resonance imaging. 61
23143311 2013
106
Hemodynamic assessment after complete repair of pulmonary atresia with major aortopulmonary collaterals. 61
23453744 2013
107
Volumetric and functional assessment using cardiac magnetic resonance imaging in young children exposed to acute pulmonary regurgitation: is pulmonary regurgitation just a long-term matter? 61
23356430 2013
108
Bicuspid pulmonary valve implantation using polytetrafluoroethylene membrane: early results and assessment of the valve function by magnetic resonance imaging. 61
22761492 2013
109
Hybrid procedure for pulmonary atresia with ventricular septal defect in a low birth weight neonate. 61
23423321 2013
110
[Results of surgical treatment of pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries]. 61
24738195 2013
111
Aortic root dilatation in adults with surgically repaired tetralogy of fallot: a multicenter cross-sectional study. 61
23224208 2013
112
Clinical results of combined palliative procedures for cyanotic congenital heart defects with intractable hypoplasia of pulmonary arteries. 61
23652050 2013
113
Pulmonary position cryopreserved homograft in non-Ross patients: how to improve the results? 61
22573719 2012
114
[Clinical value of ECG-gated dual-source computed tomography and angiography in assessing pulmonary atresia with ventricular septal defect]. 61
23469535 2012
115
Management of patients with pulmonary atresia, ventricular septal defect, hypoplastic pulmonary arteries and major aorto-pulmonary collaterals: Focus on the strategy of rehabilitation of the native pulmonary arteries. 61
23199622 2012
116
Contegra valved conduit in the paediatric population: an exciting prospect for right ventricle to pulmonary artery reconstruction; experience and outcomes at Aga Khan University. 61
23866464 2012
117
Unusual differential diagnosis of common arterial trunk. 61
22327230 2012
118
Late outcomes in patients undergoing aortopulmonary window for pulmonary atresia/stenosis and major aortopulmonary collaterals. 61
22857982 2012
119
Surgical outcomes for patients with pulmonary atresia/major aortopulmonary collaterals and Alagille syndrome. 61
22402453 2012
120
[Surgical strategy for pulmonary atresia with ventricular septal defect associated with severely hypoplastic or absent central pulmonary artery]. 61
22868427 2012
121
Pulmonary atresia with ventricular septal defect and multifocal pulmonary blood supply: does an intensive interventional approach improve the outcome? 61
22171603 2012
122
Detecting 22q11.2 deletion in Chinese children with conotruncal heart defects and single nucleotide polymorphisms in the haploid TBX1 locus. 61
22185286 2011
123
Longest survivor of pulmonary atresia with ventricular septal defect: well-developed major aortopulmonary collateral arteries demonstrated by multidetector computed tomography. 61
22064959 2011
124
Coronary artery-to-pulmonary artery fistula in a case of pulmonary atresia with ventricular septal defect. 61
21769503 2011
125
Fetal and post-natal diagnosis of major congenital heart disease: implications for medical and psychological care in the current era. 61
21449901 2011
126
Left pulmonary artery coarctoplasty by using the right pulmonary artery flap near the arterial duct. 61
21871324 2011
127
Atypical truncus arteriosus operated at 28 years of age: importance of differential diagnosis. 61
22002033 2011
128
Durability of bioprosthetic valves in the pulmonary position: long-term follow-up of 181 implants in patients with congenital heart disease. 61
21281951 2011
129
Left Main Coronary Artery Compression by Right Ventricle-to-Pulmonary Artery Conduit Relieved by Anterior Translocation of the Right Pulmonary Artery. 61
23804005 2011
130
A case of tetralogy of Fallot associated with left anterior descending coronary artery to pulmonary artery fistula. 61
21976889 2011
131
Surgical management of pulmonary atresia with ventricular septal defect: early total correction versus shunt. 61
21481840 2011
132
Surgical strategy for pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries. 61
21740761 2011
133
[The anatomy features and surgical significance of the pulmonary circuits of pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries]. 61
21733393 2011
134
Determinants of outcome after surgical treatment of pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries. 61
20850144 2010
135
Outcomes of spinal fusion in children with congenital heart disease. 61
20864851 2010
136
[Combined palliative procedures for cyanotic congenital heart defects with intractable hypoplasia of pulmonary arteries]. 61
21029625 2010
137
[Staged surgical treatment of pulmonary atresia with ventricular septal defect]. 61
20646509 2010
138
A novel two-stage complete repair method for pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries. 61
20193241 2010
139
Role of 64-MDCT in evaluation of pulmonary atresia with ventricular septal defect. 61
20028912 2010
140
Hospital mortality in surgery for reconstruction outflow right ventricle with pulmonary homograft. 61
20563464 2010
141
Unifocalization of major aortopulmonary collateral arteries in pulmonary atresia with ventricular septal defect is essential to achieve excellent outcomes irrespective of native pulmonary artery morphology. 61
19846121 2009
142
Completion angiography after cardiac surgery for congenital heart disease: complementing the intraoperative imaging modalities. 61
19629575 2009
143
Conotruncal anomalies in fetal life: accuracy of diagnosis, associated defects and outcome. 61
19481856 2009
144
[Changes of seral TNF-alpha, IL-6 and IL-10 level after implantation of valved bovine jugular vein conduit in complex congenital heart diseases]. 61
19662998 2009
145
Survival into sixth decade of untreated pulmonary atresia with ventricular septal defect and major aorto-pulmonary collaterals: a magnetic resonance imaging study. 61
19359994 2009
146
Transcatheter perforation followed by pulmonary valvuloplasty in neonates with pulmonary atresia and ventricular septal defect. 61
19520328 2009
147
[Results of surgical treatment of 1,387 infants under 6 months of age with congenital heart disease]. 61
19555560 2009
148
Appendectomy for an adult with cyanotic congenital heart disease. 61
19190564 2009
149
Surgical management of pulmonary atresia with ventricular septal defect and major aortopulmonary collaterals: a protocol-based approach. 61
19349030 2009
150
Sildenafil therapy in complex pulmonary atresia with pulmonary arterial hypertension. 61
18006164 2008
151
[Coexistence of partial anomalous pulmonary venous drainage and pulmonary atresia with ventricular septal defect: a report of two cases]. 61
19155649 2008
152
Foetal echocardiographic assessment of tetralogy of Fallot and post-natal outcome. 61
18467321 2008
153
Prenatal diagnosis of tetralogy of Fallot with pulmonary atresia. 61
18490232 2008
154
Pre-operative evaluation with magnetic resonance imaging in tetralogy of fallot and pulmonary atresia with ventricular septal defect. 61
18575288 2008
155
Diagnostic role of magnetic resonance imaging in identifying aortic arch anomalies. 61
18380760 2008
156
The first experience with the high-resolution multi-slice CT-angiography in pediatric cardiology in Slovakia. 61
18630806 2008
157
Coronary artery fistulas in pulmonary atresia and ventricular septal defect. 61
18245702 2008
158
Cardiac defects and results of cardiac surgery in 22q11.2 deletion syndrome. 61
18636635 2008
159
Twenty-year trends in diagnosis of life-threatening neonatal cardiovascular malformations. 61
17556383 2008
160
Evaluation of pulmonary atresia with 64-slice multidetector computed tomography (MDCT). 61
17894582 2007
161
Clinical results of staged repair with complete unifocalization for pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries. 61
17512210 2007
162
Radiofrequency perforation of the right ventricular outflow tract as a palliative strategy for pulmonary atresia with ventricular septal defect. 61
17377999 2007
163
[Rehabilitation of hypoplastic pulmonary arteries in pulmonary atresia with ventricular septal defect. Medium term results]. 61
17646768 2007
164
Annuloplasty of cryopreserved pulmonary homograft with Delrin stent in pulmonary atresia with ventricular septal defect. 61
17589616 2007
165
[Chemotherapy against polycythemia due to a cyanotic congenital heart disease in adults. One case report]. 61
17657936 2007
166
[Transfer of cardiac catheterisation from a paediatric to an adult cardiological centre: results at 3 years]. 61
17646764 2007
167
Early restenosis following biodegradable stent implantation in an aortopulmonary collateral of a patient with pulmonary atresia and hypoplastic pulmonary arteries. 61
17330269 2007
168
Successful use of a new Amplatzer Vascular plug for percutaneous closure of a large aortopulmonary collateral artery in a pulmonary atresia with ventricular septal defect prior to complete repair. 61
17052781 2007
169
Surgical management of pulmonary atresia with ventricular septal defect in late adolescence and adulthood. 61
17222560 2007
170
Right aortic arch detected in fetal life. 61
17086578 2006
171
[Role of interventional catheterization in adults with congenital heart disease]. 61
17171987 2006
172
Prenatally diagnosed pulmonary atresia with ventricular septal defect: echocardiography, genetics, associated anomalies and outcome. 61
16547205 2006
173
[Surgical treatments and results of pulmonary atresia with ventricular septal defect]. 61
17147878 2006
174
[The use of implantable cardioverter-defibrillators (ICD) in children and adolescents]. 61
16947095 2006
175
Unifocalization of major aortopulmonary collaterals in single-ventricle patients. 61
16928512 2006
176
The rapid prototyping of anatomic models in pulmonary atresia. 61
16872948 2006
177
Unifocalization and repair of pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries. 61
16801161 2006
178
Pregnancy after biventricular repair for pulmonary atresia with ventricular septal defect. 61
16828605 2006
179
Independent factors associated with mortality, reintervention, and achievement of complete repair in children with pulmonary atresia with ventricular septal defect. 61
16580535 2006
180
Correction of tetralogy of Fallot and of pulmonary atresia with ventricular septal defect in adults. 61
16305890 2005
181
Cardiovascular malformations among preterm infants. 61
16322141 2005
182
Normality of cardiopulmonary capacity in children operated on to correct congenital heart defects. 61
16275798 2005
183
Long-term outcome of right ventricular outflow tract reconstruction using a handmade tri-leaflet conduit. 61
15848318 2005
184
[Pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries]. 61
15966595 2005
185
[Medico-surgical treatment of occlusion of the left pulmonary artery by extension of ductal tissue (pulmonary coarctation)]. 61
15966593 2005
186
Clinical manifestations of Deletion 22q11.2 syndrome (DiGeorge/Velo-Cardio-Facial syndrome). 61
22368650 2005
187
Oversizing pulmonary homograft conduits does not significantly decrease allograft failure in children. 61
15784349 2005
188
Construction of a pulmonary artery pump for unifocalization and repair of pulmonary atresia with ventricular septal defect and major aortopulmonary collaterals. 61
15918448 2005
189
Pulmonary atresia with ventricular septal defect and an atypical duct. 61
25696288 2004
190
Laterality of the aortic arch and anomalies of the subclavian artery-reliable indicators for 22q11.2 deletion syndromes? 61
15300432 2004
191
Bovine valved xenograft in pulmonary position: medium-term follow-up with excellent hemodynamics and freedom from calcification. 61
15464502 2004
192
Dual-catheter balloon occlusion aortography in pulmonary atresia with ventricular septal defect and major aorto-pulmonary collaterals. 61
15185050 2004
193
[Quantitative structural study of pulmonary artery in patients with pulmonary atresia with ventricular septal defect ]. 61
15266823 2004
194
Stenting stenosed aortopulmonary collateral arteries in pulmonary atresia with ventricular septal defect. 61
15584570 2004
195
[Surgical treatment of pulmonary atresia with ventricular septal defect]. 61
15688819 2004
196
[Intermediate results of the integrated approach to pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries]. 61
15080532 2004
197
Primary repair of pulmonary atresia with ventricular septal defect and major aortopulmonary collaterals: a useful approach. 61
14752431 2004
198
Assessment of right ventricular fibrosis in different forms of pulmonary atresia with ventricular septal defect. 61
19641724 2004
199
Pulmonary atresia, ventricular septal defect, and multiple aorta pulmonary collateral arteries. 61
15283357 2004
200
Common arterial trunk in the fetus: characteristics, associations, and outcome in a multicentre series of 23 cases. 61
14617557 2003
201
Staged repair of pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries: experience with 104 patients. 61
14688682 2003
202
Management of Pulmonary Atresia with Ventricular Septal Defect. 61
12941209 2003
203
Deletion of chromosome 22q11.2 and outcome in patients with pulmonary atresia and ventricular septal defect. 61
12902105 2003
204
Infectious false aneurysm of the right ventricular outflow tract after repair of congenital heart defect treated with Freestyle aortic bioprosthesis. 61
17670002 2003
205
[Early complications of stenting in children and young adults with congenital heart disease]. 61
12838836 2003
206
Increasing experience with integrated approach to pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries. 61
12754024 2003
207
[Experience of implantation of prefitted Palmaz Corinthian stents]. 61
12838835 2003
208
Birthweight distribution in southern Chinese infants with symptomatic congenital heart disease. 61
12654142 2003
209
Absent or hypoplastic thymus on ultrasound: a marker for deletion 22q11.2 in fetal cardiac defects. 61
12493042 2002
210
Co-occurrence of chromosome 22q11.2 microdeletion and trisomy 21 mosaicism. 61
12239730 2002
211
Intermediate follow-up of a composite stentless porcine valved conduit of bovine pericardium in the pulmonary circulation. 61
12118743 2002
212
[Three-dimensional multislice CT scanner: value in patients with pulmonary atresia with septal defect]. 61
12085740 2002
213
Bovine jugular vein as right ventricle-to-pulmonary artery valved conduit. 61
12000167 2002
214
Use of small stents for rehabilitation of hypoplastic pulmonary arteries in pulmonary atresia with ventricular septal defect. 61
11793499 2002
215
Endovascular stent implantation in a coronary artery to pulmonary artery fistula in a patient with pulmonary atresia with ventricular septal defect and severe cyanosis. 61
11747165 2001
216
Pulmonary atresia with ventricular septal defect, extremely hypoplastic pulmonary arteries, major aorto-pulmonary collaterals. 61
11509284 2001
217
[Right ventricular outflow tract reconstruction for pulmonary atresia with ventricular septal defect: the possibility of ventriculo-arterial direct anastomosis]. 61
11517528 2001
218
Pulmonary atresia with ventricular septal defect and persistent airway hyperresponsiveness. 61
11436051 2001
219
Classification of pulmonary atresia with ventricular septal defect. 61
11465219 2001
220
[Right ventricular outflow tract reconstruction using monocusp valved outflow patch for pulmonary atresia with ventricular septal defect: influence of the presence of major aorto-pulmonary collateral arteries]. 61
11517530 2001
221
Origin of the main pulmonary artery from the left coronary artery in complex pulmonary atresia. 61
11455407 2001
222
Pulmonary atresia with ventricular septal defect: prevalence of deletion 22q11 in the different anatomic patterns. 61
11392644 2001
223
[Rehabilitation of hypoplastic pulmonary arteries and anatomic correction of pulmonary atresia with interventricular communication]. 61
11434011 2001
224
Prevalence of 22q11 deletion in fetuses with conotruncal cardiac defects: a 6-year prospective study. 61
11295715 2001
225
Right ventricular outflow tract reconstruction with an allograft conduit. 61
11269473 2001
226
Valveless outflow reconstruction using autologous tissue as a posterior wall for pulmonary atresia with ventricular septal defect. 61
11393109 2001
227
Pre-operative evaluation with MR in tetralogy of fallot and pulmonary atresia with ventricular septal defect. 61
11167334 2001
228
[The best in 2000 on pediatric cardiology]. 61
11260839 2001
229
Limitation of transthoracic echocardiography in the diagnosis of congenital heart diseases. 61
11194000 2000
230
Natural and unnatural history of pulmonary atresia. 61
11040008 2000
231
Heat shock protein 72 expression in the right ventricle of patients undergoing congenital cardiac surgery. 61
10925734 2000
232
Five- to fifteen-year follow-up of fresh autologous pericardial valved conduits. 61
10788806 2000
233
Transaortic closure of residual intramural ventricular septal defect. 61
10881829 2000
234
[Prenatal diagnosis of conotruncal heart diseases. Results in 337 cases]. 61
10858856 2000
235
Early and intermediate outcomes after repair of pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries: experience with 85 patients. 61
10769284 2000
236
Permissive hypoxemia permitted postoperative weaning from artificial ventilation after repair of pulmonary atresia. 61
10815306 2000
237
[Early postoperative dysfunction of a modified Blalock-Taussig shunt: successful therapy with angioplasty and stent implantation in the subclavian artery]. 61
10768280 2000
238
Nitrofen-induced congenital malformations of the heart and great vessels in rats: an animal model. 61
10626854 1999
239
[Microdeletion of 22q11 and conotruncal cardiopathies: contribution of prenatal diagnosis]. 61
10598346 1999
240
Branch pulmonary artery growth after blalock-taussig shunts in tetralogy of fallot and pulmonary atresia with ventricular septal defect: a retrospective, echocardiographic study. 61
10441692 1999
241
[Anesthetic management of an infant with pulmonary atresia and ventricular septal defect accompanied by excess pulmonary blood flow for systemic-pulmonary shunt operation]. 61
10339934 1999
242
[Aorto-pulmonary collaterals in an infant with 22q11 monosomy]. 61
12555381 1999
243
Images in cardiovascular medicine. Combined angiography and three-dimensional computed tomography for assessing systemic-to-pulmonary collaterals in pulmonary atresia with ventricular septal defect. 61
9860797 1998
244
Total repair of pulmonary atresia with ventricular septal defect and major aortopulmonary collaterals: an integrated approach. 61
9832681 1998
245
MR imaging of non-visualized pulmonary arteries at angiography in patients with congenital heart disease. 61
9886167 1998
246
Heparin as a risk factor for perigraft seroma complicating the modified Blalock-Taussig shunt. 61
9699582 1998
247
[A pulmonary vascularization study in pulmonary atresia with an interventricular defect in relation to the presence of a chromosome 22 deletion]. 61
9672779 1998
248
Truncus arteriosus with anterior origin of a hypoplastic main pulmonary artery. 61
9659203 1998
249
Prevalence of 22q11 region deletions in patients with velopharyngeal insufficiency. 61
9557885 1998
250
Lung transplantation and repair of complex congenital heart lesions in patients with pulmonary hypertension. 61
9620463 1998
251
Thirty-year incidence of infective endocarditis after surgery for congenital heart defect. 61
9486754 1998
252
The use of bovine pericardium for pulmonary valve reconstruction or conduit replacement: long-term clinical follow up. 61
9502140 1998
253
Pulmonary atresia with ventricular septal defect: a case for central venous pressure and oxygen saturation monitoring. 61
9713951 1998
254
[A rare combination of partial trisomy 9 with pulmonary atresia]. 61
9244820 1997
255
Use of Palmaz stents to palliate pulmonary atresia with ventricular septal defect and stenotic aortopulmonary collaterals. 61
9096942 1997
256
Three-vessel view of the fetal upper mediastinum: an easy means of detecting abnormalities of the ventricular outflow tracts and great arteries during obstetric screening. 61
9165680 1997
257
Pulmonary atresia, "intact ventricular septum", and aortopulmonary collateral arteries. 61
9068403 1997
258
Homografts for right ventricular outflow tract reconstruction in congenital heart disease. 61
9455784 1997
259
Unifocalization for pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries. 61
8751508 1996
260
[Pulmonary arborization abnormalities in complex forms of pulmonary atresia with ventricular septal defect: unification, unifocalization and complete repair]. 61
8758564 1996
261
[Evaluation of pulmonary arteries using nuclear magnetic resonance in patients with pulmonary atresia]. 61
8744389 1996
262
One-stage repair of pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries by a handmade trifurcated valved conduit. 61
8811410 1996
263
Complete repair of PA-VSD with diminutive or discontinuous pulmonary arteries by transverse thoracosternotomy. 61
8572781 1996
264
Experience with repair of congenital heart defects using adjunctive endovascular devices. 61
7475204 1995
265
Valved conduits of bovine pericardium for right ventricle to pulmonary artery connections. 61
7548322 1995
266
[Pulmonary atresia with ventricular septal defect: therapeutic strategy in newborn infants]. 61
7646277 1995
267
Midline one-stage complete unifocalization and repair of pulmonary atresia with ventricular septal defect and major aortopulmonary collaterals. 61
7739241 1995
268
[Systemic pulmonary shunts in the neonatal period. Short and medium-term results]. 61
7646279 1995
269
The 'Rastelli' operation--results at the Singapore General Hospital. 61
7676266 1995
270
Usefulness of interlocking detachable coil for embolization of the major aorto-pulmonary collateral artery: a case report. 61
7621550 1995
271
Coronary artery-pulmonary artery fistula in pulmonary atresia with ventricular septal defect. 61
7673088 1995
272
The restricted surgical relevance of morphologic criteria to classify systemic-pulmonary collateral arteries in pulmonary atresia with ventricular septal defect. 61
7934105 1994
273
[Transcatheter embolization of aorto-pulmonary collateral arteries in cyanotic congenital heart disease]. 61
8207891 1994
274
[Pulmonary atresia with open septum: analysis of therapeutic management apropos of 47 cases]. 61
7857186 1994
275
Surgical management of pulmonary atresia with ventricular septal defect and multiple aortopulmonary collaterals. 61
7514160 1994
276
Surgical treatment of tetralogy of Fallot and pulmonary atresia with ventricular septal defect. 61
8279911 1994
277
Surgical management of pulmonary atresia with ventricular septal defect and multiple aortopulmonary collaterals. 61
8118597 1994
278
Pulmonary atresia with ventricular septal defect in adults. 61
8281653 1994
279
[Reoperation with a bifurcated nonvalved extracardiac conduit for stenosis of the valved conduit and the pulmonary bifurcation after a Ross-Rastelli operation]. 61
8308385 1994
280
Detection of major aortopulmonary collateral arteries by transesophageal echocardiography in pulmonary atresia with ventricular septal defect. 61
8237775 1993
281
[Surgical treatment of the patients with pulmonary atresia, ventricular septal defect associated with major aorto-pulmonary collateral arteries--a report of two cases]. 61
8283091 1993
282
Pulmonary blood supply by a branch from the distal ascending aorta in pulmonary atresia with ventricular septal defect: differential diagnosis of fifth aortic arch. 61
8255798 1993
283
[Attempt at allo-aortal conduits in the correction of congenital heart defects]. 61
8148165 1993
284
Radiofrequency-assisted "reconstruction" of the right ventricular outflow tract in muscular pulmonary atresia with ventricular septal defect. 61
8489867 1993
285
Successful repair of pulmonary atresia with ventricular septal defect without the use of a conduit: a new surgical option. Report of two cases. 61
1389766 1992
286
[Pulmonary valve atresia with ventricular septum defect: interventional recanalization of the right ventricular outflow tract]. 61
1441703 1992
287
Use of endovascular stents to increase pulmonary blood flow in pulmonary atresia with ventricular septal defect. 61
1378695 1992
288
Repair of conotruncal abnormalities with the use of the valved conduit: improved early and midterm results with the cryopreserved homograft. 61
1607524 1992
289
Ductus arteriosus in pulmonary atresia with and without ventricular septal defect. Anatomic and functional differences. 61
1439650 1992
290
[Right atrial isomerism with pulmonary atresia: the angiocardiographic characteristics and pulmonary circulatory patterns]. 61
1743448 1991
291
Pulmonary atresia with ventricular septal defect. Selection of patients for systemic-to-pulmonary artery shunt based on echocardiography. 61
1702046 1991
292
Staged repair of pulmonary atresia with ventricular septal defect and major systemic to pulmonary artery collaterals. 61
1985579 1991
293
Unifocalization for pulmonary atresia with ventricular septal defect. 61
1985581 1991
294
Congenital heart disease and Robinow syndrome: coincidence or an additional component of the syndrome? 61
2260599 1990
295
Congenital polyvalvular disease in trisomy 18: echocardiographic diagnosis. 61
2395741 1990
296
Coronary artery fistula as source of pulmonary circulation in pulmonary atresia with ventricular septal defect. 61
2309224 1990
297
Surgical correction of pulmonary atresia with ventricular septal defect and no central pulmonary arteries. 61
2296901 1990
298
[Limits of early ambulation following heart surgery from the viewpoint of the pediatric cardiologist]. 61
2082605 1990
299
Doppler color flow imaging and determination of pulmonary blood supply in infants with pulmonary atresia with ventricular septal defect. 61
2685080 1989
300
The value of Doppler color flow mapping in determining pulmonary blood supply in infants with pulmonary atresia with ventricular septal defect. 61
2685079 1989
301
Cervical collateral arteries in pulmonary atresia with ventricular septal defect. 61
3195490 1988
302
Pulmonary atresia with ventricular septal defect and coronary artery fistula: a late presentation. 61
3179145 1988
303
Solitary arterial trunk with pulmonary atresia and arteries with supply to the left lung from both an arterial duct and systemic-pulmonary collateral arteries. 61
3403079 1988
304
Pulmonary atresia with ventricular septal defect and coronary artery fistula: a late presentation. 61
3355730 1988
305
Correction of pulmonary atresia with ventricular septal defect in the absence of the pulmonary trunk and the central pulmonary arteries (so-called truncus type IV). 61
3682860 1987
306
Pulmonary atresia and aortic valve stenosis. 61
3610392 1987
307
[Pulmonary atresia with ventricular septal defect: the significance of collateral lung perfusion for the prognosis of corrective operations]. 61
2442896 1987
308
[Surgical treatment of pulmonary atresia with ventricular septal defect]. 61
3509218 1987
309
Pulmonary atresia with ventricular septal defect in adult patients. 61
3594946 1987
310
Detection of infection of a cardiac xenograft by gallium-67 scan. 61
3771006 1986
311
Late results of right ventricular outflow tract reconstruction with Björk-Shiley valved conduits. 61
3964504 1986
312
Pulmonary atresia with ventricular septal defect: preoperative and postoperative responses to exercise. 61
3950243 1986
313
Coronary artery--pulmonary artery fistula in tetralogy of Fallot with pulmonary atresia. 61
4054143 1985
314
Direct reconstruction of pulmonary artery arborization anomaly and intracardiac repair of pulmonary atresia with ventricular septal defect. 61
4003316 1985
315
[Collateral pulmonary circulation in Fallot's tetralogy]. 61
3929719 1985
316
[Major aortopulmonary collateral-pulmonary arterial shunt for pulmonary atresia with ventricular septal defect and hypoplastic pulmonary arteries]. 61
4020193 1985
317
Tetralogy of Fallot with major aortopulmonary collateral arteries. 61
3966958 1985
318
Surgical repair of cyanotic cardiac defects in young adults. The Fontan procedure and use of the extracardiac valved conduit. 61
6567149 1984
319
[Pulmonary atresia with ventricular septal defect and right coronary-pulmonary artery fistula]. 61
6503101 1984
320
Consecutive repair of complex congenital heart disease using hypothermic cardioplegic arrest--its results and ultrastructural study of the myocardium. 61
6198769 1984
321
Coexistence of ductal and systemic pulmonary arterial supply in pulmonary atresia with ventricular septal defect. 61
6695739 1984
322
Postoperative assessment of porcine-valved right ventricular-pulmonary artery conduits. 61
6691263 1984
323
Diagnosis of right ventricular outflow obstruction in infants by cross sectional echocardiography. 61
6639811 1983
324
[Balloon occlusion aortography in the angiographic study of pulmonary atresia with interventricular defect]. 61
6667807 1983
325
[Pulmonary atresia with ventricular septal defect: palliative operations of primarily inoperable forms]. 61
6196920 1983
326
Pulmonary atresia with ventricular septal defect and aortic regurgitation: diagnosis by echocardiography with diastolic vibration of both right and left sides of the ventricular septum. 61
6869298 1983
327
[Pulmonary atresia with major hypoplasia of the pulmonary branches. A radical 2-stage correction]. 61
6411024 1983
328
[Pulmonary atresia with interventricular communication. Review of concepts]. 61
6625753 1983
329
Two-dimensional echocardiographic study of right ventricular outflow and great artery anatomy in pulmonary atresia with ventricular septal defects and in truncus arteriosus. 61
6823810 1983
330
Unusual vascular ring in infant with pulmonary atresia and ventricular septal defect. 61
7093088 1982
331
Classic shunting operations for congenital cyanotic heart defects. 61
7087545 1982
332
Aortic regurgitation in tetrad of Fallot and pulmonary atresia. 61
7081079 1982
333
Surgical repair of pulmonary atresia with ventricular septal defect and hypoplastic pulmonary arteries: a different approach. 61
7278357 1981
334
Duplicate sources of pulmonary blood supply in pulmonary atresia with ventricular septal defect. 61
7295419 1981
335
[Cardiological problems in the neonatal period (author's transl)]. 61
7199220 1981
336
The systemic pulmonary circulation in pulmonary atresia with ventricular septal defect: concept of reciprocal development of the fourth and sixth aortic arches. 61
7468440 1981
337
Pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries. Effect of systemic pulmonary anastomosis. 61
7459172 1981
338
Management of pulmonary atresia with ventricular septal defect and hypoplastic pulmonary arteries by right ventricular outflow construction. 61
6158634 1980
339
Collateral arteries in pulmonary atresia with ventricular septal defect. A precarious blood supply. 61
7426161 1980
340
Growth and development of pulmonary circulation in pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries. 61
7426156 1980
341
Left ventricular function in cyanotic congenital heart disease. 61
7377122 1980
342
Absent right superior vena cava with persistent left superior vena cava: implications and management. 61
7350758 1980
343
[Radiology of the bronchial arteries in pulmonary atresia with ventricular septal defect]. 61
550768 1979
344
Histology of pulmonary arterial supply in pulmonary atresia with ventricular septal defect. 61
487540 1979
345
[Valve-fitted prosthetic tubes in the pulmonary outflow tract. Results of a series of 45 operations]. 61
115398 1979
346
Systemic-pulmonary arterial supply in pulmonary atresia with ventricular septal defect: postmortem angiograms and histologic survey. 61
738129 1978
347
Special problems in pulmonary atresia with ventricular septal defect: extreme hypoplasia of intrapericardial pulmonary arteries and autofocal collateral vessels. 61
720368 1978
348
Open-heart palliative surgery for pulmonary atresia with ventricular septal defect and hypoplastic pulmonary arteries. 61
83013 1978
349
Congenital pulmonary atresia with ventricular septal defect: angiographic and surgical correlates. 61
566452 1978
350
A radiographic study of congenital pulmonary atresia with ventricular septal defect. 61
413353 1977
351
Pulmonary atresia with ventricular septal defect. Further anatomical observations. 61
588378 1977
352
[Pulmonary atresia with ventricular septal defect. Follow up and surgical results from 1963 to 1976 and diagnostic measures with special reference to large systemic-pulmonary collaterals (author's transl)]. 61
899138 1977
353
Pulmonary atresia with ventricular septal defect in three relatively asymptomatic children. 61
11170 1976
354
Echo-phonocardiographic and contrast studies in conditions associated with systemic arterial trunk overriding the ventricular septum: truncus arteriosus, tetralogy of Fallot, and pulmonary atresia with ventricular septal defect. 61
1253387 1976
355
[Pulmonary atresia (with ventricular septal defect)]. 61
1016741 1976
356
Association of congenital heart defects with season and population density. 61
943860 1976
357
Pulmonary atresia with ventricular septal defect: report of the oldest known surviving case. 61
123847 1975
358
The surgical anatomy of pulmonary atresia with ventricular septal defect: pseudotruncus. 61
1127970 1975
359
Conduit reconstruction of right ventricular outflow tract. Experience with 17 patients. 61
123441 1975
360
Haemodynamic and anatomical characteristics of pulmonary blood supply in pulmonary atresia with ventricular septal defect - including a case of persistent fifth aortic arch. 61
4451583 1974
361
Proceedings: Preoperative measurement of central pulmonary artery pressure in pulmonary atresia with ventricular septal defect. 61
4433439 1974
362
Surgical treatment of congenital pulmonary atresia with ventricular septal defect. 61
5540464 1971
363
Bronchopulmonary arterial communications in pulmonary atresia with ventricular septal defect. 61
5811539 1969
364
[Longevity and extremely high heart weight in pulmonary atresia with ventricular septal defect]. 61
4241563 1969
365
The surgery of tetralogy of Fallot, pulmonary atresia with ventricular septal defect and transposition of the great vessels. 61
5711069 1968
366
Congenital pulmonary atresia with ventricular septal defect. Review of the clinical course of fifty patients with assessment of the results of palliative surgery. 61
4171379 1968
367
Continuous murmurs in tetralogy of Fallot and pulmonary atresia with ventricular septal defect. 61
5923992 1966

Variations for Pulmonary Atresia with Ventricular Septal Defect

ClinVar genetic disease variations for Pulmonary Atresia with Ventricular Septal Defect:

6 (showing 1, show less) ‎‎
# Gene Name Type Significance ClinVarId dbSNP ID GRCh37 Pos GRCh38 Pos
1 FOXP1 NM_032682.6(FOXP1):c.1702C>T (p.Pro568Ser)SNV Benign/Likely benign 55847 rs147674680 3:71019907-71019907 3:70970756-70970756

Expression for Pulmonary Atresia with Ventricular Septal Defect

Search GEO for disease gene expression data for Pulmonary Atresia with Ventricular Septal Defect.

Pathways for Pulmonary Atresia with Ventricular Septal Defect

GO Terms for Pulmonary Atresia with Ventricular Septal Defect

Sources for Pulmonary Atresia with Ventricular Septal Defect

3 CDC
7 CNVD
9 Cosmic
10 dbSNP
11 DGIdb
17 EFO
18 ExPASy
19 FMA
28 GO
29 GTR
30 HMDB
31 HPO
32 ICD10
33 ICD10 via Orphanet
34 ICD9CM
35 IUPHAR
36 KEGG
37 LifeMap
39 LOVD
41 MedGen
43 MeSH
44 MESH via Orphanet
45 MGI
48 NCI
49 NCIt
50 NDF-RT
53 NINDS
54 Novoseek
56 OMIM
57 OMIM via Orphanet
61 PubMed
63 QIAGEN
68 SNOMED-CT via HPO
69 TGDB
70 Tocris
71 UMLS
72 UMLS via Orphanet
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