CTEPH
MCID: PLM101
MIFTS: 37

Pulmonary Hypertension, Chronic Thromboembolic, Without Deep Vein Thrombosis (CTEPH)

Categories: Blood diseases, Cardiovascular diseases, Rare diseases, Respiratory diseases

Aliases & Classifications for Pulmonary Hypertension, Chronic Thromboembolic, Without Deep Vein...

MalaCards integrated aliases for Pulmonary Hypertension, Chronic Thromboembolic, Without Deep Vein Thrombosis:

Name: Pulmonary Hypertension, Chronic Thromboembolic, Without Deep Vein Thrombosis 57
Pulmonary Hypertension, Chronic Thromboembolic, Without Deep Vein Thrombosis, Susceptibility to 57 13
Chronic Thromboembolic Pulmonary Hypertension 58 71
Cteph, Dvt-Negative, Susceptibility to 57
Cteph, Dvt-Negative 57
Cteph 58

Characteristics:

Orphanet epidemiological data:

58
chronic thromboembolic pulmonary hypertension
Inheritance: Not applicable; Prevalence: 1-9/100000 (Europe); Age of onset: Adult;

Classifications:

Orphanet: 58  
Rare respiratory diseases


External Ids:

OMIM® 57 612862
UMLS via Orphanet 72 C2363973
Orphanet 58 ORPHA70591
UMLS 71 C2363973

Summaries for Pulmonary Hypertension, Chronic Thromboembolic, Without Deep Vein...

MalaCards based summary : Pulmonary Hypertension, Chronic Thromboembolic, Without Deep Vein Thrombosis, also known as pulmonary hypertension, chronic thromboembolic, without deep vein thrombosis, susceptibility to, is related to chronic thromboembolic pulmonary hypertension and pulmonary hypertension. An important gene associated with Pulmonary Hypertension, Chronic Thromboembolic, Without Deep Vein Thrombosis is CTEPH1 (Pulmonary Hypertension, Chronic Thromboembolic, Without Deep Vein Thrombosis, Susceptibility To). The drugs Selexipag and Treprostinil have been mentioned in the context of this disorder. Affiliated tissues include heart, endothelial and lung, and related phenotypes are depressivity and fatigue

More information from OMIM: 612862

Related Diseases for Pulmonary Hypertension, Chronic Thromboembolic, Without Deep Vein...

Diseases related to Pulmonary Hypertension, Chronic Thromboembolic, Without Deep Vein Thrombosis via text searches within MalaCards or GeneCards Suite gene sharing:

(show top 50) (show all 158)
# Related Disease Score Top Affiliating Genes
1 chronic thromboembolic pulmonary hypertension 12.1
2 pulmonary hypertension 11.6
3 pulmonary embolism 11.2
4 pulmonary hypertension, primary, 1 11.2
5 thrombophilia due to thrombin defect 10.9
6 cardiac arrest 10.9
7 vascular disease 10.7
8 pulmonary edema 10.7
9 antiphospholipid syndrome 10.7
10 tricuspid valve insufficiency 10.7
11 thrombosis 10.6
12 syncope 10.6
13 thrombophilia 10.6
14 respiratory failure 10.5
15 lung disease 10.5
16 hemopericardium 10.4
17 pericardial effusion 10.4
18 hypothyroidism 10.4
19 congestive heart failure 10.4
20 connective tissue disease 10.4
21 vasculitis 10.4
22 sarcoidosis 1 10.4
23 pulmonary disease, chronic obstructive 10.4
24 hydrocephalus 10.4
25 sarcoma 10.4
26 heart disease 10.4
27 spindle cell sarcoma 10.4
28 pulmonary venoocclusive disease 10.4
29 mediastinitis 10.4
30 fibrosing mediastinitis 10.4
31 cardiogenic shock 10.4
32 arteries, anomalies of 10.3
33 fibrosis of extraocular muscles, congenital, 1 10.3
34 multinucleated neurons, anhydramnios, renal dysplasia, cerebellar hypoplasia, and hydranencephaly 10.3
35 lipoprotein quantitative trait locus 10.3
36 sleep apnea 10.3
37 hepatic veno-occlusive disease 10.3
38 thrombocytopenia 10.3
39 heritable pulmonary arterial hypertension 10.3
40 sickle cell disease 10.3
41 autoimmune disease 10.2
42 varicose veins 10.2
43 hypertension, early-onset, autosomal dominant, with severe exacerbation in pregnancy 10.2
44 anxiety 10.2
45 cyanosis, transient neonatal 10.2
46 inflammatory bowel disease 10.2
47 osteomyelitis 10.2
48 nasopharyngitis 10.2
49 portal hypertension 10.2
50 cardiac tamponade 10.2

Graphical network of the top 20 diseases related to Pulmonary Hypertension, Chronic Thromboembolic, Without Deep Vein Thrombosis:



Diseases related to Pulmonary Hypertension, Chronic Thromboembolic, Without Deep Vein Thrombosis

Symptoms & Phenotypes for Pulmonary Hypertension, Chronic Thromboembolic, Without Deep Vein...

Human phenotypes related to Pulmonary Hypertension, Chronic Thromboembolic, Without Deep Vein Thrombosis:

58 (show all 37)
# Description HPO Frequency Orphanet Frequency HPO Source Accession
1 depressivity 58 Occasional (29-5%)
2 fatigue 58 Frequent (79-30%)
3 congestive heart failure 58 Very frequent (99-80%)
4 obesity 58 Occasional (29-5%)
5 autoimmunity 58 Occasional (29-5%)
6 inflammation of the large intestine 58 Very rare (<4-1%)
7 neoplasm 58 Very rare (<4-1%)
8 osteomyelitis 58 Very rare (<4-1%)
9 pulmonary embolism 58 Frequent (79-30%)
10 pulmonary arterial hypertension 58 Very frequent (99-80%)
11 syncope 58 Occasional (29-5%)
12 right bundle branch block 58 Occasional (29-5%)
13 reduced vital capacity 58 Frequent (79-30%)
14 elevated c-reactive protein level 58 Occasional (29-5%)
15 abnormality of blood and blood-forming tissues 58 Occasional (29-5%)
16 edema 58 Occasional (29-5%)
17 exertional dyspnea 58 Frequent (79-30%)
18 abnormal t-wave 58 Occasional (29-5%)
19 deep venous thrombosis 58 Frequent (79-30%)
20 antiphospholipid antibody positivity 58 Occasional (29-5%)
21 myeloproliferative disorder 58 Very rare (<4-1%)
22 central sleep apnea 58 Occasional (29-5%)
23 left ventricular dysfunction 58 Occasional (29-5%)
24 palpitations 58 Frequent (79-30%)
25 increased hdl cholesterol concentration 58 Occasional (29-5%)
26 increased pulmonary vascular resistance 58 Very frequent (99-80%)
27 right ventricular failure 58 Occasional (29-5%)
28 lupus anticoagulant 58 Occasional (29-5%)
29 right ventricular dilatation 58 Occasional (29-5%)
30 obstructive deficit on pulmonary function testing 58 Frequent (79-30%)
31 cardiac shunt 58 Occasional (29-5%)
32 recurrent thromboembolism 58 Occasional (29-5%)
33 dysfibrinogenemia 58 Occasional (29-5%)
34 abnormality of von willebrand factor 58 Occasional (29-5%)
35 hypocapnia 58 Occasional (29-5%)
36 right atrial enlargement 58 Occasional (29-5%)
37 increased factor viii activity 58 Occasional (29-5%)

Clinical features from OMIM®:

612862 (Updated 05-Mar-2021)

Drugs & Therapeutics for Pulmonary Hypertension, Chronic Thromboembolic, Without Deep Vein...

Drugs for Pulmonary Hypertension, Chronic Thromboembolic, Without Deep Vein Thrombosis (from DrugBank, HMDB, Dgidb, PharmGKB, IUPHAR, NovoSeek, BitterDB):

(show all 45)
# Name Status Phase Clinical Trials Cas Number PubChem Id
1
Selexipag Approved Phase 3 475086-01-2
2
Treprostinil Approved, Investigational Phase 3 81846-19-7 54786 6918140
3
Edoxaban Approved Phase 3 480449-70-5
4
Warfarin Approved Phase 3 81-81-2 6691 54678486
5
Macitentan Approved Phase 3 441798-33-0
6
Ambrisentan Approved, Investigational Phase 3 177036-94-1 6918493
7 Calamus Phase 3
8 Anticoagulants Phase 3
9 Antithrombins Phase 3
10 Serine Proteinase Inhibitors Phase 3
11 HIV Protease Inhibitors Phase 3
12 Factor Xa Inhibitors Phase 3
13
protease inhibitors Phase 3
14 Antithrombin III Phase 3
15 Endothelin A Receptor Antagonists Phase 3
16 Endothelin Receptor Antagonists Phase 3
17 Antihypertensive Agents Phase 3
18
Serine Investigational, Nutraceutical Phase 3 56-45-1 5951
19
Riociguat Approved Phase 2 625115-55-1
20 Radiopharmaceuticals Phase 2
21
Nitric Oxide Approved Phase 1 10102-43-9 145068
22
Iodine Approved, Investigational 7553-56-2 807
23
Acetylcysteine Approved, Investigational 616-91-1 12035
24
Thrombin Approved, Investigational
25
Iloprost Approved, Investigational 78919-13-8 6443959
26
Epoprostenol Approved 61849-14-7, 35121-78-9 5280427 5282411
27
Tadalafil Approved, Investigational 171596-29-5 110635
28
Bosentan Approved, Investigational 147536-97-8 104865
29
Cysteine Approved, Nutraceutical 52-90-4 5862
30
Cadexomer iodine Experimental 94820-09-4
31 Tezosentan Investigational 180384-57-0
32 Protective Agents
33 Respiratory System Agents
34 Antioxidants
35 Anti-Infective Agents
36 Antiviral Agents
37 Expectorants
38 N-monoacetylcystine
39 Antidotes
40 Hemostatics
41 Coagulants
42 Phosphodiesterase 5 Inhibitors
43 Sildenafil Citrate 171599-83-0
44 Fluorodeoxyglucose F18
45 Deoxyglucose

Interventional clinical trials:

(show top 50) (show all 74)
# Name Status NCT ID Phase Drugs
1 CHANGE-MRI (CTEPH DIAGNOSIS Europe - MRI) Unknown status NCT02791282 Phase 3
2 Prospective, Randomized, Placebo-controlled, Double-blind, Multicenter, Parallel Group Study to Assess the Efficacy, Safety and Tolerability of Bosentan in Patients With Inoperable Chronic Thromboembolic Pulmonary Hypertension (CTEPH) Completed NCT00313222 Phase 3 bosentan
3 Long-term Open-label Extension Study in Patients With Inoperable Chronic Thromboembolic Pulmonary Hypertension (CTEPH) Who Completed Protocol AC-052-366 (BENEFIT, NCT00313222) Completed NCT00319111 Phase 3 bosentan
4 Randomized, Double-blind, Placebo-controlled, Multi-centre, Multi-national Study to Evaluate the Efficacy and Safety of Oral BAY63-2521 (1 mg, 1.5 mg, 2 mg, or 2.5 mg Tid) in Patients With Chronic Thromboembolic Pulmonary Hypertension (CTEPH) Completed NCT00855465 Phase 3 Riociguat (Adempas, BAY63-2521);Placebo
5 Long-term Extension, Multicentre, Multi-international Study to Evaluate the Safety and Tolerability of Oral BAY63-2521 (1mg, 1.5 mg, 2.0 mg, 2.5 mg Tid) in Patients With Chronic Thromboembolic Pulmonary Hypertension (CTEPH). Completed NCT00910429 Phase 3 Riociguat (Adempas, BAY63-2521)
6 Effect of Long-term Oxygen Therapy on Exercise Capacity and Quality of Life in Patients With Pulmonary Arterial and Chronic Thromboembolic Pulmonary Hypertension Completed NCT01884012 Phase 3
7 A Prospective, Randomized, Double-blind, Multicenter, Placebo-controlled, Parallel Group, Adaptive Phase 3 Study With Open-label Extension to Evaluate Efficacy and Safety of Macitentan 75 mg in Inoperable or Persistent/Recurrent Chronic Thromboembolic Pulmonary Hypertension Recruiting NCT04271475 Phase 3 Macitentan;Placebo
8 A Multicenter, Randomized, Double-blind, Placebo-controlled, Parallel-group, Group-sequential, Adaptive, Phase 3 Study With Open-label Extension Period to Assess the Efficacy and Safety of Selexipag as an add-on to Standard of Care Therapy in Subjects With Inoperable or Persistent/Recurrent After Surgical and/or Interventional Treatment Chronic Thromboembolic Pulmonary Hypertension Recruiting NCT03689244 Phase 3 Selexipag;Placebo
9 A Double Blind Controlled Clinical Study to Investigate the Efficacy and Tolerability of Subcutaneous Treprostinil Sodium in Patients With Severe Non-operable Chronic Thromboembolic Pulmonary Hypertension (CTREPH) Active, not recruiting NCT01416636 Phase 3 Treprostinil sodium
10 An Investigator-initiated, Phase III Trial, Randomized, Single-blind, Double-dummy, Parallel-group, Multi-center Study for the Evaluation of Efficacy and Safety of Warfarin Versus Edoxaban in Subjects With CTEPH Taking Warfarin: KABUKI Not yet recruiting NCT04730037 Phase 3 Edoxaban;Warfarin Potassium;Warfarin Potassium placebo;Edoxaban placebo
11 A Prospective, Multicenter, Open-label, Single Arm, Phase III Study to Assess the Efficacy and Safety of Macitentan (ACT-064992) in Subjects With Chronic Thromboembolic Pulmonary Hypertension (CTEPH) Terminated NCT03809650 Phase 3 macitentan 10 mg
12 A Randomised, Multicentre, Double-Blind, Placebo-Controlled Study Of Ambrisentan In Subjects With Inoperable Chronic Thromboembolic Pulmonary Hypertension (CTEPH). Terminated NCT01884675 Phase 3 Ambrisentan 5 mg;Placebo
13 An Open-label Extension Study of the Long-term Safety, Tolerability and Efficacy of Ambrisentan in Subjects With Inoperable Chronic Thromboembolic Pulmonary Hypertension (CTEPH) Terminated NCT01894022 Phase 3 Ambrisentan 5 mg
14 Randomized Pilot Trial of Interventional Treatment of Residual Pulmonary Hypertension in Patients After Pulmonary Thromboendarterectomy Unknown status NCT02745106 Phase 2
15 Effect of Short-term Oxygen Therapy on Cardiopulmonary Exercise Capacity in Patients With Pulmonary Arterial and Chronic Thromboembolic Pulmonary Hypertension Completed NCT01748474 Phase 2
16 Prospective, Randomized, Placebo-controlled, Double-blind, Multicenter, Parallel-group, 24-week Study to Assess the Efficacy, Safety and Tolerability of Macitentan in Subjects With Inoperable Chronic Thromboembolic Pulmonary Hypertension Completed NCT02021292 Phase 2 Macitentan;Placebo
17 Evaluation of Right Ventricular Function and Metabolism Following Riociguat for the Treatment of Chronic Thromboembolic Pulmonary Hypertension- Images of Rio Completed NCT02094001 Phase 2
18 The Effect of Riociguat for Peak Cardiac Index on Cardiopulmonary Exercise Test in CTEPH Patients After Normalization of Pulmonary Artery Pressure by Combination Treatment of Riociguat and Balloon Pulmonary Angioplasty Recruiting NCT04600492 Phase 2 Riociguat Oral Tablet
19 Prospective, Randomized, Controlled Trial of the Effect of Long-term Oxygen Therapy on 6-minute Walking Distance, Clinical Parameters and Hemodynamics in Patients With PAH and CTEPH Recruiting NCT04207593 Phase 2 Oxygen
20 MERIT-2 : Long Term, Multicenter, Single-arm, Open-label Extension Study of the MERIT-1 Study, to Assess the Safety, Tolerabilty and Efficacy of Macitentan in Subjects With Inoperable Chronic Thromboembolic Pulmonary Hypertension (CTEPH) Active, not recruiting NCT02060721 Phase 2 Macitentan
21 A Phase 2, Randomised, Double-Blind, Placebo-Controlled, Multicentre, Prospective Study to Assess Efficacy of Riociguat in Patients With Operable CTEPH Prior to Pulmonary Endarterectomy With High Preoperative Pulmonary Vascular Resistance Terminated NCT03273257 Phase 2 Riociguat;Placebo
22 A Non-randomized Two Part Multi-Center, Open-label, Single Dose Trial With an Escalation Part in Untreated Pulmonary Arterial Hypertension (PAH) and Chronic Thromboembolic Pulmonary Hypertension (CTEPH) Patients (Part A), Followed by a Parallel Group Part in Untreated and Pre-treated Patients With PAH and CTEPH (Part B) to Investigate the Safety, Tolerability and Pharmacodynamics of Inhaled BAY1237592 Recruiting NCT03754660 Phase 1 BAY1237592;PH-monotherapy;PH-combination therapy
23 Prospective Registry to Evaluate the Effective Incidence of Chronic Thromboembolic Pulmonary Hypertension in Germany Unknown status NCT02660463
24 Assessment of Safety and Efficacy of Balloon Pulmonary Angioplasty in Non-operable CTEPH Patients Unknown status NCT02964390
25 Lung Perfusion Measured With Dual-Energy CT (DECT) in Patients With Chronic Thromboembolic Pulmonary Hypertension (CTEPH): Comparative Study With Right Heart Catheterization and Ventilation/Perfusion Scintigraphy (V/Q) Unknown status NCT03450304
26 IodiNe Subtraction maPpIng in the Diagnosis of chRonic Pulmonary thromboEmbolic Disease (INSPIRE): An Observational Diagnostic Study Unknown status NCT03806907
27 Gene Mutations in Secondary Pulmonary Hypertension Unknown status NCT00348803
28 Three-dimensional Echocardiographic Assessment of Right Ventricular Function in Patients Undergoing Pulmonary Endarterectomy Unknown status NCT02426203
29 Inspiratory Muscle Training in Patients With Chronic Thromboembolic Pulmonary Hypertension: a Randomized Controlled Trial Unknown status NCT03102294
30 Local Registry of Patients With Chronic Thromboembolic Pulmonary Hypertension in Novosibirsk Region Unknown status NCT03349164
31 Long-term Right Ventricular Resynchronization Therapy for Chronic Thromboembolic Pulmonary Hypertension Unknown status NCT01163422
32 National, Prospective, Multicenter,Observational Registry Study on Pulmonary Arterial Hypertension or Chronic Thromboembolic Pulmonary Hypertension in China Unknown status NCT01417338
33 Epidemiological Study of Chronic Thromboembolic Pulmonary Hypertension in China Unknown status NCT01717092
34 Russian National Registry of Patients With Pulmonary Arterial Hypertension and Chronic Thromboembolic Pulmonary Hypertension Unknown status NCT03707561
35 Incidence of CTEPH in Dependence of Thrombus Location in Patients With Acute Pulmonary Embolism and Index Fibrinolysis Unknown status NCT01672203
36 Early Non-invasive Detection of CTEPH After Pulmonary Embolism - The InShape-2 Study Completed NCT02555137
37 United States CTEPH Registry Completed NCT02429284
38 New International CTEPH Database Completed NCT02656238
39 Riociguat Versus Balloon Pulmonary Angioplasty in Non-operable Chronic thromboEmbolic Pulmonary Hypertension Completed NCT02634203 Riociguat
40 Evaluation of Pulmonary Perfusion Heterogeneity in Patients With Chronic Thromboembolic Pulmonary Hypertension Using Functional PET Imaging Completed NCT02114047
41 A Prospective Single Blind Controlled Study to Assess the Efficacy of a Lung Protective Ventilation Strategy in the Prevention of Reperfusion Lung Injury Following PTE Completed NCT00747045
42 Identification Of The Predictive Angiographic And Computed Tomographic (CT) Criteria Of The Success Of The Thromboendarterectomy In Chronic Pulmonary Hypertension Completed NCT00657722
43 The Right Ventricle in Chronic Pressure Overload: Identifying Novel Molecular Targets for Functional Imaging Completed NCT03199131
44 Efficacy of Medical Therapy for Pulmonary Arterial and Inoperable Chronic Thromboembolic Pulmonary Hypertension in a Real Life Setting Completed NCT03198910
45 Role of Inflammation and Angiogenesis in Chronic Thromboembolic Pulmonary Hypertension Completed NCT04472533
46 EMEA CTEPH Registry: An International Prospective Registry Investigating the Epidemiology, Diagnosis and Treatment of CTEPH Patients in EMEA Countries Completed NCT02637050
47 Identification of CTEPH on Standard Computerised Tomography Pulmonary Angiography Performed in the Work-up of Suspected Pulmonary Embolism Completed NCT03083093
48 Retrospective Chart Review of Patients With PAH or Inoperable/Persistent/Recurrent CTEPH Who Transition Their PH Treatment to Adempas Completed NCT02545465 Riociguat (Adempas, BAY63-2521)
49 The Precise Surgical Treatment of Chronic Thromboembolic Pulmonary Hypertension: Pulmonary Endarterectomy Guided by Three-dimensional Pulmonary Angiography Recruiting NCT03795740
50 Sleep-Disordered Breathing in Chronic Thromboembolic Pulmonary Hypertension - a Prospective, Descriptive Cohort Study Recruiting NCT03074539 Riociguat

Search NIH Clinical Center for Pulmonary Hypertension, Chronic Thromboembolic, Without Deep Vein Thrombosis

Genetic Tests for Pulmonary Hypertension, Chronic Thromboembolic, Without Deep Vein...

Anatomical Context for Pulmonary Hypertension, Chronic Thromboembolic, Without Deep Vein...

MalaCards organs/tissues related to Pulmonary Hypertension, Chronic Thromboembolic, Without Deep Vein Thrombosis:

40
Heart, Endothelial, Lung, Brain, Smooth Muscle, Neutrophil, Kidney

Publications for Pulmonary Hypertension, Chronic Thromboembolic, Without Deep Vein...

Articles related to Pulmonary Hypertension, Chronic Thromboembolic, Without Deep Vein Thrombosis:

(show top 50) (show all 2081)
# Title Authors PMID Year
1
HLA-DPB1 and NFKBIL1 may confer the susceptibility to chronic thromboembolic pulmonary hypertension in the absence of deep vein thrombosis. 61 57
19165231 2009
2
Chronic Thromboembolic Disease and Chronic Thromboembolic Pulmonary Hypertension. 61
33541619 2021
3
The role of balloon pulmonary angioplasty and pulmonary endarterectomy: Is chronic thromboembolic pulmonary hypertension still a life-threatening disease? 61
33086125 2021
4
Three treatment options and the combination for patients with chronic thromboembolic pulmonary hypertension - established or not. 61
33221350 2021
5
Pulmonary angioplasty: A step further in the continuously changing landscape of chronic thromboembolic pulmonary hypertension management. 61
33524919 2021
6
NEDD9 is a Novel and Modifiable Mediator of Platelet-Endothelial Adhesion in the Pulmonary Circulation. 61
33523764 2021
7
Evaluating the Right Ventricle in Acute and Chronic Pulmonary Embolism: Current and Future Considerations. 61
33548932 2021
8
Effect of Normobaric Hypoxia on Exercise Performance in Pulmonary Hypertension: Randomized Trial. 61
32918899 2021
9
Characteristics and long-term survival of patients with chronic thromboembolic pulmonary hypertension in China. 61
32954622 2021
10
Evolution of patients with chronic thromboembolic pulmonary hypertension treated by balloon pulmonary angioplasty, according to their anticoagulant regimens. 61
33582861 2021
11
Balloon pulmonary angioplasty vs. pulmonary endarterectomy in patients with chronic thromboembolic pulmonary hypertension: a systematic review and meta-analysis. 61
33544306 2021
12
Correlation Between Perfusion Abnormalities Extent in Ventilation/Perfusion SPECT/CT with Hemodynamic Parameters in Patients with Chronic Thromboembolic Pulmonary Hypertension 61
33586404 2021
13
Treatment effect prediction using CT after balloon pulmonary angioplasty in chronic thromboembolic pulmonary hypertension. 61
33569619 2021
14
Possible immune regulation mechanisms for the progression of chronic thromboembolic pulmonary hypertension. 61
33316641 2021
15
Pulmonary atherosclerosis in a patient with chronic thromboembolic pulmonary hypertension. 61
33316138 2021
16
Risk stratification in chronic thromboembolic pulmonary hypertension predicts survival. 61
32586166 2021
17
Systematic Staged Percutaneous Balloon Pulmonary Angioplasty in Severe Inoperable Chronic Thromboembolic Pulmonary Hypertension. 61
33566998 2021
18
Clinical characteristics and aetiological analysis of 133 patients for pulmonary embolism combined with haemoptysis. 61
32975914 2021
19
Determinants and Management of the Post-Pulmonary Embolism Syndrome. 61
33548930 2021
20
Effect of EZH2 on pulmonary artery smooth muscle cell migration in pulmonary hypertension. 61
33313943 2021
21
Pulmonary manifestations of antiphospholipid syndrome: a retrospective analysis of 67 patients. 61
33386561 2021
22
Sleep-related breathing disorders and pulmonary hypertension. 61
32747397 2021
23
Clinical Significance of Guanylate Cyclase Stimulator, Riociguat, on Right Ventricular Functional Improvement in Patients with Pulmonary Hypertension. 61
33238268 2021
24
Peripheral microangiopathy in precapillary pulmonary hypertension: a nailfold video capillaroscopy prospective study. 61
33478514 2021
25
An evaluation of selexipag for the treatment of pulmonary hypertension. 61
32867545 2021
26
Balloon pulmonary angioplasty in the treatment of chronic thromboembolic pulmonary hypertension: recent advances and future perspectives. 61
33463996 2021
27
Comparison of 68Ga-FAPI imaging and cardiac magnetic resonance in detection of myocardial fibrosis in a patient with chronic thromboembolic pulmonary hypertension. 61
33474696 2021
28
Epidemiology of pulmonary arterial hypertension and chronic thromboembolic pulmonary hypertension: identification of the most accurate estimates from a systematic literature review. 61
33456755 2021
29
Direct oral anticoagulant therapy in patients with morbid obesity after intermediate- or high-risk pulmonary emboli. 61
33569503 2021
30
Evaluation of microvasculopathy using dual-energy computed tomography in patients with chronic thromboembolic pulmonary hypertension. 61
33532057 2021
31
Chronic thromboembolic pulmonary hypertension in patients with persistent chest symptoms after acute pulmonary embolism. 61
33382052 2021
32
Soluble ST2 as a Biomarker for Early Complications in Patients with Chronic Thromboembolic Pulmonary Hypertension Treated with Balloon Pulmonary Angioplasty. 61
33467121 2021
33
Patient Journey and Disease-Related Burden in Japanese Patients With Chronic Thromboembolic Pulmonary Hypertension: A Mixed Methods Study. 61
33476859 2021
34
Chronic thromboembolic pulmonary hypertension: evaluation of V/Q SPECT/CT and V/Q Quotient SPECT findings with postoperative results of pulmonary endarterectomy. 61
33443395 2021
35
When Imaging in Chronic Thromboembolic Pulmonary Hypertension Is Not Enough. 61
33026826 2021
36
Model of Chronic Thromboembolic Pulmonary Hypertension in Rats Caused by Repeated Intravenous Administration of Partially Biodegradable Sodium Alginate Microspheres. 61
33498971 2021
37
Right Ventricular Extracellular Volume with Dual-Layer Spectral Detector CT: Value in Chronic Thromboembolic Pulmonary Hypertension. 61
33497315 2021
38
Radiological differences between chronic thromboembolic pulmonary disease (CTEPD) and chronic thromboembolic pulmonary hypertension (CTEPH). 61
33507354 2021
39
Chronic thromboembolic pulmonary hypertension due to an implantable cardioverter-defibrillator's lead thrombosis. 61
33524614 2021
40
Interventional and pharmacological management of chronic thromboembolic pulmonary hypertension. 61
33465538 2021
41
Recurrent chronic thromboembolic disease despite optimal anticoagulation in setting of recent COVID-19 infection. 61
33509878 2021
42
Does kidney function matter in pulmonary thromboembolism management? 61
33470418 2021
43
Chronic thromboembolic pulmonary hypertension and totally implantable central venous access systems. 61
32675214 2021
44
Neutrophil extracellular traps promote fibrous vascular occlusions in chronic thrombosis. 61
33512471 2020
45
Balloon Pulmonary Angioplasty for Inoperable Chronic Thromboembolic Pulmonary Hypertension: First Experience at the Israeli National CTEPH Referral Center. 61
33381946 2020
46
Preoperative right ventricular strain predicts sustained right ventricular dysfunction after balloon pulmonary angioplasty in patients with chronic thromboembolic pulmonary hypertension. 61
33107156 2020
47
Why, Whom, and How to Screen for Chronic Thromboembolic Pulmonary Hypertension after Acute Pulmonary Embolism. 61
33348411 2020
48
[A retrospective study of balloon pulmonary angioplasty for chronic thromboembolic pulmonary hypertension]. 61
33333638 2020
49
A Survey-based Estimate of COVID-19 Incidence and Outcomes among Patients with Pulmonary Arterial Hypertension or Chronic Thromboembolic Pulmonary Hypertension and Impact on the Process of Care. 61
32726561 2020
50
Riociguat treatment in patients with pulmonary arterial hypertension: Final safety data from the EXPERT registry. 61
33422952 2020

Variations for Pulmonary Hypertension, Chronic Thromboembolic, Without Deep Vein...

Expression for Pulmonary Hypertension, Chronic Thromboembolic, Without Deep Vein...

Search GEO for disease gene expression data for Pulmonary Hypertension, Chronic Thromboembolic, Without Deep Vein Thrombosis.

Pathways for Pulmonary Hypertension, Chronic Thromboembolic, Without Deep Vein...

GO Terms for Pulmonary Hypertension, Chronic Thromboembolic, Without Deep Vein...

Sources for Pulmonary Hypertension, Chronic Thromboembolic, Without Deep Vein...

3 CDC
7 CNVD
9 Cosmic
10 dbSNP
11 DGIdb
17 EFO
18 ExPASy
19 FMA
20 GARD
28 GO
29 GTR
30 HMDB
31 HPO
32 ICD10
33 ICD10 via Orphanet
34 ICD9CM
35 IUPHAR
36 KEGG
37 LifeMap
39 LOVD
41 MedGen
44 MeSH
45 MESH via Orphanet
46 MGI
49 NCI
50 NCIt
51 NDF-RT
53 NINDS
54 Novoseek
56 OMIM via Orphanet
57 OMIM® (Updated 05-Mar-2021)
61 PubMed
63 QIAGEN
68 SNOMED-CT via HPO
69 TGDB
70 Tocris
71 UMLS
72 UMLS via Orphanet
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