MCID: PLM064
MIFTS: 22

Pulmonary Sequestration

Categories: Blood diseases, Cardiovascular diseases, Fetal diseases, Rare diseases, Respiratory diseases

Aliases & Classifications for Pulmonary Sequestration

MalaCards integrated aliases for Pulmonary Sequestration:

Name: Pulmonary Sequestration 20

Classifications:



Summaries for Pulmonary Sequestration

GARD : 20 Pulmonary sequestration is a rare congenital (present from birth) malformation where non-functioning lung tissue is separated from the rest of the lung and supplied with blood from an unusual source, often an artery from systemic circulation. Pulmonary sequestrations may be defined as intralobular or extralobular, depending on their location. Symptoms may include a chronic or recurrent cough, respiratory distress or lung infection. Treatment depends on the location and may involve surgery.

MalaCards based summary : Pulmonary Sequestration is related to congenital pulmonary sequestration and intralobar congenital pulmonary sequestration. An important gene associated with Pulmonary Sequestration is DICER1 (Dicer 1, Ribonuclease III). Affiliated tissues include lung, neutrophil and fetal lung.

Wikipedia : 73 A pulmonary sequestration is a medical condition wherein a piece of tissue that ultimately develops into... more...

Related Diseases for Pulmonary Sequestration

Diseases in the Pulmonary Sequestration family:

Congenital Pulmonary Sequestration

Diseases related to Pulmonary Sequestration via text searches within MalaCards or GeneCards Suite gene sharing:

(show top 50) (show all 158)
# Related Disease Score Top Affiliating Genes
1 congenital pulmonary sequestration 11.2
2 intralobar congenital pulmonary sequestration 11.1
3 extralobar congenital pulmonary sequestration 11.1
4 virus-associated trichodysplasia spinulosa 10.5
5 bronchogenic cyst 10.5
6 diaphragmatic hernia, congenital 10.4
7 bronchiectasis 10.4
8 total anomalous pulmonary venous return 1 10.4
9 aspergillosis 10.4
10 aneurysm 10.3
11 hydrops fetalis, nonimmune 10.3
12 lymphatic malformation 7 10.3
13 diaphragmatic eventration 10.2
14 pneumothorax 10.2
15 ventricular septal defect 10.2
16 heart septal defect 10.2
17 pleural empyema 10.2
18 polyhydramnios 10.2
19 pulmonary hypertension 10.2
20 lung abscess 10.2
21 neuroblastoma 10.2
22 cyanosis, transient neonatal 10.1
23 respiratory failure 10.1
24 bronchopneumonia 10.1
25 teratoma 10.1
26 dextrocardia 10.1
27 atrial standstill 1 10.1
28 gastroesophageal reflux 10.1
29 emphysema, congenital lobar 10.1
30 pectus excavatum 10.1
31 patent ductus arteriosus 1 10.1
32 dilated cardiomyopathy 10.1
33 aortic aneurysm 10.1
34 pneumonia 10.1
35 vasculitis 10.1
36 carcinoid syndrome 10.1
37 cystic adenomatoid malformation of lung 10.1
38 immune hydrops fetalis 10.1
39 hernia, hiatus 10.0
40 meckel diverticulum 10.0
41 triiodothyronine receptor auxiliary protein 10.0
42 williams-beuren syndrome 10.0
43 infective endocarditis 10.0
44 dextro-looped transposition of the great arteries 10.0
45 benign teratoma 10.0
46 endocarditis 10.0
47 atrial heart septal defect 10.0
48 benign mesothelioma 10.0
49 cystic teratoma 10.0
50 congestive heart failure 10.0

Graphical network of the top 20 diseases related to Pulmonary Sequestration:



Diseases related to Pulmonary Sequestration

Symptoms & Phenotypes for Pulmonary Sequestration

Drugs & Therapeutics for Pulmonary Sequestration

Search Clinical Trials , NIH Clinical Center for Pulmonary Sequestration

Genetic Tests for Pulmonary Sequestration

Anatomical Context for Pulmonary Sequestration

MalaCards organs/tissues related to Pulmonary Sequestration:

40
Lung, Neutrophil, Fetal Lung, Bone Marrow, Endothelial, Pancreas, Lymph Node

Publications for Pulmonary Sequestration

Articles related to Pulmonary Sequestration:

(show top 50) (show all 1603)
# Title Authors PMID Year
1
Intralobar pulmonary sequestration in an adult female patient mimicking asthma: a case report. 61 20
25159547 2014
2
Identical twins concordant for pulmonary sequestration communicating with the esophagus and discordant for the VACTERL association. 20 61
15937657 2005
3
Familial recurrence of pulmonary sequestration. 61 20
8677110 1996
4
Pulmonary sequestration: What the radiologist should know. 61
33310586 2021
5
Combined surgical therapy for pulmonary sequestration and aberrant artery from the abdominal aorta. 61
33743137 2021
6
Video-assisted thoracoscopic right lower lobectomy for pulmonary sequestration supplied by a large feeding vessel from the abdominal aorta. 61
32721070 2021
7
A Modified VATS Procedure for Treating Adult Intralobar Pulmonary Sequestration. 61
33202478 2021
8
Three-dimensional computed tomography and indocyanine green-guided technique for pulmonary sequestration surgery. 61
33074471 2021
9
Prenatal Imaging Diagnosis of Suprarenal Lesions. 61
33730724 2021
10
Thoracoscopic Management of Pediatric Patients with Congenital Lung Malformations: Results of a European Multicenter Survey. 61
33428520 2021
11
Bilateral pulmonary sequestration complicated with a bibasal pneumonia in an adult patient. 61
33363681 2021
12
Rare cause of haemoptysis: bronchopulmonary sequestration. 61
33653840 2021
13
Incidence and outcomes of patients with congenital diaphragmatic hernia and pulmonary sequestration. 61
33752909 2021
14
Reference range of fetal thorax using two-dimensional and three-dimensional ultrasound VOCAL technique and application in fetal thoracic malformations. 61
33618694 2021
15
Video-assisted thoracoscopic surgery: The preferred method to manage pulmonary sequestration. 61
33605934 2021
16
Intraoperative real-time hemodynamics in intralobar pulmonary sequestration using indocyanine green and near-infrared thoracoscopy. 61
32761512 2021
17
An uncommon cause of massive haemothorax and treatment under cardiopulmonary bypass. 61
33537705 2021
18
Successful endovascular treatment of intralobar pulmonary sequestration - an effective alternative to surgery. 61
33758636 2021
19
Combined endovascular and surgical approaches to treat intralobar pulmonary sequestration: a case report. 61
32969253 2021
20
Preoperative Embolization Facilitates Segmental Resection of Pulmonary Sequestration in an Infant. 61
33532170 2021
21
Extralobar Supradiaphragmatic Pulmonary Sequestration Arising from the Retroperitoneum Through a Congenital Diaphragmatic Defect. 61
33767019 2021
22
Neurally-Adjusted Ventilatory Assist Can Facilitate Extubation in Neonates With Congenital Diaphragmatic Hernia. 61
32753531 2021
23
Imaging of solid congenital abdominal masses: a review of the literature and practical approach to image interpretation. 61
33252758 2020
24
Neutrophil extracellular traps are not produced in pediatric patients with one-lung ventilation: a prospective, single-center, observational study. 61
33457299 2020
25
Synergistic effects of EMPs and PMPs on pulmonary vascular leakage and lung injury after ischemia/reperfusion. 61
33225929 2020
26
Succinate Activation of SUCNR1 Predisposes Severely Injured Patients to Neutrophil-Mediated ARDS. 61
33214479 2020
27
Hybrid and Endovascular Treatment of Pulmonary Sequestration: Two Case Reports and Literature Review. 61
32745655 2020
28
Treatment of an Aberrant Arterial Aneurysm with Intralobar Pulmonary Sequestration: A Case Report. 61
32768541 2020
29
Extralobar pulmonary sequestration with elevated serum neuron-specific enolase: A case report and review of the literature. 61
33019470 2020
30
Giant Pulmonary Sequestration Presented as a Paravertebral Mass. 61
33115602 2020
31
Lung ultrasound completely replaced chest X-ray for diagnosing neonatal lung diseases: a 3-year clinical practice report from a neonatal intensive care unit in China. 61
33032479 2020
32
Intralobar pulmonary sequestration: incidental finding in an asymptomatic patient. 61
32874379 2020
33
Pulmonary Sequestration Associated with Actinomycosis: A Case Report. 61
33050328 2020
34
Pulmonary intralobar sequestration associated with aspergillosis and aspiration. 61
33088511 2020
35
[UNILATERAL MULTI-CYSTIC LUNG DISEASE IN A PRETERM INFANT]. 61
33103392 2020
36
Anomalous Systemic Arterial Supply to the Lung: To Which Category Should This Belong? 61
32349946 2020
37
Ganglioneurofibroma arising within the extralobar pulmonary sequestration. 61
32917239 2020
38
Treatment for hemoptysis after percutaneous closure of a large intralobar pulmonary sequestration in elderly patient. 61
33117424 2020
39
Macrophage Subpopulation Dynamics Shift following Intravenous Infusion of Mesenchymal Stromal Cells. 61
32531238 2020
40
Extralobar pulmonary sequestration with a cyst: a case report. 61
32953769 2020
41
How to optimize the treatment strategy for patients of pulmonary sequestration with an elevated risk of fatal hemorrhage during operation: case discussion. 61
32944358 2020
42
Use of a vascular plug to block an anomalous artery originating from the descending aorta in a patient with pulmonary sequestration. 61
32182343 2020
43
Novel Findings on SPECT-CT Tc-99 Sestamibi Imaging for Primary Hyperparathyroidism. 61
32289578 2020
44
Congenital intrathoracic accessory spleen is a very rare trick of nature: a case report. 61
32867804 2020
45
Postnatally diagnosed coexisting congenital diaphragmatic hernia with pulmonary sequestration: a report of two cases. 61
32689778 2020
46
Extralobar pulmonary sequestration with a complication of torsion: A case report and literature review. 61
32702859 2020
47
Intralobar Pulmonary Sequestration With A Patent Bronchus; A Rare Presentation. 61
32829564 2020
48
Surgical treatment of pulmonary sequestration in adults and children: long-term results. 61
32300793 2020
49
Intrapulmonary Sequestration: A Rare Occurrence. 61
32642370 2020
50
Feasibility investigation of uniportal video-assisted thoracoscopic anatomical lung resection for pulmonary sequestration. 61
32404207 2020

Variations for Pulmonary Sequestration

Expression for Pulmonary Sequestration

Search GEO for disease gene expression data for Pulmonary Sequestration.

Pathways for Pulmonary Sequestration

GO Terms for Pulmonary Sequestration

Sources for Pulmonary Sequestration

3 CDC
7 CNVD
9 Cosmic
10 dbSNP
11 DGIdb
17 EFO
18 ExPASy
19 FMA
20 GARD
28 GO
29 GTR
30 HMDB
31 HPO
32 ICD10
33 ICD10 via Orphanet
34 ICD9CM
35 IUPHAR
36 KEGG
37 LifeMap
39 LOVD
41 MedGen
44 MeSH
45 MESH via Orphanet
46 MGI
49 NCI
50 NCIt
51 NDF-RT
53 NINDS
54 Novoseek
56 OMIM via Orphanet
57 OMIM® (Updated 05-Apr-2021)
61 PubMed
63 QIAGEN
68 SNOMED-CT via HPO
69 Tocris
70 UMLS
71 UMLS via Orphanet
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