MCID: VLV038
MIFTS: 23

Vulvar Sarcoma

Categories: Cancer diseases, Reproductive diseases

Aliases & Classifications for Vulvar Sarcoma

MalaCards integrated aliases for Vulvar Sarcoma:

Name: Vulvar Sarcoma 12 15
Sarcoma of Vulva 12 70
Vulva Sarcoma 17

Classifications:



External Ids:

Disease Ontology 12 DOID:2096
NCIt 50 C40317
SNOMED-CT 67 254897006
UMLS 70 C0238525

Summaries for Vulvar Sarcoma

Disease Ontology : 12 A vulva cancer that has material basis in connective tissue.

MalaCards based summary : Vulvar Sarcoma, also known as sarcoma of vulva, is related to spindle cell sarcoma and sarcoma. An important gene associated with Vulvar Sarcoma is ZNF444 (Zinc Finger Protein 444). Affiliated tissues include kidney, ovary and myeloid.

Related Diseases for Vulvar Sarcoma

Diseases related to Vulvar Sarcoma via text searches within MalaCards or GeneCards Suite gene sharing:

(show top 50) (show all 67)
# Related Disease Score Top Affiliating Genes
1 spindle cell sarcoma 30.0 EWSR1 CD34
2 sarcoma 30.0 SMARCB1 NR4A3 EWSR1
3 epithelioid sarcoma 29.9 SMARCB1 CD34
4 fibrous histiocytoma 29.6 EWSR1 CD34
5 vulvar leiomyosarcoma 11.1
6 vulvar alveolar soft part sarcoma 11.1
7 vulvar liposarcoma 11.1
8 glomangiosarcoma 10.1 ZNF444 CD34
9 central nervous system angiosarcoma 10.1 SMARCB1 CD34
10 leiomyosarcoma 10.1
11 plexiform schwannoma 10.1 SMARCB1 CD34
12 kidney rhabdoid cancer 10.1 SMARCB1 EWSR1
13 rhabdoid cancer 10.1 SMARCB1 EWSR1
14 retroperitoneal sarcoma 10.1 SMARCB1 CD34
15 cellular schwannoma 10.1 SMARCB1 CD34
16 epithelioid malignant peripheral nerve sheath tumor 10.1 SMARCB1 CD34
17 olfactory nerve neoplasm 10.1 SMARCB1 EWSR1
18 epithelial-myoepithelial carcinoma 10.1 SMARCB1 PLAG1
19 cranial nerve malignant neoplasm 10.1 SMARCB1 EWSR1
20 kidney fibrosarcoma 10.1 SMARCB1 EWSR1
21 central epithelioid sarcoma 10.1 SMARCB1 CD34
22 vulvar leiomyoma 10.1 PLAG1 CD34
23 vulvar proximal-type epithelioid sarcoma 10.1 SMARCB1 CD34
24 cranial nerve neoplasm 10.0 SMARCB1 EWSR1
25 clear cell meningioma 10.0 SMARCB1 CD34
26 kidney clear cell sarcoma 10.0 SMARCB1 EWSR1
27 lung sarcoma 10.0 EWSR1 CD34
28 bladder leiomyoma 10.0 EWSR1 CD34
29 mixed cell type cancer 10.0 PLAG1 CD34
30 epithelioid cell synovial sarcoma 10.0 EWSR1 CD34
31 pediatric fibrosarcoma 10.0 EWSR1 CD34
32 bladder sarcoma 10.0 EWSR1 CD34
33 peritoneal benign neoplasm 10.0 CD34 ACTG2
34 mesenchymal cell neoplasm 9.9 EWSR1 CD34
35 neurilemmoma 9.9 SMARCB1 CD34
36 connective tissue benign neoplasm 9.9 EWSR1 CD34
37 neuroma 9.9 SMARCB1 CD34
38 pseudosarcomatous fibromatosis 9.9 CD34 ACTG2
39 ewing sarcoma 9.9
40 clear cell sarcoma 9.9
41 myeloid sarcoma 9.9
42 posttransplant acute limbic encephalitis 9.9
43 myxofibrosarcoma 9.9 EWSR1 CD34
44 myxoid chondrosarcoma 9.9 SMARCB1 NR4A3 EWSR1
45 skin benign neoplasm 9.9 EWSR1 CD34
46 sweat gland disease 9.9 ZNF444 PLAG1 EWSR1
47 myoepithelioma 9.9 SMARCB1 PLAG1 EWSR1
48 rhabdomyosarcoma 2 9.8
49 dermatofibrosarcoma protuberans 9.8
50 malignant fibrous histiocytoma 9.8

Graphical network of the top 20 diseases related to Vulvar Sarcoma:



Diseases related to Vulvar Sarcoma

Symptoms & Phenotypes for Vulvar Sarcoma

Drugs & Therapeutics for Vulvar Sarcoma

Search Clinical Trials , NIH Clinical Center for Vulvar Sarcoma

Genetic Tests for Vulvar Sarcoma

Anatomical Context for Vulvar Sarcoma

MalaCards organs/tissues related to Vulvar Sarcoma:

40
Kidney, Ovary, Myeloid, Bone, Skeletal Muscle, Lung, Skin

Publications for Vulvar Sarcoma

Articles related to Vulvar Sarcoma:

(show all 32)
# Title Authors PMID Year
1
Vulvar sarcoma outcomes by histologic subtype: a Surveillance, Epidemiology, and End Results (SEER) database review. 61
32641392 2020
2
Myeloid Sarcoma Of Vulva: A Short Update. 61
27408359 2016
3
Clear cell sarcoma of vulva. A case report. 61
27869448 2016
4
Primary Ewing sarcoma of vulva, confirmed with molecular cytogenetic analysis: A rare case report with diagnostic and treatment implications. 61
26275259 2015
5
Vulvar sarcomas: Short guideline for histopathological recognition and clinical management. Part 2. 61
25816393 2015
6
SMARCB1-deficient Vulvar Neoplasms: A Clinicopathologic, Immunohistochemical, and Molecular Genetic Study of 14 Cases. 61
25651469 2015
7
A rare association between neurofibromatosis type 1 and vulvar sarcoma. 61
24819769 2014
8
Primary Ewing's sarcoma of vulva: a case report and a review of the literature. 61
23106919 2013
9
Case of lung carcinoma revealed by vulvar metastasis associated with systemic scleroderma and literature review. 61
24416551 2013
10
Primary metastasized extraskeletal Ewing sarcoma of the vulva: report of a case and review of the literature. 61
21805144 2012
11
Sarcoma of vulva, vagina and ovary. 61
21816677 2011
12
Pleomorphic type of malignant fibrous histiocytoma with myxoid stroma of the vulva in a young woman. 61
21564409 2011
13
Pregnancy and genital sarcoma: a systematic review of the literature. 61
19288396 2009
14
A case of epithelioid sarcoma arising in the vulva. 61
19471567 2008
15
Leiomyosarcoma of the vulva: a case report. 61
16285585 2005
16
Rapid growth of myxoid leiomyosarcoma of the vulva during pregnancy: a case report. 61
14764049 2004
17
Epithelioid sarcoma of vulva: a case report and review of the literature. 61
15579921 2004
18
Vulvar epithelioid sarcoma in pregnancy. 61
11925150 2002
19
[Sarcoma of vulva: a clinical retrospective analysis of 10 cases]. 61
8565697 1995
20
Vulvar sarcoma: clinical implications. 61
7821491 1994
21
Vulvar sarcoma: a report of four cases. 61
1526519 1992
22
Vulvar leiomyosarcoma in pregnancy. 61
2301486 1990
23
Malignant fibrous histiocytoma of the vulva. 61
3032755 1987
24
Dermatofibrosarcoma protuberans of the vulva. 61
6629128 1983
25
Nodular fasciitis (pseudosarcomatous fasciitis) of the vulva. 61
7185766 1982
26
Pregnancy and sarcoma. 61
665173 1978
27
[Vulvar sarcoma (apropos of 3 cases)]. 61
340829 1977
28
[Vulvar sarcoma (clinical study of 3 cases)]. 61
4824378 1974
29
[Vulvar sarcoma; apropos of 3 cases]. 61
5153229 1971
30
[Vulvar sarcoma in childhood]. 61
4910012 1969
31
[A contribution to the clinical aspects and histology of vulvar sarcoma]. 61
5728882 1968
32
[A rare case of vulvar sarcoma in the region of Bartholin's glands (hemangioendothelial sarcoma)]. 61
14439074 1960

Variations for Vulvar Sarcoma

Expression for Vulvar Sarcoma

Search GEO for disease gene expression data for Vulvar Sarcoma.

Pathways for Vulvar Sarcoma

GO Terms for Vulvar Sarcoma

Cellular components related to Vulvar Sarcoma according to GeneCards Suite gene sharing:

# Name GO ID Score Top Affiliating Genes
1 cell periphery GO:0071944 8.62 CD34 ACTG2

Biological processes related to Vulvar Sarcoma according to GeneCards Suite gene sharing:

# Name GO ID Score Top Affiliating Genes
1 positive regulation of gene expression GO:0010628 8.8 PLAG1 CD34 ACTG2

Sources for Vulvar Sarcoma

3 CDC
7 CNVD
9 Cosmic
10 dbSNP
11 DGIdb
17 EFO
18 ExPASy
19 FMA
20 GARD
28 GO
29 GTR
30 HMDB
31 HPO
32 ICD10
33 ICD10 via Orphanet
34 ICD9CM
35 IUPHAR
36 KEGG
37 LifeMap
39 LOVD
41 MedGen
44 MeSH
45 MESH via Orphanet
46 MGI
49 NCI
50 NCIt
51 NDF-RT
53 NINDS
54 Novoseek
56 OMIM via Orphanet
57 OMIM® (Updated 20-May-2021)
61 PubMed
63 QIAGEN
68 SNOMED-CT via HPO
69 Tocris
70 UMLS
71 UMLS via Orphanet
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